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ISHIGAKI SHINSUKE  石垣 診祐

… Alternative Names

ISHIGAKI Shinsuke  石垣 診祐

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Researcher Number 40378170
Other IDs
  • ORCIDhttps://orcid.org/0000-0002-9555-0659
Affiliation (Current) 2025: 滋賀医科大学, 神経難病研究センター, 教授
Affiliation (based on the past Project Information) *help 2021 – 2025: 滋賀医科大学, 神経難病研究センター, 教授
2018 – 2022: 名古屋大学, 医学系研究科, 特任准教授
2016 – 2017: 名古屋大学, 医学系研究科, 寄附講座助教
2015: 名古屋大学, 医学(系)研究科(研究院), 助教
2015: 名古屋大学, 医学(系)研究科(研究院), 特任助教 … More
2014 – 2015: 名古屋大学, 医学系研究科, 特任助教
2013: 名古屋大学, 医学(系)研究科(研究院), 特任助教
2012 – 2013: 名古屋大学, 医学(系)研究科(研究院), 助教 Less
Review Section/Research Field
Principal Investigator
Basic Section 51030:Pathophysiologic neuroscience-related / Neurology / Basic Section 52020:Neurology-related
Except Principal Investigator
Basic Section 44010:Cell biology-related / Basic Section 59040:Nutrition science and health science-related / Medium-sized Section 59:Sports sciences, physical education, health sciences, and related fields / Neurology / Neurochemistry/Neuropharmacology / Biological Sciences
Keywords
Principal Investigator
ALS / 前頭側頭葉変性症 / SFPQ / FUS / FTLD / PSP / タウ / tau / 核酸医薬 / RNA結合タンパク質 … More / FTLDスペクトラム / RNP / CBD / 認知症 / 大脳皮質基底核変性症 / 進行性核上性麻痺 / タウオパチー / 筋萎縮性側索硬化症 / 成体神経新生 / adult neurogenesis / Adult neurogenesis / 小胞体ストレス / 神経変性疾患 / ER stress … More
Except Principal Investigator
ERAD / ERストレス / FAM134B / 小胞体ストレス / 小胞体 / IDR / 相分離 / エクソン / 神経変性疾患 / RNA結合タンパク / 液ー液相分離 / スプライシング / 天然変性領域 / TFE3 / ATF6/CREB3ファミリー / CREB3L2 / CREB3 / CREB3ファミリー / 小胞体関連分解 / FAM143B / ATF6/CREB3 family / CREB3 family / ゴルジ体ストレス / オートファジー / Golgi stress / ER stress / ER-phagy / TDP-43 / 運動ニューロン疾患 / インスリン / 糖尿病 / エクソサイトーシス / 運動ニューロン / 筋萎縮性側索硬化症 / ノックアウトマウス / 質量分析 / HRD1 / Dorfin / RNF19B / 神経細胞 / EDAD / エンドソーム / RNF19B / 膜輸送 / γ-セクレターゼ / 酸化ストレス / アミロイドβ / APP / ユビキチンリガーゼ / アルツハイマー病 / 樹状突起 / 過活動 / 局在 / タウ / 脳神経疾患 / 神経科学 / 神経細胞死 / リン酸化 / 凝集 / 脳機能 / 認知症 / 老化 / Aβ / タウタンパク質 Less
  • Research Projects

    (11 results)
  • Research Products

    (149 results)
  • Co-Researchers

    (36 People)
  •  タウisoform制御に基づくアルツハイマー病疾患修飾薬の開発Principal Investigator

    • Principal Investigator
      石垣 診祐
    • Project Period (FY)
      2025 – 2028
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Review Section
      Basic Section 51030:Pathophysiologic neuroscience-related
    • Research Institution
      Shiga University of Medical Science
  •  天然変性領域 (IDR) 形成を支えるスプライシング機構から俯瞰する相分離現象

    • Principal Investigator
      増田 章男
    • Project Period (FY)
      2021 – 2024
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Review Section
      Basic Section 44010:Cell biology-related
    • Research Institution
      Nagoya University
  •  FTLDスペクトラムにおける核内RNP複合体の機能変化に基づく核酸医療の開発Principal Investigator

    • Principal Investigator
      石垣 診祐
    • Project Period (FY)
      2021 – 2024
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Shiga University of Medical Science
  •  Exploration of ER-phagy substrates involved in brain aging and its application to the control of neuronal senescence

    • Principal Investigator
      Oh-hashi Kentaro
    • Project Period (FY)
      2020 – 2022
    • Research Category
      Grant-in-Aid for Challenging Research (Exploratory)
    • Review Section
      Medium-sized Section 59:Sports sciences, physical education, health sciences, and related fields
    • Research Institution
      Gifu University
  •  Analysis of novel mechanisms of aging-related diseases focusing on Golgi stress signaling

    • Principal Investigator
      Oh-hashi Kentaro
    • Project Period (FY)
      2019 – 2023
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Review Section
      Basic Section 59040:Nutrition science and health science-related
    • Research Institution
      Gifu University
  •  Common pathogenesis in a wide-range of FTLD spectrum including ALS/FTLD and tauopathiesPrincipal Investigator

    • Principal Investigator
      Ishigaki Shinsuke
    • Project Period (FY)
      2018 – 2021
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 51030:Pathophysiologic neuroscience-related
    • Research Institution
      Nagoya University
  •  Elucidation of dysregulation of exocytosis in sporadic amyotrophic lateral sclerosis

    • Principal Investigator
      KATSUNO Masahisa
    • Project Period (FY)
      2016
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Adult neurogenesis in the mouse models of ALS/FTLDPrincipal Investigator

    • Principal Investigator
      Ishigaki Shinsuke
    • Project Period (FY)
      2015 – 2017
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Mechanism of tau protein aging and neurodegeneration

    • Principal Investigator
      Takashima Akihiko
    • Project Period (FY)
      2014 – 2018
    • Research Category
      Grant-in-Aid for Scientific Research on Innovative Areas (Research in a proposed research area)
    • Review Section
      Biological Sciences
    • Research Institution
      Gakushuin University
      National Center for Geriatrics and Gerontology
  •  Establishment of a system for monitoring endoplasmic reticulum redox state in mammalian cellsPrincipal Investigator

    • Principal Investigator
      ISHIGAKI Shinsuke
    • Project Period (FY)
      2012 – 2013
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Involvement of novel ubiquitin ligases in the pathogenic mechanism of Alzheimer's disease and drug discovery for fundamental therapeutic agent

    • Principal Investigator
      Nomura Yasuyuki
    • Project Period (FY)
      2012 – 2015
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurochemistry/Neuropharmacology
    • Research Institution
      Kurume University
      Yokohama College of Pharmacy

All 2022 2021 2020 2019 2018 2017 2016 2015 2014 2013 2012 Other

All Journal Article Presentation Book Patent

  • [Book] 【認知症の予防と対策】 前頭側頭型認知症への新しいアプローチ2016

    • Author(s)
      石垣 診祐, 祖父江 元
    • Publisher
      Medical Science Digest
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Journal Article] TDP-43 Proteinopathy and Tauopathy: Do They Have Pathomechanistic Links?2022

    • Author(s)
      Riku Yuichi、Yoshida Mari、Iwasaki Yasushi、Sobue Gen、Katsuno Masahisa、Ishigaki Shinsuke
    • Journal Title

      International Journal of Molecular Sciences

      Volume: 23 Issue: 24 Pages: 15755-15755

    • DOI

      10.3390/ijms232415755

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-23K21410
  • [Journal Article] The SYNGAP1 3'UTR variant in ALS patients causes aberrant SYNGAP1 splicing and dendritic spine loss by recruiting HNRNPK2022

    • Author(s)
      Yokoi S, Ito T, Sahashi K, Nakatochi M, Tohnai G, Nakamura R, Fujioka Y, Ishigaki S, Udagawa T, Izumi Y, Morita M, Kano O, Oda M, Sone T, Okano H, Atsuta N, Katsuno M, Okada Y*, Sobue G*
    • Journal Title

      Journal of Neuroscience

      Volume: 42 Issue: 47 Pages: 8881-8896

    • DOI

      10.1523/jneurosci.0455-22.2022

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07539, KAKENHI-PROJECT-19K07969, KAKENHI-PROJECT-19K07973, KAKENHI-PROJECT-21K07471, KAKENHI-PROJECT-22K07509, KAKENHI-PROJECT-22K07515, KAKENHI-PROJECT-22K07545, KAKENHI-PROJECT-20K16611, KAKENHI-PROJECT-21K15622, KAKENHI-PROJECT-17K19465, KAKENHI-PROJECT-18K15470, KAKENHI-PROJECT-19H03576, KAKENHI-PROJECT-23K24249, KAKENHI-PROJECT-23K21410
  • [Journal Article] Actin-binding protein filamin-A drives tau aggregation and contributes to progressive supranuclear palsy pathology2022

