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Tanaka Fumiaki  田中 章景

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… Alternative Names

TANAKA Fumiaki  田中 章景

国中 章景  タナカ フミアキ

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Researcher Number 30378012
Other IDs
Affiliation (Current) 2025: 横浜市立大学, 医学研究科, 教授
Affiliation (based on the past Project Information) *help 2015 – 2024: 横浜市立大学, 医学研究科, 教授
2015: 横浜市立大学, 医学研究科神経内科, 教授
2011 – 2015: 横浜市立大学, 医学(系)研究科(研究院), 教授
2014: 名古屋大学, 大学院医学系研究科, 准教授
2013: 横浜市立大学, 医学系研究科, 教授 … More
2012 – 2013: 横浜市立大学, 医学研究科, 教授
2010 – 2011: 名古屋大学, 医学系研究科, 准教授
2010: 名古屋大学, 医学系研究科, 教授
2007 – 2010: Nagoya University, 大学院・医学系研究科, 准教授
2007: Nagoya University, Graduate School of Medicine, Assistant Professor
2005 – 2006: 名古屋大学, 大学院医学系研究科, COE特任助教授
2005: Nagoya University, Graduate School of Medicine, COE Designated Associate Professor, 大学院・医学系研究科, COE特任助教授
2004: 名古屋大学, 大学院・医学系研究科, COE助教授(研究員) Less
Review Section/Research Field
Principal Investigator
Neurology / Basic Section 52020:Neurology-related / Biological Sciences
Except Principal Investigator
Neurology / Basic Section 52020:Neurology-related / Basic Section 51030:Pathophysiologic neuroscience-related / Basic Section 59010:Rehabilitation science-related / Nerve anatomy/Neuropathology / Neurochemistry/Neuropharmacology / Biological Sciences
Keywords
Principal Investigator
ALS / 運動ニューロン / オートファジー / LOTUS / siRNA / ポリグルタミン病 / 遺伝子発現解析 / dynactin1 / 遺伝子治療 / 病態解析 … More / リピート病 / RAN translation / RFC1 / FISH / 病理学的解析 / RNA foci / CANVAS / PIR-B / Nogo / autophagy / gene expression analysis / motor neuron / cDNAマイクロアレイ / 核内封入体 / RNA結合タンパク / PCBP / 神経科学 / 脳神経疾患 / UBQLN2 / マウスモデル / 神経変性 / 孤発性ALS / 線虫モデル / dynactin-1 / 家族性ALS / 病因遺伝子 / 遺伝子診断 / エクソーム解析 / 次世代シーケンサー / 封入体 / dynactinl / 疾患モデル / 線虫 / cyclin C … More
Except Principal Investigator
球脊髄性筋萎縮症 / 神経変性疾患 / ポリグルタミン病 / 脊髄小脳変性症 / アンドロゲン受容体 / ポリグルタミン / 筋萎縮性側索硬化症 / CAGリピート / 分子シャペロン / ALS / LOTUS / トランスジェニックマウス / 核内封入体 / 運動ニューロン / ミクログリア / パーキンソン病 / spinal and bulbar muscular atrophy / バイオマーカー / 多発性硬化症 / Nogo / Dorfin / 神経変性 / GGA / 17-AAG / 転写障害 / バーチャルリアリティー / リハビリテーション / microglia / 軸索変性 / Nogo受容体 / 神経核内封入体病 / 認知症 / GGCリピート / NOTCH2NLC / 神経炎症 / マクロファージ / 単球系細胞 / UBQLN2 / SALS / FTLD / 脳神経疾患 / dynactin1 / polyglutamine / p97 / VCP / 血液 / 脳脊髄液 / multiple sclerosis / biomarker / カルシウムチャネル / 白質脳症 / 皮膚生検 / NIID / アミロイド / JNK / 細胞周期 / 連鎖解析 / TDP-43 / ユビキチン-プロテアソーム / HSP / 軸索輸送 / 17-DMAG / プロテアソーム / ユビキチン / TGF-β / シャペロン / 細胞モデル / aphasia / disconnectome / 原発性進行性失語症 / 失語症 / RFC1 / CANVAS / RNA結合タンパク質 / 非膜オルガネラ / 全身炎症 / アミロイドβ / タウ / RIPK1 / amyloid-beta / tau / てんかん / 自己免疫性脳炎 / 辺縁系脳炎 / 扁桃体腫大 / 側頭葉てんかん / CACNA1G / 光遺伝学 / 疾患修飾療法 / 書字障害 / VR / 上肢巧緻運動障害 / neuroinflammation / マイクログリア / 神経核内封入体病(NIID) / トリプレットリピート / リピート病 / DWI / DDX17 / DDX5 / Dead box RNA helicase / 孤発性ALS / DEAD box RNA helicase / DEAD box protein / IL-19 / アストロサイト / コンディショナルノックアウト / ノックアウトマウス / マウスモデル / 脊髄小脳失調症 / calcium channel / mouse model / spinocerebellar ataxia / 神経科学 / 臨床 / 脳・神経 / MRI / 認知機能 / 表情 / 情動 / 記憶 / amimia / Parkinson / 仮面様顔貌 / 活性酸素 / 尿酸トランスポーター / 酸化ストレス / 尿酸 / 多系統萎縮症 / MATR3 / TDP43 / matrin3 / 診断マーカー / 髄液 / MRM法 / ELISA法 / 神経障害 / 動作解析 / 3次元解析 / 3次元動作解析 / 小脳性運動失調 / 運動解析 / エクソーム / exome / muscle weakness / muscle atrophy / neurotrophic factor / CAG repeat / androgen receptor / transgenic mouse / hepatocyte erowth factor / ダブルトランスジェニックマウス / ドランスジェニックマウス / 筋力低下 / 筋萎縮 / 神経栄養因子 / 肝細胞増殖因子 / heat shock protein / ubiquitin-proteasome / molecular chaperone / gene expression profiles / LHRH analog / amyotrophic lateral sclerosis / motor neuron / ユビキチンリガーゼ / ヒストン脱アセチル化 / 臨床試験 / 遺伝子発現解析 / LHRHアナログ / 二次進行型 / 再発寛解型 / カルシウムシグナリング / ターゲットキャプチャー / カスタムキャプチャー / 次世代シーケンサー / ゲノム解析 / 次世代シークエンサー / AAVベクター / Dicer / miR-196a / 運動ニューロン病 / CELF2 / miRNA / アンドロゲンレセプター / セロトニン受容体 / 神経ペプチド / naratriptan / CGRP1 / マイクロアレイ / サイクリン依存性キナーゼ / 多発神経炎 / 家族性アミロイドポリニューロパチー / トランスサイレチン / calcitonin-related polypeptide(CGRP1) / calcitonin / calcitonin/calcitonin-related polypeptide(CGRP1) / セロトニン受容体アゴニスト / ユビチキン / )球脊髄性筋萎縮症 / オートファジー / ユビキチン-プロテアゾーム系 / ユビキチンープロテアソーム系 / Hsp90阻害剤 / ユビキチン-プロテアソーム系 / ペオニ抽出物 / NIHID / 翻訳後修飾 / 核タンパク質 / プロテオーム / ジスルフィド結合 / ユビキチン化 / タンパク質凝集 / 変異SOD1 / 筋萎縮性側索硬化症(ALS) / 熱ショック蛋白質 / ユビキチン・プロテアソーム / リュープロレリン / ユビキチンープロテアソーム / 神経分子病態学 / ニューロフィラメント / dnactin1 / モーター蛋白質 / CHIP / 脊髄小脳失調症(SCA) / 球脊髄性筋萎縮症(SBMA) Less
  • Research Projects

    (50 results)
  • Research Products

    (457 results)
  • Co-Researchers

    (61 People)
  •  Development of Gene Therapy Targeting LOTUS for ALSPrincipal Investigator

    • Principal Investigator
      田中 章景
    • Project Period (FY)
      2024 – 2026
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  Development of a novel biomarker for ALS based on LOTUS, the functional molecule for neural regeneration

    • Principal Investigator
      高橋 慶太
    • Project Period (FY)
      2024 – 2026
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  新規動物モデル、iPS細胞モデルを用いたCANVASの病態解明

    • Principal Investigator
      土井 宏
    • Project Period (FY)
      2024 – 2026
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  脊髄小脳変性症に対する没入型VRを用いた実用性の高いリハビリテーション法の開発

    • Principal Investigator
      上田 直久
    • Project Period (FY)
      2024 – 2026
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 59010:Rehabilitation science-related
    • Research Institution
      Yokohama City University
  •  Pathophysiological Investigation and Symptom Prediction Modeling of Language Network Disorders in Aphasia using Disconnectome Analysis

    • Principal Investigator
      東山 雄一
    • Project Period (FY)
      2024 – 2026
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 59010:Rehabilitation science-related
    • Research Institution
      Yokohama City University
  •  Elucidation of the pathogenesis of neuronal intranuclear inclusion disease and development of radical treatment

    • Principal Investigator
      曽根 淳
    • Project Period (FY)
      2023 – 2027
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Review Section
      Basic Section 51030:Pathophysiologic neuroscience-related
    • Research Institution
      Aichi Medical University
  •  UBQLN2・HSC70/HSPA1複合体の機能低下に着目した筋萎縮性側索硬化症の病態解明

    • Principal Investigator
      田中 健一
    • Project Period (FY)
      2023 – 2025
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  Analysis of pathological dynamics of membrane-less organelles in SALS

    • Principal Investigator
      多田 美紀子
    • Project Period (FY)
      2022 – 2024
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 51030:Pathophysiologic neuroscience-related
    • Research Institution
      Yokohama City University
  •  Development of disease-modifying therapy for spinocerebellar ataxia type 42 and elucidation of pathophysiological basis using optogenetic methods

    • Principal Investigator
      DOI Hiroshi
    • Project Period (FY)
      2021 – 2023
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 51030:Pathophysiologic neuroscience-related
    • Research Institution
      Yokohama City University
  •  扁桃体腫大を伴う側頭葉てんかんの病態背景の解明と新規治療法の開発

    • Principal Investigator
      國井 美紗子
    • Project Period (FY)
      2021 – 2025
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  Elucidation of amyloid-tau association and development of new therapeutic methods based on analysis of microglia RIPK1

    • Principal Investigator
      KATSUMOTO Atsuko
    • Project Period (FY)
      2021 – 2023
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  Establishment of a pathophysiological analysis model for novel intronic repeat disease CANVASPrincipal Investigator

    • Principal Investigator
      Tanaka Fumiaki
    • Project Period (FY)
      2021 – 2023
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  Elucidation of the mechanism of neurodegenerative disease progression by systemic inflammation

    • Principal Investigator
      Takeuchi Hideyuki
    • Project Period (FY)
      2021 – 2023
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  Development of innovative treatment for multiple sclerosis based on control of neurodegeneration and inflammation by applying function of LOTUS

    • Principal Investigator
      TAKAHASHI Keita
    • Project Period (FY)
      2020 – 2022
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 51030:Pathophysiologic neuroscience-related
    • Research Institution
      Yokohama City University
  •  Development of novel motor training in Parkinson's disease using VR and motor learning transfer

    • Principal Investigator
      Ueda Naohisa
    • Project Period (FY)
      2020 – 2023
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 59010:Rehabilitation science-related
    • Research Institution
      Yokohama City University
  •  DEAD box RNA helicases are involved in sporadic ALS pathology

    • Principal Investigator
      TADA Mikiko
    • Project Period (FY)
      2019 – 2021
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 51030:Pathophysiologic neuroscience-related
    • Research Institution
      Yokohama City University
  •  Genetical and pathological study of neuronal intranuclear inclusion disease

    • Principal Investigator
      Sone Jun
    • Project Period (FY)
      2019 – 2021
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Aichi Medical University
      National Hospital Organization Suzuka National Hospital
  •  Elucidation of pathophysiology and development of treatment for spinocerebellar ataxia using a novel mouse model

    • Principal Investigator
      DOI Hiroshi
    • Project Period (FY)
      2018 – 2020
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  Analysis of UBQLN2 based on loss of function model

    • Principal Investigator
      TANAKA Kenichi
    • Project Period (FY)
      2018 – 2020
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  Development of novel therapeutic strategy against neurodegenerative diseases by modulation of monocyte-lineage cell

    • Principal Investigator
      TAKEUCHI Hideyuki
    • Project Period (FY)
      2018 – 2020
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  Development of ALS therapy targeting LOTUS, a functional molecule for neuronal regenerationPrincipal Investigator

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2018 – 2020
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Yokohama City University
  •  Study of pathogenesis caused by hypouricemia in multiple system atrophy

    • Principal Investigator
      KOYANO Shigeru
    • Project Period (FY)
      2017 – 2019
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Yokohama City University
  •  Development of objective evaluation method of cerebellar ataxia using 3D motion analysis system

    • Principal Investigator
      Ueda Naohisa
    • Project Period (FY)
      2016 – 2018
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Yokohama City University
  •  Neural substrates of masked-face in Parkinson disease: A quantitative analysis of facial expression.

    • Principal Investigator
      Yuichi HIGASHIYAMA
    • Project Period (FY)
      2016 – 2017
    • Research Category
      Grant-in-Aid for Young Scientists (B)
    • Research Field
      Neurology
    • Research Institution
      Yokohama City University
  •  Analysis of genetic back ground and pathomechanism of spinocerebellar degeneration

    • Principal Investigator
      DOI Hiroshi
    • Project Period (FY)
      2015 – 2017
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Yokohama City University
  •  Development of blood biomarker for neuronal injury

    • Principal Investigator
      TAKEI Kohtaro
    • Project Period (FY)
      2015 – 2016
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurochemistry/Neuropharmacology
    • Research Institution
      Yokohama City University
  •  Analysis of polyglutamine aggregation protein in ALS/FTLD

    • Principal Investigator
      TADA Mikiko
    • Project Period (FY)
      2015 – 2016
    • Research Category
      Grant-in-Aid for Young Scientists (B)
    • Research Field
      Nerve anatomy/Neuropathology
    • Research Institution
      Yokohama City University
  •  Calcium-signaling abnormality of polyglutamine diseases

    • Principal Investigator
      KOYANO Shigeru
    • Project Period (FY)
      2014 – 2016
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Yokohama City University
  •  Elucidation of pathogeneis and development of a new biomarker associated with LOTUS in multiple sclerosis

    • Principal Investigator
      SUZUKI Yume
    • Project Period (FY)
      2014 – 2015
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Yokohama City University
  •  Analysis of RNA binding proteins in polyglutamine diseasePrincipal Investigator

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2014 – 2015
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Yokohama City University
  •  Integrated research of polyglutamine disease and ALS/FTLD by analysis of UBQLN2Principal Investigator

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2013 – 2015
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Yokohama City University
  •  Establishment of diagnosis method and analysis of genetic background of adult leukoencephalopathy patients with desktop next-generation sequencer

    • Principal Investigator
      Ueda Naohisa
    • Project Period (FY)
      2013 – 2015
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Yokohama City University
  •  Identification of NIID causative gene with next generation sequencer

    • Principal Investigator
      SONE Jun
    • Project Period (FY)
      2012 – 2014
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of therapy targeting dysregulation of cell cycle and JNK pathway in polyglutamine diseases

    • Principal Investigator
      KATSUNO MASAHISA
    • Project Period (FY)
      2011 – 2013
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Novel therapeutic approaches using the delivery of specific miRNAs for polyglutamine diseases

    • Principal Investigator
      ADACHI Hiroaki
    • Project Period (FY)
      2011 – 2013
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Exploration of disease-related genes based on personal genome analysis and elucidation of pathogenesis in ALSPrincipal Investigator

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2010 – 2014
    • Research Category
      Grant-in-Aid for Scientific Research on Innovative Areas (Research in a proposed research area)
    • Review Section
      Biological Sciences
    • Research Institution
      Yokohama City University
      Nagoya University
  •  Elucidation of pathogenesis and therapy development of sporadic ALS by disease modelPrincipal Investigator

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2010 – 2012
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Yokohama City University
      Nagoya University
  •  Development of Molecular Targeted Disease Modifying Therapy for Polyglutamine Diseases

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2009 – 2013
    • Research Category
      Grant-in-Aid for Scientific Research (S)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Clarifying the mechanisms of amyloid deposition in familial amyloid polyneuropathy and its application to therapy

    • Principal Investigator
      KOIKE Huaruki
    • Project Period (FY)
      2009 – 2011
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  孤発性ALSのオートファジー機能解明と新規疾患モデルの確立Principal Investigator

    • Principal Investigator
      田中 章景
    • Project Period (FY)
      2009
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Therapeutic strategy for polyglutamine-mediated motor neuron disease via molecular chaperone-ubiquitin proteasome system

    • Principal Investigator
      ADACHI Hiroaki
    • Project Period (FY)
      2008 – 2010
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Pathogenesis-based therapy development for polyglutamine diseases

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Scientific Research (A)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of animal model for sporadic ALSPrincipal Investigator

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Research on the molecular pathogenetic mechanism of tissue-specific toxicity mediated by ALS-linked mutant SOD1

    • Principal Investigator
      NIWA Jun-ichi
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Aichi Medical University
  •  エオジン好性核内封入体(NIHID)の原因遺伝子の探索・同定Principal Investigator

    • Principal Investigator
      田中 章景, KOIKE Haruki
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of therapies in polyglutamine diseases using hepatocyte growth factor (HGF)

    • Principal Investigator
      ADACHI Hiroaki
    • Project Period (FY)
      2006 – 2007
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of pathogenesis-based therapy for polyglutamine diseases

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2005 – 2009
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas
    • Review Section
      Biological Sciences
    • Research Institution
      Nagoya University
  •  Treatment of polyglutamine disease using small molecular compound

