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NAKANISHI Koichi  中西 浩一

… Alternative Names

中西 浩一  ナカニシ コウイチ

Less
Researcher Number 50336880
Other IDs
  • ORCIDhttps://orcid.org/0000-0001-8681-9129
External Links
Affiliation (Current) 2025: 琉球大学, 医学(系)研究科(研究院), 教授
Affiliation (based on the past Project Information) *help 2017 – 2023: 琉球大学, 医学(系)研究科(研究院), 教授
2015 – 2016: 和歌山県立医科大学, 医学部, 准教授
2004 – 2014: 和歌山県立医科大学, 医学部, 講師
2004: Wakayama Medical University, Department of Pediatrics, Lecturer, 小児科, 講師
2002 – 2004: 和歌山県立医科大学, 医学部, 助手
Review Section/Research Field
Principal Investigator
Pediatrics / Basic Section 52050:Embryonic medicine and pediatrics-related / Pediatrics
Except Principal Investigator
Pediatrics / Basic Section 52050:Embryonic medicine and pediatrics-related / Embryonic/Neonatal medicine / Kidney internal medicine
Keywords
Principal Investigator
多発性嚢胞腎 / WT1 / 増殖 / 分泌 / 上皮間葉移行 / 細胞外基質 / ACTN4 / NPHS2 / NPHS1 / 疾患特異的治療 … More / miRNA / CD2AP / α-Actinin-4 / podocin / nephrin / 糸球体上皮細胞 / α-アクチニン4 / ポドシン / ネフリン / 先天性ネフローゼ症候群 / 多発性のう胞腎 / TRPV4 / 組織トランスグルタミナーゼ / 脂質メディエーター / 遺伝子 / スリット膜 / 先天性ネフローゼ症候 / Congenital nephrotic syndrome / 遺伝子変異 / 線維化 / マイクロアレイ / マイクロRNA / 上皮間葉移行(EMT) / ユビキチン・プロテアソーム / CPKマウス / N-cadherin / β-catenin / E-cadherin / 間葉系マーカー / PCKラット / 遺伝性腎疾患 … More
Except Principal Investigator
IgA腎症 / 紫斑病性腎炎 / 腎生検組織 / 腎生検 / 尿バイオマーカー / 免疫複合体 / 糖鎖異常IgA1特異的IgG / 糖鎖異常IgA1 / Gd- IgA1特異的IgG / 血中Gd-IgA1 / 小児IgA腎症 / 血中バイオマーカー / ステロイド抵抗性 / 慢性GVHD / CD4+CD28null / CD4+CD28null T細胞 / ステロイド抵抗性慢性移植片対宿主病 / 長寿命B細胞 / CD38陽性細胞 / 原発性シェ-グレン症候群 / 小児期発症シェーグレン症候群 / 小児期発症リウマチ性疾患 / 長寿命細胞 / 小児期発症原発性シェーグレン症候群 / pSS / 小児期シェーグレン症候群 / FACS解析 / CD138 / CD38 / 腺症状 / 腺外症状 / 一次性シェーグレン症候群 / 小児期発症自己免疫疾患 / 小児紫斑病性腎炎 / 紫斑病勢腎炎 / 非侵襲的診断 / 蛋白尿 / 疾患活動性 / KIM-1 / Smad3部位特異的リン酸化 / 多発性嚢胞腎 / smad3リン酸化 / smadリン酸化 / cpkマウス / 嚢胞性腎疾患 / microRNA / 小児IgA腎症 / gene / slit diaahraam / glomerular podocyte / glomerular capillary wall / nephritic syndrome / 遺伝子 / スリット膜 / 糸球体上皮細胞 / 糸球体係蹄壁 / ネフローゼ症候群 / hemolytic uremic syndrome / hemorrhagic colitis / Verotoxin (VT)-producing / 溶血性尿毒症症候群 / 腸管出血性大腸菌 / ベロ毒素産生 / 開発 / 新治療法 / IL-18 / IL-1β / caspase 1 / NLRP3 / インフラマソーム / マイクロサテライトマーカー / 乳児ネフローゼ症候群 / 先天性ネフローゼ症候群 / PLEC1 / ラミニンβ2 / WT1 / ポドシン / ネフリン Less
  • Research Projects

    (19 results)
  • Research Products

    (301 results)
  • Co-Researchers

    (17 People)
  •  TRPV4の多面的作用に着目した多発性嚢胞腎病態に基づく疾患特異的治療の開発Principal Investigator

    • Principal Investigator
      中西 浩一
    • Project Period (FY)
      2023 – 2025
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52050:Embryonic medicine and pediatrics-related
    • Research Institution
      University of the Ryukyus
  •  Involvement of glycosylated IgA1 and its specific IgG in pediatric IgA nephropathy and IgA vasculitis with nephritis

    • Principal Investigator
      島 友子
    • Project Period (FY)
      2023 – 2025
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52050:Embryonic medicine and pediatrics-related
    • Research Institution
      Wakayama Medical University
  •  CD4+CD28-T細胞を標的としたステロイド抵抗性慢性GVHDの治療開発

    • Principal Investigator
      浜田 聡
    • Project Period (FY)
      2022 – 2024
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52050:Embryonic medicine and pediatrics-related
    • Research Institution
      University of the Ryukyus
  •  小児期シェーグレン症侯群におけるCD38による腺外組織障害への進展機序の解明

    • Principal Investigator
      金城 紀子
    • Project Period (FY)
      2021 – 2024
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52050:Embryonic medicine and pediatrics-related
    • Research Institution
      University of the Ryukyus
  •  Development of disease-specific treatments based on pathophysiology of polycystic kidney disease with a focus on tissue transglutaminasePrincipal Investigator

    • Principal Investigator
      Nakanishi Koichi
    • Project Period (FY)
      2020 – 2022
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52050:Embryonic medicine and pediatrics-related
    • Research Institution
      University of the Ryukyus
  •  Development of a new diagnostic method for pediatric HSPN using urinary biomarkers

    • Principal Investigator
      Shima Yuko
    • Project Period (FY)
      2018 – 2021
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52050:Embryonic medicine and pediatrics-related
    • Research Institution
      Wakayama Medical University
  •  Development of disease-specific therapy based on polycystic kidney disease pathophysiology focusing on lipid mediatorsPrincipal Investigator

    • Principal Investigator
      Nakanishi Koichi
    • Project Period (FY)
      2017 – 2019
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      University of the Ryukyus
  •  Elucidation of pathology and development of therapeutic agents in polycystic kidney disease focusing on Smad3 site-specific phosphorylation

    • Principal Investigator
      Sato Masashi
    • Project Period (FY)
      2017 – 2019
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Embryonic/Neonatal medicine
    • Research Institution
      Wakayama Medical University
  •  Establishment of new diagnostic biomarker for childhood IgA nephropathy

    • Principal Investigator
      Shima Yuko
    • Project Period (FY)
      2015 – 2018
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Wakayama Medical University
  •  Development of disease specific therapy based on pathophysiology of IgA nephropathy focusing on microRNA

    • Principal Investigator
      Yoshikawa Norishige
    • Project Period (FY)
      2015 – 2017
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Wakayama Medical University
  •  Development of disease specific therapy based on microRNA in polycystic kidney diseasePrincipal Investigator

    • Principal Investigator
      Nakanishi Koichi
    • Project Period (FY)
      2014 – 2016
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Wakayama Medical University
  •  Role of imflammasome in IgA nephropathy

    • Principal Investigator
      YOSHIKAWA Norishige
    • Project Period (FY)
      2012 – 2014
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Pediatrics
    • Research Institution
      Wakayama Medical University
  •  Disease specific therapy of polycystic kidney disease based on its pathophysiology considering the ubiquitin-proteasome proteolysis mechanismPrincipal Investigator

    • Principal Investigator
      NAKANISHI Koichi
    • Project Period (FY)
      2011 – 2013
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Wakayama Medical University
  •  Mutation analysis in Japanese patients with congenital and infantile nephritic syndrome

    • Principal Investigator
      YOSHIKAWA Norishige
    • Project Period (FY)
      2009 – 2011
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Wakayama Medical University
  •  Epithelial-to-mesenchymal transition (EMT) in polycystic kidney diseasePrincipal Investigator

    • Principal Investigator
      NAKANISHI Koichi
    • Project Period (FY)
      2008 – 2010
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Wakayama Medical University
  •  Genetic analysis of glomerular podocyte molecules in children with nephrotic syndrome

    • Principal Investigator
      YOSHIKAWA Norishige
    • Project Period (FY)
      2006 – 2007
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Wakayama Medical University
  •  Analysis of NPHS1, NPHS2, ACTN4, WT1 and CD2AP in Japanese patients with congenital nephrotic syndromePrincipal Investigator

    • Principal Investigator
      KOICHI Nakanishi
    • Project Period (FY)
      2005 – 2007
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Wakayama Medical University
  •  Genetic analysis in children with Escherichia coli O157-associated hemolytic uremic syndrome

    • Principal Investigator
      YOSHIKAWA Norishige
    • Project Period (FY)
      2003 – 2004
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Kidney internal medicine
    • Research Institution
      Wakayama Medical University
  •  Analysis of NPHS1, NPHS2, ACTN4 and WT1 in Japanese patients with congenital nephrotic syndromePrincipal Investigator

    • Principal Investigator
      NAKANISHI Koichi
    • Project Period (FY)
      2002 – 2004
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Wakayama Medical University

All 2023 2022 2021 2020 2019 2018 2017 2016 2015 2014 2013 2012 2011 2010 2009 2008 2007 2006 2005 2004 Other

All Journal Article Presentation Book

  • [Book] アルポート症候群診療ガイドライン 2017 Ⅱ.疫学・予後2017

    • Author(s)
      2.飯島一誠、柏原直樹、中西浩一、井藤奈央子、楠原仙太郎、朽方豊夢、島友子、仲野敦子、野津寛大、濱田陸、林宏樹、南川将吾、山村智彦
    • Total Pages
      89
    • Publisher
      診断と治療社
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Book] Pediatric Nephrology 7th edition2016

    • Author(s)
      Nakanishi K, Yoshikawa N
    • Total Pages
      2730
    • Publisher
      Springer
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Book] 遺伝学的検査・診断・遺伝カウンセリングの上手な進め方2016

    • Author(s)
      中西浩一
    • Total Pages
      217
    • Publisher
      診断と治療社
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Book] のう胞性腎疾患.「疾患からみる画像診断の進め方・読み方(小児科診療増刊号)」2015

    • Author(s)
      中西浩一、吉川徳茂
    • Total Pages
      348
    • Publisher
      診断と治療社、東京
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Book] こどもの病気遺伝について聞かれたら2015

    • Author(s)
      中西浩一
    • Total Pages
      260
    • Publisher
      診断と治療社
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Book] 多発性のう胞腎診療ガイドQ&A改訂第2版2015

    • Author(s)
      中西浩一
    • Total Pages
      184
    • Publisher
      診断と治療社
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Book] Immunoglobulin A nephropathies in children (includes HSP). "Pediatric Nephrology 7th ed."2015

    • Author(s)
      Nakanishi K, Yoshikawa N
    • Total Pages
      2730
    • Publisher
      Springer, Heidelberg
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Book] 疾患からみる画像診断の進め方・読み方(小児科診療増刊号)2015

    • Author(s)
      中西浩一、吉川徳茂
    • Total Pages
      348
    • Publisher
      診断と治療社
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Book] Pediatric Nephrology 7th ed.2015

    • Author(s)
      Nakanishi K, Yoshikawa N
    • Total Pages
      2730
    • Publisher
      Springer, Heidelberg
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Book] 臨床腎臓内科学2013

    • Author(s)
      中西浩一, 吉川徳茂
    • Total Pages
      1051
    • Publisher
      南山堂
    • Data Source
      KAKENHI-PROJECT-24390265
  • [Book] 遺伝性嚢胞性疾患. 臨床腎臓内科学2013

    • Author(s)
      中西浩一, 吉川徳茂
    • Publisher
      南山堂
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Book] 多発性嚢胞腎 14章 腎・尿細管機能異常 嚢胞性疾患 多発性嚢胞腎 「先天代謝異常ハンドブック」2013

    • Author(s)
      中西浩一,吉川徳茂(総編集 遠藤文夫 専門編集 山口清次,大浦敏博,奥山虎之)
    • Publisher
      中山書店 東京
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Book] 遺伝性嚢胞性疾患.臨床腎臓内科学2013

    • Author(s)
      中西浩一,吉川徳茂(安田隆,平和伸仁,小山雄太編)
    • Publisher
      南山堂 東京
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Book] 小児科診断・治療ガイド2012

    • Author(s)
      中西浩一,吉川徳茂
    • Total Pages
      1132
    • Publisher
      中山書店
    • Data Source
      KAKENHI-PROJECT-24390265
  • [Book] 小児科診療75巻増刊 【小児の診療手技100】2012

    • Author(s)
      島友子,中西浩一,吉川徳茂
    • Total Pages
      474
    • Publisher
      診断と治療社
    • Data Source
      KAKENHI-PROJECT-24390265
  • [Book] 小児疾患の診断治療基準 第4版 小児内科44増刊号2012

    • Author(s)
      中西浩一,吉川徳茂
    • Total Pages
      960
    • Publisher
      東京医学社
    • Data Source
      KAKENHI-PROJECT-24390265
  • [Book] 腎疾患治療マニュアル2012-20132012

    • Author(s)
      中西浩一,吉川徳茂
    • Total Pages
      754
    • Publisher
      東京医学社
    • Data Source
      KAKENHI-PROJECT-24390265
  • [Book] 多発性嚢胞腎(小児) 「腎疾患治療マニュアル2012-2013」2012

    • Author(s)
      中西浩一,吉川徳茂( 編集 「腎と透析」編集委員会)
    • Publisher
      東京医学社
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Book] 腎臓症候群(第2版) -その他の腎臓疾患を含めて- 別冊日本臨床 新領域別症候群シリーズ172012

    • Author(s)
      戸川寛子,中西浩一,吉川徳茂
    • Total Pages
      859
    • Publisher
      日本臨牀社
    • Data Source
      KAKENHI-PROJECT-24390265
  • [Book] 第II部ARPKD(常染色体劣性多発性嚢胞腎) 多発性嚢胞腎診療ガイドQ&A2011

    • Author(s)
      中西浩一(監修 松尾清一 編集 堀江重郎)
    • Publisher
      診断と治療社
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Book] Alport症候群と家族性良性血尿の異同(50の典型例で学ぶ小児の腎泌尿器疾患)2011

    • Author(s)
      中西浩一, 吉川徳茂
    • Publisher
      診断と治療社
    • Data Source
      KAKENHI-PROJECT-21591396
  • [Book] ARPKD(常染色体劣性多発性嚢胞腎) 多発性嚢胞腎診療ガイドQ&A2011

    • Author(s)
      中西浩一 監修 松尾清一 編集 堀江重郎
    • Publisher
      診断と治療社
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Book] Drash症候群, 50の典型例で学ぶ小児の腎泌尿器疾患2011

    • Author(s)
      中西浩一, 吉川徳茂
    • Publisher
      診断と治療社
    • Data Source
      KAKENHI-PROJECT-21591396
  • [Book] ネフローゼ症候群(小児科疾患アルゴリズム)2009

    • Author(s)
      中西浩一, 吉川徳茂
    • Publisher
      中山書店
    • Data Source
      KAKENHI-PROJECT-21591396
  • [Book] 多発性嚢胞腎(小児疾患診療のための病態生理1-改定第4版-)(『小児内科』『小児外科』編集委員会共編)東京2008

    • Author(s)
      中西浩一, 吉川徳茂
    • Publisher
      東京医学者
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Book] 多発性嚢胞腎 小児疾患診療のための病態生理1-改定第4版-2008

    • Author(s)
      中西浩一
    • Publisher
      東京医学者
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Book] ARPKD Annual Review腎臓20072007

    • Author(s)
      中西 浩一
    • Publisher
      中外医学社
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17591111
  • [Book] New専門医を目指すケース・メソッド・アプローチ5腎臓疾患2007

    • Author(s)
      中西 浩一
    • Publisher
      日本医事新報社
    • Data Source
      KAKENHI-PROJECT-17591111
  • [Journal Article] 特集Genetics in CKD 疾患編 常染色体潜性(劣性)多発性嚢胞腎2023

