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HARA Kenjyu  原 賢寿

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… Alternative Names

原 賢寿  ハラ ケンジュ

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Researcher Number 10377195
External Links
Affiliation (based on the past Project Information) *help 2008: 新潟大学, 脳研究所・神経内科
2006: 新潟大学, 医歯学総合病院, 助手
2006: 新潟大学, 医歯学総合病院, 医員
2005: 新潟大学, 脳研究所, 助手
Review Section/Research Field
Principal Investigator
Neurology
Except Principal Investigator
Biological Sciences / Neurology
Keywords
Principal Investigator
連鎖解析 / 家族性多系統萎縮症 / フリードライヒ失調症 / sacsin / SCA15 / 脊髄小脳変性症
Except Principal Investigator
1本鎖DNA損傷修復 / EAOH / グアム島 / パーキンソン症候群 … More / 認知症 / タウオパチー / タウ蛋白 / 酸化ストレス / TDP-43 / アルツハイマー神経原線維変化 / 遺伝子 / パーキンソン認知症複合 / 筋萎縮性側索硬化症 / 紀伊半島 / ARSACS / DNA 3'block / DNA break repair / single strand DNA break / AOAl / ataxia / aprataxin / サクシン欠損症 / 運動失調症 / nucleophosmin / 分子病態 / アプラタキシン欠損症 / 劣性遺伝 / 脊髄小脳変性症 / 1本鎖DNA損傷 / アプラタキシン / 劣性遺伝性脊髄小脳変性症 Less
  • Research Projects

    (4 results)
  • Research Products

    (48 results)
  • Co-Researchers

    (16 People)
  •  Molecular biological study on the cause and pathogenesis of amyotrophic lateral sclerosis and parkinsonism-dementia complex of the Kii peninsula of Japan

    • Principal Investigator
      KUZUHARA Shigeki
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      National Center of Neurology and Psychiatry
      Mie University
  •  劣性遺伝性脊髄小脳変性症の分子病態の解明

    • Principal Investigator
      西澤 正豊
    • Project Period (FY)
      2006 – 2007
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas
    • Review Section
      Biological Sciences
    • Research Institution
      Niigata University
  •  劣性遺伝性脊髄小脳変性症の分子病態の解明

    • Principal Investigator
      西澤 正豊
    • Project Period (FY)
      2005
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas
    • Review Section
      Biological Sciences
    • Research Institution
      Niigata University
  •  未解明遺伝性脊髄小脳変性症の臨床・分子遺伝学的解析Principal Investigator

    • Principal Investigator
      原 賢寿
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Young Scientists (B)
    • Research Field
      Neurology
    • Research Institution
      Niigata University

All 2009 2008 2007 2006 2005 Other

All Journal Article Presentation Book

  • [Book] 中毒性疾患, 最新自律神経学(宇尾野 公義, 入來正躬 監修)2007

    • Author(s)
      葛原 茂樹
    • Total Pages
      10
    • Publisher
      新興医学出版社,東京
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Book] Huntington病, 今日の診断基準(大田 健, 奈良 信雄 編集)2007

    • Author(s)
      葛原 茂樹
    • Total Pages
      1
    • Publisher
      南江堂,東京
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Book] 精神・神経疾患画像アトラス(葛原茂樹 監修)2007

    • Author(s)
      葛原 茂樹
    • Total Pages
      167
    • Publisher
      メディカルレビュー社
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] Increased oxidative stress in patients with amyotrophic lateral sclerosis/parkinsonism-dementia comlex in the Kii Peninsula, Japan.2009

    • Author(s)
      Morimoto S, Kuzuhara S, Kokubo Y
    • Journal Title

      Mov Disord 24

      Pages: 123-126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] Increased oxidative stress in patients with amyotrophic lateral sclerosis/parkinsonism-dementia comlex in the Kii Peninsula, Japan2009

    • Author(s)
      Morimoto S, Kuzuhara S, Kokubo Y
    • Journal Title

      Mov Disord 24

      Pages: 123-126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] DP-43と神経変性疾患 紀伊半島ALS/PDCとTDP-43.2008

    • Author(s)
      葛原茂樹
    • Journal Title

      神経内科 68

      Pages: 565-570

    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] 厚生労働省特定疾患治療研究事業臨床調査個人票の集計結果からみたパーキンソン病患者の現況2008

    • Author(s)
      谷口彰, 成田有吾, 内藤寛, 葛原茂樹
    • Journal Title

      臨床神経 48

      Pages: 106-113

    • NAID

      10021187102

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] ALS患者の脳と脊髄への TDP-43蛋白の異常蓄積とTDP-43遺伝子変異の発見.2008