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Scientific Research (A)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Exploration of Target Molecules Related to Pathogenesis and Development of Therapy for Sporadic ALSPrincipal Investigator

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of low-molecular-weight compound therapy for polyglutamine diseases

    • Principal Investigator
      DOYU Manabu
    • Project Period (FY)
      2004 – 2005
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University

All 2024 2023 2022 2021 2020 2019 2018 2017 2016 2015 2014 2013 2012 2011 2010 2009 2008 2007 2006 2005 2004 Other

All Journal Article Presentation Book Other

  • [Book] 前頭側頭葉変性症療養の手引き 「前頭側頭葉変性症の経過」2017

    • Author(s)
      土井 宏、田中章景
    • Total Pages
      70
    • Publisher
      平成28年度厚生労働科学研究費補助金 難治性疾患等政策研究事業(難治性疾患政策研究事業)「神経変性疾患領域における基盤的調査研究」班
    • Data Source
      KAKENHI-PROJECT-15K09344
  • [Book] 神経内科Clinical Question & Pearls 認知症2017

    • Author(s)
      多田美紀子、田中章景
    • Publisher
      中外医学社
    • Data Source
      KAKENHI-PROJECT-15K18367
  • [Book] Clinical features and Molecular Mechanisms of spinal and bulbar muscular atrophy (SBMA).(Shamim I. Ahmad ed., In Diseases of DNA Repair.)2009

    • Author(s)
      Katsuno, M., Banno, H., Suzuki, K., Adachi, H., Tanaka, F., Sobue, G.
    • Publisher
      Landes Bioscience
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Long-read sequencing revealing intragenic deletions in exome-negative spastic paraplegias2023

    • Author(s)
      Fukuda H., Mizuguchi T., Doi H., Kameyama S., Kunii M., Joki H., Takahashi T., Komiya H., Sasaki M., Miyaji Y., Ohori S., Koshimizu E., Uchiyama Y., Tsuchida N., Fujita A., Hamanaka K., Misawa K., Miyatake S., Tanaka F. and Matsumoto N.
    • Journal Title

      J Hum Genet

      Volume: 68 Issue: 10 Pages: 689-697

    • DOI

      10.1038/s10038-023-01170-0

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23K18278, KAKENHI-PROJECT-22K15901, KAKENHI-PROJECT-23K07229, KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-23K27520, KAKENHI-PROJECT-23K27568
  • [Journal Article] 【運動失調症の病態と治療】Cerebellar ataxia with neuropathy and vestibular areflexia syndrome(CANVAS)2023

    • Author(s)
      土井 宏, 田中 章景
    • Journal Title

      脳神経内科

      Volume: 99 Pages: 518-526

    • Data Source
      KAKENHI-PROJECT-21K07440
  • [Journal Article] Lateral olfactory tract usher substance (LOTUS), an endogenous Nogo receptor antagonist, ameliorates disease progression in amyotrophic lateral sclerosis model mice2023

    • Author(s)
      Ikeda Takuya、Takahashi Keita、Higashi Minatsu、Komiya Hiroyasu、Asano Tetsuya、Ogasawara Akihiro、Kubota Shun、Hashiguchi Shunta、Kunii Misako、Tanaka Kenichi、Tada Mikiko、Doi Hiroshi、Takeuchi Hideyuki、Takei Kohtaro、Tanaka Fumiaki
    • Journal Title

      Cell Death Discovery

      Volume: 9 Issue: 1 Pages: 454-454

    • DOI

      10.1038/s41420-023-01758-7

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-21K07465
  • [Journal Article] 神経難病 フリードライヒ運動失調症(Friedreich病)2023

    • Author(s)
      橋口 俊太, 田中 章景
    • Journal Title

      Brain Nursing

      Volume: 2023夏季増刊 Pages: 219-221

    • Data Source
      KAKENHI-PROJECT-21K07440
  • [Journal Article] Cerebellar ataxia with neuropathy and vestibular areflexia syndrome (CANVAS)2023

    • Author(s)
      土井宏、田中章景
    • Journal Title

      脳神経内科

      Volume: 99 Pages: 518-526

    • Data Source
      KAKENHI-PROJECT-21K07298
  • [Journal Article] Reduced likelihood of the Poggendorff illusion in cerebellar strokes: a clinical and neuroimaging study2023

    • Author(s)
      Higashiyama Yuichi、Kuroki Miho、Kudo Yosuke、Hamada Tomoya、Morihara Keisuke、Saito Asami、Miyaji Yosuke、Kimura Katsuo、Joki Hideto、Kishida Hitaru、Doi Hiroshi、Ueda Naohisa、Takeuchi Hideyuki、Johkura Ken、Tanaka Fumiaki
    • Journal Title

      Brain Communications

      Volume: 5 Issue: 2

    • DOI

      10.1093/braincomms/fcad053

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-22K15714, KAKENHI-PROJECT-21K07298
  • [Journal Article] RNA Foci in Two bi‐Allelic RFC1 Expansion Carriers2023

    • Author(s)
      Wada Taishi、Doi Hiroshi, et al.
    • Journal Title

      Annals of Neurology

      Volume: 95 Issue: 3 Pages: 607-613

    • DOI

      10.1002/ana.26848

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-21K07440, KAKENHI-PROJECT-22K15041, KAKENHI-ORGANIZER-21H05158, KAKENHI-PLANNED-21H05159, KAKENHI-PROJECT-21H02405, KAKENHI-PROJECT-23K27520
  • [Journal Article] Association of biallelic RFC1 expansion with early‐onset Parkinson's disease2023

    • Author(s)
      Ylikotila Pauli、Sipila Jussi、Alapirtti Tiina、Ahmasalo Riitta、Koshimizu Eriko、Miyatake Satoko、Hurme‐Niiranen Anri、Siitonen Ari、Doi Hiroshi、Tanaka Fumiaki、Matsumoto Naomichi、Majamaa Kari、Kytovuori Laura
    • Journal Title

      European Journal of Neurology

      Volume: 30 Issue: 5 Pages: 1256-1261

    • DOI

      10.1111/ene.15717

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-21K07440, KAKENHI-PROJECT-23K27520
  • [Journal Article] Parallel Appearance of Polyglutamine and Transactivation-Responsive DNA-Binding Protein 43 and Their Complementary Subcellular Localization in Brains of Patients With Spinocerebellar Ataxia Type 2.2022

    • Author(s)
      Koyano S, Yagishita S, Tada M, Doi H, Uchihara T, Tanaka F
    • Journal Title

      JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY

      Volume: - Issue: 7 Pages: 535-544

    • DOI

      10.1093/jnen/nlac032

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17H03555, KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-21K07440
  • [Journal Article] Rapid and comprehensive diagnostic method for repeat expansion diseases using nanopore sequencing2022

    • Author(s)
      Satoko Miyatake, Eriko Koshimizu, Atsushi Fujita, Hiroshi Doi, et al.
    • Journal Title

      npj Genomic Medicine

      Volume: 7 Issue: 1 Pages: 62-62

    • DOI

      10.1038/s41525-022-00331-y

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-21K07440, KAKENHI-PROJECT-21K07869, KAKENHI-PROJECT-20K07907, KAKENHI-PROJECT-20K08164, KAKENHI-PROJECT-20K17936
  • [Journal Article] Anti-inflammatory effects of siponimod on astrocytes2022

    • Author(s)
      Akihiro Ogasawara, ・・Hiroshi Doi, Fumiaki Tanaka
    • Journal Title

      Neuroscience Research

      Volume: 184 Pages: 38-46

    • DOI

      10.1016/j.neures.2022.08.003

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-21K07465
  • [Journal Article] Biallelic expansion in RFC1 as a rare cause of Parkinson’s disease2022

    • Author(s)
      Kytovuori Laura、Sipila Jussi、Doi Hiroshi、Hurme-Niiranen Anri、Siitonen Ari、Koshimizu Eriko、Miyatake Satoko、Matsumoto Naomichi、Tanaka Fumiaki、Majamaa Kari
    • Journal Title

      npj Parkinson's Disease

      Volume: 8 Issue: 1 Pages: 6-6

    • DOI

      10.1038/s41531-021-00275-7

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-20K07907, KAKENHI-PROJECT-21K07298
  • [Journal Article] Repeat conformation heterogeneity in cerebellar ataxia, neuropathy, vestibular areflexia syndrome2022

    • Author(s)
      Miyatake S, Yoshida K, Koshimizu E, others, Miyake N, Shimohata T, Tanaka F, Mizuguchi T, Matsumoto N.
    • Journal Title

      Brain

      Volume: 145 Issue: 3 Pages: 1139-1150

    • DOI

      10.1093/brain/awab363

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19H03621, KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-21K07440, KAKENHI-PROJECT-20K07907, KAKENHI-PROJECT-20K08164, KAKENHI-PROJECT-23K24308
  • [Journal Article] Inhibition of Crmp1 phosphorylation at Ser522 ameliorates motor function and neuronal pathology in amyotrophic lateral sclerosis model mice2022

    • Author(s)
      Asano Tetsuya、Nakamura Haruko、Kawamoto Yuko、Tada Mikiko、Kimura Yayoi、Takano Hiroshi、Yao Ryoji、Saito Hiroya、Ikeda Takuya、Komiya Hiroyasu、Kubota Shun、Hashiguchi Shunta、Takahashi Keita、Kunii Misako、Tanaka Kenichi、Goshima Yoshio、Nakamura Fumio、Takeuchi Hideyuki、Doi Hiroshi、Tanaka Fumiaki
    • Journal Title

      eneuro

      Volume: - Issue: 3 Pages: 0133-22

    • DOI

      10.1523/eneuro.0133-22.2022

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-21K07419, KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-21K07465, KAKENHI-PROJECT-18K15457
  • [Journal Article] Phosphorylated CRMP1, axon guidance protein, is a component of spheroids and is involved in axonal pathology in amyotrophic lateral sclerosis2022

    • Author(s)
      Yuko, Kawamoto・・・Hiroshi Doi, et al.
    • Journal Title

      Frontiers in Neurology

      Volume: 13 Pages: 994676-994676

    • DOI

      10.3389/fneur.2022.994676

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-21K07465, KAKENHI-PROJECT-18K15457
  • [Journal Article] Father-to-offspring transmission of extremely long NOTCH2NLC repeat expansions with contractions: genetic and epigenetic profiling with long-read sequencing2021

    • Author(s)
      Fukuda H, Yamaguchi D, Nyquist K, Yabuki Y, Miyatake S, Uchiyama Y, Hamanaka K, Saida K, Koshimizu E, Tsuchida N, Fujita A, Mitsuhashi S, Ohbo K, Satake Y, Sone J, Doi H, Morihara K, Okamoto T, Takahashi Y, Wenger AM, Shioda N, Tanaka F, Matsumoto N, Mizuguchi T
    • Journal Title

      Clin Epigenetics

      Volume: 13 Issue: 1 Pages: 204-204

    • DOI

      10.1186/s13148-021-01192-5

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-19K07977, KAKENHI-PROJECT-20K21400, KAKENHI-PUBLICLY-20H05370, KAKENHI-PUBLICLY-21H00207, KAKENHI-PROJECT-19H03577, KAKENHI-PROJECT-20H03393, KAKENHI-PROJECT-19K07250, KAKENHI-PROJECT-20K07907, KAKENHI-PROJECT-20K08164, KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-19KK0183
  • [Journal Article] Therapeutic efficacy of heparin and direct factor Xa inhibitors in cancer-associated cryptogenic ischemic stroke with venous thromboembolism2021

    • Author(s)
      Yamaura Genpei、Ito Takeshi、Miyaji Yosuke、Ueda Naohisa、Nakae Yoshiharu、Momoo Takayuki、Nakano Tatsu、Johmura Yuji、Higashiyama Yuichi、Joki Hideto、Doi Hiroshi、Takeuchi Hideyuki、Takahashi Tatsuya、Koyano Shigeru、Yamaguchi Shigeki、Yokoyama Mutsumi、Tanaka Fumiaki
    • Journal Title

      Thrombosis Research

      Volume: 206 Pages: 99-103

    • DOI

      10.1016/j.thromres.2021.08.016

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21K07298
  • [Journal Article] Case Report: Severe Osteoporosis and Preventive Therapy in RNA Polymerase III-Related Leukodystrophy2021

    • Author(s)
      Furukawa Soma、Kunii Misako、Doi Hiroshi、Kondo Naohide、Ogura Aya、Hirabuki Koichi、Itoh Takayuki、Matsumoto Naomichi、Tanaka Fumiaki、Katsuno Masahisa、Ito Yasuhiro
    • Journal Title

      Frontiers in Neurology

      Volume: 12

    • DOI

      10.3389/fneur.2021.622355

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-21K07419
  • [Journal Article] Ablation of interleukin-19 improves motor function in a mouse model of amyotrophic lateral sclerosis2021

    • Author(s)
      Komiya Hiroyasu、Takeuchi Hideyuki、Ogawa Yuki、Suzuki Kosuke、Ogasawara Akihiro、Takahashi Keita、Azuma Yasu-Taka、Doi Hiroshi、Tanaka Fumiaki
    • Journal Title

      Molecular Brain

      Volume: 14 Issue: 1 Pages: 74-74

    • DOI

      10.1186/s13041-021-00785-8

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07531, KAKENHI-PROJECT-18K07532, KAKENHI-PROJECT-21K07298, KAKENHI-PROJECT-21K07465
  • [Journal Article] Interleukin-19 Abrogates Experimental Autoimmune Encephalomyelitis by Attenuating Antigen-Presenting Cell Activation2021

    • Author(s)
      Horiuchi Hiroshi、Parajuli Bijay、Komiya Hiroyasu、Ogawa Yuki、Jin Shijie、Takahashi Keita、Azuma Yasu-Taka、Tanaka Fumiaki、Suzumura Akio、Takeuchi Hideyuki
    • Journal Title

      Frontiers in Immunology

      Volume: 12 Pages: 615465-615465

    • DOI

      10.3389/fimmu.2021.615898

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-20K21510, KAKENHI-PROJECT-18K07531, KAKENHI-PROJECT-18K14825, KAKENHI-PROJECT-21K07465
  • [Journal Article] SGTA associates with intracellular aggregates in neurodegenerative diseases2021

    • Author(s)
      Kubota Shun、Doi Hiroshi、Koyano Shigeru、Tanaka Kenichi、Komiya Hiroyasu、Katsumoto Atsuko、Ikeda Shingo、Hashiguchi Shunta、Nakamura Haruko、Fukai Ryoko、Takahashi Keita、Kunii Misako、Tada Mikiko、Takeuchi Hideyuki、Tanaka Fumiaki
    • Journal Title

      Molecular Brain

      Volume: 14 Issue: 1 Pages: 59-59

    • DOI

      10.1186/s13041-021-00770-1

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-20K16581, KAKENHI-PROJECT-21K07465
  • [Journal Article] Molecular epidemiology of hereditary ataxia in Finland2021

    • Author(s)
      Lipponen Joonas、Helisalmi Seppo、Raivo Joose、Siitonen Ari、Doi Hiroshi、Rusanen Harri、Lehtilahti Maria、Ryytty Mervi、Laakso Markku、Tanaka Fumiaki、Majamaa Kari、Kytovuori Laura
    • Journal Title

      BMC Neurology

      Volume: 21 Issue: 1 Pages: 382-382

    • DOI

      10.1186/s12883-021-02409-z

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-21K07298
  • [Journal Article] Reply to "GGC Repeat Expansion of NOTCH2NLC is Rare in European Leukoencephalopathy"2020

    • Author(s)
      Doi H, Okubo M, Fukai R, Fujita A, Mitsuhashi S, Takahashi K, Kunii M, Tada M, Fukuda H, Mizuguchi T, Miyatake S, Miyake N, Sone J, Sobue G, Takeuchi H, Matsumoto N and Tanaka F
    • Journal Title

      Ann Neurol

      Volume: 88 Issue: 3 Pages: 642-643

    • DOI

      10.1002/ana.25819

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-20K08164, KAKENHI-PROJECT-20K16581, KAKENHI-PROJECT-18K07503
  • [Journal Article] Long-read Sequencing Identifies the Pathogenic Nucleotide Repeat Expansion in RFC1 in a Japanese Case of CANVAS2020

    • Author(s)
      Haruko Nakamura, Hiroshi Doi, Satomi Mitsuhashi, Satoko Miyatake, Kazutaka Katoh, Martin C Frith, Tetsuya Asano, Yosuke Kudo, Takuya Ikeda, Shun Kubota, Misako Kunii, Yu Kitazawa, Mikiko Tada, Mitsuo Okamoto, Hideto Joki, Hideyuki Takeuchi, Naomichi Matsumoto, Fumiaki Tanaka
    • Journal Title

      Journal of Human Genetics

      Volume: 65 Issue: 5 Pages: 475-480

    • DOI

      10.1038/s10038-020-0733-y

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-19K07977, KAKENHI-PROJECT-19K17014, KAKENHI-PROJECT-17K10080, KAKENHI-PROJECT-20K06767, KAKENHI-PROJECT-20K07907, KAKENHI-PROJECT-18K07503
  • [Journal Article] Tonsillectomy Improved Therapeutic Response in Anti-SRP Myopathy With Chronic Tonsillitis2020

    • Author(s)
      Ikeda Takuya、Takeuchi Hideyuki、Takahashi Keita、Nakamura Haruko、Kunii Misako、Katsumoto Atsuko、Tada Mikiko、Higashiyama Yuichi、Hibiya Takashi、Suzuki Shigeaki、Nishino Ichizo、Koyano Shigeru、Doi Hiroshi、Tanaka Fumiaki
    • Journal Title

      Frontiers in Immunology

      Volume: 11 Pages: 595480-595480

    • DOI

      10.3389/fimmu.2020.595480

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07503
  • [Journal Article] CGG expansion in NOTCH2NLC is associated with oculopharyngodistal myopathy with neurological manifestations2020

    • Author(s)
      Ogasawara M, Iida A, Kumutpongpanich T, Ozaki A, Oya Y, Konishi H, Nakamura A, Abe R, Takai H, Hanajima R, Doi H, Tanaka F, Nakamura H, Nonaka I, Wang Z, Hayashi S, Noguchi S, Nishino I.
    • Journal Title

      Acta Neuropathol Commun

      Volume: 8 Issue: 1 Pages: 204-204

    • DOI

      10.1186/s40478-020-01084-4

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-20K07866, KAKENHI-PROJECT-18K07082, KAKENHI-PROJECT-18K07503
  • [Journal Article] De novo CACNA1G variants in developmental delay and early-onset epileptic encephalopathies2020

    • Author(s)
      Misako Kunii, Hiroshi Doi, Shunta Hashiguchi, Toyojiro Matsuishi, Yasunari Sakai, Mizue Iai, Masaki Okubo, Haruko Nakamura, Keita Takahashi, Atsuko Katsumoto, Mikiko Tada, Hideyuki Takeuchi, Taro Ishikawa, Noriko Miyake, Hirotomo Saitsu, Naomichi Matsumoto, Fumiaki Tanaka
    • Journal Title

      Journal of the Neurological Sciences

      Volume: 416 Pages: 117047-117047

    • DOI

      10.1016/j.jns.2020.117047

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K06529, KAKENHI-PROJECT-19K08281, KAKENHI-PROJECT-20H03641, KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-19K17014
  • [Journal Article] Hepatitis B Virus-related Vasculitic Neuropathy in an Inactive Virus Carrier Treated with Intravenous Immunoglobulin2020

    • Author(s)
      Kusama Kaori、Nakae Yoshiharu、Tada Mikiko、Higashiyama Yuichi、Miyaji Yosuke、Yamaura Genpei、Kunii Misako、Tanaka Kenichi、Ohyama Ken、Koike Haruki、Joki Hideto、Doi Hiroshi、Koyano Shigeru、Tanaka Fumiaki
    • Journal Title

      Intern. Med.

