• Search Research Projects
  • Search Researchers
  • How to Use
  1. Back to previous page

FUJIMURA Yochihiro  藤村 吉博

ORCIDConnect your ORCID iD *help
… Alternative Names

FUJIMURA Yoshihiro  藤村 吉博

藤村 〓博  フジムラ ヨシヒロ

Less
Researcher Number 80118033
Other IDs
External Links
Affiliation (based on the past Project Information) *help 2014 – 2015: 奈良県立医科大学, 医学部, その他
2014: 奈良県立医科大学, 医学部, 名誉教授
2014: 奈良県立医科大学, 輸血部, 名誉教授
2003 – 2013: 奈良県立医科大学, 医学部, 教授
2010: 奈良県医科大学, 医学部, 教授 … More
2004: 奈良県立医科大学, 輸血部, 教授
1996 – 2001: Department of Blood Transfusion, Nara Medical University, Professor, 輸血部, 教授
1999 – 2000: 奈良県立医科大学, 医学部, 教授
1995: 奈良県立医科大学, 輸血部, 助教授
1994: 奈良医科大学, 医学部・附属病院, 助教授
1992 – 1993: 奈良医科大学, 輸血部, 助教授
1990 – 1993: 奈良県立医科大学, 医学部, 助教授
1992: NARA MEDICAL UNIVERSITY, TRANSFUSION, ASSOCIATE PROFESSOR, 医学部(輸血部), 助教授
1987 – 1989: 奈良県立医科大学, 輸血部, 助教授 Less
Review Section/Research Field
Principal Investigator
Hematology / Circulatory organs internal medicine / Pediatrics
Except Principal Investigator
Gastroenterology / Hematology / Sports science / Structural biochemistry / 物質生物化学 / Kidney internal medicine / Digestive surgery / Pediatrics / Applied health science
Keywords
Principal Investigator
ADAMTS13 / UL-VWFM / HUS / TTP / VWF / フォンビルブランド因子 / stellate cell / 肝墨細胞 / 肝星細胞 / UPSHAW-SCHULMAN SYNDROME … More / SHEAR-INDUCED PLATELET AGGREGATION / VWF-Cpase / PLACENTAL ECTO-ATPDase / SNAKE VENOM / VON WILLEBRAND FACTOR / マムシギン / 血小板膜等蛋白Ib結合蛋白 / Stx-1 / Upshaw-Cchulman症候群 / 胎盤ecto-ATPDase / Upshaw-Schulman症候群 / ずり応力惹起血小板凝集 / vWF-CPase / 胎盤ecoto-ATPDase / 蛇毒 / 胎盤E-NTPDase / 正常妊娠経過 / 妊娠中毒症 / 補体調節因子 / 活性型VWF / 胎盤由来E-NTPase / 胎盤由来E-NTPDase / VEF / HELLP症候群 / 妊娠関連TMA / 抗GPIbモノクロナ-ル抗体 / 血小板粘着反応 / ボトロンビン / ボトロセチン / リストセチン / GPIIb / フオン ビルブランド因子 / SS結合 / シアール酸 / bothrombin / dispase / IIIa / GPII b / GPIb / von Willebrand factor / botrocetin … More
Except Principal Investigator
ADAMTS13 / VWF / TMA / 血小板凝集 / von Willebrand factor / 血小板膜糖タンパク質(GP)Ib / ジスインテグリン / ボトロセチン / フォンビルブラント因子 / アルコール性肝炎 / 肝硬変 / 多臓器不全 / 微小循環障害 / 肝星細胞 / 脱水 / UL-VWFM / IIIa / dehydration / sweating / 発汗 / ビチスセチン / マムシギン / GPIb結合タンパク質 / vWF活性化因子 / フォンビルブランド因子 / Ristocetin / Botrocetin / Platelet Aggregation / 高分子量出血性メタロプロテアーゼ / コラーゲン / フィブリノーゲン / ボトロンビン / リストセチン / vWF / 急性肝不全 / インヒビター / 劇症肝炎 / 血栓形成 / 造血幹細胞移植 / 造血幹細胞移植学 / 肝切除 / Asparagine(N)-linked Sugar Chain / Monoclonal Antibody / Glycoprotein(GP)IIb / Glycoprotein(GP)Ib / von Willebrand Factor / セリン結合糖鎖 / トレオニン / コラーゲン結合ドメイン / ヘパリン結合ドメイン / 血液凝固第VIII因子結合ドメイン / 血小板膜糖タンパク質 / フォンビルラント因子 / エピトープ / モノクロナール抗体 / ジスルヒド結合 / アミノ酸配列 / フォルビルブラント因子 / 血小板膜GPIIb@IIIa / 血小板膜GPIb / アスパラギン結合糖鎖 / 単クロ-ン抗体 / 血小板膜GPIIb / 血小板膜GPlb / Exercise / HCT / 循環血漿量 / 夏季 / ヘマトクリット値 / スポーツ / Renal failure / HUS / TTP / 膠原病 / 腎機能障害 / thrombi formation / mild exercise / hard exercise / vWF-CPase / Ul-vWFM / 水分摂取 / 運動負荷 / VWF-CPass / 低強度運動 / 高強度運動 / Primary structure / Disintegrin / Metalloproteinase / Kaouthiagin / Bitiscetin / Platelet aggregation / Snake venom protein / ハリスターゼ / 血小板GPIb結合タンパク質 / フォンビルプラント因子(vWF) / 胎盤特異的ectoATPDase / フォンビルブラント因子(vWF) / 生理的vWFプロテナーゼ / フォンビルブランド因子(vWF) / 一次構造 / メタロプロテナーゼ / コーシャギン / ビチセチン / 蛇毒タンパク質 / Type III collagen / Extracellular matrix / GPIb-binding proteins / vWF modulator protein / aggregation / Platelet adhesion / ビチスチン / フラボセチンA,B / トカラセチン / ジャララカGPIb-BP / アルボアグレギン-B / ジャララカ GPIb-BP / III型コラーゲン / 細胞外マトリックス / 血小板粘着・凝集 / Fibrinogen / alpha-Thrombin / Bothrombin / Lectin / von Wellebrand Factor / アルボアルグレギンB / レクチン / フォンビルブラント病 / vWF subunit / vWF gene / vWD TypeIIC / vWD TypeIIB / vWD TypeIIA / vWD TypeI / von Willebrand disease / 結合能 / VNTR / RFLPs / vWF遺伝子 / 第VIII因子(F.VIII) / vWD Normandy rariant / vWD type / vWD typeIIA / vWD typeI / von Willebrand病 / vWD Type III / vWD Type IID / vWD Type IIC / vWD Type IIA / vWD Type I / vWF-Subunit / von Willebrand因子(vWF) / von Willebrand病(vWD) / VWD TypeIII / VWD TypeIID / VWD TypeIIC / VWD TypeIIA / VWD TypeI / VWF-Subunit / von Willebrand因子(VWF) / von Willebrand病(VWD) / Factor H自己抗体 / atypical HUS / H因子 / 第二経路 / 微小血管障害症 / 非典型溶血性尿毒症症候群 / C3 / Factor H / 補体 / aHUS / 血栓性微小血管症 / サイトカイン / SCT / 生体肝移植 / 第VIII因子 / 肝細胞移植 / 門脈血 / 部分肝移植 / 血友病 / 異所性肝移植 / 肝不全 / ヘマトクリット(HCT) / 水分摂取量 / 老化 / スポーツ活動 / VOD / 診断マーカー / 虚血再灌流 障害 / 拒絶反応 / von Willebrand因子 / 肝移植 Less
  • Research Projects

    (22 results)
  • Research Products

    (316 results)
  • Co-Researchers

    (38 People)
  •  Development of novel methods for diagnosis and management of thrombotic microangiopathy following stem cell transplantation

    • Principal Investigator
      Matsumoto Masanori
    • Project Period (FY)
      2013 – 2015
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Hematology
    • Research Institution
      Nara Medical University
  •  Establishment of the diagnostic system of patients with atypical hemolytic uremic syndrome, and analysis of the characteristics of aHUS patients in Japan

    • Principal Investigator
      YOSHIDA Yoko
    • Project Period (FY)
      2013 – 2014
    • Research Category
      Grant-in-Aid for Young Scientists (B)
    • Research Field
      Kidney internal medicine
    • Research Institution
      The University of Tokyo
      Nara Medical University
  •  重症肝障害におけるADAMTS13の生体内存在様式と制御機構

    • Principal Investigator
      植村 正人
    • Project Period (FY)
      2011 – 2013
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Gastroenterology
    • Research Institution
      Nara Medical University
  •  Analysis of the pathology and regulation system in pregnancy-associated thrombotic microangiopathy (TMA)Principal Investigator

    • Principal Investigator
      FUJIMURA Yoshihiro
    • Project Period (FY)
      2011 – 2014
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Hematology
    • Research Institution
      Nara Medical University
  •  Development of novel therapy for thrombotic microangiopathy after hematopoietic stem cell transplantation.

    • Principal Investigator
      MATSUMOTO Masanori
    • Project Period (FY)
      2010 – 2012
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Hematology
    • Research Institution
      Nara Medical University
  •  Heterotopic living-donor partial liver transplantation as a therapy for cure of hemophilia

    • Principal Investigator
      KO Saiho
    • Project Period (FY)
      2009 – 2011
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Digestive surgery
    • Research Institution
      Nara Medical University
  •  Elucidation of mechanism of thrombus formation in older people during sporting activity and preventive measure thereof

    • Principal Investigator
      ISHIZASHI Hiromichi
    • Project Period (FY)
      2008 – 2010
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Applied health science
    • Research Institution
      Nara Medical University
  •  Determination of ADAMTS13 and its regulation mechanism in severe liver disturbance

    • Principal Investigator
      UEMURA Masahito
    • Project Period (FY)
      2008 – 2010
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Gastroenterology
    • Research Institution
      Nara Medical University
  •  Analysis of TMA and VOD after allogenic stem cell transplantation

    • Principal Investigator
      MATSUMOTO Masanori
    • Project Period (FY)
      2007 – 2009
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Hematology
    • Research Institution
      Nara Medical University
  •  Clinical relevance of VWF cleaving protease as a new doagnostic marker in liver transplant recipients

    • Principal Investigator
      KO Saiho
    • Project Period (FY)
      2006 – 2008
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Digestive surgery
    • Research Institution
      Nara Medical University
  •  Potential Role of Dehydration on Thrombogenic Processes during Exercise

    • Principal Investigator
      ISHIZASHI Hiromichi
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Sports science
    • Research Institution
      Nara Medical University
  •  ADAMTS13の解析と重症肝疾患における微小循環障害の発生機序の解明

    • Principal Investigator
      植村 正人
    • Project Period (FY)
      2005 – 2007
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Gastroenterology
    • Research Institution
      Nara Medical University
  •  Analysis of ADATS13 in TMA patients with severe renal damage

    • Principal Investigator
      MATSUMOTO Masanori
    • Project Period (FY)
      2004 – 2006
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Kidney internal medicine
    • Research Institution
      Nara Medical University
  •  Study on the prediction of thrombosis formation during exercise

    • Principal Investigator
      ISHIZASHI Hiromichi
    • Project Period (FY)
      2003 – 2004
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Sports science
    • Research Institution
      Nara Medical University
  •  Analysis of various type thrombosis with decreased ADAMTS13 activityPrincipal Investigator

    • Principal Investigator
      FUJIMURA Yoshihiro
    • Project Period (FY)
      2003 – 2005
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Hematology
    • Research Institution
      Nara Medical University
  •  MOLECULAR DESIGN OF INHIBITORS ON THE FORMATION OF VON WILLEBRAND FACTOR-DEPENDENT PLATELET THROMBIPrincipal Investigator

    • Principal Investigator
      FUJIMURA Yoshihiro
    • Project Period (FY)
      1999 – 2001
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Circulatory organs internal medicine
    • Research Institution
      NARA MEDICAL UNIVERSITY
  •  Structure-Function Relationships of Proteins Modulating Platelet Adhesion and Aggregation

    • Principal Investigator
      TITANI Koiti
    • Project Period (FY)
      1997 – 2000
    • Research Category
      Grant-in-Aid for Scientific Research (B).
    • Research Field
      Structural biochemistry
    • Research Institution
      Fujita Health University
  •  Structure-Function Relationships of Proteins Which Modulate Platelet Aggregation.

    • Principal Investigator
      TITANI Koiti
    • Project Period (FY)
      1994 – 1996
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Structural biochemistry
    • Research Institution
      Fujita Health University
  •  抗血小板血栓剤の開発を目的とした血小板粘着反応の分子機作の解析Principal Investigator

    • Principal Investigator
      藤村 〓博 (藤村 吉博)
    • Project Period (FY)
      1991 – 1993
    • Research Category
      Grant-in-Aid for General Scientific Research (C)
    • Research Field
      Pediatrics
    • Research Institution
      Nara Medical University
  •  Structure and function of adhesive molecules involved in platelet aggregation and other lymphoid cell interactions.

    • Principal Investigator
      TITANI Koiti
    • Project Period (FY)
      1991 – 1993
    • Research Category
      Grant-in-Aid for General Scientific Research (B)
    • Research Field
      物質生物化学
    • Research Institution
      Fujita Health University
  •  Molecular genetic study on patients with various types of von Willebrand disease

    • Principal Investigator
      FUKUI Hiromu
    • Project Period (FY)
      1990 – 1992
    • Research Category
      Grant-in-Aid for General Scientific Research (B)
    • Research Field
      Pediatrics
    • Research Institution
      NARA MEDICAL UNIVERSITY
  •  Studies on platelet aggregation by structural analysis of von Willebrand factor

    • Principal Investigator
      TITANI Koiti
    • Project Period (FY)
      1987 – 1989
    • Research Category
      Grant-in-Aid for General Scientific Research (A)
    • Research Field
      物質生物化学
    • Research Institution
      Fujita Health University

All 2015 2014 2013 2012 2011 2010 2009 2008 2007 2006 2005 2004 2003 Other

All Journal Article Presentation Book Patent Other

  • [Book] ADAMTS132015

    • Author(s)
      Fujimura Y, Kokame K, Yagi H, Isonishi A, Matsumoto M, Miyata T
    • Total Pages
      184
    • Publisher
      Springer
    • Data Source
      KAKENHI-PROJECT-25461456
  • [Book] ADAMTS13 book2015

    • Author(s)
      Fujimura Y, Kokame K, Yagi H, Isonishi A, Matsumoto M, Miyata T
    • Publisher
      Springer (edited by George Rodgers)
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Book] 「後天性 TTP に対するリツキシマブ療法」 Annual Review 血液2013

    • Author(s)
      松本雅則,藤村吉博
    • Publisher
      中外医学社
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Book] Annual Review 2013 血液2013

    • Author(s)
      松本雅則、藤村吉博
    • Total Pages
      8
    • Publisher
      中外医学社
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Book] Annual Review 血液2013

    • Author(s)
      松本雅則、藤村吉博
    • Total Pages
      8
    • Publisher
      中外医学社
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Book] 新版日本輸血・細胞治療学会認定医制度指定カリキュラム2012

    • Author(s)
      藤村吉博
    • Total Pages
      3
    • Publisher
      日本輸血・細胞治療学会
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Book] Trends in alcoholic liver disease research-clinical and scientific aspects, editor Ichiro Shimizu, Chapter 10. Crucial role of ADMTS13 related to endotoxemia and subsequent cytokinemia in the progression of alcoholic hepatitis.2011

    • Author(s)
      Uemura M, Fujimura Y, Matsuyama T, et al.
    • Publisher
      In Tech d.o.o.
    • Data Source
      KAKENHI-PROJECT-23590988
  • [Book] Annual review 消化器 2011, 林 紀夫, 日比紀文, 上西紀夫, 下瀬川 徹編. 第III章 胆膵 - 膵臓2. 急性膵炎重症化と血漿ADAMTS13活性2011

    • Author(s)
      植村正人、藤村吉博、福井 博
    • Publisher
      中外医学社
    • Data Source
      KAKENHI-PROJECT-23590988
  • [Book] 『Annual Review消化器』2011急性膵炎重症化と血漿ADAMTS13活性2011

    • Author(s)
      植村正人、藤村吉博、福井博
    • Publisher
      中外医学社
    • Data Source
      KAKENHI-PROJECT-20590794
  • [Book] 重症肝・膵疾患における多臓器不全の病態解析-ADAMTS13を中心に- 消化器病学の進歩-原点から未来への情報発信-第94回日本消化器病学会総会記録誌III 複合領域2009

    • Author(s)
      植村正人、藤村吉博、福井博
    • Publisher
      日本消化器病学会
    • Data Source
      KAKENHI-PROJECT-20590794
  • [Book] ADAMTS13とTTP-最近の進歩-. Annual Review血液20092009

    • Author(s)
      松本雅則, 藤村吉博
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Book] 「腎と透析」2008年増刊号 血液浄化療法-2008, 血液浄化療法の臨床, 8. 単純血漿交換・二重膜濾過血漿交換・血漿吸着の主な適応. (北岡建樹、秋澤忠男、佐中 孔、服部元久、堀江重朗、新田孝作編)、東京医学社, 東京、2008

    • Author(s)
      植村正人, 藤村吉博.
    • Publisher
      血液疾患 (4)TTP(掲載確定)
    • Data Source
      KAKENHI-PROJECT-17590670
  • [Book] von Willebrand病-最近の進歩. Annual Review血液20082008