    • Author(s)
      葛原茂樹
    • Journal Title

      難病と在宅ケア 14

      Pages: 31-33

    • NAID

      40016323706

    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] ALS患者の脳と脊髄へのTDP-43蛋白の異常蓄積とTDP-43遺伝子変異の発見2008

    • Author(s)
      葛原茂樹
    • Journal Title

      難病と在宅ケア 14

      Pages: 31-33

    • NAID

      40016323706

    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] Mutation analyses in amyotrophic lateral sclerosis/parkinsonism-dementia complex of the Kii peninsula, Japan2008

    • Author(s)
      Tomiyama H, Kokubo Y, Sasaki R, Li Y, Imamichi Y, Funayama M, Mizuno Y, Hattori N, Kuzuhara S
    • Journal Title

      Mov Disord 23

      Pages: 2344-2348

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] 紀伊・西ニューギニアの ALS.2008

    • Author(s)
      葛原茂樹
    • Journal Title

      Clin Neurosci 26

      Pages: 292-297

    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] TDP-43と神経変性疾患 紀伊半島ALS/PDCとTDP-432008

    • Author(s)
      葛原茂樹
    • Journal Title

      神経内科 68

      Pages: 565-570

    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] LS研究の最近の進歩 : ALSとTDP-43.2008

    • Author(s)
      葛原茂樹
    • Journal Title

      臨床神経 48

      Pages: 625-633

    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] Mutation analyses in amyotrophic lateral sclerosis/parkinsonism-dementia complex of the Kii peninsula, Japan.2008

    • Author(s)
      Tomiyama H, Kokubo Y, Sasaki R, Li Y, Imamichi Y, Funayama M, Mizuno Y, Hattori N, Kuzuhara S
    • Journal Title

      Mov Disord 23

      Pages: 2344-2348

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] ALS研究の進歩:ALSとTDP-432008

    • Author(s)
      葛原茂樹
    • Journal Title

      臨床神経 48

      Pages: 625-633

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] 厚生労働省特定疾患治療研究事業臨床調査個人票の集計結果からみたパーキンソン病患者の現況.2008

    • Author(s)
      谷口彰, 成田有吾, 内藤寛, 葛原茂樹
    • Journal Title

      臨床神経学 48

      Pages: 106-113

    • NAID

      10021187102

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] 紀伊・西ニューギニアのALS2008

    • Author(s)
      葛原茂樹
    • Journal Title

      Clin Neurosci 26

      Pages: 292-297

    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] Sacsin-related ataxia with neither retinal hypermyelination nor spasticity2007

    • Author(s)
      Kenju Hara, et al.
    • Journal Title

      Movement Disorder (印刷中)

    • Data Source
      KAKENHI-PROJECT-17790575
  • [Journal Article] Multiplex families with multiple system atrophy2007

    • Author(s)
      Kenju Hara, et al.
    • Journal Title

      Archives of Neurology 64

      Pages: 545-551

    • Data Source
      KAKENHI-PROJECT-17790575
  • [Journal Article] 特集 ALS-研究と診療の進歩 紀伊ALS再訪ーALS-parkinsonism-dementia complex としての新しい概念、疫学、原因についての考察.2007

    • Author(s)
      葛原茂樹
    • Journal Title

      BRAIN and NERVE 59

      Pages: 1065-1074

    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] New mutation in the non-gigantic exon of SACS in Japanese siblings.2007

    • Author(s)
      Takado Y, Hara K, Shimohata T, Tokiguchi S, Onodera O, Nishizawa M
    • Journal Title

      Mov Disord 22

      Pages: 748-749

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18023015
  • [Journal Article] 第48回日本神経学会総会シンポジウム. 西大西洋地域の筋萎縮側索硬化症/パーキンソン痴呆複合(ALS/PDC)と関連神経変性疾患 紀伊 ALS/PDC (牟婁病)の歴史、概念、疫学.2007

    • Author(s)
      葛原茂樹
    • Journal Title

      臨床神経 47

      Pages: 962-965

    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] Sacsin-related ataxia with neither retinal hypermyelination nor spasticity2007

    • Author(s)
      Hara, K., et al.
    • Journal Title

      Movement Disorders (in press)

    • Data Source
      KAKENHI-PROJECT-18023015
  • [Journal Article] Sacsin-related ataxia with neither retinal hypermyelination nor spasticity.2007

    • Author(s)
      Hara K, Shimbo J, Nozaki H, Kikugawa K, Onodera O, Nishizawa M:
    • Journal Title

      Mov Disord 22

      Pages: 1362-1363

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18023015
  • [Journal Article] Similar topographical distribution of neurofibrillary tangles in amyotrophic lateral sclerosis and parkinsonism-dementia complex in people living in the Kii peninsula of Japan suggests a single tauopathy.2007