    • Author(s)
      Tsujikawa K,Hamanaka K, Riku Y, Hattori Y, Hara N, Iguchi Y,Miyata T, Sobue G, Matsumoto N, Sahashi K, Katsuno M, et al.
    • Journal Title

      Sci Adv

      Volume: - Issue: 21 Pages: 1-16

    • DOI

      10.1126/sciadv.abm5029

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-20H00527, KAKENHI-PROJECT-22K19506, KAKENHI-PUBLICLY-21H05624, KAKENHI-PROJECT-20H00525, KAKENHI-PROJECT-20H03589, KAKENHI-PROJECT-20K07907, KAKENHI-PROJECT-21K15330, KAKENHI-PUBLICLY-21H00446, KAKENHI-PROJECT-22H04923, KAKENHI-PROJECT-23K21410, KAKENHI-PROJECT-21H03537
  • [Journal Article] Motor neuron TDP-43 proteinopathy in progressive supranuclear palsy and corticobasal degeneration2022

    • Author(s)
      Riku Yuichi、Iwasaki Yasushi、Ishigaki Shinsuke、Akagi Akio、Hasegawa Masato、Nishioka Kenya、Li Yuanzhe、Riku Miho、Ikeuchi Takeshi、Fujioka Yusuke、Miyahara Hiroaki、Sone Jun、Hattori Nobutaka、Yoshida Mari、Katsuno Masahisa、Sobue Gen
    • Journal Title

      Brain

      Volume: - Issue: 8 Pages: 2769-2784

    • DOI

      10.1093/brain/awac091

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-20K16586, KAKENHI-PROJECT-20K16182, KAKENHI-PROJECT-21K07283, KAKENHI-PROJECT-21K15622, KAKENHI-PROJECT-22H04923, KAKENHI-PROJECT-23K21410
  • [Journal Article] Pathway from TDP-43-Related Pathology to Neuronal Dysfunction in Amyotrophic Lateral Sclerosis and Frontotemporal Lobar Degeneration2021

    • Author(s)
      Riku Yuichi、Seilhean Danielle、Duyckaerts Charles、Boluda Susana、Iguchi Yohei、Ishigaki Shinsuke、Iwasaki Yasushi、Yoshida Mari、Sobue Gen、Katsuno Masahisa
    • Journal Title

      International Journal of Molecular Sciences

      Volume: 22 Issue: 8 Pages: 3843-3843

    • DOI

      10.3390/ijms22083843

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-20K16586, KAKENHI-PROJECT-20H03589, KAKENHI-PROJECT-23K21410
  • [Journal Article] Characteristic Features of FUS Inclusions in Spinal Motor Neurons of Sporadic Amyotrophic Lateral Sclerosis.2020

    • Author(s)
      Ikenaka K, Ishigaki S, Iguchi Y, Kawai K, Fujioka Y, Yokoi S, Abdelhamid RF, Nagano S, Mochizuki H, Katsuno M, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 79 Issue: 4 Pages: 370-377

    • DOI

      10.1093/jnen/nlaa003

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-16K09690, KAKENHI-PROJECT-17K09753, KAKENHI-PROJECT-18K07367, KAKENHI-PROJECT-20H03589
  • [Journal Article] Aberrant interaction between FUS and SFPQ in neurons in a wide range of FTLD?spectrum diseases2020

    • Author(s)
      Ishigaki Shinsuke、Riku Yuichi、Fujioka Yusuke、Endo Kuniyuki、Iwade Nobuyuki、Kawai Kaori、Ishibashi Minaka、Yokoi Satoshi、Katsuno Masahisa、Watanabe Hirohisa、Mori Keiko、Akagi Akio、Yokota Osamu、Terada Seishi、Kawakami Ito、Suzuki Naoki、Warita Hitoshi、Aoki Masashi、Yoshida Mari、Sobue Gen
    • Journal Title

      Brain

      Volume: 143 Issue: 8 Pages: 2398-2405

    • DOI

      10.1093/brain/awaa196

    • NAID

      40022684971

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Journal Article] TDP-43 regulates early-phase insulin secretion via CaV1.2-mediated exocytosis in islets2019

    • Author(s)
      Araki Kunihiko、(他10名)、Ishigaki Shinsuke、Nakamichi Yoko、Tsunekawa Shin、Seino Yusuke、Yamamoto Akiko、Takayama Yasunori、Hidaka Shihomi、Tominaga Makoto、Ohara-Imaizumi Mica、Suzuki Atsushi、Ishiguro Hiroshi、Enomoto Atsushi、Yoshida Mari、Arima Hiroshi、Muramatsu Shin-ichi、Sobue Gen、Katsuno Masahisa
    • Journal Title

      Journal of Clinical Investigation

      Volume: 129 Issue: 9 Pages: 3578-3593

    • DOI

      10.1172/jci124481

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-WRAPUP-19H05447, KAKENHI-PROJECT-17H04195, KAKENHI-PROJECT-17K08547, KAKENHI-PROJECT-17K09753
  • [Journal Article] Tau Accumulation and Network Breakdown in Alzheimer’s Disease2019

    • Author(s)
      Watanabe Hirohisa、Bagarinao Epifanio、Yokoi Takamasa、Yamaguchi Hiroshi、Ishigaki Shinsuke、Mausuda Michihito、Katsuno Masahisa、Sobue Gen
    • Journal Title

      Adv Exp Med Biol

      Volume: 1184 Pages: 231-240

    • DOI

      10.1007/978-981-32-9358-8_19

    • ISBN
      9789813293571, 9789813293588
    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-WRAPUP-19H05447
  • [Journal Article] Tau isoform expression and phosphorylation in marmoset brains2019

    • Author(s)
      Sharma Govinda、Huo Anni、Kimura Taeko、Shiozawa Seiji、Kobayashi Reona、Sahara Naruhiko、Ishibashi Minaka、Ishigaki Shinsuke、Saito Taro、Ando Kanae、Murayama Shigeo、Hasegawa Masato、Sobue Gen、Okano Hideyuki、Hisanaga Shin-ichi
    • Journal Title

      Journal of Biological Chemistry

      Volume: 294 Issue: 30 Pages: 11433-11444

    • DOI

      10.1074/jbc.ra119.008415

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-PROJECT-19K06472, KAKENHI-PROJECT-19K06896, KAKENHI-PROJECT-19K06942, KAKENHI-PUBLICLY-19H05437, KAKENHI-WRAPUP-19H05447, KAKENHI-PROJECT-16H06277
  • [Journal Article] Pathogenesis of Frontotemporal Lobar Degeneration: Insights From Loss of Function Theory and Early Involvement of the Caudate Nucleus2018

    • Author(s)
      Sobue Gen、Ishigaki Shinsuke、Watanabe Hirohisa
    • Journal Title

      Frontiers in Neuroscience

      Volume: 12 Pages: 473-473

    • DOI

      10.3389/fnins.2018.00473

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004
  • [Journal Article] Involvement of the Precuneus/Posterior Cingulate Cortex Is Significant for the Development of Alzheimer’s Disease: A PET (THK5351, PiB) and Resting fMRI Study2018

    • Author(s)
      Yokoi Takamasa、Watanabe Hirohisa、Ishigaki Shinsuke、Katsuno Masahisa、Miyao Shinichi、Kato Katsuhiko、Naganawa Shinji、Harada Ryuichi、Okamura Nobuyuki、Yanai Kazuhiko、Yoshida Mari、Sobue Gen (ほか9名)
    • Journal Title

      Frontiers in Aging Neuroscience

      Volume: 10 Pages: 304-304

    • DOI

      10.3389/fnagi.2018.00304

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-PROJECT-18K19510, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-17H04259, KAKENHI-PROJECT-18H02771, KAKENHI-PROJECT-17K16117, KAKENHI-PROJECT-18K15538, KAKENHI-PLANNED-26117003
  • [Journal Article] Silencing of FUS in the common marmoset (Callithrix jacchus) brainvia stereotaxic injection of an adeno-associated virus encoding shRNA.2018

    • Author(s)
      Endo K, Ishigaki S, Masamizu Y, Fujioka Y, Watakabe A, Yamamori T, Hatanaka N, Nambu A, Okado H, Katsuno M, Watanabe H, Matsuzaki M, Sobue G
    • Journal Title

      Neurosci Res

      Volume: in press Pages: 30183-9

    • DOI

      10.1016/j.neures.2017.08.006

    • Peer Reviewed
    • Data Source
      KAKENHI-INTERNATIONAL-15K21731, KAKENHI-PLANNED-15H05873, KAKENHI-ORGANIZER-15H05871, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-26250009, KAKENHI-PROJECT-15K09310, KAKENHI-PROJECT-18K07367
  • [Journal Article] Importance of Functional Loss of FUS in FTLD/ALS2018

