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DOYU Manabu  道勇 学

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… Alternative Names

道勇 学  ドウユウ マナブ

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Researcher Number 90293703
Other IDs
External Links
Affiliation (Current) 2022: 愛知医科大学, 医学部, 教授
Affiliation (based on the past Project Information) *help 2019 – 2020: 愛知医科大学, 医学部, 教授
2015 – 2016: 愛知医科大学, 医学部, 教授
2008: 愛知医科大学, 医学部, 教授
2007: 愛知医科大学, 医学部, 特任教授
2006: Aichi Medical University, School of Medicine, Professor, 医学部, 教授 … More
2004 – 2005: Nagoya University, Graduate School of Medicine, Associate Professor, 大学院・医学系研究科, 助教授
2004 – 2005: Nagoya Univesity, Department of Neurology, Assistant Professor, 大学院医学系研究科, 助教授
2002 – 2003: 名古屋大学, 大学院・医学系研究科, 講師
2001: 名古屋大学, 大学院・医学研究科, 教授
2001: Graduate School of Medicine, Nagoya University, Assistant Professor, 大学院・医学研究科, 講師
1998 – 2000: 名古屋大学, 医学部, 講師
1998: 名古屋大学, 医学部・名古屋大学, 講師 Less
Review Section/Research Field
Principal Investigator
Neurology / Neurology / Basic Section 52020:Neurology-related
Except Principal Investigator
Neurology / Biological Sciences / Neurology / Ophthalmology
Keywords
Principal Investigator
球脊髄性筋萎縮症 / Dorfin / 筋萎縮性側索硬化症 / VCP / p97 / アンドロゲン受容体 / CAGリピート / トランスジェニックマウス / 酵母Two-Hybrid / マススペクトロメトリー … More / 蛋白分解 / DNA chip / 遺伝子発現解析 / LHRHアナログ / HSP70 / spinal and bulbar muscular atrophy / 微小管結合蛋白 / MAP1B / パーキンソン病 / アルツハイマー病 / Hsp90阻害剤 / Hsp70 / GGA / 分子インデックス法 / 遺伝子発現プロファイル / 運動ニューロン死 / 新規遺伝子 / リングフィンガーモチーフ / ユビキチン系 / 運動ニューロン疾患 / 神経悪性疾患 / Amyotrophic Lateral Screlosis / Molecular Indexing / Expressed-Gene Profile / Motor Neuron Death / Novel Genes / Ring Finger / IBR Motif / Ubiquitination / CAGリピート病 / ポリグルタミン鎖 / 神経細胞死 / アデノウイルスベクター / 培養神経系細胞モデル / ポリグルタミン凝集体 / CAG repeat disease / polyglutamine tract / neuronal cell death / Spinal and bulbar muscular atrophy / adenovirus vector / In vitro neuronal cell culture model / Gene expression analysis / 去勢術 / テストステロン / ホルモン治療 / Hsp / androgen receptor / CAG repeat / transgenic mouse / castration / LHRH analogue / protein degradation / 運動ニューロン / ポリグルタミン / 臨床試験 / バイオマーカー / 分子シャペロン / ヒストン脱アセチル化 / ユビキチンリガーゼ / motor neuron / amyotrophic lateral sclerosis / polyglutamine / LHRH analog / gene expression profiles / 疾患iPS細胞 / 骨格筋 … More
Except Principal Investigator
ポリグルタミン / 運動ニューロン / 球脊髄性筋萎縮症 / アンドロゲン受容体 / HSP / 17-AAG / GGA / ALS / dynactin1 / 遺伝子発現解析 / geranylgeranylaceone / motor neuron / heat shock protein / レーザーマイクロダイセクション法 / cDNAマイクロアレー / 球脊髄性筋萎縮症(SBMA) / 軸索輸送 / ユビキチン-プロテアソーム / 分子シャペロン / CAGリピート / 神経変性 / LHRHアナログ / ヒストン / 熱ショックタンパク質 / テストステロン / polyglutamine / histone / chemokine / chemokine receptor / Th1 / Th2 / MCP-1 / MIP-1β / RANTES / IP-10 / siRNA / パーキンソン病 / 分子インデックス法 / 病態関連遺伝子 / 遺伝子発現 / クローニング / 運動ニューロン疾患 / 筋萎縮性側索硬化症(ALS) / 発現遺伝子プロファイル / 脊髄小脳失調症(SCA) / 転写障害 / TGF-β / ユビキチン / プロテアソーム / 17-DMAG / ポリグルタミン病 / CHIP / モーター蛋白質 / dnactin1 / ニューロフィラメント / 神経分子病態学 / ユビキチンープロテアソーム / リュープロレリン / ユビキチン・プロテアソーム / 熱ショック蛋白質 / cyclin C / 線虫 / 疾患モデル / dynactinl / アロドロゲン受容体 / トランスジェニックマウス / 去勢術 / HSP70 / びまん性核内蓄積 / ホルモン治療 / Hsp / CAGリピート病 / ポリグルタミン鎖 / 神経細胞死 / アデノウイルスベクター / 培養神経系細胞モデル / DNA chip / アンドロゲン受容体(AR) / neurodegeneration / andorogen receptor / LHRH analog / 炎症性筋疾患 / 多発筋炎 / 皮膚筋炎 / 封入体筋炎 / Inflammatory myopathy / フルタミド / Neurodegeneration / androgen receptor / バイオマーカー / 神経変性疾患 / spinal and bulbar muscular atrophy / molecular chaperone / ubiquitin-proteasome / biomarker / オートファジー / cDNAマイクロアレイ / gene expression analysis / autophagy / 甲状腺眼症 / 平滑筋線維 / 筋線維芽細胞 / 脱分化 / 平滑筋細胞 / 外眼筋周囲脂肪組織 / 線維芽細胞 Less
  • Research Projects

