KOBAYASHI Masao 小林正夫

Researcher Number	00162016
Other IDs
Affiliation *help	2017 : 広島大学, 医歯薬保健学研究科(医), 教授 2014 – 2015 : 広島大学, 医歯薬保健学研究院(医), 教授 2015 : 広島大学, 医歯薬保健学研究院, 教授 2012 – 2013 : 広島大学, その他の研究科, 教授 2013 : 広島大学, 医歯薬保健学研究院, 教授 … More
Research Field	Principal Investigator Pediatrics Except Principal Investigator Pediatrics / Pediatrics / 環境影響評価(含放射線生物学) / 実験系心理学 / Tumor biology and related fields
Keywords	Principal Investigator 単球機能 / STAT1 / iPS細胞 / 原発性免疫不全症 / 食細胞 / 破骨細胞 Except Principal Investigator 異種間移植 / 先天性好中球減少症 / 免疫不全マウス / 異種移植 … More

iPS細胞を用いた先天性骨髄不全症候群からの白血病発症機序解明と新規治療法の開発Ongoing
- Principal Investigator
  
  望月慎史
- Project Period (FY)
  2017 – 2018
- Research Category
  
  Challenging Research (Exploratory)
- Research Field
  
  Tumor biology and related fields
- Research Institution
  Hiroshima University
Analysis of abnormal STAT1 disorders using disease-specific iPS cells.Principal Investigator
- Principal Investigator
  
  Kobayashi Masao
- Project Period (FY)
  2014 – 2015
- Research Category
  
  Grant-in-Aid for Challenging Exploratory Research
- Research Field
  
  Pediatrics
- Research Institution
  Hiroshima University
Gene editing of iPS cells derived from patients with congenital phagocytic disordersPrincipal Investigator
- Principal Investigator
  
  Kobayashi Masao
- Project Period (FY)
  2013 – 2015
- Research Category
  
  Grant-in-Aid for Scientific Research (B)
- Research Field
  
  Pediatrics
- Research Institution
  Hiroshima University
Application of humanized mice to analyses and therapeutics of phagocytic disordersPrincipal Investigator
- Principal Investigator
  
  KOBAYASHI Masao
- Project Period (FY)
  2010 – 2012
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  Hiroshima University
The cell-surface modification enhances the engraftment of human CD34-positive cells into immunodeficient micePrincipal Investigator
- Principal Investigator
  
  KOBAYASHI Masao
- Project Period (FY)
  2007 – 2008
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  Hiroshima University
Basic research for the establishment of the intra-bone marrow stem cell transplantation
- Principal Investigator
  
  SATO Takashi
- Project Period (FY)
  2004 – 2005
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  HIROSHIMA UNIVERSITY
Purification, expansion, and reconstitution of mesodermal stemcells from human bone marrowPrincipal Investigator
- Principal Investigator
  
  KOBAYASHI Masao
- Project Period (FY)
  2003 – 2004
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  HIROSHIMA UNIVERSITY
Neupsycological study for the development of cognitive and emotional qualia in infants.
- Principal Investigator
  
  TOSHIMA Tamotsu
- Project Period (FY)
  2002 – 2005
- Research Category
  
  Grant-in-Aid for Scientific Research (A)
- Research Field
  
  実験系心理学
- Research Institution
  HIROSHIMA UNIVERSITY
GENE EXPRESSIONS DURING PROLIFERATION AND DIFFERENTIATION OF MYELOID CELIS IN SEVERE CONCENITAL NEUTROPENIAPrincipal Investigator
- Principal Investigator
  
  KOBAYASHI Masao
- Project Period (FY)
  2001 – 2002
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  HIROSHIMA UNICERSITY
Identification of Human facilitating cells
- Principal Investigator
  
  SATO Takashi
- Project Period (FY)
  2001 – 2002
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  HIROSHIMA UNIVERSITY
EXPANSION OF HUMAN BONE MARROW CELLS CAPABLE OF REPOPULATING IN MICE BY COCULTURE WITH BONE MARROW STROMAL CELLSPrincipal Investigator
- Principal Investigator
  
  KOBAYASHI Masao
- Project Period (FY)
  1999 – 2000
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  HIROSHIMA UNIVERSITY
A study for a transcription factor gene regulating radiation sensitivity
- Principal Investigator
  
  KATOH Osamu
- Project Period (FY)
  1999 – 2000
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  環境影響評価(含放射線生物学)
- Research Institution
  HIROSHIMA UNIVERSITY
CHARACTERIZATION OF PURIFIED HUMAN HEMATOPOIETIC PROGENITOR CELLS OF BONE MARROW AND THEIR RECONSTITUTING ABILITY IN GENOGENEIC TRANSPLANTATIONPrincipal Investigator
- Principal Investigator
  
  KOBAYASHI Masao
- Project Period (FY)
  1997 – 1998
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  HIROSHIMA UNIVERSITY
小児急性リンパ性白血病の微少残存白血病の検出に関する研究
- Principal Investigator
  
  上田一博
- Project Period (FY)
  1993
- Research Category
  
  Grant-in-Aid for General Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  Hiroshima University
補体第7成分(C7)の分子遺伝学的研究
- Principal Investigator
  
  UEDA Kazuhiro
- Project Period (FY)
  1990
- Research Category
  
  Grant-in-Aid for General Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  Hiroshima University
顆粒球の機能的分化とロイコトリエン・リセプタ-、走代因子リセプタ-に関する研究
- Principal Investigator
  
  上田一博
- Project Period (FY)
  1989
- Research Category
  
  Grant-in-Aid for General Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  Hiroshima University
小児悪性腫瘍細胞における癌遺伝子の形質発現に関する研究
- Principal Investigator
  
  田中丈夫
- Project Period (FY)
  1986
- Research Category
  
  Grant-in-Aid for General Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  Hiroshima University

[Book] 今日の小児治療指針「好中球減少症」2011
- Author(s)
  小林正夫
- Total Pages
  2
- Publisher
  医学書院
- Data Source
  KAKENHI-PROJECT-22591161
[Book] 好中球減少症2011
- Author(s)
  小林正夫
- Publisher
  医学書院
- Data Source
  KAKENHI-PROJECT-22591161
[Book] 骨髄不全症候群とリボゾームの異常2010
- Author(s)
  岡田賢, 小林正夫
- Total Pages
  9
- Publisher
  中外医学社
- Data Source
  KAKENHI-PROJECT-22591161
[Book] Annual Review 20102010
- Author(s)
  岡田賢,小林正夫
- Publisher
  中外医学社
- Data Source
  KAKENHI-PROJECT-22591161
[Book] Annual Review 血液 20082008
- Author(s)
  小林正夫, 岡田賢, 三木瑞香
- Publisher
  中外医学社, 東京
- Data Source
  KAKENHI-PROJECT-19591250
[Book] Annual Review血液20082008
- Author(s)
  小林正夫, 岡田賢, 三木瑞香
- Publisher
  中外医学社,東京
- Data Source
  KAKENHI-PROJECT-19591250
[Book] 先天性好中球減少症の成因(Annual Review)2008
- Author(s)
  小林正夫, 岡田賢, 三木瑞香
- Publisher
  中外医学社東京
- Data Source
  KAKENHI-PROJECT-19591250
[Book] 血小板及び顆粒球抗原・抗体の臨床と技術2005
- Author(s)
  佐藤貴, 小林正夫, 平岡朝子
- Total Pages
  200
- Publisher
  日本血小板・顆粒球型ワークショップ
- Data Source
  KAKENHI-PROJECT-16591031
[Book] Annual Review 血液 20052005
- Author(s)
  川口浩史, 中村和洋, 小林正夫
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] Monogenic mutations differentially affect the quantity and quality of T follicular helper cells in patients with human primary immunodeficiencies.2016
- Author(s)
  Ma CS, Wong N, Tangye SG, et al.
- Journal Title
  
  J Allergy Clin Immunol
  
  Volume : 136 Pages : 993-1006
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-26293250, KAKENHI-PROJECT-15K15396, KAKENHI-PROJECT-15K15392, KAKENHI-PROJECT-26670501, KAKENHI-PROJECT-25293231, KAKENHI-PROJECT-25293232, KAKENHI-PROJECT-25713039
[Journal Article] Impairment of IL-17A/F immunity to Candida and IFN-γ immunity to Mycobacterium in humans with inherited RORγT deficiency.2015
- Author(s)
  Okada S, Markle JG, Deenick EK, Federico Mele F, Averbuch D, Kobayashi M, Abel L, Cooper AM, Notarangelo LD, Boisson-Dupuis S, Puel A, Sallusto F, Bustamante J, Tangye SG, Casanova JL
- Journal Title
  
