• Search Research Projects
  • Search Researchers
  • How to Use
  1. Back to previous page

SEKIJIMA YOSHIKI  関島 良樹

ORCIDConnect your ORCID iD *help
… Alternative Names

Sekijima Yoshiki  関島 良樹

SEKIJIMA Yoshiki  関島 良樹

Less
Researcher Number 60322715
Other IDs
External Links
Affiliation (Current) 2025: 信州大学, 学術研究院医学系, 教授
Affiliation (based on the past Project Information) *help 2019 – 2023: 信州大学, 学術研究院医学系, 教授
2015 – 2017: 信州大学, 学術研究院医学系, 准教授
2013: 信州大学, 医学部, 准教授
2007 – 2012: Shinshu University, Hospital, Associate Professor
2010: 信州大学, 医学部・附属病院, 准教授
2006: 信州大学, 医学部附属病院, 助教授
Review Section/Research Field
Principal Investigator
Neurology / Basic Section 52010:General internal medicine-related / Basic Section 52020:Neurology-related / General internal medicine (including Psychosomatic medicine)
Except Principal Investigator
Neurology / Human pathology
Keywords
Principal Investigator
トランスサイレチン / アミロイド / アミロイドーシス / 蛋白質 / ATTRアミロイドーシス / 神経科学 / 薬学 / ミスフォールディング / 老化 / 自己抗体 … More / 野生型ATTRアミロイドーシス / PiB-PET / 脳アミロイドアンギオパチー / 遺伝性ATTRアミロイドーシス / バイオマーカー / Transthvretin / Misfolding / Amyloid / Gene / Pharmacology / Neuroscience / Neurolopical Diseases / Protein / 遺伝子 / タンパク質 / 遣伝子 / 脳神経疾患 / 老人性全身性アミロイドーシス / 家族性アミロイドポリニューロパチー / 新規治療 / 早期診断 / 心疾患 / 老年医学 … More
Except Principal Investigator
トランスサイレチン / アミロイドーシス / 野生型TTR / ジフルニサル / 肝移植 / amyloid turnover / FAP / 線維融解 / 低分子薬剤 / アミロイド融解 / FAP / amyloid regression / amyloid turn-over / アミロイド線維融解 / 家族性アミロイドポリニューロパチー / 分子病理 Less
  • Research Projects

    (8 results)
  • Research Products

    (365 results)
  • Co-Researchers

    (19 People)
  •  Elucidation of the pathogenesis of wild-type ATTR amyloidosis, especially focusing on autoimmune mechanismPrincipal Investigator

    • Principal Investigator
      関島 良樹
    • Project Period (FY)
      2022 – 2024
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52010:General internal medicine-related
    • Research Institution
      Shinshu University
  •  Construction of infrastructure for elucidation of pathogenesis and therapeutic development of ATTR-type cerebral amyloid angiopahtyPrincipal Investigator

    • Principal Investigator
      Sekijima Yoshiki
    • Project Period (FY)
      2019 – 2021
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Shinshu University
  •  Development of biomarkers useful for early diagnosis and treatment optimization of ATTR amyloidosisPrincipal Investigator

    • Principal Investigator
      Sekijima Yoshiki
    • Project Period (FY)
      2015 – 2017
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Shinshu University
  •  Elucidation of preventive effect of amyloidogenesis by low molecule drugs in FAP

    • Principal Investigator
      YAZAKI Masahide
    • Project Period (FY)
      2013 – 2015
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Shinshu University
  •  Establishment of early diagnosis method and new non-invasive therapy for transthyretin amyloidosisPrincipal Investigator

    • Principal Investigator
      SEKIJIMA Yoshiki
    • Project Period (FY)
      2011 – 2013
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Shinshu University
  •  A study of the pathomechanism of amyloid fibril turnover in FAP patients after liver transplantation

    • Principal Investigator
      YAZAKI Masahide
    • Project Period (FY)
      2010 – 2012
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Human pathology
    • Research Institution
      Shinshu University
  •  New therapeutic strategies to ameliorate senile systemic amyloidosis by native state stabilization of TTR protein.Principal Investigator

    • Principal Investigator
      SEKIJIMA Yoshiki
    • Project Period (FY)
      2008 – 2010
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      General internal medicine (including Psychosomatic medicine)
    • Research Institution
      Shinshu University
  •  Development of a new therapeutic method for familial amyloid polyneuropathyPrincipal Investigator

    • Principal Investigator
      SEKIJIMA Yoshiki
    • Project Period (FY)
      2006 – 2007
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Shinshu University

All 2022 2021 2020 2019 2018 2017 2016 2015 2014 2013 2012 2011 2010 2009 2008 2007 2006 Other

All Journal Article Presentation Book Other

  • [Book] 今日の治療方針 私はこう治療している2022

    • Author(s)
      関島良樹
    • Total Pages
      2
    • Publisher
      医学書院
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Book] アミロイドーシスのすべて2017

    • Author(s)
      関島良樹
    • Total Pages
      250
    • Publisher
      医歯薬出版
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Book] 遺伝カウンセリングマニュアル2016

    • Author(s)
      関島良樹
    • Total Pages
      472
    • Publisher
      南江堂
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Book] Annual Review2015 神経2015

    • Author(s)
      関島良樹
    • Publisher
      株式会社中外医学社
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Book] 非家族性全身性アミロイドーシスの臨床:Annual Review神経20122012

    • Author(s)
      関島良樹(鈴木則宏ら編集)
    • Publisher
      中外医学社
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Book] Annual Review神経20122012

    • Author(s)
      関島良樹
    • Publisher
      中外医学社
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Book] Familial Transthyretin Amyloidosis (January 2012) in: Gene Reviews at GeneTests : Medical Genetics Information Resource2012

    • Author(s)
      Sekijima Y, Yoshida K, Tokuda T, Ikeda S
    • Publisher
      Copyright, University of Washington, Seattle (database online)
    • URL

      http://www.genetests.org.

    • Data Source
      KAKENHI-PROJECT-23591237
  • [Book] 家族性アミロイドポリニューロパチー:新しい診断と治療のABC 75末梢神経障害2012

    • Author(s)
      関島良樹,池田修一(祖父江元編集)
    • Publisher
      最新医学社
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Book] アミロイドニューロパチー:今日の治療指針2011年版2011

    • Author(s)
      関島良樹(山口徹,北原光夫,福井次矢編集)
    • Publisher
      医学書院
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Book] トランスサイレチンアミロイドーシスに対する新規治療法の開発:アミロイドーシス診療のすべて2011

    • Author(s)
      関島良樹(山田正仁編集)
    • Publisher
      医歯薬出版株式会社
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Book] 今日の治療指針2011年版2011

    • Author(s)
      関島良樹
    • Publisher
      医学書院
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Book] アミロイドーシス診療のすべて2011

    • Author(s)
      関島良樹
    • Publisher
      医歯薬出版株式会社
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Book] 今日の治療指針2011

    • Author(s)
      関島良樹
    • Total Pages
      2
    • Publisher
      医学書院
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Book] アミロイドーシス診療のすべて2011

    • Author(s)
      関島良樹
    • Total Pages
      9
    • Publisher
      医歯薬出版社
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] 核酸医薬を用いたトランスサイレンチン型アミロイドーシス治療2022

    • Author(s)
      関島良樹
    • Journal Title

      DEMENTIA JAPAN

      Volume: 36 Pages: 258-264

    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Journal Article] Cervical myelopathy due to amyloid deposition with accompanying cardiac abnormalities2022

    • Author(s)
      Uehara Masashi、Kuraishi Shugo、Ikegami Shota、Oba Hiroki、Takizawa Takashi、Munakata Ryo、Hatakenaka Terue、Kamanaka Takayuki、Miyaoka Yoshinari、Sekijima Yoshiki、Takahashi Jun
    • Journal Title

      The Journal of Spinal Cord Medicine

      Volume: - Issue: 4 Pages: 1-5

    • DOI

      10.1080/10790268.2022.2027322

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Amyloid nomenclature 2022: update, novel proteins, and recommendations by the International Society of Amyloidosis (ISA) Nomenclature Committee2022

    • Author(s)
      Buxbaum JN, Dispenzieri A, Eisenberg DS, Fandrich M, Merlini G, Saraiva MJM, Sekijima Y, Westermark P
    • Journal Title

      Amyloid

      Volume: 29 Issue: 4 Pages: 213-219

    • DOI

      10.1080/13506129.2022.2147636

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Journal Article] AH amyloid neuropathy: a novel clinical phenotype confirmed by histopathology and mass spectrometry2022

    • Author(s)
      Ohashi Nobuhiko、Katoh Nagaaki、Kasuga Kazuki、Yoshinaga Tsuneaki、Kametani Fuyuki、Yazaki Masahide、Sekijima Yoshiki
    • Journal Title

      Amyloid

      Volume: - Issue: 2 Pages: 1-2

    • DOI

      10.1080/13506129.2022.2049745

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-21K06884, KAKENHI-PROJECT-22K07393
  • [Journal Article] Evidence from a Cohort of 77 Cardiac Biopsy Cases2022

    • Author(s)
      Hasegawa Kanae、Uzui Hiroyasu、Fukuoka Yoshitomo、Miyanaga Dai、Shiomi Yuichiro、Tama Naoto、Ikeda Hiroyuki、Ishida Kentaro、Miyazaki Shinsuke、Sekijima Yoshiki、Naiki Hironobu、Tada Hiroshi
    • Journal Title

      Int. Heart J.

      Volume: 63 Issue: 1 Pages: 49-55

    • DOI

      10.1536/ihj.21-430

    • NAID

      130008145721

    • ISSN
      1349-2365, 1349-3299
    • Year and Date
      2022-01-29
    • Language
      English
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Therapeutic Outcome of Lenalidomide-dexamethasone in Patients with Relapsed or Refractory Systemic Immunoglobulin Light Chain (AL) Amyloidosis : A Single-center Analysis and Review of the Literature2022

    • Author(s)
      Ueno A,Katoh N,Ezawa N,Yoshinaga T,Yazaki M,Sekijima Y
    • Journal Title

      Shinshu Med J

      Volume: 70 Pages: 29-38

    • NAID

      120007188839

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Journal Article] Novel histopathological deposition patterns of EGF-containing fibulin-like extracellular matrix protein 1 amyloidosis: an autopsy case exhibiting a possible association between AEFEMP1 amyloidosis and elastic fibres2022

    • Author(s)
      Ichimata Shojiro、Hata Yukiko、Katoh Nagaaki、Kametani Fuyuki、Yazaki Masahide、Sekijima Yoshiki、Nishida Naoki
    • Journal Title

      Amyloid

      Volume: - Issue: 2 Pages: 1-2

    • DOI

      10.1080/13506129.2021.2020754

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-21K06884, KAKENHI-PROJECT-22K07393
  • [Journal Article] Guidelines and new directions in the therapy and monitoring of ATTRv amyloidosis2022

    • Author(s)
      Ando Y, Adams D, Benson MD, Berk JL, Plant-Bordeneuve V, Coelho T, Conceicao I, Ericzon BG, Obici L, Rapezzi C, Sekijima Y, Ueda M, Palladini G, Merlini Gi
    • Journal Title

      Amyloid

      Volume: 29 Issue: 3 Pages: 143-155

    • DOI

      10.1080/13506129.2022.2052838

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-22K07393, KAKENHI-PROJECT-22K07528, KAKENHI-PROJECT-23K24245
  • [Journal Article] CSF/plasma levels, transthyretin stabilisation and safety of multiple doses of tolcapone in subjects with hereditary ATTR amyloidosis2022

    • Author(s)
      Takahashi Yusuke、Ohashi Nobuhiko、Takasone Ken、Yoshinaga Tsuneaki、Yazaki Masahide、Roberts Michael、Glidden Paul F.、Sekijima Yoshiki
    • Journal Title

      Amyloid

      Volume: - Issue: 3 Pages: 1-7

    • DOI

      10.1080/13506129.2022.2056011

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-21K06884, KAKENHI-PROJECT-22K07393
  • [Journal Article] Somatostatin-derived amyloid deposition associated with duodenal neuroendocrine tumour (NET): a report of novel localised amyloidosis associated with NET2021

    • Author(s)
      Ichimata Shojiro、Katoh Nagaaki、Abe Ryuta、Yoshinaga Tsuneaki、Kametani Fuyuki、Yazaki Masahide、Kusama Yukiko、Sano Kenji、Uehara Takeshi、Sekijima Yoshiki
    • Journal Title

      Amyloid

      Volume: 29 Issue: 1 Pages: 64-65

    • DOI

      10.1080/13506129.2021.1979513

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-21K06884, KAKENHI-PROJECT-22K07393
  • [Journal Article] Absolute quantitative analysis of cardiac amyloidosis using SPECT/CT with 99mTc-pyrophosphate2021

    • Author(s)
      Shin Yanagisawa、Yusuke Takahashi、Jun Sasaki、Ken Takasone、Koji Yoshie、Jun Koyama、Nagaaki Katohi、Masahide Yazaki、Koichiro Kuwahara、Yasunari Fujinaga、Yoshiki Sekijima
    • Journal Title

      Amyloid

      Volume: - Issue: 3 Pages: 1-2

    • DOI

      10.1080/13506129.2021.1903418

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-20K16695, KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-21K06884
  • [Journal Article] Expert consensus on the monitoring of transthyretin amyloid cardiomyopathy2021

    • Author(s)
      Garcia‐Pavia Pablo、Bengel Frank、Brito Dulce、Damy Thibaud、Duca Franz、Dorbala Sharmila、Nativi‐Nicolau Jose、Obici Laura、Rapezzi Claudio、Sekijima Yoshiki、Elliott Perry M.
    • Journal Title

      European Journal of Heart Failure

      Volume: 23 Issue: 6 Pages: 895-905

    • DOI

      10.1002/ejhf.2198

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] アミロイドニューロパチー2021

    • Author(s)
      関島 良樹
    • Journal Title

      CLINICAL NEUROSCIENCE

      Volume: 39 Pages: 1444-1446

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] 遺伝性ATTRアミロイドーシス2021

    • Author(s)
      関島 良樹
    • Journal Title

      Pharma Medica

      Volume: 39 Pages: 39-43

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] 遺伝性ATTRアミロイドーシス2021

    • Author(s)
      関島良樹
    • Journal Title

      Pharma Medica 39(3):39-43

      Volume: 39 Pages: 39-43

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Development of diagnostic antibodies against immunoglobulin heavy chain variable region for heavy chain amyloidosis (AH amyloidosis)2021

    • Author(s)
      Nakagawa Mayuko、Yazaki Masahide、Kametani Fuyuki、Katoh Nagaaki、Yoshinaga Tsuneaki、Higuchi Keiichi、Sekijima Yoshiki
    • Journal Title

      Pathology International

      Volume: 71 Issue: 4 Pages: 245-254

    • DOI

      10.1111/pin.13081

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-21K06884
  • [Journal Article] ATTRアミロイドーシスは決してめずらしい病気ではない2021

    • Author(s)
      関島 良樹
    • Journal Title

      内科

      Volume: 12 Pages: 617-619

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] アミロイドーシス治療の進歩2021

    • Author(s)
      関島 良樹
    • Journal Title

      日本内科学会雑誌

      Volume: 110 Pages: 1170-1177

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] 遺伝性神経疾患の遺伝カウンセリングと発症前診断2021

    • Author(s)
      中村 勝哉,関島 良樹
    • Journal Title

      臨床神経学

      Volume: 61 Pages: 588-593

    • NAID

      130008093293

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Feasibility of assessing progression of transthyretin amyloid polyneuropathy using nerve conduction studies: Findings from the Transthyretin Amyloidosis Outcomes Survey (THAOS)2021