    • Author(s)
      中西浩一
    • Journal Title

      腎と透析

      Volume: 94 Pages: 393-397

    • Data Source
      KAKENHI-PROJECT-23K07228
  • [Journal Article] Factors related to recurrence of proteinuria in childhood IgA nephropathy2023

    • Author(s)
      Shima Yuko、Mukaiyama Hironobu、Tanaka Yu、Shimabukuro Wataru、Nozu Kandai、Kaito Hiroshi、Tanaka Ryojiro、Sako Mayumi、Iijima Kazumoto、Tokuhara Daisuke、Yoshikawa Norishige、Nakanishi Koichi
    • Journal Title

      Pediatric Nephrology

      Volume: 39 Issue: 2 Pages: 463-471

    • DOI

      10.1007/s00467-023-06116-4

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23K07300
  • [Journal Article] Rituximab in combination with cyclosporine and steroid pulse therapy for childhood-onset multidrug-resistant nephrotic syndrome: a multicenter single-arm clinical trial (JSKDC11 trial)2023

    • Author(s)
      Nozu Kandai、Sako Mayumi、Tanaka Seiji、Kano Yuji、Ohwada Yoko、Morohashi Tamaki、Hamada Riku、Ohtsuka Yasufumi、Oka Masafumi、Kamei Koichi、Inaba Aya、Ito Shuichi、Sakai Tomoyuki、Kaito Hiroshi、Shima Yuko et al.
    • Journal Title

      Clinical and Experimental Nephrology

      Volume: 28 Issue: 4 Pages: 337-348

    • DOI

      10.1007/s10157-023-02431-0

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-23K07300, KAKENHI-PROJECT-21KK0147, KAKENHI-PROJECT-23K27617
  • [Journal Article] Long-term outcome of combination therapy with corticosteroids, mizoribine and RAS inhibitors as initial therapy for severe childhood IgA vasculitis with nephritis2023

    • Author(s)
      Nagai Sadayuki、Horinouchi Tomoko、Ninchoji Takeshi、Ichikawa Yuta、Tanaka Yu、Kitakado Hideaki、Ueda Chika、Kondo Atsushi、Aoto Yuya、Sakakibara Nana、Kaito Hiroshi、Tanaka Ryojiro、Shima Yuko、Fujimura Junya、Kamiyoshi Naohiro、Ishimori Shingo、Nakanishi Koichi、Yoshikawa Norishige、Iijima Kazumoto、Nozu Kandai
    • Journal Title

      Pediatric Nephrology

      Volume: 38 Issue: 12 Pages: 4023-4031

    • DOI

      10.1007/s00467-023-06052-3

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23K07300
  • [Journal Article] Comprehensive genetic analysis using next-generation sequencing for the diagnosis of nephronophthisis-related ciliopathies in the Japanese population2022

    • Author(s)
      Sakakibara N, Nozu K, Yamamura T, Horinouchi T, Nagano C, Ye MJ, Ishiko S, Aoto Y, Rossanti R, Hamada R, Okamoto N, Shima Y, Nakanishi K, Matsuo M, Iijima K, Morisada N.
    • Journal Title

      J Hum Genet.

      Volume: - Issue: 7 Pages: 427-440

    • DOI

      10.1038/s10038-022-01020-5

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-22K08351
  • [Journal Article] 遺伝性腎疾患2022

    • Author(s)
      中西浩一
    • Journal Title

      周産期医学

      Volume: 52 Pages: 747-750

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20K08162
  • [Journal Article] Clinical features of autosomal recessive polycystic kidney disease in the Japanese population and analysis of splicing in PKHD1 gene for determination of phenotypes2022

    • Author(s)
      Ishiko S, Morisada N, Kondo A, Nagai S, Aoto Y, Okada E, Rossanti R, Sakakibara N, Nagano C, Horinouchi T, Yamamura T, Ninchoji T, Kaito H, Hamada R, Shima Y, Nakanishi K, Matsuo M, Iijima K, Nozu K.
    • Journal Title

      Clin Exp Nephrol .

      Volume: 26 Issue: 2 Pages: 140-153

    • DOI

      10.1007/s10157-021-02135-3

    • NAID

      120007188940

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-19K08726
  • [Journal Article] 常染色体潜性多発性嚢胞腎の基礎と臨床―up date2022

    • Author(s)
      中西浩一
    • Journal Title

      医学と薬学

      Volume: 79 Pages: 927-934

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20K08162
  • [Journal Article] ARPKDの病因と病態2022

    • Author(s)
      中西浩一
    • Journal Title

      腎と透析

      Volume: 93 Pages: 489-492

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20K08162
  • [Journal Article] Use of renin-angiotensin system inhibitors as initial therapy in children with Henoch-Schonlein purpura nephritis of moderate severity2022

    • Author(s)
      Nagai S, Horinouchi T, Ninchoji T, Kondo A, Aoto Y, Ishiko S, Sakakibara N, Nagano C, Yamamura T, Kaito H, Tanaka R, Shima Y, Fujimura J, Kamiyoshi N, Ishimori S, Nakanishi K, Yoshikawa N, Iijima K, Nozu K.
    • Journal Title

      Pediatr Nephrol.

      Volume: - Issue: 8 Pages: 1845-1853

    • DOI

      10.1007/s00467-021-05395-z

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Journal Article] Efficacy of combination therapy for childhood complicated focal IgA nephropathy2022

    • Author(s)
      Aoto Y, Ninchoji T, Kaito H, Shima Y, Fujimura J, Kamiyoshi N, Ishimori S, Nakanishi K, Minamikawa S, Ishiko S, Sakakibara N, Nagano C, Horinouchi T, Yamamura T, Nagai S, Kondo A, Inaguma Y, Tanaka R, Yoshikawa N, Iijima K, Nozu K.
    • Journal Title

      Clin Exp Nephrol.

      Volume: - Issue: 6 Pages: 561-570

    • DOI

      10.1007/s10157-022-02190-4

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Journal Article] Non-immunosuppressive therapies for childhood IgA nephropathy2021

    • Author(s)
      Shima Yuko、Nakanishi Koichi、Yoshikawa Norishige
    • Journal Title

      Pediatric Nephrology

      Volume: - Issue: 10 Pages: 3057-3065

    • DOI

      10.1007/s00467-021-04954-8

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Journal Article] ARPKD 1)病態生理と治療2021

    • Author(s)
      中西浩一
    • Journal Title

      腎臓内科

      Volume: 14 Pages: 560-566

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20K08162
  • [Journal Article] 多発性嚢胞腎と移行期医療2021

    • Author(s)
      中西浩一
    • Journal Title

      腎臓内科

      Volume: 14 Pages: 184-191

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20K08162
  • [Journal Article] Examination of the predicted prevalence of Gitelman syndrome by ethnicity based on genome database2021

    • Author(s)
      Kondo A, Nagano C, Ishiko S, Omori T, Aoto Y, Rossanti R, Sakakibara N, Horinouchi T, Yamamura T, Nagai S, Okada E, Shima Y, Nakanishi K, Ninchoji T, Kaito H, Takeda H, Nagase H, Morisada N, Iijima K, Nozu K.
    • Journal Title

      Sci Rep.

      Volume: 11 Issue: 1 Pages: 16099-16099

    • DOI

      10.1038/s41598-021-95521-6

    • NAID

      120007131929

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Journal Article] Utility of glomerular Gd-IgA1 staining for indistinguishable cases of IgA nephropathy or Alport syndrome2021

    • Author(s)
      Ishiko Shinya、Tanaka Akihito、Takeda Asami、Hara Masayuki、Hamano Naoto、Koizumi Masahiro、Ueno Toshinori、Hayashi Hiroki、Kondo Atsushi、Nagai Sadayuki、Aoto Yuya、Nozu Kandai
    • Journal Title

      Clinical and Experimental Nephrology

      Volume: Epub Issue: 7 Pages: 779-787

    • DOI

      10.1007/s10157-021-02054-3

    • NAID

      120007125745

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-19K08726, KAKENHI-PROJECT-20K17295, KAKENHI-PROJECT-18K07799
  • [Journal Article] Clinicopathological significance of glomerular capillary IgA deposition in childhood IgA nephropathy2021

    • Author(s)
      Shima Y, Nakanishi K, Mukaiyama H, Tanaka Y, Wada T, Tanaka R, Kaito H, Nozu K, Sako M, Iijima K, Yoshikawa N.
    • Journal Title

      Pediatric Nephrology

      Volume: 36 Issue: 4 Pages: 899-908

    • DOI

      10.1007/s00467-020-04772-4

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Journal Article] Last Nucleotide Substitutions of COL4A5 Exons Cause Aberrant Splicing2021

    • Author(s)
      Aoto Y, Horinouchi T, Yamamura T, Kondo A, Nagai S, Ishiko S, Okada E, Rossanti R, Sakakibara N, Nagano C, Awano H, Nagase H, Shima Y, Nakanishi K, Matsuo M, Iijima K, Nozu K.
    • Journal Title

      Kidney Int Rep.

      Volume: 7 Issue: 1 Pages: 108-116

    • DOI

      10.1016/j.ekir.2021.10.012

    • NAID

      120007188929

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-19K08726
  • [Journal Article] Systematic Review of Genotype-Phenotype Correlations in Frasier Syndrome2021

    • Author(s)
      Tsuji Y, Yamamura T, Nagano C, Horinouchi T, Sakakibara N, Ishiko S, Aoto Y, Rossanti R, Okada E, Tanaka E, Tsugawa K, Okamoto T, Sawai T, Araki Y, Shima Y, Nakanishi K, Nagase H, Matsuo M, Iijima K, Nozu K.
    • Journal Title

      Kidney Int Rep .

      Volume: 6 Issue: 10 Pages: 2585-2593

    • DOI

      10.1016/j.ekir.2021.07.010

    • NAID

      120007165718

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-19K08726
  • [Journal Article] 多発性嚢胞腎2020

    • Author(s)
      中西浩一
    • Journal Title

      小児科臨床

      Volume: 73 Pages: 782-785

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20K08162
  • [Journal Article] Pathogenic evaluation of synonymous COL4A5 variants in X‐linked Alport syndrome using a minigene assay2020

    • Author(s)
      Horinouchi Tomoko、Yamamura Tomohiko、Minamikawa Shogo、Nagano China、Sakakibara Nana、Nakanishi Koichi、Shima Yuko、Morisada Naoya、Ishiko Shinya、Aoto Yuya、Nagase Hiroaki、Takeda Hiroki、Rossanti Rini、Ishimori Shingo、Kaito Hiroshi、Matsuo Masafumi、Iijima Kazumoto、Nozu Kandai
    • Journal Title

      Molecular Genetics & Genomic Medicine

      Volume: 8 Issue: 8

    • DOI

      10.1002/mgg3.1342

    • NAID

      120006879547

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-19K08726, KAKENHI-PROJECT-18K08243
  • [Journal Article] A case with somatic and germline mosaicism in COL4A5 detected by multiplex ligation-dependent probe amplification in X-linked Alport syndrome2020

    • Author(s)
      Aoto Yuya、Kise Tomoo、Nakanishi Koichi、Nagano China、Horinouchi Tomoko、Yamamura Tomohiko、Ishiko Shinya、Sakakibara Nana、Shima Yuko、Morisada Naoya、Iijima Kazumoto、Nozu Kandai
    • Journal Title

      CEN Case Reports

      Volume: 9 Issue: 4 Pages: 431-436

    • DOI

      10.1007/s13730-020-00503-8

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-18K08243
  • [Journal Article] Genotype-phenotype correlations influence the response to angiotensin-targeting drugs in Japanese patients with male X-linked Alport syndrome2020

    • Author(s)
      Yamamura Tomohiko、Horinouchi Tomoko、Nagano China、Omori Takashi、Sakakibara Nana、Aoto Yuya、Ishiko Shinya、Nakanishi Koichi、Shima Yuko、Nagase Hiroaki、Takeda Hiroki、Rossanti Rini、Ye Ming Juan、Nozu Yoshimi、Ishimori Shingo、Ninchoji Takeshi、Kaito Hiroshi、Morisada Naoya、Iijima Kazumoto、Nozu Kandai
    • Journal Title

      Kidney International

      Volume: 98 Issue: 6 Pages: 1605-1614

    • DOI

      10.1016/j.kint.2020.06.038

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-19K08726, KAKENHI-PROJECT-18K08243
  • [Journal Article] 遺伝学的に診断できた常染色体劣性多発性嚢胞腎の遺伝型と臨床像2020

    • Author(s)
      森貞直哉, 野津寛大, 中西浩一, 飯島一誠
    • Journal Title

      発達腎研究会誌

      Volume: 28 Pages: 33-35

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20K08162
  • [Journal Article] 多発性嚢胞腎-ARとADを含めて-2020

    • Author(s)
      中西浩一
    • Journal Title

      腎と透析

      Volume: 89 Pages: 856-861

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20K08162
  • [Journal Article] Comprehensive genetic diagnosis of Japanese patients with severe proteinuria.2020

    • Author(s)
      Nagano C, Yamamura T, Horinouchi T, Aoto Y, Ishiko S, Sakakibara N, Shima Y, Nakanishi K, Nagase H, Iijima K, Nozu K.
    • Journal Title

      Sci Rep.

      Volume: 10(1) Issue: 1 Pages: 428-437

    • DOI

      10.1038/s41598-019-57149-5

    • NAID

      120006884200

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-19K08726, KAKENHI-PROJECT-18KK0244, KAKENHI-PROJECT-18K15713
  • [Journal Article] Comparison of clinical and genetic characteristics between Dent disease 1 and Dent disease 22020

    • Author(s)
      Sakakibara Nana、Nagano China、Ishiko Shinya、Horinouchi Tomoko、Yamamura Tomohiko、Minamikawa Shogo、Shima Yuko、Nakanishi Koichi、Ishimori Shingo、Morisada Naoya、Iijima Kazumoto、Nozu Kandai
    • Journal Title

      Pediatric Nephrology

      Volume: 35 Issue: 12 Pages: 2319-2326

    • DOI

      10.1007/s00467-020-04701-5

    • NAID

      120007052636

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-19K08726, KAKENHI-PROJECT-18K08243
  • [Journal Article] Crescentic IgA nephropathy in children.2020

    • Author(s)
      Shima Y, Nakanishi K, Hama T, Mukaiyama H, Sato M, Tanaka Y, Tanaka R, Kaito H, Nozu K, Sako M, Iijima K, Yoshikawa N.
    • Journal Title

      Pediatr Nephrol.

      Volume: - Issue: 6 Pages: 1005-1014

    • DOI

      10.1007/s00467-020-04483-w

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Journal Article] ARPKD2019

    • Author(s)
      中西浩一
    • Journal Title

      腎と透析

      Volume: 87 Pages: 744-748

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K10150
  • [Journal Article] Determination of the pathogenicity of known COL4A5 intronic variants by in vitro splicing assay.2019

    • Author(s)
      Horinouchi T, Nozu K, Yamamura T, Minamikawa S, Nagano C, Sakakibara N, Nakanishi K, Shima Y, Morisada N, Ishiko S, Aoto Y, Nagase H, Takeda H, Rossanti R, Kaito H, Matsuo M, Iijima K.
    • Journal Title

      Sci Rep.

      Volume: 9(1) Issue: 1 Pages: 12696-12696

    • DOI

      10.1038/s41598-019-48990-9

    • NAID

      120006825910

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-18K08243, KAKENHI-PROJECT-19K08726, KAKENHI-PROJECT-17H04189, KAKENHI-PROJECT-18K15712
  • [Journal Article] Clinical spectrum of male patients with OFD1 mutations.2019

    • Author(s)
      Sakakibara N, Morisada N, Nozu K, Nagatani K, Ohta T, Shimizu J, Wada T, Shima Y, Yamamura T, Minamikawa S, Fujimura J, Horinouchi T, Nagano C, Shono A, Ye MJ, Nozu Y, Nakanishi K, Iijima K.
    • Journal Title

      J Hum Genet.

      Volume: 64 Issue: 1 Pages: 3-9

    • DOI

      10.1038/s10038-018-0532-x

    • NAID

      120006888530

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-18K08243, KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-16K10066
  • [Journal Article] Comparison between conventional and comprehensive sequencing approaches for genetic diagnosis of Alport syndrome.2019

    • Author(s)
      Yamamura T, Nozu K, Minamikawa S, Horinouchi T, Sakakibara N, Nagano C, Aoto Y, Ishiko S, Nakanishi K, Shima Y, Nagase H, Rossanti R, Ye MJ, Nozu Y, Ishimori S, Morisada N, Kaito H, Iijima K.
    • Journal Title

      Mol Genet Genomic Med.