  Science
  
  Volume : 349 Pages : 606-613
- Peer Reviewed / Open Access / Acknowledgement Compliant / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-26670501, KAKENHI-PROJECT-25293231, KAKENHI-PROJECT-25713039
[Journal Article] STAT3 is a critical cell intrinsic regulator of human unconventional T cell numbers and function.2015
- Author(s)
  Wilson RP, Ives ML, Rao G, Lau A, Payne K, Kobayashi M, Holland SM, Casanova JL, Uzel G, Ma CS, Tangye SG, Deenick EK
- Journal Title
  
  Journal of Experimental Medicine
  
  Volume : 212 Pages : 855-864
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-26670501, KAKENHI-PROJECT-25293231
[Journal Article] Paroxysmal nocturnal hemoglobinuria and telomere length predicts response to immunosuppressive therapy in pediatric aplastic anemia.2015
- Author(s)
  Narita A, Muramatsu H, Sekiya Y, Okuno Y, Sakaguchi H, Nishio N, Yoshida N, Wang X, Xu Y, Kawashima N, Doisaki S, Hama A, Takahashi Y, Kudo K, Moritake H, Kobayashi M, Kobayashi R, Ito E, Yabe H, Ohga S, Ohara A, Kojima S; Japan Childhood Aplastic Anemia Study Group.
- Journal Title
  
  Haematologica.
  
  Volume : 100 Pages : 1546-1552
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-15K09647, KAKENHI-PROJECT-26670501, KAKENHI-PROJECT-25293231
[Journal Article] Mosaicism of an ELANE mutation in an asymptomatic mother in a familial case of cyclic neutropenia.2015
- Author(s)
  Hirata O, Matsumura I, Kobayashi M,et al.
- Journal Title
  
  J Clin Immunol.
  
  Volume : 35 Pages : 512-516
- Peer Reviewed / Open Access / Acknowledgement Compliant
- Data Source
  KAKENHI-PROJECT-15K09461, KAKENHI-PROJECT-15K21189, KAKENHI-PROJECT-26670501, KAKENHI-PROJECT-25293231, KAKENHI-PROJECT-25713039
[Journal Article] he International Immune Tolerance Induction Study and its follow-up study on Japanese hemophilia A patients with inhibitors2015
- Author(s)
  Yoshioka A, Ishii E, Ueno T, Usami I, Kobayashi M, Kobayashi R, Sotomatsu M, Shirahata A, Suzuki T, Taki M, Ishida Y, Matsushita T, Shima M, Nogami K, Sakai M,Kigasawa H, Hukutake K
- Journal Title
  
  International Journal of Hematology
  
  Volume : 101 Pages : 362-368
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-26670501, KAKENHI-PROJECT-25461445
[Journal Article] Simple diagnosis of STAT1 gain-of-function alleles in patients with chronic mucocutaneous candidiasis.2014
- Author(s)
  Mizoguchi Y, Tsumura M, Okada S, Hirata O, Minegishi S, Imai K, Hyakuna N, Muramatsu H, Kojima S, Ozaki Y, Imai T, Takeda S, Okazaki T, Ito T, Yasunaga S, Takihara Y, Bryant VL, Kong XF, Cypowyj S, Boisson-Dupuis S, Puel A, Casanova JL, Morio T, Kobayashi M.
- Journal Title
  
  J. Leukoc. Biol.
  
  Volume : 95 Pages : 667-76
- Peer Reviewed / Open Access / Acknowledgement Compliant
- Data Source
  KAKENHI-PROJECT-23390270, KAKENHI-PROJECT-25293231, KAKENHI-PROJECT-25293232, KAKENHI-PROJECT-25713039, KAKENHI-PROJECT-25870468, KAKENHI-PROJECT-26501004, KAKENHI-PROJECT-26670501, KAKENHI-PROJECT-26670502
[Journal Article] Simple diagnosis of STAT1 gain-of-function alleles in patients with chronic mucocutaneous candidiasis.2014
- Author(s)
  Mizoguchi Y., Tsumura M., Okada S., Hirata O., Minegishi S., Imai K., Hyakuna N., Muramatsu H.,. Kojima S., Ozaki Y., Imai T., Takeda S., Okazaki T., Ito T, Yasunaga S., Takihara Y., Bryant V.L., Kong X.F., Cypowyj S., Boisson-Dupuis S., Puel A., Casanova J.L., Morio T. & Kobayashi M.
- Journal Title
  
  J. Leukoc. Biol.
  
  Volume : 95(4) Pages : 667-676
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-23618008, KAKENHI-PUBLICLY-25118717, KAKENHI-PUBLICLY-25130708, KAKENHI-PROJECT-25293231
[Journal Article] A 2-year-old Japanese girl with TNF receptor-associated periodic syndrome: A case report of the youngest diagnosed proband in Japan.2014
- Author(s)
  Yasumura J, Wago M, Okada S, Nishikomori R, Takei S, Kobayashi M
- Journal Title
  
  Modern Rheumatology
  
  Volume : 20 Pages : 1-4
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-25293231
[Journal Article] Genetic correction of HAX1 in induced pluripotent stem cells from a patient with severe congenital neutropenia improves defective granulopoiesis2014
- Author(s)
  Morishima T, Watanabe K, Niwa A, Hirai H, Saida S, Tanaka T, Kato I, Umeda K, Hiramatsu H, Saito M, Matsubara K, Adachi S, Kobayashi M, Nakahata T, Heike T
- Journal Title
  
  Haematologica
  
  Volume : 99 Pages : 19-27
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-25293231
[Journal Article] A 2-year-old Japanese girl with TNF receptor-associated periodic syndrome: A case report of the youngest diagnosed proband in Japan2014
- Author(s)
  Yasumura J, Wago M, Okada S, Nishikomori R, Takei S, Kobayashi M
- Journal Title
  
  Modern Rheumatology
  
  Volume : 20 Pages : 1-4
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-26670501
[Journal Article] Detection of Mucor velutinosus in a blood culture after autologous peripheral blood stem cell transplantation: a pediatric case report.2014
- Author(s)
  Joichi Y, Chijimatsu I, Yarita K, Kamei K, Miki M, Onodera M, Harada M, Yokozaki M, Kobayashi M, Ohge H
- Journal Title
  
  Medical Mycology Journal
  
  Volume : 55
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-25293231, KAKENHI-PROJECT-26670501
[Journal Article] HAX1 in induced pluripotent stem cells from a patient with severe congenital neutropenia improves defective granulopoiesis.2014
- Author(s)
  Morishima T, Watanabe K, Niwa A, Hirai H, Saida S, Tanaka T, Kato I, Umeda K, Hiramatsu H, Saito MK, Matsubara K, Adachi S, Kobayashi M, Nakahata T, Heike T
- Journal Title
  
  Haematologica
  
  Volume : 99(1) Pages : 19-27
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-24390244, KAKENHI-PROJECT-24659461, KAKENHI-PROJECT-24659496, KAKENHI-PROJECT-25293231, KAKENHI-PROJECT-25430149, KAKENHI-PROJECT-25461415, KAKENHI-PROJECT-25461591, KAKENHI-PROJECT-26670498, KAKENHI-PROJECT-26670501, KAKENHI-PROJECT-24591548
[Journal Article] Identification of the integrin β3 L718P mutation in a pedigree with autosomal dominant thrombocytopenia with anisocytosis.2013
- Author(s)
  Kobayashi Y, Matsui H, Kanai A, Tsumura M, Okada S, Miki M, Nakamura K, Kunishima S, Inaba T, Kobayashi M
- Journal Title
  
  British Journal of Haematology
  
  Volume : 160 Pages : 521-529
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-25293231, KAKENHI-PROJECT-22591161
[Journal Article] Wnt3a stimulates maturation of impaired neutrophils developed from severe congenital neutropenia-derived pluipotent stem cells with heterozygous ELANE mutation.2013
- Author(s)
  Hiramoto T
- Journal Title
  