    • Author(s)
      Waddington‐Cruz M?rcia、Ando Yukio、Amass Leslie、Kiszko Jan、Chapman Doug、Sekijima Yoshiki、THAOS investigators
    • Journal Title

      Journal of the Peripheral Nervous System

      Volume: 26 Issue: 2 Pages: 160-166

    • DOI

      10.1111/jns.12444

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Non-invasive detection and differentiation of cardiac amyloidosis using 99mTc-pyrophosphate scintigraphy and 11C-Pittsburgh compound B PET imaging2020

    • Author(s)
      Takasone Ken、Katoh Nagaaki、Takahashi Yusuke、Abe Ryuta、Ezawa Naoki、Yoshinaga Tsuneaki、Yanagisawa Shin、Yazaki Masahide、Oguchi Kazuhiro、Koyama Jun、Sekijima Yoshiki
    • Journal Title

      Amyloid

      Volume: 27 Issue: 4 Pages: 266-274

    • DOI

      10.1080/13506129.2020.1798223

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] 遺伝性 ATTR アミロイドーシス(家族性アミロイドポリニューロパチー)2020

    • Author(s)
      関島良樹
    • Journal Title

      Clinical Neuroscience

      Volume: 38 Pages: 336-338

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Characteristics of Patients with Hereditary Transthyretin Amyloidosis and an Evaluation of the Safety of Tafamidis Meglumine in Japan: An Interim Analysis of an All-case Postmarketing Surveillance2020

    • Author(s)
      Ishii Tomonori、Hirano Yoko、Matsumoto Noriko、Takata Ami、Sekijima Yoshiki、Ueda Mitsuharu、Ando Yukio
    • Journal Title

      Clinical Therapeutics

      Volume: 42 Issue: 9 Pages: 1728-1737.e6

    • DOI

      10.1016/j.clinthera.2020.07.001

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-18K07502, KAKENHI-PROJECT-19H03565
  • [Journal Article] JCS 2020 Guideline on Diagnosis and Treatment of Cardiac Amyloidosis2020

    • Author(s)
      Kitaoka H, Izumi C, Izumiya Y, Inomata T, Ueda M, Kubo T, Koyama J, Sano M, Sekijima Y, Tahara N, Tsukada N, Tsujita K, Tsutsui H, Tomita T, Amano M, Endo J, Okada A, Oda S, Takashio S, Baba Y, Misumi Y, Yazaki M, Anzai T, Ando Y, Isobe M, Kimura T, Fukuda K; Japanese Circulation Society Joint Working Group.
    • Journal Title

      Cir J

      Volume: 84 Issue: 9 Pages: 1610-1671

    • DOI

      10.1253/circj.cj-20-0110

    • NAID

      130007890677

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K08078, KAKENHI-PROJECT-18K08110, KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-18K07502
  • [Journal Article] Dialysis-related amyloidosis associated with a novel β2-microglobulin variant2020

    • Author(s)
      Mizuno Hiroki、Hoshino Junichi、So Masatomo、Kogure Yuta、Fujii Takeshi、Ubara Yoshifumi、Takaichi Kenmei、Nakaniwa Tetsuko、Tanaka Hideaki、Kurisu Genji、Kametani Fuyuki、Nakagawa Mayuko、Yoshinaga Tsuneaki、Sekijima Yoshiki、Higuchi Keiichi、Goto Yuji、Yazaki Masahide
    • Journal Title

      Amyloid

      Volume: 28 Issue: 1 Pages: 42-49

    • DOI

      10.1080/13506129.2020.1813097

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959, KAKENHI-PLANNED-17H06352
  • [Journal Article] 心アミロイドーシスの治療 -ATTRv, ATTRwtに対する治療-2020

    • Author(s)
      関島良樹
    • Journal Title

      Heart View

      Volume: 24 Pages: 1092-1098

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Human amyloidosis, still intractable but becoming curable: the essential role of pathological diagnosis in the selection of type-specific therapeutics.2020

    • Author(s)
      Naiki H, Sekijima Y, Ueda M, Ohashi K, Hoshii Y, Shimoda M, Ando Y.
    • Journal Title

      Pathol Int

      Volume: 70 Issue: 4 Pages: 191-198

    • DOI

      10.1111/pin.12902

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-16H05170, KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-18K07502, KAKENHI-PROJECT-19H03565
  • [Journal Article] A case of novel amyloidosis: glucagon-derived amyloid deposition associated with pancreatic neuroendocrine tumour2020

    • Author(s)
      Ichimata Shojiro、Katoh Nagaaki、Abe Ryuta、Yoshinaga Tsuneaki、Kametani Fuyuki、Yazaki Masahide、Uehara Takeshi、Sekijima Yoshiki
    • Journal Title

      Amyloid

      Volume: 28 Issue: 1 Pages: 72-73

    • DOI

      10.1080/13506129.2020.1785417

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Monitoring of asymptomatic family members at risk of hereditary transthyretin amyloidosis for early intervention with disease-modifying therapies2020

    • Author(s)
      Ueda Mitsuharu、Sekijima Yoshiki、Koike Haruki、Yamashita Taro、Yoshinaga Tsuneaki、Ishii Tomonori、Ando Yukio
    • Journal Title

      Journal of the Neurological Sciences

      Volume: 414 Pages: 116813-116813

    • DOI

      10.1016/j.jns.2020.116813

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-18K07502, KAKENHI-PROJECT-19H03565
  • [Journal Article] 遺伝性ATTRアミロイドーシス2020

    • Author(s)
      関島良樹
    • Journal Title

      遺伝子医学

      Volume: 32 Pages: 513-516

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] 不治の病から治療可能な疾患に ―アミロイドーシス治療の最前線―2020

    • Author(s)
      関島良樹
    • Journal Title

      自律神経

      Volume: 57 Pages: 114-117

    • NAID

      130007873275

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] 野生型ATTRアミロイドーシス2020

    • Author(s)
      関島良樹
    • Journal Title

      BioClinica

      Volume: 35 Pages: 513-516

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] An autopsy case of amyloid tubulopathy exhibiting characteristic spheroid-type deposition.2020

    • Author(s)
      Ichimata S, Hata Y, Abe R, Yoshinaga T, Katoh N, Kametani F, Yazaki M, Sekijima Y, Ehara T, Nishida N
    • Journal Title

      Virchows Arch

      Volume: 477 Issue: 1 Pages: 157-163

    • DOI

      10.1007/s00428-019-02740-4

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-17K08739
  • [Journal Article] 遺伝性ATTRアミロイドーシス(FAP)を見逃すな! ―手根管症候群は重要なサイン―2020

    • Author(s)
      関島良樹
    • Journal Title

      Peripheral Nerve 31(2); 250-51

      Volume: 31 Pages: 250-251

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Distribution of amyloidosis subtypes based on tissue biopsy site ? Consecutive analysis of 729 patients at a single amyloidosis center in Japan2020

    • Author(s)
      Abe Ryuta、Katoh Nagaaki、Takahashi Yusuke、Takasone Ken、Yoshinaga Tsuneaki、Yazaki Masahide、Kametani Fuyuki、Sekijima Yoshiki
    • Journal Title

      Pathology International

      Volume: 71 Issue: 1 Pages: 70-79

    • DOI

      10.1111/pin.13041

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Amyloid nomenclature 2020: update and recommendations by the International Society of Amyloidosis (ISA) nomenclature committee2020

    • Author(s)
      Benson Merrill D.、Buxbaum Joel N.、Eisenberg David S.、Merlini Giampaolo、Saraiva Maria J. M.、Sekijima Yoshiki、Sipe Jean D.、Westermark Per
    • Journal Title

      Amyloid

      Volume: 27 Issue: 4 Pages: 217-222

    • DOI

      10.1080/13506129.2020.1835263

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] 野生型トランスサイレチンアミロイドーシスと脳塞栓症2020

    • Author(s)
      関島良樹
    • Journal Title

      神経内科

      Volume: 93 Pages: 476-480

    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Electrophysiological demyelinating features in hereditary ATTR amyloidosis.2019

    • Author(s)
      Ohashi N, Kodaira M, Morita H, Sekijima Y.
    • Journal Title

      Amyloid

      Volume: 26 Issue: 1 Pages: 15-23

    • DOI

      10.1080/13506129.2018.1564903

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] The current status of the Transthyretin Amyloidosis Outcomes Survey (THAOS) in Japan2019

    • Author(s)
      Sekijima Yoshiki、Mundayat Rajiv、Ishii Tomonori、Ando Yukio
    • Journal Title

      Amyloid

      Volume: 26 Issue: sup1 Pages: 61-62

    • DOI

      10.1080/13506129.2019.1583182

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-19H03565
  • [Journal Article] Patient profile with ATTR-FAP and evaluation of the safety and efficacy of tafamidis meglumine in Japan - interim analysis in post-marketing surveillance2019

    • Author(s)
      Ishii Tomonori、Sekijima Yoshiki、Ando Yukio
    • Journal Title

      Amyloid

      Volume: 26 Issue: sup1 Pages: 45-46

    • DOI

      10.1080/13506129.2019.1582508

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-19H03565
  • [Journal Article] Length-dependent truncal Aδ-fiber dysfunction in hereditary transthyretin amyloidosis: An intra-epidermal electrical stimulation study2019

    • Author(s)
      Kodaira Minori、Ohashi Nobuhiko、Morita Hiroshi、Sekijima Yoshiki
    • Journal Title

      Clinical Neurophysiology

      Volume: 130 Issue: 6 Pages: 903-910

    • DOI

      10.1016/j.clinph.2019.03.007

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] A case of cerebral amyloid angiopathy-type hereditary ATTR amyloidosis with Y69H (p.Y89H) variant displaying transient focal neurological episodes as the main symptom2019

    • Author(s)
      Yamada Yumi、Fukushima Takao、Kodama Satoshi、Shimizu Hiroshi、Kakita Akiyoshi、Makino Kunihiko、Sekijima Yoshiki
    • Journal Title

      Amyloid

      Volume: 26 Issue: 4 Pages: 251-252

    • DOI

      10.1080/13506129.2019.1632829

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] Transthyretin deposition in the eye in the era of effective therapy for hereditary ATTRV30M amyloidosis2019

    • Author(s)
      Buxbaum Joel N.、Brannagan Thomas、Buades-Reines Juan、Cisneros Eugenia、Conceicao Isabel、Kyriakides Theodoros、Merlini Giampaolo、Obici Laura、Plante-Bordeneuve Violaine、Rousseau Antoine、Sekijima Yoshiki、Imai Akira、Waddington Cruz M?rcia、Yamada Masahito
    • Journal Title

      Amyloid

      Volume: 26 Issue: 1 Pages: 10-14

    • DOI

      10.1080/13506129.2018.1554563

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Journal Article] A Statement on the Appropriate Administration of Tafamidis in Patients With Transthyretin Cardiac Amyloidosis2019

    • Author(s)
      Endo Jin、Sano Motoaki、Izumiya Yasuhiro、Tsujita Kenichi、Nakamura Kazufumi、Tahara Nobuhiro、Kuwahara Koichiro、Inomata Takayuki、Ueda Mitsuharu、Sekijima Yoshiki、Ando Yukio、Tsutsui Hiroyuki、Isobe Mitsuaki、Fukuda Keiichi
    • Journal Title

      Circ J

      Volume: 84 Issue: 1 Pages: 15-17

    • DOI

      10.1253/circj.CJ-19-0811

    • NAID

      130007772713

    • ISSN
      1346-9843, 1347-4820
    • Year and Date
      2019-12-25
    • Language
      English
    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07502, KAKENHI-PROJECT-18K08110, KAKENHI-PROJECT-19K07959, KAKENHI-PROJECT-19K08493, KAKENHI-PROJECT-19H03565, KAKENHI-PROJECT-17K09564
  • [Journal Article] Diagnosis and management of transthyretin familial amyloid polyneuropathy in Japan: red-flag symptom clusters and treatment algorithm.2018

    • Author(s)
      Sekijima Y, Ueda M, Koike H, Misawa S, Ishii T, Ando Y
    • Journal Title

      Orphanet J Rare Dis

      Volume: 13 Issue: 1 Pages: 6-6

    • DOI

      10.1186/s13023-017-0726-x

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-15H04841, KAKENHI-PROJECT-15K09336, KAKENHI-PROJECT-18K07502
  • [Journal Article] Visualization of multiple organ amyloid involvement in systemic amyloidosis using (11)C-PiB PET imaging2018

    • Author(s)
      Ezawa N, Katoh N, Oguchi K, Yoshinaga T, Yazaki M, Sekijima Y
    • Journal Title

      Eur J Nucl Med Mol Imaging

      Volume: 45 Issue: 3 Pages: 452-461

    • DOI

      10.1007/s00259-017-3814-1

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K08739, KAKENHI-PROJECT-16K21066, KAKENHI-PROJECT-15K09336
  • [Journal Article] 遺伝性ATTRアミロイドーシス2018

    • Author(s)
      関島良樹
    • Journal Title

      Clinical Neuroscience

      Volume: 36 Pages: 198-199

    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] ATTR型CAAの臨床的意義2018

    • Author(s)
      関島良樹
    • Journal Title

      神経内科

      Volume: 88 Pages: 300-304

    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] アミロイドニューロパチーの診断と治療の最前線2017

    • Author(s)
      関島良樹
    • Journal Title

      Peripheral Nerve

      Volume: 28 Pages: 246-250

    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] Peptide probes detect misfolded transthyretin oligomers in the plasma of hereditary amyloidosis patients2017

    • Author(s)
      Schonhoft JD, Monteiro C, Plate L, Eisele YS, Kelly JM, Boland D, Parker CG, Cravatt BF, Teruya S, Helmke S, Maurer M, Berk J, Sekijima Y, Novais M, Coelho T, Powers ET, Kelly JW
    • Journal Title

      Sci Transl Med

      Volume: 9 Issue: 407

    • DOI

      10.1126/scitranslmed.aam7621

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] Pseudo-homozygous mutation due to a primer site polymorphism in hereditary ATTR amyloidosis -A pitfall of PCR-based genetic testing-2017

    • Author(s)
      Shibata Y, Matsushima M, Yabe I, Matsuda K, Nagai A, Kano T, Yamada M, Sekijima Y, Sasaki H
    • Journal Title

      Amyloid

      Volume: 印刷中 Issue: 1 Pages: 66-67

    • DOI

      10.1080/13506129.2017.1307821

    • NAID

      120006425604

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] First nationwide survey on systemic wild-type ATTR amyloidosis in Japan2017

    • Author(s)
      Sekijima Y、Yazaki M、Ueda M、Koike H、Yamada M、Ando Y
    • Journal Title

      Amyloid

      Volume: 25 Issue: 1 Pages: 8-10

    • DOI

      10.1080/13506129.2017.1409706

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K08739, KAKENHI-PROJECT-15H04841, KAKENHI-PROJECT-15K09318, KAKENHI-PROJECT-15K09336
  • [Journal Article] Cardiac amyloidosis associated with amyloidogenic transthyretin V122I variant in an elderly Japanese woman2017

    • Author(s)
      Yoshinaga T, Yazaki M, Ohno M, Komada S, Koyama J, Sekijima Y
    • Journal Title

      Circulation Journal

      Volume: 印刷中

    • NAID

      130005679610

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] Marked biochemical difference in amyloid proportion between intra- and extraocular tissues in a liver-transplanted patient with hereditary ATTR amyloidosis.2017

    • Author(s)
      Yoshinaga T, Yazaki M, Kametani F, Sekijima Y, Iesato Y, Miyahara T, Tsuchiya-Suzuki A, Sano K, Higuchi K, Ikeda SI.
    • Journal Title

      Amyloid.