    (19 results)
  • Research Products

    (96 results)
  • Co-Researchers

    (14 People)
  •  Elucidaion of muscular pathology of SBMA using disease specific iPSCsPrincipal Investigator

    • Principal Investigator
      道勇 学
    • Project Period (FY)
      2019 – 2021
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Aichi Medical University
  •  甲状腺眼症における筋線維芽細胞の起源の研究

    • Principal Investigator
      柿崎 裕彦
    • Project Period (FY)
      2015 – 2016
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Ophthalmology
    • Research Institution
      Aichi Medical University
  •  Pathogenesis-based therapy development for polyglutamine diseases

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Scientific Research (A)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of animal model for sporadic ALS

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of pathogenesis-based therapy for polyglutamine diseases

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2005 – 2009
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas
    • Review Section
      Biological Sciences
    • Research Institution
      Nagoya University
  •  分子シャペロンによる運動ニューロン疾患治療法の開発-SBMA・ALSを中心に-Principal Investigator

    • Principal Investigator
      道勇 学
    • Project Period (FY)
      2005
    • Research Category
      Grant-in-Aid for Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Treatment of polyglutamine disease using small molecular compound

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Scientific Research (A)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Exploration of Target Molecules Related to Pathogenesis and Development of Therapy for Sporadic ALS

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  ユビキチンリガーゼDorfinの基質タンパク質の探索-神経変性との関連Principal Investigator

    • Principal Investigator
      道勇 学
    • Project Period (FY)
      2004
    • Research Category
      Grant-in-Aid for Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of low-molecular-weight compound therapy for polyglutamine diseasesPrincipal Investigator

    • Principal Investigator
      DOYU Manabu
    • Project Period (FY)
      2004 – 2005
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  孤発性ALSにおけるユビキチンリガーゼDorfinの基質タンパク質の探索Principal Investigator

    • Principal Investigator
      道勇 学
    • Project Period (FY)
      2003
    • Research Category
      Grant-in-Aid for Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of Pathogenesis-based treatment for spinal and bulbar muscular atrophy

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2003 – 2004
    • Research Category
      Grant-in-Aid for Scientific Research (A)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Investigation into pathology of CAG repeat diseases and development of therapiesPrincipal Investigator

    • Principal Investigator
      DOYU Manabu
    • Project Period (FY)
      2002 – 2003
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  investigation of pathomechanism of inflammatory myopathy (in view of chemokines)

    • Principal Investigator
      INUKAI Akira
    • Project Period (FY)
      2002 – 2003
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      NAGOYA UNIVERSITY
  •  運動ニューロン疾患の神経細胞死に係わる分子群の同定

