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ORII Koji  折居 恒治

ORCIDConnect your ORCID iD *help
Researcher Number 30377668
Affiliation (based on the past Project Information) *help 2006: GIFU UNIVERSITY, GRADUATE SCHOOL OF MEDICINE, PART-TIME LECTURER, 医学系研究科, 非常勤講師
2006: 岐阜大学, 大学院医学系研究科, 非常勤講師
2005: 岐阜大学, 医学部, 非常勤講師
2005: 岐阜大学, 大学院・医学系研究科, 助手
Review Section/Research Field
Principal Investigator
Pediatrics
Except Principal Investigator
Pediatrics
Keywords
Principal Investigator
カタラーゼ染色 / 軽症型変異 / ペルオキシソーム病 / ケミカルシャペロン / 温度感受性 / Zellweger症候群
Except Principal Investigator
SCREEN SYSTEM OF PEROXISOMAL DISEASES / LIFE-STYLE RELATED DISEASE / FATTY ACID β-OXIDATION / PEROXISOME … More / ペルオキシソーム病診断システム / 先天異常 / 生活習慣病 / ペルオキシソーム Less
  • Research Projects

    (2 results)
  • Research Products

    (5 results)
  • Co-Researchers

    (1 People)
  •  ケミカルシャペロンを用いたペルオキシソーム病治療の基礎的研究Principal Investigator

    • Principal Investigator
      折居 恒治
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Young Scientists (B)
    • Research Field
      Pediatrics
    • Research Institution
      Gifu University
  •  PATHOGENIC MECHANISM OF CONGENITAL ANOMALY AND LIFE-STYLE RELATED DISEASES BASED ON PEROXISOMAL METABOLISM

    • Principal Investigator
      SHIMOZAWA Nobuyuki
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Gifu University

All 2006 2005

All Journal Article Book

  • [Book] けいれん、意識障害を起こす疾患の治療・管理のポイント 有機酸代謝異常症2006

    • Author(s)
      折居 恒治, 深尾 敏幸
    • Total Pages
      3
    • Publisher
      東京医学社
    • Data Source
      KAKENHI-PROJECT-17790697
  • [Journal Article] Portal hypertension in a patient with Hunter disease.2006

    • Author(s)
      Kato T, Isogai K, Orii K, Kuratsubo I, Kondo N, Orii T, Suzuki Y
    • Journal Title

      J Inherit Metab Dis 29(5)

      Pages: 686-686

    • Data Source
      KAKENHI-PROJECT-17790697
  • [Journal Article] Development of MPS IVA mouse (Galnstm(hC79S.mC76S)slu) tolerant to human N-acetylgalactosamine-6-sulfate sulfatase.2005

    • Author(s)
      Tomatsu S, Gutierrez M, Nishioka T, Yamada M, Yamada M, Tosaka Y, Grubb JH, Montano AM, Vieira MB, Trandafirescu GG, Pena OM, Yamaguchi S, Orii KO, Orii T, Noguchi A, Laybauer L.
    • Journal Title

      Hum Mol Genet. 14(22)

      Pages: 3321-3335

    • Data Source
      KAKENHI-PROJECT-17790697
  • [Journal Article] Defining the pathway for Tat-mediated delivery of beta-glucuronidase in cultured cells and MPS VII mice.2005

    • Author(s)
      Orii KO, Grubb JH, Vogler C, Levy B, Tan Y, Markova K, Davidson BL, Mao Q, Orii T, Kondo N, Sly WS
    • Journal Title

      Mol Ther. 12(2)

      Pages: 345-352

    • Data Source
      KAKENHI-PROJECT-17790697
  • [Journal Article] Keratan sulphate levels in mucopolysaccharidoses and mucolipidoses.2005

    • Author(s)
      Tomatsu S, Okamura K, Maeda H, Taketani T, Castrillon SV, Gutierrez MA, Nishioka T, Fachel AA, Orii KO, Grubb JH, Cooper A, Thornley M, Wraith E, Barrera LA, Laybauer LS, Giugliani R, Schwartz IV, Frenking GS, Beck M, Kircher SG, Paschke E, Yamaguchi S, Ullrich K, Haskins M, Isogai K, Suzuki Y, Orii T, Kondo N, Creer M, Okuyama T, Tanaka A, Noguchi A.
    • Journal Title

      J Inherit Metab Dis. 28(2)

      Pages: 187-202

    • Data Source
      KAKENHI-PROJECT-17790697
  • 1.  SHIMOZAWA Nobuyuki (00240797)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results

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