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NAGAO Kazuaki  長尾 和右

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… Alternative Names

長尾 和右  ナガオ カズアキ

Nagao Kazuaki  長尾 和右

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Researcher Number 60392487
Other IDs
Affiliation (Current) 2025: 北里大学, 医学部, 講師
Affiliation (based on the past Project Information) *help 2023: 北里大学, 医学部, 講師
2018 – 2020: 北里大学, 医学部, 講師
2016: 北里大学, 医学部, 講師
2015: 北里大学, 医学部, 助教
2013: 北里大学, 医学部, 助教
2008: Kitasato University, 医学部, 助教
2007: National Research Institute for Child Health and Development, 成育遺伝研究部, 流動研究員
Review Section/Research Field
Principal Investigator
Basic Section 56050:Otorhinolaryngology-related / Basic Section 50010:Tumor biology-related / Human genetics / Pediatrics
Except Principal Investigator
Basic Section 52050:Embryonic medicine and pediatrics-related / Pediatrics / Tumor biology
Keywords
Principal Investigator
iPS細胞 / NBCCS / 髄芽腫 / 母斑基底細胞癌症候群 / EYA4 / 難聴 / iPS / Gorlin / ソニックヘッジホッグ / ゴーリン症候群 … More / CRISPR/Cas9 / ヘッジホッグシグナル伝達系 / PTCH1 / 遺伝子編集 / 遺伝病 / CRSPR/Cas9 / 奇形腫 / CRISPR/Cas9システム / 発生・分化 / 脳神経疾患 / ゲノム / 遺伝子 / Gli / Sonic hedgehog / Mddle interhemispheric valiant / Holoprosencephaly / マイクロアレイ / MIH / 全前脳症 / SIX3 … More
Except Principal Investigator
PTCH1 / 母斑基底細胞癌症候群 / 基底細胞母斑症候群 / 骨密度 / 骨代謝 / ヘッジホッグ / Gorlin症候群 / CRISPR/Cas9 / モザイク / LOH / 髄芽腫 / 遺伝子編集 / iPS細胞 / CRISPR/Cas9システム / 歯原性腫瘍 / 癌抑制遺伝子 Less
  • Research Projects

    (7 results)
  • Research Products

    (37 results)
  • Co-Researchers

    (9 People)
  •  EYA4遺伝子変異難聴患者iPS細胞を用いた病態解明と治療候補薬剤スクリーニングPrincipal Investigator

    • Principal Investigator
      長尾 和右
    • Project Period (FY)
      2023 – 2025
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 56050:Otorhinolaryngology-related
    • Research Institution
      Kitasato University
  •  Molecular mechanism of bone metabolism in Gorlin syndrome

    • Principal Investigator
      藤井 克則
    • Project Period (FY)
      2023 – 2025
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52050:Embryonic medicine and pediatrics-related
    • Research Institution
      Chiba University
  •  Generating a cancer model using CRISPR/Cas9 systemPrincipal Investigator

    • Principal Investigator
      Nagao Kazuaki
    • Project Period (FY)
      2018 – 2020
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 50010:Tumor biology-related
    • Research Institution
      Kitasato University
  •  Medulloblastoma generation in nevoid basal cell carcinoma syndromee-induced pluripotent stem cells.Principal Investigator

    • Principal Investigator
      NAGAO Kazuaki
    • Project Period (FY)
      2015 – 2016
    • Research Category
      Grant-in-Aid for Young Scientists (B)
    • Research Field
      Human genetics
    • Research Institution
      Kitasato University
  •  Basic studies toward CRISPR/Cas9-mediated cell therapy

    • Principal Investigator
      Miyashita Toshiyuki
    • Project Period (FY)
      2014 – 2016
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Kitasato University
  •  Dysregulation of hedgehog signaling and tumorigenesis

    • Principal Investigator
      MIYASHITA Toshiyuki
    • Project Period (FY)
      2011 – 2013
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Tumor biology
    • Research Institution
      Kitasato University
  •  Searching for a novel gene responsible for holoprosencephalyPrincipal Investigator

    • Principal Investigator
      NAGAO Kazuaki
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Young Scientists (B)
    • Research Field
      Pediatrics
    • Research Institution
      Kitasato University
      National Research Institute for Child Health and Development