    • Principal Investigator
      祖父江 元
    • Project Period (FY)
      2000
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas (A)
    • Research Institution
      Nagoya University
  •  Elucidation of molecular mechanism of neuronal cell death in spinal and bulbar muscular atrophy

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2000 – 2004
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas
    • Review Section
      Biological Sciences
    • Research Institution
      Nagoya University
  •  Elucidation of pathogenesis in CAG-repeat diseases using DNA chipPrincipal Investigator

    • Principal Investigator
      DOYU Manabu
    • Project Period (FY)
      2000 – 2001
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  遺伝子発現プロファイリングによるパーキンソン病の病態関連遺伝子の同定

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      1998
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas (A)
    • Research Institution
      Nagoya University
  •  Detection of Relating Molecules for the Pathology of Amyotrophic Lateral Screlosis by the Expressed-Gene ProfilingPrincipal Investigator

    • Principal Investigator
      DOYU Manabu
    • Project Period (FY)
      1998 – 1999
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University

All 2021 2020 2019 2010 2009 2007 2006 2005 2004 2003 2001

All Journal Article Presentation

  • [Journal Article] Modulation of oxygen tension, acidosis, and cell density is crucial for neural differentiation of human induced pluripotent stem cells2021

    • Author(s)
      Okada R, Onodera K, Ito T, Doyu M, Okano HJ, Okada Y
    • Journal Title

      Neurosci Res.

      Volume: - Pages: 30043-2

    • DOI

      10.1016/j.neures.2020.01.015

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19K07969, KAKENHI-PROJECT-18K15470, KAKENHI-PROJECT-18K07539, KAKENHI-PROJECT-17K19465, KAKENHI-PROJECT-20K16611, KAKENHI-PROJECT-19H03576, KAKENHI-PROJECT-19J40240
  • [Journal Article] 疾患特異的iPS細胞を用いた神経変性疾患の病態解析と新規治療法開発2020

    • Author(s)
      Onodera K, Shimojo D, Ishihara Y, Yano M, Miya F, Banno H, Kuzumaki N, Ito T, Okada R, Ohyama M, Yoshida M, Tsunoda T, Katsuno M, Doyu M, Sobue G, Okano H, Okada Y
    • Journal Title

      Molecular Brain

      Volume: 13 Pages: 1315-1319

    • DOI

      10.1186/s13041-020-0561-1

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07539, KAKENHI-PROJECT-19K07969, KAKENHI-PROJECT-17K19465, KAKENHI-PROJECT-17H04195, KAKENHI-PROJECT-19H03576, KAKENHI-PROJECT-18K15470, KAKENHI-PROJECT-20K16587, KAKENHI-PROJECT-20K16611, KAKENHI-PROJECT-19J40240
  • [Journal Article] Motor Improvement-Related Regional Cerebral Blood Flow Changes in Parkinson's Disease in Response to Antiparkinsonian Drugs.2019

    • Author(s)
      Taguchi S, Tanabe N, Niwa JI, Doyu M.
    • Journal Title

      Parkinsons Dis.

      Volume: 0 Pages: 7503230-7503230

    • Data Source
      KAKENHI-PROJECT-19K07969
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis.2010

    • Author(s)
      Sone J, Niwa JI, Kawai K, Ishigaki S, Yamada SI, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci Res. 88

      Pages: 123-135

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno, H., Katsuno, M., Suzuki, K., Takeuchi, Y., Kawashima, M., Suga, N., Takamori, M., Ito, M., Nakamura, T., Matsuo, K., Yamada, S., Oki, Y., Adachi, H., Minamiyama, M., Waza, M., Atsuta, N., Watanabe, H., Fujimoto, Y., Nakashima, T., Tanaka, F., Doyu, M., Sobue, G.
    • Journal Title

      Ann Neurol 65

      Pages: 140-150

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann. Neurol 65

      Pages: 140-150

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      Ann Neurol. 65

      Pages: 140-150

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G.
    • Journal Title

      Neurobiol Dis 25

      Pages: 331-341

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Nonmyelinating Schwann cell involvement with well-preserved unmyelinated axons in Charco-Matie-Tooth disease type 1A2007