    • Author(s)
      Mimuro M, Kokubo Y, Kuzuhara S
    • Journal Title

      Acta Neuropathol 113

      Pages: 653-658

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] 第48回日本神経学会総会 会長講演. 紀伊半島の牟婁(むろ)病(筋萎縮性側索硬化症・パーキンソン・認知症複合)2007

    • Author(s)
      葛原茂樹
    • Journal Title

      臨床神経 47

      Pages: 695-702

    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] Similar topographical distribution of neurofibrillary tangles in amyotrophic lateral sclerosis and parkinsonism dementia complex in people living in the Kii peninsula of Japan suggests a single tauopathy2007

    • Author(s)
      Mimuro M, Kokubo Y, Kuzuhara S
    • Journal Title

      Acta Neuropathol 113

      Pages: 653-658

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] 第48回日本神経学会総会 シンポジウム 西大西洋地域の筋萎縮性側索硬化症/パーキンソン・認知症複合(ALS/PDC)と関連神経変性疾患.紀伊ALS/PDCの分子遺伝学的.2007

    • Author(s)
      原 賢寿、桑野良三、宮下哲典、小久保康昌、佐々木良元、中原安雄、後藤 順、西澤正豊、葛原茂樹、辻 省次
    • Journal Title

      臨床神経 47

      Pages: 974-976

    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] Pressure ulcers in ALS patients on admission at a university hospital in Japan2007

    • Author(s)
      Hayashi T, Narita Y, Okugawa N, Hamaguchi E, Shibahara M, Kuzuhara S
    • Journal Title

      Amyotrophic Lateral Sclerosis 8

      Pages: 310-313

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] Protein-bound crotonaldehyde accumulates in the spinal cord of superoxide dismutase-1 mutation-associated familial amyotrophic lateral sclerosis and its transgenic mouse model2007

    • Author(s)
      Shibata N, S, Kokubo Y, Kuzuhara S, et. al.
    • Journal Title

      Neuropathology 27

      Pages: 49-61

    • NAID

      10021235172

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] 多系統萎縮症の分子遺伝学(多施設共同研究体制 : JAMSAC)2006

    • Author(s)
      百瀬義雄, 原 賢寿, 中原康雄, 後藤 順, 辻 省次
    • Journal Title

      神経研究の進歩 50

      Pages: 421-427

    • Data Source
      KAKENHI-PROJECT-17790575
  • [Journal Article] 家族性MSAとMSAの分子遺伝学2006

    • Author(s)
      原 賢寿, 百瀬義雄
    • Journal Title

      CLINICAL NEUROSCIENCE 24

      Pages: 1028-1031

    • Data Source
      KAKENHI-PROJECT-17790575
  • [Journal Article] Sacsin-related autosomal recessive ataxia witnout prominent retinal myelinated Fibers in Japan.2005

    • Author(s)
      Hara K
    • Journal Title

      Mov Disord 20

      Pages: 380-382

    • Data Source
      KAKENHI-PROJECT-17025018
  • [Journal Article] TRPM7 is not associated with amyotrophic lateral sclerosis-parkinsonism dementia complex in the Kii peninsula of Japan

    • Author(s)
      Hara K, Kokubo Y, Ishiura H, Fukuda Y, Miyashita A, Kuwano R, Sasaki R, Goto J, Nishizawa M, Kuzuhara S, Tsuji S
    • Journal Title

      Am J Med Genet Part B (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Journal Article] TRPM7 is not associated with amyotrophic lateral sclerosis-parkinsonism dementia complex in the Kii peninsula of Japan.

    • Author(s)
      Hara K, Kokubo Y, Ishiura H, Fukuda Y, Miyashita A, Kuwano R, Sasaki R, Goto J, Nishizawa M, Kuzuhara S, Tsuji S:
    • Journal Title

      Am J Med Genet Part B (in press)

      Pages: 0-0

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] 「紀伊半島に多発するALS」風土病としてALS研究から、日本と世界のALSの原因解明へ2008

    • Author(s)
      葛原茂樹
    • Organizer
      日本ALS協会群馬県支部総会
    • Place of Presentation
      群馬県社会福祉総合センター
    • Year and Date
      2008-05-31
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] 紀伊半島に多発するALS」風土病としてALS研究から、日本と世界のALS の原因解明へ2008

    • Author(s)
      葛原茂樹
    • Organizer
      日本ALS協会群馬県支部総会
    • Year and Date
      2008-05-31
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] Immunohistochemical study on phosphorylated TDP-43 protein in amyotrophic lateral sclerosis/parkinsonism-dementia complex of the Kii peninsula of Japan2008