      Volume: 13 (1) Issue: 1 Pages: 1-7

    • DOI

      10.1080/13506129.2016.1276055

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-26293084, KAKENHI-PROJECT-26670152, KAKENHI-PROJECT-16K21066, KAKENHI-PROJECT-17K08739, KAKENHI-PROJECT-15K09336
  • [Journal Article] Cardiac Amyloidosis Associated With Amyloidogenic Transthyretin V122I Variant in an Elderly Japanese Woman2017

    • Author(s)
      Yoshinaga T, Yazaki M, 他4名
    • Journal Title

      Circ J

      Volume: 81 Issue: 6 Pages: 893-894

    • DOI

      10.1253/circj.CJ-16-1202

    • NAID

      130005679610

    • ISSN
      1346-9843, 1347-4820
    • Language
      English
    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-17K08739, KAKENHI-PROJECT-16K21066, KAKENHI-PROJECT-15K09336
  • [Journal Article] 家族性アミロイドポリニューロパチーの新規薬物治療2016

    • Author(s)
      関島良樹
    • Journal Title

      自律神経

      Volume: 53 Pages: 145-148

    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] トランスサイレチン型家族性アミロイドポリニューロパチーにおける薬物療法の機序と治療効果2016

    • Author(s)
      関島良樹
    • Journal Title

      神経内科

      Volume: 84 Pages: 150-155

    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] 心アミロイドーシスの診断と治療の最近の進歩2016

    • Author(s)
      関島良樹
    • Journal Title

      心血管薬物治療

      Volume: 4 Pages: 43-47

    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] 遺伝性ATTRアミロイドーシスの診断と治療2016

    • Author(s)
      関島良樹
    • Journal Title

      Peripheral Nerve

      Volume: 26 Pages: 157-160

    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] Extremely early onset hereditary ATTR amyloidosis with G47R (p.G67R) mutation2016

    • Author(s)
      Kobayashi Y, Sekijima Y, Ogawa Y, Kondo Y, Miyazaki D, Ikeda SI
    • Journal Title

      Amyloid

      Volume: 23 Issue: 3 Pages: 205-206

    • DOI

      10.1080/13506129.2016.1185410

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] Carpal tunnel syndrome: a common initial symptom of systemic wild-type ATTR (ATTRwt) amyloidosis.2016

    • Author(s)
      Nakagawa M, Sekijima Y, Yazaki M, Tojo K, Yoshinaga T, Doden T, Koyama J,
    • Journal Title

      Amyloid

      Volume: 23 Issue: 1 Pages: 58-63

    • DOI

      10.3109/13506129.2015.1135792

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461275, KAKENHI-PROJECT-15K09336, KAKENHI-PROJECT-16K21066
  • [Journal Article] Cerebral amyloid angiopathy in post-transplant patients with hereditary ATTR amyloidosis2016

    • Author(s)
      Sekijima Y, Yazaki M, Oguchi K, Ezawa N, Yoshinaga T, Yamada M, Yahikozawa H, Watanabe M, Kametani F, Ikeda SI.
    • Journal Title

      Neurology

      Volume: in press

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] Comparison of the standard and speckle tracking echocardiographic features of wild type and mutated transthyretin cardiac amyloidoses.2016

    • Author(s)
      Minamisawa M, Koyama J, Sekijima Y, Ikeda S-I, Kozuka A, Ebisawa S, Miura T, Motoki H, Okada A, Izawa A, Ikeda U.
    • Journal Title

      Eur Heart J Cardiovasc Imaging

      Volume: 17 Issue: 4 Pages: 402-10

    • DOI

      10.1093/ehjci/jew003

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-26461061, KAKENHI-PROJECT-15K09336
  • [Journal Article] Effects of tafamidis treatment on transthyretin (TTR) stabilization, efficacy, and safety in Japanese patients with familial amyloid polyneuropathy (TTR-FAP) with Val30Met and non-Varl30Met: A phase III, open-label study.2016

    • Author(s)
      Ando Y, Sekijima Y, Obayashi K, Yamashita T, Ueda M, Misumi Y, Morita H, Machii K, Ohta M, Takata A, Ikeda S.
    • Journal Title

      J Neurol Sci

      Volume: 362 Pages: 266-271

    • DOI

      10.1016/j.jns.2016.01.046

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-15K09318, KAKENHI-PROJECT-15K09336, KAKENHI-PROJECT-15K15195, KAKENHI-PROJECT-15H04841, KAKENHI-PROJECT-26860672
  • [Journal Article] Cerebral amyloid angiopathy in post-transplant patients with hereditary ATTR amyloidosis2016

    • Author(s)
      Sekijima Y, Yazaki M, Oguchi K, 他7名.
    • Journal Title

      Neurology

      Volume: in press

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Journal Article] ATTRアミロイドーシスによる心臓アミロイドーシスの治療2016

    • Author(s)
      関島良樹
    • Journal Title

      Heart View

      Volume: 20 Pages: 187-193

    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] Cerebral amyloid angiopathy in post-transplant patients with hereditary ATTR amyloidosis2016

    • Author(s)
      Sekijima Y, Yazaki M, Oguchi K, Ezawa N, Yoshinaga T, Yamada M, Yahikozawa H, Watanabe M, Kametani F, Ikeda SI
    • Journal Title

      Neurology

      Volume: 87 Issue: 8 Pages: 773-781

    • DOI

      10.1212/wnl.0000000000003001

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-15K09336, KAKENHI-PROJECT-16K21066
  • [Journal Article] 遺伝性ATTRアミロイドーシスの新規治療指針2016

    • Author(s)
      関島良樹
    • Journal Title

      医学のあゆみ

      Volume: 258 Pages: 671-676

    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] アミロイドーシスの診断と治療の進歩2016

    • Author(s)
      関島良樹,加藤修明
    • Journal Title

      病理と臨床

      Volume: 34 Pages: 466-471

    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] a serious complication in post-transplant patients with familial amyloid polyneuropathy2015

    • Author(s)
      Sekijima Y
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 86 Issue: 2 Pages: 124-124

    • DOI

      10.1136/jnnp-2014-308576

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] Safety and efficacy of long-term diflunisal administration in hereditary transthyretin (ATTR) amyloidosis2015

    • Author(s)
      Sekijima Y, Tojo K, Morita H, Koyama J, Ikeda SI
    • Journal Title

      Amyloid

      Volume: 22 Issue: 2 Pages: 79-83

    • DOI

      10.3109/13506129.2014.997872

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] The first pure form of Ostertag type amyloidosis in Japan: a sporadic case of hereditary fibrinogen Aa-chain amyloidosis associated with a novel frameshift variant2015

    • Author(s)
      Yazaki M, Yoshinaga T, Sekijima Y, Nishio S, Kanizawa Y, Kametani F, Miyashita K, Hachiya N, Higuchi K, Ikeda S.
    • Journal Title

      Amyloid

      Volume: 印刷中

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Journal Article] The first pure form of Ostertag-type amyloidosis in Japan: a sporadic case of hereditary fibrinogen Aα-chain amyloidosis associated with a novel frameshift variant2015

    • Author(s)
      Yazaki M, Yoshinaga T, Sekijima Y, Nishio S, Kanizawa Y, Kametani F, Miyashita K, Hachiya N, Higuchi K, Ikeda SI.
    • Journal Title

      Amyloid

      Volume: 22 Issue: 2 Pages: 142-144

    • DOI

      10.3109/13506129.2015.1037389

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-15K09336, KAKENHI-PROJECT-26670152, KAKENHI-PROJECT-25461275, KAKENHI-PROJECT-25293094, KAKENHI-PROJECT-26293084
  • [Journal Article] Left ventricular deformation and torsion assessed by speckle-tracking echocardiography in patients with mutated transthyretin-associated cardiac amyloidosis and the effect of diflunisal on myocardial function2015

    • Author(s)
      Koyama J, Minamisawa M, Sekijima Y, Ikeda SI, Kozuka A, Ebisawa S, Miura T, Motoki H, Okada A, Izawa A, Ikeda U.
    • Journal Title

      IJC Heart & Vasculature

      Volume: 9 Pages: 1-10

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] Transthyretin (ATTR) amyloidosis: clinical spectrum, molecular pathogenesis and disease-modifying treatments2015

    • Author(s)
      Sekijima Y
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 86 Issue: 9 Pages: 1036-1043

    • DOI

      10.1136/jnnp-2014-308724

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] Regression of localized ureter amyloidosis after treatment with steroids suggested by Tc-99 m pyrophosphate scintigraphy2015

    • Author(s)
      Ikeda J, Katoh N, Sekijima Y, Ikeda S
    • Journal Title

      Amyloid

      Volume: 22 Issue: 4 Pages: 257-258

    • DOI

      10.3109/13506129.2015.1089860

    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Journal Article] The pathological and biochemical identification of possible seed-lesions of transmitted transthyretin amyloidosis after domino liver transplantaion.2015

    • Author(s)
      Yoshinaga, T, Yazaki M, Sekijima Y, Kametani F, Miyashita K, Hachiya N, Tanaka T, Koaudo N, Higuchi K, Ikeda S.
    • Journal Title

      J Path: Clin Res 2015

      Volume: 1 Issue: 2 Pages: 1-8

    • DOI

      10.1002/cjp2.36

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-26660176, KAKENHI-PROJECT-26670152, KAKENHI-PROJECT-25461275, KAKENHI-PROJECT-26293084, KAKENHI-PROJECT-15K09336, KAKENHI-PROJECT-16K21066
  • [Journal Article] Pathological, biochemical, and biophysical characteristics of the transthyretin variant Y114H (p.Y134H) explain its very mild clinical phenotype2015

    • Author(s)
      Sekijima Y, Campos RI, Hammarstrom P, Nilsson KP, Yoshinaga T, Nagamatsu K, Yazaki M, Kametani F, Ikeda SI.
    • Journal Title

      Peripher Nerv Syst

      Volume: 20 Issue: 4 Pages: 372-379

    • DOI

      10.1111/jns.12143

    • Peer Reviewed / Acknowledgement Compliant / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336, KAKENHI-PROJECT-25461275
  • [Journal Article] p.E66Q Mutation in the GLA Gene is Associated with a High Risk of Cerebral Small-Vessel Occlusion in Elderly Japanese Males2014

    • Author(s)
      Nakamura K, Sekijima Y, NakamuraK, Hattori K, Nagamatsu K, Shimizu Y, Yazaki M, Sakurai A, Endo F, Fukushima Y, Ikeda S
    • Journal Title

      Eur J Neurol

      Volume: 21 Issue: 1 Pages: 49-56

    • DOI

      10.1111/ene.12214

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591504, KAKENHI-PROJECT-25461275
  • [Journal Article] High prevalence of ATTR amyloidosis in endomyocardial biopsy-proven cardiac amyloidosis patients2013

    • Author(s)
      Nakagawa M, Sekijima Y, Tojo K, Ikeda SI
    • Journal Title

      Amyloid

      Volume: 20 Issue: 2 Pages: 138-40

    • DOI

      10.3109/13506129.2013.790809

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] 家族性アミロイドポリニューロパチー2013

    • Author(s)
      関島良樹,池田修一
    • Journal Title

      医学のあゆみ

      Volume: 247 Pages: 515-520

    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] Bullous formation in a patient with familial amyloid polyneuropathy type I2013

    • Author(s)
      Kobayashi A, Uhara H, Kido K, Sekijima Y, Tojo K, Ikeda S, Okuyama R
    • Journal Title

      Int J Dermatol

      Volume: 52 Issue: 11 Pages: 1398-400

    • DOI

      10.1111/j.1365-4632.2011.05146.x

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591237, KAKENHI-PROJECT-23591615
  • [Journal Article] Repurposing diflunisal for familial amyloid polyneuropathy: a randomized clinical trial2013

    • Author(s)
      Berk JL, Suhr OB, Obici L, Sekijima Y, Zeldenrust SR, Yamashita T, Heneghan MA, Gorevic PD, Litchy WJ, Wiesman JF, Nordh E, Corato M, Lozza A, Cortese A, Robinson-Papp J, Colton T, Rybin DV, Bisbee AB, Ando Y, Ikeda S, Seldin DC, Merlini G, Skinner M, Kelly JW, Dyck PJ; Diflunisal Trial Consortium
    • Journal Title

      JAMA

      Volume: 310 Issue: 24 Pages: 2658-2667

    • DOI

      10.1001/jama.2013.283815

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23500430, KAKENHI-PROJECT-23591237
  • [Journal Article] Follow-up nationwide survey on predictive genetic testing for late-onset hereditary neurological diseases in Japan2013

    • Author(s)
      Tanaka K, Sekijima Y, Yoshida K, Tamai M, Kosho T, Sakurai A, Wakui K, Ikeda SI, Fukushima Y
    • Journal Title

      J Hum Genet

      Volume: 58 Issue: 8 Pages: 560-563

    • DOI

      10.1038/jhg.2013.34

    • NAID

      10031195287

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591237, KAKENHI-PROJECT-23613004
  • [Journal Article] 家族性アミロイドポリニューロパチーに対する新規治療法の開発と臨床応用2013

    • Author(s)
      関島良樹
    • Journal Title

      日本遺伝カウンセリング学会誌

      Volume: 34 Pages: 31-37

    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] Steady turnover of amyloid fibril proteins in gastric mucosa after liver transplantation in familial amyloid polyneuropathy2013

    • Author(s)
      Tsuchiya-Suzuki A, Yazaki M, Sekijima Y, Kametani F, Ikeda S
    • Journal Title

      Amyloid

      Volume: 20 Issue: 3 Pages: 156-163

    • DOI

      10.3109/13506129.2013.807790

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591237, KAKENHI-PROJECT-25461275
  • [Journal Article] Steady turnover of amyloid fibril proteins in gastric mucosa after liver transplantation in familial amyloid polyneuropathy.2013

    • Author(s)
      Tsuchiya-Suzuki A, Yazaki M, Sekijima Y, Kametani F, Ikeda S.
    • Journal Title

      Amyloid

      Volume: (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590332
  • [Journal Article] 信州大学医学部附属病院遺伝子診療部における遺伝性神経筋疾患の発症前診断の現状2013

    • Author(s)
      田中敬子,関島良樹,吉田邦広,水内麻子,山下浩美,玉井真理子,池田修一,福嶋義光
    • Journal Title

      臨床神経学

      Volume: 53 Pages: 196-204

    • NAID

      40019608487

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] The Diflunisal Trial: study accrual and drug tolerance.2012

    • Author(s)
      Berk JL, Suhr OB, Sekijima Y, Yamashita T, Heneghan M, Zeldenrust SR, Ando Y, Ikeda S, Gorevic P, Merlini G, Kelly JW, Skinner M, Bisbee AB, Dyck PJ, Obici L
    • Journal Title

      Amyloid

      Volume: Suppl 1 Issue: sup1 Pages: 37-38

    • DOI

      10.3109/13506129.2012.678509

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23500430, KAKENHI-PROJECT-23591237, KAKENHI-PROJECT-23659303, KAKENHI-PROJECT-24249036
  • [Journal Article] Arterial thromboembolism in senile systemic amyloidosis: report of two cases2012

    • Author(s)
      Nakagawa M, Tojo K, Sekijima Y, Yamazaki KH, Ikeda S.
    • Journal Title

      Amyloid

      Volume: 19 Issue: 2 Pages: 118-121

    • DOI

      10.3109/13506129.2012.685131

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] Two Siblings Diagnosed to Have Transthyretin-related Familial Amyloid Cardiomyopathy Around the Same Time at Different Hospitals2012

    • Author(s)
      Miyamura M, Terasaki F, Ishibashi K, Shimazaki C, Kimura F, Kuwabara H, Tsuji M, Shibayama Y, Sekijima Y, Tojo K, Ishizaka N.
    • Journal Title

      Intern. Med.