    • Author(s)
      松本雅則, 藤村吉博
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Book] 「腎と透析」2008年増刊号 血液浄化療法-2008, 血液浄化療法の臨床, 8.単純血漿交換・二重膜濾過血漿交換・血漿吸着の主な適応2)血液疾患(4)TTP2008

    • Author(s)
      植村 正人, 藤村 吉博
    • Publisher
      東京医学社(掲載確定)
    • Data Source
      KAKENHI-PROJECT-17590670
  • [Book] Thrombotic microangiopathy. Recent Advances of Thrombosis and Hemaostasis.2008

    • Author(s)
      Fujimura Y, Matsumoto M, Yagi H
    • Publisher
      Springer Verlag
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Book] Recent Advances of Thrombosis and Hemaostasis.2008

    • Author(s)
      Fujimura Y, Matsumoto M, 他1名
    • Publisher
      Springer Verlag(In press)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Book] 血栓と循環急性腎不全 2)血栓性血小板減少性紫斑病2008

    • Author(s)
      植村正人, 藤村吉博
    • Publisher
      メディカルレビュー社
    • Data Source
      KAKENHI-PROJECT-20590794
  • [Book] 血栓性血小板減少性紫斑病、三輪血液学2005

    • Author(s)
      松本雅則, 藤村吉博
    • Total Pages
      2070
    • Publisher
      文光堂
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Book] 薬剤によるTTPの発症機序とその場合の治療について教えてください2005

    • Author(s)
      植村正人, 藤村吉博
    • Publisher
      メデイカルレビュウ社
    • Data Source
      KAKENHI-PROJECT-17590670
  • [Journal Article] von Willebrand Factor-Rich Platelet Thrombi in the Liver Cause Sinusoidal Obstruction Syndrome following Oxaliplatin-Based Chemotherapy.2015

    • Author(s)
      Nishigori N, Matsumoto M, Koyama F, Hayakawa M, Hatakeyayama K, Ko S, Fujimura Y, Nakajima Y.
    • Journal Title

      PLoS One

      Volume: 10 Issue: 11 Pages: e0143136-e0143136

    • DOI

      10.1371/journal.pone.0143136

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-25461456
  • [Journal Article] A Novel Quantitative Hemolytic Assay Coupled with Restriction Fragment Length Polymorphisms Analysis Enabled Early Diagnosis of Atypical Hemolytic Uremic Syndrome and Identified Unique Predisposing Mutations in Japan.2015

    • Author(s)
      Yoshida Y, Miyata T, Matsumoto M, Shirotani-Ikejima H, Uchida Y, Ohyama Y, Kokubo T, Fujimura Y.
    • Journal Title

      PLos One

      Volume: 印刷中

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-25860685
  • [Journal Article] Poor-responder to plasma exchange therapy in acquired TTP is associated with ADAMTS13 inhibitor boosting: Visualization of an ADAMTS13-inhibitor complex, and its proteolytic clearance from plasma.2015

    • Author(s)
      Isonishi A, Bennett CL, Plaimauer B, Scheiflinger F, Matsumoto M, Fujimura Y.
    • Journal Title

      Transfusion

      Volume: in press

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-25461456
  • [Journal Article] A unique case involving a female patient with Upshaw-Schulman syndrome: low titers of antibodies against ADAMTS13 prior to pregnancy disappeared after successful deliver.2015

    • Author(s)
      Ogawa Y, Matsumoto M, Sadakata H, Isonishi A, Kato S, Nojima Y, Fujimura Y.
    • Journal Title

      Transfus Med Hemother.

      Volume: 42 Issue: 1 Pages: 59-63

    • DOI

      10.1159/000370225

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-25461456
  • [Journal Article] Familial C3 glomerulonephritis associated with mutations in the gene for complement factor B.2015

    • Author(s)
      Imamura H, Konomoto T, Tanaka E, Hisano S, Yoshida Y, Fujimura Y, Miyata T, Nunoi H.
    • Journal Title

      Nephrol Dial Transplant.

      Volume: 30 Issue: 5 Pages: 862-864

    • DOI

      10.1093/ndt/gfv054

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-24390250, KAKENHI-PROJECT-25860873
  • [Journal Article] Poor responder to plasma exchange therapy in acquired thrombotic thrombocytopenic purpura is associated with ADAMTS13 inhibitor boosting: visualization of an ADAMTS13 inhibitor complex and its proteolytic clearance from plasma.2015

    • Author(s)
      Isonishi A, Bennett CL, Plaimauer B, Scheiflinger F, Matsumoto M, Fujimura Y.
    • Journal Title

      Transfusion

      Volume: 55 Issue: 10 Pages: 2321-2330

    • DOI

      10.1111/trf.13182

    • Peer Reviewed / Acknowledgement Compliant / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-25461456
  • [Journal Article] A rapid, fully automatic and highly sensitive ADAMTS13 gold particle immunoassay using a routine biochemistry analyser.2015

    • Author(s)
      Kato S, Tanaka M, Isonishi A, Matsumoto M, Samori T, Fujimura Y.
    • Journal Title

      Brit J Haematol

      Volume: in press Issue: 4 Pages: 655-658

    • DOI

      10.1111/bjh.13425

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-25461456
  • [Journal Article] Familial C3 glomerulonephritis associated with mutations in the gene for complement factor B.2015

    • Author(s)
      Imamura H, Konomoto T, Tanaka E, Hisano S, Yoshida Y, Fujimura Y, Miyata T, Nunoi H.
    • Journal Title

      Nephrol Dial Transplant.

      Volume: 印刷中

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25860685
  • [Journal Article] A Novel Quantitative Hemolytic Assay Coupled with Restriction Fragment Length Polymorphisms Analysis Enabled Early Diagnosis of Atypical Hemolytic Uremic Syndrome and Identified Unique Predisposing Mutations in Japan.2015

    • Author(s)
      Yoshida Y, Miyata T, Matsumoto M, Shirotani-Ikejima H, Uchida Y, Ohyama Y, Kokubo T, Fujimura Y.
    • Journal Title

      PLos One.

      Volume: 10 Issue: 5 Pages: e0124655-e0124655

    • DOI

      10.1371/journal.pone.0124655

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-25461456, KAKENHI-PROJECT-15K06953
  • [Journal Article] Poor-responder to plasma exchange therapy in acquired TTP is associated with ADAMTS13 inhibitor boosting: Visualization of an ADAMTS13-inhibitor complex, and its proteolytic clearance from plasma.2015

    • Author(s)
      Isonishi A, Bennett C.L., Plaimauer B, Scheiflinger F, Matsumoto M, Fujimura Y.
    • Journal Title

      Transfusion

      Volume: in press

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Eculizumab in the treatment of atypical hemolytic uremic syndrome in an infant leads to cessation of peritoneal dialysis and improvement of severe hypertension.2015

    • Author(s)
      Ohta T, Urayama K, Tada Y, Furue T, Imai S, Matsubara K, Ono H, Sakano T, Jinno K, Yoshida Y, Miyata T, Fujimura Y.
    • Journal Title

      Pediatr Nephrol.

      Volume: 30 Issue: 4 Pages: 603-608

    • DOI

      10.1007/s00467-014-2975-4

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-24390250, KAKENHI-PROJECT-25860685
  • [Journal Article] STEC:O111-HUS complicated by acute encephalopathy in a young girl was successfully treated with a set of hemodiafiltration, steroid pulse, and soluble thrombomodulin, under plasma exchange.2015

    • Author(s)
      Yada N, Fujioka M, Bennett CL, Inoki K, Miki T, Watanabe A, Yoshida T, Hayakawa M, Matsumoto M, Fujimura Y.
    • Journal Title

      Clin Case Rep.

      Volume: 3 Issue: 4 Pages: 208-212

    • DOI

      10.1002/ccr3.196

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-25461456
  • [Journal Article] Candidate gene analysis using genomic quantitative PCR: identification of ADAMTS13 large deletions in two patients with Upshaw-Schulman syndrome.2014

    • Author(s)
      Eura Y, Kokame K, Takafuta T, Tanaka R, Kobayashi H, Ishida F, Hisanaga S, Matsumoto M, Fujimura Y, Miyata T.
    • Journal Title

      olecular Genetics & Genomic Medicine.

      Volume: 2 Issue: 3 Pages: 240-244

    • DOI

      10.1002/mgg3.64

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-24390250, KAKENHI-PROJECT-25440060, KAKENHI-PROJECT-25461456
  • [Journal Article] Response to 'Death during pregnancy: thrombotic thrombocytopenic purpura or septic shock?'.2014

    • Author(s)
      Takuma Y, Fujimura Y, Emoto Y, Kuriu Y, Iino M, Matoba R.
    • Journal Title

      J Obstet Gynaecol Res.

      Volume: 40 Issue: 3 Pages: 887-887

    • DOI

      10.1111/jog.12220

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] A first bout of thrombotic thrombocytopenic purpura triggered by herpes simplex infection in a 45-year-old nulliparous female with Upshaw-Schulman syndrome.2014

    • Author(s)
      Morioka M, Matsumoto M, Saito M, Kokame K, Miyata T, Fujimura Y.
    • Journal Title

      Blood Transfus.

      Volume: 12

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] 非典型HUSにおける補体異常とその解析2014

    • Author(s)
      吉田瑶子、藤村吉博、宮田敏行
    • Journal Title

      細胞 The cell

      Volume: 46 Pages: 7-10

    • Data Source
      KAKENHI-PROJECT-25860685
  • [Journal Article] Analysis of patients with atypical hemolytic uremic syndrome treated at the Mie University Hospital: Concentration of C3 p.I1157T mutation.2014

    • Author(s)
      Matsumoto T, Fan X, Ishikawa E, Ito M, Amano K, Toyoda H, Komada Y, Ohishi K, Katayama N, Yoshida Y, Matsumoto M, Fujimura Y, Ikejiri M, Wada H, Miyata T.
    • Journal Title

      Int J Hematol.

      Volume: 100 Issue: 5 Pages: 437-442

    • DOI

      10.1007/s12185-014-1655-2

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-24390250, KAKENHI-PROJECT-25461413, KAKENHI-PROJECT-25461456, KAKENHI-PROJECT-25860685
  • [Journal Article] Case of maternal and fetal deaths due to severe congenital thrombotic thrombocytopenic purpura (Upshaw-Schulman syndrome) during pregnancy.2014

    • Author(s)
      Tanaka H, Tenkumo C, Mori N, Kokame K, Fujimura Y, Hata T.
    • Journal Title

      J Obset Gynaecol Res.

      Volume: 40 Issue: 1 Pages: 247-249

    • DOI

      10.1111/jog.12125

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-25440060
  • [Journal Article] Postoperative atypical hemolytic uremic syndrome associated with complement c3 mutation.2014

    • Author(s)
      Matsukuma E, Imamura A, Iwata , Takeuchi T, Yoshida Y, Fujimura Y, Fan X, Miyata T, Kuwahara T.
    • Journal Title

      Case Rep Nephrol.

      Volume: 2014 Pages: 784943-784943

    • DOI

      10.1155/2014/784943

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-24390250, KAKENHI-PROJECT-25860685
  • [Journal Article] A first bout of thrombotic thrombocytopenic purpura triggered by herpes simplex infection in a 45-year-old nulliparous female with Upshaw-Schulman syndrome.2014

    • Author(s)
      Morioka M, Matsumoto M, Saito M, Kokame K, Miyata T, Fujimura Y.
    • Journal Title

      Blood Transfus

      Volume: Supp 1

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461456
  • [Journal Article] Diagnostic criteria for atypical hemolytic uremic syndrome proposed by the Joint Committee of the Japanese Society of Nephrology and the Japan Pediatric Society.2014

    • Author(s)
      Sawai T, Nangaku M, Ashida A, Fujimaru R, Hataya H, Hidaka Y, Kaname S, Okada H, Sato W, Yasuda T, Yoshida Y, Fujimura Y, Hattori M, Kagami S.
    • Journal Title

      Clin Exp Nephrol.

      Volume: 18 Issue: 1 Pages: 4-9

    • DOI

      10.1007/s10157-013-0911-8

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-25860685
  • [Journal Article] Identification of N-linked glycosylation and putative O-fucosylation, C-mannosylation sites in plasma derived ADAMTS13.2014

    • Author(s)
      Sorvillo N, Kaijen PH, Matsumoto M, Fujimura Y, van der Zwaan C, Verbij FC, Pos W, Fijnheer R, Voorberg J, Meijer AB.
    • Journal Title

      J Thromb Haemost

      Volume: 12 Pages: 670-679

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461456
  • [Journal Article] 非典型溶血性尿毒症症候群-病態・診断およびエクリズマブの効果-2014

    • Author(s)
      吉田瑶子、藤村吉博
    • Journal Title

      Medical Practice

      Volume: 31 Pages: 100-102

    • Data Source
      KAKENHI-PROJECT-25860685
  • [Journal Article] Effect of ADAMTS-13 on cerebrovascular microthrombosis and neuronal injury after experimental subarachnoid hemorrhage.2014

    • Author(s)
      Muroi C, Fujioka M, Mishima K, Irie K, Fujimura Y, Nakano T, Fandino J, Keller E, Iwasaki K, Fujiwara M.
    • Journal Title

      J Thromb Haemost.

      Volume: 12(4) Issue: 4 Pages: 505-514

    • DOI

      10.1111/jth.12511

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23590654, KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-26462170
  • [Journal Article] 非典型溶血性尿毒症症候群(aHUS)の病態と治療戦略2014

    • Author(s)
      吉田瑶子, 藤村吉博.
    • Journal Title

      血液内科

      Volume: 69 Pages: 589-594

    • NAID

      40020237165

    • Data Source
      KAKENHI-PROJECT-25860685
  • [Journal Article] ADAMTS13 unbound to larger von Willebrand factor multimers in cryosupernatant :Implications for selection of plasma preparations for TTP treatment2013

    • Author(s)
      Hori Y, Hayakawa M, Isonishi A, Soejima K, Matsumoto M, Fujimura Y
    • Journal Title

      Transfusion

      Volume: (in press)

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Limited renal prophylaxis in regular plasmatherapy for heritable ADAMTS13 deficiency.2013

    • Author(s)
      Doi T, Ohga S, Ito N, Ishimura M, Suga N, Nomura A, Takada H, Matsumoto M, Fujimura Y, Hara T.
    • Journal Title

      Pediatr Blood Cancer.

      Volume: 60 Issue: 9 Pages: 1557-1558

    • DOI

      10.1002/pbc.24553

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-24591551
  • [Journal Article] Analysis of genetic and predisposing factors in Japanese patients with atypical hemolytic uremic syndrome2013

    • Author(s)
      Fan X, Yoshida Y, Honda S, Matsumoto M, Sawada Y, Hattori M, Hisanaga S, Hiwa R, Nakamura F, Tomomori M, Miyagawa S, Fujimaru R, Yamada H, Sawai T, Ikeda Y, Iwata N, Uemura O, Matsukuma E, Aizawa Y, Harada H, Wada H, Ishikawa E, Ashida A, Nangaku M, Miyata T, Fujimura Y
    • Journal Title

      Mol Immunol

      Volume: 54 Pages: 238-246

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Drug-induced Thrombotic Thrombocytopenic Purpura Successfully Treated with Recombinant Human Soluble Thrombomodulin.2013

    • Author(s)
      Nishijima Y, Hirata H, Himeno A, Kida H, Matsumoto M, Takahashi R, Otani Y, Inoue K, Nagatomo I, Takeda Y, Kijima T, Tachibana I, Fujimura Y, Kumanogoh A.
    • Journal Title

      Intern Med.

      Volume: 52 Pages: 1111-1114

    • NAID

      130003365599

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Limited renal prophylaxis in regular plasmatherapy for heritable ADAMTS13 deficiency2013

    • Author(s)
      Doi T, Ohga S, Ito N, Ishimura M, Suga N, Nomura A, Takada H, Matsumoto M, Fujimura Y, Hara T
    • Journal Title

      Pediatr Blood Cancer

      Volume: (in press)

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] ADAMTS13 unbound to larger von Willebrand factor multimers in cryosupernatant: implications for selection of plasma preparations for thrombotic thrombocytopenic purpura treatment.2013

    • Author(s)
      Hori Y, Hayakawa M, Isonishi A, Soejima K, Matsumoto M, Fujimura Y.
    • Journal Title

      Transfusion.

      Volume: 53 Issue: 12 Pages: 3192-3202

    • DOI

      10.1111/trf.12182

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-25461456
  • [Journal Article] Therapeutic Modality of 11 Patients with TTP in a Single Institution in Miyazaki from 2000 to 20112013

    • Author(s)
      Kawano N, Yokota-Ikeda N, Yoshida S, Kuriyama T, Yamashita K, Sugio Y, Makino S, Ono N, Inoue Y, Himeji D, Kodama K, Uezono S, Shimao Y, Ueda A, Matsumoto M, Iino H, Fujimura Y.
    • Journal Title

      Intern. Med.