      Volume: 59 Issue: 23 Pages: 3075-3078

    • DOI

      10.2169/internalmedicine.4498-20

    • NAID

      130007948802

    • ISSN
      0918-2918, 1349-7235
    • Year and Date
      2020-12-01
    • Language
      English
    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-20K07882, KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-18K07504
  • [Journal Article] CCR2 is localized in microglia and neurons, as well as infiltrating monocytes, in the lumbar spinal cord of ALS mice.2020

    • Author(s)
      Komiya H, Takeuchi H (責任著者), Ogawa Y, Hatooka Y, Takahashi K, Katsumoto A, Kubota S, Nakamura H, Kunii M, Tada M, Doi H, Tanaka F
    • Journal Title

      Molecular Brain

      Volume: 13 Issue: 1 Pages: 64-64

    • DOI

      10.1186/s13041-020-00607-3

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07531, KAKENHI-PROJECT-19K17014, KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-18K07532
  • [Journal Article] Non-traumatic Acute Epidural Hematoma in Multiple Sclerosis Treated With Fingolimod2019

    • Author(s)
      Fukai Ryoko、Takahashi Keita、Abe Hiroyuki、Higashiyama Yuichi、Doi Hiroshi、Takeuchi Hideyuki、Tanaka Fumiaki
    • Journal Title

      Frontiers in Neurology

      Volume: 10 Pages: 763-763

    • DOI

      10.3389/fneur.2019.00763

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-18K15459
  • [Journal Article] Proteomic analysis of exosome-enriched fractions derived from cerebrospinal fluid of amyotrophic lateral sclerosis patients2019

    • Author(s)
      Hayashi Noriko、Doi Hiroshi、Kurata Yoichi、Kagawa Hiroyuki、Atobe Yoshitoshi、Funakoshi Kengo、Tada Mikiko、Katsumoto Atsuko、Tanaka Kenichi、Kunii Misako、Nakamura Haruko、Takahashi Keita、Takeuchi Hideyuki、Koyano Shigeru、Kimura Yayoi、Hirano Hisashi、Tanaka Fumiaki
    • Journal Title

      Neuroscience Research

      Volume: in press Pages: 30487-0

    • DOI

      10.1016/j.neures.2019.10.010

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-18K07504, KAKENHI-PROJECT-19K17014, KAKENHI-PROJECT-18K15460, KAKENHI-PROJECT-19H03774
  • [Journal Article] Novel <i>VRK1</i> Mutations in a Patient with Childhood-onset Motor Neuron Disease2019

    • Author(s)
      Yamaura Genpei、Higashiyama Yuichi、Kusama Kaori、Kunii Misako、Tanaka Kenichi、Koyano Shigeru、Nakashima Mitsuko、Tsurusaki Yoshinori、Miyake Noriko、Saitsu Hirotomo、Iwahashi Yukiko、Joki Hideto、Matsumoto Naomichi、Doi Hiroshi、Tanaka Fumiaki
    • Journal Title

      Intern. Med.

      Volume: 58 Issue: 18 Pages: 2715-2719

    • DOI

      10.2169/internalmedicine.2126-18

    • NAID

      130007706950

    • ISSN
      0918-2918, 1349-7235
    • Year and Date
      2019-09-15
    • Language
      English
    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-18K07504, KAKENHI-PROJECT-19K17014, KAKENHI-PROJECT-17H01539, KAKENHI-PROJECT-17K19536
  • [Journal Article] Tau Pathology in Chronic Traumatic Encephalopathy and Alzheimer's Disease: Similarities and Differences.2019

    • Author(s)
      Katsumoto A, Takeuchi H (責任著者), Tanaka F
    • Journal Title

      Frontiers in Neurology

      Volume: 10 Pages: 980-980

    • DOI

      10.3389/fneur.2019.00980

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07531, KAKENHI-PROJECT-18K15460
  • [Journal Article] Adult-onset vocal cord paralysis in slow-channel congenital myasthenic syndrome2019

    • Author(s)
      Nakamura Haruko、Komiya Hiroyasu、Uematsu Eri、Nakae Yoshiharu、Tanaka Kenichi、Kunii Misako、Tada Mikiko、Joki Hideto、Koyano Shigeru、Matsumoto Naomichi、Doi Hiroshi、Takeuchi Hideyuki、Tanaka Fumiaki
    • Journal Title

      Neurology: Clinical Practice

      Volume: 9 Issue: 5

    • DOI

      10.1212/cpj.0000000000000599

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-18K07504, KAKENHI-PROJECT-19K17014, KAKENHI-PROJECT-17H01539
  • [Journal Article] Recurrent NUS1 canonical splice donor site mutation in two unrelated individuals with epilepsy, myoclonus, ataxia and scoliosis - a case report2019

    • Author(s)
      Den Kouhei、Kudo Yosuke、Kato Mitsuhiro、Watanabe Kosuke、Doi Hiroshi、Tanaka Fumiaki、Oguni Hirokazu、Miyatake Satoko、Mizuguchi Takeshi、Takata Atsushi、Miyake Noriko、Mitsuhashi Satomi、Matsumoto Naomichi
    • Journal Title

      BMC Neurology

      Volume: 19 Issue: 1 Pages: 253-253

    • DOI

      10.1186/s12883-019-1489-x

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-17H01539, KAKENHI-PROJECT-19H03621, KAKENHI-PROJECT-16H06254, KAKENHI-PROJECT-16K09975, KAKENHI-PROJECT-17K10080
  • [Journal Article] 【もっとうまくいく!病診連携の「伝え方」 わかりやすく伝えるための診療情報提供書作成のコツ】第II章<診療科別>コンサルトのポイント E. 脳神経内科へのコンサルト 歩行障害.2018

    • Author(s)
      土井 宏、田中 章景
    • Journal Title

      内科

      Volume: 122 Pages: 564-566

    • Data Source
      KAKENHI-PROJECT-18K07503
  • [Journal Article] Cerebrospinal fluid level of Nogo receptor 1 antagonist lateral olfactory tract usher substance (LOTUS) correlates inversely with the extent of neuroinflammation2018

    • Author(s)
      Takahashi Keita、Takeuchi Hideyuki、Kurihara Yuji、Doi Hiroshi、Kunii Misako、Tanaka Kenichi、Nakamura Haruko、Fukai Ryoko、Tomita-Katsumoto Atsuko、Tada Mikiko、Higashiyama Yuichi、Joki Hideto、Koyano Shigeru、Takei Kohtaro、Tanaka Fumiaki
    • Journal Title

      Journal of Neuroinflammation

      Volume: 15 Issue: 1 Pages: 46-46

    • DOI

      10.1186/s12974-018-1084-x

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-17K16128, KAKENHI-PROJECT-16K19518, KAKENHI-PROJECT-16K21268, KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-18K15458
  • [Journal Article] Two cases of anaphylactic shock by methylprednisolone in neuromyelitis optica2018

    • Author(s)
      Takahashi Keita、Asano Tetsuya、Higashiyama Yuichi、Koyano Shigeru、Doi Hiroshi、Takeuchi Hideyuki、Tanaka Fumiaki
    • Journal Title

      Multiple Sclerosis Journal

      Volume: 24 Issue: 11 Pages: 1514-1516

    • DOI

      10.1177/1352458518763099

    • NAID

      120006808928

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-18K15458
  • [Journal Article] 【中枢神経疾患における末梢神経障害】 有棘赤血球舞踏病における末梢神経障害.2018

    • Author(s)
      土井 宏、田中 章景
    • Journal Title

      神経内科

      Volume: 89 Pages: 457-462

    • Data Source
      KAKENHI-PROJECT-18K07503
  • [Journal Article] Cerebellar ataxia-dominant phenotype in patients with ERCC4 mutations2018

    • Author(s)
      Doi H、Koyano S、Miyatake S、Nakajima S、Nakazawa Y、Kunii M、Tomita-Katsumoto A、Oda K、Yamaguchi Y、Fukai R、Ikeda S、Kato R、Ogata K、Kubota S、Hayashi N、Takahashi K、Tada M、Tanaka K、Nakashima M、Tsurusaki Y et al.
    • Journal Title

      Journal of Human Genetics

      Volume: 63 Issue: 4 Pages: 417-423

    • DOI

      10.1038/s10038-017-0408-5

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-17K19536, KAKENHI-PROJECT-17K16128, KAKENHI-PROJECT-15H05333, KAKENHI-PROJECT-17H00783, KAKENHI-PROJECT-16H05357, KAKENHI-PROJECT-15K09344, KAKENHI-PROJECT-16K15526, KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-18K07504, KAKENHI-PROJECT-18K11639, KAKENHI-PROJECT-17H01539, KAKENHI-PROJECT-17H01877, KAKENHI-PROJECT-18H03372, KAKENHI-PROJECT-15H02654
  • [Journal Article] Matrin 3 Is a Component of Neuronal Cytoplasmic Inclusions of Motor Neurons in Sporadic Amyotrophic Lateral Sclerosis2018

    • Author(s)
      Tada Mikiko、Doi Hiroshi、Koyano Shigeru、Kubota Shun、Fukai Ryoko、Hashiguchi Shunta、Hayashi Noriko、Kawamoto Yuko、Kunii Misako、Tanaka Kenichi、Takahashi Keita、Ogawa Yuki、Iwata Ryo、Yamanaka Shoji、Takeuchi Hideyuki、Tanaka Fumiaki
    • Journal Title

      The American Journal of Pathology

      Volume: 188 Issue: 2 Pages: 507-514

    • DOI

      10.1016/j.ajpath.2017.10.007

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K14956, KAKENHI-PROJECT-17K16128, KAKENHI-PROJECT-15K09344
  • [Journal Article] Confirmation of SLC5A7-related distal hereditary motor neuropathy 7 in a family outside Wales2018

    • Author(s)
      Hamanaka K.、Takahashi K.、Miyatake S.、Mitsuhashi S.、Hamanoue H.、Miyaji Y.、Fukai R.、Doi H.、Fujita A.、Imagawa E.、Iwama K.、Nakashima M.、Mizuguchi T.、Takata A.、Miyake N.、Takeuchi H.、Tanaka F.、Matsumoto N.
    • Journal Title

      Clinical Genetics

      Volume: 94 Issue: 2 Pages: 274-275

    • DOI

      10.1111/cge.13369

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K10080, KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-17H01539, KAKENHI-PROJECT-16H06254, KAKENHI-PROJECT-17K15630
  • [Journal Article] Genetic analysis of adult leukoencephalopathy patients using a custom-designed gene panel2018

    • Author(s)
      Kunii M.、Doi H.、Ishii Y.、Ohba C.、Tanaka K.、Tada M.、Fukai R.、Hashiguchi S.、Kishida H.、Ueda N.、Kudo Y.、Kugimoto C.、Nakano T.、Udaka N.、Miyatake S.、Miyake N.、Saitsu H.、Ito Y.、Takahashi K.、Nakamura H.、Tomita-Katsumoto A.、Takeuchi H.、Koyano S.、Matsumoto N.、Tanaka F.
    • Journal Title

      Clinical Genetics

      Volume: - Issue: 2 Pages: 232-238

    • DOI

      10.1111/cge.13371

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K16128, KAKENHI-PROJECT-15K09344, KAKENHI-PROJECT-17K10080, KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-18K07504, KAKENHI-PROJECT-17H01539
  • [Journal Article] 【ニューロジェネティクス新時代 次世代シークエンサーが拓く新しい世界】 筋疾患・神経疾患のジェネティクス 筋萎縮性側索硬化症.2018

    • Author(s)
      土井 宏、田中 章景
    • Journal Title

      Clinical Neuroscience

      Volume: 36 Pages: 206-209

    • Data Source
      KAKENHI-PROJECT-18K07503
  • [Journal Article] White matter hyperintensities on MRI in dementia with Lewy bodies, Parkinson's disease with dementia, and Alzheimer's disease2018

    • Author(s)
      Joki Hideto、Higashiyama Yuichi、Nakae Yoshiharu、Kugimoto Chiharu、Doi Hiroshi、Kimura Katsuo、Kishida Hitaru、Ueda Naohisa、Nakano Tatsu、Takahashi Tatsuya、Koyano Shigeru、Takeuchi Hideyuki、Tanaka Fumiaki
    • Journal Title

      Journal of the Neurological Sciences

      Volume: 385 Pages: 99-104

    • DOI

      10.1016/j.jns.2017.12.018

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07503
  • [Journal Article] A Japanese Family of Spinocerebellar Ataxia Type 21: Clinical and Neuropathological Studies2018

    • Author(s)
      Yahikozawa Hiroyuki、Miyatake Satoko、Sakai Toshiaki、Uehara Takeshi、Yamada Mitsunori、Hanyu Norinao、Futatsugi Yasuhiro、Doi Hiroshi、Koyano Shigeru、Tanaka Fumiaki、Suzuki Atsushi、Matsumoto Naomichi、Yoshida Kunihiro
    • Journal Title

      The Cerebellum

      Volume: 印刷中 Issue: 5 Pages: 525-530

    • DOI

      10.1007/s12311-018-0941-6

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K10080, KAKENHI-PROJECT-15K09344, KAKENHI-PROJECT-18K07503, KAKENHI-PROJECT-17H01539
  • [Journal Article] A Case of McLeod Syndrome with A Novel XK Missense Mutation2018

    • Author(s)
      Komiya H, Takasu M, Hashiguchi S, Uematsu E, Fukai R, Tanaka K, Tada M, Joki H, Takahashi T, Koyano S, Doi H, Takeuchi H, Tanaka F
    • Journal Title

      Mov Disord Clin Pract.

      Volume: 5 Issue: 3 Pages: 333-336

    • DOI

      10.1002/mdc3.12614

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-18K07504
  • [Journal Article] 孤発性ALSの早期診断2017

    • Author(s)
      土井 宏、田中章景
    • Journal Title

      神経内科

      Volume: 86 Pages: 9-16

    • Data Source
      KAKENHI-PROJECT-15K09344
  • [Journal Article] 軸索再生関連分子の多発性硬化症診断マーカーへの応用2016

    • Author(s)
      高橋慶太, 田中章景, 竹居光太郎
    • Journal Title

      Brain and Nerve

      Volume: 68(1) Pages: 82-89

    • NAID

      40020711603

    • Data Source
      KAKENHI-PROJECT-15K14353
  • [Journal Article] Autosomal recessive spinocerebellar ataxias in Japan2016

    • Author(s)
      田中章景、土井 宏、國井美紗子
    • Journal Title

      Rinsho Shinkeigaku

      Volume: 56 Issue: 6 Pages: 395-399

    • DOI

      10.5692/clinicalneurol.cn-000879

    • NAID

      130005158857

    • ISSN
      0009-918X, 1882-0654
    • Language
      Japanese
    • Data Source
      KAKENHI-PROJECT-15K09344
  • [Journal Article] 多発性硬化症の新規病勢診断マーカー2016

    • Author(s)
      高橋慶太, 田中章景, 竹居光太郎
    • Journal Title

      臨床神経科学(Clinical Neuroscience)

      Volume: 34(4) Pages: 484-485

    • Data Source
      KAKENHI-PROJECT-15K14353
  • [Journal Article] Relationship between cortex and pulvinar abnormalities on diffusion-weighted imaging in status epilepticus.2016

    • Author(s)
      Nakae Y, Kudo Y, Yamamoto R, Dobashi Y, Kawabata Y, Ikeda S, Yokoyama M, Higashiyama Y, Doi H, Johkura K, Tanaka F.
    • Journal Title

      J Neurol.