    • Author(s)
      Koike H, Iijima M, Mori K, Yamamoto M, Hattori N, Katsuno M, Tanaka F, Watanabe H, Doyu M, Yoshikawa H, Sobue G
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 1027-1036

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] CHIP overexpression reduces mutant androgen receptor protein and ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci 27

      Pages: 5115-5126

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] CHIP Overexpression Reduces Mutant Androgen Receptor Protein and Ameliorates Phenotypes of the Spinal and Bulbar Muscular Atrophy Transgenic Mouse Model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J. Neurosci 27

      Pages: 5115-5126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Neuropathol Appl Neurobiol 33

      Pages: 135-151

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Neuropathol Appl Neurobiol 33

      Pages: 135-151

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity.2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G
    • Journal Title

      Neurobiol of Dis 25

      Pages: 331-341

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD12007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Biol Chem 282

      Pages: 28087-28095

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD12007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 282

      Pages: 28087-28095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Reduces Mutant Androgen Receptor protein and Ameliorates Phenotypes of the Spinal and Bulbar Muscular Atrophy Transgenic Mouse Model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Minamiyama M, Tanak F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 27

      Pages: 5115-5126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expressions specifically detected in motor neurons (dynactin 1, early growth response 3, Acetyl-CoA transporter, death receptor 5, and cyclin C) differentially correlate to athologic markers in sporadic amyotrophic lateral sclerosis2007

    • Author(s)
      Jiang Y, Yamamoto M, Tanaka F, Ishigaki S, Katsuno M, Adachi H, Niwia J, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Neuropathol Exp Neurol 66

      Pages: 617-627

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD12007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 282

      Pages: 28087-28095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Gene expressions specifically detected in motor neurons (dynactin l, early growth response 3, Acetyl-CoA transporter, death receptor 5, and cyclin C) differentially correlate to athologic markers in sporadic amyotrophic lateral sclerosis2007

    • Author(s)
      Jiang Y, Yamamoto M, Tanaka F, Ishigaki S, Katsuno M, Adachi H, Niwia J, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Neuropathol Exp Neurol 66

      Pages: 617-627

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      Neuropathol Appl Neurobiol 33

      Pages: 135-151

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G
    • Journal Title

      Neurobiol of Dis 25

      Pages: 331-341

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SODI proteins and reduce their cellular toxicity2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G
    • Journal Title

      Neurobiol Dis 25

      Pages: 331-241

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G
    • Journal Title

      Neurobiol of Dis 25

      Pages: 331-341

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Nonmyelinating Schwann cell involvement with well-preserved unmyelinated axons in Charco-Matie-Tooth disease type 1A2007

    • Author(s)
      Koike H, Iijima M, Mori K, Yamamoto M, Hattori N, Katsuno M, Tanaka F, Watanabe H, Doyu M, Yoshikawa H, Sobue G
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 1027-1036

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SODI proteins and reduce their cellular toxicity2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G
    • Journal Title

      Neurobiol Dis 25

      Pages: 331-241

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] CHIP overexpression reduces mutant androgen receptor protein and ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2007

    • Author(s)
      Adachi, H., Waza, M., Tokui, K., Katsuno, M., Minamiyama, M., Tanaka, F., Doyu, M., Sobue, G.
    • Journal Title

      J. Neurosci 27

      Pages: 5115-5126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Neuropathol. Appl. Neurobiol 33

      Pages: 135-151

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Reduces Mutant Androgen Receptor Protein and Ameliorates Phenotypes of the Spinal and Bulbar Muscular Atrophy Transgenic Mouse Model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Minamiyama M, Tanak F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 27

      Pages: 5115-5126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Gene expressions specifically detected in motor neurons (dynactin 1, early growth response 3, acetyl-CoA transporter, death receptor 5, and cyclin C) differentially correlate to pathologic markers in sporadic amyotrophic lateral sclerosis2007

    • Author(s)
      Jiang YM, Yamamoto M, Tanaka F, Ishigaki S, Katsuno M, Adachi H, Niwa J, Doyu M, Yoshida M, Hashizume Y, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 617-627