  Proc Natl Acad Sci USA
  
  Volume : 110 Pages : 3023-3028
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161, KAKENHI-PROJECT-25293231
[Journal Article] Naïve and memory human B cells have distinct requirements for STAT3 activation to differentiate into antibody-secreting plasma cells.2013
- Author(s)
  Deenick EK, Avery DT, Chan A, Berglud LJ, Ives ML, Bustamante J, Boisson-Dupuis S, Tsumura M, Kobayashi M, Arkwright PD, Averbuch D, Engelhard D, Roesler J, Peake J, Wong M, Adelstein S, Choo S, Smart JM, French MA, Fulcher DA, Cook MC, Picard C, Durandy A, Klein C, Holland SM, Uzel G, Casanova JL, Ma CS, Tangye SG
- Journal Title
  
  Journal of Experimental Medicine
  
  Volume : 210 Pages : 2739-2753
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-25293231
[Journal Article] Heterozygosity for the Y701C STAT1 mutation in a multiplex kindred with multifocal osteomyelitis.2013
- Author(s)
  Hirata O, Okada S, Tsumura M, Kagawa R, Miki M, Kawaguchi H, Nakamura K, Boisson-Dupuis S, Casanova JL, Takihara Y, Kobayashi M
- Journal Title
  
  Haematologica
  
  Volume : 98 Pages : 1641-1649
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-25293231
[Journal Article] : IL-21 signalling via STAT3 primes human naïve B cells to respond to IL-2 to enhance their differentiation into plasmablasts.2013
- Author(s)
  Berglund LJ, Ma CS, Avery DT, Moens L, Deenick EK, Bustamante J, Boisson-Dupuis S, Wong M, Adelstein S, Arkwright PD,Fulcher DA, Ziegler JB, Smart JM, Kobayashi M, Casanova JL, Cook MC, Uzel G, Tangye SG
- Journal Title
  
  Blood
  
  Volume : 122 Pages : 3940-3950
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-25293231
[Journal Article] Signal transducer and activator of transcription 3 (STAT3) mutations underlying autosomal dominant hyper-IgE syndrome impair human CD8(+) T-cell memory formation and function.2013
- Author(s)
  Ives ML, Ma CS, Palendira U,Chan A, Bustamante J, Boisson-Dupuis S, Arkwright PD, Engelhard D, Averbuch D, Magdorf K, Roesler J, Peake J, Wong M, Adelstein S, Choo S, Smart JM, Frnch MA, Fulcher DA, Cook MC, Picard C, Durandy A, Tsumura M, Kobayashi M, Uzel G, Casanova JL, Tangye SG, Deenick EK
- Journal Title
  
  Journal of Allergy and Clinical Immunology
  
  Volume : 132 Pages : 400-411
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-25293231
[Journal Article] Identification of the integrin b3 L718P mutation in a pedigree with autosomal dominant thrombocytopenia with anisocytosis2013
- Author(s)
  Kobayashi Y, Matsui H, Kanai A, Tsumura M, Okada S, Miki M, Nakamura K, Kunishima S, Inaba T, Kobayashi M
- Journal Title
  
  British Journal of Haematology
  
  Volume : 160 Pages : 521-529
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Wnt3a stimulates maturation of impaired neutrophils developed from severe congenital neutropenia-derived pluipotent stem cells with heterozygous ELANEmutation2013
- Author(s)
  Hiramoto T, Ebihara Y, Mizoguchi Y, Nakamura K, Yamaguchi K, Ueno K, Mochizuki S, Yamamoto S, Nagasaki M, Furukawa Y, Tani K, Nakauchi H, Kobayashi M, Tsuji K
- Journal Title
  
  Proc Natl Acad Sci USA
  
  Volume : 110 Pages : 3023-8
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Glanzmann thrombasthenia (GT) の遺伝子組み換え活性型第Glanzmann thrombasthenia (GT) の遺伝子組み換え活性型第VII因子製剤による止血効果因子製剤による止血効果2012
- Author(s)
  溝口洋子,鎌田綾,三木瑞香,谷博雄,世羅康彦,中村和洋,小林正夫
- Journal Title
  
  日本小児血液・がん学会雑誌
  
  Volume : 49 Pages : 61-66
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Regulation of hematopoietic stem cells using transduction domain-fused polycomb2012
- Author(s)
  Kajiume T, Sera Y, Kawahara Y, Matsumoto M, Fukazawa T, Imura T, Yuge L, Kobayashi M
- Journal Title
  
  Experimantal Hematology
  
  Volume : 40 Pages : 751-760
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Frequent somatic mosaicism of NEMO in T cells of patients with X-linked anhidrotic ectodermal dysplasia and immunodeficiency2012
- Author(s)
  Kawai T, Nishikomori R, Izawa K, Murata Y, Tanaka N, Sakai H, Saito M, Yasumi T, Takaoka Y, Nakahata T, Mizukami T, Nunoi H, Kiyohara Y, Yoden A, Murata T, Sasaki S, Ito E, Akutagawa H, Kawai T, Imai C, Okada S, Kobayashi M, Heike T
- Journal Title
  
  Blood
  
  Volume : 119 Pages : 5458-5466
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Dominant-negative STAT1 SH2 domain mutations in unrelated patients with Mendelian susceptibility to mycobacterial disease2012
- Author(s)
  Tsumura M, Okada S, Sakai H, Yasunaga S, Ohtsubo M, Murata T, Obata H, Yasumi T, Kong XF, Abhyankar A, Heike T, Nakahata T, Nishikomori R, Al-Muhsen S, Boisson-Dupuis S, Casanova JL, Alzahrani M, Shehri MA, Elghazali G, Takihara Y, Kobayashi M
- Journal Title
  
  Human Mutation
  
  Volume : 33 Pages : 1377-1387
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Transmission of a maternal EDTA-dependent anticoagulant.2012
- Author(s)
  Ohno N, Kobayashi M, Hayakawa S, Utsunomiya A, Karakawa
- Journal Title
  
  Platelets
  
  Volume : 23 Pages : 399-400
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Oncogenic fusion E2A-HLF sensitizes t(17:19)-positive acute lymphoblastic leukemia to TRAIL-mediated apoptosis by upregulating the expression of death receptors2012
- Author(s)
  Zhang X, Inukai T, Hirose K, Akahane K, Kuroda I, Honna-Oshiro H, Kagami K, Goi K, Nakamura K, Kobayashi M, Endo M, Yagita H, Kurosawa H, Look TA, Honda H, Inaba T, Nakazawa S, Sugita K
- Journal Title
  
  Leukemia
  
  Volume : 26 Pages : 2843-93
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] 慢性皮膚粘膜カンジダ症と機能獲得性STAT1 変異2012
- Author(s)
  溝口洋子,津村弥来,岡田賢,小林正夫
- Journal Title
  
  臨床免疫・アレルギー科
  
  Volume : 57 Pages : 437-443
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] 輸血後蕁麻疹発症前の末梢血一般検査所見2012
- Author(s)
  梶梅輝之,浅野孝基,世羅康彦,小林正夫
- Journal Title
  
  アレルギー
  
  Volume : 61 Pages : 1086-1091
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Quantification of k-deleting recombination excision in Guthrie cards for identi fication of early B-cell maturation defects2011
- Author(s)
  Nakagawa K, Kobayashi M, et al
- Journal Title
  
  Journal of Allergy & Clinical Immunology
  
  Volume : 128 Pages : 223-225
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Gain of function of human STAT1 mutations impair IL17 immunity and undelie chronic mucocutaneous candidiasis2011
- Author(s)
  Liu L, Kobayashi M, et al
- Journal Title
  
  Journal of Experimental Medicine
  
  Volume : 208 Pages : 1635-1648
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Decreased expression in nuclear factor-kB essential modulator due to a novel-site mutation causes X-linked ectordermal dysplasia with immunodeficiency2011
- Author(s)
  Karakawa S, Kobayashi M, et al
- Journal Title
  
  Journal of Clinical Immunology
  
  Volume : 31 Pages : 762-772
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Clinical and host genetic characteristics of Mendelian susceptibility to mycobacterial diseases in Japan2011
- Author(s)
  Hoshina T, Kobayashi M, et al
- Journal Title
  
