Matsuda Junko 松田純子

… Alternative Names

MATSUDA Junko 松田純子

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Researcher Number	60363149
Other IDs
External Links
Affiliation (Current)	2025: 川崎医科大学, 医学部, 教授
Affiliation (based on the past Project Information) *help	2019 – 2023: 川崎医科大学, 医学部, 教授 2013 – 2017: 川崎医科大学, 医学部, 教授 2012: 東海大学, 糖鎖科学研究所, 教授 2008 – 2010: Tokai University, 糖鎖科学研究所, 准教授 2007: Tokai University, Future Science and Technology Joint Research Center, Associate Professor … More 2005 – 2006: Tokai University, Technology Joint Management Office, Associate Professor, 未来科学技術共同研究センター, 助教授 2004: 徳島大学, 大学院・ヘルスバイオサイエンス研究部, 助手 2003: Tokushima Univ., Sch.of Med., Instructor, 医学部, 助手 Less
Review Section/Research Field	Principal Investigator Pediatrics / Basic Section 56030:Urology-related / Basic Section 52050:Embryonic medicine and pediatrics-related / Structural biochemistry / General physiology / Neurochemistry/Neuropharmacology Except Principal Investigator Basic Section 52050:Embryonic medicine and pediatrics-related / Dermatology / Neurochemistry/Neuropharmacology / Pediatrics
Keywords	Principal Investigator スフィンゴ脂質 / スフィンゴ糖脂質 / スフィンゴリピドーシス / セラミド骨格 / 細胞極性 / サポシン / model mouse / sphingolipidosis / モデルマウス / セラミド … More / 上皮細胞 / 小腸上皮細胞 / 構造多様性 / 移行上皮細胞 / 膀胱 / フィトセラミド / 膀胱移行上皮 / リソソーム病 / パーキンソン病 / プロサポシン / リソソーム蓄積病 / 膜輸送 / neuropathology / saposin / Gaucher disease / 神経病変 / ゴーシェ病 / cerebellar Purkinje cell death / ceramide / saposin D deficient mouse / sphingolipid / lysosomal disease / 神経細胞死抑制効果 / 小脳プルキンエ細胞死 / サポシンD欠損マウス / ライソゾーム病 / 生体膜 / 膜脂質 / 小腸 / 脂肪酸水酸化酵素 / スフィンゴ脂質-C4-水酸化酵素(Des2) / 脳海馬体 / スフィンゴ脂質-C4-水酸化酵素(DES2) / フィトスフィンゴ脂質 / ノックアウトマウス / 尿細管上皮 / 小腸上皮 / 海馬 … More Except Principal Investigator クラッベ病 / スフィンゴ脂質 / サイコシン / ラクトシルセラミド / ガラクトシルセラミド / Krabbe病 / 神経セロイドリポフスチン症 / オートファジー / リソソーム / グリオーシス / ロドプシン / アポトーシス / 網膜色素変性症 / プロサポシン / Merkel cell nerve endings / electron microscopy / three-dimensional analysis / confocal laser scannina microscopy / demyelination / trigeminal nerve system / myelinated nerve fibers / cutaneous recentors / 80 / F4 / 三叉神経系 / 皮膚感覚神経 / PGP9.5 / メルケル終末 / 電子顕微鏡 / 三次元構造解析 / 共焦点顕微鏡 / 脱髄 / 三叉神経 / 有髄神経線維 / 皮膚感覚 / Purkinje cell / cerebellum / ceramide / neuropathology / model mouse / sphingolipidosis / glycosphingolipid / プルキンエ細胞 / 小脳 / セラミド / 脳病態 / モデルマウス / スフィンゴリピドーシス / スフィンゴ糖脂質 / Therapy / Protection of demyelination / Estrogen / Sex hormone / Saposin A deficient mouse / Knockout mouse / Krabbe disease / Genetic leukodystrophy / 治療法 / 脱髄抑制効果 / エストロゲン / 性ホルモン / サポシンA欠損マウス / ノックアウトマウス / 遺伝性脳白質変性症 Less

クラッベ病の病態を悪化させるメカニズムの探索
- Principal Investigator
  
  渡邉昂
- Project Period (FY)
  2023 – 2025
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Review Section
  
  Basic Section 52050:Embryonic medicine and pediatrics-related
- Research Institution
  Kawasaki Medical School
Structural diversity of ceramide moiety responsible for apical membrane function of bladder transitional epithelial cellsPrincipal Investigator
- Principal Investigator
  
  松田純子
- Project Period (FY)
  2023 – 2025
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Review Section
  
  Basic Section 56030:Urology-related
- Research Institution
  Kawasaki Medical School
Elucidation of novel functions of prosaposin in autophagy
- Principal Investigator
  
  石塚佑太
- Project Period (FY)
  2022 – 2024
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Review Section
  
  Basic Section 52050:Embryonic medicine and pediatrics-related
- Research Institution
  Kawasaki Medical School
Neuropathological mechanism common to lysosomal sphingolipid storage disease and Parkinson's diseasePrincipal Investigator
- Principal Investigator
  
  Matsuda Junko
- Project Period (FY)
  2019 – 2021
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Review Section
  
  Basic Section 52050:Embryonic medicine and pediatrics-related
- Research Institution
  Kawasaki Medical School
Operating principle of cell polarity via membrane lipidPrincipal Investigator
- Principal Investigator
  
  Matsuda Junko
- Project Period (FY)
  2015 – 2017
- Research Category
  
  Grant-in-Aid for Challenging Exploratory Research
- Research Field
  
  Structural biochemistry
- Research Institution
  Kawasaki Medical School
Biological role of ceramide structure of glycosphingolipids in the small intestinal epithelial cellsPrincipal Investigator
- Principal Investigator
  
  Matsuda Junko
- Project Period (FY)
  2012 – 2015
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  General physiology
- Research Institution
  Kawasaki Medical School
  Tokai University
Function of sphingolipid in the nervous systemPrincipal Investigator
- Principal Investigator
  
  MATSUDA Junko
- Project Period (FY)
  2008 – 2010
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Neurochemistry/Neuropharmacology
- Research Institution
  Tokai University
Generation of the mouse model of neuronopathic Gaucher diseasse aiming the development of new therapy for the neurological involvementPrincipal Investigator
- Principal Investigator
  
  MATSUDA Junko
- Project Period (FY)
  2006 – 2007
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  Tokai University
Morphology of skin sensory nerve endings in mouse models of a genetic demyelinating disease.
- Principal Investigator
  
  EBARA Satomi
- Project Period (FY)
  2006 – 2007
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Dermatology
- Research Institution
  Meiji College of Oriental Medicine
Functional analyses of sphingolipids in the development, maintenance and diseases of the brain.
- Principal Investigator
  
  SUZUKI Kunihiko
- Project Period (FY)
  2005 – 2006
- Research Category
  
  Grant-in-Aid for Scientific Research (B)
- Research Field
  
  Neurochemistry/Neuropharmacology
- Research Institution
  Tokai University
Analysis of physiological function of sphingolipids in the nervous system using the new mouse models of lysosomal diseasesPrincipal Investigator
- Principal Investigator
  
  MATSUDA Junko
- Project Period (FY)
  2004 – 2005
- Research Category
  
  Grant-in-Aid for Scientific Research (C)
- Research Field
  
  Pediatrics
- Research Institution
  Tokai University
  The University of Tokushima
Clarification of the protective mechanisms of pregnancy to the phenotype of saposin A deficient mice, mouse model for a late-onset, chronic form of globoid cell leukodystrophy
- Principal Investigator
  