      Volume: 263 Issue: 1 Pages: 127-132

    • DOI

      10.1007/s00415-015-7948-4

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09344
  • [Journal Article] Next-generation sequencing of 28 ALS-related genes in a Japanese ALS cohort2016

    • Author(s)
      Ryoichi Nakamura, Jun Sone, Naoki Atsuta, Genki Tohnai, Hazuki Watanabe, Daichi Yokoi, Masahiro Nakatochi, Hirohisa Watanabe, Mizuki Ito, Jo Senda, Masahisa Katsuno, Fumiaki Tanaka, Yuanzhe Li, Yuishin Izumi, Mitsuya Morita, Akira Taniguchi, Osamu Kano, Masaya Oda, Satoshi Kuwabara, Koji Abe.
    • Journal Title

      Neurobiology of Aging

      Volume: 39 Pages: 219-219

    • DOI

      10.1016/j.neurobiolaging.2015.11.030

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-15K19485, KAKENHI-PROJECT-221S0002, KAKENHI-PROJECT-25461277, KAKENHI-PROJECT-15K15337, KAKENHI-PROJECT-26670439, KAKENHI-PROJECT-26670445, KAKENHI-PROJECT-25860725, KAKENHI-PROJECT-25293207, KAKENHI-ORGANIZER-26117001, KAKENHI-PROJECT-15H05667, KAKENHI-PROJECT-26461319
  • [Journal Article] Association of Cerebrospinal Fluid Levels of Lateral Olfactory Tract Usher Substance (LOTUS) With Disease Activity in Multiple Sclerosis2015

    • Author(s)
      Takahashi K, Kurihara Y, Suzuki Y, Goshima Y, Tanaka F, Takei K.
    • Journal Title

      JAMA Neurol

      Volume: 72 Issue: 2 Pages: 176-179

    • DOI

      10.1001/jamaneurol.2014.3613

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-25293207, KAKENHI-PROJECT-26670444, KAKENHI-PROJECT-26870480
  • [Journal Article] Association of multiple sclerosis with lateral olfactory tract usher substance (LOTUS), a possible endogenous inhibitor of axonal degeneration2015

    • Author(s)
      Takahashi, K., Takei, K., and Tanaka, F.
    • Journal Title

      Clinical and Experimental Neuroimmunology,

      Volume: 6 Pages: 64-69

    • Acknowledgement Compliant / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K14353
  • [Journal Article] Clinicopathologic features of folate-deficiency neuropathy.2015

    • Author(s)
      Koike H, Takahashi M, Ohyama K, Hashimoto R, Kawagashira Y, Iijima M, Katsuno M, Doi H, Tanaka F, Sobue G.
    • Journal Title

      Neurology

      Volume: 84 Issue: 10 Pages: 1026-1033

    • DOI

      10.1212/wnl.0000000000001343

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09344, KAKENHI-PROJECT-26461292, KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-25461278
  • [Journal Article] A Japanese case of cerebellar ataxia, spastic paraparesis and deep sensory impairment associated with a novel homozygous TTC19 mutation2015

    • Author(s)
      Kunii M, Doi H, Higashiyama Y, Kugimoto C, Ueda N, Hirata J, Tomita-Katsumoto A, Kashikura-Kojima M, Kubota S, Taniguchi M, Murayama K, Nakashima M, Tsurusaki Y, Miyake N, Saitsu H, Matsumoto N, Tanaka F.
    • Journal Title

      J Hum Genet

      Volume: 60 Issue: 4 Pages: 187-191

    • DOI

      10.1038/jhg.2015.7

    • NAID

      40020433141

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PLANNED-22129005, KAKENHI-PROJECT-15K19660, KAKENHI-ORGANIZER-24118001, KAKENHI-PLANNED-24118007, KAKENHI-PROJECT-25461287, KAKENHI-PROJECT-26670445, KAKENHI-PROJECT-25293207, KAKENHI-PROJECT-25293235
  • [Journal Article] Association of cerebrospinal fluid levels of lateral olfactory usher substance protein with disease activity in multiple sclerosis.2015

    • Author(s)
      Takahashi, K., Kurihara, Y., Suzuki, Y., Goshima, Y., Tanaka, F., and Takei,
    • Journal Title

      JAMA Neurology

      Volume: 72 Pages: 176-179

    • Peer Reviewed / Acknowledgement Compliant / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K14353
  • [Journal Article] LOTUS, a possible endogenous inhibitor of axonal degeneration, as a biomarker for multiple sclerosis.2015

    • Author(s)
      Takahashi, K., Tanaka, F., and Takei, K.
    • Journal Title

      Neural Degenerative Disease Management

      Volume: 5 Issue: 6 Pages: 469-472

    • DOI

      10.2217/nmt.15.47

    • Peer Reviewed / Acknowledgement Compliant / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K14353, KAKENHI-PUBLICLY-26111718
  • [Journal Article] Association of multiple sclerosis with lateral olfactory tract usher substance (LOTUS), a possible endogenous inhibitor of axonal degeneration2015

    • Author(s)
      Takahashi K, Takei K, Tanaka F
    • Journal Title

      Clin Exp Neuroimmunol

      Volume: 6 Issue: S1 Pages: 64-69

    • DOI

      10.1111/cen3.12272

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-26670445, KAKENHI-PROJECT-25293207
  • [Journal Article] A novel mutation in ELOVL4 leading to spinocerebellar ataxia (SCA) with the hot cross bun sign but lacking erythrokeratodermia: a broadened spectrum of SCA34.2015

    • Author(s)
      Ozaki K, Doi H, Mitsui J, Sato N, Iikuni Y, Majima T, Yamane K, Irioka T, Ishiura H, Doi K, Morishita S, Higashi M, Sekiguchi T, Koyama K, Ueda N, Miura Y, Miyatake S, Matsumoto N, Yokota T, Tanaka F, Tsuji S, Mizusawa H, Ishikawa K.
    • Journal Title

      JAMA Neurology

      Volume: 72 Issue: 7 Pages: 797-805

    • DOI

      10.1001/jamaneurol.2015.0610

    • Peer Reviewed / Acknowledgement Compliant / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09335, KAKENHI-PROJECT-15K09344, KAKENHI-PROJECT-26461549, KAKENHI-PROJECT-221S0002, KAKENHI-ORGANIZER-24118001, KAKENHI-PLANNED-24118007, KAKENHI-PROJECT-25461287
  • [Journal Article] Association of Cerebrospinal Fluid Levels of Lateral Olfactory Tract Usher Substance (LOTUS) With Disease Activity in Multiple Sclerosis2015

    • Author(s)
      Keita Takahashi; Yuji Kurihara; Yume Suzuki; Yoshio Goshima; Fumiaki Tanaka; Kohtaro Takei,
    • Journal Title

      JAMA Neurology

      Volume: 72 Pages: 176-179

    • Peer Reviewed / Acknowledgement Compliant / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26670444
  • [Journal Article] Quantitative analysis of intraneuronal transport in human iPS neurons2015

    • Author(s)
      Nakamura H, Yamashita N, Kanamaru Y, Tachibana T, Sekino Y, Chen S, Gotoh T, Tanaka F, Goshima Y
    • Journal Title

      J Pharmacol Sci

      Volume: 128 Issue: 4 Pages: 170-178

    • DOI

      10.1016/j.jphs.2015.06.006

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-26670445, KAKENHI-PROJECT-25293207
  • [Journal Article] Neuronal intranuclear inclusion disease cases with leukoencephalopathy diagnosed via skin biopsy.2014

    • Author(s)
      Sone J, Kitagawa N, Sugawara E, Iguchi M, Nakamura R, Koike H, Iwasaki Y, Yoshida M, Takahashi T, Chiba S, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 85(3) Issue: 3 Pages: 354-356

    • DOI

      10.1136/jnnp-2013-306084

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24591257, KAKENHI-PROJECT-25461276
  • [Journal Article] Neuropathological staging of spinocerebellar ataxia type 2 by semiquantitative 1C2-positive neuron typing Nuclear translocation of cytoplasmic 1C2 underlies disease progression of spinocerebellar ataxia type 2.2014

    • Author(s)
      Koyano S, Yagishita S, Kuroiwa Y, Tanaka F, Uchihara T.
    • Journal Title

      Brain Pathol

      Volume: 26 Issue: 6 Pages: 599-606

    • DOI

      10.1111/bpa.12146

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23591279, KAKENHI-PROJECT-25293207, KAKENHI-PROJECT-25430057, KAKENHI-PROJECT-26670445
  • [Journal Article] Late-onset spastic ataxia phenotype in a patient with a homozygous DDHD2 mutation2014

    • Author(s)
      Doi H, Ushiyama M, Baba T, Tani K, Shiina M, Ogata K, Miyatake S, Yuzawa YF, Tsuji S, Nakashima M, Tsurusaki Y, Miyake N, Saitsu H, Ikeda S, Tanaka F, Matsumoto N, Yoshida K
    • Journal Title

      Sci Rep

      Volume: 4 Issue: 1 Pages: 7132-7132

    • DOI

      10.1038/srep07132

    • NAID

      120007100602

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PLANNED-22129005, KAKENHI-ORGANIZER-24118001, KAKENHI-PLANNED-24118005, KAKENHI-PLANNED-24118007, KAKENHI-PROJECT-24249019, KAKENHI-PROJECT-24591255, KAKENHI-PROJECT-25293207, KAKENHI-PROJECT-25293235, KAKENHI-PROJECT-25461287, KAKENHI-PROJECT-26330331, KAKENHI-PROJECT-26440105, KAKENHI-PROJECT-26461549, KAKENHI-PROJECT-26670445
  • [Journal Article] Tongue pressure as a novel biomarker of spinal and bulbar muscular atrophy (SBMA)2014

    • Author(s)
      Mano T, Katsuno M, Banno H, Suzuki K, Suga N, Hashizume A, Araki A, Watanabe H, Tanaka S, Yamamoto M, Sobue G
    • Journal Title

      Neurology

      Volume: 82 Issue: 3 Pages: 255-262

    • DOI

      10.1212/wnl.0000000000000041

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-24659428
  • [Journal Article] Schwann cell involvement in the peripheral neuropathy of spinocerebellar ataxia type 3.2014

    • Author(s)
      Suga N, Katsuno M, Koike H, Banno H, Suzuki K, Hashizume A, Mano T, Iijima M, Kawagashira Y, Hirayama M, Nakamura T, Watanabe H, Tanaka F, Sobue G
    • Journal Title

      Neuropathol Appl Neurobiol.

      Volume: 40 Issue: 5 Pages: 628-639

    • DOI

      10.1111/nan.12055

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-24500458, KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-25461278, KAKENHI-PROJECT-26293206, KAKENHI-PROJECT-26670445
  • [Journal Article] Early onset epileptic encephalopathy caused by de novo SCN8A mutations2014

    • Author(s)
      Ohba C, Kato M, Takahashi S, Lerman-Sagie T, Lev D, Terashima H, Kubota M, Kawawaki H, Matsufuji M, Kojima Y, Tateno A, Goldberg-Stern H, Straussberg R, Marom D, Leshinsky-Silver E, Nakashima M, Nishiyama K, Tsurusaki Y, Miyake N, Tanaka F, Matsumoto N, Saitsu H:
    • Journal Title

      Epilepsia

      Volume: 55 Issue: 7 Pages: 994-1000

    • DOI

      10.1111/epi.12668

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22129005, KAKENHI-ORGANIZER-24118001, KAKENHI-PLANNED-24118007, KAKENHI-PROJECT-24249019, KAKENHI-PROJECT-24591500, KAKENHI-PROJECT-25293085, KAKENHI-PROJECT-25293235, KAKENHI-PROJECT-25860915
  • [Journal Article] 神経細胞変性のメカニズム「蛋白質凝集と神経変性」2014

    • Author(s)
      土井 宏, 田中章景
    • Journal Title

      BRAIN MEDICAL

      Volume: 26 Pages: 73-79

    • Data Source
      KAKENHI-PROJECT-25293207
  • [Journal Article] Translational research on disease-modifying therapies for neurodegenerative diseases2013

    • Author(s)
      Katsuno M, Watanabe H, Tanaka F, Sobue G
    • Journal Title

      Neurology and Clinical Neuroscience

      Volume: 1 Issue: 1 Pages: 3-10

    • DOI

      10.1002/ncn3.7

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-24659428
  • [Journal Article] ALSのパーソナルゲノム解析2013

    • Author(s)
      田中章景,曽根 淳,熱田直樹,中村亮一,土井 宏,児矢野 繁,祖父江 元
    • Journal Title

      Brain and Nerve

      Volume: 65 Pages: 257-265

    • Data Source
      KAKENHI-PLANNED-22129005
  • [Journal Article] RNP2 of RNA recognition motif 1 plays a central role in the aberrant modification of TDP-43.2013

    • Author(s)
      Takagi S, Iguchi Y, Katsuno M, Ishigaki S, Ikenaka K, Fujioka Y, Honda D, Niwa J, Tanaka F, Watanabe H, Adachi H, Sobue G.
    • Journal Title

      PLoS One.

      Volume: 28 Issue: 6 Pages: e66966-e66966

    • DOI

      10.1371/journal.pone.0066966

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-25293207
  • [Journal Article] Neck weakness is a potent prognostic factor in sporadic amyotrophic lateral sclerosis patients.2013

    • Author(s)
      Nakamura R, Atsuta N, Watanabe H, Hirakawa A, Watanabe H, Ito M, Senda J, Katsuno M, Tanaka F, Izumi Y, Morita M, Ogaki K, Taniguchi A, Aiba I, Mizoguchi K, Okamoto K, Hasegawa K, Aoki M, Kawata A, Abe K, Oda M, Konagaya M, Imai T, Nakagawa M, Tsuji S, Kaji R, Nakano I, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 84 Issue: 12 Pages: 1365-1371

    • DOI

      10.1136/jnnp-2013-306020

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PLANNED-22129005, KAKENHI-PROJECT-23591231, KAKENHI-PROJECT-24406030, KAKENHI-PROJECT-25461277, KAKENHI-PROJECT-25461312
  • [Journal Article] Heat shock factor-1 influences pathological lesion distribution of polyglutamine-induced neurodegeneration2013

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Tohnai G, Nakatsuji H, Ishigaki S, Fujioka Y, Watanabe H, Tanaka F, Nakai A, Sobue G
    • Journal Title

      Nat Commun

      Volume: 4 Issue: 1 Pages: 1405-1405

    • DOI

      10.1038/ncomms2417

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-24659428, KAKENHI-PLANNED-22110005
  • [Journal Article] dnc-1/dynactin 1 knockdown disrupts transport of autophagosomes and induces motor neuron degeneration2013

    • Author(s)
      Ikenaka K, Kawai K, Katsuno M, Huang Z, Jiang YM, Iguchi Y, Kobayashi K, Kimata T, Waza M, Tanaka F, Mori I, Sobue G
    • Journal Title

      PLoS One

      Volume: 8

    • NAID

      120007001030

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Distinct acoustic features in spinal and bulbar muscular atrophy patients with laryngospasm.2013

    • Author(s)
      Tanaka S, Banno H, Katsuno M, Suzuki K, Suga N, Hashizume A, Mano T, Araki A, Watanabe H, Adachi H, Tatsumi H, Yamamoto M, Sobue G.
    • Journal Title

      J Neurol Sci.