All 2019 2018 2017 2016 2015 2013 2012 2011 Other

All Journal Article Presentation

  • [Journal Article] Dysregulated DNA methylation of GLA gene was associated with dysfunction of autophagy2019

    • Author(s)
      Hiroko Yanagisawa, Mohammad Arif Hossaina, Takashi Miyajima, KazuakiNagao, Toshiyuki Miyashita, Yoshikatsu Eto
    • Journal Title

      Molecular Genetics and Metabolism

      Volume: 126 Issue: 4 Pages: 460-465

    • DOI

      10.1016/j.ymgme.2019.03.003

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07205, KAKENHI-PROJECT-17K10061
  • [Journal Article] Somatic mosaicism containing double mutations in PTCH1 revealed by generation of induced pluripotent stem cells from nevoid basal cell carcinoma syndrome.2017

    • Author(s)
      Ikemoto, Y., Takayama, Y., Fujii, K., Masuda, M., Kato, C., Hatsuse, H., Fujitani, K., Nagao, K., Kameyama, K., Ikehara, H., Toyoda, M., Umezawa, A. and Miyashita, T.
    • Journal Title

      Journal of Medical Genetics

      Volume: - Issue: 8 Pages: 579-584

    • DOI

      10.1136/jmedgenet-2016-104490

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-26461530, KAKENHI-PROJECT-15K19041, KAKENHI-PROJECT-15K09729, KAKENHI-PROJECT-16K09960, KAKENHI-PROJECT-17K10061
  • [Journal Article] Nevoid basal cell carcinoma syndrome caused by splicing mutations in the PTCH1 gene.2017

    • Author(s)
      Kato, C., Fujii, K., Arai, Y., Hatsuse, H., Nagao, K., Takayama, Y., Kameyama, K., Fujii, K., and Miyashita, T.
    • Journal Title

      Familial Cancer

      Volume: 16 Issue: 1 Pages: 131-138

    • DOI

      10.1007/s10689-016-9924-2

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-26461530, KAKENHI-PROJECT-16K09960
  • [Journal Article] Molecular pathogenesis of keratocystic odontogenic tumors developing in nevoid basal cell carcinoma syndrome.2013

    • Author(s)
      Suzuki, M.,Nagao, K., Hatsuse, H., Sasaki, R., Saito, K., Fujii, K., Miyashita, T.
    • Journal Title

      Oral Surg. Oral Med. Oral Pathol. Oral Radiol.

      Volume: 116 Issue: 3 Pages: 348-353

    • DOI

      10.1016/j.oooo.2013.06.017

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Journal Article] Molecular pathogenesis of keratocystic odontogenic tumors developing in nevoid basal cell carcinoma syndrome2013

    • Author(s)
      Suzuki, M., Nagao, K., Hatsuse, H., Sasaki, R., Saito, K., Fujii, K., and Miyashita, T
    • Journal Title

      Oral Surg. Oral Med. Oral Pathol. Oral Radiol

      Volume: 116 Pages: 348-353

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Journal Article] Selective haploinsufficiency of longer isoforms of PTCH1 protein can cause nevoid basal cell carcinoma syndrome2012

    • Author(s)
      Suzuki, M., Hatsuse, H., Nagao, K., Takayama, Y., Kameyama, K., Kabasawa, Y., Omura, K., Yoshida, M., Fujii, K., and Miyashita, T
    • Journal Title

      J. Hum. Genet

      Volume: 57 Pages: 422-426

    • NAID

      10030965596

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Journal Article] Heterozygous Tandem Duplication Within the PTCH1 Gene Results in Nevoid Basal Cell Carcinoma Syndrome2012

    • Author(s)
      Kosaki, R., Nagao, K., Kameyama, K., Suzuki, M., Fujii, K., and Miyashita T
    • Journal Title

      Am. J. Med. Genet A

      Volume: 158A Pages: 1724-1728

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Journal Article] Selective haploinsufficiency of longer isoforms of PTCH1 protein can cause nevoid basal cell carcinoma syndrome2012

    • Author(s)
      Suzuki, M., Hatsuse, H., Nagao, K., Takayama, Y., Kameyama, K., Kabasawa, Y., Omura, K., Yoshida, M., Fujii, K., and Miyashita, T.
    • Journal Title