    • Author(s)
      Ishigaki Shinsuke、Sobue Gen
    • Journal Title

      Frontiers in Molecular Biosciences

      Volume: 5 Pages: 44-44

    • DOI

      10.3389/fmolb.2018.00044

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004
  • [Journal Article] Pathologic Involvement of Glutamatergic Striatal Inputs From the Cortices in TAR DNA-Binding Protein 43kDa-Related Frontotemporal Lobar Degeneration and Amyotrophic Lateral Sclerosis.2017

    • Author(s)
      Riku Y, Watanabe H, Yoshida M, Mimuro M, Iwasaki Y, Masuda M, Ishigaki S.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 76(9) Issue: 9 Pages: 759-768

    • DOI

      10.1093/jnen/nlx055

    • Peer Reviewed
    • Data Source
      KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15K09310
  • [Journal Article] Altered tau isoform ratio caused by loss of Fus and Sfpq function leads to FTLD-like phenotypes2017

    • Author(s)
      Ishigaki S, Fujioka Y, Okada Y, Riku Y, Udagawa T, Honda D, Yokoi S, Endo K, Ikenaka K, Takagi S, Iguchi Y, Sahara N, Takashima A, Okano H, Yoshida M, Warita H, Aoki M, Watanabe H, Okado H, Katsuno H, Sobue G.
    • Journal Title

      Cell Reports

      Volume: 18 Issue: 5 Pages: 1118-1131

    • DOI

      10.1016/j.celrep.2017.01.013

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PUBLICLY-15H01568, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117007, KAKENHI-PROJECT-26290016, KAKENHI-PROJECT-16K15480, KAKENHI-PROJECT-25640038, KAKENHI-PROJECT-16K14569, KAKENHI-PROJECT-17K09753, KAKENHI-ORGANIZER-26117001, KAKENHI-PROJECT-15H04278, KAKENHI-PLANNED-26117004, KAKENHI-PLANNED-26117008, KAKENHI-PROJECT-17H04195, KAKENHI-PROJECT-15K06793, KAKENHI-PROJECT-15K09310
  • [Journal Article] Altered GluA1 (Gria1) Function and Accumbal Synaptic Plasticity in the ClockΔ19 Model of Bipolar Mania.2017

    • Author(s)
      Parekh PK, Becker-Krail D, Sundaravelu P, Ishigaki S, Okado H, Sobue G, Huang Y, McClung CA.
    • Journal Title

      Biol Psychiatry

      Volume: S0006 Issue: 11 Pages: 31721-3

    • DOI

      10.1016/j.biopsych.2017.06.022

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15K09310
  • [Journal Article] Marked Involvement of the Striatal Efferent System in TAR DNA-Binding Protein 43 kDa-Related Frontotemporal Lobar Degeneration and Amyotrophic Lateral Sclerosis.2017

    • Author(s)
      Riku Y., Watanabe H., Yoshida M., Mimuro M., Iwasaki Y., Masuda M., Ishigaki S., Katsuno M., Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: in press Issue: 8 Pages: 801-811

    • DOI

      10.1093/jnen/nlw053

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-26461269, KAKENHI-PROJECT-15K15338, KAKENHI-PROJECT-15K19483, KAKENHI-PROJECT-15K09310, KAKENHI-ORGANIZER-26117001
  • [Journal Article] 3'UTR Length-Dependent Control of SynGAP Isoform α2 mRNA by FUS and ELAV-like Proteins Promotes Dendritic Spine Maturation and Cognitive Function.2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M.
    • Journal Title

      Cell Rep

      Volume: 20(13) Issue: 13 Pages: 3071-3084

    • DOI

      10.1016/j.celrep.2017.08.100

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-17H04195, KAKENHI-PROJECT-15K09310
  • [Journal Article] R-spondin 2 promotes acetylcholine receptor clustering at the neuromuscular junction via Lgr5.2016

    • Author(s)
      Nakashima H., Ohkawara B., Ishigaki S., Fukudome T., Ito K., Tsushima M., Konishi H., Okuno T., Yoshimura T., Ito M., Masuda A., Sobue G., Kiyama H., Ishiguro N., Ohno K.
    • Journal Title

      Sci Rep

      Volume: 22 Issue: 1 Pages: 28512-28512

    • DOI

      10.1038/srep28512

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15H04840, KAKENHI-PROJECT-25430049, KAKENHI-PROJECT-15K06707, KAKENHI-PROJECT-15K06755, KAKENHI-PROJECT-15K09310, KAKENHI-PROJECT-16K07055, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Gene Expression Profile of Inflammatory Myopathy with Malignancy is Similar to that of Dermatomyositis rather than Polymyositis2016

    • Author(s)
      Noda, T., Iijima, M., Noda, S., Maeshima, S., Nakanishi, H., Kimura, S., Koike, H., Ishigaki, S., Iguchi, Y., Katsuno, M., and Sobue, G.
    • Journal Title

      Intern. Med.

      Volume: 55 Issue: 18 Pages: 2571-2580

    • DOI

      10.2169/internalmedicine.55.6706

    • NAID

      130005414859

    • ISSN
      0918-2918, 1349-7235
    • Language
      English
    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15K09310, KAKENHI-PROJECT-16K09693, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Marked Involvement of the Striatal Efferent System in TAR DNA-Binding Protein 43kDa-Related Frontotemporal Lobar Degeneration and Amyotrophic Lateral Sclerosis.2016

    • Author(s)
      Riku Y, Watanabe H, Yoshida M, Mimuro M, Iwasaki Y, Masuda M, Ishigaki S, Katsuno M, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 印刷中

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Journal Article] A rapid functional decline type of amyotrophic lateral sclerosis is linked to low expression of TTN.2016

    • Author(s)
      Watanabe H, Atsuta N, Hirakawa A, Nakamura R, Nakatochi M, Ishigaki S, Iida A, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: in press Issue: 8 Pages: 851-8

    • DOI

      10.1136/jnnp-2015-311541

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09310, KAKENHI-PROJECT-26461319, KAKENHI-PROJECT-25461277, KAKENHI-PROJECT-26670439, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15K15338, KAKENHI-PROJECT-15K19485
  • [Journal Article] Involvement of the caudate nucleus head and its networks in sporadic amyotrophic lateral sclerosis-frontotemporal dementia continuum.2016

    • Author(s)
      Masuda, M., Senda, J., Watanabe, H., Epifanio, B., Tanaka, Y., Imai, K., Riku, Y., Li, Y., Nakamura, R., Ito, M., Ishigaki, S., Atsuta, N., Koike, H., Katsuno, M., Hattori, N., Naganawa, S., and Sobue, G.
    • Journal Title

      Amyotroph Lateral Scler Frontotemporal Degener

      Volume: 17 Pages: 571-579

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Journal Article] Involvement of the caudate nucleus head and its networks in sporadic amyotrophic lateral sclerosis-frontotemporal dementia continuum.2016

    • Author(s)
      Masuda M, Senda J, Watanabe H, Epifanio B, Tanaka Y, Imai K, Riku Y, Li Y, Nakamura R, Ito M, Ishigaki S, Atsuta N, Koike H, Katsuno M, Hattori N, Naganawa S, and Sobue G.
    • Journal Title

      Amyotroph Lateral Scler Frontotemporal Degener

      Volume: 17 Pages: 571-579

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Journal Article] Transcriptional and post-transcriptional regulation of transmembrane protein 132A.2015

    • Author(s)
      Oh-Hashi K, Sone A, Hikiji T, Hirata Y, Vitiello M, Fedele M, Ishigaki S, Sobue G, Kiuchi K.
    • Journal Title

      Mol Cell Biochem.

      Volume: in press

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Journal Article] Transcriptional and post-transcriptional regulation of transmembrane protein 132A.2015

    • Author(s)
      Oh-Hashi, K., Sone, A., Hikiji, T., Hirata, Y., Vitiello, M., Fedele, M., Ishigaki S., Sobue, G., and Kiuchi, K.
    • Journal Title

      Mol Cell Biochem

      Volume: 405 Issue: 1-2 Pages: 291-299

    • DOI

      10.1007/s11010-015-2419-x

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09310, KAKENHI-PLANNED-26117004
  • [Journal Article] Microglial keratan sulfate epitope elicits in central nervous tissues of transgenic model mice and patients with amyotrophic lateral sclerosis.2015

    • Author(s)
      Foyez T, Takeda-Uchimura Y, Ishigaki S, Narentuya, Zhang Z, Sobue G, Kadomatsu K, Uchimura K.
    • Journal Title

      Am J Pathol

      Volume: 185 Issue: 11 Pages: 3053-3065

    • DOI

      10.1016/j.ajpath.2015.07.016

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-15K08265, KAKENHI-PROJECT-15K09310, KAKENHI-ORGANIZER-23110001, KAKENHI-PLANNED-23110002, KAKENHI-PLANNED-26117004
  • [Journal Article] Position-specific binding of FUS to nascent RNA regulates mRNA length.2015

    • Author(s)
      Masuda A, Takeda J, Okuno T, Okamoto T, Ohkawara B, Ito M, Ishigaki S, Sobue G, Ohno K.
    • Journal Title

      Gen. Dev.