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol in press

    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : amolecular-targeted therapy against disease-causing protein2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular targeted therapy against disease-causing protein.2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med (in press)

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 1-10

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular-targeted therapy against disease-causing protein2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Pathogenesis, animal models and therapeutics in Spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol 200

      Pages: 8-18

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 1-10

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol (in press)

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular-targeted therapy against disease-causing protein.2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular-targeted therapy against disease-causing protein2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol (in press)

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Reversible disruption of dynactin 1-mediated retrograde axonal transport in polyglutamine-induced motor neuron degeneration2006

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Tokui K, Banno H, Suzuki K, Onoda Y, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 26

      Pages: 12106-12117

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Archaeal proteasomes effectively degrade aggregation-prone proteins and reduce cellular toxicities in mammalian cells.2006

    • Author(s)
      Yamada S, Niwa J, Ishigaki S, Takahashi M, Ito T, Sone J, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 281

      Pages: 23842-23851

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker.2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol (in press)

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular targeted therapy against disease-causing protein.2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med (in press)

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker.2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Pathogenesis, animal models and therapeutics in Spinal and bulbar muscular atrophy (SBMA)2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol 200

      Pages: 8-18

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Reversible disruption of dynactin 1-mediated retrograde axonal transport in polyglutamine-induced motor neuron degeneration2006

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Tokui K, Banno H, Suzuki K, Onoda Y, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 26

      Pages: 12106-12117

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann NY Acad Sci 1086

      Pages: 1-10

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Archaeal proteasomes effectively degrade aggregation-prone proteins and reduce cellular toxicities in mammalian cells2006

    • Author(s)
      Yamada S, Niwa J, Ishigaki S, Takahashi M, Ito T, Sone J, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 281

      Pages: 23842-23851

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker.2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis.2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann NY Acad Sci 1086

      Pages: 1-10

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Reversible disruption of dynactin 1-mediated retrograde axonal transport in polyglutamine-induced motor neuron degeneration.2006

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Tokui K, Banno H, Suzuki K, Onoda Y, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 26

      Pages: 12106-12117

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Pathogenesis, animal models and therapeutics in Spinal and bulbar muscular atrophy (SBMA)2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol 200

      Pages: 8-18

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Archaeal proteasomes effectively degrade aggregation-prone proteins and reduce cellular toxicities in mammalian cells2006

    • Author(s)
      Yamada S, Niwa J, Ishigaki S, Takahashi M, Ito T, Sone J, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 281

      Pages: 23842-23851

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Widespread nuclear and cytoplasmic accumulation of mutant androgen receptor in SBMA patients.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci USA 102

      Pages: 16801-16806

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Widespread nuclear and cytoplasmic mutant androgen receptor accumulation in spinal and bulbar muscular atrophy.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Waza M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration.2005

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Sang C, Tanaka F, Inukai A, Doyu M, Sobue G
    • Journal Title

      Nature Med 11

      Pages: 1088-1095

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci Usa 102

      Pages: 16801-16806

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Widespread nuclear and cytoplasmic mutant androgen receptor accumulation in spinal and bulbar muscular atrophy.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Waza M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci USA 102

      Pages: 16801-16806

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Widespread nuclear and cytoplasmic mutant androgen receptor accum ulation in spinal and bulbar muscular atrophy.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Waza M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration2005

    • Author(s)
      Waza, M., Adachi, H., Katsuno, M., Minamiyama, M., Sang, C., Tanaka, F., Inukai, A., Doyu, M., Sobue, G.
    • Journal Title

      Nat. Med. 11

      Pages: 1088-1095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration.2005

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Sang C, Tanaka F, Inukai A, Doyu M, Sobue G
    • Journal Title

      Nature Med 11

      Pages: 1088-1095

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease2005

    • Author(s)
      Katsuno, M., Sang, C., Adachi, H., Minamiyama, M., Waza, M., Tanaka, F., Doyu, M., Sobue, G.
    • Journal Title

      Proc. Natl. Acad. Sci. U.S.A. 102

      Pages: 16801-16806

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci USA 102

      Pages: 16801-16806

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration.2005

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Sang C, Tanaka F, Inukai A, Doyu M, Sobue G
    • Journal Title