      J. Hum. Genet.

      Volume: 57 Issue: 7 Pages: 422-426

    • DOI

      10.1038/jhg.2012.45

    • NAID

      10030965596

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Journal Article] Heterozygous Tandem Duplication Within the PTCH1 Gene Results in Nevoid Basal Cell Carcinoma Syndrome2012

    • Author(s)
      Kosaki, R., Nagao, K., Kameyama, K., Suzuki, M., Fujii, K., and Miyashita T.
    • Journal Title

      Am. J. Med. Genet. A

      Volume: 158A Issue: 7 Pages: 1724-1728

    • DOI

      10.1002/ajmg.a.35412

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Journal Article] RCAN1 is an important mediator of glucocorticoid-induced apoptosis in human leukemic cells2012

    • Author(s)
      Nagao, K., Iwai Y., and Miyashita T.
    • Journal Title

      PLOS ONE

      Volume: 7 Issue: 11 Pages: e49926-e49926

    • DOI

      10.1371/journal.pone.0049926

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Journal Article] Entire PTCH1 deletion is a common event in point mutation-negative cases with nevoid basal cell carcinoma syndrome in Japan2011

    • Author(s)
      Nagao, K., Fujii, K., Saito, K., Sugita, K., Endo, M., Motojima, T., Hatsuse, H. and Miyashita, T.
    • Journal Title

      Clinical Genetics

      Volume: 79 Issue: 2 Pages: 196-198

    • DOI

      10.1111/j.1399-0004.2010.01527.x

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Journal Article] Entire PTCH1 deletion is a common event in point mutation-negative cases with nevoid basal cell carcinoma syndrome in Japan2011

    • Author(s)
      Nagao, K., Fujii, K., Saito, K., Sugita, K., Endo, M., Motojima, T., Hatsuse, H. and Miyashita, T
    • Journal Title

      Clin. Genet

      Volume: 79 Pages: 196-198

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Presentation] 次世代シークエンサーを用いたGorlin症候群患者に発症した各種腫瘍の遺伝子解析2018

    • Author(s)
      兼友 裕大、高山 吉永、初瀬 洋美、藤谷 和子、長尾 和右、亀山 孝三、宮下 俊之
    • Organizer
      第41回日本分子生物学会年会
    • Data Source
      KAKENHI-PROJECT-18K07205
  • [Presentation] マウスのインプリンティング型X染色体不活化においてRNF12はREX1の抑制によって父由来non-coding RNA Tsix を抑制する2018

    • Author(s)
      中村 茜里、福田 篤、長尾 和右、阿久津 英憲、宮下 俊之
    • Organizer
      第41回日本分子生物学会年会
    • Data Source
      KAKENHI-PROJECT-18K07205
  • [Presentation] CRISPR/Cas9システムを用いたNBCCSモデルiPS細胞の作製2018

    • Author(s)
      長尾 和右、高山 吉永、宮下 俊之
    • Organizer
      第77回日本癌学会学術総会
    • Data Source
      KAKENHI-PROJECT-18K07205
  • [Presentation] 母斑基底細胞癌症候群患者由来細胞を用いた腫瘍の作製2018

    • Author(s)
      長尾 和右、加藤 千勢、初瀬 洋美、高山 吉永、亀山 孝三、梅澤 明弘、藤井 克則、宮下 俊之
    • Organizer
      第41回日本分子生物学会年会
    • Data Source
      KAKENHI-PROJECT-18K07205
  • [Presentation] Entire PTCH1 deletions detected in 9 families with nevoid basal cell carcinoma syndrome2016

    • Author(s)
      高山吉永、長尾一右、藤井克則、宮下俊之
    • Organizer
      第75回日本癌学会学術総会
    • Place of Presentation
      パシフィコ横浜(横浜市)
    • Year and Date
      2016-10-06
    • Data Source
      KAKENHI-PROJECT-26461530
  • [Presentation] Gorlin症候群患者由来iPS細胞を用いた髄芽腫の作製2016