      Volume: in press

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Journal Article] FUS regulates AMPA receptor function and FTLD/ALS-associated behaviour via GluA1 mRNA stabilization.2015

    • Author(s)
      Udagawa, T., Fujioka, Y., Tanaka, M., Honda, D., Yokoi, S., Riku, Y., Ibi, D., Nagai, T., Yamada, K., Watanabe, H., Katsuno, M., Inada, T., Ohno, K., Sokabe, M., Okado, H., Ishigaki S*., and Sobue, G.
    • Journal Title

      Nat Commun

      Volume: 6 Issue: 1 Pages: 7098-7098

    • DOI

      10.1038/ncomms8098

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-15K09310, KAKENHI-PUBLICLY-25118508, KAKENHI-PROJECT-221S0003, KAKENHI-PLANNED-26116003, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-24247028, KAKENHI-PROJECT-15H06719, KAKENHI-PROJECT-25460093, KAKENHI-PROJECT-15K15337, KAKENHI-PROJECT-26670439, KAKENHI-PROJECT-25860708, KAKENHI-PROJECT-26293206, KAKENHI-PLANNED-26117002, KAKENHI-ORGANIZER-26117001
  • [Journal Article] FUS regulates AMPA receptor function and FTLD/ALS-associated behavior via GluA1 mRNA stabilization.2015

    • Author(s)
      Udagawa T, Fujioka Y, Tanaka M, Honda D, Yokoi S, Riku Y, Ibi D, Nagai T, Yamada K, Watanabe H, Katsuno M, Inada T, Ohno K, Sokabe M, Okado H, Ishigaki S*, Sobue G*.
    • Journal Title

      Nat Commun.

      Volume: in press

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Journal Article] Position-specific binding of FUS to nascent RNA regulates mRNA length.2015

    • Author(s)
      Masuda A, Takeda J, Okuno T, Okamoto T, Ohkawara B, Ito M, Ishigaki S, Sobue G, Ohno K.
    • Journal Title

      Genes Dev.

      Volume: 29(10) Issue: 10 Pages: 1045-57

    • DOI

      10.1101/gad.255737.114

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-15K06707, KAKENHI-PROJECT-15K06755, KAKENHI-PROJECT-15K09310, KAKENHI-PROJECT-25430049, KAKENHI-PUBLICLY-25118508, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15H04840, KAKENHI-PROJECT-24500469
  • [Journal Article] A highly sensitive assay of IRE1 activity using the small luciferase NanoLuc: Evaluation of ALS-related genetic and pathological factors.2015

    • Author(s)
      Hikiji, T., Norisada, J., Hirata, Y., Okuda, K., Nagasawa, H., Ishigaki S., Sobue, G., Kiuchi, K., and Oh-hashi, K.
    • Journal Title

      Biochem Biophys Res Commun

      Volume: 463 Issue: 4 Pages: 881-887

    • DOI

      10.1016/j.bbrc.2015.05.132

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09310, KAKENHI-PLANNED-26117004
  • [Journal Article] Lower motor neuron involvement in TAR DNA-binding protein of 43 kDa-related frontotemporal lobar degeneration and amyotrophic lateral sclerosis.2014

    • Author(s)
      Riku Y, Watanabe H, Yoshida M, Tatsumi S, Mimuro M, Iwasaki Y, Katsuno M, Iguchi Y, Masuda M, Senda J, Ishigaki S, Udagawa T, Sobue G
    • Journal Title

      JAMA Neurol.

      Volume: 71 Issue: 2 Pages: 172-179

    • DOI

      10.1001/jamaneurol.2013.5489

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-24659429, KAKENHI-PROJECT-25461312, KAKENHI-PROJECT-26293206
  • [Journal Article] Establishment of a system for monitoring endoplasmic reticulum redox state in mammalian cells.2013

    • Author(s)
      Kanekura K, Ishigaki S, Merksamer P, Papa F, Urano F.
    • Journal Title

      Lab Invest.

      Volume: 93 Issue: 11 Pages: 1254-8

    • DOI

      10.1038/labinvest.2013.112

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Journal Article] FUS-regulated region- and cell-type-specific transcriptome is associated with cell selectivity in ALS/FTLD.2013

    • Author(s)
      Fujioka Y, Ishigaki S, Masuda A, Iguchi Y, Udagawa T, Watanabe H, Katsuno M, Ohno K, Sobue G.
    • Journal Title

      Sci Rep.

      Volume: 3 Issue: 1 Pages: 2388-2388

    • DOI

      10.1038/srep02388

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24500469, KAKENHI-PROJECT-24659429
  • [Journal Article] The ALS/FTLD-related RNA-binding proteins TDP-43 and FUS have common downstream RNA targets in cortical neurons2013

    • Author(s)
      Honda D, Ishigaki S, Iguchi Y, Fujioka Y, Udagawa T, Masuda A, Ohno K, Katsuno M, Sobue G.
    • Journal Title

      FEBS Open Bio.

      Volume: 20 Issue: 1 Pages: 1-10

    • DOI

      10.1016/j.fob.2013.11.001

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24500469, KAKENHI-PROJECT-24659429, KAKENHI-PROJECT-25860708
  • [Journal Article] Position-dependent FUS-RNA interactions regulate alternative splicing events and transcriptions.2012

    • Author(s)
      Ishigaki S, Masuda A, Fujioka Y, Iguchi Y, Katsuno M, Shibata A, Urano F, Sobue G, Ohno K
    • Journal Title

      Sci Rep

      Volume: 2 Issue: 1 Pages: 529-529

    • DOI

      10.1038/srep00529

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23659452, KAKENHI-PROJECT-24390221, KAKENHI-PROJECT-24500469, KAKENHI-PROJECT-24659429, KAKENHI-PLANNED-22110005
  • [Journal Article] Thioredoxin-interacting protein mediates ER stress-inducedβcell death through initiation of the inflammasome2012

    • Author(s)
      Oslowski CM, Hara T, O'Sullivan-Murphy B, Kanekura K, Lu S, Hara M, Ishigaki S, Zhu LJ, Hayashi E, Hui ST, Greiner D, Kaufman RJ, Bortell R, Urano F.
    • Journal Title

      Cell Metab

      Volume: 16(2) Issue: 2 Pages: 265-73

    • DOI

      10.1016/j.cmet.2012.07.005

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Patent] タウのスプライシングを制御するアンチセンスオリゴヌクレオチド及びその用途2019

    • Inventor(s)
      石垣診祐、祖父江元、佐橋健太郎、遠藤邦幸、他3名
    • Industrial Property Rights Holder
      国立大学法人名古屋大学、神戸天然物化学株式会社
    • Industrial Property Rights Type
      特許
    • Filing Date
      2019
    • Overseas
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Patent] タウのスプライシングを制御するアンチセンスオリゴヌクレオチド及びその用途2018

    • Inventor(s)
      祖父江元、石垣診祐、他5名
    • Industrial Property Rights Holder
      名古屋大学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2018
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Patent] TDP-43の発現量を調節するアンチセンスオリゴヌクレオチド及びその用途2018

    • Inventor(s)
      祖父江、石垣、佐橋 、永井、前田、武内、閨、藤原、松田
    • Industrial Property Rights Holder
      国立大学法人名古屋大学、国立大学法人大阪大学、神戸天然物化学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2018
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Patent] TDP-43の発現量を調節するアンチセンスオリゴヌクレオチド及びその用途2018

    • Inventor(s)
      祖父江元、石垣診祐、他7名
    • Industrial Property Rights Holder
      名古屋大学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2018
    • Overseas
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Patent] タウのスプライシングを制御するアンチセンスオリゴヌクレオチド及びその用途2018

    • Inventor(s)
      祖父江、石垣、佐橋、遠藤、閨、藤原、松田
    • Industrial Property Rights Holder
      国立大学法人名古屋大学、神戸天然物化学株式会社
    • Industrial Property Rights Type
      特許
    • Filing Date
      2018
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Patent] 細胞内容物の回収方法および回収装置2017

