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Orii Kenji  折居 建治

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ORII Kenji  折居 建治

折居 建治  オリイ ケンジ

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Researcher Number 30332688
Other IDs
Affiliation (Current) 2025: 岐阜大学, 医学部附属病院, 非常勤講師
Affiliation (based on the past Project Information) *help 2014 – 2016: 岐阜大学, 医学部附属病院, 准教授
2010: Gifu University, 医学部附属病院, 准教授
2008 – 2009: Gifu University, 医学部附属病院, 助教
2006: 岐阜大学, 大学院医学系研究科, 助手
2005: 岐阜大学, 医学部附属病院, 助手
2002: 岐阜大, 医学部附属病院, 助手
2001: 岐阜大学, 医学部・附属病院, 助手
Review Section/Research Field
Principal Investigator
Pediatrics / Pediatrics
Keywords
Principal Investigator
神経変性 / ウロン酸 / サイトカイン / ポリ硫酸ペントサン / 骨関節症状 / 新規治療薬 / ムコ多糖症 / 先天代謝異常症 / 遺伝子修復 / 遺伝子 … More / 脳神経疾患 / 小脳変性症 / 小児神経学 / NBS1 / Mre11 / ATM / 毛細血管拡張性運動失調症 / TIR Domain / Death Domain / 立体構造解析 / MyD88 Less
  • Research Projects

    (4 results)
  • Research Products

    (12 results)
  • Co-Researchers

    (3 People)
  •  Study on the safety and effect of novel therapeutic agents for mucopolysaccharidosisPrincipal Investigator

    • Principal Investigator
      Orii Kenji
    • Project Period (FY)
      2014 – 2016
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Gifu University
  •  The analysis of congenital DNA-repair abnormality with cerebellar degenerationPrincipal Investigator

    • Principal Investigator
      ORII Kenji
    • Project Period (FY)
      2008 – 2010
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Gifu University
  •  毛細血管拡張性運動失調症における神経変性機構を解明するための基礎的研究Principal Investigator

    • Principal Investigator
      折居 建治
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Young Scientists (B)
    • Research Field
      Pediatrics
    • Research Institution
      Gifu University
  •  病的なサイトカイン血症を来す病因関連蛋白質の立体構造解析と新たな治療法の開発Principal Investigator

    • Principal Investigator
      折居 建治
    • Project Period (FY)
      2001 – 2002
    • Research Category
      Grant-in-Aid for Young Scientists (B)
    • Research Field
      Pediatrics
    • Research Institution
      Gifu University

All 2016 2015 2010 2009 2006

All Journal Article Presentation

  • [Journal Article] STXBP1 mutations in early infantile epileptic encephalopathy with suppression-burst pattern.2010

    • Author(s)
      Hirotomo Saitsu, Mitsuhiro Kato, Ippei Okada, Kenji E. Orii, Tsukasa Higuchi, Hideki Hoshino, Masaya Kubota, Hiroshi Arai, Tstsuzo Tagawa, Shigeru Kimura, Akira Sudo, Sahoko Miyama, Yuichi Takami, Toshihide Watanabe, Akira Nishimura, Kiyomi Nishimura, Noriko Miyake, Takahito Wada, Hitoshi Osaka, Naomi Kondo, Kiyoshi Hayasaka, Naomichi Matsumoto
    • Journal Title

      Epilepsia Vol.51

      Pages: 1528-1168

    • Data Source
      KAKENHI-PROJECT-20591220
  • [Journal Article] STXBP1 mutations in early infantile epileptic encephalopathy with suppression-burst pattern.2010

    • Author(s)
      Hirotomo Saitsu, Mitsuhiro Kato, Ippei Okada, Kenji E. Orii, Tsukasa Higuchi, Hideki Hoshino, Masaya Kubota, Hiroshi Arai, Tstsuzo Tagawa, Shigeru Kimura, Akira Sudo, Sahoko Miyama, Yuichi Takami, Toshihide Watanabe, Akira Nishimura, Kiyomi Nishimura, Noriko Miyake, Takahito Wada, Hitoshi Osaka, Naomi Kondo, Kiyoshi Hayasaka, Naomichi Matsumoto
    • Journal Title

      Epilepsia

      Volume: Vol.51(12) Pages: 1528-1167

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20591220
  • [Journal Article] Developmental changes of radiological findings in Fukuyama-type congenital muscular dystrophy.2010