      Volume: 7(9) Issue: 9

    • DOI

      10.1002/mgg3.883

    • NAID

      120006733124

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-18K08243, KAKENHI-PROJECT-19K08726, KAKENHI-PROJECT-17H04189
  • [Journal Article] ADPKDの最近の知見2019

    • Author(s)
      中西浩一
    • Journal Title

      日本腎臓学会誌

      Volume: 61 Pages: 1098-1101

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K10150
  • [Journal Article] Lisinopril versus lisinopril and losartan for mild childhood IgA nephropathy: a randomized controlled trial (JSKDC01 study).2019

    • Author(s)
      Shima Y, Nakanishi K, Sako M, Saito-Oba M, Hamasaki Y, Hataya H, Honda M, Kamei K, Ishikura K, Ito S, Kaito H, Tanaka R, Nozu K, Nakamura H, Ohashi Y, Iijima K, Yoshikawa N; Japanese Study Group of Kidney Disease in Children (JSKDC).
    • Journal Title

      Pediatr Nephrol.

      Volume: 34 Issue: 5 Pages: 837-846

    • DOI

      10.1007/s00467-018-4099-8

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-15K09694
  • [Journal Article] Clinicopathological characteristics and renal outcomes of childhood-onset lupus nephritis with acute kidney injury: A multicenter study.2018

    • Author(s)
      Ishimori S, Kaito H, Shima Y, Kamioka I, Hamahira K, Nozu K, Nakanishi K, Tanaka R, Yoshikawa N, Iijima K.
    • Journal Title

      Mod Rheumatol.

      Volume: 印刷中 Issue: 6 Pages: 970-976

    • DOI

      10.1080/14397595.2018.1532861

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-15K09694
  • [Journal Article] Serine Protease Inhibitor Kazal Type I (SPINK1) Mutation: A Risk Factor for Early-onset Chronic Pancreatitis?2018

    • Author(s)
      Hama T, Nakanishi N, Suzuki M, Shima Y, Suzuki H.
    • Journal Title

      J Pediatr Gastroenterol Nutr.

      Volume: 67 Issue: 2

    • DOI

      10.1097/mpg.0000000000002024

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-15K09694
  • [Journal Article] Strong Association of the HLA-DR/DQ Locus with Childhood Steroid-Sensitive Nephrotic Syndrome in the Japanese Population.2018

    • Author(s)
      Jia X, Horinouchi T, Hitomi Y, Shono A, Khor SS, Omae Y, Kojima K, Kawai Y, Nagasaki M, Kaku Y, Okamoto T, Ohwada Y, Ohta K, Okuda Y, Fujimaru R, Hatae K, Kumagai N, Sawanobori E, Nakazato H, Ohtsuka Y, Nakanishi K, Shima Y, Tanaka R, Ashida A, Kamei K, Ishikura K, Nozu K, Tokunaga K, Iijima K
    • Journal Title

      J Am Soc Nephrol.

      Volume: 29 Issue: 8 Pages: 2189-2199

    • DOI

      10.1681/asn.2017080859

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-18KK0244, KAKENHI-PLANNED-18H05511, KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-16K10066
  • [Journal Article] Clinical and Genetic Characteristics in Patients With Gitelman Syndrome.2018

    • Author(s)
      Fujimura J, Nozu K, Yamamura T, Minamikawa S, Nakanishi K, Horinouchi T, Nagano C, Sakakibara N, Nakanishi K, Shima Y, Miyako K, Nozu Y, Morisada N, Nagase H, Ninchoji T, Kaito H, Iijima K.
    • Journal Title

      Kidney Int Rep.

      Volume: 4 Issue: 1 Pages: 119-125

    • DOI

      10.1016/j.ekir.2018.09.015

    • NAID

      120006847258

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-18K08243, KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-19K08726
  • [Journal Article] Detection of Splicing Abnormalities and Genotype-Phenotype Correlation in X-linked Alport Syndrome.2018

    • Author(s)
      Horinouchi T, Nozu K, Yamamura T, Minamikawa S, Omori T, Nakanishi K, Fujimura J, Ashida A, Kitamura M, Kawano M, Shimabukuro W, Kitabayashi C, Imafuku A, Tamagaki K, Kamei K, Okamoto K, Fujinaga S, Oka M, Igarashi T, Miyazono A, Sawanobori E, Fujimaru R, Nakanishi K, Shima Y et al
    • Journal Title

      J Am Soc Nephrol.

      Volume: 29 Issue: 8 Pages: 2244-2254

    • DOI

      10.1681/asn.2018030228

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-18K08243, KAKENHI-PROJECT-17H04189, KAKENHI-PROJECT-15K09694
  • [Journal Article] Study protocol: high-dose mizoribine with prednisolone therapy in short-term relapsing steroid-sensitive nephrotic syndrome to prevent frequent relapse (JSKDC05 trial).2018

    • Author(s)
      Hama T, Nakanishi K, Ishikura K, Ito S, Nakamura H, Sako M, Saito-Oba M, Nozu K, Shima Y, Iijima K, Yoshikawa N; Japanese Study Group of Kidney Disease in Children (JSKDC).
    • Journal Title

      BMC Nephrol.

      Volume: 19 Issue: 1 Pages: 223-223

    • DOI

      10.1186/s12882-018-1033-z

    • NAID

      120006523804

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-18KK0244, KAKENHI-PROJECT-15K09694
  • [Journal Article] Combination therapy with or without warfarin and dipyridamole for severe childhood IgA nephropathy: an RCT.2018

    • Author(s)
      Shima Y, Nakanishi K, Kaku Y, Ishikura K, Hataya H, Matsuyama T, Honda M, Sako M, Nozu K, Tanaka R, Iijima K, Yoshikawa N; Japanese Pediatric IgA Nephropathy Treatment Study Group.
    • Journal Title

      Pediatr Nephrol.

      Volume: 33 Issue: 11 Pages: 2103-2112

    • DOI

      10.1007/s00467-018-4011-6

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-15K09694
  • [Journal Article] Development of ultra-deep targeted RNA sequencing for analyzing X-chromosome inactivation in female Dent disease2018

    • Author(s)
      Minamikawa S, Nozu K, Nozu Y, Yamamura T, Taniguchi-Ikeda M, Nakanishi K, Fujimura J, Horinouchi T, Shima Y, Nakanishi K, Hattori M, Kanda K, Tanaka R, Morisada N, Nagano C, Sakakibara N, Nagase H, Morioka I, Kaito H, Iijima K.
    • Journal Title

      Journal of Human Genetics

      Volume: 63 Issue: 5 Pages: 589-595

    • DOI

      10.1038/s10038-018-0415-1

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-15K09261, KAKENHI-PROJECT-15K09691, KAKENHI-PROJECT-18K07799, KAKENHI-PROJECT-18K08243
  • [Journal Article] Natural History and Genotype?Phenotype Correlation in Female X-Linked Alport Syndrome2017

    • Author(s)
      Yamamura Tomohiko、Nozu Kandai、Fu Xue Jun、Nozu Yoshimi、Ye Ming Juan、Shono Akemi、Yamanouchi Satoko、Minamikawa Shogo、Morisada Naoya、Nakanishi Koichi、Shima Yuko、Yoshikawa Norishige、Ninchoji Takeshi、Morioka Ichiro、Kaito Hiroshi、Iijima Kazumoto
    • Journal Title

      Kidney Int Rep.

      Volume: 2 Issue: 5 Pages: 850-855

    • DOI

      10.1016/j.ekir.2017.04.011

    • NAID

      120006373817

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-16K10066, KAKENHI-PROJECT-26293203, KAKENHI-PROJECT-17H04189, KAKENHI-PROJECT-15K09695, KAKENHI-PROJECT-16K19642
  • [Journal Article] Crescentic IgA nephropathy in a child: Effect of a new combination therapy2017

    • Author(s)
      Okamoto M, Yokoyama N, Nozu K, Nakanishi K, Yoshikawa N
    • Journal Title

      Pediatr Int

      Volume: 59 Issue: 4 Pages: 501-503

    • DOI

      10.1111/ped.13225

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Journal Article] Diagnostic strategy for inherited hypomagnesemia.2017

    • Author(s)
      Horinouchi T, Nozu K, Kamiyoshi N, Kamei K, Togawa H, Shima Y, Urahama Y, Yamamura T, Minamikawa S, Nakanishi K, Fujimura J, Morioka I, Ninchoji T, Kaito H, Nakanishi K, Iijima K.
    • Journal Title

      Clin Exp Nephrol.

      Volume: 印刷中 Issue: 6 Pages: 1003-1010

    • DOI

      10.1007/s10157-017-1396-7

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-15K09691
  • [Journal Article] IgA nephropathy with presentation of nephrotic syndrome at onset in children.2017

    • Author(s)
      Shima Y, Nakanishi K, Sato M, Hama T, Mukaiyama H, Togawa H, Tanaka R, Nozu K, Sako M, Iijima K, Suzuki H, Yoshikawa N.
    • Journal Title

      Pediatr Nephrol.

      Volume: 32(3) Issue: 3 Pages: 457-465

    • DOI

      10.1007/s00467-016-3502-6

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-15K09695
  • [Journal Article] High incidence of idiopathic nephrotic syndrome in East Asian children: a nationwide survey in Japan (JP-SHINE study)2017

    • Author(s)
      Kikunaga K, Ishikura K, Terano C, Sato M, Komaki F, Hamasaki Y, Sasaki S, Iijima K, Yoshikawa N, Nakanishi K, Nakazato H, Matsuyama T, Ando T, Ito S, Honda M, On behalf of the Japanese Pediatric Survey Holding Information of Nephrotic syndrome (JP-SHINE) study of the Japanese Study Group of Renal Disease in Children
    • Journal Title

      Clin Exp Nephrol

      Volume: in press Issue: 5 Pages: 889-894

    • DOI

      10.1007/s10157-016-1376-3

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Journal Article] Aberrant Smad3 phosphoisoforms in cyst-lining epithelial cells in the cpk mouse, a model of autosomal recessive polycystic kidney disease2017

    • Author(s)
      Hama Taketsugu、Nakanishi Koichi、Sato Masashi、Mukaiyama Hironobu、Togawa Hiroko、Shima Yuko、Miyajima Masayasu、Nozu Kandai、Nagao Shizuko、Takahashi Hisahide、Sako Mayumi、Iijima Kazumoto、Yoshikawa Norishige、Suzuki Hiroyuki
    • Journal Title

      American Journal of Physiology-Renal Physiology

      Volume: 313 Issue: 6 Pages: F1223-F1231

    • DOI

      10.1152/ajprenal.00697.2016

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-17K10150, KAKENHI-PROJECT-17K16278, KAKENHI-PROJECT-15K08435, KAKENHI-PROJECT-15K09695
  • [Journal Article] ARPKDの診断と治療2016

    • Author(s)
      中西浩一
    • Journal Title

      腎と透析増刊

      Volume: 80増刊 Pages: 425-427

    • Data Source
      KAKENHI-PROJECT-26461618
  • [Journal Article] Somatic mosaicism and variant frequency detected by next-generation sequencing in X-linked Alport syndrome.2016

    • Author(s)
      Fu XJ, Nozu K, Kaito H, Ninchoji T, Morisada N, Nakanishi K, Yoshikawa N, Ohtsubo H, Matsunoshita N, Kamiyoshi N, Matsumura C, Takagi N, Maekawa K, Taniguchi-Ikeda M, Iijima K
    • Journal Title

      Eur J Hum Genet

      Volume: 24 Issue: 3 Pages: 387-391

    • DOI

      10.1038/ejhg.2015.113

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-26461618, KAKENHI-PROJECT-26293203, KAKENHI-PROJECT-26860800, KAKENHI-PROJECT-15K09695
  • [Journal Article] Pathogenesis of hypokalemia in autosomal dominant hypocalcemia type 1.2016

    • Author(s)
      Kamiyoshi N, Nozu K, Urahama Y, Matsunoshita N, Yamamura T, Minamikawa S, Ninchoji T, Morisada N, Nakanishi K, Kaito H, Iijima K.
    • Journal Title

      Clin Exp Nephrol.

      Volume: 20 Issue: 2 Pages: 253-257

    • DOI

      10.1007/s10157-015-1160-9

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-15K09691, KAKENHI-PROJECT-26461618, KAKENHI-PROJECT-26293203, KAKENHI-PROJECT-26860800, KAKENHI-PROJECT-15K09261
  • [Journal Article] X-linked Alport syndrome associated with a synonymous p.Gly292Gly mutation alters the splicing donor site of the type IV collagen alpha chain 5 gene.2016

    • Author(s)
      Fu XJ, Nozu K, Eguchi A, Nozu Y, Morisada N, Shono A, Taniguchi-Ikeda M, Shima Y, Nakanishi K, Vorechovsky I, Iijima K.
    • Journal Title

      Clin Exp Nephrol.

      Volume: 20(5) Pages: 699-702

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Journal Article] Insignificant impact of VUR on the progression of CKD in children with CAKUT.2016

    • Author(s)
      Ishikura K, Uemura O, Hamasaki Y, Nakai H, Ito S, Harada R, Hattori M, Ohashi Y, Tanaka R, Nakanishi K, Kaneko T, Iijima K, Honda M; Pediatric CKD Study Group in Japan in conjunction with the Committee of Measures for Pediatric CKD of the Japanese Society for Pediatric Nephrology
    • Journal Title

      Pediatr Nephrol

      Volume: 31 Issue: 1 Pages: 105-112

    • DOI

      10.1007/s00467-015-3196-1

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-26461618, KAKENHI-PROJECT-25461637, KAKENHI-PROJECT-26293203, KAKENHI-PROJECT-15H04880
  • [Journal Article] Genetic, Clinical, and Pathologic Backgrounds of Patients with Autosomal Dominant Alport Syndrome.2016

    • Author(s)
      Kamiyoshi N, Nozu K, Fu XJ, Morisada N, Nozu Y, Ye MJ, Imafuku A, Miura K, Yamamura T, Minamikawa S, Shono A, Ninchoji T, Morioka I, Nakanishi K, Yoshikawa N, Kaito H, Iijima K
    • Journal Title

      Clin J Am Soc Nephrol.

      Volume: 11 Issue: 8 Pages: 1441-1449

    • DOI

      10.2215/cjn.01000116

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-26293203, KAKENHI-PROJECT-15K09261, KAKENHI-PROJECT-15K09682, KAKENHI-PROJECT-15K09695, KAKENHI-PROJECT-16K10066
  • [Journal Article] Congenital nephrotic syndrome with a novel NPHS1 mutation2016

    • Author(s)
      Yoshizawa C, Kobayashi Y, Ikeuchi Y, Tashiro M, Kakegawa S, Watanabe T, Goto Y, Nakanishi K, Yoshikawa N, Arakawa H
    • Journal Title

      Pediatr Int

      Volume: 58 Issue: 4 Pages: 1211-1215

    • DOI

      10.1007/s10157-016-1319-z

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Journal Article] Differential diagnosis of Bartter syndrome, Gitelman syndrome, and pseudo-Bartter/Gitelman syndrome based on clinical characteristics2016

    • Author(s)
      Matsunoshita N, Nozu K, Shono A, Nozu Y, Fu XJ, Morisada N, Kamiyoshi N, Ohtsubo H, Ninchoji T, Minamikawa S, Yamamura T, Nakanishi K, Yoshikawa N, Shima Y, Kaito H, Iijima K
    • Journal Title

      Genetics in Medicine

      Volume: 18 Issue: 2 Pages: 180-188

    • DOI

      10.1038/gim.2015.56

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-15K09691, KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-26461618, KAKENHI-PROJECT-26860800, KAKENHI-PROJECT-26293203, KAKENHI-PROJECT-15K09695
  • [Journal Article] マイクロRNAに着目した多発性のう胞腎疾患特異的治療の開発2016

    • Author(s)
      中西浩一
    • Journal Title

      別冊BIO Clinica

      Volume: 5 Pages: 148-151

    • Data Source
      KAKENHI-PROJECT-26461618
  • [Journal Article] ARPKDの診療指針2016

    • Author(s)
      中西浩一
    • Journal Title

      腎と透析

      Volume: 80 Pages: 835-840

    • Data Source
      KAKENHI-PROJECT-26461618
  • [Journal Article] Long-term outcome of childhood IgA nephropathy with minimal proteinuria.2015

    • Author(s)
      Higa A, Shima Y, Hama T, Sato M, Mukaiyama H, Togawa H, Tanaka R, Nozu K, Sako M, Iijima K, Nakanishi K, Yoshikawa N.
    • Journal Title

      Pediatr Nephrol.