    • Inventor(s)
      宇理須恒雄、石垣診祐、宇野秀隆、高村禅
    • Industrial Property Rights Holder
      名古屋大学、北陸先端科学技術大学院大学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2017
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Patent] TDP-43の発現量を調節するアンチセンスオリゴヌクレオチド及びその用途2017

    • Inventor(s)
      祖父江、石垣、佐橋、永井、前田、武内、閨、藤原、松田
    • Industrial Property Rights Holder
      国立大学法人 名古屋大学/大阪大学, (株)神戸天然物化学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2017
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Patent] 細胞内容物の回収方法および回収装置2017

    • Inventor(s)
      宇理須恒夫、石垣診祐、宇野秀隆、高村禅
    • Industrial Property Rights Holder
      国立大学法人名古屋大学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2017
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Patent] TDP-43の発現量を調節するアンチセンスオリゴヌクレオチド及びその用途2017

    • Inventor(s)
      祖父江元、石垣診祐、他7名
    • Industrial Property Rights Holder
      名古屋大学、大阪大学、神戸天然物化学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2017
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Patent] 疾患モデル動物および疾患治療剤2016

    • Inventor(s)
      祖父江元、石垣診祐、横井聡
    • Industrial Property Rights Holder
      国立大学法人名古屋大学
    • Industrial Property Rights Type
      特許
    • Industrial Property Number
      2016-139308
    • Filing Date
      2016-07-14
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] FUSの機能から再考するFTLDの病態 Redefinition of FTLD based on the molecular pathogenesis2022

    • Author(s)
      石垣 診祐
    • Organizer
      第45回日本神経科学大会(NEURO2022)
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-23K21410
  • [Presentation] Alteration of Tau metabolism through FUS in FTLD-spectrum disorders including ALS.2022

    • Author(s)
      Ishigaki, S.
    • Organizer
      2nd Taiwan Society for Neuroscience, ALS Satellite Meeting
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-23K21410
  • [Presentation] Modulation of liquid-liquid phase separation of Fused in Sarcoma (FUS) by oligonucleotide therapeutics2022

    • Author(s)
      石垣 診祐
    • Organizer
      第45回日本分子生物学会年会
    • Data Source
      KAKENHI-PROJECT-23K21410
  • [Presentation] Aberrant FUS-SFPQ interactions in the neuronal nuclei in ALS and FTLD spectrum diseases, a possible pathogenesis.2021

    • Author(s)
      Ishigaki, S., Sobue, G.
    • Organizer
      The 1st China-Japan-Korea International Meeting/ The 44th Annual Meeting of the Japan Neuroscience Society
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-23K21410
  • [Presentation] FTLDスペクトラムにおけるFUSのタウ制御機構2021

    • Author(s)
      石垣 診祐
    • Organizer
      第62回神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-23K21410
  • [Presentation] FTLDスペクトラムにおけるFUSのタウ制御機構の機能的側面から考えるFTLDの新たな疾患概念2021

    • Author(s)
      石垣 診祐
    • Organizer
      第36回日本老年精神医学会
    • Invited
    • Data Source
      KAKENHI-PROJECT-23K21410
  • [Presentation] Aberrant FUS-SFPQ interaction in a wide-range of FTLD spectrum diseases2020

    • Author(s)
      Ishigaki S, Riku Y, Yoshida M, Sobue G.
    • Organizer
      第39回日本認知症学会学術集会
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] Tau plays a key role in adult hippocampal neurogenesis alteration caused by environmental changes2020

    • Author(s)
      Iwade N, Ishigaki S, Fujioka Y, Endo K, Kawai K, Miyasaka T, Katsuno M, Watanabe H, Sobue G.
    • Organizer
      第61回神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] Impaired dopamine release response in the NAcc is in the center of “binge-like eating” mechanism. -Attempt to detect “Binge like eating” as the early sign of neurodegenerative disease -2020

    • Author(s)
      Fujioka Y, Kawai K, Endo K, Ishibashi M, Yokoi S, Iwade N, Katsuno M, Watanabe H, Ishigaki S, Sobue G.
    • Organizer
      第61回神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] Functional loss of RNA binding proteins in tauopathies2020

    • Author(s)
      石垣診祐
    • Organizer
      第61回神経学会学術大会 シンポジウム
    • Invited
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] A novel State-of-the-art System for the single cell transcriptome analysis based on planar patch clamp.2019

    • Author(s)
      Ishigaki S, Uno H, Wang Z-H, Ukita Y, Bhardwaj R, Tue PT, Iwabuchi S, Hashimoto S, Oka T, Kawahara K, Takamura Y, Urisu T, Sobue G.
    • Organizer
      The 49th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] Development of a single cell analysis tool for neuroscience on 2D planar-patch-clamp plate with positional information2019

    • Author(s)
      Ishigaki S, Uno H, Wang Z-H, Ukita Y, Bhardwaj R, Tue PT, Hashimoto S, Oka T, Kawahara K, Sobue G, Urisu T, Takamura Y
    • Organizer
      The 12th International workshop on approaches to single cell analysis
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Tau in marmoset brains, its isoform expression and phosphorylation.2019

    • Author(s)
      Sharma, G., Huo, A., Kimura, T., Shiozawa, S., Kobayashi, R., Sahara, N., Ishibashi, M., Ishigaki, S., Saito, T., Ando, K., Murayama, S., Hasegawa, M., Sobue, G., Okano, H., Hisanaga, S.
    • Organizer
      AD/PD 2019
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Tau Phosphorylation at AT8 Pathological Site during Brain Development2019

    • Author(s)
      Dilina Tuerde, Kotaro Furusawa, Toshiyuki Takasugi, Taeko Kimura, Shinsuke Ishigaki, Kanae Ando, Shin-ichi Hisanaga, Gen Sobue
    • Organizer
      The 42nd annual Meeting of the Japan Neuroscience Society
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] Aberrant interaction between FUS and SFPQ in the brain of a wide-ranged FTLD spectrum including amyotrophic lateral sclerosis (ALS) and progressive supranuclear palsy (PSP)2019

    • Author(s)
      Shinsuke Ishigaki, Yuichi Riku, Mari Yoshida, Gen Sobue
    • Organizer
      第60回神経病理学会総会学術研究会
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] Real-time monitoring and quantification of binge-like eating behaviors in animal models.2019

    • Author(s)
      Fujioka Y, Kawai K, Endo K, Ishibashi M, Yokoi S, Iwade N, Katsuno M, Watanabe H, Ishigaki S, Sobue G.
    • Organizer
      The 49th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] Involvement of SFPQ in the pathogenesis of a wide-ranged FTLD spectrum2019

    • Author(s)
      Shinsuke Ishigaki, Yuichi Riku, Yusuke Fujioka, Minaka Ishibashi, Satoshi Yokoi, Kuniyuki Endo, Nobuyuki Iwade, Kaori Kawai, Hirohisa Watanabe, Masahisa Katsuno, Mari Yoshida, Gen Sobue
    • Organizer
      The 42nd annual Meeting of the Japan Neuroscience Society
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] Aberrant interaction between FUS and SFPQ in a wide-ranged FTLD spectrum including ALS and PSP2019

    • Author(s)
      Shinsuke Ishigaki, Yuichi Riku, Yusuke Fujioka, Satoshi Yokoi, Kuniyuki Endo, Nobuyuki Iwade, Kaori Kawai, Minaka Ishibashi, Masahisa Katsuno, Hirohisa Watanabe, Keiko Mori, Mari Yoshida, Gen Sobue
    • Organizer
      第60回神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] The roles of tau isoforms in adult hippocampal neurogenesis2019

    • Author(s)
      Nobuyuki Iwade, Shinsuke Ishigaki, Yusuke Fujioka, Kaori Kawai, Tomohiro Miyasaka, Hirohisa Watanabe, Masahisa Katsuno, Gen Sobue
    • Organizer
      第60回神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] Tau phosphorylation at AT8 pathological site during brain development(ポスター)2018

    • Author(s)
      Tuerde D, Furusawa K, Takasugi T, Kimura T, Ishigaki S, Ando K, Sobue G, Hisanaga SI.
    • Organizer
      The 48th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] タウisoformの成体神経新生における役割2018

    • Author(s)
      石垣診祐、岩出展行、藤岡祐介、遠藤邦幸、河合香里、石橋みなか、勝野雅央、渡辺宏久、宮坂知宏、祖父江元
    • Organizer
      第13回 臨床ストレス応答学会大会
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Aberrant interaction between FUS and SFPQ in the nucleus of neurons in sporadic FTLD/ALS and PSP brains(ポスター)2018

    • Author(s)
      Fujioka Y, Ishigaki S, Riku Y, Ishibashi M, Yokoi S, K. Endo K, Iwade N, Kawai K, Watanabe H, Katsuno M, Yoshida M, Sobue G
    • Organizer
      The 48th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Development of a single cell analysis tool for neurological disorders on 2D planar-patch-clamp plate with positional information2018