  KURODA Yasuhiro
- Project Period (FY)
  2002 – 2003
- Research Category
  
  Grant-in-Aid for Scientific Research (B)
- Research Field
  
  Pediatrics
- Research Institution
  The University of Tokushima

[Book] ライソゾーム病－最新の病態、診断、治療の進歩　改訂第2版　シアリドーシス2023
- Author(s)
  松田純子
- Total Pages
  4
- Publisher
  診断と治療社
- ISBN
  9784787825971
- Data Source
  KAKENHI-PROJECT-23K08792
[Book] 先天代謝異常症クリニカルファイル：ガラクトシアリドーシス2023
- Author(s)
  松田純子
- Total Pages
  3
- Publisher
  診断と治療社
- ISBN
  9784787825889
- Data Source
  KAKENHI-PROJECT-23K08792
[Book] ライソゾーム病－最新の病態、診断、治療の進歩　改訂　第2版：サポシン欠損症2023
- Author(s)
  松田純子
- Total Pages
  5
- Publisher
  診断と治療社
- ISBN
  9784787825971
- Data Source
  KAKENHI-PROJECT-23K08792
[Book] 糖鎖の新機能開発・応用ハンドブック．2015
- Author(s)
  松田純子
- Total Pages
  6
- Publisher
  （株）エヌ・ティ－・エス
- Data Source
  KAKENHI-PROJECT-24590285
[Book] 糖鎖蓄積症: 新機能開発・応用ハンドブック．－創薬・医療から食品開発まで－．2015
- Author(s)
  松田純子
- Total Pages
  6
- Publisher
  株）エヌ・ティ－・エス
- Data Source
  KAKENHI-PROJECT-15K14465
[Book] 糖鎖蓄積症．糖鎖の新機能開発・応用ハンドブック．－創薬・医療から食品開発まで－2015
- Author(s)
  松田純子
- Total Pages
  6
- Publisher
  株）エヌ・ティ－・エス
- Data Source
  KAKENHI-PROJECT-24590285
[Book] 別冊:神経症候群III一その他の神経疾患を含めて一[第2版]2014
- Author(s)
  松田純子
- Total Pages
  4
- Publisher
  日本臨牀
- Data Source
  KAKENHI-PROJECT-24590285
[Book] シアリドーシス．神経症候群Ⅲ．2014
- Author(s)
  松田純子
- Total Pages
  4
- Publisher
  日本臨牀
- Data Source
  KAKENHI-PROJECT-24590285
[Book] サポシン欠損症.ライソゾーム病-最新の病態、診断、治療の進歩2011
- Author(s)
  松田純子, 他
- Publisher
  診断と治療社(印刷中)
- Data Source
  KAKENHI-PROJECT-20500343
[Book] サポシン欠損症(ライソゾーム病-最新の病態、診断、治療の進歩)2011
- Author(s)
  松田純子
- Publisher
  診断と治療社(印刷中)
- Data Source
  KAKENHI-PROJECT-20500343
[Book] シアリドーシス(ライソゾーム病-最新の病態、診断、治療の進歩)2011
- Author(s)
  松田純子
- Publisher
  診断と治療社(印刷中)
- Data Source
  KAKENHI-PROJECT-20500343
[Book] Sphingolipid activator proteins. In Experimental Glycoscience : glycobiology(edited by Taniguchi, N. et al)2008
- Author(s)
  松田純子
- Publisher
  Springer
- Data Source
  KAKENHI-PROJECT-20500343
[Book] Sphingolipid activator proteins. In Experimental Glycoscience : glycobiology, edited by Taniguchi, N., et al.2008
- Author(s)
  Matsuda J.
- Total Pages
  5
- Publisher
  Springer
- Data Source
  KAKENHI-PROJECT-20500343
[Book] Lysosomal Storage Disorders, (edited by Barranger, J., Cabrera-Salazar, M.A.)2007
- Author(s)
  Matsuda J, et. al.
- Total Pages
  15
- Publisher
  Springer,New York..
- Data Source
  KAKENHI-PROJECT-18591169
[Book] Lysosomal Storage Disorders (edited by Barranger, J., Cabrera-Salazar, M.A.)2007
- Author(s)
  Matsuda J et al.
- Total Pages
  15
- Publisher
  Springer, New York.
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-17300122
[Book] Lysosomal Storage Disorders, (edited by Barranger, J., Cabrera-Salazar, M.A.)2007
- Author(s)
  Matsuda J, et. al.
- Total Pages
  15
- Publisher
  Springer,New York
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Book] Lysosomal Storage Disorders edited by Barranger,J.,Cabrera-Salazar,M.A.2006
- Author(s)
  Matsuda J et al.
- Total Pages
  15
- Publisher
  Spriger,New York.
- Data Source
  KAKENHI-PROJECT-17300122
[Book] Krabbe disease (globoid cell leukodystrophy). In Lysosomal Storage Disease.2006
- Author(s)
  Matsuda J, et al.
- Total Pages
  15
- Publisher
  Springer, New York
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-16591032
[Book] Krabbe disease (globoid cell leukodystrophy). Lysosomal Storage Disease.2006
- Author(s)
  Matsuda J, et al.
- Total Pages
  15
- Publisher
  Springer, New York
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-16591032
[Book] Lysosomal Storage Disorders edited by Barranger, J., Cabrera-Salazar, M.A.2006
- Author(s)
  Matsuda J et al.
- Total Pages
  15
- Publisher
  Springer, New York.
- Data Source
  KAKENHI-PROJECT-18591169
[Book] Functional Glycomics News Letter (No.7)-糖鎖フラッシュ号-2005
- Author(s)
  松田純子
- Total Pages
  8
- Publisher
  文部科学省科学研究費補助金特定領域研究糖鎖によるたんぱく質と分子複合体の機能調節領域代表古川鋼一
- Data Source
  KAKENHI-PROJECT-17300122
[Book] Functional Glycomics News Letter (No.7)-糖鎖フラッシュ号-2005
- Author(s)
  松田純子
- Total Pages
  8
- Publisher
  文部科学省科学研究費補助金特定領域研究糖鎖によるたんぱく質と分子複合体の機能調節領域代表古川鋼一
- Data Source
  KAKENHI-PROJECT-16591032
[Journal Article] Genetic ablation of Saposin-D in Krabbe disease eliminates psychosine accumulation but does not significantly improve demyelination2023
- Author(s)
  Takashi Watanabe, Kazuhito Tsuboi, Nobuaki Matsuda, Yuta Ishizuka, Shinji Go, Etsuko Watanabe, Ayaka Ono, Yasuo Okamoto, Junko Matsuda
- Journal Title
  
  Journal of Neurochemistry
  
  Volume: 166 Issue: 4 Pages: 720-746
- DOI
  10.1111/jnc.15876
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-22K08295, KAKENHI-PROJECT-23K07323, KAKENHI-PROJECT-23K08792, KAKENHI-PROJECT-23K10973
[Journal Article] Bifunctional DEGS2 has higher hydroxylase activity toward substrates with very-long-chain fatty acids in the production of phytosphingosine-ceramides2023
- Author(s)
  Ota Ai, Morita Hiroya, Naganuma Tatsuro, Miyamoto Masatoshi, Jojima Keisuke, Nojiri Koki, Matsuda Junko, Kihara Akio
- Journal Title
  
  Journal of Biological Chemistry
  
  Volume: 10 Issue: 4 Pages: 104603-104603
- DOI
  10.1016/j.jbc.2023.104603
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-22K06583, KAKENHI-PROJECT-22H04986, KAKENHI-PROJECT-23K08792
[Journal Article] Mass Spectrometry of Neutral Glycosphingolipids2023
- Author(s)
  Suzuki Akemi、Silsirivanit Atit、Watanabe Takashi、Matsuda Junko、Inamori Kei-ichiro、Inokuchi Jin-ichi
- Journal Title
  
  Methods in molecular biology
  
  Volume: 2613 Pages: 127-144
- DOI
  10.1007/978-1-0716-2910-9_11
- ISBN
  9781071629093, 9781071629109
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-21K15892, KAKENHI-PROJECT-23K08792, KAKENHI-PROJECT-20H03452
[Journal Article] Involvement of acid ceramidase in the degradation of bioactive N-acylethanolamines2021
- Author(s)
  Tsuboi Kazuhito、Tai Tatsuya、Yamashita Ryouhei、Ali Hanif、Watanabe Takashi、Uyama Toru、Okamoto Yoko、Kitakaze Keisuke、Takenouchi Yasuhiro、Go Shinji、Rahman Iffat Ara Sonia、Houchi Hitoshi、Tanaka Tamotsu、Okamoto Yasuo、Tokumura Akira、Matsuda Junko、Ueda Natsuo
- Journal Title
  
