MORI Akira 森麗

Researcher Number	70608877
Other IDs
Affiliation (based on the past Project Information) *help	2014 – 2015: 熊本大学, 医学部附属病院, 非常勤診療医師 2013: 熊本大学, 医学部附属病院, 特任助教 2011 – 2012: 熊本大学, 医学部附属病院, 医員
Review Section/Research Field	Principal Investigator Neurology
Keywords	Principal Investigator 運動ニューロン / 小胞体ストレス / 筋萎縮性側索硬化症 / FUS / TDP-43 / NB2a細胞 / 遺伝子治療 / 変異SOD1 / 小胞体関連分野 / iPS細胞 … More / induced Pluripotent Stem (iPS) 細胞 / アデノ随伴ウイルス / 神経細胞死 / 変異 SOD1 / Derlin-1 Less

Is endoplasmic reticulum stress essential for motor neuron degeneration?Principal Investigator
- Principal Investigator
  
  Mori Akira
- Project Period (FY)
  2013 – 2015
- Research Category
  
  Grant-in-Aid for Young Scientists (B)
- Research Field
  
  Neurology
- Research Institution
  Kumamoto University
Gene therapy for neuromuscular diseasePrincipal Investigator
- Principal Investigator
  
  MORI Akira
- Project Period (FY)
  2011 – 2012
- Research Category
  
  Grant-in-Aid for Research Activity Start-up
- Research Field
  
  Neurology
- Research Institution
  Kumamoto University

All 2015 2013 2012 2011

All Journal Article Presentation

[Journal Article] Clinicopathological features of the first Asian family having vocal cord and pharyngeal weakness with distal myopathy due to a MATR3 mutation.2015
- Author(s)
  Yamashita S, Mori A, Nishida Y, Kurisaki R, Tawara N, Nishikami T, Misumi Y, Ueyama H, Imamura S, Higuchi Y, Hashiguchi A, Higuchi I, Morishita S, Yoshimura J, Uchino M, Takashima H, Tsuji S, Ando Y.
- Journal Title
  
  Neuropathol Appl Neurobiol
  
  Volume: 41 Issue: 3 Pages: 391-398
- DOI
  10.1111/nan.12179
- Peer Reviewed / Acknowledgement Compliant / Open Access
- Data Source
  KAKENHI-PROJECT-24591269, KAKENHI-PROJECT-25860718, KAKENHI-PROJECT-26860674, KAKENHI-PROJECT-221S0002
[Journal Article] Muscle biopsy findings predictive of malignancy in rare infiltrative dermatomyositis2013
- Author(s)
  Uchino M, Yamashita S, Uchino K, Mori A, Hara A, Suga T, Hirahara T, Koide T, Kimura E, Yamashita T, Ueda A, Kurisaki R, Suzuki J, Honda S, Maeda Y, Hirano T, Ando Y
- Journal Title
  
  Clin Neurol Neurosurg
  
  Volume: 115(5) Issue: 5 Pages: 603-6
- DOI
  10.1016/j.clineuro.2012.07.019
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-23500430, KAKENHI-PROJECT-23890163, KAKENHI-PROJECT-24591269, KAKENHI-PROJECT-24591284, KAKENHI-PROJECT-24790891, KAKENHI-PROJECT-25860718
[Journal Article] Significant CMAP decrement by repetitive nerve stimulation is more frequent in median than ulnar nerves of patients with amyotrophic lateral sclerosis2012
- Author(s)
  Satoshi Yamashita, Hideya Sakaguchi, Akira Mori
- Journal Title
  
  Muscle Nerve
  
  Volume: 45 Issue: 3 Pages: 426-428
- DOI
  10.1002/mus.22301
- NAID
  120005123115
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-23890163, KAKENHI-PROJECT-24591269, KAKENHI-PROJECT-24591284
[Journal Article] Significant CMAP decrement byrepetitive nerve stimulation is morefrequent in median than ulnar nerves ofpatients with amyotrophic lateralsclerosis2012
- Author(s)
  Satoshi Yamashita, HideyaSakaguchi, Akira Mori, En Kimura, MaedaYasushi, Hirano Teruyuki, Uchino Makoto
- Journal Title
  