      Volume: 51 Issue: 5 Pages: 465-469

    • DOI

      10.2169/internalmedicine.51.6369

    • NAID

      130002061902

    • ISSN
      0918-2918, 1349-7235
    • Language
      English
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] 心アミロイドーシスの診断と治療2012

    • Author(s)
      関島良樹
    • Journal Title

      循環器内科

      Volume: 71 Pages: 526-533

    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] 家族性アミロイドポリニューロパチー2012

    • Author(s)
      関島良樹,池田修一
    • Journal Title

      新しい診断と治療のABC

      Volume: 75 Pages: 186-195

    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] Two Siblings Diagnosed to Have Transthyretin-related Familial Amyloid Cardiomyopathy Around the Same Time at Different Hospitals2012

    • Author(s)
      Miyamura M, Terasaki F, Ishibashi K, Shimazaki C, Kimura F, Kuwabara H, Tsuji M, Shibayama Y, Sekijima Y, Tojo K, Ishizaka N
    • Journal Title

      Intern Med

      Volume: 51 Pages: 465-9

    • NAID

      130002061902

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] Wild-type transthyretin significantly contributes to the formation of amyloid fibrils in familial amyloid polyneuropathy patients with amyloidogenic transthyretin Val30Met.2011

    • Author(s)
      Tsuchiya-Suzuki A, Yazaki M, Kametani F,Sekijima Y, Ikeda S.
    • Journal Title

      Hum Pathol.

      Volume: 42 Issue: 2 Pages: 236-243

    • DOI

      10.1016/j.humpath.2010.06.014

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590332
  • [Journal Article] Wild-type transthyretin significantly contributes to the formation of amyloid fibrils in familial amyloid polyneuropathy patients with amyloidogenic transthyretin Val30Met.2011

    • Author(s)
      Tsuchiya-Suzuki A, Yazakia M, Kametani F, Sekijima Y, Ikeda SI
    • Journal Title

      Hum Pathol 42

      Pages: 236-243

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] High prevalence of wild-type transthyretin deposition in patients with idiopathic carpal tunnel syndrome : a common cause of carpal tunnel syndrome in the elderly2011

    • Author(s)
      Sekijima Y, Uchiyama S, Tojo K, Sano K, Shimizu Y, Imaeda T, Hoshii Y, Kato H, Ikeda SI
    • Journal Title

      Hum Pathol

      Volume: 42 Issue: 11 Pages: 1785-91

    • DOI

      10.1016/j.humpath.2011.03.004

    • NAID

      120007107381

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] High prevalence of wild-type transthyretin deposition in patients with idiopathic carpal tunnel syndrome : a common cause of carpal tunnel syndrome in the elderly2011

    • Author(s)
      Sekijima Y, Uchiyama S, Tojo K, Sano K, Shimizu Y, Imaeda T, Hoshii Y, Kato H, Ikeda SI
    • Journal Title

      Hum Pathol

      Volume: 印刷中

    • NAID

      120007107381

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] 家族性アミロイドポリニューロパチーの新しい治療戦略2011

    • Author(s)
      関島良樹
    • Journal Title

      神経内科

      Volume: 74 Pages: 360-366

    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] High prevalence of wild-type transthyretin deposition in patients with idiopathic carpal tunnel syndrome : a common cause of carpal tunnel syndrome in the elderly.2011

    • Author(s)
      Sekijima Y, Uchiyama S, Tojo K, Sano K, Shimizu Y, Imaeda T, Hoshii Y, Kato H, Ikeda SI
    • Journal Title

      Hum Pathol in press

    • NAID

      120007107381

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] Wild-type transthyretin significantly contributes to the formation of amyloid fibris in familial amyloid polyneuropathy patients with amyloidogenic transthyretin Val30Met.2011

    • Author(s)
      Tsuchiya-Suzuki A, Yazakia M, Kametani F, Sekijima Y, Ikeda SI.
    • Journal Title

      Hum Pathol

      Volume: 42 Pages: 236-243

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] Diagnostic value of abdominal wall fat pad biopsy in senile systemic amyloidosis2011

    • Author(s)
      Ikeda SI, Sekijima Y, Tojo K, Koyama J
    • Journal Title

      Amyloid

      Volume: 18 Issue: 4 Pages: 211-5

    • DOI

      10.3109/13506129.2011.623199

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] 非家族性全身性アミロイドーシスの疫学と臨床2011

    • Author(s)
      関島良樹
    • Journal Title

      臨床神経

      Volume: 51 Pages: 1130-1133

    • Data Source
      KAKENHI-PROJECT-23591237
  • [Journal Article] Upper limb neuropathy such as carpal tunnel syndrome as an initial manifestation of ATTR Val30Met familial amyloid polyneuropathy.2010

    • Author(s)
      Tojo K, Tsuchiya-Suzuki A, Sekijima Y, Morita H, Sumita N, Ikeda S.
    • Journal Title

      Amyloid 17

      Pages: 32-35

    • NAID

      120007110418

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] Upper limb neuropathy such as carpal tunnel syndrome as an initial manifestation of ATTR Val30Met familial amyloid polyneuropathy.2010

    • Author(s)
      Tojo K, Tsuchiya-Suzuki A, Sekijima Y, Morita H, Sumita N, Ikeda S
    • Journal Title

      Amyloid 17

      Pages: 32-35

    • NAID

      120007110418

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] 家族性アミロイドポリニューロパチーの病因と治療戦略2010

    • Author(s)
      関島良樹
    • Journal Title

      神経治療学 27

      Pages: 801-807

    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] 家族性アミロイドポリニューロパチーの病因と治療戦略2010

    • Author(s)
      関島良樹
    • Journal Title

      神経治療学

      Volume: 27 Pages: 801-807

    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] SELDI-TOF MS evaluation of variant transthyretins for diagnosis and pathogenesis of familial amyloidotic polyneuropathy.2009

    • Author(s)
      Ueda M, Misumi Y, Mizuguchi M, Nakamura M, Yamashita T, Sekijima Y, Ota K, Shinriki S, Jono H, Ikeda SI, Suhr OB, Ando Y.
    • Journal Title

      Clin Chem 55

      Pages: 1223-1227

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] TTRアミロイド沈着の分子機構とその抑制2009

    • Author(s)
      関島良樹
    • Journal Title

      医学のあゆみ 229

      Pages: 349-356

    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] Familial Transthyretin Amyloidosis2009

    • Author(s)
      Sekijima Y, Yoshida K, Tokuda T, Ikeda S-I
    • Journal Title

      GeneReviews at GeneTests : Medical Genetics Information Resource [database online]. Copyright, University of Washington, Seattle. updated September 2009(database online)

    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] 手根管症候群を呈した野生型トランスサイレチンアミロイドーシス4例の臨床像の検討2008

    • Author(s)
      関島良樹
    • Journal Title

      信州医学雑誌 56

      Pages: 115-124

    • NAID

      10025624948

    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] 家族性アミロイドポリニューロパチーの遺伝子診断2008

    • Author(s)
      関島良樹, 吉田邦広
    • Journal Title

      神経内科 69

      Pages: 513-521

    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] Non-senile wild-type transthyretin systemic amyloidoses presenting as bilateral carpal tunnel syndrome.2008

    • Author(s)
      Kodaira M, Sekijima Y, Tojo K, Tsuchiya A, Yazaki M, Ikeda S, Hoshii Y, Tachibana S.
    • Journal Title

      J Peripher Nerv Syst 13

      Pages: 148-150

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] Pathogenesis of and therapeutic strategies to ameliorate the transthyretin amyloidoses.2008

    • Author(s)
      Sekijima Y. Kelly JW, Ikeda S.
    • Journal Title

      Curr Pharm Des 14

      Pages: 3219-3230

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] 手根管症候群を呈した野生型トランスサイレチンアミロイドーシス4例の臨床像の検討2008

    • Author(s)
      小平農, 関島良樹, 武井洋一, 土屋彩子, .東城加奈, 矢崎正英, 森田洋, 吉田邦広, 星井嘉信, 池田修一
    • Journal Title

      末梢神経 19

      Pages: 54-63

    • NAID

      10025624948

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] 手根管症候群を呈した野生型トランスサイレチンアミロイドーシス4例の臨床像の検討2008

    • Author(s)
      小平農, 関島良樹, 武井洋一, 土屋彩子, 東城加奈, 矢崎正英, 森田洋, 吉田邦広, 星井嘉信, 池田修一
    • Journal Title

      末梢神経 19

      Pages: 54-63

    • NAID

      10025624948

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] 蛋白質ミスフォールディング病の発症機序と治療戦略2008

    • Author(s)
      関島良樹
    • Journal Title

      信州医学雑誌 56

      Pages: 115-124

    • NAID

      130004551700

    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] Non-senile wild-type transthyretin systemic amyloidosis presenting as bilateral carpal tunnel syndrome.2008

    • Author(s)
      Kodaira M, Sekijima Y, Tojo K, Tsuchiya A, Yazaki M, Ikeda S, Hoshii Y, Tachibana S.
    • Journal Title

      J Peripher Nerv Syst 13

      Pages: 148-150

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Journal Article] トランスサイレンチンアミロイドーシスの発症メカニズムと治療戦略2007

    • Author(s)
      関島良樹
    • Journal Title

      細胞工学 26

      Pages: 162-167

    • Data Source
      KAKENHI-PROJECT-18590932
  • [Journal Article] アミロイドーシス発症の分子機構解明を目指して-現状と展望、夢-2007

    • Author(s)
      後藤裕児、桑田一夫、関島良樹、田中元雅、内木宏廷、永井義隆、松崎勝己、樋口京一
    • Journal Title

      細胞工学 26

      Pages: 181-185

    • Data Source
      KAKENHI-PROJECT-18590932
  • [Journal Article] アミロイドーシス発症の分子機構解明を目指して-現状と展望,夢-2007

    • Author(s)
      後藤祐児, 桑田一夫, 関島良樹, 田中元雅, 内木宏延, 永井義隆, 松崎勝巳, 樋口京一
    • Journal Title

      細胞工学 26

      Pages: 181-185

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-18590932
  • [Journal Article] トランスサイレチンアミロイドーシスの発症メカニズムと治療戦略2007

    • Author(s)
      関島良樹
    • Journal Title

      細胞工学 26

      Pages: 162-167

    • Data Source
      KAKENHI-PROJECT-18590932
  • [Journal Article] トランスサイレチンアミロイドーシスの発症メカニズムと治療戦略.2007

    • Author(s)
      関島良樹
    • Journal Title

      細胞工学 26

      Pages: 162-167

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-18590932
  • [Journal Article] R104H may suppress transthyretin amyloidogenesis by thermodynamic stabilization, but not by the kinetic mechanism characterizing T119M trans-suppression.2006

    • Author(s)
      Sekijima Y, Dendle MT, Wiseman LR, White JT, Haeze W, Kelly JW.
    • Journal Title

      Amyloid 13・2

      Pages: 57-66

    • Data Source
      KAKENHI-PROJECT-18590932
  • [Journal Article] R104H may suppress transthyretin amyloidogenesis by thermodynamic stabilization, but not by the kinetic mechanism characterizing T119M trans-suppression2006

    • Author(s)
      Sekijima Y, Dendle MT, Wiseman LR, White JT, D'Haeze W, Kelly JW
    • Journal Title

      Amyloid 13

      Pages: 67-66

    • Description
      「研究成果報告書概要(和文)」より
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18590932
  • [Journal Article] Diflunisal stabilizes familial amyloid polyneuropathy-associated transthyretin variant tetramers in serum against dissociation required for amyloidogenesis2006

    • Author(s)
      Tojo K, Sekijima Y (correspondingauthor), Kelly JW, Ikeda S
    • Journal Title

      Neuroscience Research 56

      Pages: 441-449

    • NAID

      10019273683

    • Description
      「研究成果報告書概要(和文)」より
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18590932
  • [Journal Article] Diflunisal stabilizes familial amyloid polyneuropathy-associated transthyretin variant tetramers in serum against dissociation required for amyloidogenesis.2006

    • Author(s)
      Tojo K, Sekijima Y, Kelly JW, Ikeda S.
    • Journal Title

      Neuroscience Research 56・4

      Pages: 441-449

    • NAID

      10019273683

    • Data Source
      KAKENHI-PROJECT-18590932
  • [Journal Article] Orally administered diflunisal stabilizes transthyretin against dissociation required for amyloidogenesis2006

    • Author(s)
      Sekijima Y, Dendle MT, Kelly JW
    • Journal Title

      Amyloid 13

      Pages: 236-249

    • Description
      「研究成果報告書概要(和文)」より
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18590932
  • [Journal Article] Orally administered diflunisal stabilizes transthyretin against dissociation required for amyloidogenesis.2006

    • Author(s)
      Sekijima Y, Dendle MT, Kelly JW.
    • Journal Title

      Amyloid 13・4

      Pages: 236-249

    • Data Source
      KAKENHI-PROJECT-18590932
  • [Presentation] Progression and distribution pattern of cerebral amyloid angiopathy in hereditary ATTR amyloidosis patients visualized by 11C-PiB-PET imaging2022

    • Author(s)
      Takahashi Y, Oguchi K, Mochizuki Y, Takasone K, Ezawa N, Matsushima A, Katoh N, Yazaki M, Sekijima Y
    • Organizer
      XVⅢInternational Symposium On Amyloidosis
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] Siblings with a novel type of amyloid neuropathy,hereditary Aβ2M amyloid neuropathy:Report of the second family in the world2022

    • Author(s)
      Katoh N,Yoshinaga T, Yazaki M, Kusaba T, Yamano T, Miyagawa-Hayashino A, Sekijima Y
    • Organizer
      XVⅢ International Symposium On Amyloidosis
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] RNAi薬のATTRvアミロイドーシスへの治療効果判定に対するNfLの有用性2022

    • Author(s)
      関島良樹
    • Organizer
      第40回日本神経治療学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] Reduction of cardiac AL amyloid deposition after complete response visualized by PiB-PET imaging2022

    • Author(s)
      Katoh N, Oguchi K, Mochizuki Y, Takahashi Y,Ueno A, Takasone K, Sekijima Y
    • Organizer
      XVⅢ International Symposium On Amyloidosis
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] 早期治療介入を見据えた病態理解と診断のポイント2022

    • Author(s)
      関島良樹
    • Organizer
      第63回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] ATTR型脳アミロイドアンギオパチーの臨床的特徴およびアミロイド沈着の分布と進展2022

    • Author(s)
      高橋佑介、小口和浩、望月祐介、高曽根健、江澤直樹、松嶋聡、加藤修明、矢崎正英、関島良樹
    • Organizer
      第41回日本認知症学会学術集会/ 第37回日本老年精神医学会 合同開催
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] これからのATTRvアミロイドーシス診療を考える2022

    • Author(s)
      関島良樹
    • Organizer
      第9回日本アミロイドーシス学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] ATTRアミロイドーシスの最新の治療戦略2022

    • Author(s)
      関島良樹
    • Organizer
      第63回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] ATTRアミロイドーシスの病理・病態に迫る  ―QOL・生命予後改善を目指して―2022