      Nature Med 11

      Pages: 1088-1095

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Dorfin prevents cell death by reducing mitochondrial localizing mutant superoxide dismutase 1 in a neuronal cell model of familial amyotrophic lateral sclerosis.2004

    • Author(s)
      Takeuchi H, Niwa J, Hishikawa N, Ishigaki S, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurochem. 89

      Pages: 64-72

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Sodium butyrate ameliorates phenotypic expression in a transgenic mouse model of spinal and bulbar muscular atrophy.2004

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Waza M, Sang C, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Sobue G.
    • Journal Title

      Hum Mol Genet 13

      Pages: 1183-1192

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Dorfin prevents cell death by reducing mitochondrial localising mutant superoxide dismutase 1 in a neuronal cell model of familial amyotrophic lateral sclerosis.2004

    • Author(s)
      Takeuchi H, Niwa J, Hishikawa N, Ishigaki S, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurochem 89

      Pages: 64-72

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Sodium butyrate ameliorates phenotypic expression in a transgenic mouse model of spinal and bulbar muscular atrophy.2004

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Waza M, Sang C, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Sobue G
    • Journal Title

      Hum Mol Genet 13

      Pages: 1183-1192

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Sodium butyrate ameliorates phenotypic expression in a transgenic mouse model of spinal and bulbar muscular atrophy.2004

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Waza M, Sang C, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Sobue G
    • Journal Title

      Hum Mol Genet 13

      Pages: 1183-1192

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Dorfin localizes to the ubiquitilated inclusions in Parkinson's disease, dementia with Lewy bodies, multiple system atrophy, and amyotrophic lateral sclerosis.2003

    • Author(s)
      Hishikawa N, Niwa J, Doyu M, Ito T, Ishigaki S, Hashizume Y, Sobue G
    • Journal Title

      Am J Pathol 163(2)

      Pages: 609-619

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Caspase-1 and -3 are differentially upregulated in motor neurons and glial cells in mutant SOD1 transgenic mouse spinal cord : a study usign laser microdissection and real time RT-PCR.2003

    • Author(s)
      Ando Y, Liang Y, Ishigaki S, Niwa J, Jiang Y, Kobayashi Y, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Neurochem Res 28

      Pages: 839-846

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Dorfin localizes to Lewy bodies and ubiquitylates synphilin-1.2003

    • Author(s)
      Ito T, Niwa J, Hishikawa N, Ishigaki S, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 278(31)

      Pages: 29106-29114

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Leuprorelin rescue polyglutamine-dependent phenotypes in a transgenic mouse model of spinal and bulbar muscular atrophy.2003

    • Author(s)
      Katsuno M, Adachi H, Doyu M, Minamiyama M, Sang C, Kobayashi Y, Inukai A, Sobue G
    • Journal Title

      Nature Medicine 9(6)

      Pages: 768-773

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Heat shock protein 70 chaperone overexpression ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model by reducing nuclear-localized mutant androgen receptor protein.2003

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Sang C, Pagoulatous G, Angelidis C, Kusakabe M, Yoshiki A, Kobayashi Y, Doyu M, Sobue G
    • Journal Title

      J Neurosci 23(6)

      Pages: 2203-2211

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Gene expression profile in Alzheimer's brain screened by molecular indexing.2001

    • Author(s)
      Doyu M
    • Journal Title

      Brain Res, Mol Brain Res 87

      Pages: 1-11

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-12210010
  • [Journal Article] Gene expression profile in Alzheimer's brain screened by molecular indexing.2001

    • Author(s)
      Doyu M
    • Journal Title

      Mol Brain Res 87

      Pages: 1-11

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-12210010
  • [Presentation] 疾患iPS細胞による神経・筋共培養を活用した神経変性疾患の病態解析2020

    • Author(s)
      伊藤卓治, 小野寺一成, 小野寺一成, 下門大祐, 下門大祐, 田中智史, 田中智史, 岡田梨奈, RASHID Muhammad Irfanur, 道勇学, 岡野栄之, 岡田洋平
    • Organizer
      日本再生医療学会総会
    • Data Source
      KAKENHI-PROJECT-19K07969
  • [Presentation] Reconstruction of motor function in peripheral nerves by transplanatation of human iPSC-derived motor neuron progenitors.2019