  Biochimica et Biophysica Acta (BBA) - Molecular and Cell Biology of Lipids
  
  Volume: 1866 Issue: 9 Pages: 158972-158972
- DOI
  10.1016/j.bbalip.2021.158972
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-19K07165, KAKENHI-PROJECT-19K07353, KAKENHI-PROJECT-19K08288, KAKENHI-PROJECT-19K08634, KAKENHI-PROJECT-19K11731, KAKENHI-PROJECT-20K19732, KAKENHI-PROJECT-18K06120, KAKENHI-PROJECT-20K11571, KAKENHI-PROJECT-21K15892
[Journal Article] Reduction in MIR-219 expression underlies cellular pathogenesis of oligodendrocytes in a mouse model of Krabbe disease.2021
- Author(s)
  Inamura N, Go S, Watanabe T, Takase H, Takakura N, Nakayama A, Takebayashi H, Matsuda J, Enokido Y.
- Journal Title
  
  Brain Pathology
  
  Volume: － Issue: 5 Pages: 12951-12951
- DOI
  10.1111/bpa.12951
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-19K08288, KAKENHI-PROJECT-20K08248, KAKENHI-PROJECT-18K06120, KAKENHI-PROJECT-19K08313, KAKENHI-PROJECT-20K08224, KAKENHI-PROJECT-21K15892
[Journal Article] 視覚障害を契機に副腎白質ジストロフィーと診断された1例2020
- Author(s)
  春石和子、三木淳司、荒木俊介、後藤克聡、赤池洋人、松田純子、尾内一信、桐生純一．
- Journal Title
  
  神経眼科
  
  Volume: 37 Pages: 165-170
- NAID
  130007871323
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19K08288
[Journal Article] Variants in saposin D domain of prosaposin gene linked to Parkinson’s disease2020
- Author(s)
  Oji Y, Hatano T, Ueno SI, Funayama M, Ishikawa KI, Okuzumi A, Noda S, Sato S, Satake W, Toda T, Li Y, Hino-Takai T, Kakuta S, Tsunemi T, Yoshino H, Nishioka K, Hattori T, Mizutani Y, Mutoh T, Yokochi F, et al.
- Journal Title
  
  Brain
  
  Volume: 143 Issue: 4 Pages: 1190-1205
- DOI
  10.1093/brain/awaa064
- Peer Reviewed / Open Access / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-19K08003, KAKENHI-PROJECT-19K22603, KAKENHI-PROJECT-19K16928, KAKENHI-PROJECT-19K17019, KAKENHI-PROJECT-18H04043, KAKENHI-PROJECT-18K15463, KAKENHI-PROJECT-19K08288, KAKENHI-PROJECT-18K07510, KAKENHI-PROJECT-19K23782
[Journal Article] 新生児マススクリーニングでC5-OH 持続高値例の遺伝子型についての検討2020
- Author(s)
  小林正久、松田純子、笹井英雄、石毛信之、大橋十也、井田博幸．
- Journal Title
  
  日本マススクリーニング学会誌
  
  Volume: 30 Pages: 53-57
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-19K08288
[Journal Article] Novel neuroblastoma amplified sequence (NBAS) mutations in a Japanese boy with fever-triggered recurrent acute liver failure.2019
- Author(s)
  Ono S, Matsuda J, Watanabe E, Akaike H, Teranishi H, Miyata I, Otomo T, Sadahira Y, Mizuochi T, Kusano H, Kage M, Ueno H, Yoshida K, Shiraishi Y, Chiba K, Tanaka H, Miyano S, Ogawa S, Hayashi Y, Kanegane H, Ouchi K.
- Journal Title
  
  Hum Genome Var.
  
  Volume: 7;6:2 Issue: 1 Pages: 1-9
- DOI
  10.1038/s41439-018-0035-5
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-17K10130, KAKENHI-PROJECT-19K08288, KAKENHI-PLANNED-15H05909, KAKENHI-PROJECT-19H05656
[Journal Article] A case of sitosterolemia due to compound heterozygous mutations in <i>ABCG5</i>: clinical features and treatment outcomes obtained with colestimide and ezetimibe2017
- Author(s)
  Ono S, Matsuda J, Saito A, Yamamoto Y, Fujimoto W, Shimizu H, Dateki S, Ouchi K.
- Journal Title
  
  Clinical Pediatric Endocrinology
  
  Volume: 26 Issue: 1 Pages: 17-23
- DOI
  10.1297/cpe.26.17
- NAID
  130005308194
- ISSN
  0918-5739, 1347-7358
- Language
  English
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-15K14465, KAKENHI-PROJECT-17K10053
[Journal Article] スフィンゴ脂質活性化タンパク質‐サポシン‐の生理機能と疾患2017
- Author(s)
  松田純子
- Journal Title
  
  生化学
  
  Volume: 89 Pages: 808-819
- NAID
  40021438669
- Open Access
- Data Source
  KAKENHI-PROJECT-15K14465
[Journal Article] Numerous intertriginous xanthomas in infant: A diagnostic clue for sitosterolemia.2016
- Author(s)
  Yamamoto T, Matsuda J, Dateki S, Ouchi K, Fujimoto W.
- Journal Title
  
  J Dermatol.
  
  Volume: 43 Issue: 11 Pages: 1340-1344
- DOI
  10.1111/1346-8138.13511
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-15K14465
[Journal Article] The effects of chemically synthesized saposin C onglucosylceramide-β-glucosidase.2015
- Author(s)
  Yoneshige A, Muto M, Watanabe T, Hojo H, Matsuda J.
- Journal Title
  
  Clinical Biochemistry
  
  Volume: 48 Issue: 16-17 Pages: 1177-1180
- DOI
  10.1016/j.clinbiochem.2015.06.004
- Peer Reviewed / Open Access
- Data Source
  KAKENHI-PROJECT-23700515, KAKENHI-PROJECT-15K14465, KAKENHI-PROJECT-15J03876, KAKENHI-PROJECT-24590285
[Journal Article] Improved high-fat diet-induced glucose intolerance by an oral administration of phytosphingosine.2013
- Author(s)
  Murakami I, Mitsutake S, Kobayashi N, Matsuda J, Suzuki A, Shigyo T, Igarashi Y.
- Journal Title
  
  Biosci Biotechnol Biochem.
  
  Volume: 77 Pages: 194-197
- NAID
  10031164712
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-24590285
[Journal Article] Endosomal sorting by Semaphorin 4A in retinal pigment epithelium supports photoreceptor survival.2012
- Author(s)
  Toyofuku T, Nojima S, Ishikawa T, Takamatsu H, Tsujimura T, Uemura A, Matsuda J, Seki T, Kumanogoh A
- Journal Title
  
  Genes Dev
  
  Volume: 26 Issue: 8 Pages: 816-829
- DOI
  10.1101/gad.184481.111
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-22689046, KAKENHI-PROJECT-23390069, KAKENHI-PROJECT-23790444, KAKENHI-PROJECT-24590285
[Journal Article] サポシン欠損と神経機能障害2011
- Author(s)
  松田純子
- Journal Title
  
  脳21「特集;糖鎖と神経疾患糖脂質」金芳堂 14
  
  Pages: 55-60
- Data Source
  KAKENHI-PROJECT-20500343
[Journal Article] サポシン欠損と神経機能障害2011
- Author(s)
  松田純子
- Journal Title
  
  脳21「特集;糖鎖と神経疾患糖脂質」金芳堂
  
  Volume: 14 Pages: 55-60
- Data Source
  KAKENHI-PROJECT-20500343
[Journal Article] Synthesis of the sphingolipid activator protein, saposin C, using an azido-protected O-acyl isopeptide as an aggregation-disrupting element.2011
- Author(s)
  Hojo H, Katayama H, Tano C, Nakahara Y, Yoneshige A, Matsuda J, Sohma Y, Kiso Y, Nakahara Y.
- Journal Title
  
  Tetrahedron Lett. 52
  
  Pages: 635-639
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-20500343
[Journal Article] A Mutation in the Saposin C Domain of the Sphingolipid Activator Protein (Prosaposin) Gene Causes Neurodegenerative Disease in Mice.2010
- Author(s)
  Yoneshige A, Suzuki K, Suzuki K, Matsuda J
- Journal Title
  
  J.Neurosci.Res. 88
  
  Pages: 2118-2134
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-20500343
[Journal Article] Developmental changes in glycolipids and synchronized expression of nutrient transporters in the mouse small intestine.2010
- Author(s)
  Yoneshige A, Sasaki A, Miyazaki M, Kojima N, Suzuki A, Matsuda J
- Journal Title
  
