NIBA TABE EMMA EKO ニバタベ・エマ・エコ

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ニバタベ・エマ・エコニバタベ・エマ・エコ

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Researcher Number	00727810
Other IDs
Affiliation (Current)	2025: 順天堂大学, 大学院医学研究科, 准教授
Affiliation (based on the past Project Information) *help	2022 – 2023: 順天堂大学, 大学院医学研究科, 准教授 2017 – 2018: 神戸大学, 医学研究科, 助教 2016: 神戸学院大学, 総合リハビリテーション学部, 研究員
Review Section/Research Field	Principal Investigator Basic Section 44010:Cell biology-related / Medical genome science
Keywords	Principal Investigator Epithelial/mesenchymal / tumor / DMD / taurine / serine / slc1a5 / spindle cell sarcoma / alanine / metabolomics / rhabdomyosarcoma … More / mdx mouse / tumor suppressor / dystrophin / AO therapy / Splicing / Intron retention / Dystrophin / tumor suppressor gene, / tumor, / rhabdomyosarcoma, / antisense chemistry, / dystrophin, / intron retention, / splicing, / Rhabdomyosarcoma / Antisense oligo, / Dystrophin, / Intron retention, / Splicing、 Less

Metabolomic analysis of Mdx mouse tumorsPrincipal Investigator
- Principal Investigator
  
  ニバタベ・エマ・エコ
- Project Period (FY)
  2022 – 2024
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Review Section
  
  Basic Section 44010:Cell biology-related
- Research Institution
  Juntendo University
Dystrophin intron retention analysis to identify new targets for Antisense Oligonucleotide mediated RNA modulation in RhabdomyosarcomaPrincipal Investigator
- Principal Investigator
  
  NIBA TABE EMMA EKO
- Project Period (FY)
  2016 – 2018
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Medical genome science
- Research Institution
  Kobe University
  Kobe Gakuin University

All 2024 2023 2022 2021 2018 2017 2016

All Journal Article Presentation

[Journal Article] Correction: Noguchi et al. PCR-Based Screening of Spinal Muscular Atrophy for Newborn Infants in Hyogo Prefecture, Japan. Genes 2022, 13, 21102023
- Author(s)
  Noguchi Yoriko、Bo Ryosuke、Nishio Hisahide、Matsumoto Hisayuki、Matsui Keiji、Yano Yoshihiko、Sugawara Masami、Ueda Go、Wijaya Yogik Onky Silvana、Niba Emma Tabe Eko、Shinohara Masakazu、Bouike Yoshihiro、Takeuchi Atsuko、Lee Tomoko、Takeshima Yasuhiro、Iijima Kazumoto、Nozu Kandai、Awano Hiroyuki
- Journal Title
  
  Genes
  
  Volume: 14 Issue: 3 Pages: 759-759
- DOI
  10.3390/genes14030759
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-22K06224
[Journal Article] Spinal Muscular Atrophy: The Past, Present, and Future of Diagnosis and Treatment2023
- Author(s)
  Nishio Hisahide、Niba Emma Tabe Eko、Saito Toshio、Okamoto Kentaro、Takeshima Yasuhiro、Awano Hiroyuki
- Journal Title
  
  International Journal of Molecular Sciences
  
  Volume: 24 Issue: 15 Pages: 11939-11939
- DOI
  10.3390/ijms241511939
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-22K06224, KAKENHI-PROJECT-23K07279
[Journal Article] PCR-Based Screening of Spinal Muscular Atrophy for Newborn Infants in Hyogo Prefecture, Japan2022
- Author(s)
  Noguchi Yoriko、Bo Ryosuke、Nishio Hisahide、Matsumoto Hisayuki、Matsui Keiji、Yano Yoshihiko、Sugawara Masami、Ueda Go、Wijaya Yogik Onky Silvana、Niba Emma Tabe Eko、Shinohara Masakazu、Bouike Yoshihiro、Takeuchi Atsuko、Okamoto Kentaro、Saito Toshio、Shimomura Hideki、Lee Tomoko、Takeshima Yasuhiro....Awano Hiroyuki
- Journal Title
  
  Genes
  
  Volume: 13 Issue: 11 Pages: 2110-2110
- DOI
  10.3390/genes13112110
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-22K06224, KAKENHI-PROJECT-20K08197
[Journal Article] High Concentration or Combined Treatment of Antisense Oligonucleotides for Spinal Muscular Atrophy Perturbed SMN2 Splicing in Patient Fibroblasts2022
- Author(s)
  Wijaya Yogik Onky Silvana、Niba Emma Tabe Eko、Nishio Hisahide、Okamoto Kentaro、Awano Hiroyuki、Saito Toshio、Takeshima Yasuhiro、Shinohara Masakazu
- Journal Title
  