    • Author(s)
      Niwa S, Saeki M, Shinkai H, Kurimoto S, Hirata H, Doyu M, Okada Y
    • Organizer
      ISSCR 2019 Annual Meeting, LosAngeles
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-19K07969
  • [Presentation] Pathophysiological analysis of spinal and bulbar muscular atrophy using disease-specific iPSCs.2019

    • Author(s)
      Onodera K, Shimojo D, Yoda M, Ishihara Y, Ito T, Okada R, Doyu M, Katsuno M, Okano H, Sobue G, Okada Y
    • Organizer
      第60回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-19K07969
  • [Presentation] Elucidation of non-cell autonomous neurodegeneration in spinal and bulbar muscular atrophy using iPSC-derived neuromuscular models.2019

    • Author(s)
      Ito T, Tanaka S, Shimojo D, Doyu M, Okano H, Okada Y
    • Organizer
      ISSCR 2019 Annual Meeting, LosAngeles
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-19K07969
  • [Presentation] The effects of hypoxia on differentiation and maturation of human induced pluripotent stem cell-derived neural progenitors.2019

    • Author(s)
      Okada Y, Okada R, Li J, Onodera K, Ito T, Okano HJ, Doyu M
    • Organizer
      ISSCR 2019 Annual Meeting, LosAngeles
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-19K07969
  • [Presentation] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno, H., Katsuno, M., Suzuki, K., Takeuchi, Y., Kawashima, M., Suga, N., Takamori, M., Ito, M., Nakamura, T., Matsuo, K., Yamada, S., Oki, Y., Adachi, H., Minamiyama, M., Waza, M., Atsuta, N., Watanabe, H., Fujimoto, Y., Nakashima, T., Tanaka, F., Doyu, M., Sobue, G.
    • Organizer
      61th American Academy of Neurology Annual Meeting
    • Place of Presentation
      Seattle, USA
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy.2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G.
    • Organizer
      61th American Academy of Neurology Annual Meeting
    • Place of Presentation
      Seattle, USA
    • Year and Date
      2009-04-26
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] 孤発性ALS疾患モデルの開発 : dynactin1ノックダウン細胞の解析2007

    • Author(s)
      田中章景、黄哲、蒋月梅、松尾幸治、和座雅浩、山本正彦、道勇学、祖父江元
    • Organizer
      第48回日本神経学会総会
    • Place of Presentation
      名古屋
    • Year and Date
      2007-05-16
    • Data Source
      KAKENHI-PROJECT-19390238
  • [Presentation] Gen expression profile of spinal motor neurons in sporadic amyotrophic lateral sclerosis2006

    • Author(s)
      Tanaka, F., Jiang, Y.M., Yamamoto, M., Huang, Z., Katsuno, M., Adachi, H., Niwa, J.I., Doyu, M., Sobue, G.
    • Organizer
      17th International Symposium on ALS/MND
    • Place of Presentation
      Yokohama, Japan
    • Data Source
      KAKENHI-PROJECT-17025020
  • 1.  SOBUE Gen (20148315)
    # of Collaborated Projects: 14 results
    # of Collaborated Products: 86 results
  • 2.  TANAKA Fumiaki (30378012)
    # of Collaborated Projects: 8 results
    # of Collaborated Products: 66 results
  • 3.  INUKAI Akira (30314016)
    # of Collaborated Projects: 6 results
    # of Collaborated Products: 3 results
  • 4.  KATSUNO Masahisa (50402566)
    # of Collaborated Projects: 3 results
    # of Collaborated Products: 39 results
  • 5.  ADACHI Hiroaki (40432257)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 10 results
  • 6.  IIJIMA Masahiro (40437041)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 7.  YAMAMOTO Masahiko (40378039)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 8.  服部 直樹 (10402570)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 1 results
  • 9.  柿崎 裕彦 (20329783)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 10.  中野 隆 (30148332)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 11.  高橋 靖弘 (70557206)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 12.  岡田 洋平 (30383714)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 7 results
  • 13.  伊藤 卓治 (30794151)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 1 results
  • 14.  若井 正一
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results

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