  Journal of Clinical Immunology
  
  Volume : 31 Pages : 309-314
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Quantification of κ-deleting recombination excision circles in Guthrie cards for the identification of early B-cell maturation defects2011
- Author(s)
  Nakagawa N, Imai K, Kanegane H, Sato H, Yamada M, Kondoh K, Okada S, Kobayashi M, Agematsu K, Takada H, Mitsuiki N, Oshima K, Ohara O, Suri D, Rawat A, Singh S, Pan-Hammarstrom Q, Hammarstrom L, Reichenbach J, Seger R, Ariga T, Hara T, Miyawaki T, Nonoyama S
- Journal Title
  
  Journal of Allergy & Clinical Immunology
  
  Volume : 128 Pages : 223-225
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Clinical and host genetic characteristics of Mendelian susceptibility to mycobacterial diseases in Japan2011
- Author(s)
  Hoshina T, Takada H, Sasaki-Mihara Y, Kusuhara K, Ohshima K, Okada S, Kobayashi M, Ohara O, Hara T
- Journal Title
  
  Journal of Clinical Immunology
  
  Volume : 31 Pages : 309-14
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Gain of function of human STAT1 mutations impair IL17 immunity and underlie chronic mucocutaneous candidiasis2011
- Author(s)
  Liu L, Okada S, Kong XF, Kreins AY, Cypowyj S, Abhyankar A, Toubiana J, Itan Y, Audry M, Nitschke P, Masson C, Toth B, Flatot J, Migaud M, Chrabieh M, Kochetkov T, Bolze A, Borghesi A, Toulon A, Hiller J, Eyerich S, Eyerich K, Gulacsy V, Chernyshova L, Chernyshov V, Bondarenko A, Maria Cortes Grimaldo R, Blancas-Galicia L, Madrigal Beas IM, Roesler J, Magdorf K, Engelhard D, Thumerelle C, Burgel PR, Hoernes M, Drexel B, Seger R, Kusuma T, Jansson AF, Sawalle-Belohradsky J, Belohradsky B, Jouanguy E, Bustamante J, Bue M, Karin N, Wildbaum G, Bodemer C, Lortholary O, Fischer A, Blanche S, Al-Muhsen S, Reichenbach J, Kobayashi M, Rosales FE, Lozano CT, Kilic SS, Oleastro M, Etzioni A, Traidl-Hoffmann C, Renner ED, Abel L, Picard C, Marodi L, Boisson-Dupuis S, Puel A, Casanova JL
- Journal Title
  
  Journal of Experimental Medicine
  
  Volume : 208 Pages : 1635-48
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Decreased Expression in Nuclear Factor-κB Essential Modulator Due to a Novel Splice-Site Mutation Causes X-linked Ectodermal Dysplasia with Immunodeficiency2011
- Author(s)
  Karakawa S, Okada S, Tsumura M, Mizoguchi Y, Ohno N, Yasunaga S, Ohtsubo M, Kawai T, Nishikomori R, Sakaguchi T, Takihara Y, Kobayashi M
- Journal Title
  
  Journal of Clinical Immunology
  
  Volume : 31 Pages : 762-77
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] 血液疾患における病態解析研究の進歩:先天性好中球減少症発症機構解明の進展2010
- Author(s)
  溝口洋子, 岡田賢, 小林正夫
- Journal Title
  
  血液・腫瘍科
  
  Volume : 127 Pages : 118-628
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Maternal breast milk odour induces frontal lobe activation in neonates.2010
- Author(s)
  Aoyama S, Kobayashi M, et al.
- Journal Title
  
  Early Human Development
  
  Volume : 86 Pages : 541-545
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] 好中球減少症2010
- Author(s)
  溝口洋子, 小林正夫
- Journal Title
  
  小児科
  
  Volume : 51 Pages : 985-994
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Significance of immature platelet fraction and CD-41-positive cells at birth in early onset neonatal thrombocytopenia.2010
- Author(s)
  Kihara H, Kobayashi M, et al.
- Journal Title
  
  International Journal of Hematology
  
  Volume : 91 Pages : 245-251
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Molecular pathogenesis of a novel mutation, G108D, in short-chain acyl-CoA dehydrogenase identified in subjects with short-chain acyl-CoA dehydrogenase deficiency.2010
- Author(s)
  Shirao K, Kobayashi M, et al.
- Journal Title
  
  Human Genetics
  
  Volume : 127 Pages : 619-628
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Hoxb4 transduction down-regulates Geminin protein, providing hematopoietic stem and progenitor cells with proliferation potential.2010
- Author(s)
  Ohno Y, Kobayashi M, et al.
- Journal Title
  
  Proc Natl Acad Sci USA
  
  Volume : 107 Pages : 21529-21534
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Molecular pathogenesis of a novel mutation, G108D, in short-chain acyl-CoA dehydrogenase identified in subjects with short-chain acyl-CoA dehydrogenase deficiency2010
- Author(s)
  Shirao K, Okada S, Tajima G, Tsumura M, Hara K, Yasunaga S, Ohtsubo M, Hata I, Sakura N, Shigematsu Y, Takihara Y, Kobayashi M
- Journal Title
  
  Human Genetics
  
  Volume : 127 Pages : 619-28
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Significance of immature platelet fraction and CD-41-positive cells at birth in early onset neonatal thrombocytopenia2010
- Author(s)
  Kihara H, Ohno N, Karakawa W, Mizoguchi Y, Fukuhara R, Hayashidani M, Nomura S, Nakamura K, Kobayashi M
- Journal Title
  
  International Journal of Hematology
  
  Volume : 91 Pages : 245-251
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Hoxb4 transduction down-regulates Geminin protein, providing hematopoietic stem and progenitor cells with proliferation potential2010
- Author(s)
  Ohno Y, Yasunaga S, Ohtsubo M, Ori S, Tsumura M, Okada S, Ohta T, Kiyoshi Ohtani, Kobayashi M, Takihara Y
- Journal Title
  
  Proc. Natl. Acad. Sci
  
  Volume : 107(50) Pages : 21529-34
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Hematological malignancies in congenital neutropenia2010
- Author(s)
  Okada S, Nakamura K, Kobayashi M
- Journal Title
  
  Rinsho Ketsueki
  
  Volume : 51 Pages : 553-558
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] 血液疾患における病態解析研究の進歩:先天性好中球減少症発症機構解明の進展2010
- Author(s)
  溝口洋子,岡田賢,小林正夫
- Journal Title
  
  血液・腫瘍科
  
  Volume : 60(2) Pages : 118-124
- Data Source
  KAKENHI-PROJECT-22591161
[Journal Article] Ela2 mutations and clinical manifestations in familial congenital neutropenia2009
- Author(s)
  Shiohara M, Shigemura T, Saito S, Tanaka M, Yanagisawa R, Sakashita K, Asada H, Ishii E, Koike K, Chin M, Kobayashi M, Koike K
- Journal Title
  
  Journal of Pediatric Hematology Oncology 31
  
  Pages : 319-324
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] 重症先天性好中球減少症の分子病態2009
- Author(s)
  小林正夫 ,岡田賢 ,溝口洋子
- Journal Title
  
  分子細胞治療 8
  
  Pages : 110-116
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Short-term culture of umbilical cord blood-derived CD34^+ cells enhances the engraftment into NOD/SCID mice through the increased expression of CXCR42009
- Author(s)
  Ohno N, Kajiume T, Sera Y, Sato T, Kobayashi M
- Journal Title
  
  Stem Cells & Developments (in press)
  
  Pages : 0-0
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Respiratory complications after haematopoietic stem cell transplantation in a patient with chronic granulomatous disease2009
- Author(s)
  Hara K, Kajiume T, Kondo T, Sera Y, Kawaguchi H, Kobayashi M
- Journal Title
  
  Journal of Transfusion Medicine (in press)
  
  Pages : 0-0
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Cardiac infiltration in Early-Onset Sarcoidosis Associated with a Novel Heterozygous Mutation, G481D, in CARD152009
- Author(s)
  Okada S, Konishi N, Tsumura M, Shirao K, Yasunga S, Sakai H, Nishikomori R, Takihara Y, Kobayashi M
- Journal Title
  
  Rheumatology (in press)
  
  Pages : 1093-1094
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Deficiency of regulatory T cells in children with autoimmune neutropenia2009
- Author(s)
  Nakamura K, Miki M, Karakawa S, Sato T, Kobayashi M
- Journal Title
  
  British Journal of Haematology (in press)
  