      Volume: 52 Issue: 17 Pages: 1883-1891

    • DOI

      10.2169/internalmedicine.52.8253

    • NAID

      130003365801

    • ISSN
      0918-2918, 1349-7235
    • Language
      English
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] 抗CFH抗体陽性およびCFHR1遺伝子欠損を伴うDEAP-HUSの1例2013

    • Author(s)
      岡政史、大塚泰史、稲田由紀子、佐藤忠司、吉田瑶子、藤村吉博、Xinping Fan、宮田敏行、濱崎雄平
    • Journal Title

      日本小児腎臓病学会雑誌

      Volume: 26 Pages: 109-115

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25860685
  • [Journal Article] Drug-induced thrombotic thrombocytopenic purpura success- fully treated with recombinant human soluble thrombomodulin2013

    • Author(s)
      Nishijima Y, Hirata H, Himeno A, Kida H, Matsumoto M, Takahashi R, Otani Y, Inoue K, Nagatomo I, Takeda Y, Kijima T, Tachibana I, Fujimura Y, Kumanogoh A
    • Journal Title

      Inter Med

      Volume: 52 Pages: 1111-1114

    • NAID

      130003365599

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Long term follow up of congenital thrombotic thrombocytopenic purpura (Upshaw-Schulman syndorome) on hemodialysis for 19 years: a case report2013

    • Author(s)
      Mise K, Ubara Y, Matsumoto M, Sumida K, Hiramatsu R, Hasegawa E, Yamanouchi M, Hayami N, Suwabe T, Hoshino J, Sawa N, Ohashi K, Kokame K, Miyata T, Fujimura Y, Takaichi K.
    • Journal Title

      BMC Nephrol.

      Volume: 14 Issue: 1 Pages: 156-156

    • DOI

      10.1186/1471-2369-14-156

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-24390250, KAKENHI-PROJECT-25440060, KAKENHI-PROJECT-25461456
  • [Journal Article] Limited renal prophylaxis in regular plasmatherapy for heritable ADAMTS13 deficiency2013

    • Author(s)
      Doi T, Ohga S, Ito N, Ishimura M, Suga N, Nomura A, Takada H, Matsumoto M, Fujimura Y, Hara T
    • Journal Title

      Pediatric Blood & Cancer

      Volume: 印刷中

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Ticlopidine-associated ADAMTS13 activity deficient thrombotic thrombocytopenic purpura in 22 persons in Japan: a report from the Southern Network on Adverse Reactions (SONAR).2013

    • Author(s)
      Bennett CL, Jacob S, Dunn BL, et al. (Fujimura Y, last author)
    • Journal Title

      Br J Haematol.

      Volume: 印刷中

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] 非典型溶血性尿毒症症候群(aHUS)2013

    • Author(s)
      藤村吉博、吉田瑶子、範新萍、宮田敏行
    • Journal Title

      臨床血液

      Volume: 54 Pages: 351-360

    • NAID

      10031196335

    • Data Source
      KAKENHI-PROJECT-25860685
  • [Journal Article] ADAMTS13 unbound to larger von Willebrand factor multimers in cryosupernatant: Implications for selection of plasma preparations for TTP treatment2013

    • Author(s)
      Hori Y, Hayakawa M, Isonishi A, Soejima K, Matsumoto M, Fujimura Y
    • Journal Title

      Transfusion

      Volume: 印刷中

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] ADAMTS13 activity and genetic mutations in Japanese subjects.2013

    • Author(s)
      Toshiyuki Miyata, Koichi Kokame, Masanori Matsumoto, and Yoshihiro Fujimura.
    • Journal Title

      Haemostaselolgie

      Volume: 33 Issue: 02 Pages: 131-137

    • DOI

      10.5482/hamo-12-11-0017

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22570151, KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-24390250, KAKENHI-PROJECT-25440060
  • [Journal Article] The first bout of TTP triggered by herpes simplex infection in a 45-year-old nonparous female with Upshaw-Schulman syndrome2013

    • Author(s)
      Morioka M, Matsumoto M, Saito M, Kokame K, Miyata T, Fujimura Y.
    • Journal Title

      Blood Transfusion.

      Volume: 印刷中

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Ticlopidine-associated ADAMTS13 activity deficient thrombotic thrombocytopenic purpura in 22 persons in Japan: a report from the Southern Network on Adverse Reactions (SONAR).2013

    • Author(s)
      Bennett CL, Jacob S, Fujimura Y (last author).
    • Journal Title

      Br J Haematol.

      Volume: 161 Issue: 6 Pages: 896-898

    • DOI

      10.1111/bjh.12303

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Drug-induced Thrombotic Thrombocytopenic Purpura Successfully Treated with Recombinant Human Soluble Thrombomodulin2013

    • Author(s)
      Nishijima Y, Hirata H, Himeno A, Kida H, Matsumoto M, Takahashi R, Otani Y, Inoue K, Nagatomo I, Takeda Y, Kijima T, Tachibana I, Fujimura Y, Kumanogoh A.
    • Journal Title

      Intern. Med.

      Volume: 52 Issue: 10 Pages: 1111-1114

    • DOI

      10.2169/internalmedicine.52.9180

    • NAID

      130003365599

    • ISSN
      0918-2918, 1349-7235
    • Language
      English
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23591425
  • [Journal Article] ADAMTS13 activity and genetic mutations in Japanese subjects2013

    • Author(s)
      Miyata T, Kokame K, Matsumoto M, Fujimura Y.
    • Journal Title

      Hamostaseologie

      Volume: 印刷中

    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] 補体制御異常症関連HUSの診断2013

    • Author(s)
      吉田瑶子、藤村吉博
    • Journal Title

      腎と透析

      Volume: 74 Pages: 1103-1108

    • Data Source
      KAKENHI-PROJECT-25860685
  • [Journal Article] Hereditary thrombotic thrombocytopenic purpura (Upshaw-Schulman syndrome) and the hereditary TTP registry2013

    • Author(s)
      Mansouri M-T,von Krogh A-S, Fujimura Y, George JN, Hrachovinova I, Knӧbl PN, Quist-Paulsen P, Schneppenheim R, Lӓmmle B, Kremer-Hovinga JA
    • Journal Title

      Hamostaseologie

      Volume: 印刷中

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] ADAMTS13 activity and genetic mutations in Japanese subjects2013

    • Author(s)
      Miyata T, Kokame K, Matsumoto M, Fujimura Y
    • Journal Title

      Hamostaseologie (review)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Autopsy case of sudden maternal death from thrombotic thrombocytopenic purpura.2013

    • Author(s)
      Yamamoto T, Fujimura Y, Emoto Y, Kuriu Y, Iino M, Matoba R.
    • Journal Title

      J obset Gynaecol Res.

      Volume: 39 Issue: 1 Pages: 351-354

    • DOI

      10.1111/j.1447-0756.2012.01941.x

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Analysis of genetic and predisposing factors in Japanese patients with atypical hemolytic uremic syndrome.2013

    • Author(s)
      Fan X, Yoshida Y, Honda S, et al. (Matsumoto M 4番目)
    • Journal Title

      Mol Immunol.

      Volume: 54 Issue: 2 Pages: 238-246

    • DOI

      10.1016/j.molimm.2012.12.006

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-24390250, KAKENHI-PROJECT-25461456, KAKENHI-PROJECT-25860685
  • [Journal Article] Ratio of von Willebrand Factor Propeptide to ADAMTS13 Is Associated With Severity of Sepsis.2013

    • Author(s)
      Fukushima H, Nishio K, Asai H, Watanabe T, Seki T, Matsui H, Sugimoto M, Matsumoto M, Fujimura Y, Okuchi K.
    • Journal Title

      Shock.

      Volume: 39 Issue: 5 Pages: 409-414

    • DOI

      10.1097/shk.0b013e3182908ea7

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-24592744, KAKENHI-PROJECT-25461456
  • [Journal Article] Ticlopidine -associated ADAMTS13 activity deficient thrombotic thrombo- cytopenic purpura in 22 persons in Japan: A Report from the Southern Network on Adverse Reactions (SONAR)2013

    • Author(s)
      Bennett CL, Jacob S, Dunn BL, Georgantopoulos P, Zheng XL, Kwaan HC, McKoy JM, Magwood JS, Bandarenko N, Winters JL, Raife TJ, Carey PM, Sarode R, Kiss JE, Danielson C, Ortel TL, Clark WF, Ablin R, Rock G, Matsumoto M, Fujimura Y
    • Journal Title

      Br J Haematol

      Volume: (in press)

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Ratio of von Willebrand factor propeptide to ADAMTS13 Is Associated With Severity of Sepsis2013

    • Author(s)
      Fukushima H, Nishio K, Asai H, Watanabe T, Seki T, Matsui H, Sugimoto M, Matsumoto M, Fujimura Y, Okuchi K
    • Journal Title

      Shock

      Volume: 39 Pages: 409-414

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Therapeutic modality of 11 patients with TTP: Experience in a single institution in Miyazaki during 2000-20112013

    • Author(s)
      Kawano N, Yokota-Ikeda N, Sugio Y, Yoshida S, Ono N, Kuriyama T, Yamashita K, Makino S, Inoue Y, Himeji D, Kodama K, Uezono S, Shimao Y, Matsumoto M, Iino H, Fujimura Y
    • Journal Title

      Intern Med.

      Volume: 印刷中

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Hereditary thrombotic thrombocytopenic purpura and the hereditary TTP registry.2013

    • Author(s)
      Mansouri Taleghani M, von Krogh AS, Fujimura Y, George JN, Hrachovinová I, Knöbl PN, Quist-Paulsen P, Schneppenheim R, Lämmle B, Kremer Hovinga JA.
    • Journal Title

      Hamostaseologie.

      Volume: 33 Issue: 02 Pages: 138-143

    • DOI

      10.5482/hamo-13-04-0026

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Acquired idiopathic ADAMTS13 activity deficient thrombotic thrombocyt openic purpura in a population from Japan2012

    • Author(s)
      Matsumoto M, Bennett CL, Isonishi A, Qureshi Z, Hori Y, Hayakawa M, Yoshida Y, Yagi H, Fujimura Y
    • Journal Title

      PLoS ONE

      Volume: 7 Issue: 3 Pages: e33029-e33029

    • DOI

      10.1371/journal.pone.0033029

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23591425
  • [Journal Article] Paucity of CD34-positive cells and increased expression of high-mobility group box 1 in coronary thrombus with type 2 diabetes mellitus2012

    • Author(s)
      Yamashita A, Nishihira K, Matsuura Y, Ito T, Kawahara K, Hatakeyama K, Hashiguchi T, Maruyama I, Yagi H, Matsumoto M, Fujimura Y, Kitamura K, Shibata Y, Asada Y
    • Journal Title

      Atherosclerosis

      Volume: 224 Pages: 511-514

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Identification of epitopes on ADAMTS13 recognized by a panel of monoclonal antibodies with functional or non-functional effects on catalytic activity.2012

    • Author(s)
      Igari A, Nakagawa T, Moriki T, Yamaguchi Y, Matsumoto M, Fujimura Y, Soejima K, Murata M.
    • Journal Title

      Thromb Res.

      Volume: 130 Issue: 3 Pages: e79-e83

    • DOI

      10.1016/j.thromres.2012.06.006

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23591425
  • [Journal Article] Paucity of CD34-positive cells and increased expression of high-mobility group box 1 in coronary thrombus with type 2 diabetes mellitus.2012

    • Author(s)
      Yamashita A, Nishihira K, Matsuura Y, Ito T, Kawahara K, Hatakeyama K, Hashiguchi T, Maruyama I, Yagi H, Matsumoto M, Fujimura Y, Kitamura K, Shibata Y, Asada Y.
    • Journal Title

      Atherosclerosis.

      Volume: 224 Issue: 2 Pages: 511-514

    • DOI

      10.1016/j.atherosclerosis.2012.07.027

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23390412, KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-23790410, KAKENHI-PROJECT-24659804
  • [Journal Article] Reduced larger VWF multimers at dawn in OSA plasmas reflect severity of apneic episodes2012

    • Author(s)
      Koyama N, Matsumoto M, Tamaki S, Yoshikawa M, Fujimura Y, Kimura H
    • Journal Title

      Eur Resp J

      Volume: 40 Pages: 657-664

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] A typical HUS2012

    • Author(s)
      吉田瑶子、松本雅則、早川正樹、藤村吉博
    • Journal Title

      日本アフェレシス学会雑誌

      Volume: 31 Pages: 27-32

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Acquired idiopathic ADAMTS13 activity deficient thrombotic thrombo- cytopenic purpura in a population from Japan2012

    • Author(s)
      Matsumoto M, Bennett CL, Isonishi A, Qureshi Z, Hori Y, Hayakawa M, Yoshida Y, Yagi H, Fujimura Y
    • Journal Title

      PLoS One

      Volume: 7

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] 血栓性血小板減少性紫斑病(TTP)2012

    • Author(s)
      石西綾美、早川正樹、松本雅則、八木秀男、藤村吉博
    • Journal Title

      日本アフェレシス学会雑誌

      Volume: 31 Pages: 7-13

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Pediatric idiopathic TTP diagnosed with decreased ADAMTS13 activity.2012

    • Author(s)
      Morishima T, Nomura A, Saida S, Watanabe K, Yagi H, Matsumoto M, Fujimura Y, Heike T, Nakahata T, Adachi S.
    • Journal Title

      Pediatr Int.

      Volume: 54 Issue: 3 Pages: 422-423

    • DOI

      10.1111/j.1442-200x.2011.03467.x

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23591425
  • [Journal Article] The ADAMTS13 activity may predict the cumulative survival of patients with liver cirrhosis-in comparison with the Child-Turcotte-Pugh score and the MELD score2012

    • Author(s)
      Takaya H, Uemura M, Fujimura Y, Matsumoto M, Matsuyama T, Kato S, Morioka C, Ishizashi H, Hori Y, Fujimoto M, Tsujimoto T, Kawaratani H, Kurumatani N, FukuiH
    • Journal Title

      Hepatology research

      Volume: 42 Issue: 5 Pages: 459-459

    • DOI

      10.1111/j.1872-034x.2011.00950.x

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23590988, KAKENHI-PROJECT-23591425
  • [Journal Article] A novel Wiskott-Aldrich syndrome protein mutation in an infant with thrombotic thrombocytopenic purpura.2012

    • Author(s)
      Kawasaki Y, Toyoda H, Otsuki S, Iwasa T, Iwamoto S, Azuma E, Itoh-Habe N, Wada H, Fujimura Y, Morio T, Imai K, Mitsuiki N, Ohara O, Komada Y.
    • Journal Title

      Eur J Haematol.

      Volume: 90 Issue: 2 Pages: 164-168

    • DOI

      10.1111/ejh.12057

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390213, KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23390270, KAKENHI-PROJECT-23591425, KAKENHI-PROJECT-23591561
  • [Journal Article] Identification and recombinant analysis of botrocetin-2, a snake venom cofactor for von Willebrand factor-induced platelet agglutination2012

    • Author(s)
      Yamamoto-Suzuki Y, Sakurai Y, Fujimura Y, Matsumoto M, Hamako J, Kokubo T, Kitagawa H, Kawsar SMA, Fujii Y, Ozeki Y, Matsushita F, Matsui T
    • Journal Title

      Biochemistry

      Volume: 51 Issue: 26 Pages: 5329-5338

    • DOI

      10.1021/bi300442c

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22580226, KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23370077, KAKENHI-PROJECT-24657119
  • [Journal Article] Paradigm shift of childhood TTP with severe ADAMTS13 deficiency2012

    • Author(s)
      Yagi H, Matsumoto M, Fujimura Y
    • Journal Title

      Presse Med

      Volume: 41 Pages: 137-155

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Two newborn-onset patients of Upshaw-Schulman syndrome with distinct subsequent clinical courses2012

    • Author(s)
      Tanabe S, Yagi H, Kimura T, Isonishi A, Kato S, Yoshida Y, Hayakawa M, Matsumoto M, Ohtaki S, Takahashi Y, Fujimura Y
    • Journal Title

      Int J Hematol

      Volume: 96 Pages: 789-797

    • NAID

      10031144620

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Reduced larger VWF multimers at dawn in OSA plasmas reflect severity of apneic episodes2012

    • Author(s)
      Koyama N, Matsumoto M, Tamaki S, Yoshikawa M, Fujimura Y, Kimura H
    • Journal Title

      Eur Resp J

      Volume: (印刷中) Issue: 3 Pages: 657-664

    • DOI

      10.1183/09031936.00186210

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23591425
  • [Journal Article] 重症感染症における ADAMTS13 活性の低下2012

    • Author(s)
      加藤隆之、川嶋隆久、石井昇、 松本雅則、藤村吉博、安藤維洋、吉田剛
    • Journal Title

      日本救急医学会雑誌

      Volume: 23 Pages: 285-294

    • NAID

      130004840934

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] The homozygous p.C1024R- ADAMTS13 gene mutation links to a late-onset phenotype of Upshaw-Schulman syndrome in Japan2012

    • Author(s)
      Taguchi F, Yagi H, Matsumoto M, Sadamura S, Isonishi A, Soejima K, Fujimura Y
    • Journal Title

      Thromb Haemost

      Volume: 107 Pages: 1003-1005

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] 難治性血栓性血小板減少性紫斑病に対して血漿交換とリツキシマブの併用療法で救命し得た症例2012

    • Author(s)
      萱島道徳、岩下祐一、小西康司、浅井英樹、西尾健治、奥地一夫。石西綾美、松本雅則、藤村吉博
    • Journal Title

      日本急性血液浄化学会雑誌

      Volume: 3 Pages: 78-81

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Cilostazol down-regulates the height of mural platelet thrombi formed under a high-shear rate flow in the absence of ADAMTS13 activity2012

    • Author(s)
      Yagi H, Yamaguchi N, Shida Y, Hayakawa M, Matsumoto M, Sugimoto M, Wada H, Tsubaki K, Fujimura Y
    • Journal Title

      Eur J Pharm

      Volume: 691 Pages: 151-155

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] ADAMTS13 activity may predict the cumulative survival of patients with liver cirrhosis in comparison with the Child-Turcotte-Pugh score and the Model for End-Stage Liver Disease score2012

    • Author(s)
      Takaya H, Uemura M, Fujimura Y, Matsumoto M, Matsuyama T, Kato S, Morioka C, Ishizashi H, Hori Y, Fujimoto M, Tsujimoto T, Kawaratani H, Toyohara M, Kurumatani N, Fukui H
    • Journal Title

      Hepatol Res

      Volume: 42 Pages: 459-72

    • NAID

      10031144260

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Two newborn-onset patients of Upshaw-Schulman syndrome with distinct subsequent clinical courses2012

    • Author(s)
      Tanabe S, Yagi H, Kimura T, Isonishi A, Kato S, Yoshida Y, Hayakawa M, Matsumoto M, Ohtaki S, Takahashi Y, Fujimura Y.
    • Journal Title

      Int J Hematol.