    • Author(s)
      関島良樹
    • Organizer
      第63回日本神経病理学会総会学術研究会
    • Invited
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] アルツハイマー病以外の疾患に対するPiB-PETの有用性2022

    • Author(s)
      関島良樹
    • Organizer
      第14回関東脳核医学研究会 - KBNM -
    • Invited
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] HELIOS-A:Study of Vutrisiran in Patients with Hereditary transthyretin-madiated(hATTR) Amyloidosis2022

    • Author(s)
      Sekijima Y,D Adams,Il Tournev,Ms Taylor,T Coelho,V Plante-bordeneuve,Jl Berk,A Gonzalez-duarte,Jd Gillmore,Sc Low,L Obici,C Chen,P Badri,S Arum,J Vest,M Polydefkis
    • Organizer
      第63回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] 遺伝性ATTRアミロイドーシス治療の最前線2022

    • Author(s)
      関島良樹
    • Organizer
      第40回日本神経治療学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-22K07393
  • [Presentation] Recent Progress in the Diagnosis and Treatment of ATTR Amyloidosis2021

    • Author(s)
      関島良樹
    • Organizer
      WCC2021-World Congress of Cardiology 2021
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 肝移植後長期生存例に多発する脳アミロイドアンギオパチー2021

    • Author(s)
      関島 良樹
    • Organizer
      第8回日本アミロイドーシス学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 進化を遂げる遺伝性ATTRアミロイドーシス治療2021

    • Author(s)
      関島 良樹
    • Organizer
      日本人類遺伝学会66回大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 神経内科医が知っておくべきトランスサイレチン型アミロイドーシスの診断と治療 最前線2021

    • Author(s)
      関島 良樹
    • Organizer
      第62回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] ATTRvアミロイドーシスの治療ゴールを見据えた早期診断の重要性とsiRNA治療薬への期待2021

    • Author(s)
      関島 良樹
    • Organizer
      第31回日本心臓核医学会総会・学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] Recent progress in the Diagnosis and Treatment of ATTR Amyloidosis2021

    • Author(s)
      Sekijima Y
    • Organizer
      第85回日本循環器学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] ATTRアミロイド-シスの病態解明と治療の最先端2021

    • Author(s)
      関島 良樹
    • Organizer
      第62回日本神経病理学会総会学術研究会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 高齢者の手根管症候群に潜むATTRアミロイドーシスの早期診断2021

    • Author(s)
      関島 良樹
    • Organizer
      第62回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 家族性アミロイドーシスに対するパティシランの臨床2021

    • Author(s)
      関島 良樹
    • Organizer
      第62回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] ATTRアミロイドーシス治療の最前線2021

    • Author(s)
      関島 良樹
    • Organizer
      第39回日本神経治療学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] Central neurological manifestations2021

    • Author(s)
      Sekijima Y
    • Organizer
      3rd European ATTR Amyloidosis meeting for Patients and Doctors
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 日常診療に潜むATTRvアミロイドーシス2021

    • Author(s)
      関島 良樹
    • Organizer
      第39回日本神経治療学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 核酸医薬を用いたトランスサイレチン型アミロイドーシス治療2020

    • Author(s)
      関島良樹
    • Organizer
      73回日本自律神経学会総会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 全内科横断的疾患”アミロイドーシス”の診断と治療の最前線-全身性アミロイド-シスからアルツハイマー病まで-2020

    • Author(s)
      関島良樹
    • Organizer
      日本内科学会第144回信越地方会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] FAP患者における体幹部長さ依存性Aδ線維機能障害と四肢末梢神経障害との関連2020

    • Author(s)
      小平農、大橋信彦、森田洋、関島良樹
    • Organizer
      第60回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 電気生理学的脱髄所見を呈するATTR-FAPとDADS型CIDPの差2020

    • Author(s)
      大橋信彦、小平農、森田洋、関島良樹
    • Organizer
      第30回日本末梢神経学会学術集会
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] ATTR型脳軟膜アミロイドーシス/脳アミロイドアンギオパチーの臨床的特徴2020

    • Author(s)
      中尾聡、宮﨑大吾、吉長恒明、矢﨑正英、関島良樹
    • Organizer
      第7回日本アミロイドーシス学会学術集会
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] アミロイドーシスの診断と治療 update ―ガイドラインとその先の展望―2020

    • Author(s)
      関島良樹
    • Organizer
      第37回日本神経治療学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 進歩を遂げた遺伝性ATTRアミロイドーシス/FAP治療-siRNA 製剤の可能性-2020

    • Author(s)
      関島良樹
    • Organizer
      第37回日本神経治療学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 本邦の単一アミロイドーシス診断センターにおける連続729例のアミロイドーシス診断実績2020

    • Author(s)
      阿部隆太、吉長恒明、加藤修明、矢﨑正英、亀谷富由樹、関島良樹
    • Organizer
      第7回日本アミロイドーシス学会学術集会
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 核酸医薬を用いたトランスサイレチン型アミロイドーシス治療2020

    • Author(s)
      関島良樹
    • Organizer
      第39回日本認知症学会学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 遺伝性ATTRアミロイドーシス患者の心筋・末梢神経における沈着アミロイド蛋白の臓器内多様性の検討2020

    • Author(s)
      中川真優子、矢﨑正英、吉長恒明、関島良樹、亀谷富由樹
    • Organizer
      第7回日本アミロイドーシス学会学術集会
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 99mTc-PypとC-PiB PETを用いた非侵襲的な心アミロイドーシス診断法の確立2020

    • Author(s)
      高曽根健、高橋佑介、阿部隆太、小口和浩、吉長恒明、加藤修明、矢﨑正英、関島良樹
    • Organizer
      第7回日本アミロイドーシス学会学術集会
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 電気生理学的に脱髄所見を呈するATTR-FAPとDADS型CIDPの差異2020

    • Author(s)
      大橋信彦、小平農、森田洋、関島良樹
    • Organizer
      第60回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 伝性神経疾患の発症前診断と遺伝カウンセリング ~家族性アミロイドポリニューロパチーを中心に~2020

    • Author(s)
      関島良樹
    • Organizer
      第44回日本遺伝カウンセリング学会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] V30M型ATTRアミロイドーシス患者での脳アミロイドーシスのPiB-PETを用いた経時的変化の検討2020

    • Author(s)
      高橋佑介、高曽根健、阿部隆太、吉長恒明、加藤 修明、小口和浩、矢﨑正英、関島良樹
    • Organizer
      第7回日本アミロイドーシス学会学術集会
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 遺伝性ATTRアミロイドーシス,New Stage ~病態形成から考えるsiRNAによる治療意義~2020

    • Author(s)
      関島良樹
    • Organizer
      第38回日本神経治療学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] siRNAによる遺伝性ATTRアミロドーシスの最新治療と非集積地での診断2020

    • Author(s)
      関島良樹
    • Organizer
      第61回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 全身性アミロイドーシスの最近の話題 -野生型ATTRアミロイドーシスを中心に-2020

    • Author(s)
      関島良樹
    • Organizer
      第7回日本アミロイドーシス学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 遺伝性神経疾患の発症前診断と遺伝カウンセリング2020

    • Author(s)
      関島良樹
    • Organizer
      第60回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 全身性アミロイドーシス治療の最近の進歩 -蛋白質天然構造の安定化から核酸医薬まで-2020

    • Author(s)
      関島良樹
    • Organizer
      第5回JCVA学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] アミロイドーシスタイピング依頼例における陰性例の要因検討2020

    • Author(s)
      吉長恒明、高曽根健、高橋佑介、阿部隆太、中川真優子、加藤修明、矢﨑正英、関島良樹
    • Organizer
      第7回日本アミロイドーシス学会学術集会
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 遺伝性神経疾患の発症前診断と遺伝カウンセリング ~家族性アミロイドポリニューロパチーを中心に~2020

    • Author(s)
      関島良樹
    • Organizer
      第43回日本遺伝カウンセリング学会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] Utility of LMD and LC-MS/MS for immunostaining negative cases in diagnosis of amyloidosis2020

    • Author(s)
      Yoshinaga T, Yazaki M, Abe R, Takasone K, Takahashi Y, Katoh N, Kametani F, Sekijima Y
    • Organizer
      第60回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 不治の病から治療可能な疾患に ―アミロイドーシス治療の最前線―2020

    • Author(s)
      関島良樹
    • Organizer
      第72回日本自律神経学会総会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 遺伝性ATTRアミロイドーシス(FAP)を見逃すな -手根管症候群は重要なサイン-2020

    • Author(s)
      関島良樹
    • Organizer
      第31回日本末梢神経学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] Red flags for Early Diagnosis in Hereditary ATTR Amyloidosis.2020

    • Author(s)
      Sekijima Y
    • Organizer
      XVII International Symposium on Amyloidosis
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] Amyloid Interactome2020

    • Author(s)
      亀谷富由樹、吉長恒明、矢﨑正英、関島良樹
    • Organizer
      第7回日本アミロイドーシス学会学術集会
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 遺伝性ATTR(ATTRv)アミロイドーシス治療の現状と課題2020

    • Author(s)
      関島良樹
    • Organizer
      第60回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] 核酸医薬によるATTRアミロイドーシス治療の最前線 -実臨床における有用性と今後の展望-2020

    • Author(s)
      関島良樹
    • Organizer
      核酸医薬シンポジウム2020
    • Invited
    • Data Source
      KAKENHI-PROJECT-19K07959
  • [Presentation] Japanese consensus of treatments for hereditary ATTR amyloidosis2018

    • Author(s)
      Sekijima Y, Ueda M, Koike H, Misawa S, Ando Y
    • Organizer
      The XVIth International Symposium on Amyloidosis
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] First nationwide survey on systemic wild-type ATTR amyloidosis in Japan2018

    • Author(s)
      Sekijima Y, Yazaki M, Ueda M, Koike H, Yamada M, Ando Y
    • Organizer
      The XVIth International Symposium on Amyloidosis
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Tools to define the earliest diagnosis2018

    • Author(s)
      Sekijima Y
    • Organizer
      The XVIth International Symposium on Amyloidosis
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Treatment for ATTR Amyloidosis2017

    • Author(s)
      Sekijima Y
    • Organizer
      Samsung amyloidosis symposium 2017
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Transthyretin (ATTR)-type cerebral amyloid angiopathy2017

    • Author(s)
      Sekijima Y
    • Organizer
      第36回日本認知症学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 遺伝性ATTRアミロイドーシスの病態に基づいた疾患修飾療法の開発2017

    • Author(s)
      関島良樹
    • Organizer
      第35回日本神経治療学会総会
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Current topics in Amyloidosis -from Alzheimer disease to ATTR amyloidosis-2017

    • Author(s)
      Sekijima Y
    • Organizer
      XXIII World Congress of Neurology
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] アミロイドーシス全国疫学調査における本邦の野生型ATTRアミロイドーシス診療の実態2017

    • Author(s)
      関島良樹,矢崎正英,植田光晴,小池春樹,山田正仁,安東由喜雄
    • Organizer
      第5回日本アミロイドーシス研究会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 野生型ATTRアミロイドーシスの早期診断2017

    • Author(s)
      関島良樹
    • Organizer
      第5回日本アミロイドーシス研究会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Prevalence of Transthyretin-type cerebral amyloid angiopathy in ATTR-FAP patients and its early diagnosis using PiB-PET Imaging2017

    • Author(s)
      Sekijima Y
    • Organizer
      2017 Peripheral Nerve Society Annual Meeting
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Laser microdissectionを用いたアミロイドーシス沈着病態解析への応用2016

    • Author(s)
      矢崎正英、吉長恒明、関島良樹、池田修一、亀谷富由樹
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸国際会議場(神戸)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Transthyretin-type cerebral amyloid angiopathy in posttransplant patients with hereditary ATTR amyloidosis: Correlates between clinical findings and PIB-PET imaging2016

    • Author(s)
      Yoshiki Sekijima
    • Organizer
      The XV International Symposium on Amyloidosis
    • Place of Presentation
      Uppsala Concert and Congress(Uppsala, Sweden)
    • Year and Date
      2016-07-03
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Diagnosis of Hereditary ATTR Amyloidosis using 11C-PIB-PET2016

    • Author(s)
      Naoki Ezawa, Yoshiki Sekijima, Masahide Yazaki, Kazuhiro Oguchi, Shu-ichi Ikeda
    • Organizer
      The XV International Symposium on Amyloidosis
    • Place of Presentation
      Uppsala Concert and Congress (Uppsala, Sweden)
    • Year and Date
      2016-07-03
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] The first pathological and biochemical identification of seed-lesions of transmitted transthyretin amyloidosis after domino liver transplantation2016

    • Author(s)
      Tsuneaki Yoshinaga, Masahide Yazaki, Yoshiki Sekijima, Fuyuki Kametani, Naomi Hachiya, Keiichi Higuchi, Shu-ichi Ikeda
    • Organizer
      The XV International Symposium on Amyloidosis
    • Place of Presentation
      Uppsala Concert and Congress (UKK) in Uppsala, Sweden
    • Year and Date
      2016-07-03
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 13歳で発症した遺伝性ATTRアミロイドーシスの一例2016

    • Author(s)
      小林優也、小川有香、近藤恭史、宮崎大吾、関島良樹、池田修一
    • Organizer
      第4回日本アミロイドーシス研究会 学術集会
    • Place of Presentation
      KKRホテル東京(東京)
    • Year and Date
      2016-08-19
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 家族性アミロイドーシスの治療最前線2016

    • Author(s)
      関島良樹
    • Organizer
      第59回日本腎臓学会学術総会
    • Place of Presentation
      パシフィコ横浜(横浜)
    • Year and Date
      2016-06-17
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Val30Met TTR型FAP患者に対するTTR四量体安定化薬の長期的効果2016

    • Author(s)
      大橋信彦、小平農、関島良樹、森田洋、池田修一
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸国際会議場(神戸)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 病態に基づいたアミロイドーシスに対する疾患修飾療法2016

    • Author(s)
      関島良樹
    • Organizer
      第9回日本自律神経学会総会
    • Place of Presentation
      くまもと県民交流館パレア(熊本)
    • Year and Date
      2016-11-10
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Clinicopathological characterizations of transmitted transthyretin amyloidosis after domino liver transplantation: a single-center experience2016

    • Author(s)
      Tsuneaki Yoshinaga, Masahide Yazaki, Yoshiki Sekijima, Toshihiko Ikegami, Shinichi Miyagawa, Shu-ichi Ikeda
    • Organizer
      The XV International Symposium on Amyloidosis
    • Place of Presentation
      Uppsala Concert and Congress (Uppsala, Sweden)
    • Year and Date
      2016-07-03
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Transthyretin-type Cerebral Amyloid Angiopathy in Post-transplant Patients with Hereditary ATTR Amyloidosis: Correlates between Clinical Findings and Amyloid-PET Imaging2016

    • Author(s)
      Yoshiki Sekijima, Masahide Yazaki, Kazuhiro Oguchi, Tsuneaki Yoshinaga, Shu-Ichi Ikeda
    • Organizer
      第13回国際人類遺伝学会
    • Place of Presentation
      国立京都国際会館 (京都)
    • Year and Date
      2016-04-03
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] ドミノ移植後アミロイドーシスの臨床病理学的検討 一施設検討2016

    • Author(s)
      吉長恒明、矢崎正英、関島良樹、亀谷富由樹、池田修一
    • Organizer
      第4回日本アミロイドーシス研究会 学術集会
    • Place of Presentation
      KKRホテル東京(東京)
    • Year and Date
      2016-08-19
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] TTRアミロイド線維沈着部位のプロテオミクス解析2016