  Muscle Nerve
  
  Volume: 45(3) Pages: 426-8
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-23890163
[Journal Article] Muscle biopsy findings predictive ofmalignancy in rare infiltrativedermatomyositis.2012
- Author(s)
  Makoto Uchino, Satoshi Yamashita, Katshhisa Uchino, Akira Mori, Akio Hara, Tomohiro Suga, Tomoo Hirahara, Tatsuya Koide, En Kimura, Taro Yamashita, Akihiko Ueda, Reiichi Kurisaki, Junko SuzukiShoji Honda, Yasushi Maeda, Teruyuki Hirano, Yukio Ando. Clin Neurol Neurosurg
- Journal Title
  
  Clin Neurol Neurosurg
  
  Volume: 115 Pages: 603-606
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-23890163
[Journal Article] Derlin-1 overexpression ameliorates mutant SOD1-induced endopla smic reticulum stress by reducing mutant SOD1 accumulation2011
- Author(s)
  Akira Mori, Satoshi Yamashita
- Journal Title
  
  Neurochemistry International
  
  Volume: 58 Issue: 3 Pages: 344-353
- DOI
  10.1016/j.neuint.2010.12.010
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-23890163
[Journal Article] Derlin-1 overexpression amelioratesmutant SOD1-induced endoplasmic reticulumstress by reducing mutant SOD1accumulation.2011
- Author(s)
  Akira Mori, SatoshiYamashita, Katsuhisa Uchino, TomohiroSuga, Tokunori Ikeda, Koutaro Takamatsu,Masatoshi Ishizaki, Tatsuya Koide, EnKimura, Shuji Mita, Yasushi Maeda,Teruyuki Hirano and Makoto Uchino.
- Journal Title
  
  Neurochemistry International
  
  Volume: 58(3) Pages: 344-53
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-23890163
[Journal Article] Sporadic juvenile amyotrophic lateralsclerosis caused by mutant FUS/TLS:possible association of mentalretardation with this mutation.2011
- Author(s)
  SatoshiYamashita, Akira Mori, Hideya Sakaguchi,Tomohiro Suga, Daijiro Ishihara, AkihikoUeda, Taro Yamashita, Yasushi Maeda,Makoto Uchino, Teruyuki Hirano
- Journal Title
  
  Journal ofNeurology
  
  Volume: 259(6) Pages: 1039-44
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-23890163
[Journal Article] Sporadic juvenile amyotrophic lateral sclerosis caused by mutant FUS/TLS : possible association of mental retardation with this mutation2011
- Author(s)
  Satoshi Yamashita, Akira Mori, Hideya Sakaguchi
- Journal Title
  
  Journal of Neurplogy
  
  Volume: 259 Issue: 6 Pages: 1039-1044
- DOI
  10.1007/s00415-011-6292-6
- Peer Reviewed
- Data Source
  KAKENHI-PROJECT-23890163, KAKENHI-PROJECT-24591269, KAKENHI-PROJECT-24790891
[Presentation] Significant CMAP decrement by repetitive nerve stimulation is more frequent in median than ulnar nerves of patients with amyotrophic lateral sclerosis.2012
- Author(s)
  1. Mori A, Yamashita S, Sakaguchi H, Kimura E, Maeda Y, Hirano T, Uchino M, Ando Y.
- Organizer
  23th international Symposium on ALS/MND,
- Place of Presentation
  Chicago, IL, USA
- Data Source
  KAKENHI-PROJECT-23890163
[Presentation] Significant CMAP decrement by repetitivenerve stimulation is more frequent inmedian than ulnar nerves of patients withamyotrophic lateral sclerosis2012
- Author(s)
  Mori A, Yamashita S, Sakaguchi H, KimuraE, Maeda Y, Hirano T, Uchino M, Ando Y
- Organizer
  23th international Symposium on ALS/MND
- Place of Presentation
  Chicago, IL, USA
- Data Source
  KAKENHI-PROJECT-23890163
[Presentation] 精神発達遅滞が先行し、FUS/TLS遺伝子のdeletion/frameshift変異を有する孤発性若年性ALSの1例2011
- Author(s)
  森麗
- Organizer
  第189回日本神経学会九州地方会
- Place of Presentation
  久留米大学(福岡)
- Year and Date
  2011-06-18
- Data Source
  KAKENHI-PROJECT-23890163
[Presentation] Derlin-1過剰発現は変異SOD1蓄積軽減により小胞体ストレスを軽減する2011
- Author(s)
  森麗
- Organizer
  第52回日本神経学会学術大会
- Place of Presentation
  名古屋国際会議場(愛知)
- Year and Date
  2011-05-19
- Data Source
  KAKENHI-PROJECT-23890163