  Pages : 0-0
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Reciprocal expression of Bmi1 and Mel-18 is associated with the functioning of primitive hematopoietic cells2009
- Author(s)
  Kajiume T, Ohno N, Sera Y, Kawahara Y, Yuge L, Kobayashi M
- Journal Title
  
  Experimental Hematology (in press)
  
  Pages : 0-0
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Neurodevelopmental abnormalities associated with severe congenital neutropenia due to the R86X mutation in the HAX1 gene.2008
- Author(s)
  Ishikawa N, Okada s, Miki M, Takihara Y, Kobayashi M, et al
- Journal Title
  
  Journal of Medical Genetics 45
  
  Pages : 802-807
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Short-term culture of umbilical cord blood-derived CD34^+ cells enhances the engraftment into NOD/SCID mice through the increased expression of CXCR4.2008
- Author(s)
  Ohno N, Kajiume T, Sera Y, Satoh T, Kobayashi M
- Journal Title
  
  Stem Cells & Development (Epub ahead of print)
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Polycomb-group complex 1 acts as an E3 ubiquitin ligase for Geminin to sustain hematopoietic stem cell activity.2008
- Author(s)
  Ohtsubo M, Yasunaga s, Ohno Y, Kobayashi M, Takihara Y, et al.
- Journal Title
  
  Proc. Natl. Acad. Sci. USA 105
  
  Pages : 10396-10401
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Polycomb-group complex 1 acts as an E3 ubiquitin ligase for Geminin to sustain hematopoietic stem cell activity2008
- Author(s)
  Ohtsubo M, Yasunaga S, Ohno Y, Tsumura M, Okada S, Ishikawa N, Shirao K, Kikuchi A, Nishitani H, Kobayashi M, Takihara Y
- Journal Title
  
  Proc. Natl. Acad. Sci. USA 105(30)
  
  Pages : 10396-10401
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] The mobility of Bach2 nuclear foci is regulated by SUMO-1 modification2008
- Author(s)
  Kono K, Harano Y, Hoshino H, Kobayashi M, Bazett-Jones DP, Muto A, Igarashi K, Tashiro S
- Journal Title
  
  Experimental Cell Research 314(4)
  
  Pages : 903-13
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] 好中球異常症2008
- Author(s)
  小林正夫, 世羅康彦, 岡田賢
- Journal Title
  
  アレルギー・免疫 15
  
  Pages : 1350-1360
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] 非結核性抗酸菌による多発性骨髄炎を呈したインターフェロンγ受容体1 異常症の2例2008
- Author(s)
  岡田賢, 末永麻由美, 川口浩史, 小林正夫
- Journal Title
  
  日本小児科学会雑誌 112
  
  Pages : 1818-1825
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Development of a new enzymatic diagnosis method for very-long-chain acyl-CoA dehydrogenase deficiency by detecting 2-hexadecenoyl-CoA production and its application in tandem mass spectrometry-based selective screening and newborn screening in Japan2008
- Author(s)
  Tajima G, Sakura N, Shirao K, Okada S, Tsumura M, Nishimura Y, Ono H, Hata I, Naito E, Yamaguchi S, Shigematsu Y, Kobayashi M
- Journal Title
  
  Pediatric Research 64
  
  Pages : 667-672
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Neurodevelopmental abnormalities associated with severe congenital neutropenia due to the R86X mutation in the HAX1 gene2008
- Author(s)
  Ishikawa N, Okada S, Miki M, Shirao K, Kihara H, Tsumura M, Nakamura K, Kawaguchi H, Ohtsubo M, Yasunaga S, Matsubara K, Sako M, Hara J, Shiohara M, Kojima S, Sato T, Takihara Y, Kobayashi M
- Journal Title
  
  Journal of Medical Genetics 45(12)
  
  Pages : 802-807
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] 好中球異常による先天性免疫不全症2008
- Author(s)
  岡田賢, 津村弥来, 小林正夫
- Journal Title
  
  小児科臨床 61
  
  Pages : 1791-1796
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Severe developmental delay and epilepsy in a Japanese patient with severe congenital neutropenia due to HAX1 deficiency.2007
- Author(s)
  Matsubara K, Imai K, Okada S, Kobayashi M, et. al.
- Journal Title
  
  Haematologica 92
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] The novel IFNGR1 mutation 774del4 produces a truncated form of interferon-γ receptor 1 and has a dominant-negative effect on interferon-γ signal transduction.2007
- Author(s)
  Okada S, Ishikawa N, Kobayashi M, et. al.
- Journal Title
  
  Journal of Human Genetics 44
  
  Pages : 485-491
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Floating culture promotes the maintenance of hematopoietic stem cells.2007
- Author(s)
  Kajiume T, Yuge L, Kawahara Y, Kobayashi M, et. al.
- Journal Title
  
  FEBS Letters 581
  
  Pages : 4645-4650
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19591250
[Journal Article] Cyclic neutropenia2005
- Author(s)
  Kawaguchi H, Nakamura K, Kobayashi M
- Journal Title
  
  Hematology Frontier 15
  
  Pages : 69-75
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] Neutropenia in childhood.2005
- Author(s)
  Kobayashi M
- Journal Title
  
  Japanese Journal of the Japan Pediatric Society 109
  
  Pages : 614-622
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] Acomparison of the defective granulopoiesis in childhood cyclicneutropenia and in severe congenital neuropenia2005
- Author(s)
  Sera, Y., Kawaguchi, H., Nakamura, K., Sato, T., Habara, M., Okada, S., Ihikawa, N., Katoh, O., Kobayashi, M.
- Journal Title
  
  The hematology Journal 908・90
  
  Pages : 1032-1047
- Data Source
  KAKENHI-PROJECT-14201012
[Journal Article] 小児好中球減少症.2005
- Author(s)
  小林正夫
- Journal Title
  
  日本小児科学会雑誌 109・5
  
  Pages : 614-622
- Data Source
  KAKENHI-PROJECT-14201012
[Journal Article] Congenital neutropenia in infants.2005
- Author(s)
  Kobayashi, M.
- Journal Title
  
  The Journal of the Japan Pediatiric Society 109,5
  
  Pages : 614-622
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-14201012
[Journal Article] Acomparison of the defective granulopoiesis in childhood cyclicneutropenia and in severe congenital neuropenia.2005
- Author(s)
  Sera, Y., Kawaguchi, H., Nakamura, K., Sato, T., Habara, M., Okada, S., Ihikawa, N., Katoh.O., Kobayashi, M.
- Journal Title
  
  The hematology Journal 908. 90
  
  Pages : 1032-1047
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-14201012
[Journal Article] 周期性好中球減少症2005
- Author(s)
  川口浩史, 中村和洋, 小林正夫
- Journal Title
  
  血液フロンティア 15
  
  Pages : 69-75
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] 小児好中球減少症2005
- Author(s)
  小林正夫
- Journal Title
  
  日本小児科学会雑誌 109
  
  Pages : 614-622
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] 周期性好中球減少症2005
- Author(s)
  川口浩史, 中村和洋, 小林正夫
- Journal Title
  
  血液フロンティア 15
  
  Pages : 69-76
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] Acomperison of the defective granulopoiesis in childood cyclicneutropenia and in severe congenital neuropenia2005
- Author(s)
  Sera, Y., Kawaguchi, H., Nakamura, K., Sato, T., Habara, M., Okaba, S., Ihikawa, N., Katoh.O, Kobayashi,M.
- Journal Title
  
  The hematology Journal 908・90
  
  Pages : 1032-1047
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-14201012
[Journal Article] 小児好中球減少症.2005
- Author(s)
  小林正夫
- Journal Title
  
  日本小児科学会雑誌 109・5
  
  Pages : 614-622
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-14201012
[Journal Article] Significance of human neutrophil antigen-2a (NB1) expression and neutrophil number in pregnancy.2004
- Author(s)
  Taniguchi K, Nagata H, Katsuki I, Nakashima C, Onodera R, Hiraoka A, Takata N, Kobayashi M, Kambe M
- Journal Title
  
  Transfusion 44
  
  Pages : 581-585
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] Significance of human neutrophil antigen-2a (NB1) expression and neutrophil number in pregnancy.2004
- Author(s)
  Taniguchi K, Kobayashi M, et al.
- Journal Title
  
  Transfusion 44
  
  Pages : 581-585
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] G-CSF製剤,Epo製剤,M-CSF製剤2004
- Author(s)
  小林正夫, 佐藤貴, 上田一博
- Journal Title
  