    • Author(s)
      亀谷富由樹、吉長恒明、鈴木彩子、関島良樹、矢崎正英、池田修一
    • Organizer
      第4回日本アミロイドーシス研究会 学術集会
    • Place of Presentation
      KKRホテル東京(東京)
    • Year and Date
      2016-08-19
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 遺伝性ATTRアミロイドーシスにおける11C-PIB-PETの有効性2016

    • Author(s)
      江澤直樹、関島良樹、矢崎正英、小口和浩、池田修一
    • Organizer
      第4回日本アミロイドーシス研究会 学術集会
    • Place of Presentation
      KKRホテル東京(東京)
    • Year and Date
      2016-08-19
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 11C-PIB-PETを用いた遺伝性ATTRアミロイドーシス診断の試み2016

    • Author(s)
      江澤直樹、関島良樹、矢崎正英、小口和浩、池田修一
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸国際会議場(神戸)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 肝移植後FAP患者の眼内アミロイド蛋白の laser microdissection (LMD)を用いた詳細な生化学的検討2016

    • Author(s)
      矢崎正英、吉長恒明、関島良樹、池田修一、宮原照良、亀谷富由樹
    • Organizer
      第4回日本アミロイドーシス研究会 学術集会
    • Place of Presentation
      KKRホテル東京(東京)
    • Year and Date
      2016-08-19
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Cerebral Amyloid Angiopathy in Post-transplant Patients with Hereditary ATTR Amyloidosis2016

    • Author(s)
      Yoshiki Sekijima, Masahide Yazaki, Kazuhiro Oguchi, Tsuneaki Yoshinaga, Shu-ichi Ikeda
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸国際会議場(神戸)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] アミロイドーシスを疑う、診断する2016

    • Author(s)
      関島良樹
    • Organizer
      第4回日本アミロイドーシス研究会 学術集会
    • Place of Presentation
      KKRホテル東京(東京)
    • Year and Date
      2016-08-19
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Recent progress in the treatment of hereditary ATTR amyloidosis-beginning of a new era of hereditary neurodegenerative disease therapy and genetic counseling-2016

    • Author(s)
      Yoshiki Sekijima
    • Organizer
      第13回国際人類遺伝学会
    • Place of Presentation
      国立京都国際会館 (京都)
    • Year and Date
      2016-04-03
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Cutting-edge therapies for amyloid neuropathy2016

    • Author(s)
      Yoshiki Sekijima
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸国際会議場 (神戸)
    • Year and Date
      2016-05-18
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Extremely Early Onset Hereditary ATTR Amyloidosis with p.G67R (G47R) Mutation2016

    • Author(s)
      Yuya Kobayashi, Yoshiki Sekijima, Yuka Ogawa, Yasuhumi Kondo, Daigo Miyazaki, Shu-ichi Ikeda,
    • Organizer
      The XV International Symposium on Amyloidosis
    • Place of Presentation
      Uppsala Concert and Congress (Uppsala, Sweden)
    • Year and Date
      2016-07-03
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] de novo amyloidosis(医原性FAP)における生化学的解析とその臨床像2016

    • Author(s)
      吉長恒明、矢崎正英、関島良樹、亀谷富由樹、池田修一
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸国際会議場 (神戸)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 遺伝性ATTRアミロイドーシス長期生存例における脳アミロイドアンギオパチーの出現とその11C-PIB-PET所見の解析2016

    • Author(s)
      関島良樹、矢崎正英、小口和浩、江澤直樹、吉長恒明、池田修一
    • Organizer
      第4回日本アミロイドーシス研究会 学術集会
    • Place of Presentation
      KKRホテル東京(東京)
    • Year and Date
      2016-08-19
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Carpal Tunnel Syndrome: The Most Common Initial Symptom of Systemic Wild-type ATTR (ATTRwt) Amyloidosis2016

    • Author(s)
      Yoshiki Sekijima, Michitaka Nakagawa, Kana Tojo, Tsuneaki Yoshinaga, Masahide Yazaki, Jun koyama, Shu-ichi Ikeda
    • Organizer
      The XV International Symposium on Amyloidosis
    • Place of Presentation
      Uppsala Concert and Congress (UKK) in Uppsala, Sweden
    • Year and Date
      2016-07-03
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 肝移植後遺伝性ATTRアミロイドーシス患者における脳アミロイドアンギオパチー2015

    • Author(s)
      関島良樹、矢崎正英、小口和浩、吉長恒明、東城加奈、池田修一
    • Organizer
      第3回日本アミロイドーシス研究会学術集会
    • Place of Presentation
      KKRホテル東京(東京都)
    • Year and Date
      2015-08-21
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Mechanistic linkage between ATTR therapies and clinical benefit: Results from a quantitative ELISA assay demonstrates a dramatic reduction in non-native TTR levels in FAP patients treated with tafamidis2015

    • Author(s)
      Justin Chapman, Teresa Coelho, Yoshiki Sekijima, Jeffery W. Kelly, Xin Jiang
    • Organizer
      140th Annual Meeting of the American Neurological Association
    • Place of Presentation
      Chicago Marriott Downtown Magnificent Mile(Chicago,USA)
    • Year and Date
      2015-09-27
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 家族性アミロイドポリニューロパチーの病態に基づいた疾患修飾療法の開発2015

    • Author(s)
      関島良樹
    • Organizer
      日本人類遺伝学会第60回大会
    • Place of Presentation
      京王プラザホテル(東京都)
    • Year and Date
      2015-10-14
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 各種アミロイドタンパク質沈着組織のレーザーマイクロ ダイセクションおよび質量分析を用いたプロテオミクス解析2015

    • Author(s)
      亀谷富由樹、吉長恒明、鈴木彩子、関島良樹、矢崎正英、池田修一
    • Organizer
      第3回日本アミロイドーシス研究会 学術集会
    • Place of Presentation
      KKRホテル(東京)
    • Year and Date
      2015-08-21
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] トランスサイレチン・アミロイドーシスの診断と治療2015

    • Author(s)
      関島良樹
    • Organizer
      第63回日本心臓病学会学術集会
    • Place of Presentation
      パシフィコ横浜(神奈川県横浜市)
    • Year and Date
      2015-09-18
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] アミロイドーシスの最新トピックス -アルツハイマー病からATTRアミロイドーシスまで-2015

    • Author(s)
      関島良樹
    • Organizer
      第48回日本神経病理学会北海道地方会
    • Place of Presentation
      北海道大学医学部(北海道札幌市)
    • Year and Date
      2015-10-31
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 家族性アミロイドポリニューロパチーの診断と治療選択 ―肝移植と薬剤の使い分け―2015

    • Author(s)
      関島良樹
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ (新潟県新潟市)
    • Year and Date
      2015-05-20
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] アミロイドニューロパチー診断のポイント~臨床所見と検査の実際~2015

    • Author(s)
      関島良樹
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ (新潟県新潟市)
    • Year and Date
      2015-05-20
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 家族性アミロイドポリニューロパチーの新規薬物治療2015

    • Author(s)
      関島良樹
    • Organizer
      第68回日本自律神経学会総会
    • Place of Presentation
      ウインクあいち(愛知県名古屋市)
    • Year and Date
      2015-10-29
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] ドミノ肝移植レシピエントにおけるde novo amyloidosis(医原性FAP)の検討2015

    • Author(s)
      矢崎正英,吉長恒明,関島良樹,池田修一,三田篤義,池上俊彦,宮川眞一
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ (新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 自験例ドミノ肝移植レシピエントにおける医原性アミロイドーシスの臨床病理学的検討2015

    • Author(s)
      吉長恒明、矢﨑正英、関島良樹、三田篤義、池上俊彦、宮川眞一、池田修一
    • Organizer
      第33回日本肝移植研究会
    • Place of Presentation
      ホテルオークラ神戸(兵庫県神戸市)
    • Year and Date
      2015-05-28
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Laser microdissection-LC-MS/MSを用いたプロテオーム解析によるアミロイドーシス病型診断の有効性と分子病態解析への応用2015

    • Author(s)
      矢崎正英、吉長恒明、関島良樹、亀谷富由樹、八谷如美、池田修一
    • Organizer
      第3回日本アミロイドーシス研究会学術集会
    • Place of Presentation
      KKRホテル東京(東京都)
    • Year and Date
      2015-08-21
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] トランスサイレチン型家族性ポリニューロパチーに対するタファミジスの第三相試験成績2015

    • Author(s)
      関島良樹、大林光念、森田洋、池田修一、山下太郎、植田光晴、三隅洋平、町井克行、大田誠、高田亜実、安東由喜雄
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ (新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Laser microdissection-LC-MS/MSを用いたプロテオーム解析による アミロイドーシス病型診断の有効性と分子病態解析への応用2015

    • Author(s)
      矢崎正英、吉長恒明、関島良樹、亀谷富由樹、八谷如美、池田修一
    • Organizer
      第3回日本アミロイドーシス研究会 学術集会
    • Place of Presentation
      KKRホテル(東京)
    • Year and Date
      2015-08-21
    • Invited
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] 肝移植後遺伝性ATTRアミロイドーシス患者における 脳アミロイドアンギオパチー2015

    • Author(s)
      関島良樹、矢崎正英、小口和浩、吉長恒明、東城加奈、池田修一
    • Organizer
      第3回日本アミロイドーシス研究会 学術集会
    • Place of Presentation
      KKRホテル(東京)
    • Year and Date
      2015-08-21
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] 交通外傷後に脳表ヘモジデリン沈着症と多髄節性筋萎縮症を発症した53歳男性例2015

    • Author(s)
      高橋佑介、木下朋実、岸田大、矢崎正英、関島良樹、池田修一
    • Organizer
      第215回日本神経学会関東・甲信越地方会
    • Place of Presentation
      砂防会館(東京)
    • Year and Date
      2015-12-05
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP)に対する肝移植54例の治療評価2015

    • Author(s)
      鈴木 彩子、矢﨑正英、武井洋一、関島良樹、池田修一
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] 疾患修飾療法が可能になった遺伝性ニューロパチー・心筋症の診断と治療2015

    • Author(s)
      関島良樹
    • Organizer
      第3回日本アミロイドーシス研究会学術集会
    • Place of Presentation
      KKRホテル東京(東京都)
    • Year and Date
      2015-08-21
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 心アミロイドーシスにおける虚血性脳血管障害の危険因子についての検討2015

    • Author(s)
      道傳 整、中川道隆、中村勝哉、安出卓司、東城加奈、関島良樹、池田修一
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ (新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 遺伝性 ATTR アミロイドーシスの治療の現状と今後の展望2015

    • Author(s)
      関島良樹
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 各種アミロイドタンパク質沈着組織のレーザーマイクロダイセクションおよび質量分析を用いたプロテオミクス解析2015

    • Author(s)
      亀谷富由樹、吉長恒明、鈴木彩子、関島良樹、矢崎正英、池田修一
    • Organizer
      第3回日本アミロイドーシス研究会学術集会
    • Place of Presentation
      KKRホテル東京(東京都)
    • Year and Date
      2015-08-21
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 家族性アミロイドポリニューロパチー (FAP) の診断と治療2015

    • Author(s)
      関島良樹
    • Organizer
      第26回日本末梢神経学会学術集会
    • Place of Presentation
      ホテルブエナビスタ(長野県松本市)
    • Year and Date
      2015-09-18
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 肝移植後22年後に脳アミロイドアンギオパチーで脳出血を起こした家族性アミロイドポリニューロパチーの1例2015

    • Author(s)
      大橋信彦、池田淳司、小平農、関島良樹、池田修一
    • Organizer
      第214回日本神経学会関東・甲信越地方会
    • Place of Presentation
      砂防会館(東京都)
    • Year and Date
      2015-09-05
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 本邦における遺伝性腎アミロイドーシスの分子病態2015

    • Author(s)
      矢﨑正英、吉長恒明、関島良樹、西尾妙織、山中修一郎、池田修一
    • Organizer
      第112回日本内科学会総会
    • Place of Presentation
      みやこめっせ(京都市)
    • Year and Date
      2015-04-10
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] アミロイドーシスと感染症 ―歴史に秘められた意外な関係―2015

    • Author(s)
      関島良樹
    • Organizer
      第20回日本神経感染症学会総会・学術大会
    • Place of Presentation
      ホテルメルパルク長野(長野県長野市)
    • Year and Date
      2015-10-22
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Laser microdissection(LMD)を用いて診断した 本邦初のFibrinogen型アミロイドーシスの一例2015

    • Author(s)
      吉長恒明、矢崎正英、関島良樹、亀谷富由樹、西尾妙織、蟹沢祐司、奥村伸生、池田修一
    • Organizer
      第3回日本アミロイドーシス研究会 学術集会
    • Place of Presentation
      KKRホテル(東京)
    • Year and Date
      2015-08-21
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] Val30Met TTR型FAP患者の末梢神経障害に対するジフルニサルの中期的効果2015

    • Author(s)
      大橋 信彦、関島良樹、小平農、森田洋、池田修一
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ (新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] Val30Met TTR型FAP患者の末梢神経障害に対するジフルニサルの中期的効果2015

    • Author(s)
      大橋信彦、関島良樹、小平農、森田洋、池田修一
    • Organizer
      第45回日本臨床神経生理学会学術大会
    • Place of Presentation
      大阪国際会議場(大阪府大阪市)
    • Year and Date
      2015-11-05
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP)に対する肝移植54例の治療評価2015

    • Author(s)
      鈴木 彩子、矢﨑正英、武井洋一、関島良樹、池田修一
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ (新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09336
  • [Presentation] 自験例ドミノ肝移植レシピエントにおける医原性アミロイドーシスの臨床病理学的検討2015

    • Author(s)
      吉長恒明、矢﨑正英、関島良樹、三田篤義、池上俊彦、宮川眞一、池田修一
    • Organizer
      第33回日本肝移植研究会
    • Place of Presentation
      ホテルオークラ神戸(神戸市)
    • Year and Date
      2015-05-28
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] 家族性アミロイドーシスの病態に基づいた新規治療法の開発と遺伝カウンセリング2014

    • Author(s)
      関島良樹
    • Organizer
      第100回千葉大学遺伝子診療部セミナー
    • Place of Presentation
      千葉
    • Year and Date
      2014-02-20
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 家族性アミロイドポリニューロパチーの基礎から治療へ2014

    • Author(s)
      関島良樹
    • Organizer
      東京都医学研セミナー
    • Place of Presentation
      (公財)東京都医学総合研究所(東京都世田谷区)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] ドミノ肝移植後1年でde novo TTR amyloid沈着を認めた66歳女性例2014

    • Author(s)
      吉長恒明、矢崎正英、関島良樹、菅原寧彦、田中智弘、池田修一
    • Organizer
      第2回日本アミロイドーシス研究会学術集会
    • Place of Presentation
      KKRホテル(東京)
    • Year and Date
      2014-08-22
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] 家族性アミロイドポリニューロパチーの基礎から治療へ2014

    • Author(s)
      関島良樹
    • Organizer
      東京都医学研セミナー
    • Place of Presentation
      東京
    • Year and Date
      2014-02-21
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] アミロイド心筋症を有する肝移植後FAP患者に対するジフルニサルの治療効果の検討2014

    • Author(s)
      関島良樹、吉長恒明、矢崎正英、小山潤、池田修一
    • Organizer
      第2回日本アミロイドーシス研究会学術集会
    • Place of Presentation
      KKRホテル(東京)
    • Year and Date
      2014-08-22
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] 家族性アミロイドーシスの病態に基づいた新規治療法の開発と遺伝カウンセリング2014