    • Author(s)
      Ishigaki S, Uno H, Wang Z-H, Ukita Y, Bhardwaj R, Tue PT, Hashimoto S, Oka T, Kawahara K, Takamura Y, Urisu T, Sobue G.
    • Organizer
      The 48th Society for Neuroscience annual meeting, Nano symposium
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] Functional Loss of FUS in neurodegenerative diseases2018

    • Author(s)
      Ishigaki,S, Sobue,G
    • Organizer
      The 41st annual Meeting of the Japan Neuroscience Society Symposium
    • Invited
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] ALS/FTLDおよび4R-tau優位のタウオパチーにおけるFUSとSFPQの結合性の低下 Aberrant interaction between FUS and SFPQ in FTLD/ALS and 4R-tau dominant tauopathies2018

    • Author(s)
      Ishigaki S, RIku Y, Fujioka Y, Yokoi S, Endo K, Iwade N, Kawai K, Ishibashi M, Watanabe H, Katsuno M, Yoshida M, Sobue G
    • Organizer
      The 41st annual Meeting of the Japan Neuroscience Society 2018
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] タウ蛋白は摂食量及び体重を制御する  Tau regulates food intake and body weight2018

    • Author(s)
      Fujioka Y, Ishigaki S, Kawai K, Iwade N, Endo K, Ishibashi M, Yokoi S, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 41st annual Meeting of the Japan Neuroscience Society
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Functional Loss of FUS in neurodegenerative diseases2018

    • Author(s)
      Ishigaki,S, Sobue,G
    • Organizer
      The 41st annual Meeting of the Japan Neuroscience Society
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] RNA結合タンパク質FUSの機能と神経変性疾患への関わり2018

    • Author(s)
      Ishigaki S, Sobue G
    • Organizer
      第41回日本分子生物学会年会 ワークショップ
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] Development of a single cell analysis tool for neurological disorders on 2D planar-patch-clamp plate with positional information2018

    • Author(s)
      Ishigaki S, Uno H, Wang Z-H, Ukita Y, Bhardwaj R, Tue PT, Hashimoto S, Oka T, Kawahara K, Takamura Y, Urisu T, Sobue G
    • Organizer
      The 48th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] FUS/TLSに関連するALS/FTLDの分子病態2018

    • Author(s)
      石垣診祐
    • Organizer
      第59神経学会学術大会 シンポジウム
    • Invited
    • Data Source
      KAKENHI-PROJECT-18K07367
  • [Presentation] マーモセット尾状核でのFUS KDは、グリア炎症を伴い神経線維の短縮を引き起こす Silencing of FUS in common marmoset caudate induces shortening of fiber tracts accompanied with glial inflammation2018

    • Author(s)
      Endo K, Ishigaki S, Watanabe H, Hatanaka N, Hata J, Watakabe A, Nambu A, Okano H, Yamamori T, Katsuno M, Sobue G
    • Organizer
      The 41st annual Meeting of the Japan Neuroscience Society 2018/7/26-29 Kobe, Japan
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] RNA結合タンパク質FUSの機能と神経変性疾患への関わり Importance of Functional Loss of FUS in in neurodegenerative diseases2018

    • Author(s)
      Ishigaki S, Sobue G
    • Organizer
      第41回日本分子生物学会年会 ワークショップ
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] FUS/TLSに関連するALS/FTLDの分子病態 Functional Significance of FUS/TLS in ALS/FTLD2018

    • Author(s)
      石垣診祐
    • Organizer
      第59神経学会学術大会
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] ALS/FTLDにおけるFUSの機能の重要性2017

    • Author(s)
      石垣 診祐
    • Organizer
      2017年度 生命科学系学会合同年次大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Development of a single cell analysis tool for neurological disorders on 2D-plate with positional information. (ポスター)2017

    • Author(s)
      Ishigaki S, Uno H, Wang Z-H, Ukita Y, Bhardwaj R, Tue PT, Yurino H, Hashimoto S, Oka T, Kawahara K, Urisu T, Takamura Y, and Sobue G.
    • Organizer
      The 40th annual Meeting of the Japan Neuroscience Society
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Silencing of FUS in the brain of non-human primates via stereotaxic injection of an adeno-associated virus encoding shRNA.2017

    • Author(s)
      Endo K, Ishigaki S, Fujioka Y, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      WCN 2017
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Aberrant interaction between FUS and SFPQ in 4R-tau dominant tauopathy brains. (ポスター)2017

    • Author(s)
      Ishigaki S, Riku Y, Fujioka Y, Honda D, Yokoi S, Endo K, Kawai K, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Aberrant interaction between FUS and SFPQ in 4R-tau dominant tauopathy brains.2017

    • Author(s)
      Ishigaki S, Riku Y, Fujioka Y, Honda D, Yokoi S, Endo K., Kawai K, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Silencing of FUS in the non-human primate brain via stereotaxic injection of an adeno-associated virus encoding shRNA. (ポスター)2017

    • Author(s)
      Endo K, Ishigaki S, Fujioka Y, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Establishment of adeno-associated virus vector system for silencing FUS in common marmoset brain. (ポスター)2017

    • Author(s)
      Endo K, Ishigaki S, Masamizu Y, Hatanaka N, Fujioka Y, Watakabe A, Yamamori T, Katsuno M, Watanabe H, Matsuzaki M, Nambu A, Sobue G.
    • Organizer
      The 40th annual Meeting of the Japan Neuroscience Society
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] 3’UTR length-dependent control of SynGAP isoform α2 mRNA by FUS and ELAV-like proteins promotes dendritic spine maturation and cognitive function. (ポスター)2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      WCN 2017
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Silencing of FUS in the non-human primate brain via stereotaxic injection of an adeno-associated virus encoding shRNA.2017

    • Author(s)
      Endo K, Ishigaki S, Fujioka Y, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Silencing of FUS in the brain of non-human primates via stereotaxic injection of an adeno-associated virus encoding shRNA.(ポスター)2017

    • Author(s)
      Endo K, Ishigaki S, Fujioka Y, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      WCN 2017
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] FUS and ELAV-like proteins cooperatively control SynGAP isoform α2 in a 3'UTR length-dependent manner to promote dendritic spine maturation and cognitive function.2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] FUS and ELAV-like proteins cooperatively control SynGAP isoform α2 in a 3'UTR length-dependent manner to promote dendritic spine maturation and cognitive function.2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] ALS/FTLDにおけるFUSの機能の重要性2017

    • Author(s)
      石垣診祐
    • Organizer
      2017年度 生命科学系学会合同年次大会
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Cooperative control of SynGAP isoform α2 mRNA stability by FUS and ELAV-like proteins promotes dendritic spine maturation and cognitive function. (ポスター)2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      The 40th annual Meeting of the Japan Neuroscience Society
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] 3’UTR length-dependent control of SynGAP isoform α2 mRNA by FUS and ELAV-like proteins promotes dendritic spine maturation and cognitive function.2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      WCN 2017
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Loss of PSF/SFPQ, an intra-nuclear counterpart of FUS causes FTLD-like phenotypes2016

    • Author(s)
      Fujioka Y, Ishigaki S, Yokoi S, Honda D, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 39th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      パシフィコ横浜(神奈川県 横浜市)
    • Year and Date
      2016-07-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Loss of SFPQ, an intra-nuclear counterpart of FUS causes FTLD-like phenotypes2016

    • Author(s)
      Fujioka Y, Ishigaki S, Yokoi S, Honda D, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 46th Society for Neuroscience annual meeting
    • Place of Presentation
      San Diego, CA(ポスター)
    • Year and Date
      2016-11-12
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] 前頭側頭葉変性症と筋萎縮性側索硬化症の線条体ではstriosomeの障害が特徴である2016

    • Author(s)
      陸 雄一、渡辺 宏久、吉田 眞里、三室 マヤ、岩崎 靖、石垣 診祐、祖父江 元、勝野 雅央
    • Organizer
      第57回神経学会学術大会
    • Place of Presentation
      神戸(ポスター)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Accumulation of phosphorylated tau in neurons in FUS-silenced mice2016

    • Author(s)
      Ishigaki S, Fujioka Y, Honda D, Yokoi S, Endo K., Okado H, Watanabe H, Katsuno M, Takashima A., Sobue G.
    • Organizer
      The 46th Society for Neuroscience annual meeting
    • Place of Presentation
      San Diego, CA
    • Year and Date
      2016-11-12
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Functional linkage between FUS and tau in ALS/FTLD2016