  J.Nutr.Biochem. 21
  
  Pages: 214-226
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-20500343
[Journal Article] Regional expression of prosaposin in the wild-type and saposin D-deficient mouse brain detected by an anti-mouse prosaposin-specific antibody.2009
- Author(s)
  Yoneshige A, Suzuki K, Kojima N, Matsuda J
- Journal Title
  
  Proceedings of the Japan Academy, Ser.B. 85
  
  Pages: 422-434
- NAID
  130000137985
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-20500343
[Journal Article] HPTLC-MS for rapid analysis of neutral glycosphingolipids.2008
- Author(s)
  Miyazaki M, Yoneshige A, Matsuda J, Kuroda Y, Kojima N, Suzuki A.
- Journal Title
  
  J AOAC Int. 91
  
  Pages: 1218-1226
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-20500343
[Journal Article] The function of sphingolipids in the nervous system : Lessons learnt from mouse models of specific sphingolipid activator protein deficiencies.2007
- Author(s)
  Matsuda J et al.
- Journal Title
  
  J. Neurochem. (in press)
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] The function of sphingolipids in the nervous system:Lessons learnt from mouse models of specific sphingolipid activator protein deficiencies.2007
- Author(s)
  Matsuda J, et. al.
- Journal Title
  
  J. Neurochem. 103
  
  Pages: 32-38
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-18591169
[Journal Article] The function of sphinggolipids in the nervous system : Lessons leamt from mouse models of specific sphingolpid activator protei deficiencies.2007
- Author(s)
  Matsuda J et al.
- Journal Title
  
  J.Neurochem. (in press)
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] The function of sphingolipids in the nervous system : Lessons learnt from mouse models of specific sphingolipid activator protein deficiencies2007
- Author(s)
  Matsuda J et al.
- Journal Title
  
  J. Neurochem in press
- Data Source
  KAKENHI-PROJECT-18591169
[Journal Article] Krabbe disease(Globoid cell leukodystrophy)2007
- Author(s)
  Matsuda, J., Suzuki, K
- Journal Title
  
  In Lysosomal Storage Disorders edited by Barranger, J., Cabrera-Sala7ar, M.A., Springer, New York
  
  Pages: 269-283
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Journal Article] The function of sphingolipids in the nervous system : Lessons learnt from mouse models of specific sphingolipid activator protein deficiencies2007
- Author(s)
  Matsuda, J., Yoneshige, A., Suzuki, K
- Journal Title
  
  J. Neurochem 103
  
  Pages: 32-38
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Journal Article] Krabbe disease (globoid cell leukodystrophy).2007
- Author(s)
  Matsuda J, Suzuki K.
- Journal Title
  
  Lysosomal Storage Disease., Springer, New York (in press)
  
  Pages: 15-15
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] The function of sphingolipids in the nervous system:Lessons learnt from mouse models of specific sphingolipid activator protein deficiencies2007
- Author(s)
  Matsuda J, et. al.
- Journal Title
  
  J.Neurochem. 103
  
  Pages: 32-38
- Description
  「研究成果報告書概要(和文)」より
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-18591169
[Journal Article] Combined saposin C and D deficiencies in mice lead to a neuronopathic phenotype, glucosylceramide and a-hydroxy ceramide accumulation, and altered prosaposin trafficking2007
- Author(s)
  Sun, Y., Witte, DP., Zamzow, M., Ran, H., Quinn, B., Matsuda, J., Grabowski, GA
- Journal Title
  
  Human Molecular Genetics 16
  
  Pages: 957-971
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Journal Article] Combined saposin C and D deficiencies in mice lead to a neuronopathic phenotype, glucosylceramide and α-hydroxy ceramide accumulation, and altered prosaposin trafficking.2007
- Author(s)
  Sun Y, Witte DP, Zamzow M, Ran H, Quinn B, Matsuda J, Grabowski GA.
- Journal Title
  
  Human Molecular Genetics 16
  
  Pages: 957-971
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] The function of sphingolipids in the nervous system : Lessons learnt from mouse models of specific sphingolipid activator protein deficiencies.2007
- Author(s)
  Matsuda J, Yoneshige A, Suzuki K.
- Journal Title
  
  Journal of Neurochemistry (in press)
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] スフィンゴリピドーシスの新たな疾患モデルマウスの作成;神経系におけるスフィンゴ糖脂質の生理機能の理解と神経病変治療法の開発をめざして.2006
- Author(s)
  松田純子
- Journal Title
  
  日本先天代謝異常学会雑誌 22
  
  Pages: 35-41
- NAID
  10016759751
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] スフィンゴリピドーシスの新たな疾患モデルマウスの作成;神経系におけるスフィンゴ糖脂質の生理機能の理解と神経病変治療法の開発をめざして2006
- Author(s)
  松田純子
- Journal Title
  
  日本先天代謝異常学会雑誌 22
  
  Pages: 35-41
- NAID
  10016759751
- Data Source
  KAKENHI-PROJECT-18591169
[Journal Article] スフィンゴリピドーシスの新たな疾患モデルマウスの作成 : 神経系におけるスフィンゴ糖脂質の生理機能の理解と神経病変治療法の開発をめざして.2006
- Author(s)
  松田純子
- Journal Title
  
  日本先天代謝異常学会雑誌 22
  
  Pages: 35-41
- NAID
  10016759751
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] GD3-and O-acetylated GD3-ganglopsides in the GM2 synthase-deficient mouse brain and their immunohistochemical localization.2006
- Author(s)
  Matsuda J et al.
- Journal Title
  
  Proc.Jpn.Acad.,Ser.B. 82
  
  Pages: 189-196
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] GD3-and O-acetylated GD3-ganglopsides in the GM2 synthase-deficient mouse brain and their immunohistochemical localization2006
- Author(s)
  Matsuda J, et. al.
- Journal Title
  
  Proc.Jpn.Acad., Ser.B. 82
  
  Pages: 189-196
- Description
  「研究成果報告書概要(和文)」より
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-18591169
[Journal Article] GD-and O-acetylated GD3-ganglopsides in the GM2 synthase-deficient mouse brain and their immunohistochemical localization2006
- Author(s)
  Matsuda J et al.
- Journal Title
  
  Proc. Jan. Acad., Ser. B. 82
  
  Pages: 189-196
- Data Source
  KAKENHI-PROJECT-18591169
[Journal Article] GD3-and O-acetylated GD3-ganglopsides in the GM2 synthase-deficient mouse brain and theii immunohistochemical localization2006
- Author(s)
  Matsuda, J., Vanier, MT., Popa, I., Portoukalian, J., Suzuki, K
- Journal Title
  
  Proc. Jpn. Acad, Ser. B 82
  
  Pages: 189-196
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Journal Article] GD3-and O-acetylated GD3-ganglopsides in the GM2 synthase-deficient mouse brain and their immunohistochemical localization.2006
- Author(s)
  Matsuda J, Vanier MT, Popa I, Portoukalian J, Suzuki K.
- Journal Title
  
  Proc. Jpn. Acad, Ser. B. 82
  
  Pages: 189-196
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] Generation of new mouse models for sphingolipidoses.2006
- Author(s)
  Matsuda J.
- Journal Title
  
  Japanese Journal for Inherited Metabolic Diseases. 22
  
  Pages: 35-41
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] GD3-and O-acetylated GD3-ganglopsides in the GM2 synthase-deficient mouse brain and their immunohistochemical localization.2006
- Author(s)
  Matsuda J et al.
- Journal Title
  
  Proc. Jpn. Acad., Ser. B. 82
  
  Pages: 189-196
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] 遺伝性脱髄疾患マウスモデルにおける三叉神経系皮膚神経の形態変化2006
- Author(s)
  榎原智美, 松田純子, 鈴木邦彦, 熊本賢三
- Journal Title
  
  解剖学雑誌 (Acta Anatomica Nipponica) 82・抄録
  
  Pages: 217-217
- Data Source
  KAKENHI-PROJECT-18591263
[Journal Article] Patterned cerebellar Purkinje cell death with accumulation of HFA-ceramide in the new mouse model of sphingolipidosis.2005
- Author(s)
  Matsuda J, Yamazaki A, Kido M, Toida K, Tadano-Aritomi K, Ishizuka I, Suzuki K.
- Journal Title
  