    • Author(s)
      池本優、豊田雅士、那須道世、初瀬洋美、長尾和右、高山吉永、亀山孝三、梅澤明弘、宮下俊之
    • Organizer
      第39回日本分子生物学会年会
    • Place of Presentation
      パシフィコ横浜 (神奈川県横浜市)
    • Year and Date
      2016-11-30
    • Data Source
      KAKENHI-PROJECT-15K19041
  • [Presentation] Gorlin症候群患者由来iPS細胞を用いた髄芽腫の作製2016

    • Author(s)
      池本 優、豊田 雅士、那須 道世、初瀬 洋美、長尾 和右、高山 吉永、亀山 孝三、梅澤 明弘、宮下 俊之
    • Organizer
      第39回日本分子生物学会年会
    • Place of Presentation
      パシフィコ横浜(横浜市)
    • Year and Date
      2016-11-30
    • Data Source
      KAKENHI-PROJECT-26461530
  • [Presentation] Establishment of the cell lines with a large genomic deletion by CRISPR/Cas9 system.2015

    • Author(s)
      長尾和右、高山吉永、宮下俊之
    • Organizer
      第74回日本癌学会学術総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-10-08
    • Data Source
      KAKENHI-PROJECT-26461530
  • [Presentation] CRISPR/Cas9システムを用いた2点同時切断による目的ゲノム領域除去細胞株の作製2015

    • Author(s)
      加藤千勢、長尾和右、初瀬洋美、高山吉永、亀山孝三、宮下俊之
    • Organizer
      第38回日本分子生物学会年会 第88回日本生化学会大会 合同大会
    • Place of Presentation
      神戸ポートアイランド
    • Year and Date
      2015-12-01
    • Data Source
      KAKENHI-PROJECT-15K19041
  • [Presentation] CRISPR/Cas9システムを用いた2点同時切断による目的ゲノム領域除去細胞株の作製2015

    • Author(s)
      加藤千勢、長尾和右、初瀬洋美、高山吉永、亀山孝三、宮下俊之
    • Organizer
      第38回日本分子生物学会年会
    • Place of Presentation
      神戸国際会議場(兵庫県神戸市)
    • Year and Date
      2015-12-01
    • Data Source
      KAKENHI-PROJECT-26461530
  • [Presentation] Establishment of the cell lines with a large genomic deletion by CRISPR/Cas92015

    • Author(s)
      Kazuaki Nagao, Yoshinaga Takayama, Toshiyuki Miyashita
    • Organizer
      第74回日本癌学会学術総会
    • Place of Presentation
      名古屋国際会議場
    • Year and Date
      2015-10-08
    • Data Source
      KAKENHI-PROJECT-15K19041
  • [Presentation] Functional analysis of a sonic hedgehog signaling pathway inhibitor SUFU2013

    • Author(s)
      長尾和右、宮下俊之
    • Organizer
      第72回日本癌学会学術総会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Presentation] PTCH2とSUFU遺伝子に配偶子変異をもつ母斑基底細胞癌症候群の検討2012

    • Author(s)
      鈴木麻衣子、長尾和右、高山吉永、岡秀宏、藤井克則、宮下俊之
    • Organizer
      第71回日本癌学会学術総会
    • Place of Presentation
      札幌
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Presentation] PTCH2とSUFU 遺伝子に配偶子変異をもつ母斑基底細胞癌症候群の検討2012

    • Author(s)
      鈴木麻衣子、長尾和右、高山吉永、岡秀宏、藤井克則、宮下俊之
    • Organizer
      第71回日本癌学会学術総会
    • Place of Presentation
      札幌
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Presentation] 母斑基底細胞癌症候群で見出されたスプライシング変異と異常mRNAの分解2012

    • Author(s)
      志村将人、鈴木麻衣子、初瀬洋美、長尾和右、高山吉永、亀山孝三、藤井克則、宮下俊之
    • Organizer
      第35回日本分子生物学会年会
    • Place of Presentation
      福岡
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Presentation] 母斑基底細胞癌症候群で見出されたスプライシング変異と異常mRNA の分解2012

    • Author(s)
      志村将人、鈴木麻衣子、初瀬洋美、長尾和右、高山吉永、亀山孝三、藤井克則、宮下俊之
    • Organizer
      第35回日本分子生物学会年会
    • Place of Presentation
      福岡
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Presentation] 母斑基底細胞癌症候群に発症した角化嚢胞性歯原性腫瘍の発症機序の解析2011