    • Author(s)
      Ishigaki S, Fujioka Y, Honda D, Yokoi S, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 39th annual Meeting of the Japan Neuroscience Society Symposium
    • Place of Presentation
      Yokohama, Japan
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Loss of PSF/SFPQ, an intra-nuclear counterpart of FUS causes FTLD-like phenotypes2016

    • Author(s)
      藤岡 祐介、石垣 診祐、本田 大祐、横井 聡、岡戸 晴生、渡辺 宏久、勝野 雅央、祖父江 元
    • Organizer
      第57回神経学会学術大会
    • Place of Presentation
      神戸
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Loss of SFPQ, an intra-nuclear counterpart of FUS causes FTLD-like phenotypes.2016

    • Author(s)
      28.Fujioka Y, Ishigaki S, Yokoi S, Honda D, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 46th Society for Neuroscience annual meeting
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2016-11-12
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Loss of PSF/SFPQ, an intra-nuclear counterpart of FUS causes FTLD-like phenotypes2016

    • Author(s)
      Fujioka Y, Ishigaki S, Yokoi S, Honda D, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 39th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      横浜(ポスター)
    • Year and Date
      2016-07-20
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Functional linkage between FUS and tau in ALS/FTLD2016

    • Author(s)
      Ishigaki S, Fujioka Y, Honda D, Yokoi S, Okado H, Watanabe H, Katsuno M, Sobue G
    • Organizer
      The 39th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      パシフィコ横浜(神奈川県 横浜市)
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Loss of FUS causes phosphorylated tau accumulation in aged mice2016

    • Author(s)
      石垣 診祐、藤岡 祐介、本田 大祐、横井 聡、岡戸 晴生、渡辺 宏久、勝野 雅央、祖父江 元
    • Organizer
      第57回神経学会学術大会
    • Place of Presentation
      神戸
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] DEVELOPMENT OF A MOLECULAR ANALYSIS CHIP FOR SINGLE CELLS ON 2D-PLANE WITH POSITIONAL INFORMATION2016

    • Author(s)
      Takamura Y, Uno H, Wang Z-H, Ishigaki S, Shimura R, Tue PT, Miyuki C, Shimoda T, Ukita Y, Urisu T, Kawahara K
    • Organizer
      International conference on single cell research 2016
    • Place of Presentation
      Tokyo(ポスター)
    • Year and Date
      2016-11-16
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Loss of SFPQ, an intra-nuclear counterpart of FUS cause FTLD-like phenotypes.2016

    • Author(s)
      Fujioka Y, Ishigaki S, Yokoi S, Honda D, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      Neuroscience 2016
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2016-11-12
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-16K15480
  • [Presentation] Accumulation of phosphorylated tau in neurons in FUS-silenced mice.2016

    • Author(s)
      Ishigaki S, Fujioka Y, Honda D, Yokoi S, Endo K, Okado H, Watanabe H, Katsuno M, Takashima A, Sobue G.
    • Organizer
      Neuroscience 2016
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2016-11-12
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-16K15480
  • [Presentation] Accumulation of phosphorylated tau in neurons in FUS-silenced mice.2016

    • Author(s)
      27.Ishigaki S, Fujioka Y, Honda D, Yokoi S, Endo K., Okado H, Watanabe H, Katsuno M, Takashima A., Sobue G.
    • Organizer
      The 46th Society for Neuroscience annual meeting
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2016-11-12
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] プレーナパッチクランプによる単一細胞解析と外部汚染の検証2016

    • Author(s)
      宇野 秀隆, 王 志宏, 石垣 診祐, 浮田 昭, 高村 禅, 宇理須 恒雄
    • Organizer
      第77用物理学会秋季学術講演会
    • Place of Presentation
      新潟(ポスター)
    • Year and Date
      2016-09-13
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] A rapid functional decline type of sporadic ALS is linked to low expression of TTN2016

    • Author(s)
      Naoki Atsuta, Hazuki Watanabe, AkihiroHirakawa, Ryoichi Nakamura, Masahiro Nakatochi, Shinsuke Ishigaki, Aritoshi Iida, Shiro Ikegawa, Daichi Yokoi, Masahisa Katsuno, Yuishin Izumi, Mitsuya Morita, Akira Taniguchi, Koji Abe, Kouichi Mizoguchi, Osamu Kano, Ryuji Kaji, Gen Sobue,
    • Organizer
      第57回神経学会学術大会
    • Place of Presentation
      神戸(ポスター)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Accumulation of phosphorylated tau in FUS-silenced mice2016

    • Author(s)
      Ishigaki S
    • Organizer
      Brain Protein Aging and Dementia Control International Workshop 2016
    • Place of Presentation
      Nagoya(ポスター)
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] Quality loss of FUS and SFPQ alters the ratio of Tau isoforms, which recapitulates FTLD accompanied with aberrant adult neurogenesis.2015

    • Author(s)
      Ishigaki S, Fujioka Y, Honda D, Yokoi S, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 45th Society for Neuroscience annual meeting
    • Place of Presentation
      Chicago, IL USA
    • Year and Date
      2015-10-17
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Involvement of caudate nucleus head connectivities in ALS2015

    • Author(s)
      渡辺 宏久、桝田 道人、千田 譲、Bagarinao, Epifanio、田中 康博、陸 雄一、中村 良一、渡辺 はづき、伊藤 瑞規、石垣 診祐、熱田 直樹、勝野 雅央、長縄 慎二、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] FTLD-like phenotypes accompanied with aberrant adult neurogenesis are regulated by altered Tau isoforms in FUS-silenced mice2015

    • Author(s)
      Ishigaki S, Fujioka Y, Honda D, Yokoi S, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 10th brain research conference
    • Place of Presentation
      Chicago, IL USA
    • Year and Date
      2015-10-15
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] FUS regulates AMPA receptor function and FTLD-associated behavior2015

    • Author(s)
      本田 大祐、宇田川 剛、藤岡 祐介、田中 基樹、永井 拓、山田 清文、横井 聡、石垣 診祐、渡辺 宏久、勝野 雅央、大野 欽司、曽我部 正博、岡戸 晴生、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Loss of FUS causes a decrease in brain volume accompanied with neuronal loss2015

    • Author(s)
      Fujioka Y, Ishigaki S, Yokoi S, Honda D, Udagawa T, Okado H, Yoshikawa M, Takashima A, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 45th Society for Neuroscience annual meeting
    • Place of Presentation
      Chicago, IL USA
    • Year and Date
      2015-10-17
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Striatum is systematically affected in TDP-43-related FTLD; a pathological study2015

    • Author(s)
      陸 雄一、渡辺 宏久、吉田 眞理、三室 マヤ、岩崎 靖、桝田 道人、勝野 雅央、石垣 診祐、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] FUSの質的機能喪失によるALS/FTLDの病態機構 Quality loss of FUS is involved in the pathogenesis of ALS/FTLD.2015

    • Author(s)
      Ishigaki S, Sobue G
    • Organizer
      第56回神経学会学術大会 シンポジウム
    • Place of Presentation
      新潟県 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-22
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Loss of FUS affects adult neurogenesis by modulating Tau isoforms2015

    • Author(s)
      石垣 診祐、藤岡 祐介、本田 大祐、横井 聡、岡田 洋平、岡戸 晴生、渡辺 宏久、勝野 雅央、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] The loss of FUS leads to brain atrophy accompanied with neuronal loss.2015

    • Author(s)
      Fujioka Y, Ishigaki S, Yokoi S, Honda D, Udagawa T, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 38th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      兵庫県 神戸市 神戸国際会議場
    • Year and Date
      2015-07-28
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] FUSの機能喪失はTau isoform依存的にadult neurogenesis抑制を引き起こす2015

    • Author(s)
      石垣 診祐、 藤岡 祐介、本田 大祐、横井 聡、渡辺 宏久、勝野 雅央、祖父江 元
    • Organizer
      第34回日本認知症学会学術集会
    • Place of Presentation
      青森県 青森市 リンクステーション青森
    • Year and Date
      2015-10-02
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] FUS regulates AMPA receptor function and FTLD/ALS-associated behavior via GluA1 mRNA stabilization2015

    • Author(s)
      Honda D, Udagawa T, Fujioka Y, Tanaka M, Yokoi S, Nagai T, Yamada K, Ishigaki S, Watanabe H, Katsuno M, Ohno K, Sokabe M, Okado H, Sobue G.
    • Organizer
      The 38th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      兵庫県 神戸市 神戸国際会議場
    • Year and Date
      2015-07-28
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] ALS/FTLDの病態におけるFUSの役割 Quality loss of function of FUS in ALS/FTLD2015

    • Author(s)
      石垣 診祐、祖父江 元
    • Organizer
      第15回日本蛋白質科学会年会 ワークショップ
    • Place of Presentation
      徳島県 徳島市 あわぎんホール
    • Year and Date
      2015-06-26
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] FUS knockdown causes the morphologic abnormities of dendritic spines2015