  Journal of Neurochemistry 94 (suppl.2)
  
  Pages: 227-227
- Data Source
  KAKENHI-PROJECT-16591032
[Journal Article] Patterned cerebellar Purkinje death with accumulation of HFA-ceramide in the new mouse model of sphingolipidosis.2005
- Author(s)
  Matsuda J, et al.
- Journal Title
  
  Journal of Neurochemistry 94(suppl.2)
  
  Pages: 227-227
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-16591032
[Journal Article] Apoptosis accompanied by up-regulation of TNF-a death pathway genes in the brain of Niemann-Pick type C disease.2005
- Author(s)
  Wu YP, Mizukami H, Matsuda J, Saito Y, Proia LR, Suzuki K.
- Journal Title
  
  Molecular Genetics and Metabolism 84
  
  Pages: 9-17
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] Hematopoietic cell transplantation ameliorates clinical phenotype and progression of the CNS pathology in the mouse model of late onset Krabbe disease.2005
- Author(s)
  Yagi T, Matsuda J, Tominaga K, Suzuki K, Suzuki K.
- Journal Title
  
  Journal of Neuropathology and Experimental Neurology 65
  
  Pages: 565-575
- Data Source
  KAKENHI-PROJECT-16591032
[Journal Article] Hematopoietic cell transplantation ameliorates clinical phenotype and progression of the CNS pathology in the mouse model of late onset Krabbe disease.2005
- Author(s)
  Yagi T, Matsuda J, Tominaga K, Suzuki K, Suzuki K.
- Journal Title
  
  Journal of Neuropathology and Experimental Neurology 65
  
  Pages: 565-575
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] Apoptosis accompanied by up-regulation of TNF-α death pathway genes in the brain of Niemann-Pick type C disease.2005
- Author(s)
  Wu YP, Mizukami H, Matsuda J, Saito Y, Proia LR, Suzuki K.
- Journal Title
  
  Molecular Genetics and Metabolism 84
  
  Pages: 9-17
- Data Source
  KAKENHI-PROJECT-16591032
[Journal Article] Patterned cerebellar Purkinje cell death with accumulation of HFA-ceramide in the new mouse model of sphingolipidosis.2005
- Author(s)
  Matsuda J, et al.
- Journal Title
  
  Journal of Neurochemistry 94 (suppl.2)
  
  Pages: 227-227
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-16591032
[Journal Article] Patterned cerebellar Purkinje cell death with accumulation of HFA-ceramide in the new mouse model of sphingolipidosis.2005
- Author(s)
  Matsuda J, Yamazaki A, Kido M, Toida K, Tadano-Aritomi K, Ishizuka I, Suzuki K.
- Journal Title
  
  Journal of Neurochemistry 94 (suppl.2)
  
  Pages: 227-227
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] Apoptosis accompanied by up-regulation of TNF-α death pathway genes in the brain of Niemann-Pick type C disease.2005
- Author(s)
  Wu YP, Mizukami H, Matsuda J, Saito Y, Proia LR, Suzuki K.
- Journal Title
  
  Molecular Genetics and Metabolism 84
  
  Pages: 9-17
- Data Source
  KAKENHI-PROJECT-17300122
[Journal Article] Comparative Clinico-Pathological study of saposin-A deficient (SAP-A-/-) and twitcher mice.2004
- Author(s)
  Yagi T, Matsuda J, et al.
- Journal Title
  
  J Neuropathol Exp Neurol. 63
  
  Pages: 721-734
- Data Source
  KAKENHI-PROJECT-16591032
[Journal Article] Genetic background markedly influences vulnerability of the hippocampal neuronal organization in the "twitcher" mouse model of globoid cell leukodystrophy.2004
- Author(s)
  Tominaga K, Matsuda J, et al.
- Journal Title
  
  J.Neurosci.Res. 77
  
  Pages: 507-516
- Data Source
  KAKENHI-PROJECT-16591032
[Journal Article] Mutation in saposin D domain of sphingolipid activator protein gene causes urinary system defects and cerebellar Purkinje cell degeneration with a ccumulation of hydroxy fatty acid-containing ceramide in the mouse.2004
- Author(s)
  Matsuda J, et al.
- Journal Title
  
  Human Molecular Genetics 13・21
  
  Pages: 2709-2723
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-16591032
[Journal Article] Mutation in saposin D domain of sphingolipid activator protein gene causes urinary system defects and cerebellar Purkinje cell degeneration with accumulation of hydroxy fatty acid-containing ceramide in the mouse.2004
- Author(s)
  Matsuda.J, et al.
- Journal Title
  
  Human Molecular Genetics 13
  
  Pages: 2709-2723
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-16591032
[Journal Article] Mutation in saposin D domain of sphingolipid activator protein gene causes urinary system defects and cerebellar Purkinje cell degeneration with accumulation of hydroxy fatty acid-containing cerarmide in the mouse.2004
- Author(s)
  Matsuda J, et al.
- Journal Title
  
  Hum.Mol.Genet. 13,21
  
  Pages: 2709-2723
- Data Source
  KAKENHI-PROJECT-16591032
[Journal Article] Apoptosis accompanied by up-regulation of TNF-a death pathway genes in the brain of Niemann-Pick type C disease.2004
- Author(s)
  Wu YP, Mizukami H, Matsuda J, et al.
- Journal Title
  