      Volume: 337 Issue: 1-2 Pages: 193-200

    • DOI

      10.1016/j.jns.2013.12.010

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005
  • [Journal Article] dnc-1/dynactin 1 knockdown disrupts transport of autophagosomes and induces motor neuron degeneration2013

    • Author(s)
      Ikenaka K
    • Journal Title

      PLoS One

      Volume: 8 Issue: 2 Pages: e54511-e54511

    • DOI

      10.1371/journal.pone.0054511

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175, KAKENHI-PROJECT-24247001, KAKENHI-PROJECT-25293207, KAKENHI-PLANNED-22110005, KAKENHI-PLANNED-22123010
  • [Journal Article] p62/SQSTM1 differentially removes the toxic mutant androgen receptor via autophagy and inclusion formation in a spinal and bulbar muscular atrophy mouse model2013

    • Author(s)
      Doi H, Adachi H, Katsuno M, Minamiyama M, Matsumoto S, Kondo N, Miyazaki Y, IidaM,Tohnai G, Qiang Q, Tanaka F, Yanagawa T, WarabiE,Ishii T, Sobue G
    • Journal Title

      J Neurosci

      Volume: 33 Issue: 18 Pages: 7710-7727

    • DOI

      10.1523/jneurosci.3021-12.2013

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23390231, KAKENHI-PROJECT-24659428, KAKENHI-PROJECT-25220103
  • [Journal Article] Ablation of Keratan Sulfate Accelerates Early Phase Pathogenesis of ALS.2013

    • Author(s)
      Kenichi Hirano, Tomohiro Ohgomori, Kazuyoshi Kobayashi, Fumiaki Tanaka, Tomohiro Matsumoto, Takamitsu Natori, Yukihiro Matsuyama, Kenji Uchimura, Kazuma Sakamoto, Hideyuki Takeuchi, Akihiro Hirakawa, Akio Suzumura, Gen Sobue, Naoki Ishiguro, Shiro Imagama, Kenji Kadomatsu
    • Journal Title

      PLoS ONE

      Volume: 8(6) Issue: 6 Pages: e66969-e66969

    • DOI

      10.1371/journal.pone.0066969

    • NAID

      120005946841

    • Peer Reviewed
    • Data Source
      KAKENHI-PUBLICLY-24111520, KAKENHI-PROJECT-24890084, KAKENHI-PROJECT-25293207, KAKENHI-PROJECT-25860234
  • [Journal Article] Spliceosome integrity is defective in the motor neuron diseases ALS and SMA2013

    • Author(s)
      Tsuiji H, Iguchi Y, Furuya A, Kataoka A, Hatsuta H, Atsuta N, Tanaka F, Hashizume Y, Akatsu H, Murayama S, Sobue G, Yamanaka K
    • Journal Title

      EMBO Mol Med

      Volume: 5 Issue: 2 Pages: 221-234

    • DOI

      10.1002/emmm.201202303

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PLANNED-22129005, KAKENHI-PROJECT-23700455, KAKENHI-PROJECT-24500431, KAKENHI-PROJECT-24700371, KAKENHI-PLANNED-23111006
  • [Journal Article] A novel SCARB2 mutation causing late-onset progressive myoclonus epilepsy2013

    • Author(s)
      Higashiyama Y, Doi H, Wakabayashi M, Tsurusaki Y, Miyake N, Saitsu H, Ohba C, Fukai R, Miyatake S, Joki H, Koyano S, Suzuki Y, Tanaka F, Kuroiwa Y, Matsumoto N
    • Journal Title

      Mov Disord

      Volume: 28 Issue: 4 Pages: 552-553

    • DOI

      10.1002/mds.25296

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22129005, KAKENHI-PLANNED-24118007, KAKENHI-PROJECT-24249019, KAKENHI-PROJECT-24790893, KAKENHI-PROJECT-25293235, KAKENHI-PROJECT-25860915
  • [Journal Article] Increased number of astrocytes and macrophages/microglial cells in the corpus callosum in amyotrophic lateral sclerosis2013

    • Author(s)
      Sugiyama M, Takao M, Hatsuta H, Funabe S, Ito S, Obi T, Tanaka F, Kuroiwa Y, Murayama S.
    • Journal Title

      Neuropathology

      Volume: 34 Issue: 6 Pages: 591-9

    • DOI

      10.1111/neup.12027

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23500435, KAKENHI-PROJECT-24700371, KAKENHI-PROJECT-25293207
  • [Journal Article] 次世代シーケンサーによる神経変性疾患の解析と展望 ALSのパーソナルゲノム解析2013

    • Author(s)
      田中章景
    • Journal Title

      BRAIN and NERVE

      Volume: 65 Pages: 19-30

    • Data Source
      KAKENHI-PLANNED-22129005
  • [Journal Article] Discrimination of spinal and bulbar muscular atrophy from amyotrophic lateral sclerosis using sensory nerve action potentials.2012

    • Author(s)
      Hama T, Hirayama M, Hara T, Nakamura T, Atsuta N, Banno H, Suzuki K, Katsuno M, Tanaka F, Sobue G.
    • Journal Title

      Muscle Nerve

      Volume: 45 Issue: 2 Pages: 169-174

    • DOI

      10.1002/mus.22291

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-21600003, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986, KAKENHI-PROJECT-24500458
  • [Journal Article] Natural history of trans thyretin Val 30 Met familial amyloid polyneuropathy : analysis of late-onset cases from non-endemic areas2012

    • Author(s)
      Koike H, Tanaka F, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Fujitake J, Kawanami T, Kato T, Yamamoto M, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 83 Pages: 152-158

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Neuropathology and omics in motor neuron diseases2012

    • Author(s)
      Tanaka F
    • Journal Title

      Neuropathology

      Volume: 32 Issue: 4 Pages: 458-462

    • DOI

      10.1111/j.1440-1789.2011.01281.x

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Journal Article] c-Abl inhibition delays motor neuron degeneration in the G93A mouse2012

    • Author(s)
      Katsumata R, Ishigaki S, Katsuno M, Kawai K, Sone J, Huang Z, Adachi H,Tanaka F, Urano F, Sobue G
    • Journal Title

      an animal model of amyotrophic lateral sclerosis

      Volume: 7

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Viral delivery of miR-196a ameliorates the SBMA phenotype via the silencing of CELF22012

    • Author(s)
      Miyazaki Y, Adachi H, Katsuno M, Minamiyama M, Jiang YM, Huang Z, Doi H, Matsumoto S, Kondo N, Iida M, Tohnai G, Tanaka F, Muramatsu S, Sobue G
    • Journal Title

      Nat Med

      Volume: 18 Issue: 7 Pages: 1136-1141

    • DOI

      10.1038/nm.2791

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390231, KAKENHI-PROJECT-23590473, KAKENHI-PUBLICLY-23110515
  • [Journal Article] Naratriptan mitigates CGRP1-associated motor neuron degeneration caused by expanded polyglutamine2012

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Iida M, Ishigaki S, Fujioka Y, Matsumoto S, Miyazaki Y, Tanaka F, Kurihara H, Sobue G
    • Journal Title

      Nat Med

      Volume: 18 Issue: 10 Pages: 1531-1538

    • DOI

      10.1038/nm.2932

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PUBLICLY-23013007, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23659107, KAKENHI-PROJECT-24249047
  • [Journal Article] Differential change of clinical outcome measures in spinal and bulbar muscular atrophy: comparison of natural history with placebo-treated group.2012

    • Author(s)
      Hashizume A, Katsuno M, Banno H, Suzuki K, Suga N, Tanaka F, Sobue G.
    • Journal Title

      J Neurol.

      Volume: 259 Issue: 4 Pages: 712-719

    • DOI

      10.1007/s00415-011-6251-2

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986
  • [Journal Article] A novel MPZ mutation in Charcot-Marie-Tooth disease type 1B with focally folded myelin and multiple entrapment neuropathies2012

    • Author(s)
      Iida M, Koike H, Ando T, Sugiura M, Yamamoto M, Tanaka F, Sobue G.
    • Journal Title

      Neuromuscul Disord

      Volume: 22 Pages: 166-169

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Defective axonal transport in motor neuron diseases.2012

    • Author(s)
      Ikenaka K, Katsuno M, Kawai K, Ishigaki S, Tanaka F, Sobue G.
    • Journal Title

      Int J Mol Sci.

      Volume: 13 Issue: 1 Pages: 1225-1238

    • DOI

      10.3390/ijms13011225

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230
  • [Journal Article] Current status of treatment of spinal and bulbar muscular atrophy2012

    • Author(s)
      Tanaka F, Katsuno M, Banno H, Suzuki K, Adachi H, Sobue G
    • Journal Title

      Neural Plast

      Volume: 2012 Pages: 369284-369284

    • DOI

      10.1155/2012/369284

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23790986, KAKENHI-PROJECT-24659428
  • [Journal Article] Molecular pathophysiology and disease-Modifying therapies for spinal and bulbar muscular atrophy2012

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Adachi H, Tanaka F, Sobue G
    • Journal Title

      Arch Neurol

      Volume: 69 Issue: 4 Pages: 436-440

    • DOI

      10.1001/archneurol.2011.2308

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986, KAKENHI-PROJECT-24659428
  • [Journal Article] Cross-sectional and longitudinal analysis of an oxidative stress biomarker for spinal and bulbar muscular atrophy.2012

    • Author(s)
      Mano, T., Katsuno, M., Banno, H., Suzuki, K., Suga, N., Hashizume, A., Tanaka, F., Sobue, G.
    • Journal Title

      Muscle Nerve

      Volume: 46 Issue: 5 Pages: 692-697

    • DOI

      10.1002/mus.23413

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986
  • [Journal Article] Perspectives on molecular targeted therapies and clinical trials for neurodegenerative diseases2012

    • Author(s)
      Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 83 Issue: 3 Pages: 329-335

    • DOI

      10.1136/jnnp-2011-301307

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-24659428
  • [Journal Article] Oxidative stress induced by glutathione depletion reproduces pathological modifications of TDP-43 linked to TDP-43 proteinopathies.2012

    • Author(s)
      Iguchi Y,Katsuno M,Takagi S.Ishigaki S,Niwa JI,Hasegawa M,Tanaka F,Sobue G
    • Journal Title

      Neurobiol Dis

      Volume: 45 Issue: 3 Pages: 862-870

    • DOI

      10.1016/j.nbd.2011.12.002

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-22390175, KAKENHI-PUBLICLY-23110526, KAKENHI-PROJECT-23240050, KAKENHI-PROJECT-23659452
  • [Journal Article] Natural history of transthyretin Val30Met familial amyloid polyneuropathy : analysis of late-onset cases from non-endemic areas2012

    • Author(s)
      Koike H, Tanaka F, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Fujitake J, Kawanami T, Kato T, Yamamoto M, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 83 Pages: 152-158

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Neuropathology and omics in motor neuron diseases2012

    • Author(s)
      Tanaka F, Ikenaka K, Yamamoto M, Sobue G
    • Journal Title

      Neuropathology

      Volume: 32 Pages: 458-462

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Loss of TDP-43 causes age-dependent progressive motor neuron degeneration2012

    • Author(s)
      Iguchi Y, Katsuno M, Niwa JI, Takagi S, Ishigaki S, Ikenaka K, Kawai K, Watanabe H, Yamanaka K, Takahashi R, Misawa H, Sasaki S, Tanaka F, Sobue G
    • Journal Title

      Brain

      Volume: 136 Pages: 1371-1382

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Disruption of axonal transport in motor neuron diseases2012

    • Author(s)
      Ikenaka K, Katsuno M, Kawai K, Ishigaki S, Tanaka F, Sobue G
    • Journal Title

      Int J Mol Sci

      Volume: 13 Pages: 1225-1238

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Longitudinal changes of outcome measures in spinal and bulbar muscular atrophy.2012

    • Author(s)
      Hashizume, A., Katsuno, M., Banno, H., Suzuki, K., Suga, N., Mano, T., Atsuta, N., Oe, H., Watanabe, H., Tanaka, F., Sobue, G.
    • Journal Title

      Brain

      Volume: 35 Issue: 9 Pages: 2838-2848

    • DOI

      10.1093/brain/aws170

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy (SBMA).2012

    • Author(s)
      Banno, H., Katsuno, M., Suzuki, K., Tanaka, F., Sobue, G.
    • Journal Title

      Cell Tissue Res

      Volume: 349 Issue: 1 Pages: 313-320

    • DOI

      10.1007/s00441-012-1377-9

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23790986, KAKENHI-PROJECT-24659428
  • [Journal Article] Pathogenesis and therapy of spinal and bulbar muscular atrophy (SBMA)2012

    • Author(s)
      Katsuno M, Tanaka F, Adachi H, Banno H, Suzuki K, Watanabe H, Sobue G
    • Journal Title

      Prog Neurobiol

      Volume: 99 Issue: 3 Pages: 246-256

    • DOI

      10.1016/j.pneurobio.2012.05.007

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986, KAKENHI-PROJECT-24659428
  • [Journal Article] 神経疾患治療の進歩2011年 運動ニューロン疾患の治療の進歩2012

    • Author(s)
      田中章景
    • Journal Title

      神経治療学

      Volume: 29 Pages: 401-403

    • Data Source
      KAKENHI-PLANNED-22129005
  • [Journal Article] Oxidative stress induced by glutathione depletion reproduces pathological modifications of TDP-43linked to TDP-43 proteinopathies2012

    • Author(s)
      Iguchi Y, Katsuno M, Takagi S, Ishigaki S, Niwa J, Hasegawa M, Tanaka F, Sobue G.
    • Journal Title

      Neurobiol Dis

      Volume: 45 Pages: 862-870

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Disruption of axonal transport in motor neuron diseases2012

    • Author(s)
      Ikenaka K, Katsuno M, Kawai K, Ishigaki S, Tanaka F, Sobue G
    • Journal Title

      Int J Mol Sci

      Volume: 13 Pages: 1225-1238

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Skin biopsy is usefui for the antcmortem diagnosis of neuronal intranuclear inclusion disease.2011

    • Author(s)
      Sone J, Tanaka F, Koike H, Inukai A, Katsuno M, Yoshida M, Watanabe H, Sobue G.
    • Journal Title

      Neurology

      Volume: in press

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Spatial distribution of nerve fiber pathology and vasculitis in microscopic polyangiitis-associated neuropathy2011

    • Author(s)
      Morozumi S, Koike H, Tomita M, Kawagashira Y, Iijima M, Katsuno M, Hattori N, Tanaka F, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 70 Pages: 340-348

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Diagnosis of sporadic trans thyretin Val 30 Metfamilial amyloid polyneuropathy : a practical analysis2011

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Tanaka F, Sobue G.
    • Journal Title

      Amyloid

      Volume: 18 Pages: 53-62

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Transforming growth factor-β signaling in motor neuron diseases.2011

    • Author(s)
      Katsuno M, Adachi H, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      Current Mol Med.

      Volume: 11 Pages: 48-56

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Transforming growth factor-β signaling in motor neuron diseases2011

    • Author(s)
      Katsuno M, Adachi H, Banno H, Suzuki K, Tanaka F, Sobue G
    • Journal Title

      Curr Mol Med

      Volume: 11 Pages: 48-56

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Transforming Growth Factor-β Signaling in Motor Neuron Diseases.2011

    • Author(s)
      Katsuno M, Adachi H, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      Curr Mol Med 11

      Pages: 48-56

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] シャルコー・マリー・トゥース病200例のマイクロアレイDNAチップによる遺伝子診断2011

    • Author(s)
      橋口昭大, 徳永章子, 中村友紀, 岡本裕嗣, 有村公良, 小池春樹, 田中章景, 祖父江元, 高嶋博
    • Journal Title

      Peripheral Nerve

      Volume: 22 Pages: 64-71

    • NAID

      10029413624

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Para neoplastic neuropathy : wide-ranging clinicopathological manifestations2011

    • Author(s)
      Koike H, Tanaka F, Sobue G.
    • Journal Title

      Curr Opin Neurol

      Volume: 24 Pages: 504-510

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Skin biopsy is useful for the antemortem diagnosis of neuronal intranuclear inclusion disease2011

    • Author(s)
      Sone J, Tanaka F, Koike H, Inukai A, Katsuno M, Yoshida M, Watanabe H, Sobue G.
    • Journal Title

      Neurology

      Volume: 76 Pages: 1372-1376

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Central nervous system invoivement in n-hexane polyneuropathy demonstrated by MRI and proton MR spectroscopy.2011

    • Author(s)
      Hashizume A, Koike H, Kawagashira Y, Banno H, Suzuki K, Ito M, Katsuno M, Watanabe H, Tanaka F, Naganawa S, Kaneko R, Ishii A, Sobue G.
    • Journal Title

      Clin Neurol Neurosurg

      Volume: in press

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Central nervous system involvement in n-hexane polyneuropathy demonstrated by MRI and proton MR spectroscopy2011

    • Author(s)
      Hashizume A, Koike H, Kawagashira Y, Banno H, Suzuki K, Ito M, Katsuno M, Watanabe H, Tanaka F, Naganawa S, Kaneko R, Ishii A, Sobue G.
    • Journal Title

      Clin Neurol Neurosurg

      Volume: 113 Pages: 493-495

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Clinical features and molecular mechanisms of spinal and bulbar muscular atrophy (SBMA).2010

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Adachi H, Tanaka F, Sobue G.
    • Journal Title

      Adv Exp Med Biol 685

      Pages: 64-74

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis2010

    • Author(s)
      Sone J, Niwa J, Kawai K, Ishigaki S, Yamada S, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci Res

      Volume: 88 Pages: 123-135

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Morphological progression of myelin abnormalities in IgM-monoclonal gammopathy of undetermined significance anti-myelin-associated glycoprotein neuropathy.2010

    • Author(s)
      Kawagashira Y, Koike H, Tomita M, Morozumi S, Iijima M, Nakamura T, Katsuno M, Tanaka F, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 69 Pages: 1143-1157

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Segmental copy-number gain within the region of isopentenyl diphosphate isomerase genes in sporadic amyotrophic lateral sclerosis2010

    • Author(s)
      Kato T, Emi M, Sato H, Arawaka S, Wada M, Kawanami T, Katagiri T, Tsuburaya K, Toyoshima I, Tanaka F, Sobue G, Matsubara K
    • Journal Title

      Biophys Res Commun

      Volume: 402 Pages: 438-442

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis.2010

    • Author(s)
      Sone J, Niwa J, Kawai K, Ishigaki S, Yamada S, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci Res 88

      Pages: 123-135

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis2010

    • Author(s)
      Sone J, Niwa JI, Kawai K, Ishigaki S, Yamada SI, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci Res. 88

      Pages: 123-135

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Doi H, Kondo N, Mizoguchi H, Nitta A, Yamada K, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      J Neurosci. 30

      Pages: 5702-5712

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Clinical features and molecular mechanisms of spinal and bulbar muscular atrophy (SBMA).2010

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Adachi H, Tanaka F, Sobue G.
    • Journal Title

      Adv Exp Med Biol.