  Genes
  
  Volume: 13 Issue: 4 Pages: 685-685
- DOI
  10.3390/genes13040685
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-22K06224, KAKENHI-PROJECT-20K08197
[Journal Article] Stability and Oligomerization of Mutated SMN Protein Determine Clinical Severity of Spinal Muscular Atrophy2021
- Author(s)
  Niba ETE, Nishio H, Wijaya YOS, Ar Rochmah M, Takarada T, Takeuchi A, Kimizu T, Okamoto K, Saito T, Awano H, Takeshima Y, Shinohara M.
- Journal Title
  
  Genes (Basel)
  
  Volume: 13 Issue: 2 Pages: 205-205
- DOI
  10.3390/genes13020205
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-20K08197, KAKENHI-PROJECT-22K06224
[Journal Article] Intron-retained transcripts of the spinal muscular atrophy genes, SMN1 and SMN2.2018
- Author(s)
  Harahap NIF, Niba ETE, Ar Rochmah M, Wijaya YOS, Saito T, Saito K, Awano H, Morioka I, Iijima K, Lai PS, Matsuo M, Nishio H, Shinohara M.
- Journal Title
  
  Brain & Devwlopment
  
  Volume: 40 Issue: 8 Pages: 670-677
- DOI
  10.1016/j.braindev.2018.03.001
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-17K10077, KAKENHI-PROJECT-16K07216
[Journal Article] Detection of Dystrophin Dp71 in Human Skeletal Muscle Using an Automated Capillary Western Assay System2018
- Author(s)
  Kawaguchi T*, Niba ETE*, Rani AQM, Onishi Y, Koizumi M, Awano
- Journal Title
  
  International Journal of Molecular Science
  
  Volume: 19 (6) Issue: 6 Pages: 1546-1546
- DOI
  10.3390/ijms19061546
- NAID
  120006496733
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-16K07216
[Journal Article] DMD transcripts in CRL-2061 rhabdomyosarcoma cells show high levels of intron retention by intron-specific PCR amplification2017
- Author(s)
  Niba ETE, Yamanaka R, Rani AQM, Awano H, Matsumoto M, Nishio H, Matsuo M
- Journal Title
  
  Cancer Cell international
  
  Volume: 17 Issue: 1 Pages: 58-73
- DOI
  10.1186/s12935-017-0428-4
- NAID
  120006373783
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-16K07216, KAKENHI-PROJECT-17K10077
[Journal Article] Gender effects on the clinical phenotype in Japanese patients with spinal muscular atrophy.2017
- Author(s)
  Ar Rochmah M, Shima A, Harahap NIF, Niba ETE, Morisada N, Yanagisawa S, Saito T, Kaneko K, Saito K, Morioka I, Iijima K, Lai PS, Bouike Y, Nishio H, Shinohara M
- Journal Title
  
  Kobe J Med Sci
  
  Volume: 63(2)
- Open Access
- Data Source
  KAKENHI-PROJECT-16K07216
[Journal Article] Cryptic splice activation but not exon skipping is observed in minigene assays of dystrophin c.9361+1G4A mutation identified by NGS2017
- Author(s)
  Emma Tabe Eko Niba
- Journal Title
  
  Journal of Human Genetics
  
  Volume: 1-7 Issue: 5 Pages: 531-537
- DOI
  10.1038/jhg.2016.162
- Peer Reviewed / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-16K07216, KAKENHI-PROJECT-17K10077
[Journal Article] DMD transcripts in CRL-2061 rhabdomyosarcoma cells show high levels of intron retention by intron-specific PCR amplification2017
- Author(s)
  Emma Tabe Eko Niba
- Journal Title
  
  Cancer cell International
  
  Volume: -
- Peer Reviewed / Acknowledgement Compliant
- Data Source
  KAKENHI-PROJECT-16K07216
[Journal Article] New, improved version of the mCOP-PCR screening system for detection of spinal muscular atrophy Gene (SMN1) deletion.2017
- Author(s)
  Shinohara M, Ar Rochmah M, Nakanishi K, Harahap NIF, Niba ETE, Saito T, Saito K, Takeuchi A, Bouike Y, Nishio H
- Journal Title
  