    • Author(s)
      関島良樹
    • Organizer
      第100回千葉大学遺伝子診療部セミナー
    • Place of Presentation
      千葉大学医学部附属病院(千葉県千葉市)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 神経疾患の治療に関する最近の話題と今後の展望2013

    • Author(s)
      関島良樹
    • Organizer
      第48回信越支部主催生涯教育講演会
    • Place of Presentation
      長野
    • Year and Date
      2013-06-09
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Steady amyloid turn-over after liver transplantation in FAP patients2013

    • Author(s)
      Yazaki M, Tsuchiya-Suzuki A, Sekijima Y, Kametani F, Ikeda S
    • Organizer
      IX^<th> International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Rio de Janeiro, Brazil
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Safety and efficacy of long-term diflunisal administration in late-onset ATTR Val30Met FAP2013

    • Author(s)
      Sekijima Y, Tojo K, Morita H, Koyama J, Koike H, Sobue G, Ikeda S
    • Organizer
      IX^<th> International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Rio de Janeiro, Brazil
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Steady amyloid turn-over after liver transplantation in FAP patients2013

    • Author(s)
      Yazaki M, Tsuchiya-Suzuki A, Sekijima Y, Kametani F, Ikeda S
    • Organizer
      IXth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Federal University of Rio deJaneiro(Rio de Janeiro,Brazil)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 心筋生検組織のアミロイド分析からみた心アミロイド―シスの基礎疾患の検討2013

    • Author(s)
      関島良樹,中川道隆,東城加奈,池田修一
    • Organizer
      第1回日本アミロイド―シス研究会学術大会
    • Place of Presentation
      KKRホテル東京(東京都千代田区)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 小胞体関連分解によるトランスサイレチンアミロイド―シスに対する自己防御機構と病態に基づいた新規治療法の開発2013

    • Author(s)
      関島良樹
    • Organizer
      第8回臨床ストレス応答学会
    • Place of Presentation
      キッセイ文化ホール(長野県松本市)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 小胞体関連分解によるトランスサイレチンアミロイド―シスに対する自己防御機構と病態に基づいた新規治療法の開発2013

    • Author(s)
      関島良樹
    • Organizer
      第8回臨床ストレス応答学会
    • Place of Presentation
      松本
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Steady amyloid turn-over after liver transplantation in FAP patients2013

    • Author(s)
      Yazaki M, Tsuchiya-Suzuki A, Sekijima Y, Kametani F, Ikeda S
    • Organizer
      IXth International symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Federal University of Rio deJaneiro(Rio de Janeiro, Brazil)
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] 心筋生検組織のアミロイド分析からみた心アミロイドーシスの基礎疾患の検討2013

    • Author(s)
      関島良樹,中川道隆,東城加奈,池田修一
    • Organizer
      第1回日本アミロイド―シス研究会学術大会
    • Place of Presentation
      東京
    • Year and Date
      2013-08-30
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 高齢発症ATTR Val30Met FAP患者の末梢神経機能に対するジフルニサルの有効性の検討2013

    • Author(s)
      関島良樹,東城加奈,森田洋,小池春樹,祖父江元,池田修一
    • Organizer
      第54回日本神経学会学術集会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 遺伝性・先天性疾患に対する横断的診療連携体制の構築・信州大学医学部附属病院遺伝子診療部の取り組み2013

    • Author(s)
      石河真澄、古庄知己、黄瀬恵美子、中村勝哉、山嵜雅則、玉井真理子、山下浩美、高津亜希子、菊池範彦、大平哲史、金井誠、丸山孝子、河村理恵、涌井敬子、関島良樹、櫻井晃洋、福嶋義光
    • Organizer
      第58回日本人類遺伝学会
    • Place of Presentation
      江陽グランドホテル(宮城県仙台市)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 高齢発症ATTR Val30Met FAP患者の末梢神経機能に対するジフルニサルの有効性の検討2013

    • Author(s)
      関島良樹,東城加奈,森田洋,小池春樹,祖父江元,池田修一
    • Organizer
      第54回日本神経学会学術集会
    • Place of Presentation
      東京国際フォーラム(東京都千代田区)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Safety and efficacy of long-term diflunisal administration in late-onset ATTR Val30Met FAP2013

    • Author(s)
      Sekijima Y, Tojo K, Morita H, Koyama J, Koike H, Sobue G, Ikeda S
    • Organizer
      IXth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Federal University of Rio deJaneiro(Rio de Janeiro,Brazil)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 神経疾患の治療に関する最近の話題と今後の展望2013

    • Author(s)
      関島良樹
    • Organizer
      第48回 信越支部主催生涯教育講演会
    • Place of Presentation
      長野市若里市民文化ホール(長野県長野市)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 手根菅症候群で発症したATTR Tyr114His型家族性アミロイドポリニューロパチーの1例2012

    • Author(s)
      永松清志郎,田澤浩一,関島良樹,池田修一
    • Organizer
      第130回日本内科学会信越地方会
    • Place of Presentation
      新潟
    • Year and Date
      2012-06-02
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] The Diflunisal Trial:Demographics,baseline neurologic sraging, and adverse events2012

    • Author(s)
      Berk JL, Obici L, Zeldenrust SR, Sekijima Y, Yamashita T, Heneghan M, Ikeda S, Ando Y,Gorevic P, Merlini G, Kelly JW, Skinner M Bisbee AB, Dyck PJ, Suhr OR, Familial Amyloidosis Consortium
    • Organizer
      XIIIthe International Symposium on Amyloidosis
    • Place of Presentation
      Groningen
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP)に対する新規治療法の開発と臨床応用2012

    • Author(s)
      関島良樹
    • Organizer
      第36回日本遺伝カウンセリング学会学術集会
    • Place of Presentation
      松本
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP) に対する新規治療法の開発と臨床応用2012

    • Author(s)
      関島良樹
    • Organizer
      第36回日本遺伝カウンセリング学会学術集会
    • Place of Presentation
      松本
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Neurological manifestations of senile systemic amyloidosis2012

    • Author(s)
      Ikeda S, Sekijima Y, Tojo K, Nakagawa M, Morita H, Koyama J
    • Organizer
      XIIIthe International Symposium on Amyloidosis
    • Place of Presentation
      Groningen
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 本邦における遺伝性神経筋疾患に対する発症前診断の現状と課題2012

    • Author(s)
      関島良樹,田中敬子,吉田邦広,福嶋義光
    • Organizer
      日本人類遺伝学会第57回大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 当院における遺伝性神経疾患の発症前診断の現状2012

    • Author(s)
      関島良樹,田中敬子,吉田邦広,水内麻子,山下浩美,玉井眞理子,福嶋義光,池田修一
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] The distribution of age at onset of ATTRVal30Met FAP in Japan2012

    • Author(s)
      Sekijima Y, Tojo K, Tsuchiya-Suzaki A, Yazaki M, Ikeda S
    • Organizer
      XIIIthe International Symposium on Amyloidosis
    • Place of Presentation
      Groningen
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 全国の医療機関における遺伝性神経筋疾患に対する発症前診断の現状2012

    • Author(s)
      田中敬子,関島良樹,吉田邦広,福嶋義光
    • Organizer
      第36回日本遺伝カウンセリング学会学術集会
    • Place of Presentation
      松本
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP)患者の発症年齢の推移に関する検討2012

    • Author(s)
      池田修一,関島良樹,東城加奈,鈴木彩子,矢崎正英
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] The Diflunisal Trial : Demographics,baseline neurologic sraging, and adverse events2012

    • Author(s)
      Berk JL, Obici L, Zeldenrust SR, Sekijima Y, Yamashita T, Heneghan M, Ikeda S, Ando Y,Gorevic P, Merlini G, Kelly JW, Skinner M, Bisbee AB, Dyck PJ, Suhr OR, Familial Amyloidosis Consortium
    • Organizer
      XIII^<th> International Symposium on Amyloidosis
    • Place of Presentation
      Groningen, Netherland
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Neurological manifestations of senile systemic amyloidosis2012

    • Author(s)
      Ikeda S, Sekijima Y, Tojo K, Nakagawa M, Morita, H, Koyama J
    • Organizer
      XIII^<th> International Symposium on Amyloidosis
    • Place of Presentation
      Groningen, Netherland
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 当院における遺伝性神経疾患の発症前診断の現状2012

    • Author(s)
      関島良樹,田中敬子,吉田邦広,水内麻子,山下浩美,玉井眞理子,福嶋義光,池田修一
    • Organizer
      第36回日本遺伝カウンセリング学会学術集会
    • Place of Presentation
      松本
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] The distribution of age at onset of ATTRVal30Met FAP in Japan2012

    • Author(s)
      Sekijima Y, Tojo K, Tsuchiya-Suzaki A, Yazaki M, Ikeda S
    • Organizer
      XIII^<th> International Symposium on Amyloidosis
    • Place of Presentation
      Groningen, Netherland
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Systemic embolism in senile systemic amyloidosis : report of 2 cases2011

    • Author(s)
      Nakagawa M, Tojo K, Sekijima Y, Ikeda S, Yamazaki K. . VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 老人性全身性アミロイドーシスの早期診断における両側手根管症候群の有用性2011

    • Author(s)
      江澤直樹、東城加奈、関島良樹、池田修一
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知県)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 特発性手根管症候群患者における野生型トランスサイレチンアミロイド沈着の頻度に関する研究2011

    • Author(s)
      関島良樹、内山茂晴、東城加奈、佐野健司、清水雄策、今枝敏彦、加藤博之、池田修一
    • Organizer
      日本末梢神経学会学術集会
    • Place of Presentation
      沖縄コンベンションセンター(沖縄県那覇)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 老人性全身性アミロイドーシスの早期診断における両側手根管症候群の有用性2011

    • Author(s)
      江澤直樹,東城加奈,関島良樹,池田修一
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Diflunisalを用いた家族性アミロイドポリニューロパチーに対する新規薬物療法の開発2011

    • Author(s)
      関島良樹、東城加奈、森田洋、鈴木彩子、矢崎正英、池田修一
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知県)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] High pevalence of wild-type TTR deposition in patients with idiopathic carpal tunnel syndrome: A common cause of carpal tunnel syndrome in the elderly2011

    • Author(s)
      Sekijima Y, Uchiyama S, Tojo K, Sano K, Shimizu Y, Imaeda T, Kato H, Ikeda S
    • Organizer
      The 63rd Annual Meeting of the American Academy of Neurology
    • Place of Presentation
      Hawaii Convention Center(Honolulu)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Safety and efficacy of long-term administration of diflunisal to familial amyloid polyneuropathy patients2011

    • Author(s)
      Sekijima Y, Tojo K, Morita H, Koyama J, Suzuki A, Yazaki M, Ikeda S
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy(招待講演)
    • Place of Presentation
      The Kumamoto City Medical Association Hall(Kumamoto)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] The range of onset in ATTRVal30Met FAP and theclinical picture of the patients with this disease who started after the age of 702011

    • Author(s)
      Ikeda S, Tojo K, Sekijima Y, Yazaki M
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      The Kumamoto City Medical Association Hall(Kumamoto)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] The range of onset in ATTRVal30Met FAP and theclinical picture of the patients with this disease who started after the age of 702011

    • Author(s)
      Ikeda S, Tojo K, Sekijima Y, Yazaki M
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] The contribution of wild-type TTR to deposited amyloid onto gastroduodenum of FAP patients:the effect of liver transplantation2011

    • Author(s)
      Tsuchiya-Suzuki A, Yazaki M, Sekijima Y, Takei Y, Ikeda S, Kametami F
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      The Kumamoto City Medical Association Hall(Kumamoto)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Diflunisalを用いた家族性アミロイドポリニューロパチーに対する新規薬物療法の開発2011

    • Author(s)
      関島良樹,東城加奈,森田洋,鈴木彩子,矢崎正英,池田修一
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] The Diflunisal Trial : Study accrual and drug tolerance2011

    • Author(s)
      Berk JL, Suhr OB, Sekijima Y, Yamashita T, Heneghan M, Zeldenrust SR, Ando Y, Ikeda S-I, Gorevic P, Merlini G, Kelly JW, Skinner M, Bisbee AB, Dyck PJ, Obici L, et al
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 70歳以後に診断されたFAP-ATTRVal30Met患者の臨床像の検討2011

    • Author(s)
      池田修一,東城加奈,関島良樹,鈴木彩子,矢崎正英
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 特発性手根管症候群患者における野生型トランスサイレチンアミロイド沈着の頻度に関する研究2011

    • Author(s)
      関島良樹,内山茂晴,東城加奈,佐野健司,清水雄策,今枝敏彦,加藤博之,池田修一
    • Organizer
      第22回日本末梢神経学会学術集会
    • Place of Presentation
      那覇
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] High prevalence of wild-type TTR amyloid deposition in patients with idiopathic carpal tunnel syndrome2011

    • Author(s)
      Sekijima Y, Uchiyama S, Tojo K, Sano K, ShimizuY, Imaeda T, Hoshii Y, Kato H, Ikeda S
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 非家族性アミロイドーシスの臨床と疫学2011

    • Author(s)
      関島良樹
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 肝移植後FAP患者における組織沈着アミロイドのturn-overについて2011

    • Author(s)
      鈴木彩子、矢崎正英、関島良樹、亀谷富由樹、池田修一
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知県)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] High pevalence of wild-type TTR deposition in patients with idiopathic carpal tunnel syndrome : A common cause of carpal tunnel syndrome in the elderly2011

    • Author(s)
      Sekijima Y, Uchiyama S, Tojo K, Sano K, ShimizuY, Imaeda T, Kato H, Ikeda S
    • Organizer
      The 63rd Annual Meeting of the American Academy of Neurology
    • Place of Presentation
      Honolulu
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 非家族性アミロイドーシスの臨床と疫学2011

    • Author(s)
      関島良樹
    • Organizer
      第52回日本神経学会学術大会(招待講演)
    • Place of Presentation
      名古屋国際会議場(愛知県)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] The contribution of wild-type TTR to deposited amyloid onto gastroduodenum of FAP patients : the effect of liver transplantation2011

    • Author(s)
      Tsuchiya-Suzuki A, Yazaki M, Sekijima Y, Takei Y, Ikeda S, Kametami F
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] A follow-up study of 48 FAP patients who underwent liver transplantation2011

    • Author(s)
      Tsuchiya-Suzuki A, Yazaki M, Sekijima Y, Takei Y, Ikegami T, Miyagawa S, Matsunami H, Ikeda S
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Systemic embolism in senile systemic amyloidosis:report of 2 cases2011

    • Author(s)
      Nakagawa M, Tojo K, Sekijima Y, Ikeda S, Yamazaki K
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      The Kumamoto City Medical Association Hall(Kumamoto)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 70歳以後に診断されたFAP-ATTRVal30Met患者の臨床像の検討2011

    • Author(s)
      池田修一、東城加奈、関島良樹、鈴木彩子、矢崎正英
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知県)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] A follow-up study of 48 FAP patients who underwent liver transplantation2011

    • Author(s)
      Tsuchiya-Suzuki A, Yazaki M, Sekijima Y, Takei Y, Ikegami T, Miyagawa S, Matsunami H, Ikeda S
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      The Kumamoto City Medical Association Hall(Kumamoto)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] 肝移植後FAP患者における組織沈着アミロイドのturn-overについて2011

    • Author(s)
      鈴木彩子,矢崎正英,関島良樹,亀谷富由樹,池田修一
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] High prevalence of wild-type TTR amyloid deposition in patients with idiopathic carpal tunnel syndrome2011

    • Author(s)
      Sekijima Y, Uchiyama S, Tojo K, Sano K, Shimizu Y, Imaeda T, Hoshii Y, Kato H, Ikeda S
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      The Kumamoto City Medical Association Hall(Kumamoto)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] The Diflunisal Trial: Study accrual and drug tolerance2011