  小児科診療 67
  
  Pages : 570-576
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] Dysregulation of transcriptions in primary granule constituents during myeloid proliferation and differentiation in patients with severe congenital neutropenia.2003
- Author(s)
  Kawaguchi H, Kobayashi M, Nakamura N, Konishi N, Miyagawa S, Sato T, Toyota H, Komada Y, Kojima S, Todoroki Y, Ueda K, Katoh O
- Journal Title
  
  Journal of Leukocyte Biology 73
  
  Pages : 225-234
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] Dysregulation of transcriptions in primary granule constituents during myeloid proliferation and differentiation in patients with severe congenital neutropenia.2003
- Author(s)
  Kawaguchi H, Kobayashi M, et al.
- Journal Title
  
  Journal of Leukocyte Biology 73
  
  Pages : 225-234
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] Efficacy of the prophylactic use of trimethoprim-sulfamethoxazole in auotimmune neutropenia in infancy.2003
- Author(s)
  Kobayashi M, Sato T, et al.
- Journal Title
  
  Journal of Pediatric Hematology/Oncology 25
  
  Pages : 553-557
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-15591111
[Journal Article] 血液腫瘍疾患児の入院生活のストレスに関する研究-I.ストレッサーの同定と意義-2003
- Author(s)
  原美智子, 平賀健太郎, 浜本和子, 藤本和美, 上田一博, 小林正夫
- Journal Title
  
  日本小児血液学雑誌 17・3
  
  Pages : 111-116
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-14201012
[Journal Article] 血液腫瘍疾患児の入院生活のストレスに関する研究-II.ストレッサーの同定と意義-2003
- Author(s)
  原美智子, 平賀健太郎, 浜本和子, 藤本和美, 上田一博, 小林正夫
- Journal Title
  
  日本小児血液学雑誌 17・3
  
  Pages : 117-122
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-14201012
[Journal Article] Study on the stress in hospitalized children with hemato-oncological diseases., II. The factors causing stressful condition.2003
- Author(s)
  Hara, M., Hiraga, K., Hamamoto, K., Fujimoto, K., Ueda, K., Kobayashi, M.
- Journal Title
  
  The Japanese Journal od Pediatric Hematology 17,3
  
  Pages : 117-122
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-14201012
[Journal Article] Study on the stress in hospitalized children with hemato-oncological diseases,. I. The significance of identification of stressors.2003
- Author(s)
  Hara, M., Hiraga, K., Hamamoto, K., Fujimoto, K., Ueda, K., Kobayashi, M.
- Journal Title
  
  The Japanese Journal of Pediatric Hematology 17,3
  
  Pages : 111-116
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-14201012
[Journal Article] 慢性腎疾患患児のストレッサーの評価-ネフローゼ症候群と慢性腎炎の比較2002
- Author(s)
  平賀健太郎, 小林正夫
- Journal Title
  