  Kobe J Med Sci
  
  Volume: 63(2)
- Open Access
- Data Source
  KAKENHI-PROJECT-16K07216
[Journal Article] SMA diagnosis: Detection of SMN1 deletion with real-time mCOP-PCR system using fresh blood DNA2017
- Author(s)
  Niba ETE, Ar Rochmah M, Harahap NIF, Awano H, Morioka I, Iijima K, Saito T, Saito K, Takeuchi A, Lai PS, Bouike Y, Nishio H, Shinohara M.
- Journal Title
  
  Kobe J Med Sci
  
  Volume: 63(3)
- NAID
  120006373838
- Open Access
- Data Source
  KAKENHI-PROJECT-16K07216
[Journal Article] Genetic screening of spinal muscular atrophy using a real-time modified COP-PCR technique with dried blood-spot DNA2017
- Author(s)
  Ar Rochmah M, Harahap NIF, Niba ETE, Nakanishi K, Awano H, Morioka I, Iijima K, Saito T, Saito K, Lai PS, Takeshima Y, Takeuchi A, Bouike Y, Okamoto M, Nishio H, Shinohara M
- Journal Title
  
  Brain Dev.
  
  Volume: 39(9) Issue: 9 Pages: 774-782
- DOI
  10.1016/j.braindev.2017.04.015
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-16K07216, KAKENHI-PROJECT-17K10077
[Presentation] Mir-532-5P and Vesicular Associated Membrane Protein-1 (Vamp1) After Running Wheel Exercise in Mice2024
- Author(s)
  Ahmed Imtiaz1 , Mohammad Nasir Uddin2 , Montasir Elahi3 , Hiroshi Koide4 , Emma Niba4 , Shotaro Shimonaka1 , Madoka Nakajima6,7 , Ikuko Ogino6 , Koichi Ishiguro7 , Yumiko Motoi7,9 , Nobutaka Hattori1,5,8
- Organizer
  4th Congress, International Academy of Sportology
- Data Source
  KAKENHI-PROJECT-22K06224
[Presentation] Glioma from a DMD patient exhibits differential splicing pattern including exon 71 skipping and intron 40 retention2018
- Author(s)
  : Emma E.T. Niba, Hiroyuki Awano, Masashi Nagai, Masaaki Taniguchi, Rani Adul Qawee, Masakazu Shinohara, Hisahide Nishio, Masafumi Matsuo
- Organizer
  Molecular Biology Society of Japan
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-16K07216
[Presentation] Spontaneous development of spindle cell sarcoma in mdx mice2018
- Author(s)
  : Satoru Takafuji, Emma Niba, Khin Kyae Mon Thwin, Nobuyuki Yamamoto, Hiroyuki Awano, Suguru Uemura, Takeshi Mori, Shoji Fukushima, Kyoko Itoh, Hisahide Nishio, Masafumi Matsuo, Kazumoto Iijima, Noriyuki Nishimura
- Organizer
  International Society of Pediatric Oncology
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-16K07216
[Presentation] DMD transcription profiling in spontaneously developed tumor from three mdx mice revealed extensive intron retentions and Dp71 isoform expression2018
- Author(s)
  Emma E.T. Niba, Noriyuki Nishimura, Satoru Takafuji, Khin Kyae Mon Thwin, Nobuyuki Yamamoto, Hiroyuki Awano, Shoji Fukushima, Kyoko Itoh, Hisahide Nishio, Masafumi Matsuo
- Organizer
  American Society of Cell Biology
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-16K07216
[Presentation] Multi-intron retentions in DMD transcripts in CRL-2061 rhabdomyosarcoma cells identified by intron specific RT-PCR amplification2017
- Author(s)
  Emma Tabe Eko Niba1,2, Ryo Yamanaka2, Abdul Qawee Mahyoob Rani2, Hiroyuki Awano3, Masaaki Matsumoto3, Hisahide Nishio1, Masafumi Matsuo2
- Organizer
  Japan Society of Human Genetics
- Data Source
  KAKENHI-PROJECT-16K07216
[Presentation] Dystrophin Dp427 is lost due to multiple DMD intron retentions in rhabdomyosarcoma CRL-2061 cells2017
- Author(s)
  Emma Tabe Eko Niba1,3, Ryo Yamanaka1, Abdul Qawee Mahyoob Rani1, Hiroyuki Awano2, Masaaki Matsumoto2, Hisahide Nishio3, Masafumi Matsuo1
- Organizer
  22nd international congress of the WORLD MUSCLE SOCIETY
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-16K07216
[Presentation] Irregular transcription of the dystrophin gene in colon cancer HCT-116 cell line: no conventional transcript but 6 transcripts with intron retention out of 9 examined short introns2016
- Author(s)
  Emma Tabe Eko Niba
- Organizer
  Molecular Biology Society of Japan
- Place of Presentation
  Yokohama
- Year and Date
  2016-11-30
- Data Source
  KAKENHI-PROJECT-16K07216
[Presentation] Cryptic splice site activation by a splice donor site mutation of dystrophin intron 64 is determined by intronic splicing regulatory elements2016
- Author(s)
  Emma Tabe Eko Niba
- Organizer
  21st international congress of the WORLD MUSCLE SOCIETY
- Place of Presentation
  Granada - Spain
- Year and Date
  2016-10-04
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-16K07216