      Volume: 685 Pages: 64-74

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy2010

    • Author(s)
      Katsuno, M., Adachi, H., Minamiyama, M., Waza, M., Doi, H., Kondo, N., Mizoguchi, H., Nitta, A., Yamada, K., Banno, H., Suzuki, K., Tanaka, F., Sobue, G.
    • Journal Title

      J. Neurosci 30

      Pages: 5702-5712

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Prevention of ultraviolet B radiation-induced epidermal damage by expression of heat shock protein 70.2010

    • Author(s)
      Matsuda M, Hoshino T, Yamashita Y, Tanaka KI, Maji D, Sato K, Adachi H, Sobue G, Ihn H, Funasaka Y, Mizushima T.
    • Journal Title

      J Biol Chem 285

      Pages: 5848-5858

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] The profile of motor unit number estimation (MUNE) in spinal and bulbar Museular atrophy.2010

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Takeuchi Y, Kawashima M, Suga N, Hashizume A, Hama T, Uchida K, Yamashita F, Nakamura T, Hirayama M, Tanaka F, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry 81

      Pages: 567-571

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis.2010

    • Author(s)
      Sone J, Niwa JI, Kawai K, Ishigaki S, Yamada SI, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci Res. 88

      Pages: 123-135

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Disrupted transforming growth factor-beta signaling in spinal and bulbar muscular atrophy.2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Doi H, Kondo N, Mizoguchi H, Nitta A, Yamada K, Banno H, Suzuki K, Tanaka F, Sobue G
    • Journal Title

      J Neurosci

      Volume: 30 Pages: 5702-5712

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] The profile of motor unit number estimation (MUNE) in spinal and bulbar muscular atrophy2010

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Takeuchi Y, Kawashima M, Suga N, Hashizume A, Hama T, Uchida K, Yamashita F, Nakamura T, Hirayama M, Tanaka F, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry 81

      Pages: 567-571

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] IgM MGUS anti-MAG neuropathy with predominant muscle weakness and extensive muscle atrophy2010

    • Author(s)
      Kawagashira Y, Kondo N, Atsuta N, Iijima M, Koike H, Katsuno M, Tanaka F, Kusunoki S, Sobue G.
    • Journal Title

      Muscle Nerve

      Volume: 42 Pages: 433-435

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Disrupted transforming growth factor-beta signaling in spinal and bulbar muscular atrophy.2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Doi H, Kondo N, Mizoguchi H, Nitta A, Yamada K, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      J Neurosci 30

      Pages: 5702-5712

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Morphological progression of myelin abnormalities in Ig M-monoclonal gammopathy of undetermined significance anti-myelin-associated glycoprotein neuropathy2010

    • Author(s)
      Kawagashira Y, Koike H, Tomita M, Morozumi S, Iijima M, Nakamura T, Katsuno M, Tanaka F, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 69 Pages: 1143-1157

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy.2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Doi H, Kondo N, Mizoguchi H, Nitta A, Yamada K, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      J Neurosci. 30

      Pages: 5702-5712

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] IgM MGUS anti-MAG neuropathy with predominant muscle weakness and extensive muscle atrophy.2010

    • Author(s)
      Kawagashira Y, Kondo N, Atsuta N, Iijima M, Koike H, Katsuno M, Tanaka F, Kusunoki S, Sobue G.
    • Journal Title

      Muscle Nerve

      Volume: 42 Pages: 433-435

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Doi H, Kondo N, Mizoguchi H, Nitta A, Yamada K, Banno H, Suzuki K, Tanaka F, Sobue G
    • Journal Title

      J Neurosci

      Volume: 30 Issue: 16 Pages: 5702-5712

    • DOI

      10.1523/jneurosci.0388-10.2010

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Efficacy and safety of leuprorelin in patients with spinal and bulbar muscular atrophy (JASMITT study) : a multicentre, randomised, double-blind, placebo-controlled trial.2010

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Takeuchi Y, Kawashima M, Yabe I, Sasaki H, Aoki M, Morita M, Nakano I, Kanai K, Ito S, Ishikawa K, Mizusawa H, Yamamoto T, Tsuji S, Hasegawa K, Shimohata T, Nishizawa M, Miyajima H, Kanda F, Watanabe Y, Nakashima K, Tsujino A, Yamashita T, Uchino M, Fujimoto Y, Tanaka F, Sobue Cr ; for the Japan SBMA Interventional Trial for TAP-144-SR (JASMITT) study group.
    • Journal Title

      Lancet Neurol.

      Volume: 9 Pages: 875-884

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Sopher BL, Lin A, Fischbeck KH, Ellerby LM, Morrison RS, Taylor JP, La Spada AR. Polyglutamine-expanded androgen receptor truncation fragments activate a Bax-dependent apoptotic cascade mediated by DP5/Hrk2009

    • Author(s)
      Young JE, Garden GA, Martinez RA, Tanaka F, Sandoval CM, Smith AC
    • Journal Title

      J. Neurosci 29

      Pages: 1987-1997

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Journal Title

      J Biol Chem (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] The significance of carpal tunnel syndrome in transthyretin Val30Met familial amyloid polyneuropathy2009

    • Author(s)
      Koike H, Morozumi S, Kawagashira Y, Iijima M, Yamamoto M, Hattori N, Tanaka F, Nakamura T, Hirayama M, Ando Y, Ikeda SI, Sobue G.
    • Journal Title

      Amyloid

      Volume: 15 Pages: 1-7

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Correlation between pyramidal tract degeneration and widespread white matter involvement in amyotrophic lateral sclerosis: A study with tractography and diffusion-tensor imaging2009

    • Author(s)
      Senda J, Ito M, Watanabe H, Atsuta N, Kawai Y, Katsuno M, Tanaka F, Naganawa S, Fukatsu H, Sobue G.
    • Journal Title

      Amyotroph Lateral Scler. (in press)

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Correlation between pyramidal tract degeneration and widespread white matter involvement in amyotrophic lateral sclerosis : a study with tractography and diffusion-tensor imaging2009

    • Author(s)
      Senda J, Ito M, Watanabe H, Atsuta N, Kawai Y, Katsuno M, Tanaka F, Naganawa S, Fukatsu H, Sobue G.
    • Journal Title

      Amyotroph Lateral Scler. 10

      Pages: 288-294

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno, H., Katsuno, M., Suzuki, K., Takeuchi, Y., Kawashima, M., Suga, N., Takamori, M., Ito, M., Nakamura, T., Matsuo, K., Yamada, S., Oki, Y., Adachi, H., Minamiyama, M., Waza, M., Atsuta, N., Watanabe, H., Fujimoto, Y., Nakashima, T., Tanaka, F., Doyu, M., Sobue, G.
    • Journal Title

      Ann Neurol 65

      Pages: 140-150

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Single nucleotide polymorphism of TAG-1influences IVIg responsiveness of Japanese patients with CIDP2009

    • Author(s)
      Iijima M, Tomita M, Morozumi S, Kawagashira Y, Nakamura T, Koike H, Katsuno M, Hattori N, Tanaka F, Yamamoto M, Sobue G.
    • Journal Title

      Neurology

      Volume: 73 Pages: 1348-1352

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] 17-DMAG ameliorates polyglutamine-mediated motor neuron degeneration through well-preserved proteasome function in a SBMA model mouse2009

    • Author(s)
      Tokui K, Adachi H, Waza M, Katsuno M, Minamiyama M, Doi H, Tanaka K, Hamazaki J, Murata S, Tanaka F, Sobue G
    • Journal Title

      Hum. Mol. Genet 18

      Pages: 898-910

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Intravenous immunoglobulin treatment for painful sensory neuropathy associated with Sjogren's syndrome2009

    • Author(s)
      Morozumi S, Kawagashira Y, Iijima M, Koike H, Hattori N, Katsuno M, Tanaka F, Sobue G.
    • Journal Title

      J Neurol Sci

      Volume: 279 Pages: 57-61

    • NAID

      10025625884

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      Ann Neurol. 65

      Pages: 140-150

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Walking capacity evaluated by the 6-minute walk test in spinal and bulbar muscular atrophy2009

    • Author(s)
      Takeuchi Y, Katsuno M, Banno H, Suzuki K, Kawashima M, Atsuta N, Ito M, Watanabe H, Tanaka F, Sobue G
    • Journal Title

      Muscle Nerve 38

      Pages: 964-971

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] TDP-43 Depletion Induces Neuronal Cell Damage through Dysregulation of Rho Family GTPases.2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Journal Title

      J Biol Chem. 284

      Pages: 22059-22066

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Correlation between pyramidal tract degeneration and widespread white matter involvement in amyotrophic lateral sclerosis : A study with tractography and diffusion-tensor imaging2009

    • Author(s)
      Senda J, Ito M, Watanabe H, Atsuta N, Kawai Y, Katsuno M, Tanaka F, Naganawa S, Fukatsu H, Sobue G
    • Journal Title

      Amyotroph. Lateral Scler (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis2009

    • Author(s)
      Sone J, Niwa J, Kawai K, Ishigaki S, Yamada S, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci Res (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] 17-DMAG ameliorates polyglutamine-mediated motor neuron degeneration through well-preserved proteasome function in a SBMA model mouse2009

    • Author(s)
      Tokui, K., Adachi, H., Waza, M., Katsuno, M., Minamiyama, M., Doi, H., Tanaka, K., Hamazaki, J., Murata, S., Tanaka, F., Sobue, G.
    • Journal Title

      Hum. Mol. Genet. 18

      Pages: 898-910

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis2009

    • Author(s)
      Sone J, Niwa J, Kawai K, Is higaki S, Yamada S, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci Res (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy.2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      Ann Neurol 65

      Pages: 140-150

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] 17-DMAG ameliorates polyglutamine-mediated motor neuron degeneration through well-preserved proteasome function in a SBMA model mouse.2009

    • Author(s)
      Tokui K*, Adachi H*, Waza M, Katsuno M, Minamiyama M, Doi H, Tanaka K, Hamazaki J, Murata S, Tanaka F, Sobue G.
    • Journal Title

      Hum Mol Genet(* Evenly contributed to the study) 18

      Pages: 898-910

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] A role for HSP70 in protecting against indomethacin-induced gastric lesions.2009

    • Author(s)
      Suemasu S, Tanaka KI, Namba T, Ishihara T, Katsu T, Fujimoto M, Adachi H, Sobue G, Takeuchi K, Nakai A, Mizushima T.
    • Journal Title

      J Biol Chem 284

      Pages: 19705-19715

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Heat shock proteins in neurodegenerative diseases : pathogenic roles and therapeutic implications.2009

    • Author(s)
      Adachi H, Katsuno M, Waza M, Minamiyama M, Tanaka F, Sobue G.
    • Journal Title

      Int J Hyperthermia 25

      Pages: 647-654

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Polyglutamine-expanded androgen receptor truncation fragments activate a Bax-dependent apoptotic cascade mediated by DP5/Hrk2009

    • Author(s)
      Young JE, Garden GA, Martinez RA, Tanaka F, Sandoval CM, Smith AC, Sopher BL, Lin A, Fischbeck KH, Ellerby LM, Morrison RS, Taylor JP, La Spada AR.
    • Journal Title

      J Neurosci. 29

      Pages: 1987-1997

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Neuropathology and therapeutic intervention in spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Tanaka F, Sobue G
    • Journal Title

      Int. J. Mol. Sci (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Correlation between pyramidal tract degeneration and widespread white matter involvement in amyotrophic lateral sclerosis : a study with tractography and diffusion-tensor imaging.2009

    • Author(s)
      Senda J, Ito M, Watanabe H, Atsuta N, Kawai Y, Katsuno M, Tanaka F, Naganawa S, Fukatsu H, Sobue G.
    • Journal Title

      Amyotroph Lateral Scler. 10

      Pages: 288-294

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] 17-DMAG ameliorates polyglutamine-mediated motor neuron degeneration through well-preserved proteasome function in an SBMA model mouse2009

    • Author(s)
      Tokui K, Adachi H, Waza M, Katsuno M, Minamiyama M, Doi H, Tanaka K, Hamazaki J, Murata S, Tanaka F, Sobue G.
    • Journal Title

      Hum Mol Genet 18

      Pages: 898-910

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Research Committee on the Neurodegenerative Diseases of Japan. Age at onset influences on wide-ranged clinical features of sporadic amyotrophic lateral sclerosis2009

    • Author(s)
      Atsuta N, Watanabe H, Ito M, Tanaka F, Tamakoshi A, Nakano I, Aoki M, Tsuji S, Yuasa T, Takano H, Hayashi H, Kuzuhara S, Sobue G.
    • Journal Title

      J Neurol Sci. 276

      Pages: 163-169

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] TDP-43 Depletion Induces Neuronal Cell Damage through Dysregulation of Rho Family GTPases2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Journal Title

      J Biol Chem. 284

      Pages: 22059-22066

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G
    • Journal Title

      J Biol Chem. (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Heat shock proteins in neurodegenerative diseases : Pathogenic roles and therapeutic implications.2009

    • Author(s)
      Adachi H, Katsuno M, Waza M, Minamiyama M, Tanaka F, Sobue G.
    • Journal Title

      Int J Hyperthermia 25

      Pages: 647-654

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] TDP-43 Depletion Induces Neuronal Cell Damage through Dysregulation of Rho Family GTPases2009

    • Author(s)
      Iguchi, Y., Katsuno, M., Niwa, J., Yamada, S., Sone, J., Waza, M., Adachi, H., Tanaka, F., Nagata, K., Arimura, N., Watanabe, T., Kaibuchi, K., Sobue, G.
    • Journal Title

      J Biol Chem. 284

      Pages: 22059-22066

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] HSP70 Confers Protection against Indomethacin-Induced Lesions of the Small Intestine.2009

    • Author(s)
      Teita A, Tanaka KI, Yamakawa N, Adachi H, Sobue G, Goto H, Takeuchi K, Mizushima T.
    • Journal Title

      J Pharmacol Exp Ther 330

      Pages: 458-467

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases.2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa JI, Yamada SI, Sone J, Waza M, Adachi H, Tanaka F, Nagata KI, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Journal Title

      J Biol Chem 284

      Pages: 22059-22066

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Heat shock proteins in neurodegenerative diseases : Pathogenic roles and therapeutic implications2009

    • Author(s)
      Adachi H, Katsuno M, Waza M, Minamiyama M, Tanaka F, Sobue G.
    • Journal Title

      Int J Hyperthermia 25

      Pages: 647-654

    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann. Neurol 65

      Pages: 140-150

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] CAG repeat size correlates to electrophysiological motor and sensory phenotypes in SBMA2008

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Takeuchi Y, Atsuta N, Ito M, Watanabe H, Yamashita F, Hori N, Nakamura T, Hirayama M, Tanaka F, Sobue G.
    • Journal Title

      Brain 131

      Pages: 229-239

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Molecular Genetics and Biomarkers of Polyglutamine Diseases2008

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Takeuchi Y, Kawashima M, Adachi H, Tanaka F, Sobue G
    • Journal Title

      Current Mol. Med. 8

      Pages: 221-234

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Refractory Peripheral Neuropathy Study Group of Japan. Prevalence and incidence rates of chronic inflammatory demyelinating polyneuropathy in the Japanese population2008

    • Author(s)
      Iijima M, Koike H, Hattori N, Tamakoshi A, Katsuno M, Tanaka F, Yamamoto M, Arimura K, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry 79

      Pages: 1040-1043

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Cognitive impairment in spinocerebellar ataxia type 62008

    • Author(s)
      Suenaga M, Kawai Y, Watanabe H, Atsuta N, Ito M, Tanaka F, Katsuno M, Fukatsu H, Naganawa S, Sobue G
    • Journal Title

      J. Neurol .Neurosurg. Psychiatry 79

      Pages: 496-499

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] CAG repeat size correlates to electrophysiological motor and sensory phenotypes in SBMA2008

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Takeuchi Y, Atsuta N, Ito M, Watanabe H, Yamashita F, Hori N, Nakamura T, Hirayama M, Tanaka F, Sobue G
    • Journal Title

      Brain 131

      Pages: 229-239

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] CAG repeat size correlates to electrophysiological motor and sensory phenotypes in SBMA2008

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Yamashita F, Hori N, Nakamura T, Hirayama M, Tanaka F, Sobue G
    • Journal Title

      Brain 131

      Pages: 229-239

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Molecular genetics and biomarkers of polyglutamine diseases2008

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Takeuchi Y, Kawashima M, Tanaka F, Adachi H, Sobue G.
    • Journal Title

      Curr Mol Med. 8

      Pages: 221-234

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] CAG repeat size correlates to electrophysiological motor and sensory phenotypes in SBMA2008

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Takeuchi Y, Atsuta N, Ito M, Watanabe H, Yamashita F, Hori N, Nakamura T, Hirayama M, Tanaka F, Sobue G
    • Journal Title

      Brain 131

      Pages: 229-239

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] CAG repeat size correlates to electrophysiological motor and sensory phenotypes in SBMA2008

    • Author(s)
      Suzuki, K., Katsuno, M., Banno, H., Takeuchi, Y., Atsuta, N., Ito, M., Watanabe, H., Yamashita, F., Hori, N., Nakamura, T., Hirayama, M., Tanaka, F., Sobue, G.
    • Journal Title

      Brain 131

      Pages: 229-239

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] A strategy for developing effective amyotropic lateral sclerosis pharmacotherapy: from clinical trials to novel pharmacotherapeutic strategies2008

    • Author(s)
      Yamamoto M, Tanaka F, Tatsumi H, Sobue G.
    • Journal Title

      Expert Opin Pharmacother 9

      Pages: 1845-1857

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Walking capacity evaluated by the 6-minute walk test in spinal and bulbar muscular atrophy2008

    • Author(s)
      Takeuchi Y, Katsuno M, Banno H, Suzuki K, Kawashima M, Atsuta N, Ito M, Watanabe H, Tanaka F, Sobue G
    • Journal Title

      Muscle Nerve 38

      Pages: 946-971

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2007

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G.
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 1-10

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Therapeutic strategies for spinal and bulbar musculara atrophy (SBMA)2007

    • Author(s)
      Katsuno M, Bannno H, Suzuki K, Takeuchi Y, Minamiyama M, Waza M, Adachi H, Tanaka F, Sobue G
    • Journal Title