  小児保健研究 61・6
  
  Pages : 799-805
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-14201012
[Presentation] 好中球異常症：診断と造血幹細胞移植2015
- Author(s)
  小林正夫
- Organizer
  第77回日本血液学会教育講演
- Place of Presentation
  金沢
- Year and Date
  2015-10-16
- Invited
- Data Source
  KAKENHI-PROJECT-26670501
[Presentation] Impairment of IL-17 immunity to Candida and IFNγ immunity to Mycobacterium in humans with bi-allelic Rorc mutations.2015
- Author(s)
  Okada S, Markle J, Kobayashi M, Bustamante J, Casanova JL
- Organizer
  The 57th American Society of Hematology Annual Meeting and Exposition
- Place of Presentation
  Orlando, FL, USA
- Year and Date
  2015-12-05
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-26670501
[Presentation] A comparison of myelopoiesis from induced pluripotent stem cells with a mutation in ELANE between cyclic neutropenia and sever congenital neutropenia.2015
- Author(s)
  Saito S, Nishimura S, Tsumra M, Mizoguchi Y, Sakata S, Furue A, Kobayashi M
- Organizer
  The 57th American Society of Hematology Annual Meeting and Exposition
- Place of Presentation
  Orlando, FL, USA
- Year and Date
  2015-12-05
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-26670501
[Presentation] Impairment of IL-17 immunity to Candida and IFNγ immunity to Mycobacterium in humans with bi-allelic Rorc mutations.2015
- Author(s)
  Okada S, Markle J, Kobayashi M, Bustamante J, Casanova JL
- Organizer
  The 57th American Society of Hematology Annual Meeting and Exposition
- Place of Presentation
  Orlando, FL, USA
- Year and Date
  2015-12-05
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-25293231
[Presentation] A comparison of myelopoiesis from induced pluripotent stem cells with a mutation in ELANE between cyclic neutropenia and sever congenital neutropenia.2015
- Author(s)
  Saito S, Nishimura S, Tsumra M, Mizoguchi Y, Sakata S, Furue A, Kobayashi M
- Organizer
  The 57th American Society of Hematology Annual Meeting and Exposition
- Place of Presentation
  Orlando, FL, USA
- Year and Date
  2015-12-05
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-25293231
[Presentation] 好中球異常症：診断と造血幹細胞移植2015
- Author(s)
  小林正夫
- Organizer
  第77回日本血液学会
- Place of Presentation
  金沢
- Year and Date
  2015-10-16
- Invited
- Data Source
  KAKENHI-PROJECT-25293231
[Presentation] MSMD Patients with IFN-γ-STAT1 Signaling Defect Present Enhanced Osteoclastogenesis and Bone Resorption.2015
- Author(s)
  Nishimura S, Tsumura M, Hirata O, Reiko Kagawa, Mizoguchi Y, Okada S, Kobayashi M
- Organizer
  The 57th American Society of Hematology Annual Meeting and Exposition
- Place of Presentation
  Orlando, FL, USA
- Year and Date
  2015-12-05
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-25293231
[Presentation] MSMD Patients with IFN-γ-STAT1 Signaling Defect Present Enhanced Osteoclastogenesis and Bone Resorption.2015
- Author(s)
  Nishimura S, Tsumura M, Hirata O, Reiko Kagawa, Mizoguchi Y, Okada S, Kobayashi M
- Organizer
  The 57th American Society of Hematology Annual Meeting and Exposition
- Place of Presentation
  Orlando, FL, USA
- Year and Date
  2015-12-05
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-26670501
[Presentation] Genetic characteristic of patients with severe congenital neutropenia in Japan.2013
- Author(s)
  Masao Kobayashi, Yoko Mizoguchi, Shuhei Karakawa, Satoshi Okada, Hiroshi Kawaguchi, Kazuhiro Nakamura
- Organizer
  27th International Congress of Pediatrics
- Place of Presentation
  Melbourne, Australia
- Data Source
  KAKENHI-PROJECT-25293231
[Presentation] Identification of the integrin B3 L718P mutation in a pedigree with autosomal dominant thrombocytopenia with anisocytosis.2012
- Author(s)
  Kobayashi Y
- Organizer
  The 54th Annual meeting of American Society of Hematology
- Place of Presentation
  Atlanta, GA, USA
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] Gain-of-function mutations of STAT1 in Japanese patients with CMCD2012
- Author(s)
  Osamu Hirata, Miyuki Tsumura, Yoko Mizoguchi, Satoshi Okada, Shizuko Minegishi, Tomohiro Morio, Masao Kobayashi
- Organizer
  European Society for Immunodeficiency
- Place of Presentation
  Florence, Italy
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] Identification of integrin b3 L718P mutation in a pedigree with autosomal dominant macrothrombocytopenia2012
- Author(s)
  Yoshiyuki Kobayashi, Hirotaka Matsui, Akinori Kanai, Miyuki Tsumura, Satoshi Okada, Mizuka Miki, Kazuhiro Nakamura, Shinji Kunishima, Toshiya Inaba and Masao Kobayashi
- Organizer
  American Society of Hematology
- Place of Presentation
  Atlanta, GA
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] A Nobel Method using Extracted Human Neutrophil Antigens from HNA gene-transfected cell lines for Detection of Antibodies against Human Neutrophil Antigens2012
- Author(s)
  Rie Onodera, Kazuhiro Nakamura, Kikuyo Taniguchi, Emi Kurita, Asako Hiraoka, Kaduta Yasui, Nobuki Matsuyama, Fumiya Hirayama, and Masao Kobayashi
- Organizer
  American Society of Hematology
- Place of Presentation
  Atlanta, GA
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] Clinical and genetic characteristics of patients with severe congenital neutropenia in Japan2011
- Author(s)
  Mizoguchi Y, Kobayashi M, et al
- Organizer
  53^<rd> American Society of Hematology Annual Meeting
- Place of Presentation
  San Diego, CA, USA
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] Suppressed neutrophil development in hematopoiesis of induced pluripotent stem cells derived from a severe congenital neutropenia patient with ELA2 mutation2011
- Author(s)
  Hiramoto T, Kobayashi M, et al
- Organizer
  53^<rd> American Society of Hematology Annual Meeting
- Place of Presentation
  San Diego, CA, USA
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] JAK2 mutations and CRLF2 rearrangements in Down syndrome-associated acute lymphoblastic leukemia in Japan2011
- Author(s)
  Hanada I, Kobayashi M, et al
- Organizer
  53^<rd> American Society of Hematology Annual Meeting
- Place of Presentation
  San Diego, CA, USA
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] TsumuraM, Okada S, Sakai H, Nishikomori R, YasunagaS, Ohtsubo M, HeikeT, NakahataT, TakiharaY, KobayashiM2011
- Author(s)
  TsumuraM, Okada S, Sakai H, Nishikomori R, YasunagaS, Ohtsubo M, HeikeT, NakahataT, TakiharaY, KobayashiM
- Organizer
  第73回日本血液学会学術集会
- Place of Presentation
  名古屋
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] JAK2 mutations and CRLF2 rearrangements in Down Syndrome-Associated Acute Lymphoblastic Leukemia in Japan2011
- Author(s)
  Hanada I, Terui K, Toki T,Kudo K, Sato T, Kamio T, Sasaki S,Takahashi Y, Hayashi Y, Sugita K, Kojima S, Koike K, Kosaka Y, Kobayashi M, Ito E
- Organizer
  53rdAmerican Societey of Hematology Annual Meeting
- Place of Presentation
  San Diego, CA
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] 常染色体優性遺伝を呈する慢性皮膚粘膜カンジダ症の責任遺伝子の発見-STAT1 機能獲得性変異による慢性皮膚粘膜カンジダ症-2011
- Author(s)
  岡田賢,小林正夫,Luyan Liu, Xiao-Fei Kong, Alexandra Y. Kreins, Sophie Cypowyj, Laurent Abel, Capucine Picard, Stephanie Boisson-Dupuis, Anne Puel, Jean-Laurent Casanova
- Organizer
  第39回日本臨床免疫学会総会
- Place of Presentation
  東京
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] Clinical and genetic characteristics of patients with severe congenital neutropenia in Japan2011
- Author(s)
  Mizoguchi Y, Nakamura K, Karakawa S, Okada S, Kawaguchi H, Kobayashi M
- Organizer
  53rd American Society of Hematology Annual Meeting
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] Suppressed Neutrophil Development in Hematopoiesis of Induced Pluripotent Stem Cells Derived From a Severe Congenital Neutropenia Patient with ELA2 Mutation2011
- Author(s)
  Hiramoto T, Ebihara Y, Mizoguchi Y, Nakamura K, Mochizuki S, Yamamoto S, Matsuzaka E, Hanada S, Ohnishi R, Tani K, Eto K, Nakauchi H, Kobayashi M, Tsuji K
- Organizer
  53rdAmerican Societey of Hematology Annual Meeting
- Place of Presentation
  San Diego, CA
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] A novel mutation K673R in STAT1 impaired the STAT1 signal transduction in a dominat-negative manner identified in a Japanese boy with MSMD.2010
- Author(s)
  Tsumura M, Kobayashi M, et al.
- Organizer
  14^<th> International Congress of Immunology
- Place of Presentation
  Kobe, Japan
- Year and Date
  2010-08-25
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] Umbilical cord blood-derived stem cells cultured under low oxygen tension enhance the migratioin and homing efficacy through the increased expression of CXCR42010
- Author(s)
  Ohno N, Kajiume T, Hayakawa S, Kobayashi Y, Ytsunomiya A, Kobayashi M
- Organizer
  52nd American Society of Hematology Annual Meeting
- Place of Presentation
  Orlando FL USA
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] A Novel mutation K673R in STAT1 impaired the STAT1 signal transduction in a dominant-negative manner identified in a Japanese boy2010
- Author(s)
  Mizoguchi Y, Tsumura M, Okada S, Sakai H, Nishikomori R, Yasunaga S, Ohtsubo M, Murata T, Obata H, Yasumi T, Heike T, Nakahata T, Takaihara Y, Kobayashi M
- Organizer
  52nd American Society of Hematology Annual Meeting
- Place of Presentation
  Orlando FL USA
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] Decreased expression in NF-kB essential modulator due to a novel splice-site mutation causes ectodermal dysplasia with immunodeficiency2010
- Author(s)
  Karakawa S, Okada, S, Tsumura M, Yasunaga S, Ohtsubo M, Kawai T, Nishikomori R, Takihara Y, Kobayashi M
- Organizer
  52nd American Society of Hematology Annual Meeting
- Place of Presentation
  Orlando FL USA
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] 小児の易感染性と食細胞異常症2010
- Author(s)
  小林正夫
- Organizer
  第62回北日本小児科学会
- Place of Presentation
  札幌
- Year and Date
  2010-09-11
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] Decreased expression in NF-kB essential modulator due to a novel splice-site mutation causes ectodermal dysplasia with immunodeficiency.2010
- Author(s)
  Karakawa S, Kobayashi M, et al.
- Organizer
  American Society of Hematology (52^<nd> Annual Meeting)
- Place of Presentation
  Orlando FL, USA
- Year and Date
  2010-12-04
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] A Novel mutation K673R in STAT1 impaired the STAT1 signal transduction in a dominant-neeative manner identified in a Japanese boy.2010
- Author(s)
  Mizoguchi Y, Kobayashi M, et al.
- Organizer
  American Society of Hematology (52^<nd> Annual Meeting)
- Place of Presentation
  Orlando FL, USA
- Year and Date
  2010-12-04
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] Umbilical cord blood-derived stem cells cultured under low oxygen tension enhance the migratioin and homing efficacy through the increased expression of CXCR4.2010
- Author(s)
  Ohno N, Kobayashi M, et al.
- Organizer
  American Society of Hematology (52^<nd> Annual Meeting)
- Place of Presentation
  Orlando FL, USA
- Year and Date
  2010-12-04
- Data Source
  KAKENHI-PROJECT-22591161
[Presentation] Short-Term Culture of Umbilical Cord Blood-Derived Stem Cells Enhances the Engraftment into NOD/SCID Mice through the Increased Expression of CXCR4.2008
- Author(s)
  Ohno N, Kajiume T, Sera Y, Satoh T, Kobayashi M
- Organizer
  American Society of Hematology, 49th Annual Meeting.
- Place of Presentation
  San Francisco, CA, USA
- Year and Date
  2008-12-07
- Data Source
  KAKENHI-PROJECT-19591250
[Presentation] Short-Term Culture of Umbilical Cord Blood-Derived Stem Cells Enhances the Engraftment into NOD/SCID Mice through the Increased Expression of CXCR42008
- Author(s)
  Ohno N, Kajiume T, Sera Y, Sato T, Kobayashi M
- Organizer
  American Society of Hematology, 50th Annual Meeting
- Place of Presentation
  San Francisco, CA, U.S.A.
- Year and Date
  2008-12-06
- Data Source
  KAKENHI-PROJECT-19591250
[Presentation] Novel Heterozygous Mutation 572insA in TACI Identified in a Patient with Selective IgA Deficiency2008
- Author(s)
  Okada S, Kajiume T, Tsumura M, Shirao K, Ohno Y, Yasunaga S, Ohtsubo M, Sira MM, Kanegane H, Miyawaki T, Takihara Y, Kobayashi M
- Organizer
  American Society of Hematology, 50th Annual Meeting
- Place of Presentation
  San Francisco, CA, U.S.A.
- Year and Date
  2008-12-06
- Data Source
  KAKENHI-PROJECT-19591250
[Presentation] Reconstitution of Regulatory T Cells Involves in the Development of Acute Graft-Versus-Host Disease after Hematopoietic Stem Cell Transplantation2008
- Author(s)
  Karakawa S, Nakamura K, Hara K, Mizoguchi Y, Miki M, Kawaguchi K, Sato T, Nishimura S, Kobayashi M
- Organizer
  American Society of Hematology, 50th Annual Meeting
- Place of Presentation
  San Francisco, CA, U.S.A.
- Year and Date
  2008-12-07
- Data Source
  KAKENHI-PROJECT-19591250
[Presentation] The Decrease of Regulatory T Cells through the Low Levels of FOXP3 Expression Mediated by NFAT1 in Infancy with Autoimmune Neutropenia2007
- Author(s)
  Nakamura N, Miki M, Karakawa S, Onodera R, Kurita E, Hiraoka A, Sato T, Kobayashi M
- Organizer
  American Society of Hematology, 49th Annual Meeting
- Place of Presentation
  Atlanta, GA, U.S.A.
- Year and Date
  2007-12-10
- Data Source
  KAKENHI-PROJECT-19591250
[Presentation] Association of Neurodevelopmental Abnormalities Is a Common Clinical Character in Japanese Patients with Severe Congenital Neutropenia Due to HAX1 Deficiency2007
- Author(s)
  Okada S, Ishikawa N, Shirao K, Tsumura M, Sato T, Ohno Y, Yasunaga S, Ohtsubo M, Takihara Y, Kobayashi M
- Organizer
  American Society of Hematology, 49th Annual Meeting
- Place of Presentation
  Atlanta, GA, U.S.A.
- Year and Date
  2007-12-10
- Data Source
  KAKENHI-PROJECT-19591250
[Presentation] The Expression of Polycomb Group Genes Products, Bmi1 and Mel-18, Regulate the Function of Murine Primitive Hematopoietic Cells2007
- Author(s)
  Kajiume T, Takashi Sato T, Kobayashi M
- Organizer
  American Society of Hematology, 49th Annual Meeting
- Place of Presentation
  Atlanta, GA, U.S.A.
- Year and Date
  2007-12-08
- Data Source
  KAKENHI-PROJECT-19591250
[Presentation] Association of Neurodevelopmental Abnormalities Is a Common Clinical Character in Japanese Patients with Severe Congenital Neutropenia Due to HAX1 Deficiency.2007
- Author(s)
  Okada S, Ishikawa N, Shirao K, Kobayashi M, et. al.
- Organizer
  American Society of Hematology, 49th Annual Meeting.
- Place of Presentation
  Atlanta, GA, USA
- Year and Date
  2007-12-10
- Data Source
  KAKENHI-PROJECT-19591250
[Presentation] STAT1 gain-of-function in patients with chronic mucocutaneous candidiasis can be detected by the excessive phosphorylation of STAT1 in peripheral blood monocytes.
- Author(s)
  Yoko Mizoguchi, Satoshi Okada, Miyuki Tsumura, Osamu Hirata, Shizuko Minegishi, Jean-Laurent Casanova, Tomohiro Morio, Masao Kobayashi
- Organizer
  The 56th American Society of Hematology Annual Meeting and Expositio
- Place of Presentation
  San Francisco, CA, USA
- Year and Date
  2014-12-06 – 2014-12-09
- Data Source
  KAKENHI-PROJECT-25293231
[Presentation] Siginificant augmentation of regulatory T cells in early neonatal period.
- Author(s)
  Seiich Hayakawa, Seiko Maeno, Norioki Ohno, Satoshi Okada, Yutaka Nishimura, Michiko Hayashidani, Masao Kobayashi
- Organizer
  16th Biennial Meeting of the European Society for Immunodeficiencies
- Place of Presentation
  Prague, Czech
- Year and Date
  2014-10-29 – 2014-11-01
- Data Source
  KAKENHI-PROJECT-25293231
[Presentation] Excessive Nitric Oxide production of CGD neutrophils induces the down-regulation of NOS3 and EDN1 expression in human endothelial cells.
- Author(s)
  Akari N. Utsunomiya, Miyuki Tsumura, Norioki Ohno, Mizuka Miki, Hiroshi Kawaguchi, Kazuhiro Nakamura and Masao Kobayashi
- Organizer
  The 56th American Society of Hematology Annual Meeting and Exposition
- Place of Presentation
  San Francisco, CA, USA
- Year and Date
  2014-12-06 – 2014-12-09
- Data Source
  KAKENHI-PROJECT-25293231
[Presentation] Early elimination of Factor VIII inhibitor by ITI with high dose immunoglobulin in hemophilia A children.
- Author(s)
  Yoko Mizoguchi, Aya Furue, Ikue Chijimatsu, Mizuka Miki, Keita Tomioka, Nakao Konishi, Atsushi Ono, Hiroshi Kawaguchi, Kazuhiro Nakamura and Masao Kobayashi
- Organizer
  WORLD FEDERATION OF HEMOPHILIA, 2014 World Congress
- Place of Presentation
  Melbourne, Australia
- Year and Date
  2014-05-11 – 2014-05-15
- Data Source
  KAKENHI-PROJECT-25293231
[Presentation] STAT1 gain-of-function in patients with chronic mucocutaneous candidiasis can be detected by the excessive phosphorylation of STAT1 in peripheral blood monocytes.
- Author(s)
  Yoko Mizoguchi, Satoshi Okada, Miyuki Tsumura, Osamu Hirata, Shizuko Minegishi, Jean-Laurent Casanova, Tomohiro Morio, Masao Kobayashi
- Organizer
  The 56th American Society of Hematology Annual Meeting and Exposition
- Place of Presentation
  San Francisco, CA, USA
- Year and Date
  2014-12-06 – 2014-12-09
- Data Source
  KAKENHI-PROJECT-26670501
[Presentation] Early elimination of Factor VIII inhibitor by ITI with high dose immunoglobulin in hemophilia A children
- Author(s)
  Yoko Mizoguchi, Aya Furue, Ikue Chijimatsu, Mizuka Miki, Keita Tomioka, Nakao Konishi, Atsushi Ono, Hiroshi Kawaguchi, Kazuhiro Nakamura and Masao Kobayashi
- Organizer
  WORLD FEDERATION OF HEMOPHILIA, 2014 World Congress
- Place of Presentation
  Melbourne, Australia
- Year and Date
  2014-05-11 – 2014-05-15
- Data Source
  KAKENHI-PROJECT-26670501
[Presentation] Excessive Nitric Oxide production of CGD neutrophils induces the down-regulation of NOS3 and EDN1 expression in human endothelial cells.
- Author(s)
  Akari N. Utsunomiya, Miyuki Tsumura, Norioki Ohno, Mizuka Miki, Hiroshi Kawaguchi, Kazuhiro Nakamura and Masao Kobayashi
- Organizer
  The 56th American Society of Hematology Annual Meeting and Exposition
- Place of Presentation
  San Francisco, CA, USA
- Year and Date
  2014-12-06 – 2014-12-09
- Data Source
  KAKENHI-PROJECT-26670501