1. 松尾雅文 (10157266)

# of Collaborated Projects: 1 results

# of Collaborated Products: 6 results
2. 篠原正和 (80437483)

# of Collaborated Projects: 1 results

# of Collaborated Products: 4 results
3. AWANO HIROYUKI

# of Collaborated Projects: 1 results

# of Collaborated Products: 9 results
4. NISHIMURA NORIYUKI

# of Collaborated Projects: 1 results

# of Collaborated Products: 2 results
5. 西尾久英

# of Collaborated Projects: 0 results

# of Collaborated Products: 2 results

NIBA TABE EMMA EKO ニバ タベ・エマ・エコ

ニバ タベ・エマ・エコ ニバ タベ・エマ・エコ

Research Projects

Research Products

Co-Researchers

Metabolomic analysis of Mdx mouse tumorsPrincipal Investigator

Principal Investigator

Project Period (FY)

Research Category

Review Section

Research Institution

Dystrophin intron retention analysis to identify new targets for Antisense Oligonucleotide mediated RNA modulation in RhabdomyosarcomaPrincipal Investigator

Principal Investigator

Project Period (FY)

Research Category

Research Field

Research Institution

[Journal Article] Correction: Noguchi et al. PCR-Based Screening of Spinal Muscular Atrophy for Newborn Infants in Hyogo Prefecture, Japan. Genes 2022, 13, 21102023

Author(s)

Journal Title

DOI

Data Source

[Journal Article] Spinal Muscular Atrophy: The Past, Present, and Future of Diagnosis and Treatment2023

Author(s)

Journal Title

DOI

Data Source

[Journal Article] PCR-Based Screening of Spinal Muscular Atrophy for Newborn Infants in Hyogo Prefecture, Japan2022

Author(s)

Journal Title

DOI

Data Source

[Journal Article] High Concentration or Combined Treatment of Antisense Oligonucleotides for Spinal Muscular Atrophy Perturbed SMN2 Splicing in Patient Fibroblasts2022

Author(s)

Journal Title

DOI

Data Source

[Journal Article] Stability and Oligomerization of Mutated SMN Protein Determine Clinical Severity of Spinal Muscular Atrophy2021

Author(s)

Journal Title

DOI

Data Source

[Journal Article] Intron-retained transcripts of the spinal muscular atrophy genes, SMN1 and SMN2.2018

Author(s)

Journal Title

DOI

Data Source

[Journal Article] Detection of Dystrophin Dp71 in Human Skeletal Muscle Using an Automated Capillary Western Assay System2018

Author(s)

Journal Title

DOI

NAID

Data Source

[Journal Article] DMD transcripts in CRL-2061 rhabdomyosarcoma cells show high levels of intron retention by intron-specific PCR amplification2017

Author(s)

Journal Title

DOI

NAID

Data Source

[Journal Article] Gender effects on the clinical phenotype in Japanese patients with spinal muscular atrophy.2017

Author(s)

Journal Title

Data Source

[Journal Article] Cryptic splice activation but not exon skipping is observed in minigene assays of dystrophin c.9361+1G4A mutation identified by NGS2017

Author(s)

Journal Title

DOI

Data Source

[Journal Article] DMD transcripts in CRL-2061 rhabdomyosarcoma cells show high levels of intron retention by intron-specific PCR amplification2017

Author(s)

Journal Title

Data Source

[Journal Article] New, improved version of the mCOP-PCR screening system for detection of spinal muscular atrophy Gene (SMN1) deletion.2017

Author(s)

Journal Title

Data Source

[Journal Article] SMA diagnosis: Detection of SMN1 deletion with real-time mCOP-PCR system using fresh blood DNA2017

Author(s)

Journal Title

NAID

NIBA TABE EMMA EKO ニバタベ・エマ・エコ

ニバタベ・エマ・エコニバタベ・エマ・エコ