      Volume: 30(12) Issue: 12 Pages: 2121-7

    • DOI

      10.1007/s00467-015-3176-5

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-15K09695, KAKENHI-PROJECT-26461618, KAKENHI-PROJECT-26293203
  • [Journal Article] Renal biopsy criterion in idiopathic nephrotic syndrome with microscopic hematuria at onset2015

    • Author(s)
      Hama T, Nakanishi K, Shima Y, Sato M, Mukaiyama H, Togawa H, Hamahira K, Tanaka R, Kaito H, Nozu K, Iijima K, Yoshikawa N
    • Journal Title

      Pediatr Nephrol

      Volume: 30 Issue: 3 Pages: 445-450

    • DOI

      10.1007/s00467-014-2946-9

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24390265, KAKENHI-PROJECT-24791082, KAKENHI-PROJECT-26461618, KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-15K09695
  • [Journal Article] A multicenter randomized trial indicates initial prednisolone treatment for childhood nephrotic syndrome for two months is not inferior to six-month treatment2015

    • Author(s)
      Yoshikawa N, Nakanishi K, Sako M, Oba MS, Mori R, Ota E, Ishikura K, Hataya H, Honda M, Ito S, Shima Y, Kaito H, Nozu K, Nakamura H, Igarashi T, Ohashi Y, Iijima K
    • Journal Title

      Kidney Int

      Volume: 87 Issue: 1 Pages: 225-232

    • DOI

      10.1038/ki.2014.260

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-24390265, KAKENHI-PROJECT-24791082, KAKENHI-PROJECT-26461618, KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-15K09695, KAKENHI-PROJECT-25461637
  • [Journal Article] Morbidity in children with frequently relapsing nephrosis:10-year follow-up of a randomized controlled trial2015

    • Author(s)
      Ishikura K, Yoshikawa N, Nakazato H, Sasaki S, Nakanishi K, Matsuyama T, Ito S, Hamasaki Y, Yata N, Ando T, Iijima K, Honda M
    • Journal Title

      Pediatr Nephrol

      Volume: 30 Issue: 3 Pages: 459-468

    • DOI

      10.1007/s00467-014-2955-8

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Journal Article] 私の処方 IgA腎症・紫斑病性腎炎2015

    • Author(s)
      中西浩一、吉川徳茂
    • Journal Title

      小児科臨床

      Volume: 68 Pages: 809-815

    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Journal Article] Risk factors for persistent proteinuria after a 2-year combination therapy for severe childhood IgA nephropathy2015

    • Author(s)
      Kamei K, Nakanishi K, Ito S, Ishikura K, Hataya H, Honda M, Nozu K, Iijima K, Shima Y, Yoshikawa N
    • Journal Title

      Pediatr Nephrol

      Volume: 30 Issue: 6 Pages: 961-967

    • DOI

      10.1007/s00467-014-3019-9

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24390265, KAKENHI-PROJECT-26461618, KAKENHI-PROJECT-15K09695
  • [Journal Article] Biopsy timing and Oxford classification variables in childhood/adolescent IgA nephropathy.2015

    • Author(s)
      Shima Y, Nakanishi K, Hama T, Sato M, Mukaiyama H, Togawa H, Tanaka R, Kaito H, Nozu K, Iijima K, Yoshikawa N.
    • Journal Title

      Pediatric Nephrollogy

      Volume: 30(2) Issue: 2 Pages: 293-9

    • DOI

      10.1007/s00467-014-2862-z

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24791082, KAKENHI-PROJECT-15K09694, KAKENHI-PROJECT-15K09695
  • [Journal Article] Growth impairment in children with pre-dialysis chronic kidney disease in Japan.2015

    • Author(s)
      Hamasaki Y, Ishikura K, Uemura O, Ito S, Wada N, Hattori M, Ohashi Y, Tanaka R, Nakanishi K, Kaneko T, Honda M
    • Journal Title

      Clin Exp Nephrol

      Volume: 19 Issue: 6 Pages: 1142-1148

    • DOI

      10.1007/s10157-015-1098-y

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-26461618, KAKENHI-PROJECT-25461637
  • [Journal Article] 小児期発症のADPKDとARPKD2015

    • Author(s)
      中西浩一、吉川徳茂
    • Journal Title

      腎臓内科・泌尿器科

      Volume: 1 Pages: 212-218

    • NAID

      40022582482

    • Data Source
      KAKENHI-PROJECT-26461618
  • [Journal Article] 小児期発症のADPKDとARPKD2015

    • Author(s)
      中西浩一、吉川徳茂
    • Journal Title

      腎臓内科・泌尿器科

      Volume: 1 Pages: 212-218

    • NAID

      40022582482

    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Journal Article] 多発性嚢胞腎:診断と治療に関する最新の知見2014

    • Author(s)
      中西浩一, 吉川徳茂
    • Journal Title

      小児科診療

      Volume: 77 Pages: 757-762

    • Data Source
      KAKENHI-PROJECT-26461618
  • [Journal Article] シクロホスファミド【ネフローゼ症候群と治療:エビデンスと使い方】2014

    • Author(s)
      中西浩一, 吉川徳茂
    • Journal Title

      腎と透析

      Volume: 76 Pages: 846-849

    • Data Source
      KAKENHI-PROJECT-24390265
  • [Journal Article] 酸塩基平衡異常への輸液療法2014

    • Author(s)
      中西浩一, 吉川徳茂
    • Journal Title

      わかる輸液 小児科学レクチャー

      Volume: 4 Pages: 690-695

    • Data Source
      KAKENHI-PROJECT-24390265
  • [Journal Article] Rituximab for childhood-onset, complicated, frequently relapsing nephrotic syndrome steroid-dependent nephrotic syndrome: a multicentre, double-blind, randomised, placebo-controlled trial2014

    • Author(s)
      Iijima K, Sako M, Nozu K, Mori R, Tuchida N, Kamei K, Miura K, Aya K, Nakanishi K, Ohtomo Y, Takahashi S, Tanaka R, Kaito H, Nakamura H, Ishikura K, Ito S, Ohashi Y.
    • Journal Title

      Lancet

      Volume: 384 Issue: 9950 Pages: 1273-1281

    • DOI

      10.1016/s0140-6736(14)60541-9

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24591569, KAKENHI-PROJECT-26461618
  • [Journal Article] Natural history of genetically proven autosomal recessive Alport syndrome2014

    • Author(s)
      Oka M, Nozu K, Kaito H, Fu XJ, Nakanishi K, Hashimura Y, Morisada N, Yan K, Matsuo M, Yoshikawa N, Vorechovsky I, Iijima K
    • Journal Title

      Pediatr Nephrol

      Volume: 29 Issue: 9 Pages: 1535-1544

    • DOI

      10.1007/s00467-014-2797-4

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24390265, KAKENHI-PROJECT-25893131, KAKENHI-PROJECT-26293203, KAKENHI-PROJECT-26461618
  • [Journal Article] 多発性嚢胞腎:診断と治療に関する最新の知見2014

    • Author(s)
      中西浩一, 吉川徳茂
    • Journal Title

      小児科診療

      Volume: 77 Pages: 757-762

    • Data Source
      KAKENHI-PROJECT-24390265
  • [Journal Article] Milder clinical aspects of X-linked Alport syndrome in men positive for the collagen IV α5 chain2014

    • Author(s)
      Hashimura Y, Nozu K, Kaito H, Nakanishi K, Fu XJ, Ohtsubo H, Hashimoto F, Oka M, Ninchoji T, Ishimori S, Morisada N, Matsunoshita N, Kamiyoshi N, Yoshikawa N, Iijima K
    • Journal Title

      Kidney Int

      Volume: 85 Issue: 5 Pages: 1208-1213

    • DOI

      10.1038/ki.2013.479

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24390265, KAKENHI-PROJECT-25893131, KAKENHI-PROJECT-26293203, KAKENHI-PROJECT-26461618
  • [Journal Article] Cyclosporine C2 Monitoring for the Treatment of Frequently Relapsing Nephrotic Syndrome in Children: A Multicenter Randomized Phase II Trial.2014

    • Author(s)
      Iijima K, Sako M, Oba MS, Ito S, Hataya H, Tanaka R, Ohwada Y, Kamei K, Ishikura K, Yata N, Nozu K, Honda M, Nakamura H, Nagata M, Ohashi Y, Nakanishi K, Yoshikawa N. : Japanese Study Group of Kidney Disease in Children.
    • Journal Title

      Clin J Am Soc Nephrol

      Volume: 9(2) Issue: 2 Pages: 271-8

    • DOI

      10.2215/cjn.13071212

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591192, KAKENHI-PROJECT-24390265, KAKENHI-PROJECT-25461637, KAKENHI-PROJECT-26461618
  • [Journal Article] 臨床研究の結果のみかた.2014

    • Author(s)
      中西浩一, 吉川徳茂
    • Journal Title

      小児内科

      Volume: 46増刊 Pages: 12-18

    • Data Source
      KAKENHI-PROJECT-24390265
  • [Journal Article] Telmisartan ameliorates fibrocystic liver disease in an orthologous rat model of human autosomal recessive polycystic kidney disease.2013

    • Author(s)
      Yoshihara D, Kugita M, Sasaki M, Horie S, Nakanishi K, Abe T, Aukema HA, Yamaguchi T, Nagao S.
    • Journal Title

      PLoS One

      Volume: 8 Issue: 12 Pages: e81480-e81480

    • DOI

      10.1371/journal.pone.0081480

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591580, KAKENHI-PROJECT-24790393
  • [Journal Article] Two-year outcome of the ISKDC regimen and frequent-relapsing risk in children with idiopathic nephrotic syndrome2013

    • Author(s)
      Koichi Nakanishi、Kazumoto Iijima、Kenji Ishikura、Satoshi Sasak、Masataka Honda、Norio Yosikawa
    • Journal Title

      Clin J Am Soc Nephrol

      Volume: Vol.8 Issue: 5 Pages: 756-762

    • DOI

      10.2215/cjn.09010912

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591176, KAKENHI-PROJECT-23591192, KAKENHI-PROJECT-24390265
  • [Journal Article] ARPKDの基礎と臨床-最新の知見特集:多発性嚢胞腎-最新の知見と今後の課題2012

    • Author(s)
      中西浩一,吉川徳茂
    • Journal Title

      日本腎臓学会誌

      Volume: 54(4) Pages: 534-537

    • Data Source
      KAKENHI-PROJECT-23591580
  • [Journal Article] 繊毛病(Ciliopathy)2012

    • Author(s)
      中西浩一,吉川徳茂
    • Journal Title

      日本小児腎臓病学会雑誌

      Volume: 25(2) Pages: 127-131

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Journal Article] 常染色体劣性多発性嚢胞腎-疫学と臨床.特集:多発性嚢胞腎2012

    • Author(s)
      中西浩一,吉川徳茂,服部元史
    • Journal Title

      腎臓

      Volume: 34(3) Pages: 194-200

    • Data Source
      KAKENHI-PROJECT-23591580
  • [Journal Article] Epithelial-to-mesenchymal transition in cyst-lining epithelial cells in an orthologous PCK rat model of autosomal-recessive polycystic kidney disease.2011

    • Author(s)
      Togawa H, Nakanishi K, Yoshikawa N
    • Journal Title

      Am J Physiol Renal Physiol

      Volume: 300

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Journal Article] The relationship between arginine vasopressin levels and hyponatremia following a percutaneous renal biopsy in children receiving hypotonic or isotonic intravenous fluids2011

    • Author(s)
      Kanda K, Nozu K, Kaito H, Iijima K, Nakanishi K, Yoshikawa N, Ninchoji T, Hashimura Y, Matsuo M, Moritz ML
    • Journal Title

      Pediatr Nephrol

      Volume: 26 Pages: 99-104

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] Recurrent EIARF and PRES with Severe Renal Hypouricemia by Compound Heterozygous SLC2A9 Mutation2011

    • Author(s)
      Shima Y, Nozu K, Nozu Y, Togawa H, Kaito H, Matsuo M, Iijima K, Nakanishi K, Yoshikawa N
    • Journal Title

      Pediatrics

      Volume: 127

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] 多発性嚢胞腎診療指針2011

    • Author(s)
      乳原善文, 香村衡一, 木村理, 嶋村剛, 田邉一成, 土谷健, 成田一衛, 中西浩一, 西尾妙織, 奴田原紀久雄, 野村信介, 花岡一成, 東原英二, 堀江重郎, 武藤智, 望月俊雄
    • Journal Title

      日本腎臓学会誌

      Volume: 53 Pages: 556-583

    • NAID

      10029736800

    • Data Source
      KAKENHI-PROJECT-23591580
  • [Journal Article] Japanese pediatric IgA nephropathy treatment study group. Long-term results of a randomized controlled trial in childhood IgA nephropathy2011

    • Author(s)
      Kamei K, Nakanishi K, Ito S, Saito M, Sako M, Ishikura K, Hataya H, Honda M, Iijima K, Yoshikawa N
    • Journal Title

      Clin J Am Soc Nephrol

      Volume: 6 Pages: 1301-1307

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] Epithelial-to-mesenchymal transition in cyst-lining epithelial cells in an orthologous PCK rat model of autosomal-recessive polycystic kidney disease.2011

    • Author(s)
      Togawa H, Nakanishi K, Mukaiyama H, Hama T, Shima Y, Sako M, Miyajima M, Nozu K, Nishii K, Nagao S, Takahashi H, Iijima K, Yoshikawa N.
    • Journal Title

      Am J Physiol Renal Physiol. 300(2)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Journal Article] 進行性腎障害に関する調査研究班多発性嚢胞腎分科会厚生労働省進行性腎障害調査研究班多発性嚢胞腎診療指針2010年8月(解説)2010

    • Author(s)
      乳原善文,香村衡一,木村理,嶋村剛,田邉一成,土谷健,成田一衛,中西浩一,西尾妙織,奴田原紀久雄,野村信介,花岡一成,東原英二,堀江重郎,武藤智,望月俊雄
    • Journal Title

      日本腎臓学会誌

      Volume: 53 Pages: 556-583

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Journal Article] Japanese study group of renal disease in children. Treatment with microemulsified cyclosporine in children with frequently relapsing nephrotic syndrome2010

    • Author(s)
      Ishikura K, Yoshikawa N, Hattori S, Sasaki S, Iijima K, Nakanishi K, Matsuyama T, Yata N, Ando T, Honda M
    • Journal Title

      Nephrol Dial Transplant

      Volume: 25 Pages: 3956-3962

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] The Pharmacological Characteristics of Molecular-Based Inherited Salt-Losing Tubulopathies2010

    • Author(s)
      Nozu K, Iijima K, Kanda K, Nakanishi K, Yoshikawa N, Satomura K, Kaito H, Hashimura Y, Ninchoji T, Komatsu H, Kamei K, Miyashita R, Kugo M, Ohashi H, Yamazaki H, Mabe H, Otsubo A, Igarashi T, Matsuo M
    • Journal Title

      J Clin Endocrinol Metab

      Volume: 95

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] Japanese study group of renal disease in children. Cyclosporine and steroid therapy in children with steroid-resistant nephrotic syndrome2009

    • Author(s)
      Hamasaki Y, Yoshikawa N, Hattori S, Sasaki S, Iijima K, Nakanishi K, Matsuyama T, Ishikura K, Yata N, Kaneko T, Honda M
    • Journal Title

      Pediatr Nephrol

      Volume: 24 Pages: 2177-2185

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] Efficacy and safety of lisinopril for mild childhood IgA nephropathy : a pilot study2009

    • Author(s)
      Nakanishi K, Yoshikawa N
    • Journal Title

      Pediatr Nephrol 24

      Pages: 845-849

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] Increased chymase-positive mast cells in children with crescentic glomerulonephritis.2009

    • Author(s)
      Togawa H, Nakanishi K
    • Journal Title

      Pediatr Nephrol 24

      Pages: 1071-1075

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Journal Article] Increased chymase-positive mast cells in children with crescentic glomerulonephritis2009

    • Author(s)
      Togawa H, Nakanishi K, Shima Y, Obana M, Sako M, Nozu K, Tanaka R, Iijima K, Yoshikawa N
    • Journal Title