    • Author(s)
      鈴木麻衣子、長尾和右、高山吉永、亀山孝三、藤井克則、宮下俊之
    • Organizer
      第34回日本分子生物学会年会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Presentation] 母斑基底細胞癌症候群に発症する角化嚢胞性歯原性腫瘍の腫瘍化機序の解析2011

    • Author(s)
      鈴木麻衣子、長尾和右、高山吉永、藤井克則、宮下俊之
    • Organizer
      第70回日本癌学会学術総会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Presentation] CRISPR/Cas9システムを用いた広域欠損ゲノムを有する細胞株の作製

    • Author(s)
      長尾和右 加藤千勢 初瀬洋美 高山吉永 亀山孝三 宮下俊之
    • Organizer
      第37回日本分子生物学会年会
    • Place of Presentation
      パシフィコ横浜(神奈川県横浜市)
    • Year and Date
      2014-11-25 – 2014-11-27
    • Data Source
      KAKENHI-PROJECT-26461530
  • [Presentation] PTCH1遺伝子以外の遺伝子変異によって発症する母斑基底細胞癌症候群 ―多遺伝子1症候群?―

    • Author(s)
      宮下俊之、鈴木麻衣子、長尾和右、初瀬弘美、藤井克則
    • Organizer
      第17回日本家族性腫瘍学会学術集会
    • Place of Presentation
      別府
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Presentation] グルココルチコイド誘導性アポトーシスの解析

    • Author(s)
      岩井祐二郎、高山吉永、亀山孝三、初瀬洋美、長尾和右、宮下俊之
    • Organizer
      第26回北里大学バイオサイエンスフォーラム
    • Place of Presentation
      相模原
    • Data Source
      KAKENHI-PROJECT-23501269
  • [Presentation] CRISPR/Cas9システムを用いたソニックヘッジホッグシグナル伝達系構成遺伝子ノックアウト細胞株の作製

    • Author(s)
      長尾和右 高山吉永 宮下俊之
    • Organizer
      第73回日本癌学会学術総会
    • Place of Presentation
      パシフィコ横浜(神奈川県横浜市)
    • Year and Date
      2014-09-25 – 2014-09-27
    • Data Source
      KAKENHI-PROJECT-26461530
  • [Presentation] CRISPR/Cas9システムを用いたSNPジェノタイプ転換の試み

    • Author(s)
      高山吉永 初瀬洋美 中島早耶 鈴木香織 加藤千勢 長尾和右 亀山孝三 宮下俊之
    • Organizer
      第37回日本分子生物学会年会
    • Place of Presentation
      パシフィコ横浜(神奈川県横浜市)
    • Year and Date
      2014-11-25 – 2014-11-27
    • Data Source
      KAKENHI-PROJECT-26461530
  • [Presentation] CRISPR/Cas9システムによる欠失導入効率の検討

    • Author(s)
      加藤千勢 高山吉永 亀山孝三 初瀬洋美 長尾和右 宮下俊之
    • Organizer
      第27回北里大学バイオサイエンスフォーラム
    • Place of Presentation
      北里大学(神奈川県相模原市)
    • Year and Date
      2014-08-21 – 2014-08-22
    • Data Source
      KAKENHI-PROJECT-26461530
  • [Presentation] CRISPR/Cas9システムを用いたヘッジホッグシグナル伝達系構成遺伝子ノックアウト細胞株の作製

    • Author(s)
      長尾和右、遠藤葉月、加藤千勢、初瀬洋美、高山吉永、亀山孝三、宮下俊之
    • Organizer
      第36回日本分子生物学会年会
    • Place of Presentation
      神戸
    • Data Source
      KAKENHI-PROJECT-23501269
  • 1.  MIYASHITA Toshiyuki (60174182)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 29 results
  • 2.  KAMEYAMA Kohzoh (40214556)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 16 results
  • 3.  TAKAYAMA Yoshinaga (90245407)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 10 results
  • 4.  松崎 佐栄子 (70573400)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 5.  藤井 克則 (70344992)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 6.  塩浜 直 (10737034)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 7.  IKEMOTO Yu
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 1 results
  • 8.  KATO Chise
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 1 results
  • 9.  ARAI Yuto
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results

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