1. ERA Takumi (00273706)

# of Collaborated Projects: 1 results

# of Collaborated Products: 0 results
2. YAMASHITA Satoshi

# of Collaborated Projects: 0 results

# of Collaborated Products: 1 results
3. 安東由喜雄

# of Collaborated Projects: 0 results

# of Collaborated Products: 1 results
4. 山下太郎

# of Collaborated Projects: 0 results

# of Collaborated Products: 1 results
5. 平原智雄

# of Collaborated Projects: 0 results

# of Collaborated Products: 1 results

MORI Akira 森 麗

Research Projects

Research Products

Co-Researchers

Is endoplasmic reticulum stress essential for motor neuron degeneration?Principal Investigator

Principal Investigator

Project Period (FY)

Research Category

Research Field

Research Institution

Gene therapy for neuromuscular diseasePrincipal Investigator

Principal Investigator

Project Period (FY)

Research Category

Research Field

Research Institution

[Journal Article] Clinicopathological features of the first Asian family having vocal cord and pharyngeal weakness with distal myopathy due to a MATR3 mutation.2015

Author(s)

Journal Title

DOI

Data Source

[Journal Article] Muscle biopsy findings predictive of malignancy in rare infiltrative dermatomyositis2013

Author(s)

Journal Title

DOI

Data Source

[Journal Article] Significant CMAP decrement by repetitive nerve stimulation is more frequent in median than ulnar nerves of patients with amyotrophic lateral sclerosis2012

Author(s)

Journal Title

DOI

NAID

Data Source

[Journal Article] Significant CMAP decrement byrepetitive nerve stimulation is morefrequent in median than ulnar nerves ofpatients with amyotrophic lateralsclerosis2012

Author(s)

Journal Title

Data Source

[Journal Article] Muscle biopsy findings predictive ofmalignancy in rare infiltrativedermatomyositis.2012

Author(s)

Journal Title

Data Source

[Journal Article] Derlin-1 overexpression ameliorates mutant SOD1-induced endopla smic reticulum stress by reducing mutant SOD1 accumulation2011

Author(s)

Journal Title

DOI

Data Source

[Journal Article] Derlin-1 overexpression amelioratesmutant SOD1-induced endoplasmic reticulumstress by reducing mutant SOD1accumulation.2011

Author(s)

Journal Title

Data Source

[Journal Article] Sporadic juvenile amyotrophic lateralsclerosis caused by mutant FUS/TLS:possible association of mentalretardation with this mutation.2011

Author(s)

Journal Title

Data Source

[Journal Article] Sporadic juvenile amyotrophic lateral sclerosis caused by mutant FUS/TLS : possible association of mental retardation with this mutation2011

Author(s)

Journal Title

DOI

Data Source

[Presentation] Significant CMAP decrement by repetitive nerve stimulation is more frequent in median than ulnar nerves of patients with amyotrophic lateral sclerosis.2012

Author(s)

Organizer

Place of Presentation

Data Source

[Presentation] Significant CMAP decrement by repetitivenerve stimulation is more frequent inmedian than ulnar nerves of patients withamyotrophic lateral sclerosis2012

Author(s)

Organizer

Place of Presentation

Data Source

[Presentation] 精神発達遅滞が先行し、FUS/TLS遺伝子のdeletion/frameshift変異を有する孤発性若年性ALSの1例2011

Author(s)

Organizer

Place of Presentation

Year and Date

Data Source

[Presentation] Derlin-1過剰発現は変異SOD1蓄積軽減により小胞体ストレスを軽減する2011

Author(s)

Organizer

Place of Presentation

Year and Date

Data Source

MORI Akira 森麗