      Pediatr Nephrol

      Volume: 24 Pages: 1071-1075

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] Increased chymase-positive mast cells in children with crescentic glomerulonephritis2009

    • Author(s)
      Togawa H, Nakanishi K, Yoshikawa N
    • Journal Title

      Pediatr Nephrol 24

      Pages: 1071-1075

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] Efficacy and safety of lisinopril for mild childhood IgA nephropathy : a pilot study.2009

    • Author(s)
      Nakanishi K
    • Journal Title

      Pediatr Nephrol 24

      Pages: 845-849

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Journal Article] Detection by multiplex ligation-dependent probe amplification of large deletion mutations in the COL4A5 gene in female patients with Alport syndrome2009

    • Author(s)
      Nozu K, Krol RP, Nakanishi K, Yoshikawa N, Nozu Y, Ohtsuka Y, Iijima K, Matsuo M
    • Journal Title

      Pediatr Nephrol

      Volume: 24 Pages: 1773-1774

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article]2009

    • Author(s)
      Nakanishi K, Yoshikawa N
    • Journal Title

      Immunoglobulin A nephropathy. In : Pediatric Nephrology, 6th ed.(Springer)

      Pages: 757-781

    • Data Source
      KAKENHI-PROJECT-20591285
  • [Journal Article] Minimal change nephrotic syndrome associated with immune dysregulation, polyendocrinopathy, enteropathy, X-linked syndrome2009

    • Author(s)
      Hashimura Y, Nozu K, Kanegane H, Miyawaki T, Hayakawa A, Yoshikawa N, Nakanishi K, Takemoto M, Iijima K, Matsuo M
    • Journal Title

      Pediatr Nephrol

      Volume: 24 Pages: 1181-1186

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] Membranous nephropathy associated with thyroid-peroxidase antigen2009

    • Author(s)
      Shima Y, Nakanishi K, Togawa H, Obana M, Sako M, Miyawaki M, Nozu K, Iijima K, Yoshikawa N
    • Journal Title

      Pediatr Nephrol

      Volume: 24 Pages: 605-608

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] Membranous nephropathy associated with thyroid-peroxidase antigen.2009

    • Author(s)
      Shima Y, Nakanishi K
    • Journal Title

      Pediatr Nephrol 24

      Pages: 605-608

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Journal Article] A deep intronic mutation in the SLC12A3 gene leads to gitelman syndrome2009

    • Author(s)
      Nozu K, Iijima K, Nozu Y, Ikegami E, Imai T, Fu XJ, Kaito H, Nakanishi K, Yoshikawa N, Matsuo M
    • Journal Title

      Pediatr Res

      Volume: 66 Pages: 590-593

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] In vivo and in vitro splicing assay of SLC12A1 in an antenatal salt-losing tubulopathy patient with an intronic mutation2009

    • Author(s)
      Nozu. K, Iijima. K, Kawai. K, Nozu. Y, Nishuda. A, Takeshima. Y, Fu. X. J, Hashimura. Y, Kaito. H, Nakanishi. K, Yoshikawa. N, Matsuo M
    • Journal Title

      Hum Genet

      Volume: 126 Pages: 533-538

    • Data Source
      KAKENHI-PROJECT-21591396
  • [Journal Article] Improved renal survival in Japanese children with IgA nephropathy.2008

    • Author(s)
      Yata N, Nakanishi K
    • Journal Title

      Pediatr Nephrol 23

      Pages: 905-912

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Journal Article] IgA腎症2008

    • Author(s)
      中西 浩一
    • Journal Title

      小児科診療 71

      Pages: 233-238

    • Data Source
      KAKENHI-PROJECT-17591111
  • [Journal Article] Combination therapy with mizoribine for severe childhood IgA nephropathy : a pilot study.2008

    • Author(s)
      Yoshikawa N, Nakanishi K
    • Journal Title

      Pediatr Nephrol 23

      Pages: 757-763

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Journal Article] Molecular analysis of digenic inheritance in Bartter syndrome with sensorineural deafness2008

    • Author(s)
      Nozu, K., Inagaki, T., Fu, XZ., Nozu, Y., Kaito, H., Kanda, K., Sekine, T., Igarashi, I., Nakanishi, K., Yoshikawa, N., Iijima, K., Matsuo, M
    • Journal Title

      J Med Genetics 45

      Pages: 182-186

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18591199
  • [Journal Article] 髄質嚢胞腎2007

    • Author(s)
      中西 浩一
    • Journal Title

      日本医師会雑誌特別号 136

    • Data Source
      KAKENHI-PROJECT-17591111
  • [Journal Article] Long-term follow-up of juvenile acute nonproliferative glomerulitis(JANG)2007

    • Author(s)
      Fujita, T., Nozu, K., Iijima, K., Kamioka, I., Kaito, H., Tanaka, R., Nakanishi, K., Matsuo, M., Yoshikawa, N
    • Journal Title

      Pediatr Nephrol 22

      Pages: 1957-1961

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18591199
  • [Journal Article] Molecular analysis of patients with type III bartter syndrome : Picking up large heterozygous deletions with semiquantitative PCR2007

    • Author(s)
      Nozu, K., Fu, XJ., Nakanishi, K., Yoshikawa, N., Kaito, H., Kanda, K., Krol, RP., Miyashita, R., Kamitsuji, H., Kanda, S., Hayashi, Y., Satomura, K., Shimizu, N., Iijima, K., Mastuo, M
    • Journal Title

      Pediatr Research 62

      Pages: 1-6

    • NAID

      10025701181

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18591199
  • [Journal Article] pathological characteristics of five children with non-Shiga toxin-mediated hemolytic uremic syndrome2007

    • Author(s)
      Kamioka, I., Nozu, K., Fujita, T., Kaito, H., Tanaka, R., Yoshiya, K., Iijima, K., Nakanishi, K., Yoshikawa, N., Matsuo, M., Prognosis
    • Journal Title

      Pediatr Int 49

      Pages: 196-201

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18591199
  • [Journal Article] 嚢胞性腎疾患2007

    • Author(s)
      中西 浩一
    • Journal Title

      小児外科 39

      Pages: 913-917

    • Data Source
      KAKENHI-PROJECT-17591111
  • [Journal Article] 血清クレアチニン値・尿素窒素の異常[小児]2007

    • Author(s)
      中西 浩一
    • Journal Title

      日本医師会雑誌特別号 136

    • Data Source
      KAKENHI-PROJECT-17591111
  • [Journal Article] Gene analysis in Japanese patients with congenital nephrotic syndrome2006

    • Author(s)
      Sako M, Nakanishi K, Yoshikawa, N
    • Journal Title

      Annual Review Kidney

      Pages: 190-195

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17591111
  • [Journal Article] 糸球体上皮細胞関連蛋白と遺伝性ネフローゼ症候群2005

    • Author(s)
      中西浩一, 佐古まゆみ, 吉川徳茂
    • Journal Title

      日本小児科学会雑誌 (印刷中)

    • NAID

      10017280811

    • Data Source
      KAKENHI-PROJECT-14570763
  • [Journal Article] 糸球体上皮細胞関連蛋白と遺伝性ネフローゼ症候群2005

    • Author(s)
      中西 浩一
    • Journal Title

      日本小児科学会雑誌 109・7

      Pages: 805-814

    • NAID

      10017280811

    • Data Source
      KAKENHI-PROJECT-17591111
  • [Journal Article] Analysis of NPHS1, NPHS2, ACTN4 and WT1 in Japanese patients with congenital nephrotic syndrome2005

    • Author(s)
      Sako M, Nakanishi K, et al.
    • Journal Title

      Kidney International 67

      Pages: 1248-1255

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-14570763
  • [Journal Article] 上皮細胞構成蛋白の異常によるネフローゼ症候群2005

    • Author(s)
      中西 浩一
    • Journal Title

      腎と透析 58・3

      Pages: 295-299

    • Data Source
      KAKENHI-PROJECT-17591111
  • [Journal Article] Analysis of NPHS1, NPHS2, ACTN4 and WT1 in Japanese patients with congenital nephrotic syndrome2005

    • Author(s)
      Sako M, Nakanishi. K, et. al.
    • Journal Title

      Kidney International 67

      Pages: 1248-1255

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17591111
  • [Journal Article] Analysis of NPHS1, NPHS2, ACTN4 and WT1 in Japanese patients with congenital nephrotic syndrome2005

    • Author(s)
      Mayumi Sako, Koichi Nakanishi, et al.
    • Journal Title

      Kidney International 67

      Pages: 1248-1255

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-14570763
  • [Journal Article] 上皮細胞構成蛋白の異常によるネフローゼ症候群2005

    • Author(s)
      中西浩一, 吉川徳茂
    • Journal Title

      腎と透析 58

      Pages: 295-299

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-14570763
  • [Journal Article] Podocyte structural proteins and hereditary nephrotic syndrome2005

    • Author(s)
      Nakanishi K, Sako M, Yoshikawa, N
    • Journal Title

      J Jpn Pediatr Soc 109

      Pages: 805-814

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17591111
  • [Journal Article] Nephrotic syndrome due to abnormality of podocyte structural proteins2005

    • Author(s)
      Nakanishi K, Yoshikawa N
    • Journal Title

      Kidney and dialysis 58

      Pages: 295-299

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-14570763
  • [Journal Article] Analysis of NPHS1, NPHS2, ACTN4 and WT1 in Japanese patients with congenital nephrotic syndrome2005

    • Author(s)
      Mayumi Sako, Koichi Nakanishi, et al.
    • Journal Title

      Kidney International (印刷中)

    • Data Source
      KAKENHI-PROJECT-14570763
  • [Journal Article] Podocyte structural proteins and hereditary nephrotic syndrome2005

    • Author(s)
      Nakanishi K, Sako M, Yoshikawa N
    • Journal Title

      J Jpn Pediatr Soc (in press)

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-14570763
  • [Journal Article] 糸球体上皮細胞関連蛋白と遺伝性ネフローゼ症候群2005

    • Author(s)
      中西浩一, 佐古まゆみ, 吉川徳茂
    • Journal Title

      日本小児科学会雑誌 109(印刷中)

    • NAID

      10017280811

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-14570763
  • [Journal Article] A-20C angiotensinogen gene polymorphism and proteinuria in childhood IgA nephropathy.2004

    • Author(s)
      Nakanishi K, et al.
    • Journal Title

      Pediatr Nephrol 19

      Pages: 144-147

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15590855
  • [Journal Article] A-20C angiotensinogen gene polymorphism and proteinuria in childhood IgA nephropathy2004

    • Author(s)
      Nakanishi K, Sako M.et al.
    • Journal Title

      Pediatr Nephrol 19

      Pages: 144-147

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-15590855
  • [Journal Article] A-20C angiotensinogen gene polymorphism and proteinuria in childhood IgA nephropathy2004

    • Author(s)
      Nakanishi K, Sako M. et al.
    • Journal Title

      Pediatr Nephrol 19

      Pages: 144-147

    • Data Source
      KAKENHI-PROJECT-15590855
  • [Journal Article] Effective and safe treatment with cyclosporine in nephritic children : a prospective, randomized, multicenter trial

    • Author(s)
      Ishikura, K., Ikeda, M., Hattori, S., Yoshikawa, N., Sasaki, S., Iijima, K., Nakanishi, K., Yata, N., Honda, M
    • Journal Title

      Kidney Int (In press)

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18591199
  • [Journal Article] Improved renal survival in Japanese children with IgA nephropathy

    • Author(s)
      Yata, N., Nakanishi, K., Shima, Y., Togawa, H., Obana, M., Sako, M., Nozu, K., Tanaka, R., Iijima, K., Yoshikawa, N
    • Journal Title

      Pediatr Nephrol (in press)

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18591199
  • [Journal Article] Yoshikawa, N., Nakanishi, K., Ishikura, K., Hataya, H., Iijima, K., Honda, M

    • Author(s)
      Yoshikawa, N., Nakanishi, K., Ishikura, K., Hataya, H., Iijima, K., Honda, M
    • Journal Title

      Pediatr Nephrol (in press)

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18591199
  • [Presentation] 小児IgA腎症における蛋白尿寛解、再燃因子の検討.2023

    • Author(s)
      島友子、向山弘展、田中侑、島袋渡、貝藤裕史、田中亮二郎、野津寛大、飯島一誠、徳原大介、吉川徳茂、中西浩一
    • Organizer
      第66回日本腎臓学会学術総会
    • Data Source
      KAKENHI-PROJECT-23K07300
  • [Presentation] 発症時eGFR<90 ml/min/1.73m2を呈する小児IgA腎症の臨床像2023

    • Author(s)
      島友子、向山弘展、田中侑、島袋渡、貝藤裕史、田中亮二郎、野津寛大、飯島一誠、徳原大介、吉川徳茂、中西浩一
    • Organizer
      第58回日本小児腎臓病学会学術集会
    • Data Source
      KAKENHI-PROJECT-23K07300
  • [Presentation] Clinicopathological characteristics of the pediatric IgA nephropathy with eGFR<90 ml/min/1.73m2 at onset.2023

    • Author(s)
      Shima Y, Mukaiyama H, Tanaka Y, Shimabukuro W, Kaito H, Tanaka R, Nozu K, Iijima K, Tokuhara D, Yoshikawa N, Nakanishi K.
    • Organizer
      The 17th International Symposium on IgA Nephropathy
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-23K07300
  • [Presentation] ARPKDの診断と治療 - Annual review -2023

    • Author(s)
      中西浩一
    • Organizer
      第1回PKDカンファレンス
    • Invited
    • Data Source
      KAKENHI-PROJECT-23K07228
  • [Presentation] Clinicopathological characteristics of the pediatric IgA nephropathy with eGFR<90 ml/min/1.73m2 at onset2023

    • Author(s)
      Shima Y, Mukaiyama H, Tanaka Y, Shimabukuro W, Kaito H, Tanaka R, Nozu K, Iijima K, Tokuhara D, Yoshikawa N, Nakanishi K
    • Organizer
      The 56th Annual Meeting of the American Society of Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-23K07300
  • [Presentation] 重度の小児IgA腎症に対するプレドニゾロン、ミゾリビン、リシノプリルを用いた3剤併用治療法の有効性の検討2022

    • Author(s)
      島友子、向山弘展、田中侑、和田卓三、貝藤裕史、田中亮二郎、野津寛大、飯島一誠、吉川徳茂、中西浩一
    • Organizer
      第45回IgA 腎症研究会学術集会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] 遺伝子解析で診断しえた軽症常染色体劣性多発性嚢胞腎の長期経過2022

    • Author(s)
      島友子、向山弘展、田中侑、和田卓三、中西浩一
    • Organizer
      第35回近畿小児科学会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Oxford 分類による小児 IgA 腎症(IgAN),紫斑病性腎炎(IgAVN)の臨床病理学的検討2021

    • Author(s)
      島友子、浜武継、向山弘展、田中侑、野津寛大、田中亮二郎、飯島一誠、吉川徳茂、中西浩一
    • Organizer
      第50回日本腎臓学会学術総会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Oxford分類を用いた小児IgA腎症、紫斑病性腎炎の臨床病理学的所見の比較2021

    • Author(s)
      島友子、中西浩一、田中侑、向山弘展、和田卓三、浜武継、佐藤匡、貝藤裕史、野津寛大、田中亮二郎、飯島一誠、鈴木啓之、吉川徳茂
    • Organizer
      第124回日本小児科学会学術集会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] びまん性メサンギウム細胞増殖を呈する特発性ネフローゼ症候群の臨床病理学的検討2021

    • Author(s)
      永井貞之、山村智彦、近藤淳、青砥悠哉、石河慎也、榊原菜々、長野智那、堀之内智子、忍頂寺毅史、島友子、中西浩一、吉川徳茂、野津寛大、飯島一誠
    • Organizer
      第55回日本小児腎臓病学会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Efficacy of New Combination Therapy with Prednisolone, Mizoribine, and Lisinopril for Severe Childhood IgA Nephropathy.2021

    • Author(s)
      Shima Y, Mukaiyama H, Tanaka Y, Wada T, Kaito H, R, Tanaka R, Nozu K, Iijima K, Yoshikawa N, Nakanishi K.
    • Organizer
      The 54th Annual Meeting of the American Society of Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] IgA腎症Oxford分類を用いた病理学的重症度スコアリングの開発と検証2021

    • Author(s)
      島友子、向山弘展、田中侑、和田卓三、野津寛大、田中亮二郎、飯島一誠、吉川徳茂、中西浩一
    • Organizer
      第56回日本小児腎臓病学会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Two male relatives with OFD1 mutations.2021