      Volume: 96 Issue: 6 Pages: 789-797

    • DOI

      10.1007/s12185-012-1221-8

    • NAID

      10031144620

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Identification and Recombinant Analysis of Botrocetin-2, a Snake Venom Cofactor for von Willebrand Factor-Induced Platelet Agglutination2012

    • Author(s)
      Yamamoto-Suzuki Y, Sakurai Y, Fujimura Y, Matsumoto M, Hamako J, Kokubo T, Kitagawa H, Kawsar SM, Fujii Y, Ozeki Y, Matsushita F, Matsui T
    • Journal Title

      Biochemistry

      Volume: 51 Pages: 5329-5338

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] The homozygous p.C1024R-ADAMTS13 gene mutation links to a late-on set phenotype of Upshaw-Schulman syndrome in Japan2012

    • Author(s)
      Taguchi F, Yagi H, Matsumoto M, Sadamura S, Isonishi A, Soejima K, Fujimura Y
    • Journal Title

      Thromb Haemost

      Volume: (印刷中) Issue: 05 Pages: 1003-1005

    • DOI

      10.1160/th11-11-0799

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23591425
  • [Journal Article] 血液透析患者におけるヘパリン起因性血小板減少症(HIT)2012

    • Author(s)
      小西康司、岩下裕一、萱島道徳、米田龍生、吉田克法、石西綾美、松本雅則、藤村吉博
    • Journal Title

      日本アフェレシス学会雑誌

      Volume: 31 Pages: 53-57

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Ticlopidine-, clopidogrel-, and prasugrel-associated thrombotic thrombocytopenic purpura: a 20- year review from the Southern Network on Adverse Reactions (SONAR).2012

    • Author(s)
      Jacob S, Dunn BL, Qureshi ZP, et al. (Mastumoto M 20番目)
    • Journal Title

      Semin Thromb Hemost.

      Volume: 38 Issue: 08 Pages: 845-853

    • DOI

      10.1055/s-0032-1328894

    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23591425
  • [Journal Article] Cilostazol down-regulates the height of mural platelet thrombi formed under a high-shear rate flow in the absence of ADAMTS13 activity.2012

    • Author(s)
      Yagi H, Yamaguchi N, Shida Y, Hayakawa M, Matsumoto M, Sugimoto M, Wada H, Tsubaki K, Fujimura Y.
    • Journal Title

      Eur J Pharmacol.

      Volume: 691 Issue: 1-3 Pages: 151-155

    • DOI

      10.1016/j.ejphar.2012.07.001

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069, KAKENHI-PROJECT-23591425
  • [Journal Article] Identification and recombinant analysis of botrocetin-2, a snake venom cofactor for von Willebrand factor-induced platelet agglutination.2012

    • Author(s)
      Yamamoto-Suzuki Y, Sakurai Y, Fujimura Y, Matsumoto M, Hamako J, Kokubo T, Kitagawa H, Kawsar SM, Fujii Y, Ozeki Y, Matsushita F, Matsui T.
    • Journal Title

      Biochemistry.

      Volume: 51 Pages: 5329-5338

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Paradigm shift of childhood thrombotic thrombocytopenic purpura with severe ADAMTS13 deficiency.2012

    • Author(s)
      Yagi H, Matsumoto M, Fujimura Y.
    • Journal Title

      Presse Med.

      Volume: 41 Issue: 3 Pages: e137-e155

    • DOI

      10.1016/j.lpm.2011.10.027

    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Natural history of Upshaw-Schulman syndrome based on ADAMTS13 gene analysis in Japan2011

    • Author(s)
      Y.Fujimura, 他7名
    • Journal Title

      J Thromb Haemost

      Volume: 9(review) Pages: 283-301

    • DOI

      10.1111/j.1538-7836.2011.04341.x

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20390278, KAKENHI-PROJECT-22570151, KAKENHI-PROJECT-23591425
  • [Journal Article] Epitope analysis of autoantibodies to ADAMTS13 in patients with acquired thrombotic thrombocytopenic purpura2011

    • Author(s)
      Yamaguchi Y, Moriki T, Igari A, Nakagawa T, Wada H, Matsumoto M, Fujimura Y, Murata M
    • Journal Title

      Thromb Res

      Volume: 128 Pages: 169-73

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Determination of ADAMTS13 and Its Clinical Significance for ADAMTS13 Supplementation Therapy to Improve the Survival of Patients with Decompensated Liver Cirrhosis2011

    • Author(s)
      Uemura M, Fujimura Y, Ko S, Matsumoto M, Nakajima Y, Fukui H
    • Journal Title

      Int J Hepatol

      Volume: 759047

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Determination of ADAMTS13 and its clinical significance for ADAMTS13 supplementation therapy to improve the survival of patients with decompensated liver cirrhosis2011

    • Author(s)
      Uemura M, Fujimura Y, Ko S, et al.
    • Journal Title

      Int J Hepatol

      Volume: Epub 2011 Jul 18. Pages: 1-12

    • DOI

      10.4061/2011/759047

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23590988, KAKENHI-PROJECT-23591425
  • [Journal Article] H1N1 Influenza (Swine Flu)-Associated Thrombotic Microangiopathy with a Markedly High Plasma Ratio of von Willebrand Factor to ADAMTS132011

    • Author(s)
      Akiyama R, Komori I, Hiramoto R, Isonishi A, Matsumoto M, Fujimura Y.
    • Journal Title

      Intern. Med.

      Volume: 50 Issue: 6 Pages: 643-647

    • DOI

      10.2169/internalmedicine.50.4620

    • NAID

      130000649901

    • ISSN
      0918-2918, 1349-7235
    • Language
      English
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] Determination of ADAMTS13 and its clinical significance for ADAMTS13 suppl ementation therapy to improve the survival of patients with decompensated liver cirrhosis2011

    • Author(s)
      Uemura M, Fujimura Y, Ko S, Matsumoto M, Nakajima Y, Fukui H
    • Journal Title

      International Journal of Hepatology

      Volume: (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] Determination of ADAMTS13 and Its Clinical Significance for ADAMTS13 Supplementation Therapy to Improve the Survival of Patients with Decompensated Liver Cirrhosis2011

    • Author(s)
      Uemura M, Fujimura Y, Ko S, Matsumoto M, Nakajima Y, et al.
    • Journal Title

      Internatinal Journal of Hepatology

      Volume: 759047 Pages: 1-12

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591759
  • [Journal Article] Natural history of Upshaw-Schulman syndrome based on ADAMTS13 gene analysis in Japan2011

    • Author(s)
      Fujimura Y, Matsumoto M, Isonishi A, Yagi H, Kokame K, Soejima K, Murata M, Miyata T
    • Journal Title

      J Thromb Haemost

      Volume: 9 Supp l 1 Pages: 283-301

    • NAID

      120006669559

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Determination of ADAMTS13 and its clinical significance for ADAMTS13 supplementation therapy to improve the survival of patients with decompensated liver cirrhosis.2011

    • Author(s)
      Uemura M, Fujimura Y, Ko S, et al.
    • Journal Title

      Int J Hepatol. in press

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] Epitope analysis of autoantibodies to ADAMTS13 in patients with acquired thrombotic thrombocytopenic purpura.2011

    • Author(s)
      Yamaguchi Y, Moriki T, Igari A, Nakagawa T, Wada H, Matsumoto M, Fujimura Y, Murata M.
    • Journal Title

      Thromb Res.

      Volume: 128 Issue: 2 Pages: 169-173

    • DOI

      10.1016/j.thromres.2011.03.010

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Journal Article] 症急性膵炎における ADAMTS13 活性の動態とその臨床的意義2011

    • Author(s)
      森岡千恵,植村正人、高谷正章、松本雅則、藤村吉博、福井博
    • Journal Title

      消化器内科

      Volume: 52 Pages: 200-208

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] 『Annual Review消化器』2011.2011

    • Author(s)
      植村正人、藤村吉博、福井博
    • Journal Title

      急性膵炎重症化と血漿ADAMTS13活性(林紀夫,日比紀文、上西紀夫、下瀬川徹偏)(中外医学社)

      Pages: 237-244

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] H1N1 influenza (swine flu)-associated thrombotic microangiopathy with a gigantically high plasma ratio of von Willebrand factor to ADAMTS132011

    • Author(s)
      Akiyama R, Komori I, Hiramoto R, Isonishi A, Matsumoto M, Fujimura Y
    • Journal Title

      Intern Med

      Volume: 50 Pages: 643-647

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] ADAMTS132011

    • Author(s)
      松本雅則, 藤村吉博
    • Journal Title

      分子脳血管病

      Volume: 10 Pages: 74-77

    • NAID

      10029767493

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] 血栓性微小血管障害性(TMA)の診断と治療戦略2011

    • Author(s)
      藤村吉博、吉田瑶子、石西綾美、堀勇二、早川正樹、八木秀男、松本雅則
    • Journal Title

      血液フロンティア

      Volume: 21 Pages: 43-59

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] 溶血性尿毒症症候群、血栓性血小板減少性紫斑病2011

    • Author(s)
      藤村吉博、松本雅則、八木秀男
    • Journal Title

      日本内科学会雑誌

      Volume: 5 Pages: 1296-1307

    • NAID

      10029097169

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] 血栓性微小血管障害症(TMA)と妊娠 -その診断と治療-2011

    • Author(s)
      藤村吉博、八木秀男、石西綾美、山口直子、早川正樹、松本雅則、佐道俊幸
    • Journal Title

      日本産婦人科・新生児血液学雑誌

      Volume: 20 Pages: 83-92

    • NAID

      10029377850

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Potential Role of Enhanced Cytokinemia and Plasma Inhibitor on the Decreased Activity of Plasma ADAMTS13 in Patients With Alcoholic Hepatitis : Relationship to Endotoxemia2010

    • Author(s)
      Ishikawa M, Uemura M, Matsuyama T, Matsumoto M, Fujimura Y, et al.
    • Journal Title

      Alcohol Clin Exp Res

      Volume: 34

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591759
  • [Journal Article] Pivotal role of ADAMTS13 function in liver diseases2010

    • Author(s)
      Uemura M, Fujimura Y, Ko S, et al
    • Journal Title

      Int J Hematol 91

      Pages: 20-29

    • NAID

      10026110380

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591759
  • [Journal Article] Registry of 919 patients with thrombotic microangiopathies across Japan : Database of Nara Medical University during 1998-20082010

    • Author(s)
      Fujimura Y, Matsumoto M.
    • Journal Title

      Inter Med

      Volume: 49 Pages: 7-15

    • NAID

      130000142252

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591759
  • [Journal Article] Influenza A infection triggers thrombotic thrombocytopenic purpura by producing the anti-ADAMTS 13 IgG inhibitor.2010

    • Author(s)
      Kosugi N, Tsurutani Y, Isonishi A, Hon Y, Matsumoto M, Fujimura Y
    • Journal Title

      Inter Med 49

      Pages: 689-693

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] ADAMTS13活性測定用 ELISA キットの開発2010

    • Author(s)
      伊藤晋,山本茂一,林司,加藤誠司,日裏久英, 松本雅則, 藤村吉博
    • Journal Title

      日輸細治会誌

      Volume: 56 Pages: 27-35

    • NAID

      10027584258

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Pivotal role of ADAMTS13 function in liver diseases.2010

    • Author(s)
      Uemura M, Fujimura Y, Ko S, et al.
    • Journal Title

      Int J Hematol. 91

      Pages: 20-29

    • NAID

      10026110380

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] 奈良県立医科大学透析部におけるヘパリン起因性血小板減少症(HIT)症例の検討2010

    • Author(s)
      小西康司,吉田克法,多山幸,切畑屋智史,岩下裕一,横田基次,萱島道徳,米田龍生,石西綾美, 松本雅則, 藤村吉博
    • Journal Title

      奈透析会誌

      Volume: 15 Pages: 59-63

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] 重症急性膵炎におけるADAMTS13活性の動態とその臨床的意義2010

    • Author(s)
      森岡千恵、植村正人、高谷広章、松本雅則、藤村吉博、福井博
    • Journal Title

      消化器内科

      Volume: 52 Pages: 200-208

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] Registry of 919 patients with thrombotic microangiopathies across Japan : Database of Nara Medical University during 1998-2008.2010

    • Author(s)
      Fujimura Y, Matsumoto M.
    • Journal Title

      Inter Med

      Volume: 49 Pages: 7-15

    • NAID

      130000142252

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] 胎児治療を行った重症 RhE 不適合妊娠による新生児溶血性疾患の 1例2010

    • Author(s)
      武山雅博,藤田百合,内田賀子,柴田真里,釜本智之,新居育世,井崎和史,西久保敏也,佐道俊幸,赤坂珠理晃,小林浩,西田幸世,松本雅則,藤村吉博,高橋幸博
    • Journal Title

      日本産婦人科・新生児血液学会誌

      Volume: 19 Pages: 51-55

    • NAID

      10026710419

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Influenza A infection triggers thrombotic thrombocytopenic purpura by producing the anti-ADAMTS13 IgG inhibitor2010

    • Author(s)
      Kosugi N, Tsurutani Y, Isonishi A, Hori Y, Matsumoto M, Fujimura Y.
    • Journal Title

      Inter Med

      Volume: 49 Pages: 689-693

    • NAID

      130000251788

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] A 9-month-old infant with acquired idiopathic thrombotic thrombo- cyto penic purpura caused by inhibitory IgG-autoantibody to ADAMTS13.2010

    • Author(s)
      Sato A, Hoshi Y, Onuma M, Sato R Tsunematsu Y, Isonishi A, Mats umoto M, Fujimura Y, Imaizumi M.
    • Journal Title

      Pediatr Hematol Oncol.

      Volume: 27 Pages: 53-58

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Pivotal role of ADAMTS13 function in liver diseases2010

    • Author(s)
      Uemura M, Fujimura Y, Ko S, Matsumoto M, Nakajima Y, et al.
    • Journal Title

      Int J Hematol

      Volume: 91 Pages: 20-29

    • NAID

      10026110380

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591759
  • [Journal Article] Pivotal role of ADAMTS13 function in liver diseases2010

    • Author(s)
      Uemura M, Fujimura Y, Ko S, Matsumoto M, Nakajima Y, Fukui H
    • Journal Title

      Int J Hematol

      Volume: 91 Pages: 20-29

    • NAID

      10026110380

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Pivotal role of ADAMTS13 function in liver diseases2010

    • Author(s)
      Uemura M, Fujimura Y, Ko S, Matsumoto M, Nkajima Y, Fuku H
    • Journal Title

      International Journal of Hematology

      Volume: 91 Pages: 20-29

    • NAID

      10026110380

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] ADAMTS13 activity decreases after hepatectomy, reflecting a postoperative liver function2010

    • Author(s)
      Okano E, Ko S, Matsumoto M, Fujimura Y, Nakajima Y, et al.
    • Journal Title

      Hepato-Gastroenterology

      Volume: 57 Pages: 316-20

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591759
  • [Journal Article] Pivotal role of ADAMTS13 function in liver diseases.2010

    • Author(s)
      Uemura M, Fujimura Y, Ko S, Matsumoto M, et al
    • Journal Title

      Int J Hematol. 91(1)(Review)

      Pages: 20-29

    • NAID

      10026110380

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20500623
  • [Journal Article] Registry of 919 patients with thrombotic microangiopathies across Japan: Database of Nara Medical University during 1998-2008.2010

    • Author(s)
      Fujimura Y. Matsumoto M.
    • Journal Title

      Inter Med 49

      Pages: 7-15

    • NAID

      130000142252

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Registry of 919 patients with thrombotic microangiopathies across Japan: Database of Nara Medical University during 1998-20082010

    • Author(s)
      Fujimura Y, Matsumoto M.
    • Journal Title

      Inter Med

      Volume: 49 Pages: 7-15

    • NAID

      130000142252

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Pivotal role of ADAMTS13 function in liver diseases2010

    • Author(s)
      Uemura M, Fujimura Y, Ko S, Matsumoto M, Nkajima Y, Fukui H
    • Journal Title

      Int J Hernatol 91

      Pages: 20-29

    • NAID

      10026110380

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] H1N1 influenza (swine flu)- associated thrombotic micro- angiopathy with a gigantically high plasma ratio of von Willebrand factor to ADAMTS 13.2010