  Mol.Genet.Metab. 84
  
  Pages: 9-17
- Data Source
  KAKENHI-PROJECT-16591032
[Presentation] 質量分析計を用いたKrabbe病モデルマウスのスフィンゴ脂質の定量解析2023
- Author(s)
  渡邉　昂, 石塚佑太, 松田純子
- Organizer
  第64回日本先天代謝異常学会学術集会
- Data Source
  KAKENHI-PROJECT-23K07323
[Presentation] プロサポシントランスジェニックマウスにおける網膜視細胞変性の解析2023
- Author(s)
  石塚佑太　鎌尾浩行　渡邉昂　小野公嗣　大塚正人　松田純子
- Organizer
  第66回日本神経化学会大会
- Data Source
  KAKENHI-PROJECT-22K07856
[Presentation] プロサポシン過剰発現マウス網膜における選択的視細胞死の解析2023
- Author(s)
  石塚佑太　鎌尾浩行　渡邉昂　小野公嗣　大塚正人　松田純子
- Organizer
  第64回日本先天代謝異常学会学術集会
- Data Source
  KAKENHI-PROJECT-22K07856
[Presentation] 膀胱上皮組織には炭素数20の長鎖塩基からなるフィトセラミド構造をもつスフィンゴ糖脂質が豊富に存在する．2023
- Author(s)
  松田純子、渡邉昂、鈴木明身、郷慎司、大平伸、森谷卓也．
- Organizer
  第65回日本生化学会（福岡）
- Data Source
  KAKENHI-PROJECT-23K08792
[Presentation] 膀胱移行上皮には炭素数20のフィトセラミド構造が豊富に存在し構造維持に重要である．2023
- Author(s)
  渡邉昂、鈴木明身、大平伸、郷慎司、石塚佑太、森谷卓也、宮地禎幸、永井敦、松田純子．
- Organizer
  第64回日本生化学会中国・四国支部例会（松山）
- Data Source
  KAKENHI-PROJECT-23K08792
[Presentation] フィトセラミド構造は小腸上皮における脂質吸収に重要である．2023
- Author(s)
  渡邉昂、鈴木明身、石塚佑太、松田純子．
- Organizer
  第65回日本脂質生化学会（熊本）
- Data Source
  KAKENHI-PROJECT-23K08792
[Presentation] サポシンD欠損Twitcherマウスの神経病態はサイコシンの蓄積だけでは説明できない2023
- Author(s)
  渡辺昂, 坪井一人, 石塚佑太, 松田純子
- Organizer
  第96回日本生化学会大会
- Data Source
  KAKENHI-PROJECT-23K07323
[Presentation] Krabbe病の神経病態はサイコシンの蓄積だけでは説明できない2023
- Author(s)
  松田純子, 渡邉　昂, 坪井一人, 郷　慎司, 石塚佑太
- Organizer
  第65回日本脂質生化学会
- Data Source
  KAKENHI-PROJECT-23K07323
[Presentation] 小児代謝疾患における神経変性のメカニズム2021
- Author(s)
  松田純子
- Organizer
  第20回高松国際パーキンソン病シンポジウム in TOKYO
- Invited / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-19K08288
[Presentation] マイクロRNAがクラッベ病モデルマウスのオリゴデンドロサイトの発達異常を改善する2021
- Author(s)
  稲村直子, 郷慎司, 渡辺　昂, 高瀬弘嗣, 中山敦雄, 竹林浩秀, 松田純子, 榎戸靖
- Organizer
  第44回日本分子生物学会
- Data Source
  KAKENHI-PROJECT-19K08288
[Presentation] サポシンD欠損マウスを用いた酸性セラミダーゼのN-アシルエタノールアミン加水分解活性の検討2021
- Author(s)
  坪井一人、渡邉　昂、北風圭介、竹之内康広、松田純子、岡本安雄
- Organizer
  第94回日本生化学会大会
- Data Source
  KAKENHI-PROJECT-19K08288
[Presentation] Krabbe病の病態は「サイコシン仮説」のみでは説明できない2021
- Author(s)
  渡邉　昂、郷　慎司、坪井一人、小野綾可、松田純子
- Organizer
  第62回日本先天代謝異常大会
- Data Source
  KAKENHI-PROJECT-19K08288
[Presentation] 小児代謝疾患（スフィンゴリピドーシス）における神経変性のメカニズム2021
- Author(s)
  松田純子
- Organizer
  The 20th Takamatsu International Symposium for PD & MD in Tokyo
- Invited / Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-19K08288
[Presentation] サポシンD変異マウスの神経病態解析2019
- Author(s)
  松田純子、渡邉悦子、郷　慎司
- Organizer
  第61回日本先天代謝異常学会総会
- Data Source
  KAKENHI-PROJECT-19K08288
[Presentation] サポシンD変異マウスの神経病態解析2019
- Author(s)
  松田純子、渡邉悦子、郷　慎司
- Organizer
  第92回日本生化学会大会
- Data Source
  KAKENHI-PROJECT-19K08288
[Presentation] サポシンD変異マウスの神経病態解析2019
- Author(s)
  松田純子、渡邉悦子、郷　慎司
- Organizer
  第38回日本糖質学会年会
- Data Source
  KAKENHI-PROJECT-19K08288
[Presentation] サポシンD変異マウス脳ではプロサポシンがオリゴマー化する2019
- Author(s)
  渡邉悦子、郷　慎司、松田純子
- Organizer
  第92回日本生化学会大会
- Data Source
  KAKENHI-PROJECT-19K08288
[Presentation] O-GlcNAc修飾を介したスフィンゴ糖脂質代謝制御機構2017
- Author(s)
  郷　慎司、松田　純子、井ノ口　仁一
- Organizer
  第36回日本糖質学会
- Data Source
  KAKENHI-PROJECT-15K14465
[Presentation] Krabbe病（グロボイド細胞白質ジストロフィー）モデルマウスでみられるオリゴデンドロサイトの分化ならびにミエリン化の異常2017
- Author(s)
  稲村直子、鬼頭ももこ、浅井清文、竹林浩秀、細川昌則、松田純子、榎戸　靖
- Organizer
  生命科学系学会合同年次大会　ConBio2017
- Data Source
  KAKENHI-PROJECT-15K14465
[Presentation] スフィンゴ糖脂質の機能と疾患2016
- Author(s)
  松田純子
- Organizer
  日本小児科学会岡山地方会
- Place of Presentation
  岡山県岡山市北区奉還町（岡山国際交流センター）
- Invited
- Data Source
  KAKENHI-PROJECT-15K14465
[Presentation] Septo-Optic Dysplasiaの2症例2016
- Author(s)
  小野佐保子、松田純子、河野美奈、赤池洋人、荻田聡子、升野光雄、尾内一信
- Organizer
  日本小児内分泌学会学術集会
- Place of Presentation
  東京都千代田区丸の内（東京国際フォーラム）
- Year and Date
  2016-11-16
- Data Source
  KAKENHI-PROJECT-15K14465
[Presentation] Central nervous system pathology in the phytosphingolipid-deficient mouse2015
- Author(s)
  Matsuda J, Ono K, Watanabe T, Yoneshige A, Muto M, Suzuki A.
- Organizer
  25th Biennial Meeting of the International Society for Neurochemistry.
- Place of Presentation
  Cairns, Australia
- Year and Date
  2015-08-23
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-24590285
[Presentation] スフィンゴ糖脂質セラミド骨格の構造多様性が担う生物機能の解明．2015
- Author(s)
  松田純子、小野公嗣、渡辺　昂、鈴木明身．
- Organizer
  第20回日本ライソゾーム病研究会
- Place of Presentation
  東京慈恵会医科大学〈東京都・港区）
- Year and Date
  2015-10-02
- Data Source
  KAKENHI-PROJECT-15K14465
[Presentation] Central nervous system pathology in the phytosphingolipid-deficient mouse.2015
- Author(s)
  Matsuda J, Ono K, Watanabe T, Yoneshige A, Muto M, Suzuki A.
- Organizer
  25th Biennial Meeting of the International Society for Neurochemistry.
- Place of Presentation
  Cairns, Australia.
- Year and Date
  2015-08-23
- Int'l Joint Research
- Data Source
  KAKENHI-PROJECT-15K14465
[Presentation] スフィンゴ糖脂質セラミド骨格の構造多様性が担う生物機能の解明2015
- Author(s)
  松田純子、小野公嗣、渡辺　昂、鈴木明身．
- Organizer
  第20回日本ライソゾーム病研究会
- Place of Presentation
  東京慈恵会医科大学（東京都・港区）
- Year and Date
  2015-10-02
- Data Source
  KAKENHI-PROJECT-24590285
[Presentation] Role of hydroxylation at sphinganine C-4 of glycosphingolipids in the mouse.2012
- Author(s)
  Matsuda J, Watanabe T, Yoneshige A, Koike A, Mutou M, Suzuki A.
- Organizer
  The 26th International Carbohydrate Symposium (ICS2012), P583, Madrid, Spain.
- Place of Presentation
  スペイン（マドリード）
- Data Source
  KAKENHI-PROJECT-24590285
[Presentation] スフィンゴ糖脂質セラミド骨格の構造多様性と生物機能に関する研究2012
- Author(s)
  渡辺昂、米重あづさ、小池礼華、武藤真長、Hama,H.、鈴木明身、松田純子
- Organizer
  第54回日本脂質生化学会
- Place of Presentation
  福岡、九州大学医学部百年講堂
- Data Source
  KAKENHI-PROJECT-24590285
[Presentation] マウス消化管におけるスフィンゴ糖脂質のセラミド構造の発現制御2010
- Author(s)
  渡辺昂,米重あづさ,武藤真長,鈴木明身,松田純子
- Organizer
  BMB2010第33回日本分子生物学会年会・第83回日本生化学会大会合同大会
- Place of Presentation
  神戸
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] The differential ceramide structures of glycosphingolipids and their regulations in the mouse gastrointestinal tract2010
- Author(s)
  Watanabe T, Yoneshige A, Suzuki A, Matsuda J
- Organizer
  The 25^<th> International Carbohydrate Symposium (ICS2010).
- Place of Presentation
  Makuhari, Japan
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] サポシンC欠損twitcherマウスにおける領域特異的な神経細胞死の解析2010
- Author(s)
  米重あづさ,渡辺昂,武藤真長,松田純子
- Organizer
  BMB2010第33回日本分子生物学会年会・第83回日本生化学会大会合同大会
- Place of Presentation
  神戸
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] 微量成分セラミドのマウス大脳ガングリオシド構造解析2010
- Author(s)
  立花徳啓,松田純子,八巻聡,鈴木明身
- Organizer
  BMB2010第33回日本分子生物学会年会・第83回日本生化学会大会合同大会
- Place of Presentation
  神戸
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] Lack of prosaposin in mice causes embryonic lethal phenotype and placental dysgenesis.2010
- Author(s)
  Mutou M, Yoneshige A, Matsuda J
- Organizer
  The 25^<th> International Carbohydrate Symposium (ICS2010).
- Place of Presentation
  Makuhari, Japan
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] クラッベ病モデルマウスにおけるラクトシルセラミドの蓄積と神経細胞死2010
- Author(s)
  松田純子,米重あづさ,武藤真長,渡辺昂
- Organizer
  第15回日本ライソゾーム病研究会
- Place of Presentation
  東京
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] マウス胚発生におけるプロサポシンの役割2010
- Author(s)
  武藤真長,米重あづさ,渡辺昂,松田純子
- Organizer
  BMB2010第33回日本分子生物学会年会・第83回日本生化学会大会合同大会
- Place of Presentation
  神戸
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] The differential ceramide structures of glycosphingolipids and their regulations in the mouse gastrointestinal tract.2010
- Author(s)
  Yoneshige A, Watanabe T, Suzuki A, Matsuda J
- Organizer
  Naito conference : Glycan Expression and Regulation [I] : Functions and Disease mechanisms.
- Place of Presentation
  Kanagawa, Japan
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] Deficiency of saposin C in the mouse model of Krabbe disease showed neurodegeneration with accumulation of lactosylceramide2010
- Author(s)
  Yoneshige A, Matsuda J
- Organizer
  The 25^<th> International Carbohydrate Symposium (ICS2010).
- Place of Presentation
  Makuhari, Japan
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] The role of sphingolipid activator protein, saposins A-D in the nervous system : lessons learnt from mouse models of specific saposin deficiencies.2010
- Author(s)
  Matsuda J, Yoneshige A
- Organizer
  Naito conference : Glycan Expression and Regulation [I] : Functions and Disease mechanisms
- Place of Presentation
  Kanagawa, Japan
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] ラクトシルセラミドの蓄積と神経細胞死2010
- Author(s)
  松田純子
- Organizer
  弟8回糖鎖科学コンソーシアムシンポジウム
- Place of Presentation
  東京・品川
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] マウス胚発生におけるプロサポシンの役割2010
- Author(s)
  松田純子,武藤真長,米重あづさ,渡辺昂
- Organizer
  第52回日本先天代謝異常学会
- Place of Presentation
  大阪
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] Mutation in saposin C domain of sphingolipid activator protein (prosaposin) gene causes neurodegenerative disease in the mouse.2009
- Author(s)
  Yoneshige A, Suzuki K, Suzuki K, Matsuda J
- Organizer
  第3回国際ライソゾーム病シンポジウム