    • Author(s)
      Kokubo Y, Endo M, Arai T, Akiyama H, Hasegawa M, Kuzuhara S
    • Organizer
      6th International Conference on Frontotemporal Dementias
    • Place of Presentation
      Rotterdam, The Netherlands
    • Year and Date
      2008-09-05
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] Immunohistochemical study on phosphorylated TDP-43 protein in amyotrophic lateral sclerosis/parkinsonism-dementia complex of the Kii peninsula of Japan.2008

    • Author(s)
      Kokubo Y, Endo M, ArainT, Akiyama H, Hasegawa M, Kuzuhara S
    • Organizer
      6th International Conference on Frontotemporal Dementias Rotterdam
    • Place of Presentation
      The Netherlands
    • Year and Date
      2008-09-05
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] 紀伊半島ALS/parkinsonism-dementia complexにおけるTDP-43蓄積2007

    • Author(s)
      葛原 茂樹
    • Organizer
      第48回日本神経病理学会総会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] Duration of career as a coordinator and thought of attendance at a bad-news telling session for ALS patients in Japan.2007

    • Author(s)
      Yugo Narita, Michiko Nakai, Shigeki Kuzuhara
    • Organizer
      18th International Symposium on ALS/MND
    • Place of Presentation
      Toronto
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] 葛原茂樹: 紀伊ALS/PDCの歴史,概念,疫学2007

    • Author(s)
      葛原 茂樹
    • Organizer
      第48回日本神経学会総会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] Immunohistochemical study on TDP-43 protein in amyotrophic lateral sclerosis/parkinsonism-dementia complex of the Kii peninsula of Japan.2007

    • Author(s)
      Kokubo Y, Saito Y, Murayama S, Kuzuhara S
    • Organizer
      第26回日本認知症学会
    • Place of Presentation
      大阪市 大阪国際会議場
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] 紀伊半島の牟婁病(筋萎縮性側索硬化症/パーキンソン認知症複合 : ALS/PDC)2007

    • Author(s)
      3.葛原茂樹
    • Organizer
      第48回日本神経学会総会
    • Place of Presentation
      名古屋
    • Year and Date
      2007-05-16
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] Immunohistochemical study on tau isoform in amyotrophic lateral sclerosis/parkinsonism-dementia complex of the Kii peninsula of Japan.2007

    • Author(s)
      Kokubo Y,Saito Y, Murayama S, Kuzuhara S
    • Organizer
      18^<th> International Symposium on ALS/MND
    • Place of Presentation
      Toronto, Canada
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] I mmunohistochemical study on tau isoform in amyotronhic lateral sclerosis/parkinsonism-dementia complex of the Kii peninsula of Japan2007

    • Author(s)
      Y, Kokubo, Y, Saito, S, Murayama, S, Kuzuhara
    • Organizer
      18th International Symposium on ALS/MND
    • Place of Presentation
      Toronto
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] 第48回日本神経学会総会シンポジウム. 西大西洋地域の筋萎縮側索硬化症/パーキンソン痴呆複合(ALS/PDC)と関連神経変性疾患紀伊ALS/PDC(牟婁病)の歴史2007

    • Author(s)
      葛原茂樹
    • Organizer
      第48回日本神経学会総会,
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-19390239
  • [Presentation] 紀伊半島ALS/parkinsonism-dementia complexにおけるTDP-43蓄積2007

    • Author(s)
      葛原茂樹
    • Organizer
      第48回日本神経病理学会総会
    • Place of Presentation
      船堀東京
    • Data Source
      KAKENHI-PROJECT-19390239
  • 1.  西澤 正豊 (80198457)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 2 results
  • 2.  KUZUHARA Shigeki (70111383)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 40 results
  • 3.  KOKUBO Yasumasa (60263000)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 15 results
  • 4.  SASAKI Ryogen (60303723)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 5 results
  • 5.  KUWANO Ryouzou (20111734)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 3 results
  • 6.  TOMIYAMA Hiroyuki (20515069)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 2 results
  • 7.  HATTORI Nobutaka (80218510)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 2 results
  • 8.  TSUJI Syouji (70150612)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 3 results
  • 9.  MURAYAMA Shigeo (50183653)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 3 results
  • 10.  SAITO Yuuko (60344066)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 11.  HASEGAWA Nmasato (10251232)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 2 results
  • 12.  IWATSUBO Takeshi (50223409)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 13.  伊藤 伸朗 (10362344)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 3 results
  • 14.  MORIMOTO Satoru
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 2 results
  • 15.  AKATSUKA Naomi
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 16.  齊藤 祐子
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 3 results

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