    • Author(s)
      Yokoi S, Ishigaki S, Honda D, Fujioka Y, Udagawa T, Katsuno M, Sobue G.
    • Organizer
      The 38th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      兵庫県 神戸市 神戸国際会議場
    • Year and Date
      2015-07-28
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Aberrant adult neurogenesis in FUS-knockdown mice which exhibited FTLD-like phenotypes2015

    • Author(s)
      Ishigaki S, Fujioka Y, Honda D, Yokoi S, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 38th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      兵庫県 神戸市 神戸国際会議場
    • Year and Date
      2015-07-28
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Suppression of FUS induces the morphologic abnormities of dendritic spines2015

    • Author(s)
      横井 聡、石垣 診祐、宇田川 剛、本田 大祐、藤岡 祐介、勝野 雅央、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Loss of FUS causes a decrease in brain volume accompanied with neuronal loss2015

    • Author(s)
      Fujioka Y, Ishigaki S, Yokoi S, Honda D, Udagawa T, Okado H, Yoshikawa M, Takashima A, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 10th brain research conference
    • Place of Presentation
      Chicago, IL USA
    • Year and Date
      2015-10-15
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Loss of FUS causes a decrease in brain volume accompanied with neuronal loss2015

    • Author(s)
      藤岡 祐介、石垣 診祐、横井 聡、本田 大祐、宇田川 剛、岡戸 晴生、渡辺 宏久、勝野 雅央、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] FUS/TLSからみたALS/FTLDのRNA病態2014

    • Author(s)
      石垣診祐、祖父江 元
    • Organizer
      第33回 日本認知症学会学術集会 シンポジウム
    • Place of Presentation
      横浜市
    • Year and Date
      2014-12-01
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] FUS regulates alternative splicing patterns of Mapt by cooperating with PSF/SFPQ : a novel link between FUS and Tau in the pathogenesis of ALS and FTLD. RNA Metabolism in Neurological Disease2013

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Tsuyoshi Udagawa, Daiyu Honda, Masahisa Katsuno, and Gen Sobue
    • Organizer
      8th Brain Research Conference
    • Place of Presentation
      San Diego, CAアメリカ合衆国
    • Year and Date
      2013-11-17
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Presentation] FUS regulates alternative splicing patterns of Mapt by cooperating with PSF/SFPQ in association with clinicopathological features of ALS/FTLD : a novel link between FUS and Tau in the pathogenesis of ALS and FTLD2013

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Tsuyoshi Udagawa, Daiyu Honda, Masahisa Katsuno, and Gen Sobue
    • Organizer
      The 43rd Society for Neuroscience annual meeting
    • Place of Presentation
      San Diego, CAアメリカ合衆国
    • Year and Date
      2013-11-10
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Presentation] FUS regulates alternative splicing patterns of Mapt by cooperating with PSF/SFPQ in association with clinicopathological features of ALS/FTLD: a novel link between FUS and Tau in the pathogenesis of ALS and FTLD.2013

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Tsuyoshi Udagawa, Daiyu Honda, Masahisa Katsuno, and Gen Sobue
    • Organizer
      The 43rd Society for Neuroscience annual meeting
    • Place of Presentation
      San Diego, CA アメリカ合衆国
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Presentation] FUS regulates alternative splicing patterns of Mapt by cooperating with PSF/SFPQ in neurons: a novel link between FUS and Tau in the pathogenesis of ALS and FTLD.2012

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, and Gen Sobue
    • Organizer
      6th International Symposium of Nanomedicine
    • Place of Presentation
      Matsue, Japan
    • Invited
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Presentation] Comparison of Fus-regulating gene expression and alternative splicing profiles among different primary cells in central nervous system.2012

    • Author(s)
      Yusuke Fujioka, Shinsuke Ishigaki, Akio Masuda, Kinji Ohno, and Gen Sobue
    • Organizer
      The 35th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Presentation] ALSにおけるFUS/TLSの質的機能喪失と病態:FUS/TLSの核内高分子複合体の機能解析から2012

    • Author(s)
      石垣 診祐、 藤岡 祐介、 田中 章景、 祖父江 元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Presentation] Comparison of Fus-regulating gene expression and alternative splicing profiles among different cell lineages in the central nervous system2012

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Akio Masuda, Yohei Iguchi, Masahisa Katsuno, Kinji Ohno, and Gen Sobue
    • Organizer
      The 42nd Society for Neuroscience annual meeting
    • Place of Presentation
      New Orleans, LAアメリカ合衆国
    • Year and Date
      2012-10-14
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Presentation] FUS regulates alternative splicing patterns of Mapt by cooperating with PSF/SFPQ: a novel link between FUS and Tau in the pathogenesis of ALS and FTLD.2012

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Yohei Okada, Akio Masuda, Kinji Ohno, and Gen Sobue
    • Organizer
      The 35th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Presentation] Comparison of Fus-regulating gene expression and alternative splicing profiles among different cell lineages in the central nervous system.2012

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Akio Masuda, Yohei Iguchi, Masahisa Katsuno, Kinji Ohno, and Gen Sobue
    • Organizer
      The 42nd Society for Neuroscience annual meeting
    • Place of Presentation
      New Orleans, LA
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Presentation] 家族性ALS原因遺伝子FUS/TLSノックダウンに伴う選択的splicing変化2012

    • Author(s)
      藤岡 祐介、石垣 診祐、増田 章男、大野 欽司、祖父江 元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Presentation] Quality loss of FUS and SFPQ in the nucleus causes FTLD-like behavioral abnormalities by modulating Tau isoforms.

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Tsuyoshi Udagawa, Daiyu Honda, Satoshi Yokoi, Masahisa Katsuno, Haruo Okado, and Gen Sobue
    • Organizer
      The 37th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      Yokohama, Japan
    • Year and Date
      2014-09-11 – 2014-09-13
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] FUS regulates alternative splicing patterns of Mapt by cooperating with PSF/SFPQ: a novel link between FUS and Tau in the pathogenesis of ALS and FTLD.

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Tsuyoshi Udagawa, Daiyu Honda, Masahisa Katsuno, and Gen Sobue
    • Organizer
      RNA Metabolism in Neurological Disease, 8th Brain Research Conference
    • Place of Presentation
      San Diego, CA アメリカ合衆国
    • Data Source
      KAKENHI-PROJECT-24659429
  • [Presentation] FUSとSFPQの複合体はMaptの選択的splicingを制御しALS/FTLDの高次機能障 害に関与する

    • Author(s)
      石垣 診祐、 藤岡 祐介、 宇田川 剛、本田 大祐、横井 聡、渡辺 宏 久、勝野 雅央、祖父江 元
    • Organizer
      第33回 日本認知症学会学術集会
    • Place of Presentation
      横浜市
    • Year and Date
      2014-11-29 – 2014-12-01
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] The involvement of glial cells in FUS-related ALS/FTLD pathophysiology -FUS knock-down glial cells have a neuro-protective effect.

    • Author(s)
      Yusuke Fujioka, Shinsuke Ishigaki, Takashi Shiromizu, Tsuyoshi Udagawa,Satoshi Yokoi, Daiyu Honda, Kensuke Ikenaka, Masahisa Katsuno, Takeshi Tomonaga and Gen Sobue
    • Organizer
      The 43rd Society for Neuroscience annual meeting
    • Place of Presentation
      Washington DC, USA
    • Year and Date
      2014-11-15 – 2014-11-19
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] FUSはGluA1 mRNA安定性の調節を介してシナプス機能及びFTLD様行動を制御する

    • Author(s)
      渡辺宏久、宇田川剛、藤岡祐介、本田大祐、横井聡、石垣診祐、田中基樹、曽我 部正博、永井拓、山田清文、岡戸晴生、大野欽司、勝野雅央、祖父江元
    • Organizer
      第33回 日本認知症学会学術集会
    • Place of Presentation
      横浜市
    • Year and Date
      2014-11-29 – 2014-12-01
    • Data Source
      KAKENHI-PLANNED-26117004
  • [Presentation] The involvement of glial cells in FUS-related ALS/FTLD pathology -FUS knock-down glial cells have a neurotrophic effect.-

    • Author(s)
      Yusuke Fujioka, Shinsuke Ishigaki, Takashi Shiromizu, Tsuyoshi Udagawa, Satoshi Yokoi, Daiyu Honda, Kensuke Ikenaka, Masahisa Katsuno, Takeshi Tomonaga, and Gen Sobue
    • Organizer
      The 37th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      Yokohama, Japan
    • Year and Date
      2014-09-11 – 2014-09-13
    • Data Source
      KAKENHI-PLANNED-26117004
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