    • Author(s)
      Wada T, Shima Y, Tanaka Y, Mukaiyama H, Morisada N, Nozu K, Iijima K, Nakanishi K.
    • Organizer
      The 18th Japan-Korea-China pediatric Nephrology Seminar 2021
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-20K08162
  • [Presentation] The combination therapy for pathologically mild childhood IgA nephropathy.2021

    • Author(s)
      Aoto Y, Iijima K, Nozu K, Kaito H, Inaguma Y, Yoshikawa N, Kondo A, Nagai S, Yamamura T, Horinouchi T, Nagano C, Sakakibara N, Ishiko S, Minamikawa S, Nakanishi K, Shima Y, Ishimori S, Kamiyoshi N, Fujimura J, Ninchoji T
    • Organizer
      The 14th Asian Congress of Pediatric Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] ARPKD―今できること,そして今後の課題―2021

    • Author(s)
      中西浩一
    • Organizer
      第64回日本腎臓学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-20K08162
  • [Presentation] A case of Potter sequence with WT1 gene mutation.2021

    • Author(s)
      Shimabukuro W, Yoshino M, Takeichi M, Omura J, Yokota C, Yamamoto J, Takahashi Y, Nozu K, Morisada N, Iijima K, Nakanishi K.
    • Organizer
      The 14th Asian Congress of Pediatric Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-20K08162
  • [Presentation] Evaluation of synonymous variants of COL4A3 and COL4A4 in suspected autosomal Alport Syndrome patients using an in vitro splicing assay.2021

    • Author(s)
      Rossanti R, Horinouchi T, Yamamura T, Nagano C, Sakakibara N, Ishiko S, Aoto Y, Kondo A, Nagai S, Okada E, Ishimori S, Nagase H, Matsui S, Tamagaki K, Ubara Y, Nagahama M, Shima Y, Nakanishi K, Matsuo M, Ninchoji T, Nozu K, Iijima K.
    • Organizer
      The 14th Asian Congress of Pediatric Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] IgA腎症Oxford分類を用いた病理学的重症度スコアリングの開発と検証2021

    • Author(s)
      島友子、向山弘展、田中侑、和田卓三、野津寛大、田中亮二郎、飯島一誠、吉川徳茂、中西浩一
    • Organizer
      第44回IgA腎症研究会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] 遺伝子解析で診断しえた軽症常染色体劣性多発性嚢胞腎の長期経過2021

    • Author(s)
      島友子、島袋渡、向山弘展、田中侑、和田卓三、森貞直哉、野津寛大、飯島一誠、中西浩一
    • Organizer
      第29回発達腎研究会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Oxford分類を用いた小児IgA腎症・紫斑病性腎炎の臨床病理学的所見の比較2021

    • Author(s)
      島友子、中西浩一、浜武継、向山弘展、佐藤匡、田中侑、和田卓三、貝藤裕史、野津寛大、田中亮二郎、飯島一誠、鈴木啓之、吉川徳茂
    • Organizer
      第55回日本小児腎臓病学会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Two male relatives with OFD1 mutations.2021

    • Author(s)
      Wada T, Shima Y, Tanaka Y, Mukaiyama H, Morisada N, Nozu K, Iijima K, Nakanishi K.
    • Organizer
      The 18th Japan-Korea-China Pediatric Nephrology Seminar
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] 小児慢性腎炎における糖鎖不全IgA1(Gd-IgA1)免疫染色の有用性の検討2021

    • Author(s)
      石河慎也、野津寛大、近藤淳、永井貞之、青砥悠哉、榊原菜々、長野智那、堀之内智子、山村智彦、島 友子、中西浩一、吉川徳茂、飯島一誠
    • Organizer
      第55回日本小児腎臓病学会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Comparison of clinicopathological findings between childhood IgA nephropathy and IgA vasculitis nephritis using Oxford classification2021

    • Author(s)
      Shima Y, Nakanishi K, Mukaiyama H, Tanaka Y, Wada T, Nozu K, Tanaka R, Iijima K, Yoshikawa N
    • Organizer
      The 14th Asian Congress of Pediatric Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] A Case with Somatic and Germline Mosaicism in COL4A5 Detected by Multiplex Ligation-Dependent Probe Amplification in X-Linked Alport Syndrome2020

    • Author(s)
      Aoto Y, Nakanishi K, Nagano C, Horinouchi T, Yamamura T, Ishiko S, Sakakibara N, Shima Y, Iijima K, Nozu K
    • Organizer
      The 53rd Annual Meeting of the American Society of Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Glomerular Galactose-Deficient IgA1 Expression Analysis in Pediatric Patients with Glomerular Diseases2020

    • Author(s)
      Ishiko S, Nozu K,Fujimaru R,Shima Y, Kaito H, Tanaka R, Ishimori S, Aoto Y, Sakakibara N, Nagano C, Horinouchi T, Yamamura T, Ninchoji T, Nakanishi K, Yoshikawa N, Iijima K
    • Organizer
      The 53rd Annual Meeting of the American Society of Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Comparison of clinicopathological findings between childhood IgA nephropathy and IgA vasculitis nephritis using Oxford classification2020

    • Author(s)
      Shima Y, Nakanishi K, Mukaiyama H, Tanaka Y, Wada T, Nozu K, Tanaka R, Iijima, K, Yoshikawa N
    • Organizer
      The 53rd Annual Meeting of the American Society of Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] NPHS1 Variants Can Cause Persistent Asymptomatic Proteinuria: Genetic and Clinical Characteristics of Patients with NPHS1 Variants in Japan2020

    • Author(s)
      Yamamura T,Horinouchi T, Ishiko S, Aoto Y, Sakakibara N, Nagano C, Ninchoji T, Shima Y, Nakanishi K, Nozu K, Iijima K
    • Organizer
      The 53rd Annual Meeting of the American Society of Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] OFD1変異を持つ男性親族の2例2020

    • Author(s)
      島友子、中西浩一、田中侑、向山弘展、森貞直哉、野津寛大、飯島一誠、吉川徳茂
    • Organizer
      第50回日本腎臓学会西部学術大会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] 小児IgA 腎症におけるプレドニゾロン(PSL)+ミゾリビン+RA系阻害薬3 剤治療の有用性の検討2020

    • Author(s)
      島友子、中西浩一、浜武継、向山弘展、田中侑、吉川徳茂
    • Organizer
      第63回日本腎臓学会学術総会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Two siblings of familial hematuria with thin basement membrane and family history of end stage kidney disease.2019

    • Author(s)
      Shima Y, Nakanishi K, Nozu K, Yamamura T, Hama T, Mukaiyama H, Suzuki H, Iijima K, Yoshikawa N
    • Organizer
      The 17th Japan-Korea-China Pediatric nephrology Seminar
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Treatment with ACE-I/ARBs in Childhood Mild IgA Nephropathy. Long-Term Treatment with ACE-I/ARBs in Childhood Mild IgA Nephropathy.2019

    • Author(s)
      Shima Y, Nakanishi K, Hama T, Tanaka Y, Mukaiyama H, Sato M, Wada T, Nozu K, Iijima, K, Yoshikawa N.
    • Organizer
      52nd Annual Meeting of the American Society of Nephrology,
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] 常染色体劣性多発性嚢胞腎(ARPKD)2019

    • Author(s)
      中西浩一
    • Organizer
      日本腎臓学会学術総会
    • Invited
    • Data Source
      KAKENHI-PROJECT-17K10150
  • [Presentation] 遺伝学的に診断できた常染色体劣勢多発性嚢胞腎の遺伝型と臨床像2019

    • Author(s)
      森貞直哉,野津寛大,中西浩一,飯島一誠
    • Organizer
      嚢胞性腎疾患研究会
    • Data Source
      KAKENHI-PROJECT-17K10150
  • [Presentation] Galactose-deficient IgA1 expression analysis is a useful tool for the diagnosis of IgA nephropathy: Two pediatric cases with pathological diagnosis of IgA nephroapthy.2019

    • Author(s)
      Ishiko S, Nozu K, Shima Y, Hara S, Aoto Y, Sakakibara N, Nagano C, Minamikawa S, Yamamura T, Yoshikawa N, Nakanishi K, Iijima K
    • Organizer
      The 17th Japan-Korea-China Pediatric nephrology Seminar
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Factord related to proteinuria relapse in childhood IgA nephropathy.2019

    • Author(s)
      Shima Y, Nakanishi K, Hama T, Tanaka Y, Wada T, Mukaiyama H, Sato M, Nozu K, Kaito H, Tanaka R, Suzuki H, Iijima K, Yoshikawa N
    • Organizer
      18th Congress of International Pediateic Nephrology Association
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] 遺伝学的に診断できた常染色体劣勢多発性嚢胞腎の遺伝型と臨床像2019

    • Author(s)
      森貞直哉,野津寛大,中西浩一,飯島一誠
    • Organizer
      発達腎研究会
    • Data Source
      KAKENHI-PROJECT-17K10150
  • [Presentation] Two male relatives with OFD1 mutation.2019

    • Author(s)
      Wada T, Shima Y, Hama T, Tanaka Y, Mukaiyama H, Sato M, Morisada N, Nozu K, Yoshikawa N, Iijima K, Nakanishi K, Suzuki H.
    • Organizer
      18th Congress of International Pediateic Nephrology Association
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] 小児IgA腎症における蛋白尿再燃因子の検討2018

    • Author(s)
      島友子、中西浩一、浜武継、田中侑、貝藤裕史、野津寛大、田中亮二郎、飯島一誠、吉川徳茂、鈴木啓之
    • Organizer
      日本小児科学会学術集会
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] 小児Silent lupus nephritisに関する臨床病理学的検討2018

    • Author(s)
      島友子、中西浩一、浜武継、田中侑、佐藤匡、向山弘展、戸川寛子、貝藤裕史、野津寛大、田中亮二郎、鈴木啓之、飯島一誠、吉川徳茂
    • Organizer
      日本小児腎臓病学会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] Clinicopathological significance in juvenile-onset silent lupus nephritis2018

    • Author(s)
      Yuko Shima, Koichi Nakanishi, Taketsugu Hama, Masashi Sato, Yu Tanaka, Hironobu Mukaiyama, Hiroshi Kaito, Kandai Nozu, Ryojiro Tanaka, Hiroyuki Suzuki, Kazumoto Iijima, Norishige Yoshikawa
    • Organizer
      American Society of Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] 小児IgA腎症における蛋白尿再燃因子の検討2018

    • Author(s)
      島友子、中西浩一、浜武継、田中侑、貝藤裕史、野津寛大、田中亮二郎、飯島一誠、吉川徳茂、鈴木啓之
    • Organizer
      日本小児腎不全学会
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] 小児Silent lupus nephritisに関する臨床病理学的検討2018

    • Author(s)
      島友子、中西浩一、浜武継、田中侑、佐藤匡、向山弘展、戸川寛子、貝藤裕史、野津寛大、田中亮二郎、鈴木啓之、飯島一誠、吉川徳茂
    • Organizer
      日本小児腎臓病学会
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] Clinicopathological significance in juvenile-onset silent lupus nephritis2018

    • Author(s)
      Yuko Shima, Koichi Nakanishi, Taketsugu Hama, Masashi Sato, Yu Tanaka, Hironobu Mukaiyama, Hiroshi Kaito, Kandai Nozu, Ryojiro Tanaka, Hiroyuki Suzuki, Kazumoto Iijima, Norishige Yoshikawa
    • Organizer
      American Society of Neprology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] 小児IgA腎症における蛋白尿再燃因子の検討2018

    • Author(s)
      島友子、中西浩一、浜武継、田中侑、貝藤裕史、野津寛大、田中亮二郎、飯島一誠、吉川徳茂、鈴木啓之
    • Organizer
      日本小児科学会学術集会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] 小児IgA腎症における蛋白尿再燃因子の検討2018

    • Author(s)
      島友子、中西浩一、浜武継、田中侑、貝藤裕史、野津寛大、田中亮二郎、飯島一誠、吉川徳茂、鈴木啓之
    • Organizer
      日本小児腎不全学会
    • Data Source
      KAKENHI-PROJECT-18K07799
  • [Presentation] 1.A case of childhood IgA Nephropathy with glomerular capillary IgA deposition.2017

    • Author(s)
      Yuko Shima, Koichi Nakanishi, Masashi Sato,Taketsugu Hama, Hironobu Mukaiyama, Hiroko Togawa, Hiroyuki Suzuki, Norishige Yoshikawa
    • Organizer
      The 15th Japan-Korea-China Pediatric nephrology Seminar
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] 小児全身性エリテマトーデス(SLE)における尿所見が軽微なループス腎炎に関する臨床病理学的検討2017

    • Author(s)
      4.島友子、中西浩一、浜武継、田中侑、佐藤匡、向山弘展、戸川寛子、鈴木啓之、吉川徳茂
    • Organizer
      第39回日本小児腎不全学会
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] Foctors related to proteinuria relapse in childhood IgA Nephropathy2017

    • Author(s)
      Yuko Shima, Koichi Nakanishi, Masashi Sato, Taketsugu Hama, Yu Tanaka, Hironobu Mukaiyama, Hiroko Togawa, Hiroshi Kaito, Kandai Nozu, Ryojiro Tanaka, Kazumoto Iijima, Hiroyuki Suzuki, Norishige Yoshikawa
    • Organizer
      50th Annual Meeting of the American Society of Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] 3.Foctors related to proteinuria relapse in childhood IgA Nephropathy2017

    • Author(s)
      Yuko Shima, Koichi Nakanishi, Masashi Sato, Taketsugu Hama, Yu Tanaka, Hironobu Mukaiyama, Hiroko Togawa, Hiroshi Kaito, Kandai Nozu, Ryojiro Tanaka, Kazumoto Iijima, Hiroyuki Suzuki, Norishige Yoshikawa
    • Organizer
      50th Annual Meeting of the American Society of Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] 2.New combination therapy with prednisolone (PSL), mizoribine and lisinopril for severe childhood IgA Nephropathy (IgAN).2017

    • Author(s)
      Norishige Yoshikawa, Yuko Shima, Masashi Sato, Taketsugu Hama, Hironobu Mukaiyam, Hiroko Togawa, Hiroyuki Suzuki, Hiroshi Kaito, Kandai Nozu, Kazumoto Iijima, Koichi Nakanishi
    • Organizer
      50th anniversary meeting of the European Society for Pediatric Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] Clinicopathological significance of glomerular capillary IgA deposition in childhood IgA Nephropathy2017

    • Author(s)
      Yuko Shima, Koichi Nakanishi, Masashi Sato, Taketsugu Hama, Hironobu Mukaiyama, Hiroko Togawa, Hiroshi Kaito, Kandai Nozu, Ryojiro Tanaka, Kazumoto Iijima, Hiroyuki Suzuki, Norishige Yoshikawa
    • Organizer
      第51回日本小児腎臓病学会
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] 小児IgA腎症における糸球体毛細管系蹄IgA沈着の臨床病理学的検討2017

    • Author(s)
      1.島友子、中西浩一、濱武継、佐藤匡、向山弘展、戸川寛子、貝藤裕史、野津寛大、田中亮二郎、飯島一誠、鈴木啓之、吉川徳茂.
    • Organizer
      小児IgA腎症における糸球体毛細管系蹄IgA沈着の臨床病理学的検討
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] In vitro splicing assays to detecy intronic pathogenic variants in inherited kidney disease2017

    • Author(s)
      Nakanishi K, Nozu K, Fujimura J, Horinouchi T, Minamikawa S, Yamamura T, Ninchoji T, Kaito H, Yoshikawa N, Iijima K
    • Organizer
      50th Anniversary Meeting of the European Society for Pediatric Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] Concurrent Session 2.2 Congenital Anomalies of the Kidney and Urinary Tract (CAKUT): Outcome of CAKUT.2017

    • Author(s)
      Koichi Nakanishi
    • Organizer
      13th Asian Congress of Pediatric Nephrology
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-17K10150
  • [Presentation] New combination therapy with prednisolone (PSL), mizoribine and lisinopril for severe childhood IgA Nephropathy (IgAN)2017

    • Author(s)
      Norishige Yoshikawa, Yuko Shima, Masashi Sato, Taketsugu Hama, Hironobu Mukaiyam, Hiroko Togawa, Hiroyuki Suzuki, Hiroshi Kaito, Kandai Nozu, Kazumoto Iijima, Koichi Nakanishi
    • Organizer
      50th Anniversary Meeting of the European Society for Pediatric Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] A variety of phenotypes reflected by genotypes and laminin β2 sxpression on glomerulus in Pierson syndrome2017