- Place of Presentation
  名古屋
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] Role of hydroxylation at sphinganine C-4 of glycosphingolipids in the mouse2009
- Author(s)
  Matsuda J., et al.
- Organizer
  第82回日本生化学会大会
- Place of Presentation
  神戸ポートアイランド(兵庫県)
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] ジヒドロセラミド:スフィンガニンC4-水酸化酵素(DES2)ノックアウトマウスは腎臓および消化管のフィトスフィンゴ脂質を欠く.2009
- Author(s)
  渡辺昂、米重あづさ、鈴木明身、松田純子
- Organizer
  第82回日本生化学会大会
- Place of Presentation
  神戸
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] サポシンC欠損twitcherマウスは重症化する2009
- Author(s)
  米重あづさ、渡辺昂、松田純子
- Organizer
  第82回日本生化学会大会
- Place of Presentation
  神戸
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] Mutation in saposin C domain of sphingolipid activator protein (prosaposin) gene causes neurodegenerative disease in the mouse.2009
- Author(s)
  Yoneshige A, Suzuki K, Suzuki K, Matsuda J
- Organizer
  Neuroscience 2009 Chicago
- Place of Presentation
  USA
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] Synthetic Study of Sphingolipid Activator Glycoprotein, Saposin C.2009
- Author(s)
  Hojo H, Katayama H, Onuma Y, Nakahara Y, Yoneshige A, Matsuda J, Nakahara Y
- Organizer
  第46回ペプチド討論会
- Place of Presentation
  福岡
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] Role of hydroxylation at sphinganine C-4 of glycosphingolipids in the mouse.2009
- Author(s)
  Matsuda J, Yoneshige A, Suzuki A
- Organizer
  第82回日本生化学会大会
- Place of Presentation
  神戸
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] Mutation in saposin C domain of sphingolipid activator protein (prosaposin) gene causes neurodegenerative disease in the mouse2009
- Author(s)
  Yoneshige A, Suzuki K, Suzuki K, Matsuda J
- Organizer
  22^<nd> Biennial Meeting of the International Society for Neurochemistry.
- Place of Presentation
  Busan, Korea
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] サポシンC欠損マウスは神経変性疾患を発症する2008
- Author(s)
  松田純子、米重あづさ、佐々木彩乃
- Organizer
  第50回日本先天代謝異常学会米子市
- Place of Presentation
  鳥取県
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] 新生仔マウス小腸におけるスフィンゴ糖脂質組成の発達変化:トランスポーターの発現変化との関係2008
- Author(s)
  松田純子、米重あづさ、鈴木明身
- Organizer
  BMB2008第31回日本分子生物学会年会・第81回日本生化学会大会合同大会
- Place of Presentation
  神戸
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] 新生仔マウス小腸におけるスフィンゴ糖脂質組成の発達変化 : トランスポーターの発現変化との関係2008
- Author(s)
  松田純子, 他
- Organizer
  第31回日本分子生物学会年会・第81回日本生化学会大会合同大会
- Place of Presentation
  神戸(兵庫県)
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] サポシンC欠損マウスは神経変性疾患を発症する2008
- Author(s)
  米重あづさ、松田純子
- Organizer
  BMB2008第31回日本分子生物学会年会・第81回日本生化学会大会合同大会
- Place of Presentation
  神戸
- Data Source
  KAKENHI-PROJECT-20500343
[Presentation] Generation of th(anti-mouse prosaposin specific antibody : Regiona accumulation of prosaposin in the hippocampus of saposin D knockout mouse2007
- Author(s)
  Matsuda, J., Yoneshige, A., Suzuki, K
- Organizer
  The 57th Annual Meeting of the American Sciety of Human Genetics
- Place of Presentation
  San Diego, California, USA
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Presentation] 遺伝性脱髄疾患マウスモデルにおける三叉神経系皮膚感覚神経の形態変化2007
- Author(s)
  榎原智美、熊本賢三、松田純子、鈴木邦彦
- Organizer
  第112回日本解剖学会全国学術集会
- Place of Presentation
  大阪国際会議場
- Year and Date
  2007-03-28
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-18591263
[Presentation] Generation of the anti-mouse prosaposin specific antibody:Regional accumulation of prosaposin in the hippocampus of saposin D knockout mouse.2007
- Author(s)
  Matsuda J, et. al.
- Organizer
  The 57th Annual Meeting of the American Sciety of Human Genetics.
- Place of Presentation
  San Diego,California,USA.
- Data Source
  KAKENHI-PROJECT-18591169
[Presentation] Generation of the anti-mouse prosaposin specific antibody:Regional accumulation of prosaposin in the hippocampus of saposin D knockout mouse2007
- Author(s)
  Matsuda J, et. al.
- Organizer
  The 57th Annual Meeting of the American Sciety of Human Genetics
- Place of Presentation
  San Diego,California,USA
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Presentation] Patterned cerebellar Purkinje cell degeneration in mouse models of saposin D deficiency and Niemann-Pick type C disease is associated with selective expression of sphingosine kinase2007
- Author(s)
  Yoneshige, A., Sasaki, A., Suzuki, K., Matsuda, J
- Organizer
  International Symposium of Lysosomal Storage Diseases
- Place of Presentation
  Tokyo, Japan
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Presentation] Pattemec cerebellar Purkinje cell degeneration in mouse models of saposin D deficiency and Niemann-Pick type C disease h associated with selective expression of sphingosine kinase2007
- Author(s)
  Yoneshige, A., Matsuda, J., Sasaki, A., Suzuki, K
- Organizer
  The 57th Annual Meeting of the American Sciety of Human Genetics
- Place of Presentation
  San Diego California IJSA
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Presentation] Morphology of demyelination in the trigeminal nerve of twitcher mouse, a genetic model of human Krabbe disease2007
- Author(s)
  Satomi Ebara, Junko Matsuda, Kunihiko Suzuki, Kenzo Kumamoto
- Organizer
  112th Annual Meeting of Japan Association of Anatomists
- Place of Presentation
  Osaka International Convention Center
- Year and Date
  2007-03-28
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-18591263
[Presentation] Prosaposin is up-regulated in thebrain and placenta of lysosomal storage disorders(LSDs) in the mouse : Possible markers for the neonatal screening for LSDs ?2006
- Author(s)
  Matsuda, J., Yoneshige, A., Kubo, N., Suzuki, K
- Organizer
  The 6th meeting of the international society for neonatal screening
- Place of Presentation
  Awaji, Hyogo and Tokushima, Japan
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Presentation] Prosaposin is up-regulated in thebrain and placenta of lysosomal storage disorders (LSDs) in the mouse:Possible markers for the neonatal screening for LSDs2006
- Author(s)
  Matsuda J, et. al.
- Organizer
  The 6th meeting of the international society for neonatal screening
- Place of Presentation
  Awaji,Hyogo and Tokushima,Japan
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Presentation] The function of sphingolipid in the nervous system : Lessons learnt from mouse models of specific sphingolipid activator protein deficiency2006
- Author(s)
  Matsuda, J., Suzuki, K
- Organizer
  Second Special Meeting of the International Society of Neurochemistry, on Neural Glycoproteins and Glycoproteins
- Place of Presentation
  Antigua, West Indies
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Presentation] Generation of a specific anti-mouse prosaposin antibody : Specific up-regulation of prosaposin in the brain of saposin D knockout mouse2006
- Author(s)
  Yoneshige, A., Kubo, N., Suzuki, K., Matsuda, J
- Organizer
  The 20th IUBMB International Congress of Biochemistry and Molecular Biology and 11th FAOBMB Congress
- Place of Presentation
  Kyoto. Japan
- Description
  「研究成果報告書概要(欧文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Presentation] The function of sphingolipid in the nervous system:Lessons learnt from mouse models of specific sphingolipid activator protein deficiency2006
- Author(s)
  Matsuda J, et. al.
- Organizer
  Second Special Meeting of the International Society of Neurochemistry, on Neural Glycoproteins and Glycoproteins
- Place of Presentation
  Antigua,West Indies
- Description
  「研究成果報告書概要(和文)」より
- Data Source
  KAKENHI-PROJECT-18591169
[Presentation] プロサポシン過剰発現マウスは網膜視細胞変性を呈する
- Author(s)
  松田純子、小野公嗣、武藤真長、米重あづさ
- Organizer
  第87回日本生化学会大会
- Place of Presentation
  京都（国立京都国際会館）
- Year and Date
  2014-10-15 – 2014-10-18
- Data Source
  KAKENHI-PROJECT-24590285
[Presentation] Over expression of prosaposin causes severe retinal degeneration in mouse.
- Author(s)
  Matsuda J, Ono K, Muto M, Yoneshige A, Yoshimura S.
- Organizer
  第55回日本先天代謝異常学会
- Place of Presentation
  千葉（東京ベイ舞浜ホテルクラブリゾート）
- Data Source
  KAKENHI-PROJECT-24590285
[Presentation] スフィンゴ糖脂質のセラミド骨格の構造多様性が担う生物機能
- Author(s)
  松田純子
- Organizer
  第56回日本脂質生化学会
- Place of Presentation
  大阪（近畿大学東大阪キャンパス）
- Year and Date
  2014-06-06 – 2014-06-07
- Data Source
  KAKENHI-PROJECT-24590285
[Presentation] スフィンゴ糖脂質のセラミド骨格の構造多様性が担う生物機能
- Author(s)
  松田純子
- Organizer
  第56回日本日本脂質生化学会
- Place of Presentation
  大阪（近畿大学）
- Invited
- Data Source
  KAKENHI-PROJECT-24590285
[Presentation] Saposin D欠損マウスの2D-DIGEタンパク質発現解析 - 炭酸脱水酵素(CA2)との関連
- Author(s)
  久樹晴美、只野－有冨桂子、宮川誠、内田俊也、松田純子、戸田年総、岡崎具樹
- Organizer
  第86回日本生化学会大会
- Place of Presentation
  神奈川（横浜パシフィコ）
- Data Source
  KAKENHI-PROJECT-24590285
[Presentation] プロサポシンノックアウトマウス網膜の組織病理学的解析
- Author(s)
  小野公嗣、武藤真長、米重あづさ、松田純子
- Organizer
  第87回日本生化学会大会
- Place of Presentation
  京都（国立京都国際会館）
- Year and Date
  2014-10-15 – 2014-10-18
- Data Source
  KAKENHI-PROJECT-24590285
[]
[]