    • Author(s)
      Berk JL, Suhr OB, Sekijima Y, Yamashita T, Heneghan M, Zeldenrust SR, Ando Y, Ikeda S-I, Gorevic P, Merlini G, Kelly JW, Skinner M, Bisbee AB, Dyck PJ, Obici L, et al
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy(招待講演)
    • Place of Presentation
      The Kumamoto City Medical Association Hall(Kumamoto)
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Safety and efficacy of long-term administration of diflunisal to familial amyloid polyneuropathy patients2011

    • Author(s)
      Sekijima Y, Tojo K, Morita H, Koyama J, SuzukiA, Yazaki M, Ikeda S
    • Organizer
      VIII^<th> International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591237
  • [Presentation] Prevalence of Senile Systemic Amyloidosis in Patients with Idiopathic Carpal Tunnel Syndrome2010

    • Author(s)
      Sekijima Y, Uchiyama S, Tojo K, Sano K, Shimizu Y, Imaeda T, Hoshii Y, Kato H, Ikeda SI
    • Organizer
      The XII International Symposium on Amyloidosis
    • Place of Presentation
      ローマ
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Efficacy and safety of long-term administration of diflunisal to familial amyloid polyneuropathy patients2010

    • Author(s)
      Tojo K, Sekijima Y, Morita H, Koyama J, Suzuki A, Yazaki M, Ikeda SI
    • Organizer
      The XII International Symposium on Amyloidosis
    • Place of Presentation
      ローマ
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP)の病因と治療戦略2010

    • Author(s)
      関島良樹
    • Organizer
      第28回口本神経治療学会総会(招待講演)
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Efficacy and safety of long-term administration of diflunisal to familial amyloid polyneuropathy patients.2010

    • Author(s)
      Tojo K, Sekijima Y, Morita H, Koyama J, Suzuki A, Yazaki M, Ikeda SI.
    • Organizer
      The XII International Symposium on Amyloidosis
    • Place of Presentation
      Rome
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Familial amyloid polyneuropathy : Diflunisal2010

    • Author(s)
      関島良樹
    • Organizer
      第51回日本神経学会総会(国際シンポジウム)
    • Place of Presentation
      東京 招待講演
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Familial amyloid polyneuropathy : Diflunisal.2010

    • Author(s)
      関島良樹
    • Organizer
      第51回日本神経学会総会(国際シンポジウム)(招待講演)
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 蛋白質天然構造の安定化を介したアミロイドーシス治療の試み2010

    • Author(s)
      関島良樹
    • Organizer
      J-CAN(Japanese Consortium for Age-related Neurodegenerative disorders)
    • Place of Presentation
      東京 招待講演
    • Year and Date
      2010-08-28
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP)の病因と治療戦略2010

    • Author(s)
      関島良樹
    • Organizer
      第28回日本神経治療学会総会
    • Place of Presentation
      横浜 招待講演
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Pathogenesis of and therapeutic strategies to ameliorate the transthyretin amyloidoses2010

    • Author(s)
      Sekijima Y(招待講演)
    • Organizer
      International Symposium on Amyloidogenesis and Anti-Amyloid Therapies
    • Place of Presentation
      Tokyo
    • Year and Date
      2010-01-28
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 蛋白質天然構造の安定化を介したアミロイドーシス治療の試み2010

    • Author(s)
      関島良樹
    • Organizer
      J-CAN(Japanese Consortium for Age-related Neurodegenerative disorders)(招待講演)
    • Place of Presentation
      東京
    • Year and Date
      2010-08-28
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 特発性手根管症候群患者における老人性全身性アミロイドーシスの有病率2010

    • Author(s)
      関島良樹, 内山茂晴, 東城加奈, 佐野健司, 清水雄策, 加藤博之, 池田修一
    • Organizer
      第51回日本神経学会総会(招待講演)
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Prevalence of Senile Systemic Amyloidosis in Patients with Idiopathic Carpal Tunnel Syndrome.2010

    • Author(s)
      Sekijima Y, Uchiyama S, Tojo K, Sano K, Shimizu Y, Imaeda T, Hoshii Y, Kato H, Ikeda SI
    • Organizer
      The XII International Symposium on Amyloidosis
    • Place of Presentation
      Rome
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] FAPを中心とした遺伝性ニューロパチー2010

    • Author(s)
      関島良樹
    • Organizer
      日本人類遺伝学会第55回大会(招待講演)
    • Place of Presentation
      大宮
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 特発性手根管症候群と屈筋腱滑膜へのアミロイド沈着の有意な関連2010

    • Author(s)
      内山茂晴, 関島良樹, 佐野健司, 今枝敏彦, 加藤博之, 池田修一
    • Organizer
      第53回日本手外科学会
    • Place of Presentation
      新潟
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 特発性手根管症候群患者における老人性全身性アミロイドーシスの有病率2010

    • Author(s)
      関島良樹, 内山茂晴, 東城加奈, 佐野健司, 清水雄策, 加藤博之, 池田修一
    • Organizer
      第51回日本神経学会総会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Pathogenesis of and therapeutic strategies to ameliorate the transthyretin amyloidoses.2010

    • Author(s)
      関島良樹
    • Organizer
      Intemational Symposium on Amyloidogenesis and Anti-Amyloid Therapies(招待講演)
    • Place of Presentation
      Tokyo.
    • Year and Date
      2010-01-28
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] FAPを中心とした遺伝性ニューロパチー2010

    • Author(s)
      関島良樹
    • Organizer
      日本人類遺伝学会第55回大会
    • Place of Presentation
      大宮 招待講演
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] FAPに対するDinunisalを用いた治療の長期効果の検討2009

    • Author(s)
      関島良樹
    • Organizer
      第50回日本神経学会総会
    • Place of Presentation
      仙台
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Native state stabilizationを用いたアミロイドーシス治療2009

    • Author(s)
      関島良樹(招待講演)
    • Organizer
      大阪大学蛋白質研究所セミナー
    • Place of Presentation
      大阪
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Native state stabihzationを用いたアミロイドーシス治療.2009

    • Author(s)
      関島良樹
    • Organizer
      大阪大学蛋白質研究所セミナー(招待講演)
    • Place of Presentation
      大阪
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] FAPに対するDiflunisalを用いた治療の長期効果の検討2009

    • Author(s)
      関島良樹
    • Organizer
      第50回日本神経学会総会
    • Place of Presentation
      仙台
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP)における野生型TTR関与の臓器間比較2009

    • Author(s)
      鈴木彩子、矢崎正英、関島良樹、池田修一
    • Organizer
      第50回日本神経学会総会
    • Place of Presentation
      仙台
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] TTR-derived amyloid deposition on punched skin biopsy in patients with senile systemic amyloidosis.2008

    • Author(s)
      Ikeda S, Tojo K, Tsuchiya-Suzuki A, Yazaki M, Sekijima Y. Koyama J, Hoshi Y
    • Organizer
      VIIth International Symposium on Familial Amyloid Poluneuropathy
    • Place of Presentation
      London
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 本邦における家族性アミロイドポリニューロパチー(FAP)の地理的分布および臨床像についての検討2008

    • Author(s)
      関島良樹, 古庄知己, 和田敬仁, 涌井敬子, 櫻井晃洋, 福嶋義光, 東城加奈, 池田修一
    • Organizer
      日本人類遺伝学会第53回大会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 脳梗塞が初発症状となった老人性全身性(心)アミロイドーシス患者の臨床像2008

    • Author(s)
      池田修一、東城加奈、土屋彩子、矢崎正英、関島良樹
    • Organizer
      第49回日本神経学会総会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Val3OMet transthyretin (TTR) gene dosage effects on the phenotypes of familial amyloid polyneuropathy2008

    • Author(s)
      Tojo K, Sekijima Y. Tsuchiya-Suzuki A, Yazaki M, Ikeda S
    • Organizer
      VIIth International Symposium on Familial Amyloid Poluneuropathy
    • Place of Presentation
      London
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] The contribution of wild-type TTR to abdominal fat amyloid in FAP patients : an age-related change2008

    • Author(s)
      Tsuchiya-Suzuki A, Yazaki M, Sekijima Y, Takei Y, Ikeda S, Kametani F
    • Organizer
      VIIth International Symposium on Familial Amyloid Poluneuropathy
    • Place of Presentation
      London
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Val30Met transthyretin (TTR) gene dosage effects on the phenotypes of familial amyloid polyneuropathy.2008

    • Author(s)
      Tojo K, Sekijima Y, Tsuchiya-Suzuki A, Yazaki M, Ikeda S.
    • Organizer
      VIIth International Symposium on FamilialAmyloid Poluneuropathy
    • Place of Presentation
      London
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Long-term effects of diflunisal on familial amyloid plyneuropathy2008

    • Author(s)
      Sekijima Y. Tojo K, Morita H, Koyama J, Uchiyama T, Tsuchiya-Suzuki A, Yazaki M, Ikeda S
    • Organizer
      VIIth International Symposium on Familial Amyloid Poluneuropathy
    • Place of Presentation
      London
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 野生型トランスサイレチン由来アミロイドに伴う手根管症候群の臨床像検討2008

    • Author(s)
      小平農、土屋彩子、東城加奈、矢崎正英、関島良樹、武井洋一、森田洋、池田修一
    • Organizer
      第49回日本神経学会総会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] Long-term effects of diflunisal on familial amyloid plyneuropathy.2008

    • Author(s)
      Sekijima Y, Tojo K, Morita H, Koyama J, Uchiyama T, Tsuchiya-Suzuki A, Yazaki M, Ikeda S
    • Organizer
      VIIth International Symposium on FamilialAmyloid Poluneuropathy
    • Place of Presentation
      London
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] The contribution of wild-type TTR to abdominal fat amyloid in FAP patients : an age-related change.2008

    • Author(s)
      Tsuchiya-Suzuki A, Yazaki M, Sekijima Y, Takei Y, Ikeda S, Kametani F.
    • Organizer
      VIIth International Symposium on FamilialAmyloid Poluneuropathy
    • Place of Presentation
      London
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] TTR-derived amyloid deposition on punched skin biopsy in patients with senile systemic amyloidosis.2008

    • Author(s)
      Ikeda S, Tojo K, Tsuchiya-Suzuki A, Yazaki M, Sekijima Y, Koyama, Hoshi Y.
    • Organizer
      VIIth International Symposium on FamilialAmyloid Poluneuropathy
    • Place of Presentation
      London
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] The presence of wild-type TTR in gastroduodenal mucosal amyloid in FAP patients2008

    • Author(s)
      Yazaki M, Tsuchiya-Suzuk iA, Sekijima Y, Takei Y, Ikeda S, Kametani F
    • Organizer
      VIIth International Symposium on Familial Amyloid Poluneuropathy
    • Place of Presentation
      London
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] The presence of wild-type TTR in gastroduodenal mucosal amyloid in FAP patients.2008

    • Author(s)
      Yazaki M, Tsuchiya-Suzuki A, Sekijima Y, Takei Y, Ikeda S、Kametani F.
    • Organizer
      VIIth International Symposium on FamilialAmyloid Poluneuropathy
    • Place of Presentation
      London
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] FAP患者における腹壁および胃アミロイドにおける野生型TTRの関与2008

    • Author(s)
      土屋彩子、矢崎正英、亀谷富由樹、武井洋一、関島良樹、池田修一
    • Organizer
      第49回日本神経学会総会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] FAPの分布および臨床像についての検討2008

    • Author(s)
      東城加奈、土屋彩子、矢崎正英、関島良樹、武井洋一、池田修一
    • Organizer
      第49回日本神経学会総会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-20590695
  • [Presentation] 集積地に認められたV30M TTRホモ接合体FAP家系の臨床的,生化学的検討2007

    • Author(s)
      東城加奈, 関島良樹, 池田修一
    • Organizer
      第48回日本神経学会総会
    • Place of Presentation
      名古屋,名古屋国際会議場
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-18590932
  • [Presentation] FAP患者に対するDiflunisalを用いた新たな薬物療法の開発2007

    • Author(s)
      関島良樹, 東城加奈, 池田修一
    • Organizer
      第48回日本神経学会総会
    • Place of Presentation
      名古屋,名古屋国際会議場
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-18590932
  • [Presentation] ジフルニサル,フルフェナム酸,ピコリン酸クロムの血清変異TTR安定化作用の検討2006

    • Author(s)
      東城加奈, 関島良樹, 池田修一
    • Organizer
      第47回日本神経学会総会
    • Place of Presentation
      東京,京王プラザホテル
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-18590932
  • [Presentation] 家族性アミロイドポリニューロパチーの生物学的・化学的発症機序の研究2006

    • Author(s)
      関島良樹, 池田修一, 福嶋 義光
    • Organizer
      第51回日本人類遺伝学会
    • Place of Presentation
      米子,米子コンベンションセンター
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-18590932
  • [Presentation] TTR四量体を安定化する低分子化合物を用いたFAPに対する薬物療法の開発2006

    • Author(s)
      関島良樹, 東城加奈, Kelly JW, 池田修一
    • Organizer
      第47回日本神経学会総会
    • Place of Presentation
      東京,京王プラザホテル
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-18590932
  • [Presentation] Regression of gastroduodenal mucosal amyloid deposits in FAP patients after combined therapy with oral intake of diflunisal followed by liver transplantation.

    • Author(s)
      Yoshinaga T, Yazaki M, Sekijima Y, Kametani F, Ikeda S
    • Organizer
      The XIVth International Symposium on Amyloidosis
    • Place of Presentation
      Indianapolis, USA
    • Year and Date
      2014-04-27 – 2014-05-01
    • Data Source
      KAKENHI-PROJECT-25461275
  • [Presentation] Safety and efficacy of long-term diflunisal administration in familial amyloid polyneuropathy - Summary of ten years therapeutic experience

    • Author(s)
      Sekijima Y, Tojo K, Morita H, Koyama J, Yazaki M, Ikeda S
    • Organizer
      The XIVth International Symposium on Amyloidosis
    • Place of Presentation
      Indianapolis, USA
    • Year and Date
      2014-04-27 – 2014-05-01
    • Data Source
      KAKENHI-PROJECT-25461275
  • []

  • 1.  YAZAKI Masahide (70372513)
    # of Collaborated Projects: 3 results
    # of Collaborated Products: 18 results
  • 2.  MORITA Hiroshi (10262718)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 19 results
  • 3.  KOYAMA Jun (10303463)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 14 results
  • 4.  IKEDA Shu-ichi (60135134)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 2 results
  • 5.  TOJO Kana (10467178)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 35 results
  • 6.  佐藤 充人 (10816630)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 7.  UEDA Mitsuharu
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 2 results
  • 8.  KITAOKA Hiroaki
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 9.  KUBO Toru
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 10.  柳澤 新
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 11.  安東 由喜雄
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 4 results
  • 12.  山下 太郎
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 3 results
  • 13.  馬場 裕一
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 14.  内木 宏延
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 15.  三隅 洋平
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 16.  樋口 京一
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 17.  亀谷 富由樹
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 18.  八谷 如美
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 19.  中村 公俊
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results

URL: 

Are you sure that you want to link your ORCID iD to your KAKEN Researcher profile?
* This action can be performed only by the researcher himself/herself who is listed on the KAKEN Researcher’s page. Are you sure that this KAKEN Researcher’s page is your page?

この研究者とORCID iDの連携を行いますか?
※ この処理は、研究者本人だけが実行できます。

Information User Guide FAQ News Terms of Use Attribution of KAKENHI

Powered by NII kakenhi