    • Author(s)
      Minamikawa S, Nozu K, Fujimura J, Nakanishi K, Horinouchi T, Yamamura T, Ninchoji T, Kaito H, Yoshikawa N, Iijima K
    • Organizer
      50th Anniversary Meeting of the European Society for Pediatric Nephrology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] Crescentic IgA Nephropathy (C-IgAN) in children.2016

    • Author(s)
      Shima Y, Nakanishi K, Sato M, Nozu K, Tanaka R, Iijima K, Suzuki H, Yoshikawa N.
    • Organizer
      17th congress of International Pediatric Nephrology Association
    • Place of Presentation
      Igua&ccedil;u, Brazil
    • Year and Date
      2016-09-20
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] Genetic approach to the siblings with congenital / infantile nephrotic syndrome by targeted resequence2016

    • Author(s)
      Minamikawa S, Nozu K, Nakanishi K, Yamamura T, Ninchoji T, Nakanishi K, Yoshikawa N, Iijima K
    • Organizer
      17th International Pediatric Nephrology Association
    • Place of Presentation
      Iguac, Brazil
    • Year and Date
      2016-09-20
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] 半月体形成性糸状体腎炎(CGN)を呈する小児IgA腎症の検討2016

    • Author(s)
      島友子、中西浩一、佐藤匡、向山弘展、濱武継、野津寛大、田中亮二郎、飯島一誠、
    • Organizer
      第59回日本腎臓学会学術総会
    • Place of Presentation
      横浜
    • Year and Date
      2016-06-17
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] Differential expressions of miR-378a-3p/ADAMTS1 in cpk mice, a model of ARPKD2016

    • Author(s)
      Sato M, Koichi Nakanishi K, Hama T, Mukaiyama H, Togawa H, Yuko Shima1, Miyajima M, Nozu K, Nagao S, Takahashi H, Iijima K Yoshikawa N, Suzuki H
    • Organizer
      49th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Chicago, USA
    • Year and Date
      2016-11-15
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] 小児IgA腎症における糸球体毛細管係蹄IgA沈着の臨床病理学的検討2016

    • Author(s)
      島友子、中西浩一、佐藤匡、濱武継、向山弘展、戸川寛子、貝藤裕史、野津寛大、田中亮二郎、飯島一誠、鈴木啓之、吉川徳茂
    • Organizer
      第38回小児腎不全学会
    • Place of Presentation
      岐阜
    • Year and Date
      2016-10-27
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] 発症時急性腎炎症候群を呈する小児IgA腎症(AGN-IgAN)の検討2016

    • Author(s)
      島友子、中西浩一、濱武継、佐藤匡、向山弘展、戸川寛子、貝藤裕史、野津寛大、田中亮二郎、飯島一誠、吉川徳茂
    • Organizer
      第51回小児腎臓病学会学術集会
    • Place of Presentation
      名古屋
    • Year and Date
      2016-07-07
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] Clinical characteristics and long term outcome of diarrhea associated hemolytic uremic syndrome2016

    • Author(s)
      Nakanishi K, Ninchoji T, Horinouchi T, Fujimura J, Yamamura T, Minamikawa S, Nozu K, Nakanishi K, Yoshikawa N, Iijima K
    • Organizer
      17th International Pediatric Nephrology Association
    • Place of Presentation
      Iguac, Brazil
    • Year and Date
      2016-09-20
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] Childhood IgA nephropathy presenting acute nephritic syndrome at onset.2016

    • Author(s)
      Shima Y, Nakanishi K, Hama T, Sato M, Mukaiyama H, Togawa H, Kaito H, Nozu K, Tanaka R, Iijima K, Suzuki H, Yoshikawa N
    • Organizer
      49th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Chicago, USA
    • Year and Date
      2016-11-20
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] cpkマウスARPKDモデルにおけるmiR-378a-3p/ADAMTS12016

    • Author(s)
      佐藤匡、中西浩一、浜武継、向山弘展、戸川寛子、島友子、宮嶋正康、野津寛大、長尾枝澄香、高橋久英、飯島一誠、吉川徳茂、鈴木啓之
    • Organizer
      第25回発達腎研究会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Presentation] cpkマウスARPKDモデルにおけるmiR-378a-3p/ADAMTS12016

    • Author(s)
      佐藤匡、中西浩一、浜武継、向山弘展、戸川寛子、島友子、宮嶋正康、野津寛大、長尾枝澄香、高橋久英、飯島一誠、吉川徳茂、鈴木啓之
    • Organizer
      第24回のう胞性腎疾患研究会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Presentation] cpkマウスARPKDモデルにおけるmiR-378a-3pとADAMTS12016

    • Author(s)
      佐藤匡、中西浩一、浜武継、向山弘展、戸川寛子、島友子、宮嶋正康、野津寛大、長尾枝澄香、高橋久英、飯島一誠、吉川徳茂、鈴木啓之
    • Organizer
      第51回小児腎臓病学会
    • Place of Presentation
      名古屋
    • Year and Date
      2016-07-07
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Presentation] Crescentic IgA nephropathy in children2016

    • Author(s)
      Shima Y, Nakanishi K, Sato M, Nozu K, Tanaka R, Iijima K, Suzuki H, Yoshikawa N
    • Organizer
      17th International Pediatric Nephrology Association
    • Place of Presentation
      Iguac, Brazil
    • Year and Date
      2016-09-20
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] Genetic and clinical characteristics of female X-linked Alport syndrome : 267 cases study2016

    • Author(s)
      Yamamura Y, Nozu K, Nakanishi K, Horinouchi T, Fujimura J, Minamikawa S, Kamiyoshi N, Ninchoji T, Kaito H, Morisada N, Nakanishi K, Yoshikawa N, Iijima K
    • Organizer
      17th International Pediatric Nephrology Association
    • Place of Presentation
      Iguac, Brazil
    • Year and Date
      2016-09-20
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] Childhood IgA nephropathy presenting acute nephritic syndrome at onset2016

    • Author(s)
      Shima Y, Nakanishi K, Hama T, Sato M, Mukaiyama H, Togawa H, Kaito H, Nozu K, Tanaka R, Iijima K, Suzuki H, Yoshikawa N
    • Organizer
      49th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Chicago, USA
    • Year and Date
      2016-11-15
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] Differential expressions of miR-378a-3p/ADAMTS1 in cpk mice, a model of ARPKD2016

    • Author(s)
      Sato M, Koichi Nakanishi K, Hama T, Mukaiyama H, Togawa H, Yuko Shima1, Miyajima M, Nozu K, Nagao S, Takahashi H, Iijima K Yoshikawa N, Suzuki H
    • Organizer
      49th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Chicago
    • Year and Date
      2016-11-15
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Presentation] Dysregulation of miR-378a-3p and ADAMTS1 gene in cpk mice, a model of ARPKD.2015

    • Author(s)
      Sato M, Nakanishi K, Hama T, Mukaiyama H, Togawa H, Shima Y, Miyajima M, Nozu K, Nagao S, Takahashi H, Iijima K, Yoshikawa N
    • Organizer
      48th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2015-11-05
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Presentation] Somatic mosaicism and variant frequency detected by next-generation sequencing in X-linked Alport syndrome2015

    • Author(s)
      Kamiyoshi N, Nozu K, Yamamura T, Ninchoji T, Shima Y, Nakanishi K, Yoshikawa N, Iijima K
    • Organizer
      48th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2015-11-05
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] IgA腎症発症関連分子の腎における発現.2015

    • Author(s)
      佐藤匡,島友子,浜武継,向山弘展,戸川寛子,中西浩一,吉川徳茂
    • Organizer
      第58回日本腎臓学会学術総会
    • Place of Presentation
      名古屋
    • Year and Date
      2015-06-05
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] Evidence-based Treatments for Childhood IgA Nephropathy2015

    • Author(s)
      Nakanishi K, Yoshikawa N
    • Organizer
      The 11th Asian Society for Pediatric Research
    • Place of Presentation
      Osaka
    • Year and Date
      2015-04-15
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] Genetic, pathological and clinical backgrounds in autosomal dominant Alport syndrome2015

    • Author(s)
      Nozu K, Kamiyoshi N, Minamikawa S, Matsunoshita N, Otsubo H, Yamamura T, Ninchoji T, Nakanishi K, Yoshikawa N, Iijima K
    • Organizer
      48th annual scientific meeting of the European Society for Pediatric Nephrology
    • Place of Presentation
      Brussels, Belgium
    • Year and Date
      2015-09-03
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] Childhood IgA nephropathy with nephrotic syndrome (NS-IgAN) at onset.2015

    • Author(s)
      Shima Y, Nakanishi K, Hama T, Sato M, Togawa H, Mukaiyama H, Kaito H, Nozu K, Tanaka R, Iijima K, Yoshikawa N.
    • Organizer
      48th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2015-11-05
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] IgA腎症発症関連分子の腎における発現2015

    • Author(s)
      佐藤匡,島友子,浜武継,向山弘展,戸川寛子,中西浩一,吉川徳茂
    • Organizer
      第58回日本腎臓学会学術総会
    • Place of Presentation
      名古屋
    • Year and Date
      2015-06-05
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] 発症時ネフローゼ症候群を呈する小児IgA腎症(NS-IgAN)の検討2015

    • Author(s)
      島友子,中西浩一,濱武継,佐藤匡,向山弘展,戸川寛子,貝藤裕史,野津寛大,田中亮二郎,飯島一誠,吉川徳茂
    • Organizer
      日本小児腎臓病学会学術集会第50回記念大会
    • Place of Presentation
      神戸
    • Year and Date
      2015-06-05
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] Childhood IgA nephropathy with nephrotic syndrome (NS-IgAN) at onset2015

    • Author(s)
      Shima Y, Nakanishi K, Hama T, Sato M, Togawa H, Mukaiyama H, Kaito H, Nozu K, Tanaka R, Iijima K, Yoshikawa N
    • Organizer
      48th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2015-11-05
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] cpkマウスにおける嚢胞形成に対するsmad3ノックアウトの効果.2015

    • Author(s)
      佐藤匡,中西浩一,浜武継,向山弘展,戸川寛子,島友子,宮嶋正康,野津寛大,長尾枝澄香,高橋久英,飯島一誠,吉川徳茂
    • Organizer
      日本小児腎臓病学会学術集会第50回記念大会
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2015-06-18
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Presentation] vidence-based treatments for childhood diseases > Evidence-based Treatments for Childhood IgA Nephropathy.2015

    • Author(s)
      Nakanishi K, Yoshikawa N
    • Organizer
      The 11th Asian Society for Pediatric Research
    • Place of Presentation
      Osaka
    • Year and Date
      2015-04-15
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Presentation] 発症時ネフローゼ症候群を呈する小児IgA腎症(NS-IgAN)の検討.2015

    • Author(s)
      島友子,中西浩一,濱武継,佐藤匡,向山弘展,戸川寛子,貝藤裕史,野津寛大,田中亮二郎,飯島一誠,吉川徳茂.
    • Organizer
      日本小児腎臓病学会学術集会第50回記念大会
    • Place of Presentation
      神戸
    • Year and Date
      2015-06-18
    • Data Source
      KAKENHI-PROJECT-15K09694
  • [Presentation] Dysregulation of miR-378a-3p and ADAMTS1 gene in cpk mice, a model of ARPKD2015

    • Author(s)
      Sato M, Nakanishi K, Hama T, Mukaiyama H, Togawa H, Shima Y, Miyajima M, Nozu K, Nagao S, Takahashi H, Iijima K, Yoshikawa N
    • Organizer
      48th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2015-11-05
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09695
  • [Presentation] 遺伝性腎疾患のABC2013

    • Author(s)
      中西浩一
    • Organizer
      第14回徳島県小児膠原病・腎疾患談話会
    • Place of Presentation
      徳島(特別講演)
    • Year and Date
      2013-04-10
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] Smad3 Phosphorylated at Both Linker and COOH-Terminal Regions in Cyst-Lining Epithelia in cpk Mouse, a Model of ARPKD.2013

    • Author(s)
      Hama T, Nakanishi K, Mukaiyama H, Togawa H, Sato M, Shima Y, Miyajima M, Nozu K, Nagao S, Takahashi H, Iijima K, Yoshikawa N.
    • Organizer
      The 46th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Atlanta, USA
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] Smad3 Phosphorylated at Both Linker and COOH-Terminal Regions in Cyst-Lining Epithelia in cpk Mouse, a Model of ARPKD2013

    • Author(s)
      Hama T, Nakanishi K, Mukaiyama H, Togawa H, Sato M, Shima Y, Miyajima M, Nozu K, Nagao S, Takahashi H, Iijima K, Yoshikawa N
    • Organizer
      46^<th> Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Atlanta, USA(JASN 24:303A)
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] Possible contribution of fibrocytes to renal fibrosis in cpk mouse, a model of ARPKD2013

    • Author(s)
      Hama T, Nakanishi K, Mukaiyama H, Sato M, Togawa H, Shima Y, Miyajima M, Takahashi H, Nagao S, Iijima K, Yoshikawa N
    • Organizer
      15th Congress of the International Pediatric Nephrology Association
    • Place of Presentation
      Shanghai, China
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] cpkマウス多発性嚢胞腎モデル腎線維化におけるfibrocyteの関与2013

    • Author(s)
      浜武継,中西浩一,向山弘展,佐藤匡,戸川寛子,島友子,宮嶋正康,高橋久英,長尾静子,飯島一誠,吉川徳茂
    • Organizer
      第48回日本小児腎臓病学会学術集会
    • Place of Presentation
      徳島
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] Possible contribution of fibrocytes to renal fibrosis in cpk mouse, a model of ARPKD.2013

    • Author(s)
      Hama T, Nakanishi K, Mukaiyama H, Sato M, Togawa H, Shima Y, Miyajima M, Takahashi H, Nagao S, Iijima K, Yoshikawa N&#61486;
    • Organizer
      The 15th Congress of the International Pediatric Nephrology Association
    • Place of Presentation
      Shanghai, China
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] 常染色体劣性多発性嚢胞腎の鑑別を要した3例2013

    • Author(s)
      浜武継,中西浩一,佐藤匡,向山弘展,戸川寛子,島友子,辻本弘,神波信次,吉川徳茂
    • Organizer
      第35回日本小児腎不全学会学術集会
    • Place of Presentation
      郡山
    • Year and Date
      2013-10-24
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] cpkマウスARPKDモデルにおける病的Smad3リン酸化2013

    • Author(s)
      浜武継,中西浩一,向山弘展,戸川寛子,佐藤匡,島友子,宮嶋正康,野津寛大,高橋久英,長尾枝澄香,飯島一誠,吉川徳茂
    • Organizer
      第21回嚢胞性腎疾患研究会
    • Place of Presentation
      東京
    • Year and Date
      2013-09-21
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] Ciliopathy. Continuous Professional Development, Theme: Current Issues in Pediatric Nephrology.2013

    • Author(s)
      Nakanishi K
    • Organizer
      The 11th Korea-Japan Pediatric Nephrology Seminar 2013
    • Place of Presentation
      Seoul, Korea
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] cpkマウスにおける病的態・遺伝子診断小児嚢胞性腎疾患の病Smad3リン酸化2013

    • Author(s)
      浜武継,中西浩一,向山弘展,戸川寛子,佐藤匡,島友子,宮嶋正康,野津寛大,高橋久英,長尾枝澄香,飯島一誠,吉川徳茂
    • Organizer
      第22回発達腎研究会
    • Place of Presentation
      高槻
    • Year and Date
      2013-09-14
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] Two-year outcome of the ISKDC regimen and frequent-relapsing risk in children with idiopathic nephrotic syndrome2013

    • Author(s)
      Nakanishi K, Yoshikawa N, et al
    • Organizer
      16th Congress of the International Pediatric Nephrology Association
    • Place of Presentation
      Shanghai, China
    • Data Source
      KAKENHI-PROJECT-24390265
  • [Presentation] 繊毛病2012

    • Author(s)
      中西浩一
    • Organizer
      第47回日本小児腎臓病学会学術集会
    • Place of Presentation
      東京
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] ARPKDの病態・遺伝子診断2012

    • Author(s)
      中西浩一
    • Organizer
      第34回日本小児腎不全学会学術集会
    • Place of Presentation
      洲本(淡路島)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] ARPKDの病因・病態の解明と診断・治療の進歩2012