      Drugns of the Future 32

      Pages: 907-917

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Usefulness of combined fractional anisotropy and apparent diffusion coefficient values for detection of involvement in multiple system atropyh2007

    • Author(s)
      Ito M, Watanabe H, Kawai Y, Atsuta N, Tanaka F, Naganawa S, Fukatsu H, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 78

      Pages: 722-728

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Gene expressions specifically detected in motor neurons (dynactin 1, early growth response 3, Acetyl-CoA transporter, death receptor 5, and cyclin C) differentially correlate to athologic markers in sporadic amyotrophic lateral sclerosis2007

    • Author(s)
      Jiang Y, Yamamoto M, Tanaka F, Ishigaki S, Katsuno M, Adachi H, Niwia J, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Neuropathol Exp Neurol 66

      Pages: 617-627

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD12007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 282

      Pages: 28087-28095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Ataxic vs painful form of paraneoplastic neuropathy2007

    • Author(s)
      Oki Y, Koike H, Iijima M, Mori K, Hattori N, Katsuno M, Nakamura T, Hirayama M, Tanaka F, Shiraishi M, Yazaki S, Nokura K, Yamamoto H,Sobue G
    • Journal Title

      Neurology 69

      Pages: 564-572

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] CHIP overexpression reduces mutant androgen receptor protein and ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2007

    • Author(s)
      Adachi, H., Waza, M., Tokui, K., Katsuno, M., Minamiyama, M., Tanaka, F., Doyu, M., Sobue, G.
    • Journal Title

      J. Neurosci 27

      Pages: 5115-5126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expressions specifically detected in motor neurons (dynactin 1, early growth response 3, acetyl-CoA transporter, death receptor 5, and cyclin C) differentially correlate to pathologic markers in sporadic amyotrophic lateral sclerosis2007

    • Author(s)
      Jiang YM, Yamamoto M, Tanaka F, Ishigaki S, Katsuno M, Adachi H, Niwa J, Doyu M, Yoshida M, Hashizume Y, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 617-627

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Nonmyelinating Schwann cell involvement with well-preserved unmyelinated axons in Charco-Matie-Tooth disease type 1A2007

    • Author(s)
      Koike H, Iijima M, Mori K, Yamamoto M, Hattori N, Katsuno M, Tanaka F, Watanabe H, Doyu M, Yoshikawa H, Sobue G
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 1027-1036

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene Expressions Specifically Detected in Motor Neurons (Dynactin, 1, Early Growth Response 3, Acetyl-CoA Transporter, Death Receptor 5, and Cyclin C) Differentially Correlate to Pathologic Markers in Sporadic Amyotrophic Lateral Sclerosis2007

    • Author(s)
      Jiang, YM, Yamamoto, M, Tanaka, F, Ishigaki, S, Katsuno, M, Adachi, H, Doyu M, Yoshida, M, Hashizume, Y, Sobue, G
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 617-627

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18599002
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Neuropathol Appl Neurobiol 33

      Pages: 135-151

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD12007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Biol Chem 282

      Pages: 28087-28095

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Genetic evidence for a protective role for heat shock factor 1 and heat shock protein 70 against colitis2007

    • Author(s)
      Tanaka K, Namba T, Arai Y, Fujimoto M, Adachi H, Sobue G, Takeuchi K, Nakai A, Mizushima T
    • Journal Title

      J Biol Chem 282

      Pages: 23240-23252

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Intravenous immunoglobulin therapy markedly ameliorates muscle weakness and severe pain in proximal diabetic neuropathy2007

    • Author(s)
      Kawagashira Y, Watanabe H, Oki Y, Iijima M, Koike H, Hattori N, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 78

      Pages: 899-901

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Gene expressions specifically detected in motor neurons (dynactin l, early growth response 3, Acetyl-CoA transporter, death receptor 5, and cyclin C) differentially correlate to athologic markers in sporadic amyotrophic lateral sclerosis2007

    • Author(s)
      Jiang Y, Yamamoto M, Tanaka F, Ishigaki S, Katsuno M, Adachi H, Niwia J, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Neuropathol Exp Neurol 66

      Pages: 617-627

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      Neuropathol Appl Neurobiol 33

      Pages: 135-151

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Genetic evidence for a protective role for heat shock factor l and heat shock protein 70 against colitis2007

    • Author(s)
      Tanaka K, Namba T, Arai Y, Fujimoto M, Adachi H, Sobue G, Takeuchi K, Nakai A, Mizushima T
    • Journal Title

      J Biol Chem 282

      Pages: 23240-23252

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Ataxic vs painful form of paraneoplastic neuropathy2007

    • Author(s)
      Oki Y, Koike H, Iijima M, Mori K, Hattori N, Katsuno M, Nakamura T, Hirayama M, Tanaka F, Shiraishi M, Yazaki S, Nokura K, Yamamoto H, Sobue G
    • Journal Title

      Neurology 69

      Pages: 564-572

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Therapeutic strategies for spinal and bulbar muscular atrophy (SBMA)2007

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Takeuchi Y, Minamiyama M, Waza M, Adachi H, Tanaka F, Sobue G
    • Journal Title

      Drug Future 32

      Pages: 907-917

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi, H, Waza, M, Katsuno, M, Tanaka, F, Doyu, M, Sobue, G
    • Journal Title

      Neuropathol Appl Neurobiol 33

      Pages: 135-151

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18599002
  • [Journal Article] CHIP overexpression reduces mutant androgen receptor protein and ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci 27

      Pages: 5115-5126

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] CHIP Overexpression Reduces Mutant Androgen Receptor Protein and Ameliorates Phenotypes of the Spinal and Bulbar Muscular Atrophy Transgenic Mouse Model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J. Neurosci 27

      Pages: 5115-5126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] CHIP overexpression reduces the mutant AR protein and ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2007

    • Author(s)
      Adachi, H, Waza, M, Tokui, K, Katsuno, M, Minamiyama, M, Tanaka, F, Doyu, M, Sobue, G
    • Journal Title

      J Neurosci 27

      Pages: 5115-5126

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18599002
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis.2007

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G.
    • Journal Title

      Ann N Y Acad Sci. 1086

      Pages: 1-10

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Neuropathol. Appl. Neurobiol 33

      Pages: 135-151

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Gene expressions specifically detected in motor neurons (dynactin 1, early growth response 3, acetyl-CoA transporter, death receptor 5, and cyclin C) differentially correlate to pathologic markers in sporadic amyotrophic lateral sclerosis2007

    • Author(s)
      Jiang YM, Yamamoto M, Tanaka F, Ishigaki S, Katsuno M, Adachi H, Niwa J, Doyu M, Yoshida M, Hashizume Y, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 617-627

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of famlial amyotrophic lateral sclerosis-linked mutant SOD1.2007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Biol Chem. 282

      Pages: 28087-28095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD12007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Biol Chem 282

      Pages: 28087-28095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Neuropathol Appl Neurobiol 33

      Pages: 135-151

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expressions specifically detected in motor neurons(dynactin 1, early growth response 3, acetyl-CoA transporter, death receptor 5, and cyclin C)differentially correlate to pathologic markers in sporadic amyotrophic lateral sclerosis.2007

    • Author(s)
      Jiang YM, Yamamoto M, Tanaka F, shigaki S, Katsuno M, Adachi H, Niwa J, Doyu M, Yoshida M, Hashizune Y, Sobue G.
    • Journal Title

      J Neuropathol Exp Neural. 66

      Pages: 617-627

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD12007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 282

      Pages: 28087-28095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Nonmyelinating Schwann cell involvement with well-preserved unmyelinated axons in Charco-Matie-Tooth disease type 1A2007

    • Author(s)
      Koike H, Iijima M, Mori K, Yamamoto M, Hattori N, Katsuno M, Tanaka F, Watanabe H, Doyu M, Yoshikawa H, Sobue G
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 1027-1036

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Intravenous immunoglobulin therapy markedly ameliorates muscle weakness and severe pain in proximal diabetic neuropathy2007

    • Author(s)
      Kawagashira Y, Watanabe H, Oki Y, Iijima M, Koike H, Hattori N, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 78

      Pages: 899-901

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Usefulness of combined fractional anisotropy and apparent diffusion coefficient values for detection of involvement in multiple system atrophy2007

    • Author(s)
      Ito M, Watanabe H, Kawai Y, Atsuta N, Tanaka F, Naganawa S, Fukatsu H, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 78

      Pages: 722-728

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Therapeutic strategies for spinal and bulbar musculara atrophy (SBMA)2007

    • Author(s)
      Katsuno M, Bannno H, Suzuki K, Takeuchi Y, Minamiyama M, Waza M, Adachi H, Tanaka F, Sobue G
    • Journal Title

      Drugns of the Future 32

      Pages: 907-917

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol in press

    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular-targeted therapy against disease-causing protein2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Alleviating neurodegeneration by an anticancer agent : an Hsp90 inhibitor (17-AAG)2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Sobue G
    • Journal Title

      Ann NY Acad Sci 1086

      Pages: 21-34

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 1-10

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular-targeted therapy against disease-causing protein.2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular targeted therapy against disease-causing protein.2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med (in press)

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann NY Acad Sci 1086

      Pages: 1-10

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker.2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis.2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann NY Acad Sci 1086

      Pages: 1-10

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Alleviating neurodegeneration by an anticancer agent : an Hsp90 inhibitor (17-AAG)2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Sobue G
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 21-34

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pathogenesis, animal models and therapeutics in Spinal and bulbar muscular atrophy (SBMA)2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol 200

      Pages: 8-18

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 1-10

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol (in press)

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Natural history of spinal and bulbar muscular atrophy (SBMA) : A study of 223 Japanese patients.2006

    • Author(s)
      Atsuta N, Watanabe H, Ito M, Banno H, Suzuki K, Katsuno M, Tanaka F, Tamakoshi A, Sobue G
    • Journal Title

      Brain 129

      Pages: 1446-1455

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Reversible disruption of dynactin 1-mediated retrograde axonal transport in polyglutamine-induced motor neuron degeneration2006

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Tokui K, Banno H, Suzuki K, Onoda Y, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 26

      Pages: 12106-12117

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : amolecular-targeted therapy against disease-causing protein2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular targeted therapy against disease-causing protein.2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med (in press)

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular-targeted therapy against disease-causing protein2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol (in press)

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker.2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol (in press)

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Alleviating neurodegeneration by an anticancer agent : an Hsp90 inhibitor (17-AAG).2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Sobue G
    • Journal Title

      Ann NY Acad Sci 1086

      Pages: 21-34

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Pathogenesis, animal models and therapeutics in Spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol 200

      Pages: 8-18

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2006

    • Author(s)
      Tanaka F et al.
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 1-10

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17390253
  • [Journal Article] Alleviating neurodegeneration by an anticancer agent : an Hsp90 inhibitor (17-AAG)2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Sobue G
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 21-34

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Reversible disruption of dynactin 1-mediated retrograde axonal transport in polyglutamine-induced motor neuron degeneration2006

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Tokui K, Banno H, Suzuki K, Onoda Y, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 26

      Pages: 12106-12117

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Natural history of spinal and bulbar muscular atrophy (SBMA) : A study of 223 Japanes patients2006

    • Author(s)
      Atsuta N, Watanabe H, Ito M, Banno H, Suzuki K, Katsuno M, Tanaka F, Tamakoshi A, Sobue G
    • Journal Title

      Brain 129

      Pages: 1446-1455

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pathogenesis, animal models and therapeutics in Spinal and bulbar muscular atrophy (SBMA)2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol 200

      Pages: 8-18

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker.2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Reversible disruption of dynactin 1-mediated retrograde axonal transport in polyglutamine-induced motor neuron degeneration.2006

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Tokui K, Banno H, Suzuki K, Onoda Y, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 26

      Pages: 12106-12117

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Natural history of spinal and bulbar muscular atrophy (SBMA) : A study of 223 Japanese patients2006

    • Author(s)
      Atsuta N, Watanabe H, Ito M, Banno H, Suzuki K, Katsuno M, Tanaka F, Tamakoshi A, Sobue G
    • Journal Title

      Brain 129

      Pages: 1446-1455

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci USA 102

      Pages: 16801-16806

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] The wide spectrum of clinical manifestations in Sjogren's syndrome-associated neuropathy.2005

    • Author(s)
      Mori K, Iijima M, Koike H, Hattori N, Tanaka F, Watanabe H, Katsuno M, Fujita A, Aiba I, Ogata A, Saito T, Asakura K, Yoshida M, Hirayama M, Sobue G
    • Journal Title

      Brain 128

      Pages: 2518-2534

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration.2005

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Sang C, Tanaka F, Inukai A, Doyu M, Sobue G
    • Journal Title

      Nature Med 11

      Pages: 1088-1095

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Clinical and electrophysiologic correlates of IVIg responsiveness in CIDP.2005

    • Author(s)
      Iijima M, Yamamoto M, Hirayama M, Tanaka F, Katsuno M, Mori K, Koike H, Hattori N, Arimura K, Nakagawa M, Yoshikawa H, Hayasaka K, Onodera O, Baba M, Yasuda H, Saito T, Nakazato M, Nakashima K, Kira J, Kaji R, Oka N, Sobue G
    • Journal Title

      Neurology 64

      Pages: 1471-1475

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Widespread nuclear and cytoplasmic mutant androgen receptor accum ulation in spinal and bulbar muscular atrophy.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Waza M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration.2005

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Sang C, Tanaka F, Inukai A, Doyu M, Sobue G
    • Journal Title

      Nature Med 11

      Pages: 1088-1095

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease2005

    • Author(s)
      Katsuno, M., Sang, C., Adachi, H., Minamiyama, M., Waza, M., Tanaka, F., Doyu, M., Sobue, G.
    • Journal Title

      Proc. Natl. Acad. Sci. U.S.A. 102

      Pages: 16801-16806

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Neuronal intranuclear hyaline inclusion disease showing motor-sensory and autonomic neuropathy.2005

    • Author(s)
      Sone J, Hishikawa N, Koike H, Hattori N, Hirayama M, Nagamatsu M, Yamamoto M, Tanaka F, Yoshida M, Hashizume Y, Imamura H, Yamada E, Sobue G
    • Journal Title

      Neurology 65

      Pages: 1538-1543

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Neuronal intranuclear hyaline inclusion disease showing motor-sensory and autonomic neuropathy.2005

    • Author(s)
      Sone J, Hishikawa N, Koike H, Hattori N, Hirayama M, Nagamatsu M, Yamamoto M, Tanaka F, Yoshida M, Hashizume Y, Imamura H, Yamada E, Sobue G
    • Journal Title

      Neurology 65

      Pages: 1538-1543

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Neuronal intranuclear hyaline inclusion disease showing motor-sensory and autonomic neuropathy.2005

    • Author(s)
      Sone J, Hishikawa N, Koike H, Hattori N, Hirayama M, Nagamatsu M, Yamamoto M, Tanaka F, Yoshida M, Hashizume Y, Imamura H, Yamada E, Sobue G
    • Journal Title

      Neurology 65

      Pages: 1538-1543

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration2005

    • Author(s)
      Waza, M., Adachi, H., Katsuno, M., Minamiyama, M., Sang, C., Tanaka, F., Inukai, A., Doyu, M., Sobue, G.
    • Journal Title

      Nat. Med. 11

      Pages: 1088-1095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Neuronal intranuclear hyaline inclusion disease showing motor-sensory and autonomic neuropathy.2005

    • Author(s)
      Sone J, Hishikawa N, Koike H, Hattori N, Hirayama M, Nagamatsu M, Yamamoto M, Tanaka F, Yoshida M, Hashizume Y, Imamura H. Yamada E, Sobue G
    • Journal Title

      Neurology 65

      Pages: 1538-1543

    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] The wide spectrum of clinical manifestations in Sjogren's syndrome-associated neuropathy.2005

    • Author(s)
      Mori K, Iijima M, Koike H, Hattori N, Tanaka F, Watanabe H, Katsuno M, Fujita A, Aiba I, Ogata A, Saito T, Asakura K, Yoshida M, Hirayama M, Sobue G
    • Journal Title

      Brain 128

      Pages: 2518-2534

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Widespread nuclear and cytoplasmic mutant androgen receptor accumulation in spinal and bulbar muscular atrophy.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Waza M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] The wide spectrum of clinical manifestations in Sjogren's syndrome-associated neuropathy.2005

    • Author(s)
      Mori K, Iijima M, Koike H, Hattori N, Tanaka F, Watanabe H, Katsuno M, Fujita A, Aiba I, Ogata A, Saito T, Asakura K, Yoshida M, Hirayama M, Sobue G
    • Journal Title

      Brain 128

      Pages: 2158-2534

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Clinical and electrophysiologic correlates of IVIg responsiveness in CIDP.2005

    • Author(s)
      Iijima M, Yamamoto M, Hirayama M, Tanaka F, Katsuno M, Mori K, Koike H, Hattori N, Arimura K, Nakagawa M, Yoshikawa H, Hayasaka K, Onodera O, Baba M, Yasuda H, Saito T, Nakazato M, Nakashima K, Kira J, Kaji R, Oka N, Sobue G
    • Journal Title

      Neurology 64

      Pages: 1471-1475

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Clinical and electrophysiologic correlates of IVIg responsiveness in CIDP.2005

    • Author(s)
      Iijima M, Yamamoto M, Hirayama M, Tanaka F, Katsuno M, Mori K, Koike H, Hattori N, Arimura K, Nakagawa M, Yoshikawa H, Hayasaka K, Onodera O, Baba M, Yasuda H, Saito T, Nakazato M, Nakashima K, Kira J, Kaji R, Oka N, Sobue G
    • Journal Title

      Neurology 64

      Pages: 1471-1475

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Widespread nuclear and cytoplasmic mutant androgen receptor accumulation in spinal and bulbar muscular atrophy.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Waza M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci Usa 102

      Pages: 16801-16806

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci USA 102

      Pages: 16801-16806

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Clinical and electrophy siologic correlates of IVIg responsiveness in CIDP.2005

    • Author(s)
      Iijima M, Yamamoto M, Hirayama M, Tanaka F, Katsuno M, Mori K, Koike H, Hattori N, Arimura K, Nakagawa M, Yoshikawa H, Hayasaka K, Onodera O, Baba M, Yasuda H, Saito T, Nakazato M, Nakashima K, Kira J, Kaji R, Oka N, Sobue G
    • Journal Title

      Neurology 64

      Pages: 1471-1475

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci USA 102

      Pages: 16801-16806

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration.2005

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Sang C, Tanaka F, Inukai A, Doyu M, Sobue G
    • Journal Title

      Nature Med 11

      Pages: 1088-1095

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Spinal and bulbar muscular atrophy : ligand-dependent pathogenes is and therapeutic perspectives.2004

    • Author(s)
      Katsuno M, Adachi H, Tanaka F, Sobue G
    • Journal Title

      J Mol Med 82

      Pages: 298-307

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Sodium butyrate ameliorates phenotypic expression in a transgenic mouse model of spinal and bulbar muscular atrophy.2004

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Waza M, Sang C, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Sobue G.
    • Journal Title

      Hum Mol Genet 13

      Pages: 1183-1192

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Spinal and bulbar muscular atrophy : ligand-dependent pathogenesis and therapeutic perspectives.2004

    • Author(s)
      Katsuno M, Adachi H, Tanaka F, Sobue G.
    • Journal Title

      J Mol Med 82

      Pages: 298-307

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Sodium butyrate ameliorates phenotypic expression in a transgenic mouse model of spinal and bulbar muscular atrophy.2004

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Waza M, Sang C, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Sobue G
    • Journal Title

      Hum Mol Genet 13

      Pages: 1183-1192

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Dorfin prevents cell death by reducing mitochondrial localizing mutant superoxide dismutase 1 in a neuronal cell model of familial amyotrophic lateral sclerosis.2004

    • Author(s)
      Takeuchi H, Niwa J, Hishikawa N, Ishigaki S, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurochem. 89

      Pages: 64-72

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Transthyretin Val30 Met familial amyloid polyneuropathy in Japan. In : Halcheck IP, Vernon NR editors Amyloids : Composition, Functions and Pathology.