1. SUZUKI Kunihiko (30384895)

# of Collaborated Projects: 3 results

# of Collaborated Products: 19 results
2. KURODA Yasuhiro (20035471)

# of Collaborated Projects: 2 results

# of Collaborated Products: 0 results
3. 渡邉昂 (60817071)

# of Collaborated Projects: 2 results

# of Collaborated Products: 6 results
4. SUZUKI Akemi (70134533)

# of Collaborated Projects: 1 results

# of Collaborated Products: 14 results
5. ITO Michinori (40211057)

# of Collaborated Projects: 1 results

# of Collaborated Products: 0 results
6. TOIDA Kazunori (40253405)

# of Collaborated Projects: 1 results

# of Collaborated Products: 1 results
7. EBARA Satomi (20203648)

# of Collaborated Projects: 1 results

# of Collaborated Products: 3 results
8. KUMAMOTO Kenzo (20141509)

# of Collaborated Projects: 1 results

# of Collaborated Products: 3 results
9. ONO Koji (00548597)

# of Collaborated Projects: 1 results

# of Collaborated Products: 3 results
10. 渡邉悦子 (70378610)

# of Collaborated Projects: 1 results

# of Collaborated Products: 6 results
11. 石塚佑太 (50614179)

# of Collaborated Projects: 1 results

# of Collaborated Products: 2 results
12. 鎌尾浩行 (30388946)

# of Collaborated Projects: 1 results

# of Collaborated Products: 2 results
13. HOUCHI Hajime

# of Collaborated Projects: 0 results

# of Collaborated Products: 1 results
14. FUNAYAMA Manabu

# of Collaborated Projects: 0 results

# of Collaborated Products: 1 results
15. 坪井一人

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16. 竹之内康広

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17. 植村明嘉

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18. 岡本安雄

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19. 永沼達郎

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20. 林泰秀

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# of Collaborated Products: 1 results
21. 米重あづさ

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# of Collaborated Products: 1 results

Matsuda Junko 松田 純子

MATSUDA Junko 松田 純子

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クラッベ病の病態を悪化させるメカニズムの探索

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Structural diversity of ceramide moiety responsible for apical membrane function of bladder transitional epithelial cellsPrincipal Investigator

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Elucidation of novel functions of prosaposin in autophagy

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Neuropathological mechanism common to lysosomal sphingolipid storage disease and Parkinson's diseasePrincipal Investigator

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Operating principle of cell polarity via membrane lipidPrincipal Investigator

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Biological role of ceramide structure of glycosphingolipids in the small intestinal epithelial cellsPrincipal Investigator

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Function of sphingolipid in the nervous systemPrincipal Investigator

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Generation of the mouse model of neuronopathic Gaucher diseasse aiming the development of new therapy for the neurological involvementPrincipal Investigator

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Morphology of skin sensory nerve endings in mouse models of a genetic demyelinating disease.

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Functional analyses of sphingolipids in the development, maintenance and diseases of the brain.

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Analysis of physiological function of sphingolipids in the nervous system using the new mouse models of lysosomal diseasesPrincipal Investigator

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Clarification of the protective mechanisms of pregnancy to the phenotype of saposin A deficient mice, mouse model for a late-onset, chronic form of globoid cell leukodystrophy

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[Book] ライソゾーム病－最新の病態、診断、治療の進歩 改訂第2版 シアリドーシス2023

Author(s)

Total Pages

Matsuda Junko 松田純子

MATSUDA Junko 松田純子

[Book] ライソゾーム病－最新の病態、診断、治療の進歩　改訂第2版　シアリドーシス2023

[Book] ライソゾーム病－最新の病態、診断、治療の進歩　改訂　第2版：サポシン欠損症2023