    • Author(s)
      中西浩一
    • Organizer
      第34回日本小児腎不全学会学術集会
    • Place of Presentation
      洲本(シンポジウム,座長兼任)
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] cpkマウスにおける部位特定的リン酸化Smad3の発現2012

    • Author(s)
      向山弘展,中西浩一,浜武継,戸川寛子,島友子,宮嶋正康,高橋久英,長尾枝澄香,飯島一誠,吉川徳茂
    • Organizer
      第47回日本小児腎臓病学会学術集会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] 繊毛病プロフェッショナル-52012

    • Author(s)
      中西浩一
    • Organizer
      第47回日本小児腎臓病学会学術集会
    • Place of Presentation
      東京(教育講演)
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] Possible Contribution of Fibrocytes to Renal Fibrosis in Cpk Mouse, a Model of ARPKD2012

    • Author(s)
      Hama T, Nakanishi K, Mukaiyama H, Togawa H, Shima Y, Miyajima M, Takahashi H, Nagao S, Iijima K, Yoshikawa N
    • Organizer
      45^<th> Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      San Diego, USA(JASN 2012;23:596A)
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] 遺伝性ネフローゼ症候群と多発性嚢胞腎2012

    • Author(s)
      中西浩一
    • Organizer
      第22回北海道小児腎臓病研究会
    • Place of Presentation
      札幌(特別講演)
    • Year and Date
      2012-10-20
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] Possible Contribution of Fibrocytes to Renal Fibrosis in Cpk Mouse, a Model of ARPKD2012

    • Author(s)
      Taketsugu Hama, Koichi Nakanishi, Hironobu Mukaiyama, Hiroko Togawa, Yuko Shima, Masayasu Miyajima, Hisahide Takahashi, Shizuko Nagao, Kazumoto Iijima, Norishige Yoshikawa
    • Organizer
      45th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] アルポート症候群と多発性嚢胞腎2012

    • Author(s)
      中西浩一
    • Organizer
      第11回弘前小児腎疾患フォーラム
    • Place of Presentation
      弘前(特別講演)
    • Year and Date
      2012-10-26
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] 小児におけるADPKDの実態2011

    • Author(s)
      中西浩一
    • Organizer
      市民公開シンポジウムADPKD-次の世代を考える-
    • Place of Presentation
      東京<シンポジウム>
    • Year and Date
      2011-02-20
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] cpkマウスにおける部位特定的リン酸化Smad3の発現2011

    • Author(s)
      浜武継,中西浩一,向山弘展,戸川寛子,島友子,宮嶋正康,高橋久英,長尾枝澄香,飯島一誠,吉川徳茂
    • Organizer
      第19回嚢胞性腎疾患研究会
    • Place of Presentation
      東京
    • Year and Date
      2011-09-11
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] Acceleration of Smad3 phosphorylation at linker regions via c-Jun NH2-terminal kinase (JNK) in cyst-lining epithelial cells in cpk mouse, a model of ARPKD.2011

    • Author(s)
      Mukaiyama H, Nakanishi K, Hama T, Togawa H, Shima Y, Miyajima M, Takahashi H, Nagao S, Iijima K, Yoshikawa N
    • Organizer
      The 44th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Philadelphia
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] 小児における多発性嚢胞腎PKDの会2011

    • Author(s)
      中西浩一
    • Organizer
      第11回関西座談会
    • Place of Presentation
      大阪(講演)
    • Year and Date
      2011-11-20
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] Acceleration of Smad3 phosphorylation at linker regions via c-Jun NH2-terminal kinase (JNK) in cyst-lining epithelial cells in cpk mouse, a model of ARPKD2011

    • Author(s)
      Mukaiyama H, Nakanishi K, Hama T, Togawa H, Shima Y, Miyajima M, Takahashi H, Nagao S, Iijima K, Yoshikawa N
    • Organizer
      44^<th> Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Philadelphia, USA(JASN 22:576A)
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] cpkマウスARPKDモデルにおける上皮間葉移行(EMT)2011

    • Author(s)
      向山弘展,中西浩一,戸川寛子,濵武継,島友子,宮嶋正康,吉原大輔,長尾枝澄香,高橋久英,飯島一誠,吉川徳茂
    • Organizer
      第52回日本腎臓学会学術総会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] cpkマウスARPKDモデルにおける上皮間葉移行(EMT)2011

    • Author(s)
      向山弘展,中西浩一,戸川寛子,濵武継,島友子,宮嶋正康,吉原大輔,長尾枝澄香,高橋久英,飯島一誠,吉川徳茂
    • Organizer
      第54回日本腎臓学会学術総会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] 小児におけるADPKDの実態2011

    • Author(s)
      中西浩一
    • Organizer
      市民公開シンポジウムADPKD-次の世代を考える-
    • Place of Presentation
      東京
    • Year and Date
      2011-02-20
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] Pathophysiology of polycystic kidney disease2011

    • Author(s)
      Nakanishi K
    • Organizer
      The 11th Asian Congress of Pediatric Nephrology 2011(招待講演)
    • Place of Presentation
      Fukuoka
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] ヒトARPKDと相同遺伝子変異を有するPCK ratにおける上皮間葉移行2010

    • Author(s)
      戸川寛子, 中西浩一, 吉川徳茂
    • Organizer
      第53回日本腎臓学会学術総会
    • Place of Presentation
      神戸
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] 常染色体劣性多発性嚢胞腎(ARPKD)モデルcpkマウスの尿細管上皮細胞における上皮間葉移行(EMT)2010

    • Author(s)
      戸川寛子, 中西浩一, 島友子, 佐古まゆみ, 向山弘展, 宮嶋正康, 野津寛大, 吉原大輔, 長尾枝澄香, 飯島一誠, 吉川徳茂
    • Organizer
      第44回日本小児腎臓病学会学術集会
    • Place of Presentation
      大阪
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] Epithelial-to-Mesenchymal Transition (EMT) in Mouse,a Model of ARPKD2010

    • Author(s)
      Togawa H, Nakanishi K, Yoshikawa N
    • Organizer
      43^<th> Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Denver, USA
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] ヒトARPKDと相同遺伝子変異を有するPCKratにおける上皮間葉移行2010

    • Author(s)
      戸川寛子, 中西浩一, 島友子, 佐古まゆみ, 向山弘展, 宮嶋正康, 野津寛大, 吉原大輔, 長尾枝澄香, 飯島一誠, 吉川徳茂
    • Organizer
      第53回日本腎臓学会学術総会
    • Place of Presentation
      神戸
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] Epithelial-to-Mesenchymal Transition (EMT) in cpk Mouse, a Model of ARPKD.2010

    • Author(s)
      Togawa H, Nakanishi K, Mukaiyama H, Hama T, Shima Y, Miyajima M, Nozu K, Takahashi H, Nagao S, Iijima K, Yoshikawa N
    • Organizer
      43^<th> Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Denver, USA
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] ヒトARPKD相同遺伝子ラットモデルにおける尿細管部位特異的嚢胞形成2009

    • Author(s)
      戸川寛子, 中西浩一, 島友子, 佐古まゆみ, 宮嶋正康, 西井一宏, 長尾枝澄香, 高橋久英, 吉川徳茂
    • Organizer
      第52回日本腎臓学会学術総会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] 常染色体劣性多発性嚢胞腎(ARPKD)2009

    • Author(s)
      中西浩一
    • Organizer
      第17回嚢胞性腎疾患研究会
    • Place of Presentation
      東京<特別講演>
    • Year and Date
      2009-09-12
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] ARPKD相同遺伝子ラットモデルの尿細管上皮細胞における上皮間葉移行(EMT)2009

    • Author(s)
      戸川寛子, 中西浩一, 島友子, 佐古まゆみ, 宮嶋正康, 野津寛大, 飯島一誠, 吉原大輔, 長尾枝澄香, 吉川徳茂
    • Organizer
      第44回日本小児腎臓病学会学術集会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] CAKUT2009

    • Author(s)
      中西浩一, 吉川徳茂
    • Organizer
      第39回日本腎臓病学会西部学術大会
    • Place of Presentation
      県立文化会館(和歌山県)
    • Year and Date
      2009-10-17
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] 小児の遺伝性腎疾患2009

    • Author(s)
      中西浩一, 吉川徳茂
    • Organizer
      第32回日本小児遺伝学会
    • Place of Presentation
      奈良県
    • Year and Date
      2009-04-16
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] IgA腎症:小児科2009

    • Author(s)
      中西浩一, 吉川徳茂
    • Organizer
      第39回日本腎臓病学会西部学術大会
    • Place of Presentation
      県立文化会館(和歌山県)
    • Year and Date
      2009-10-16
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] Snail1 Is Involved in Epithelial-to-Mesenchymal Transition (EMT) in Cyst-Lining Epithelial.2009

    • Author(s)
      戸川寛子, 中西浩一, 島友子, 佐古まゆみ, 宮嶋正康, 野津寛大, 飯島一誠, 吉原大輔, 長尾枝澄香, 吉川徳茂
    • Organizer
      42^<th> Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] Epithelial-to-mesenchymal transition (EMT) in cyst-lining epithelial cells in PCK rat.2008

    • Author(s)
      Hiroko Togawa Koichi Nakanishi
    • Organizer
      The 41th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Philadelphia, USA
    • Year and Date
      2008-11-07
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] 多発性嚢胞腎(PKD)の嚢胞形成にはE-cadherin/β-cateninの破綻が関与する2008

    • Author(s)
      戸川寛子, 中西浩一, 佐古まゆみ, 尾鼻美奈, 島友子, 宮嶋正康, 西井一宏, 長尾枝澄香, 高橋久英, 吉川徳茂
    • Organizer
      第43回日本小児腎臓病学会学術集会
    • Place of Presentation
      福岡
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] Epithelial-to-Mesenchymal Transition in Cyst-Lining Epithelial Cells in PCK Rat. J Am Soc Nephrol 19 : 362A, 20082008

    • Author(s)
      Togawa H, Nakanishi K, Obana M, Shima Y, Miyajima M, Nozu K, Iijima K, Nishi K, Nagao S, Takahashi H, Yoshikawa N
    • Organizer
      41^<th> Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Philadelphia, USA
    • Data Source
      KAKENHI-PROJECT-20591285
  • [Presentation] Combination Therapy with Mizoribine for Severe Childhood IgA Nephropathy: A Pilot Study2007

    • Author(s)
      Nakanishi K
    • Organizer
      40th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      San Francisco,USA
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17591111
  • [Presentation] Combination Therapy with Mizoribine for Severe Childhood IgA Nephropathy:A Pilot Study.2007

    • Author(s)
      Nakanishi K
    • Organizer
      40^<th> Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      San Francisco,USA
    • Data Source
      KAKENHI-PROJECT-17591111
  • [Presentation] NPHS1, NPHS2, ACTN4, CD2AP and WT1 analysis in Japanese patients with congenital nephrotic syndrome2006

    • Author(s)
      Sako M, Nakanishi K, Togawa H, Shima Y, Hoshii S, Takahashi S, Wada N, Takahashi Y, Kaku Y, Satomura K, Ikeda M, Yoshikawa, N
    • Organizer
      The 2nd Congress of Asian Society for Pediatric Research
    • Place of Presentation
      Yokohama, JAPAN
    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17591111
  • [Presentation] Smad3 gene deletion ameliorates cyst formation and interstitial fibrosis in cpk mouse, a model of ARPKD

    • Author(s)
      Hama T, Nakanishi K, Mukaiyama H, Togawa H, Sato M, Shima Y, Miyajima M, Nozu K, Nagao S, Takahashi H, Iijima K, Yoshikawa N
    • Organizer
      47th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Philadelphia, USA
    • Year and Date
      2014-11-11 – 2014-11-16
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Presentation] cpkマウスARPKDモデルにおける病的Smad3リン酸化

    • Author(s)
      浜武継, 中西浩一, 向山弘展, 戸川寛子, 佐藤匡, 島 友子, 宮嶋正康, 野津寛大, 高橋久英, 長尾枝澄香, 飯島一誠, 吉川徳茂
    • Organizer
      第21回嚢胞性腎疾患研究会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] cpkマウスにおける病的Smad3リン酸化

    • Author(s)
      浜武継, 中西浩一, 向山弘展, 戸川寛子, 佐藤匡, 島 友子, 宮嶋正康, 野津寛大, 高橋久英, 長尾枝澄香, 飯島一誠, 吉川徳茂
    • Organizer
      第22回発達腎研究会
    • Place of Presentation
      高槻
    • Data Source
      KAKENHI-PROJECT-23591580
  • [Presentation] The differential diagnosis between inherited salt-losing tubulopathy and pseudo-disorder from clinical characteristics

    • Author(s)
      Matsunoshita N, Nozu K, Kamiyoshi N, Nakanishi K, Yoshikawa N, Iijima K
    • Organizer
      47th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Philadelphia, USA
    • Year and Date
      2014-11-11 – 2014-11-16
    • Invited
    • Data Source
      KAKENHI-PROJECT-24390265
  • [Presentation] IgA nephropathy with nephrotic syndrome in children

    • Author(s)
      Shima Y, Nakanishi K, Hama T, Sato M, Mukaiyama H, Togawa H, Kaito H, Nozu K, Tanaka R, Iijima K, Yoshikawa N
    • Organizer
      47th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Philadelphia, USA
    • Year and Date
      2014-11-11 – 2014-11-16
    • Data Source
      KAKENHI-PROJECT-24390265
  • [Presentation] IgA nephropathy & Henoch-Schonlein purpura

    • Author(s)
      Nakanishi K, Yoshikawa N
    • Organizer
      The XII Asian Congress of Pediatric Nephrology
    • Place of Presentation
      New Delhi, Republic of India
    • Year and Date
      2014-12-04 – 2014-12-06
    • Data Source
      KAKENHI-PROJECT-24390265
  • [Presentation] Ciliopathies: Mechanisms & therapies

    • Author(s)
      Nakanishi K
    • Organizer
      The XII Asian Congress of Pediatric Nephrology
    • Place of Presentation
      New Delhi, Republic of India
    • Year and Date
      2014-12-04 – 2014-12-06
    • Invited
    • Data Source
      KAKENHI-PROJECT-26461618
  • [Presentation] Smad3 gene deletion ameliorates cyst formation and interstitial fibrosis in cpk mouse, a model of ARPKD

    • Author(s)
      Hama T, Nakanishi K, Mukaiyama H, Togawa H, Sato M, Shima Y, Miyajima M, Nozu K, Nagao S, Takahashi H, Iijima K, Yoshikawa N
    • Organizer
      47th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Philadelphia, USA
    • Year and Date
      2014-11-11 – 2014-11-16
    • Data Source
      KAKENHI-PROJECT-24390265
  • [Presentation] Autosomal dominant Alport syndrome: molecular analysis of the COL4A3/COL4A4 genes and clinical outcome

    • Author(s)
      Kamiyoshi N, Nozu K, Matsunoshita N, Ohtsubo H, Ninchoji T, Kaito H, Nakanishi K, Yoshikawa N, Iijima K
    • Organizer
      47th Annual Meeting of the American Society of Nephrology
    • Place of Presentation
      Philadelphia, USA
    • Year and Date
      2014-11-11 – 2014-11-16
    • Data Source
      KAKENHI-PROJECT-24390265
  • 1.  YOSHIKAWA Norishige (10158412)
    # of Collaborated Projects: 12 results
    # of Collaborated Products: 189 results
  • 2.  SHIMA Yuko (60433364)
    # of Collaborated Projects: 7 results
    # of Collaborated Products: 108 results
  • 3.  HAMA Taketsugu (00508020)
    # of Collaborated Projects: 3 results
    # of Collaborated Products: 21 results
  • 4.  MUKAIYAMA Hironobu (70549740)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 10 results
  • 5.  SATO Masashi (30726716)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 7 results
  • 6.  浜田 聡 (00510083)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 0 results
  • 7.  IZUMI Genkichi (70423952)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 8.  IIJIMA Kazumoto (00240854)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 16 results
  • 9.  TOGAWA Hiroko (30445093)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 4 results
  • 10.  SUZUKI Hiroyuki (80196865)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 11.  SAKO Mayumi (60405454)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 1 results
  • 12.  金城 紀子 (70253987)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 13.  島袋 渡 (30890785)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 14.  MIURA Kenichiro
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 15.  野津 寛大
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 4 results
  • 16.  庄野 朱美
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 2 results
  • 17.  長田 道夫
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results

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