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KOBAYASHI Masao 小林 正夫

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iPS細胞を用いた先天性骨髄不全症候群からの白血病発症機序解明と新規治療法の開発Ongoing

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Analysis of abnormal STAT1 disorders using disease-specific iPS cells.Principal Investigator

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Gene editing of iPS cells derived from patients with congenital phagocytic disordersPrincipal Investigator

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Application of humanized mice to analyses and therapeutics of phagocytic disordersPrincipal Investigator

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The cell-surface modification enhances the engraftment of human CD34-positive cells into immunodeficient micePrincipal Investigator

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Purification, expansion, and reconstitution of mesodermal stemcells from human bone marrowPrincipal Investigator

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GENE EXPRESSIONS DURING PROLIFERATION AND DIFFERENTIATION OF MYELOID CELIS IN SEVERE CONCENITAL NEUTROPENIAPrincipal Investigator

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EXPANSION OF HUMAN BONE MARROW CELLS CAPABLE OF REPOPULATING IN MICE BY COCULTURE WITH BONE MARROW STROMAL CELLSPrincipal Investigator

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CHARACTERIZATION OF PURIFIED HUMAN HEMATOPOIETIC PROGENITOR CELLS OF BONE MARROW AND THEIR RECONSTITUTING ABILITY IN GENOGENEIC TRANSPLANTATIONPrincipal Investigator

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KOBAYASHI Masao 小林正夫