    • Author(s)
      Akiyama R, Komori I, Hiramoto R, Isonishi A, Matsumoto M, Fujimura Y.
    • Journal Title

      Intern Med

      Volume: 50 Pages: 643-647

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] A second national questionnaire survey of TMA2010

    • Author(s)
      Ito-Habe N, Wada H, Matsumoto M, Fujimura Y, Murata M, Izuno T, Sugita M, Ikeda Y
    • Journal Title

      Int J Hematol

      Volume: 92 Pages: 68-75

    • NAID

      10026512028

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] A 9-month-old infant with acquired idiopathic thrombotic thrombocytopenic purpura caused by inhibitory IgG-autoantibody to ADAMTS 13.2010

    • Author(s)
      Sato A, Hoshi Y, Onuma M, Sato R, Tsunematsu Y, Isonishi A, Matsumoto M, Fujimura Y, Imaizumi M.
    • Journal Title

      Pediatr Hematol Oncol 27

      Pages: 53-58

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Registry of 919 patients with thrombotic microangiopathies across Japan : Database of Nara Medical University during 1998-20082010

    • Author(s)
      Fujimura Y, Matsumoto M
    • Journal Title

      Inter Medicine 49

      Pages: 7-15

    • NAID

      130000142252

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Influenza A infection triggers thrombotic thrombocytopenic purpura by producing the anti-ADAMTS13 IgG inhibitor.2010

    • Author(s)
      Kosugi N, Tsurutani Y, Isonishi A, Hori Y, Matsumoto M, Fujimura Y.
    • Journal Title

      Inter Med

      Volume: 49 Pages: 689-693

    • NAID

      130000251788

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Potential Role of Enhanced Cytokinemia and Plasma Inhibitor on the Decreased Activity of Plasma ADAMTS13 in Patients With Alcoholic Hepatitis : Relationship to Endotoxemia2010

    • Author(s)
      Ishikawa M, Matsumoto M, Fujimura Y, 他10名
    • Journal Title

      Alcohol Clin Exp Res 34

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] ADAMTS13 activity decreases after hepatectomy, reflecting a postoperative liver function.2010

    • Author(s)
      Okano E, Ko S, Matsumoto M, Fujimura Y, Nakajima Y.
    • Journal Title

      Hepato-Gastroenterology

      Volume: 57 Pages: 316-320

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Proteolytic fragmentation and sugar chains of plasma ADAMTS13 purified by a conformation-dependent monoclonal antibody2010

    • Author(s)
      Hiura H, Matsui T, Matsumoto M, Hori Y, Isonishi A, Kato S, Iwamoto T, Mori T, Fujimura Y
    • Journal Title

      J Biochem

      Volume: 148 Pages: 403-411

    • NAID

      10027878689

    • Data Source
      KAKENHI-PROJECT-22591069
  • [Journal Article] Heterogeneous pathogenic processes of thrombotic microangiopathies in patients with connective tissue diseases.2009

    • Author(s)
      Matsuyama T, Kuwana M, Matsumoto M, Isonishi A, Inokuma S, Fujimura Y
    • Journal Title

      Thromb Haemost 102

      Pages: 371-378

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Decreased ADAMTS13 levels in patients after living donor liver transplantation2009

    • Author(s)
      Kobayashi T, Matsumoto M, Fujimura Y, et al
    • Journal Title

      Thromb Res 124

      Pages: 541-545

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591759
  • [Journal Article] Pregnancy-induced thrombocytopenia and thrombotic microangiopathy in Upshaw-Schulman syndrome : Clinical observations and ADAMT S13 gene analysis in nine patients representing six families2009

    • Author(s)
      Fujimura Y, Matsumoto M, 他18名
    • Journal Title

      Br J Haematol 144

      Pages: 742-754

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] 動脈血栓症の制圧:VWF-GPIb軸依存性血小板血栓形成を調節するADAMTS13の基礎・臨床的解析2009

    • Author(s)
      藤村吉博、松本雅則、植村正人, 他
    • Journal Title

      日本医師会雑誌 137

      Pages: 2519-2521

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] National Questionnaire Survey of TMA.2009

    • Author(s)
      Ito N, Wada H, Matsumoto M, Fujimura Y, Murata M, Izuno 1, Sugita M, Ikeda Y
    • Journal Title

      Int J Hematol 90

      Pages: 328-335

    • NAID

      10026108869

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] 動脈血栓症の制圧-VWF-GPlb軸依存性血小板血栓形成を調節するADAMTS13の基礎・臨床病態解析-2009

    • Author(s)
      藤村吉博, ほか
    • Journal Title

      最新医学 64

      Pages: 290-321

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18591522
  • [Journal Article] 動脈血栓症の制圧:VWF-GPIb軸依存性血小板血栓形成を調節するADAMTS13の基礎・臨床的解析2009

    • Author(s)
      藤村吉博, 松本雅則, 植村正人, 他
    • Journal Title

      日本医師会雑誌 137

      Pages: 2519-2521

    • Data Source
      KAKENHI-PROJECT-20500623
  • [Journal Article] Human Placental Ectonucleoside Triphosphate Diphosphohydrolase Gene Transfer via Gelatin-Coated Stents Prevents In-Stent Thrombosis.2009

    • Author(s)
      Takemoto Y, Kawata H, Soeda T, Imagawa K, Somekawa S, Takeda Y, Uemura S, Matsumoto M, Fujimura Y, Jo JI, Kimura Y, Tabata Y, Saito Y
    • Journal Title

      Arterioscier Thromb Vase Biol 29

      Pages: 857-862

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] ほか.動脈血栓症の制圧-VWF-GP1b軸依存性血小板血栓形成を調節するADAMTS13の基礎・臨床病態解析 (第45回2008年度ベルツ賞論文)2009

    • Author(s)
      藤村吉博
    • Journal Title

      最新医学 6

      Pages: 290-321

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18591522
  • [Journal Article] Increased production of ADAMTS13 in hepatic stellate cells contributes to enhanced plasma ADAMTS13 activity in rat models of cholestasis and steatohepatitis2009

    • Author(s)
      Watanabe N, Matsumoto M, Fujimura Y, 他12名
    • Journal Title

      Thromb Haemost 102

      Pages: 389-396

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Decreased ADAMTSI3 levels in patients with living donor liver transplantation.2009

    • Author(s)
      Kobayashi T, Wada H, Usui M, Sakurai H, Matsumoto T, Nobori T, Katayama N, Uemoto S, Ishizashi H, Matsumoto M, Fujimura Y, lsaji S
    • Journal Title

      Thromb Res 124

      Pages: 541-545

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Pregnancy-induced thrombocytopenia and thrombotic microangiopathy in Upshaw-Schulman syndrome: Clinical observations and ADAMTS13 gene analysis in nine patients representing six families.2009

    • Author(s)
      Fujimura Y, Matsumoto M, Kokame K, Isonishi A, Soejima K, Akiyama N, Tomiyama J, Kazuhiko Natori K, Kuranishi Y, Imamura Y, Inoue N, Higasa S, Seike M, Kozuka T, Hara M, Wada H, Murata M, Ikeda Y, Miyata T, George JN
    • Journal Title

      Br J Haematol 144

      Pages: 742-754

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] 動脈血栓症の制圧 : VWF-GPIb軸依存性血小板血栓形成を調節するADAMTS13の基礎・臨床的解析2009

    • Author(s)
      藤村吉博, 松本雅則, 植村正人, 他
    • Journal Title

      日本医師会雑誌 137

      Pages: 2519-2521

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] 重症肝・膵疾患における多臓器不全の病態解析―ADAMTS13を中心に―日本消化器病学会2009

    • Author(s)
      植村正人, 藤村吉博, 福井博
    • Journal Title

      消化器病学の進歩―原点から未来への情報発信―第94回日本消化器病学会総会記録誌III. 複合領域

      Pages: 262-266

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] The significance of ADAMTSI3 in a patient with thrombotic thrombocytopenic purpura complicated autoimmune hepatitis.2009

    • Author(s)
      Shimizu M, Nomura S, Ishii K, Mohri Y, Umei N, Suzuki S, Matsuo Y, Isonishi A, Matsumoto M, Urase F, Maeda Y, Fujimura Y
    • Journal Title

      Thromb Haemost 101

      Pages: 599-600

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] 動脈血栓症の制圧:VWF-GPIb軸依存性血小板血栓形成を調節するADAMTS13の基礎・臨床的解析2009

    • Author(s)
      藤村吉博, 松本雅則, 植村正人, 他
    • Journal Title

      日本医師会雑誌 137

      Pages: 2519-2521

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] Comprehensive analysis of ADAMTS13 in patients with liver cirrhosis.2008

    • Author(s)
      Uemura M, Fujimura Y Ishizashi H, (他11名)
    • Journal Title

      Thromb Haemost. 99(6)

      Pages: 1019-29

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20500623
  • [Journal Article] Potential role of ASDAMTS13 in the progression of alcoholic hepatitis.2008

    • Author(s)
      植村正人, 藤村吉博, 松山友美, et al.
    • Journal Title

      Current Drug Abuse Reviews

      Pages: 188-196

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] Chemotherapy-resistant intravascular lymphoma accompanied by ADAMTS13 inhibitor successfully treated with rituximab.2008

    • Author(s)
      Kanno M, Nakamura S, Kawahara M, Ueno S, Nakamine H, Matsumoto M, Fujimura Y
    • Journal Title

      Int J Hematol 88

      Pages: 345-347

    • NAID

      10023970544

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Comprehensive analysis of ADAMTS13 in patients with liver cirrhosis.2008

    • Author(s)
      植村正人, 藤村吉博, 松本雅則, et al.
    • Journal Title

      Thromb Haemost. 99

      Pages: 1019-1029

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] Acute Myocardial Infarction as a Systemic Prothrombotic Condition Evidenced by Increased von Willebrand Factor Protein Over ADAMTS13 Activity in Coronary and Systemic Circulation.2008

    • Author(s)
      Horii M, Uemura S, Uemura M, Matsumoto M, Ishizashi H, Imagawa K, Iwama H, Takeda Y, Kawata H, Nakajima T, Fujimura Y, Saito Y
    • Journal Title

      Heart and Vessels 23

      Pages: 301-307

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Comprehensive analysis of ADAMTS13 in patients with liver cirrhosis.2008

    • Author(s)
      Uemura M, Fujimura Y, Matsumoto M, Ishizashi H, et al
    • Journal Title

      Thromb Haemost. 99(6)

      Pages: 1019-1029

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20500623
  • [Journal Article] Ecto-nucleotide triphosphate diphosphohydrolase inhibits ATP-and ADP-induced vasocontriction.2008

    • Author(s)
      Furukoji E, Tanaka N, Yamashita A, Matsumoto M, Fujimura Y, Yamamoto R, Tamura S, Asada Y
    • Journal Title

      Thromb Res 121

      Pages: 583-585

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Comprehensive analysis of ADAMTS13 in patients with liver cirrhosis (査読あり)2008

    • Author(s)
      Uemura M, Fujimura Y, Matsumoto M, Ishizashi H, Kato S, Matsuyama T, Isonishi A, Ishikawa M, Yagita M, Morioka C, Yoshiji H, Tsujimoto T, Kurumatani N, Fukui H
    • Journal Title

      Thrombosis and Haemostasis (掲載確定)

    • Data Source
      KAKENHI-PROJECT-17590670
  • [Journal Article] Potential Role of ADAMTS13 in the Development of Alcoholic Hepatitis(査読あり)2008

    • Author(s)
      Uemura M, Fujimura Y, Matsuyama T, Matsumoto M, Ishikawa M, Ishizashi H, Tsujimoto T, Yoshiji H, Fukui H.
    • Journal Title

      Current Drug Abuse Reviews 1(掲載確定)

    • Data Source
      KAKENHI-PROJECT-17590670
  • [Journal Article] Inherited and de novo mutations of ADAMTS13 in a patient with Upahaw-Schulman syndrome.2008

    • Author(s)
      Kokame K, Aoyama Y, Matsumoto M, Fujimura Y, Miyata T
    • Journal Title

      J Thromb Haemost 6

      Pages: 213-215

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Plasma ADAMTS13 activity parallels the APACHE II score, reflecting an early prognostic indicator for patients with severe acute pancreatitis(査読あり)2008

    • Author(s)
      Morioka C, Uemura M, Matsuyama T, Mastumoto M, Kato S, Ishikawa M, Ishizashi H, Fujimoto M, Sawai m, Yoshida M, Mitoro A, Yamao J, Tsujimoto T, Yoshiji H, Urizono Y, Hata M, Nishio K, Okuchi K, Fujimura Y, Fukui H.
    • Journal Title

      Scan J Gastroenterol (掲載確定)

    • Data Source
      KAKENHI-PROJECT-17590670
  • [Journal Article] Comprehensive analysis of ADAMTS13 in patients with liver cirrhosis.2008

    • Author(s)
      Uemura M, Fujimura Y, Matsumoto M, et al.
    • Journal Title

      Thromb Haemost. 99

      Pages: 1019-1029

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] 動脈血栓症の制圧へ:VWF-GPIb軸/ADAMTS13依存性血小板血栓症の分子メカニズムの解明と制御 第45回2008年度ベルツ賞受賞論文2008

    • Author(s)
      藤村吉博、松本雅則、植村正人、他
    • Journal Title

      最新医学 64

      Pages: 132-163

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] 単純血漿交換・二重膜濾過血漿交換・血漿吸着-血液疾患2008

    • Author(s)
      植村正人, 藤村吉博
    • Journal Title

      血液浄化療法の臨床2009(東京医学社)TTP 88

      Pages: 421-427

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] Comprehensive analysis of ADAMTS13 in patients with liver cirrhosis2008

    • Author(s)
      Uemura M, Fujimura Y, Matsumoto M, Ishizashi H, Kato S, et al.
    • Journal Title

      Thrombosis and Haemostasis 6(掲載確定)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17590670
  • [Journal Article] 第45回 2008年度 ベルツ賞受賞論文動脈血栓症の制圧へ : VWF-GPIb軸/ADAMTS13依存性血小板血栓症の分子メカニズムの解明と制御2008

    • Author(s)
      藤村吉博, 松本雅則, 植村正人, 杉本充彦, 小亀浩市, 宮田敏行
    • Journal Title

      最新医学 64

      Pages: 132-163

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] Potential role of ASDAMTS13 in the progression of alcoholic hepatitis.2008

    • Author(s)
      Uemura M, Fujimura Y, Matsuyama T, et al.
    • Journal Title

      Current Drug Abuse Reviews 1

      Pages: 188-196

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20590794
  • [Journal Article] Potential role of ADAMTS13 in the progression of alcoholic hepatitis2008

    • Author(s)
      Uemura M, Fujimura Y, Matsuyama T, Matsumoto M, Ishikawa M, Ishizashi H, et al
    • Journal Title

      Curr Drug Abuse Rev. 1(2)(Review)

      Pages: 188-196

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20500623
  • [Journal Article] Comprehensive analysis of ADAMTS13 in patients with liver cirrhosis.2008

    • Author(s)
      Uemura M, Fujimura Y, Matsumoto M, Ishizashi H, Kato S, Matsuyama T, Isonishi A, Ishikawa M, Yagita M, Morioka C, Yoshiji H, Tsujimoto T, Kurumatani N, Fukui H
    • Journal Title

      Thromb Haemost 99

      Pages: 1019-1029

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Plasma ADAMTS 13 activity parallels the APACHE II score, reflecting an early prognostic indicator for patients with severe acute pancreatitis.2008

    • Author(s)
      Morioka C, Uemura M, Matsuyama T, Matsumoto M, Kato S, Ishikawa M,. Ishizashi H, Fujimoto M, Sawai M, Yoshida M, Mitoro A, Yamao J, Tsujimoto T, Yoshiji H, Urizono Y, Hata M, Nishio K, Okuchi K, Fujimura Y, Fukui H
    • Journal Title

      Scand J Gastroenterol 43

      Pages: 1387-1396

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Functional imaging of shear-dependent activity of ADAMTS 13 in regulating mural thrombis growth under whole blood flow conditions.2008

    • Author(s)
      Shida S, Nishio K, Sugimoto M, Mizuno T, Hamada M, Kato S, Matsumoto M, Okuchi K, Fujimura Y, Yoshioka A
    • Journal Title

      Blood 111

      Pages: 1295-1298

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Acute Myocardial Infarction as a Systemic Prothrombotic Condition EVidenced by Increased von Willebrand Factor Protein Over ADAMTS13 Activity in Coronary and Systemic Circulation(査読あり)2008

    • Author(s)
      Horii M, Uemura S, Uemura M, Matsumoto m, Ishizashi H, Imagawa K, Iwama H, Takeda Y, Kawata H, Nakajima T, Fujimura y, Saito Y.
    • Journal Title

      Heart and Vessels (掲載確定)

    • Data Source
      KAKENHI-PROJECT-17590670
  • [Journal Article] Prophylactic fresh frozen plasma infusion may prevent the development of hepatic VOD after von Willebrand factor plasma levels.(査読あり)2007

    • Author(s)
      MatSumoto M, Kawa K, Uemura M, Kato S, Ishizashi H, Isonshi A, Yagi H, Park YD, Takeshima Y, Kosaka Y, Hara H, Kai S, Kanamnru A, Fukuhara S, Hino M, Sako M, Hiraoka A. Ogawa H, Hara J, Fujimura Y.
    • Journal Title