    • Author(s)
      Zenichiro Kato, Masahiro Morimoto, Kenji E, Orii, Tomomi Kato, Naomi Kondo
    • Journal Title

      Pediatric Radiology. Vol 40 supple

    • Data Source
      KAKENHI-PROJECT-20591220
  • [Journal Article] Developmental changes of radiological findings in Fukuyama-type congenital muscular dystrophy.2010

    • Author(s)
      Zenichiro Kato, Masahiri Morimoto, Kenji E, Orii, Tomomi Kato, Naomi Kondo
    • Journal Title

      Pediatric Radiology

      Volume: Vol.40 Suppl1

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20591220
  • [Journal Article] Structural basis for the multiple interactions of the Myd88 TIR domain in TLR4 signaling2009

    • Author(s)
      Hidenori Ohnishi, Hidehiko Tochio, Zenichiro Kato, Kenji E.Orii, Ailian Li, Takeshi Kimura, Hidekazu Hiroaki, Naomi Kondo, Masahiro Shirakawa
    • Journal Title

      PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA 106 25

      Pages: 10260-10265

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20591220
  • [Journal Article] Masahiro Shirakawa Structural basis for the multiple interactions of the Myd88 TIR domain in TLR4 signaling2009

    • Author(s)
      Hidenori Ohnishi, Hidehiko Tochio, Zenichiro Kato, Rend E.Orii, Ailian Li, Takeshi Kimura Hidekazu Hiroaki, Naomi Kondo
    • Journal Title

      PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA Vol 106

      Pages: 10260-10265

    • Data Source
      KAKENHI-PROJECT-20591220
  • [Journal Article] Recurrent genomic alterations characterize medulloblastoma arising from DNA double-strand break repair deficiency.2009

    • Author(s)
      Pierre-Olivier Frappart, Youngsoo Lee, Helen R Russell, Nader Chalhoub, Yong-Dong Wang, Kenji E.Orii Jingfeng Zhao, Naomi Kondo, Suzanne J.Baker, Peter J.McKinnon
    • Journal Title

      PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATE S OF AMERICA Vol 106

      Pages: 1880-1885

    • Data Source
      KAKENHI-PROJECT-20591220
  • [Journal Article] Acute disseminated encephalomyelitis associated with enterovirus 71.2006

    • Author(s)
      Kato Z, Omoya K, Orii KE, Kondo N
    • Journal Title

      Journal of pediatric Infectious Disease 1

      Pages: 115-118

    • Data Source
      KAKENHI-PROJECT-17790696
  • [Journal Article] Selective utilization of nonhomologous end-joining and homologous recombination DNA repair pathways during nervous system development.2006

    • Author(s)
      Orii KE, Lee Y, Kondo N, McKinnon PJ
    • Journal Title

      Proceedings of National Academy of Science of the U. S. A. 103・26

      Pages: 10017-10022

    • Data Source
      KAKENHI-PROJECT-17790696
  • [Presentation] Safety study of sodium pentosan polysulfate for adult patients with mucopolysaccharidosis type II2016

    • Author(s)
      折居建治、戸松俊治、鈴木康之、Alexander Solyom、Edward H. Schuchman、Calogera M. Simonaro、折居忠夫、深尾敏幸
    • Organizer
      12th Annual WORLD Symposium 2016
    • Place of Presentation
      San Diego(アメリカ合衆国)
    • Year and Date
      2016-02-29
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26461523
  • [Presentation] ムコ多糖症II型成人患者に対するポリ硫酸ペントサン投与の検討2015

    • Author(s)
      折居建治、戸松俊治、鈴木康之、折居忠夫、深尾敏幸
    • Organizer
      第57回日本先天代謝異常学会
    • Place of Presentation
      大阪市、大阪国際会議場
    • Year and Date
      2015-11-12
    • Data Source
      KAKENHI-PROJECT-26461523
  • [Presentation] ムコ多糖症に対するペントサンの臨床研究・臨床治験について2015

    • Author(s)
      折居建治、戸松俊治
    • Organizer
      第19回日本ムコ多糖症研究会
    • Place of Presentation
      大阪市、ホテルアウィーナ大阪
    • Year and Date
      2015-09-21
    • Data Source
      KAKENHI-PROJECT-26461523
  • 1.  TOMATSU SHUNJI (70237105)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 3 results
  • 2.  SUZUKI YASUYUKI (90154559)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 2 results
  • 3.  折居 忠夫 (20045339)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 3 results

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