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ONO HIROYA  小野 洋也

… Alternative Names

小野 洋也  オノ ヒロヤ

Ono Hiroya  小野 洋也

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Researcher Number 90803578
Other IDs
  • ORCIDhttps://orcid.org/0000-0002-8439-5657
Affiliation (Current) 2026: 国立研究開発法人国立精神・神経医療研究センター, 神経研究所 遺伝子疾患治療研究部, リサーチフェロー
2026: 東北大学, 医学系研究科, 大学院非常勤講師
Affiliation (based on the past Project Information) *help 2024: 国立研究開発法人国立精神・神経医療研究センター, 神経研究所 遺伝子疾患治療研究部, リサーチフェロー
2018 – 2021: 東北大学, 医学系研究科, 大学院非常勤講師
Review Section/Research Field
Principal Investigator
Basic Section 52020:Neurology-related
Keywords
Principal Investigator
AMPK / 細胞膜修復 / dysferlin / 筋ジストロフィー
  • Research Projects

    (2 results)
  • Research Products

    (6 results)
  • Co-Researchers

    (4 People)
  •  Research for the pathogenesis and therapy of muscular dystrophy: Focusing on mechanisms of plasma membrane repairPrincipal Investigator

    • Principal Investigator
      小野 洋也
    • Project Period (FY)
      2023 – 2026
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      National Center of Neurology and Psychiatry
      Tohoku University
  •  Research for the pathogenesis and therapy of dysferlinopathy: Focusing on mechanisms of plasma membrane repairPrincipal Investigator

    • Principal Investigator
      Ono Hiroya
    • Project Period (FY)
      2018 – 2021
    • Research Category
      Grant-in-Aid for Early-Career Scientists
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Tohoku University

All 2020 2018

All Journal Article Presentation

  • [Journal Article] The genetic profile of dysferlinopathy in a cohort of 209 cases: Genotype-phenotype relationship and a hotspot on the inner DysF domain2020

    • Author(s)
      Izumi Rumiko、Takahashi Toshiaki、Suzuki Naoki、Niihori Tetsuya、Ono Hiroya、Nakamura Naoko、Katada Shinichi、Kato Masaaki、Warita Hitoshi、Tateyama Maki、Aoki Yoko、Aoki Masashi
    • Journal Title

      Human Mutation

      Volume: 41 Issue: 9 Pages: 1540-1554

    • DOI

      10.1002/humu.24036

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20K21563, KAKENHI-PROJECT-18K15437
  • [Journal Article] AMPK Complex Activation Promotes Sarcolemmal Repair in Dysferlinopathy2020

    • Author(s)
      Ono Hiroya、Suzuki Naoki、Kanno Shin-ichiro、Kawahara Genri、Izumi Rumiko、Takahashi Toshiaki、Kitajima Yasuo、Osana Shion、Nakamura Naoko、Akiyama Tetsuya、Ikeda Kensuke、Shijo Tomomi、Mitsuzawa Shio、Nagatomi Ryoichi、Araki Nobukazu、Yasui Akira、Warita Hitoshi、Hayashi Yukiko K.、Miyake Katsuya、Aoki Masashi
    • Journal Title

      Molecular Therapy

      Volume: 28 Issue: 4 Pages: 1133-1153

    • DOI

      10.1016/j.ymthe.2020.02.006

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K06831, KAKENHI-PROJECT-19K22604, KAKENHI-PROJECT-17H06112, KAKENHI-PROJECT-18K19505, KAKENHI-PROJECT-17K16107, KAKENHI-PROJECT-18K10822, KAKENHI-PROJECT-20K21563, KAKENHI-PROJECT-18K07519, KAKENHI-PROJECT-18K15437, KAKENHI-PROJECT-20H03594, KAKENHI-PROJECT-20H04078
  • [Presentation] ジスフェルリノパチーの治療法開発2020

    • Author(s)
      小野洋也, 髙橋俊明
    • Organizer
      第74回国立病院総合医学会
    • Invited
    • Data Source
      KAKENHI-PROJECT-18K15437
  • [Presentation] Dysferlinopathyに対する治療法の開発2020

    • Author(s)
      小野洋也, 鈴木直輝, 菅野新一郎, 川原玄理, 割田仁, 林由起子, 三宅克也, 青木正志
    • Organizer
      第38回日本神経治療学会学術集会
    • Invited
    • Data Source
      KAKENHI-PROJECT-18K15437
  • [Presentation] 細胞膜修復機構に着目したdysferlin異常症の病態解明と治療法開発2018

    • Author(s)
      小野洋也、鈴木直輝、菅野新一郎、川原玄理、井泉瑠美子、髙橋俊明、北嶋康雄、長名シオン、秋山徹也、池田謙輔、四條友望、光澤志緒、割田 仁、永富良一、荒木伸一、安井 明、林 由起子、三宅克也、青木正志
    • Organizer
      日本筋学会第4回学術集会
    • Data Source
      KAKENHI-PROJECT-18K15437
  • [Presentation] Novel binding partner of dysferlin is a potential therapeutic target for dysferlinopathy2018

    • Author(s)
      小野洋也、鈴木直輝、菅野新一郎、川原玄理、井泉瑠美子、髙橋俊明、北嶋康雄、長名シオン、秋山徹也、池田謙輔、四條友望、光澤志緒、割田 仁、永富良一、荒木伸一、安井 明、林 由起子、三宅克也、青木正志
    • Organizer
      第59回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-18K15437
  • 1.  SUZUKI Naoki
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 2.  青木 正志
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 3.  割田 仁
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 4.  荒木 伸一
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results

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