      Bone Marrow Transplant 40

      Pages: 51-59

    • Data Source
      KAKENHI-PROJECT-17590670
  • [Journal Article] Two mechanistic pathways for thienopyridine-associated thrombotic thrombocytopenic purpura: A report from the Surveillance, Epidemiology, and Risk Factors for Thrombotic Thrombocytopenic Purpura (SERF-TTP) Research Group.(査読あり)2007

    • Author(s)
      Bennett CL, Kim B, Zakaeijia A, Bandarenko N, Oandey Dk, Buffie CG, Mckoy JM, Tevar AD, Cursio JF, Yamold PR, Kwaan HC, DeMasi D, Sarode R, Raife TJ, Kiss JE, Raisch DW, Davidson C, Sadler JE, Ortel TL, Zheng XL, Kato S, Matsumoto M, Uemura M, Fujimura Y
    • Journal Title

      J Am Coll Cardiol 50

      Pages: 1138-1143

    • Data Source
      KAKENHI-PROJECT-17590670
  • [Journal Article] 健常人における中等量エタノール摂取後の血漿ADAMTS13活性の動態-ALDH2の遺伝子多型による差異(査読なし)2007

    • Author(s)
      松山 友美、植村 正人、加藤 誠司、石川 昌利、松本 雅則、石指 宏通、森岡 千恵、藤本 正男、辻本 達寛、北澤 利行、吉治 仁志、児山 紀子、藤村 吉博、福井 博
    • Journal Title

      アルコールと医学生物学 27

      Pages: 108-113

    • Data Source
      KAKENHI-PROJECT-17590670
  • [Journal Article] Quantitative western blot analysis of plasma ADAMTS13 antigen in patients with Upshaw-Schulman syndrome.2007

    • Author(s)
      Ishizashi H, Yagi H, Matsumoto M, Soejima K, Nakagaki T, Fujimura Y.
    • Journal Title

      Thromb Res 120

      Pages: 381-386

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16590796
  • [Journal Article] Intravenous gamma globulin for thrombotic microangiopathy of unknown etiology.2007

    • Author(s)
      Ito S, Okuyama K, Nakamura T, Tetanishi JI, Saito K, Matsumoto M, Fujimura Y, Aihara Y, Yokota S
    • Journal Title

      Pediatr Nephrol 22

      Pages: 301-305

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Increased von Willebrand factor over decreased ADAMTS 13 activity may contribute to the development of liver disturbance and multiorgan failure in patients with alcoholic hepatitis2007

    • Author(s)
      Matsuyama T, Uemura M, Ishikawa M, Matsumoto M, Ishizashi H, Kato S, Morioka C, Fujimoto M, Kojima H, Yoshiji H, Fujimura Y, Fukui H
    • Journal Title

      Alcohol Clin Exp Res 31

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Quantitative western blot analysis of plasma ADA MTS13 antigen in patients with Upshaw-Schulman syndrome.2007

    • Author(s)
      Ishizashi H, Yagi H, Matsumoto M, Soejima K, N akagaki T, Fujimura Y.
    • Journal Title

      Thrombosis Research. 120(3)

      Pages: 381-6

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17500439
  • [Journal Article] Plasma levels of ADAMTSI3 antigen, determined by an enzyme immunoassay using the neutralizing monoclonal antibody, parallel to those of the activity.2007

    • Author(s)
      Yagi H, Ito S, Kato S, Hiura H, Matsumoto M, Fujimura M
    • Journal Title

      Int Hematol 85

      Pages: 403-407

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Decreased ADAMTS13 activity in plasma from patients with thrombotic thrombocytopenic purpura.2007

    • Author(s)
      Kobayashi T, Wada H, Kamikura Y, Matsumoto T, Mori Y, Kaneko T, Nobori T, Matsumoto M, Fujimura Y, Shiku H
    • Journal Title

      Thromb Res 119

      Pages: 447-452

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Prophylactic fresh frozen plasma infusion may prevent the development of hepatic VOD after stem cell transplantation via ADAMTS 13-mediated restoration of von Willebrand factor plasma levels.2007

    • Author(s)
      Matsumoto M, Kawa K, Uemura M, Kato S, Ishizashi H, Isonishi A, Yagi H, Park YD, Takeshima Y, Kosaka Y, Hara H, Kai S, Kanamaru A, Fukuhara S, Hino M, Sako M, Hiraoka A, Ogawa H, Ham J, Fujimura Y
    • Journal Title

      Bone Marrow Transplant 40

      Pages: 251-259

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Successful Treatment of Primitive Neuroectodermal Tumor-associated Microangiopathy with Multiple Bone Metastases.2007

    • Author(s)
      Morishita T, Matsumoto M, Honoki K, Yoshida A, Takakura Y, Fujimura Y
    • Journal Title

      Jap J Cli One 37

      Pages: 66-69

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Two mechanistic pathways for thienopyridine-associated thrombotic thrombocytopenic purpura: A report from the Surveillance, Epidemiology, and Risk Factors for Thrombotic Thrombocytopenic Purpura (SERF-TTP) research group and the Research on Adverse Drug Events and Reports (RADAR) project.2007

    • Author(s)
      Bennett CL, Banjamin K, Zakarija A, Bandarenko N, Pandey DK, Buffie CG, McKoy JM, Tevar AD, Cursio JF, Yarnold PR, Kwaan HC, De Masi D, Sarode R, Raife TJ, Kiss JE, Raisch DW, Davidson C, Sadler JE, Ortel TL, Zheng XL, Kato S, Matsumoto M, Uemura M, Fujimura Y
    • Journal Title

      J Am Coll Cardiol 50

      Pages: 1138-1143

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Two mechanistic pathways for thienopyridine-associated thrombotic thrombocytopenic purpura : A report from the Surveillance, Epidemiology, and Risk Factors for Thrombotic Thrombocytopenic Purpura (SERF-TTP) Research Group and the Research on Adverse Drug Events and Reports (RADAR) Project.2007

    • Author(s)
      Bennett CL, Kim B, Zakarija A, Bandarenko N, Pandey DK, Buffie CG, McKoy JM, Tevar AD, Cursio JF, Yarnold PR, Kwaan HC, De Masi D, Sarode R, Raife TJ, Kiss JE, Raisch DW, Davidson C, Sadler JE, Ortel TL, Zheng XL, Kato S, Matsumoto M, Uemura M, Fujimura Y.
    • Journal Title

      J Am Coll Cardiol (in press)

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16590796
  • [Journal Article] Prophylactic fresh frozen plasma infusion may prevent the development of hepatic VOD after stem cell transplantation via ADAMTS13-mediated restoration of von Willebrand factor plasma levels.2007

    • Author(s)
      Matsumoto M, Kawa K, Uemura M, Kato S, Ishizashi H, Isonishi A, Yagi H, Park YD, Takeshima Y, Kosaka Y, Hara H, Kai S, Kanamaru A, Fukuhara S, Hino M, Sako M, Hiraoka A, Ogawa H, Hara J, Fujimura Y.
    • Journal Title

      Bone Marrow Transplant (in press)

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16590796
  • [Journal Article] Quantitative western blot analysis of plasma ADAMTSI3 antigen in patients with Upshaw-Schulman syndrome.2007

    • Author(s)
      Ishizashi H, Yagi H, Matsumoto M, Soejima K, Nakagaki T, Fujimura Y
    • Journal Title

      Thromb Res. 120

      Pages: 381-386

    • Data Source
      KAKENHI-PROJECT-19591130
  • [Journal Article] Plasma levels of ADAMTS13 antigen determined with an enzyme immunoassay using a neutralizing monoclonal antibody parallel ADAMTS13 activity levels.2007

    • Author(s)
      Yagi H, Ito S, Kato S, Hiura H, Matsumoto M, Fujimura Y.
    • Journal Title

      Int J Hematol 85

      Pages: 403-407

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16590796
  • [Journal Article] Plasma ADAMTS13 activity may predict early adverse events In living liver transplantation : observation in 3 cases.2006

    • Author(s)
      Ko S, Okano E, Kanehiro H, Matsumoto M, Ishizashi H, Uemura M, Fujimura Y, Tanaka K, Nakajima Y.
    • Journal Title

      Liver Transplant. 12(5)

      Pages: 859-69

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17500439
  • [Journal Article] Novel monoclonal antibody-based enzyme immunoassay for determining plasma levels of ADA2006

    • Author(s)
      Kato S, Matsumoto M, Fujimura Y, 他3名
    • Journal Title

      Transfusion (In press)

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Plasma ADAMTS13 activity may predict early adverse events in living donor liver transplantation : Observations in three cases.2006

    • Author(s)
      Saiho Ko, Eiji Okano, Hiromichi Kanehiro, Masanori Matsumoto, Hiromichi Ishizashi, Masahito Uemura, Yoshihiro Fujimura, Koichi Tanaka, Yoshiyuki Nakajima.
    • Journal Title

      Liver Transplant (in press)

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Novel monoclonal antibody-based enzyme immunoassay for determining plasma levels of ADAMTS13 activity.2006

    • Author(s)
      Seiji Kato, Masanori Matsumoto, Tomomi Matsuyama, Ayami Isonishi, Hisahide Hiura, Yoshihiro Fujimura.
    • Journal Title

      Transfusion (in press)

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Platelets treated with ticlopidine are less reactive to unusually large VWF multimers than are those treated with aspirin under high shear stress.2006

    • Author(s)
      Matsumoto M, Kawaguchi S, Ishizashi H, Yagi H, Iida J, Sakaki T, Fujimura Y.
    • Journal Title

      Pathophy Haemost. Thromb. 4(1)

      Pages: 35-40

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17500439
  • [Journal Article] Thrombotic thrombocytopenic purpura associated with polyarthritis nodosa : demonstration of the inhibitor against von Willebrand factor-cleaving protease.2006

    • Author(s)
      Fujisaki K, Matsutani K, Yoshimitsu T, Nakanishi K, Matsumoto M, Yagi H, Ishizashi H, Fujimura Y, Takeda K, Hirakata H, Iida M.
    • Journal Title

      Clinical Nerhrology 64(4)

      Pages: 305-10

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17500439
  • [Journal Article] Plasma ADAMTS13 activity may predict early adverse events in living donor liver transplantation : Observations in three cases.2006

    • Author(s)
      Ko S, Okano E, Kanehiro H, Matsumoto M, Ishizashi H, Uemura M, Fujimura Y, Tanaka K, Nakajima Y.
    • Journal Title

      Liver Transplant 12

      Pages: 859-869

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16590796
  • [Journal Article] Novel monoclonal antibody-based enzyme immunoassay for determining plasma levels of ADAMTS13 activi2006

    • Author(s)
      Kato S, Matsumoto M, Fujimura Y, 他3名
    • Journal Title

      Transfusion (In press)

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Novel monoclonal antibody-based enzyme immunoassay for determining plasma levels of ADAMTS13 activity.2006

    • Author(s)
      Kato S, Matsumoto M, Matsuyama T, Isonishi A, Hiura H, Fujimura Y.
    • Journal Title

      Transfusion 46

      Pages: 1444-1452

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16590796
  • [Journal Article] Novel compound heterozygote mutations (H234Q/R1206X) of the ADAMTS13 gene in an adult patient with Upshaw-Schulman syndrome showing predominant episodes of repeated acute renal failure.2006

    • Author(s)
      Shibagaki Y, Matsumoto M, Kokame K, Ohba S, Miyata T, Fujimura Y, Fujita T.
    • Journal Title

      Nephrol Dial Transplant (in press)

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Thrombotic thrombocytopenic purpura associated with pegylated-interferon alpha-2a by an ADAMTS13 inhibitor in a patient with chronic hepatitis C2006

    • Author(s)
      Kitano K, Gibo Y, Kamiho A, Furuta K, Oguchi S, Joshita S, Takahashi Y, Ishida F, Matsumoto M, Uemura M, Fujimura Y
    • Journal Title

      Haematologica 91(8)

    • Data Source
      KAKENHI-PROJECT-17590670
  • [Journal Article] Plasma ADAMTS13 activity may predict early adverse events in living donor liver transplantation : Observations in three cases.2006

    • Author(s)
      Ko S, Okano E, Kanehiro H, Fujimura Y, 他4名
    • Journal Title

      Liver Transplant (In press)

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Plasma ADAMTS13 activity may predict early adverse events in living donor liver transplantation: Observations in three cases.2006

    • Author(s)
      Ko S, Okano E, Kanehiro H, Fujimura Y, 他4名
    • Journal Title

      Liver Transplant (In press)

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Analyses of ADAMTS13 activity and its inhibitor in patients with thrombotic thrombocytopenic purpura secondary to connective tissue diseases : Observations in a single hospital.2006

    • Author(s)
      Sato T, Hamaoka R, Ohshima M, Miwa Y, OkazakiY, Yajima N, Ishizashi H, Matsumoto M, Fujimura Y, Inokuma S.
    • Journal Title

      Clin. Exp. Rheumatol. 24(4)

      Pages: 454-5

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17500439
  • [Journal Article] Platelets treated with ticlopidine are less reactive to unusually large VWF multimers than are those treated with aspirin under high shear stress.2005

    • Author(s)
      Matsumoto M, Kawaguchi S, Ishizashi H, Yagi H, Iida J, Sakaki T, Fujimura Y.
    • Journal Title

      Pathophy Haemost Thromb 35

      Pages: 35-40

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Localization of ADAMTS13 to the stellate cells of human2005

    • Author(s)
      Uemura M, Tatsumi K, Fujimura Y, 他7名
    • Journal Title

      Blood 106

      Pages: 922-926

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] 薬剤によるTTPの発症機序とその場合の治療について教えて下さい2005

    • Author(s)
      植村正人, 藤村吉博
    • Journal Title

      血栓と循環 13

      Pages: 204-208

    • Data Source
      KAKENHI-PROJECT-17590670
  • [Journal Article] Adenovirus-mediated transfer of human placental ecto-ATP diphosphohydrolase l to vascular smooth muscle cells suppresses platelet aggregation in vitro and arterial thrombus formation in vivo.2005

    • Author(s)
      Furukoji E.Matsumoto M, Fujimura Y, 他8名
    • Journal Title

      Circulation 111

      Pages: 808-815

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Platelets treated with ticlopidine are less reactive to unusually large VWF multimers than are those treated with aspirin under high shear stress.2005

    • Author(s)
      Matsumoto M, Kawaguchi S, Fujimura Y, 他4名.
    • Journal Title

      Pathophy Haemost Thromb 34

      Pages: 35-40

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Adenovirus-mediated transfer of human placental ecto-ATP diphosphohydrolase I to vascular smooth muscle cells suppresses platelet aggregation in vitro and arterial thrombus formation in vivo.2005

    • Author(s)
      Furukoji, Fujimura Y.他9名
    • Journal Title

      Circulation 111

      Pages: 808-815

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Development of ADAMTS13 inhibitor in a patient with hepatitis C virus-related liver cirrhosis causes thrombotic thrombocytopenic purpura.2005

    • Author(s)
      Yagita M, Fujimura Y.他9名
    • Journal Title

      J.Hepatology 42

      Pages: 420-421

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Decreased CD39 expression in coronary artherosclerotic lesions is implicated in plaque instability and thrombus formation.2005

    • Author(s)
      Hatakeyama K, Fujimura Y, 他7名
    • Journal Title

      Am J Cardiol 95

      Pages: 632-635

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Localization of ADAMTS13 to the stellate cells of human liver.2005

    • Author(s)
      Uemura M, Tatsumi K, Matsumoto M, Fujimoto M, Matsuyama T, Ishikawa M, Iwamoto T, Mon T, Wanaka A, Fukui H, Fujimura Y.
    • Journal Title

      Blood 106

      Pages: 922-924

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Platelets treated with ticlopidine are less reactive to unusually large VWF multimers than are those treated with aspirin under high shear stress.2005

    • Author(s)
      Matsumoto M, Kawaguchi S, Fujimura Y, 他4名
    • Journal Title

      Pathophy Haemost Thromb 34

      Pages: 35-40

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Rituximab provided long-term remission in a case with refractory relapsing thrombotic thrombocytopenic pu2005

    • Author(s)
      Kosugi S, Matsumoto M, Fujimura Y, 他4名
    • Journal Title

      lnt J Hematol 81

      Pages: 433-436

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Adenovirus-mediated transfer of human placent al ecto-ATP diphosphohydrolase I to vascular smooth muscle cells suppresses platelet aggregation in vitro and arterial thrombus formation in2005

    • Author(s)
      Furukoji E., Matsumoto M, Fujimura Y, 他8名
    • Journal Title

      Circulation 111

      Pages: 808-815

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Adenovirus-mediated transfer of human placental ecto-ATP diphosphohydrolase I to vascular smooth muscle cells suppresses platelet aggregation in vitro and arterial thrombus formation in vivo.2005

    • Author(s)
      Furukoji E.Matsumoto M, Yamashita A, Yagi H, Sakurai Y, Marutsuka K, Hatakeyama K, Morishita K, Fujimura Y, Tamura S, Asada Y.
    • Journal Title

      Circulation 111

      Pages: 808-815

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] VWF73, a region from D1596 to R1668 of von Willebrand factor, provides a minimal substrate for ADAMTS-13.2004

    • Author(s)
      Kokame K, Matsumoto M, Fujimura Y, Miyata T.
    • Journal Title

      Blood 103

      Pages: 607-612

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] The Japanese experience with thrombotic thrombocytopenic purpura-hemolytic uremic syndrome.2004

    • Author(s)
      Matsumoto M, Yagi H, Ishizashi H, Wada H, Fujimura Y.
    • Journal Title

      Semin Hematol 41

      Pages: 68-74

    • Data Source
      KAKENHI-PROJECT-16590796
  • [Journal Article] Identification of novel mutations in ADAMTS13 in an adult patient with congenital thrombotic thrombocytopenic purpura.2004

    • Author(s)
      Uchida T, Fujimura Y他11名
    • Journal Title

      Blood 104

      Pages: 2081-2083

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Identification of novel mutations in ADAMTS13 in an adult patient with congenital thrombotic thrombocytopenic purpura.2004

    • Author(s)
      Uchida T, Wda H, Mizutani M, Iwashita M, Ishihara H, Shibano T, Suzuki M, Matsubara Y, Soejima K, Matsumoto M, Fujimura Y, Ikeda Y, Murata M.
    • Journal Title

      Blood 104

      Pages: 2081-2083

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15500455
  • [Journal Article] The Japanese experience with thrombotic thrombocytopenic purpura-hemolytic uremic syndrome.2004

    • Author(s)
      Matsumoto M, Yagi H, Ishizashi H, Wada H, Fujimura Y.
    • Journal Title

      Semin Hematol 41

      Pages: 68-74

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] VWF73, a region from D1596 to R1668 of von Willebrand factor, provides a minimal substrate for ADAMTS-13.2004

    • Author(s)
      Kokame K, Matsumoto M, Fujimura Y, Miyata T.
    • Journal Title

      Blood 103

      Pages: 607-612

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-15500455
  • [Journal Article] The Japanese experience with thrombotic thrombocytopenic purpura-hemolytic uremic syndrome.2004

    • Author(s)
      Matsumoto M, Yagi H, Ishizashi H, Wada H, Fujimura Y.
    • Journal Title

      Seminar in Hematol 41

      Pages: 68-74

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15500455
  • [Journal Article] Molecular characterization of ADAMTS13 gene mutations in Japanese patients with Upshaw-Schulman syndrome.2004

    • Author(s)
      Matsumoto M, Fujimura Y.他16名
    • Journal Title

      Blood 103

      Pages: 305-1310

    • Data Source
      KAKENHI-PROJECT-16590796
  • [Journal Article] Molecular characterization of ADAMTS13 gene mutations in Japanese patients with Upshaw-Schulman syndrome.2004

    • Author(s)
      Matsumoto M, Kokame K, Soejima K, Miura M, Hayashi S, Fujii Y, Iwai A, Ito E, Tsuji Y, Takeda-Shitaka M, Iwadate M, Umeyama H, Yagi H, Ishizashi H, Banno F, Nakagaki T, Miyata T, Fujimura Y.
    • Journal Title

      Blood 103

      Pages: 1305-1310

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Diffuse neurodeficits in intravascular lymphomatosis with ADAMTS13 inhibitor.2004

    • Author(s)
      Kawahara M, Kanno M, Matsumoto M, Nanno H, Danno D, Murata K, Nakamura S, Fujimura Y, Ueno S.
    • Journal Title

      Neurology 63

      Pages: 1731-1733

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] The Japanese experience with thrombotic thrombocytopenic purpura-hemolytic uremic syndrome.2004

    • Author(s)
      Matsumoto M, Yagi H, Ishizashi H, Wada H, Fujimura Y.
    • Journal Title

      Semin Hematol 41

      Pages: 68-74

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-15500455
  • [Journal Article] Molecular characterization of ADAMTS13 gene mutations in Japanese patients with Upshaw-Schulman syndrome.2004

    • Author(s)
      Matsumoto M, Kokame K, Soejima K, Miura M, Hayashi S, Fujii Y, Iwai A, Ito E, Tsuji Y, Takada-Shitaka M, Iwadate M, Umeyama H, Yagi H, Ishizashi H, Banno F, Nakagaki T, Miyata T, Fujimura Y.
    • Journal Title

      Blood 103

      Pages: 1305-1310

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15500455
  • [Journal Article] Identification of novel mutations in ADAMTS13 in an adult patient with congenital thrombotic thrombocytopenic purpura.2004

    • Author(s)
      Uchida T, Wada H, Mizutani M, Iwashita M, Ishihara H, Shibano T, Suzuki M, Matsubara Y, Soejima K, Matsumoto M, Fujimura Y, Ikeda Y, Murata M.
    • Journal Title

      Blood 104

      Pages: 2081-2083

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Diffuse neurodeficits in intravascular lymphomatosis with ADAMTS13 inhibitor.2004

    • Author(s)
      Kawahara M, Fujimura Y, 他7名
    • Journal Title

      Neurology 63

      Pages: 1731-1733

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Molecular characterization of ADAMTS13 gene mutations in Japanese patients with Upshaw-Schulman syndrome.2004

    • Author(s)
      Matsumoto M, Fujimura Y.他16名
    • Journal Title

      Blood 103

      Pages: 305-1310

    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Mural thrombus generation in type 2A and 2B von Willebrabd disease under high shear conditions.2003

    • Author(s)
      Sugimoto M, Matsui H, Mizuno T, Tsuji S, Miyata S, Matsumoto M, Matsuda M, Fujimura Y, Yoshioka A.
    • Journal Title

      Blood 101

      Pages: 915-920

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] von Willebrand factor-cleaving protease activity in thrombotic microangiopathy after living donor liver transplantation.2003

    • Author(s)
      Nakazawa Y, Hashikura Y, Urata K, Ikegami T, Terada M, Yagi H, Ishizashi H, Matsumoto M, Fujimura Y, Miyagawa S.
    • Journal Title

      Liver Transplant 9

      Pages: 1328-1333

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] Significance of measuring von Willebrand factor-cleaving protease activity in thrombotic microangiopathy after living donor liver transplantation.2003

    • Author(s)
      Nakazawa Y, Hashikura Y, Ogino S, Urata K, Ikegami T, Terada M, Yagi H, Ishizashi H, Matsumoto M, Fujimura Y, Kawasaki S.
    • Journal Title

      Liver Transplant 9

      Pages: 1328-1333

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15500455
  • [Journal Article] ADAMTS-13 cysteine-rich/spacer domains are functionally essential for von Willebrand factor cleavage.2003

    • Author(s)
      Soejima K, Matsumoto M, Kokame K, Yagi H, Ishizashi H, Maeda H, Nozaki C, Miyata T, Fujimura Y, Nakagaki T.
    • Journal Title

      Blood 102

      Pages: 3232-3237

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Journal Article] ADAMTS-13 cysteine-rich/spacer domains are functionally essential for von Willebrand factor cleavage.2003

    • Author(s)
      Soejima K, Matsumoto M, Kokame K, Yagi H, Ishizashi H, Maeda H, Nozaki C, Miyata T, Fujimura Y, Nakagaki T.
    • Journal Title

      Blood 102

      Pages: 3232-3237

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15500455
  • [Journal Article] 肝産生酵素ADAMTS13と血栓症

    • Author(s)
      藤村吉博、植村正人
    • Journal Title

      臨床血液 49

      Pages: 1420-1433

    • NAID

      10021932876

    • Data Source
      KAKENHI-PROJECT-20590794
  • [Patent] 抗ADAMTS13モノクローナル抗体2004

    • Inventor(s)
      藤村 吉博, 松本 雅則, 森 俊郎
    • Industrial Property Rights Holder
      藤村 吉博, 松本 雅則, 森 俊郎
    • Filing Date
      2004-10-19
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-15591017
  • [Presentation] TMA:最近の考え方と治療法の選択2015

    • Author(s)
      藤村吉博
    • Organizer
      Nagoya Hematology Forum
    • Place of Presentation
      ヒルトン名古屋(愛知県・名古屋市)
    • Year and Date
      2015-02-06
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] 本邦における非典型溶血性尿毒症症候群患者の登録状況と診断法の確立2014

    • Author(s)
      吉田瑶子、内田裕美子、芦田明、服部元史、松本雅則、宮田敏行、藤村吉博
    • Organizer
      第49回 日本小児腎臓病学会学術集会
    • Place of Presentation
      秋田ビューホテル
    • Data Source
      KAKENHI-PROJECT-25860685
  • [Presentation] ADAMTS13と血小板輸血-過去、現在、未来2014

    • Author(s)
      藤村吉博
    • Organizer
      第20回 ADAMTS13研究会
    • Place of Presentation
      奈良ホテル(奈良県・奈良市)
    • Year and Date
      2014-09-18
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] Registry of congenital thrombotic microangiopathy in Japan.2014

    • Author(s)
      Fujimura Y
    • Organizer
      The 3rd ASEAN Federation of Hematology Congress.Plenary lecture
    • Place of Presentation
      Bangkok(Thailand)
    • Year and Date
      2014-10-23
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] Introduction of a quick assay for ADAMTS13 activity improved a survival of acquired TTP patients who received platelet transfusions.2014

    • Author(s)
      Yoshii Y, Matsumoto M, Kurumatani N, Isonishi A, Uemura M, Hori Y, Hayakawa M, Yagi H, Bennett C.L., Fujimura Y
    • Organizer
      The 56th Annual meeting of American Society of Hematology
    • Place of Presentation
      San Francisco(USA)
    • Year and Date
      2014-12-08
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] 定量的溶血試験と遺伝子解析を用いた本邦aHUS患者の病態解析2014

    • Author(s)
      吉田瑶子、Xinping Fan、大山良文、古久保哲朗、岩本顕聰、森俊雄、松本雅則、池島裕子、宮田敏行、藤村吉博
    • Organizer
      第36回 日本血栓止血学会学術集会
    • Place of Presentation
      大阪国際交流センター
    • Data Source
      KAKENHI-PROJECT-25860685
  • [Presentation] Decreased platelet thrombus size, due to a heightened proteolysis of VWF by ADAMTS13 is quickly restored after valve replacement in aortic stenosis patients.2014

    • Author(s)
      Yagi H, Hayakawa M, Yamaguchi N, Yamashita K, Taniguchi S, Matsumoto M, Tsubaki K, Fujimura Y
    • Organizer
      The 56th Annual meeting of American Society of Hematology
    • Place of Presentation
      San Francisco(USA)
    • Year and Date
      2014-12-07
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] TTP, HUS, aHUSの鑑別診断と治療.2014

    • Author(s)
      藤村吉博
    • Organizer
      第59回臨床病理近畿支部例会
    • Place of Presentation
      天理医療大学キャンパス(奈良県・天理市)
    • Year and Date
      2014-06-21
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] 本邦の非典型溶血性尿毒症症候群(aHUS)の患者登録とその 表現型-遺伝子型 解析2013

    • Author(s)
      吉田瑶子、範新萍、本田繁則、芦田明、服部元史、松本雅則、大山良文、古久保哲朗、南学正臣、宮田敏行、藤村吉博
    • Organizer
      第48回 日本小児腎臓病学会学術集会
    • Place of Presentation
      あわぎんホール
    • Data Source
      KAKENHI-PROJECT-25860685
  • [Presentation] Atypical Hemolytic Uremic Syndrome In Japan Characterized By The Inhibitory Antibody-Based Hemolytic Assay and The Gene Analysis.2013

    • Author(s)
      Yoshida Y, Fan X, Ohyama Y, Kokubo T, Matsumoto M, Yagi H, Shirotani-Ikejima H, Miyata T, FujimuraY.
    • Organizer
      55th Annual meeting of American Society of Hematology.
    • Place of Presentation
      Ernest N. Morial Convention Center (USA)
    • Data Source
      KAKENHI-PROJECT-25860685
  • [Presentation] 非典型溶血性尿毒症症候群(aHUS)2013

    • Author(s)
      藤村吉博
    • Organizer
      第75回日本血液学会学術集会
    • Place of Presentation
      ロイトン札幌
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] Phenotype modifiers of ADAMTS 13 deficiency with respect to gender, gene mutations, and inhibitor boosting2012

    • Author(s)
      藤村吉博
    • Organizer
      56. Jahrestagung der Gesellschaft für Thrombose- und Hämostaseforschung (GTH)
    • Place of Presentation
      St. Gallen (Switzerland)
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] Natural history of Upshaw-Schulman syndrome based on ADAMTS13 gene analysis in Japan2011

    • Author(s)
      藤村吉博
    • Organizer
      XXIII Congress of the International Society on Thrombosis and Haemostasis
    • Place of Presentation
      京都国際会議場(京都府)
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] TMAとDIC:血液専門医が認識すべき病態と治療のパラダイムシフト2011

    • Author(s)
      藤村吉博
    • Organizer
      第2回サイト研究会 (招待講演)
    • Place of Presentation
      ホテル阪急インターナショナル前 エコルテホール(大阪府)
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] Size of vWF multimers, modulated by therapeutic regimens in hematopoietic stem cell transprantation, determine an adverse reaction to bleeding or thrombotic microangiopathy2011

    • Author(s)
      M.Matsumoto, K.Yamada, K. Nakayama, A.Isonishi, M. Hayakawa, M.Inoue, K.Kawa, Y. Fujimura
    • Organizer
      XXIII Congress of the International Society on Thrombosis and Haemostasis
    • Place of Presentation
      Kyoto
    • Year and Date
      2011-07-27
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Presentation] 周産期TMA(血栓性血小板減少性紫斑病)の診断と治療2011

    • Author(s)
      藤村吉博
    • Organizer
      平成23年度富山県産科婦人科学会 第4回例 (招待講演)
    • Place of Presentation
      ANAクラウンプラザホテル3階飛鳥の間(富山県)
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] 止血因子VWFとその特異的切断酵素ADAMTS13の均衡破綻による血栓症のパラダイムシフト2011

    • Author(s)
      藤村吉博
    • Organizer
      奈良県医師会第一回生涯教育講座(招待講演)
    • Place of Presentation
      奈良県医師会館(奈良県)
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] A large-pore gel electrophoresis separates the complex in both of ADAMTS13 bound to VWF and to the IgG autoantibodies from the unbound in plasma milieu2011

    • Author(s)
      M.Matsumoto, A.Isonishi, Y.Hori, M.Hayakawa, K. Soejima, Y. Fujimura
    • Organizer
      The 54th American Society of Hematology annual meeting and exposition
    • Place of Presentation
      San Diego
    • Year and Date
      2011-12-08
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Presentation] Natural history of Upshaw-Schulman syndrome based on ADAMTS13 gene analysis in Japan2011

    • Author(s)
      藤村吉博
    • Organizer
      第73回日本血液学会学術集会(JSH2011)
    • Place of Presentation
      名古屋国際会議場(名古屋県)
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] ADAMTS13とFactor Hに焦点を当てた血栓性微小血管障害症(TMA)の診断と治療2011

    • Author(s)
      藤村吉博
    • Organizer
      第15回 炎症と凝固研究会 (招待講演)
    • Place of Presentation
      三重大学医学部(三重県)
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] Acquired idiopathic thrombotic thrombocytopenic purpura in a population from Japan2011

    • Author(s)
      M.Matsumoto, C.Bennett, A. Isonishi, Z. Qureshi, Y.Hori, M. Hayakawa, Y.Yoshida, H.Yagi, Y. Fujimura
    • Organizer
      The 73rd Annual Meeting of the Japanese Society of Hematology
    • Place of Presentation
      Nagoya
    • Year and Date
      2011-10-16
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Presentation] 後天性・特発性TTPでADAMTS13活性著減を示す195例と古典的pentadで診断された89例の比較検討2010

    • Author(s)
      松本政則、藤村吉博, 石指宏通
    • Organizer
      第33回日本血栓止血学会
    • Place of Presentation
      鹿児島
    • Data Source
      KAKENHI-PROJECT-20500623
  • [Presentation] TTPモデルの血小板輸血禁忌の病態2010

    • Author(s)
      藤村吉博
    • Organizer
      第58回日本輸血・細胞治療学会総会
    • Place of Presentation
      名古屋市
    • Year and Date
      2010-05-29
    • Data Source
      KAKENHI-PROJECT-21591759
  • [Presentation] 後天性・特発性TTPでADAMTS13活性著減を示す195例と古典的pentadで診断された89例の比較検討2010

    • Author(s)
      松本雅則、石西綾美、加藤誠司、堀勇二、八木秀男、藤村吉博
    • Organizer
      第33回日本血栓止血学会学術集会
    • Place of Presentation
      鹿児島
    • Year and Date
      2010-04-22
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Presentation] 肝臓外科におけるADAMTS13活性の臨床的意義2009

    • Author(s)
      岡野永嗣、高済峯、松本雅則、藤村吉博、中島祥介, 他
    • Organizer
      第21回日本肝胆膵外科学会・学術集会
    • Place of Presentation
      名古屋
    • Year and Date
      2009-06-12
    • Data Source
      KAKENHI-PROJECT-21591759
  • [Presentation] 肝切除術後の血小板メカニズムとその対策2009

    • Author(s)
      岡野永嗣、高済峯、松本雅則、藤村吉博、中島祥介, 他
    • Organizer
      第64回日本消化器外科学会総会
    • Place of Presentation
      大阪
    • Year and Date
      2009-07-16
    • Data Source
      KAKENHI-PROJECT-21591759
  • [Presentation] Two Patient Groups with Acquired Idiopathic Thrombotic Thrombocytopenic Purpura, Defined by ADAMTS13(n=195)and/or Classic Pentad(n=89)2009

    • Author(s)
      松本雅則, 藤村吉博, 他3名
    • Organizer
      51th ASH Annual Meeting
    • Place of Presentation
      New Orleans(USA)
    • Year and Date
      2009-12-07
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] TTP/HUSの診断とADAMTS132009

    • Author(s)
      松本雅則, 藤村吉博
    • Organizer
      第112回日本小児科学会学術集会
    • Place of Presentation
      奈良市
    • Year and Date
      2009-04-18
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] 生体肝移植術中ならびに術後における血中ADAMTS13活性と超高分子量von Willebrand factor重合体の動態解析2009

    • Author(s)
      高済峯、松本雅則、藤村吉博、中島祥介, 他
    • Organizer
      第45回日本移植学会総会
    • Place of Presentation
      東京
    • Year and Date
      2009-09-18
    • Data Source
      KAKENHI-PROJECT-21591759
  • [Presentation] National questionnaire survey of TMA2009

    • Author(s)
      Ito N, Wada H., Sugita M, Matsumoto M, Fujimura Y, Murata M, Ikeda Y
    • Organizer
      XXII ISTH congress
    • Place of Presentation
      Boston
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] 膠原病TMAにおけるADAMTS13解析と臨床所見との関連2009

    • Author(s)
      松本雅則, 藤村吉博, 他3名
    • Organizer
      第32回日本血栓止血学会学術集会
    • Place of Presentation
      北九州市
    • Year and Date
      2009-06-05
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Identification of 41 Japanese patients with Upshaw-Shulman syndrome, with special reference to its genotype-phenotype analysis.2009

    • Author(s)
      Fujimura Y, Kokame K, Matsumoto M, Isonishi A, Kato S., Hiura H., Miyata T
    • Organizer
      XXII ISTH congress
    • Place of Presentation
      Boston
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Multiple Mapping of Peptide Sequences Recognized by Various Monoclonal Anti-ADAMTS13 Antibodies with Functional or Nonfunctional Effects On the Catalytic Activity.2009

    • Author(s)
      Nakagawa T, Moriki T, Yamaguchi Y, Igari A, Soejima K, Matsumoto M, Fujimura Y, Murata M
    • Organizer
      51th ASH Annual Meeting
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Thrombotic thrombocytopenic purpura: Results of the patients with thrombotic micro- angiopathies across Japan by ADAMTS13 analysis during 1998-2008.2009

    • Author(s)
      Fujimura Y, Matsumoto M
    • Organizer
      XXth Regional Congress of the 1SBT, Asia-Academy program (Hemostasis)
    • Place of Presentation
      Nagoya
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Characterization of Two Patient Groups with Acquired Idiopathic Thrombotic Thrombocytopenic Purpura, Defined by ADAMTS13 (n=195) and/or Classic Pentad (n=89).2009

    • Author(s)
      Matsumoto M, Isonishi A, Kato S, Ishizashi H, Yagi H, Fujimura Y
    • Organizer
      51th ASH Annual Meeting
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] 重症肝・膵疾患における多臓器不全の病態解析-ADAMTS13を中心に2008

    • Author(s)
      植村正人, 藤村吉博, 福井博
    • Organizer
      第94回日本消化器病学会総会(ワークショップ)
    • Place of Presentation
      福岡
    • Year and Date
      2008-05-09
    • Data Source
      KAKENHI-PROJECT-20590794
  • [Presentation] Identification of ADAMTS13 peptide sequences recognized by autoantibodies in patients with acquired thrombotic thrombocytopenic purpura.2008

    • Author(s)
      Yusuke Yamaguchi, Takanori Moriki, Hideo Wada, Masanori Matsumoto, Yoshihiro Fujimura, Terumichi Nakagawa, Atsuko Igari, Yasuo Ikeda, Mitsuru Murata
    • Organizer
      50th ASH annual meeting
    • Place of Presentation
      San Francisco (USA)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] 造血幹細胞移植後TMAに対するFFP定期輸注による治療効果.2008

    • Author(s)
      松本雅則, 石西綾美, 藤村吉博
    • Organizer
      第52回日本輸血・細胞治療学会近畿支部総会学術講演会
    • Place of Presentation
      奈良県立医科大学
    • Year and Date
      2008-11-29
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Potential role of enhanced cytokinemia and endotoxemia on the decreased activity of plasma ADAMTS13 in patients with alcoholic hepatitis.2008

    • Author(s)
      Masatoshi Ishikawa, Masahito Uemura, Tomomi Matsuyama, Masanori Matsumoto, Masao Fujimoto, Hiromichi Ishizashi, Seiji Kato, Chie Morioka, Tatsuhiro Tsujimoto, Toshiyuki Kitazawa, Hidehito Kawaratani, Yoshihiro Fujimura, Hiroshi Fukui
    • Organizer
      50th ASH annual meeting
    • Place of Presentation
      San Francisco (USA)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Analysis of ADAMTS13 in patients with collagen disease-associated TMAs.2007

    • Author(s)
      Matsuyama T, Matsumoto M, Isonishi A, Uemura M, Inokuma S, Fujimura Y
    • Organizer
      XXI Congress of the ISTH
    • Place of Presentation
      Geneva (Switzerland)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Ticlopidine- and Clopidogrel- associated thrombotic thrombocytopenic purpura (TTP): final results from the serveillance epidermiology and risk factor- TTP study group.2007

    • Author(s)
      Richey EA, Bennett CL, Kwaan HC, Zakarija A, Bandarenko N, Pandey DK, Yarnold PR, Raisch DW, Winters TL, Raife TJ, Curio JF, Fisher MJ, Ortel TL, Tallman MS, Matsumoto M, Fujimura Y. Moake JL
    • Organizer
      49th ASH annual meeting
    • Place of Presentation
      Atlanta (USA)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Plasma ADAMTS13 activity markedly decreased in patients with severe acute pancreatitis: Its potential role on the development of multiorgan failure.2007

    • Author(s)
      Morioka C, Uemura M, Matsuyama T, Matsumoto M, Kato S, Ishikawa M, Ishizashi H, Fujimoto M, Tsujimoto T, Nishio K, Okuchi K, Fujimura Y, Fukui H
    • Organizer
      49th ASH annual meeting
    • Place of Presentation
      Atlanta (USA)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Alternation of von Willebrand factor and ADAMTS13 activity and its clinical significant in patients with obstructive sleep apnea syndrome.2007

    • Author(s)
      Koyama N, Makinodan K, Tamaki S, Fukuoka A, Hamada K, Matsumoto M, Fujimura Y, Kimura H
    • Organizer
      XXI Congress of the ISTH
    • Place of Presentation
      Geneva (Switzerland)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Analysis of ADAMTS13 and its IgG-autoantibodies in 170 patients with connective tissue disease-associated thrombotic microangiopathy indicates more than 2 types on its pathogenesis.2007

    • Author(s)
      Matsuyama T, Matsumoto M, Isonishi A, Inokuma S, Fujimura Y
    • Organizer
      49th ASH annual meeting
    • Place of Presentation
      Atlanta (USA)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] The ADAMTS13 analysis on thrombotic microangiopathies in Japan2007

    • Author(s)
      Matsumoto M, Fujimura Y.
    • Organizer
      6th World Congress of the International Society for Apheresis/World Apheresis Association 11th Congress
    • Place of Presentation
      Yokohama (Japan)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Immuno-purification of ADAMTS13 and its physico-chemical characterization.2007

    • Author(s)
      Hiura H, Isonoshi A, Kato S, Matsumoto M, Fujimura Y
    • Organizer
      XXI Congress of the ISTH
    • Place of Presentation
      Geneva (Switzerland)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Natural history of 33 patients with Upshaw-Schulman syndrome has revealed that all the gravida develop thrombocytopenia, often followed by thrombotic microangiopathy with stillbirth.2007

    • Author(s)
      Fujimura, Y, Matsumoto M, Kokame K, Yagi H, Isonishi A, Matsuyama T, Kato S, Ishizashi H, Shida Y, Kenji N, Akiyama N, Tomiyama J, Natori K, Kuraishi Y, lmamura Y, Inoue N, Higasa S, Seike M, Kozuka T, Hara M, Sugimoto M, Wada H, Murata M, Miyata T, Ikeda Y
    • Organizer
      49th ASH annual meeting
    • Place of Presentation
      Atlanta (USA)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] Clinical and outcomes findings for thrombotic thrombocytopenic purpura among 467 persons with severely versus not severely deficient ADAMTS-13 levels.2007

    • Author(s)
      Bennett CL, Luu TH, Zakarija A, Kwaan HC, Bandarenko N, Pandey DK, Curio JF, McKoy JM, Buffie C, Winters JL, Ortel TL, Sarode R, Zheng XL, Raife TJ, Matsumoto M, Fujimura Y. Rock GA
    • Organizer
      49th ASH annual meeting
    • Place of Presentation
      Atlanta (USA)
    • Data Source
      KAKENHI-PROJECT-19591130
  • [Presentation] A long-term phenotype analysis of 51 patients with Upshaw -Schulman Syndrome in Japan, with special references to pregnancy and renal failure that requires hemodialysis

    • Author(s)
      Fujimura Y, Yoshii Y, Matsumoto M, Isonishi A, Hayakawa M, Yoshida Y, Yagi H, Kokame K, Miyata T.
    • Organizer
      The 55th Annual meeting of American Society of Hematology
    • Place of Presentation
      Ernest N. Morial Convention Center(New Orleans, USA)
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] 均一な集団と考えられるADAMTS13 活性著減(<0.5%)後天性特発性TTP 150 例の解析.

    • Author(s)
      松本雅則,Bennett Charles,石西綾美,Qureshi Zenia,堀勇二,早川正樹,吉田瑶子,八木秀男, 藤村吉博.
    • Organizer
      第34回日本血栓止血学会学術集会.
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Presentation] 本邦でのaHUS患者のdiagnostic pathwayと登録状況

    • Author(s)
      藤村吉博
    • Organizer
      第49回補体シンポジウム
    • Place of Presentation
      大阪府立成人病センター(大阪)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] 本邦におけるTMA解析状況

    • Author(s)
      藤村吉博
    • Organizer
      第7回日本血栓止血学会学術標準化委員会シンポジウム
    • Place of Presentation
      東医健保会館(東京)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] ADAMTS13: Biology and Upshaw-Schulman Syndrome

    • Author(s)
      Yoshihiro Fujimura
    • Organizer
      23rd Annual Hemophilia Research Study Update Meeting(HRSU)
    • Place of Presentation
      THE GRAND HOTEL MALAHIDE(アイルランド)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] TMA病態に対する新鮮凍結血漿由来ADAMTS13の治療効果

    • Author(s)
      藤村吉博
    • Organizer
      石川県合同輸血療法委員会
    • Place of Presentation
      石川県地場産業振興センター(石川)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] Molecular effects of four mutations identified in the D3 region of thrombomodulin in patients with atypical hemolytic uremic syndrome.

    • Author(s)
      Ashida A, Yamamoto D, Yoshida Y, Matsumoto M, Miyata T, Hattori M, Fujimura Y, Tamai H.
    • Organizer
      American Society of Nephrology
    • Place of Presentation
      Philadelphia(USA)
    • Year and Date
      2014-11-13 – 2014-11-16
    • Data Source
      KAKENHI-PROJECT-25860685
  • [Presentation] 後天性TTPに対する血漿交換療法.

    • Author(s)
      1.松本雅則、藤村吉博.
    • Organizer
      第61回日本輸血・細胞治療学会総会
    • Place of Presentation
      横浜
    • Invited
    • Data Source
      KAKENHI-PROJECT-25461456
  • [Presentation] 均一な集団と考えられるADAMTS13 活性著減(<0.5%)後天性特発性TTP 150 例の解析.

    • Author(s)
      松本雅則,Bennett Charles,石西綾美,Qureshi Zenia,堀勇二,早川正樹,吉田瑶子,八木秀男,藤村吉博.
    • Organizer
      第34回日本血栓止血学会学術集会.
    • Place of Presentation
      ハイアットリージェンシー(東京)
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] TMA:診断と治療の新しい展開

    • Author(s)
      藤村吉博
    • Organizer
      第21回 群馬血液疾患研究会
    • Place of Presentation
      群馬ロイヤルホテル(群馬)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] Establishing a TTP diagnostic network in Japan -Experience at Nara-

    • Author(s)
      Yoshihiro Fujimura
    • Organizer
      International and ANZ Steering Committee for APMAT Research Network
    • Place of Presentation
      Melbourne Convention Center(オーストラリア)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] TMA:診断と治療の新しい展開

    • Author(s)
      藤村吉博
    • Organizer
      第19回岐阜血液研究会
    • Place of Presentation
      岐阜グランドホテル(岐阜)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] ADAMTS13-VWFの均衡破綻による血栓性微小血管障害症

    • Author(s)
      藤村吉博
    • Organizer
      第3回 Global and New Insight into HSCT研究会
    • Place of Presentation
      ウエスティン都ホテル京都(京都)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] 血小板減少症におけるHIT抗体検査の重要性-奈良医大での経験

    • Author(s)
      松本雅則、藤村吉博
    • Organizer
      2010年度第31回日本アフェレシス学会学術大会
    • Place of Presentation
      千葉
    • Data Source
      KAKENHI-PROJECT-22591069
  • [Presentation] Thrombotic thrombocytopenic purpura(TTP) と Hemolytic uremic syndrome(HUS) ~病態解明と診断のための新たなマーカー~

    • Author(s)
      藤村吉博
    • Organizer
      第35回日本血栓止血学会学術集会
    • Place of Presentation
      山形国際ホテル
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] 後天性TTPに対する血漿交換療法

    • Author(s)
      藤村吉博
    • Organizer
      第61回日本輸血・細胞治療学会総会
    • Place of Presentation
      パシフィコ横浜
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] 非典型溶血性尿毒症症候群 (aHUS): 診断と治療の進歩

    • Author(s)
      藤村吉博
    • Organizer
      第35回日本血栓止血学会学術集会
    • Place of Presentation
      山形国際ホテル
    • Invited
    • Data Source
      KAKENHI-PROJECT-23591425
  • [Presentation] Unusually large VWF multimers appearing in patient plasmas of HSCT predispose TMA:Management with plasma ADAMTS13 and recombinant soluble thrombomodulin

    • Author(s)
      Hayakawa M, Matsumoto M, Fujimura Y
    • Organizer
      Jahrestagung der Gesellschaft fur Thrombose- und Hamostaseforschung (GTH)
    • Place of Presentation
      ICM-Internationales Congress Center Munchen(ドイツ)
    • Data Source
      KAKENHI-PROJECT-23591425
  • []

  • 1.  MATSUMOTO Masanori (60316081)
    # of Collaborated Projects: 16 results
    # of Collaborated Products: 229 results
  • 2.  ISHIZASHI Hiromichi (50260807)
    # of Collaborated Projects: 4 results
    # of Collaborated Products: 20 results
  • 3.  TITANI Koiti (60179942)
    # of Collaborated Projects: 4 results
    # of Collaborated Products: 0 results
  • 4.  MATSUI Taei (90183946)
    # of Collaborated Projects: 4 results
    # of Collaborated Products: 0 results
  • 5.  UEMURA Masahito (90151836)
    # of Collaborated Projects: 3 results
    # of Collaborated Products: 39 results
  • 6.  FUKUI Hiroshi (80145838)
    # of Collaborated Projects: 3 results
    # of Collaborated Products: 13 results
  • 7.  HAYAKAWA Masaki (30516729)
    # of Collaborated Projects: 3 results
    # of Collaborated Products: 24 results
  • 8.  KO Saiho (80305713)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 8 results
  • 9.  NAKAJIMA Yoshiyuki (00142381)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 6 results
  • 10.  SEKIGUCHI Kiyotoshi (50187845)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 0 results
  • 11.  HAYASHI Nobuhiro (80267955)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 0 results
  • 12.  INOUE Yoshimitsu (70144566)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 13.  SHIBATA Masaru (50405388)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 14.  SADO Toshiyuki (50275335)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 15.  YOSHIDA Yoko (90649443)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 13 results
  • 16.  MIYATA Toshiyuki (90183970)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 10 results
  • 17.  FUKUI Hiromu (20075104)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 18.  NISHIMURA Takuya (00192253)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 19.  NISHINO Masato (60164571)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 20.  SHIMA Midori (30162663)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 21.  TAKAHSHI Yukihiro (60142379)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 22.  HAMAKO Jiharu (80180933)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 23.  YONG-DONG Park (10285364)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 24.  SAKAMOTO Yoshiharu (40291611)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 25.  OYAMA Fumitaka (40194641)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 26.  MIZUOCHI Tsuguo (90133149)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 27.  西久保 敏也 (20208169)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 28.  中島 充 (30183510)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 29.  宮田 茂樹 (20239411)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 30.  阪井 利幸 (10175359)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 31.  松原 守 (90288481)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 32.  OHARA Osamu
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 33.  IMAI Kohsuke
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 34.  FUJIWARA Michihiro
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 35.  IRIE Keiichi
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 36.  大関 泰裕
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 37.  小亀 浩市
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 38.  三島 健一
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results

URL: 

Are you sure that you want to link your ORCID iD to your KAKEN Researcher profile?
* This action can be performed only by the researcher himself/herself who is listed on the KAKEN Researcher’s page. Are you sure that this KAKEN Researcher’s page is your page?

この研究者とORCID iDの連携を行いますか?
※ この処理は、研究者本人だけが実行できます。

Information User Guide FAQ News Terms of Use Attribution of KAKENHI

Powered by NII kakenhi