    • Author(s)
      Koike H, Tanaka F, Sobue G.
    • Journal Title

      Nova Science Publishers

      Volume: (in press)

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Presentation] 両アレル性AAGGGおよびACAGGリピート伸長を持つCerebellar ataxia with neuropathy and vestibular areflexia syndrome (CANVAS) 剖検2例におけるRNA fociの形成2024

    • Author(s)
      和田大司, 土井宏, 大久保正紀, 多田美紀子, 上田直久, 冨永和奏, 小池春樹, 中村治子, 高橋慶太, 國井美紗子, 宮地洋輔, 東山雄一, 宮武聡子, 勝野雅央, 藤井誠志, 松本直通, 竹内英之 ,田中章景.
    • Organizer
      日本小脳学会 第14回学術大会
    • Data Source
      KAKENHI-PROJECT-21K07440
  • [Presentation] Analysis of genetic background of adult leukoencephalopathies.2023

    • Author(s)
      土井宏, 大久保正紀, 深井綾子, 國井美紗子, 和田大司, 岸田日帯, 工藤洋祐, 山口滋紀, 高橋慶太, 多田美紀子, 宮武聡子, 伊藤泰広, 上田直久, 児矢野繁, 竹内英之, 松本直通, 田中章景
    • Organizer
      第64回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-21K07298
  • [Presentation] Different responses of microglia-specific TAK1 deletion in the mouse models of Alzheimer's disease.2023

    • Author(s)
      Katsumoto A, Miller C, Xu G, Li X, Sato H, Lamb B, Tanaka F
    • Organizer
      第64回 日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-21K07420
  • [Presentation] Pathological evaluations of patients of CANVAS with biallelic expansion of AAGGG and ACAGG repeats.2023

    • Author(s)
      和田大司, 土井宏, 大久保正紀, 多田美紀子, 上田直久, 冨永和奏, 小池春樹, 細田航平, 中村治子, 高橋慶太, 國井美紗子, 宮地洋輔, 東山雄一, 宮武聡子, 勝野雅央, 藤井誠志, 松本直通, 竹内英之, 田中章景
    • Organizer
      第64回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-21K07298
  • [Presentation] Pathological evaluations of patients of CANVAS with biallelic expansion of AAGGG and ACAGG repeats2023

    • Author(s)
      Wada T, Doi H, Okubo M, Tada M, Ueda N, Tominaga W, Koike H, Hosoda K, Nakamura H, Takahashi K, Kunii M, Miyaji Y, Higashiyama Y, Miyatake S, Katsuno M, Fujii S, Matsumoto N, Takeuchi H, Tanaka F.
    • Organizer
      64th Annual Meeting of the Japnese Society of Neurology
    • Data Source
      KAKENHI-PROJECT-21K07440
  • [Presentation] Nogo受容体の内因性アンタゴニストであるLOTUSはALSモデルマウスの症状を改善する2022

    • Author(s)
      池田拓也,髙橋慶太,橋口俊太,田中健一,土井宏,竹居光太郎,竹内英之,田中章景
    • Organizer
      第40回日本神経治療学会学術集会
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] Ser522-phosphorylation of CRMP1 modulates the motor function of amyotrophic lateral sclerosis mice.2022

    • Author(s)
      浅野徹也,中村治子,川本裕子,多田美紀子,木村弥生,高野洋志,八尾良司,橋口俊太,髙橋慶太,國井美紗子,田中健一,五嶋良郎,中村史雄,竹内英之,土井宏,田中章景
    • Organizer
      第63回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] Ethosuximide improves clinical and pathological phenotypes of SCA42 mouse model.2022

    • Author(s)
      Shunta Hashiguchi, Hiroshi Doi, Masaki Okubo, Misako Kunii, Keita Takahashi, Mikiko Tada, Kenichi Tanaka, Hideyuki Takeuchi, Taro Ishikawa, Fumiaki Tanaka
    • Organizer
      第63回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-21K07298
  • [Presentation] CRMP1のリン酸化阻害は筋萎縮性側索硬化症モデルマウスの生存期間,運動機能の改善をもたらす2022

    • Author(s)
      浅野徹也,中村治子,川本裕子,多田美紀子,木村弥生,高野洋志,八尾良司,橋口俊太,髙橋慶太,國井美紗子,田中健一,五嶋良郎,中村史雄,竹内英之,土井宏,田中章景
    • Organizer
      第40回日本神経治療学会学術集会
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] LOTUS, an Nogo receptor antagonist, improves phenotypes of ALS.2022

    • Author(s)
      池田拓也,髙橋慶太,橋口俊太,國井美紗子,田中健一,多田美紀子,土井宏,竹居光太郎,竹内英之,田中章景
    • Organizer
      第63回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] ミクログリアに対するインフラマソームを介したシポニモドの抗炎症作用2022

    • Author(s)
      古宮裕泰,竹内英之,小笠原陽大,髙橋慶太,田中健一,多田美紀子,土井宏,田中章景
    • Organizer
      第34回日本神経免疫学会学術集会
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] Axonal accumulation of phosphorylated CRMP1 in human ALS spinal cords.2022

    • Author(s)
      川本裕子,浅野徹也,中村治子,多田美紀子,橋口俊太,髙橋慶太,國井美紗子,田中健一,五嶋良郎,竹内英之,土井宏,中村史雄,田中章景
    • Organizer
      第63回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] ミクログリア特異的TAK1遺伝子除去によるタウ/アミロイド病理変化2022

    • Author(s)
      8.勝元 敦子, Crystal Miller, Guixiang Xu, Xiaoxia Li, 佐藤瞳, Bruce Lamb, 田中章景
    • Organizer
      第41回日本認知症学会
    • Data Source
      KAKENHI-PROJECT-21K07420
  • [Presentation] Ethosuximide improves clinical and pathological phenotypes of SCA42 mouse model.2022

    • Author(s)
      Masaki Okubo, Hiroshi Doi, Shunta Hashiguchi, Misako Kunii, Keita Takahashi, Mikiko Tada, Kenichi Tanaka, Hideyuki Takeuchi, Taro Ishikawa, Fumiaki Tanaka
    • Organizer
      第45回日本神経科学大会
    • Data Source
      KAKENHI-PROJECT-21K07298
  • [Presentation] A novel automated quantitative system for LOTUS, a candidate biomarker for disease activity in MS2022

    • Author(s)
      高橋慶太、竹内英之、国井美紗子、池田拓也、橋口俊太、田中健一、勝元敦子、多田美紀子、土井宏、田中章景
    • Organizer
      第63回日本神経学会学術大会,
    • Data Source
      KAKENHI-PROJECT-20K07761
  • [Presentation] Anti-inflammatory effects of siponimod on astrocyte.2022

    • Author(s)
      小笠原陽大,竹内英之,古宮裕泰,小川有紀,髙橋慶太,橋口俊太,國井美紗子,多田美紀子,田中健一,土井宏,田中章景
    • Organizer
      第63回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] Anti-inflammatory effects of siponimod on astrocyte.2022

    • Author(s)
      小笠原陽大,竹内英之,古宮裕泰,小川有紀,髙橋慶太,橋口俊太,國井美紗子,多田美紀子,田中健一,土井宏,田中章景
    • Organizer
      第45回日本神経科学大会/第65回日本神経化学会大会/第32回日本神経回路学会大会
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] Ser522-phosphorylation of CRMP1 modulates the motor function of amyotrophic lateral sclerosis mice.2022

    • Author(s)
      浅野徹也,中村治子,川本裕子,多田美紀子,木村弥生,高野洋志,八尾良司,橋口俊太,髙橋慶太,國井美紗子,田中健一,五嶋良郎,中村史雄,竹内英之,土井宏,田中章景
    • Organizer
      第45回日本神経科学大会/第65回日本神経化学会大会/第32回日本神経回路学会大会
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] RNA helicases DDX5 and DDX17 are involved in sporadic ALS pathology.2021

    • Author(s)
      Mikiko Tada, Hiroshi Doi, Shingo Ikeda, Shunta Hashiguchi, Keita Takahashi, Misako Kunii, Kenichi Tanaka, Shigeru Koyano, Hideyuki Takeuchi, Fumiaki Tanaka
    • Organizer
      62nd Annual Meeting of Japanese Society of Neurology
    • Data Source
      KAKENHI-PROJECT-19K07845
  • [Presentation] Ablation of interleukin-19 improves motor function in a mouse model of amyotrophic lateral sclerosis.2021

    • Author(s)
      Komiya H, Takeuchi H, Ogawa Y, Ogasawara A, Takahashi K, Doi H, Tanaka F.
    • Organizer
      15th International Society of Neuroimmunology Congress
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] An Endogenous Nogo receptor antagonist LOTUS, a novel therapeutic target for ALS2021

    • Author(s)
      Takuya Ikeda, Keita Takahashi, Hiroshi Doi, Kohtaro Takei, Hideyuki Takeuchi, Fumiaki Tanaka
    • Organizer
      Pan-Asia Consortium for Treatment and Research in ALS
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-20K07761
  • [Presentation] Identification of intronic repeat expansion of RFC1 by long-read sequencer.2021

    • Author(s)
      土井宏、中村治子、宮武聡子、三橋里美、水口剛、大久保正紀、工藤洋祐、浅野徹也、國井美紗子、田中健一、多田美紀子、上木英人、竹内英之、松本直通、田中章景
    • Organizer
      第62回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-21K07298
  • [Presentation] Ablation of interleukin-19 improves motor function in a mouse model of amyotrophic lateral sclerosis.2021

    • Author(s)
      Komiya H, Takeuchi H, Ogasawara A, Ogawa Y, Takahashi K, Doi H, Tanaka F.
    • Organizer
      Pan-Asia Consortium for Treatment and Research in ALS
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] CCR2 is localized in microglia and neurons, as well as infiltrating monocytes, in the lumbar spinal cord of ALS mice.2021

    • Author(s)
      Ogasawara A, Takeuchi H, Komiya H, Ogawa Y, Takahashi K, Doi H, Tanaka F.
    • Organizer
      Pan-Asia Consortium for Treatment and Research in ALS
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] Anti-inflammatory effects of siponimod on astrocyte.2021

    • Author(s)
      Ogasawara A, Takeuchi H, Komiya H, Ogawa Y, Takahashi K, Doi H, Tanaka F.
    • Organizer
      15th International Society of Neuroimmunology Congress
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-21K07465
  • [Presentation] Ataxic phenotype with altered CaV3.1 channel property in a mouse model for spinocerebellar ataxia 422020

    • Author(s)
      橋口俊太,土井宏,國井美紗子,中村行宏,志牟田美佐,鈴木江津子,大久保正紀, 窪田瞬,多田美紀子,児矢野繁,竹内英之,石川太郎,田中章景
    • Organizer
      第61回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-18K07503
  • [Presentation] Evaluation of serum LOTUS as a biomarker of neuroinflammation2020

    • Author(s)
      Keita Takahashi, Hideyuki Takeuchi, Misako Kunii, Ken-ichi Tanaka, Mikiko Tada, Kohtaro Takei, Fumiaki Tanaka
    • Organizer
      日本神経学会
    • Data Source
      KAKENHI-PROJECT-20K07761
  • [Presentation] DDX5 accumulates in neuronal cytoplasmic inclusions with TDP-43 in SALS.2020

    • Author(s)
      Mikiko Tada, Hiroshi Doi, Shingo Ikeda, Shunta Hashiguchi, Atsuko Katsumoto, Misako Kunii, Keita Takahashi, Koyano Shigeru, Hideyuki Takeuchi, Fumiaki Tanaka
    • Organizer
      61st Annual Meeting of the Japanese Society of Neurology, Okayama, 2020,5.
    • Data Source
      KAKENHI-PROJECT-19K07845
  • [Presentation] Genetic analysis of adult leukoencephalopathies2020

    • Author(s)
      土井宏,大久保正紀,深井綾子,國井美紗子,岸田日帯,高橋慶太,勝元敦子,多田美紀子,藤田京志,三橋里美,宮武聡子,伊藤泰広, 上田直久,児矢野繁,竹内英之,松本直通,田中章景
    • Organizer
      第61回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-18K07503
  • [Presentation] DDX5 accumulates in neuronal cytoplasmic inclusions with TDP-43 in SALS.2020

    • Author(s)
      Mikiko Tada,Hiroshi Doi,Shingo Ikeda,Shunta Hashiguchi,Atsuko Katsumoto,Misako Kunii,Keita Takahashi,Koyano Shigeru, Hideyuki Takeuchi, Fumiaki Tanaka
    • Organizer
      第61回日本神経学会総会
    • Data Source
      KAKENHI-PROJECT-19K07845
  • [Presentation] Ataxic phenotype with altered CaV3.1 channel property in a mouse model for spinocerebellar ataxia 42.2019

    • Author(s)
      Hiroshi Doi, Shunta Hashiguchi, Misako Kunii, Yukihiro Nakamura, Misa Shimuta, Etsuko Suzuki, Masaki Okubo, Toshikuni Sasaoka, Hideyuki Takeuchi, Taro Ishikawa, Fumiaki Tanaka
    • Organizer
      Neuroscience 2019
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-18K07503
  • [Presentation] Clinical characteristics of four patients with ERCC4 mutations manifesting ataxia phenotype.2018

    • Author(s)
      土井 宏, 児矢野繁, 宮武聡子, 中島伸二, 中沢由華, 國井美紗子, 勝元敦子, 深井綾子, 荻朋男, 竹内英之, 松本直通, 田中章景
    • Organizer
      第59回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-18K07503
  • [Presentation] 血管内大細胞性B細胞リンパ腫を併発し、R-CHOP療法で劇的な改善を認めた抗SRP抗体陽性筋炎の1例2018

    • Author(s)
      古宮 裕泰, 児矢野 繁, 土井 宏, 西野 一三, 竹内 英之, 田中 章景
    • Organizer
      第36回日本神経治療学会学術集会
    • Data Source
      KAKENHI-PROJECT-18K07504
  • [Presentation] 四肢筋力低下で発症したMcLeod症候群の55歳男性例2017

    • Author(s)
      多賀須 むつき,古宮 裕泰,多田 美紀子,植松 絵里,田中 健一,上木 英人,児矢野 繁,田中 章景
    • Organizer
      第220回日本神経学会関東・甲信越地方会
    • Place of Presentation
      砂防会館(東京都)
    • Year and Date
      2017-03-04
    • Data Source
      KAKENHI-PROJECT-15K18367
  • [Presentation] Exome analysis of autosomal recessive or sporadic cases of cerebellar ataxia and spastic paraplegia.2017

    • Author(s)
      Doi H., Koyano S., Kunii M., Miyatake S., Nakajima S., Hashiguchi S., Ikeda S., Kubota S., Hirama N., Ogawa Y., Takahashi K., Tada M., Tanaka K., Takeuchi H., Matsumoto N., Tanaka F.
    • Organizer
      XXIII World Congress of Neurology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09344
  • [Presentation] The clinical and pathological features of autosomal-dominant SCA with CACNA1G mutation.2016

    • Author(s)
      Doi H, Koyano S, Shiina M, Ogata K, Hirashima F, Inoue Y, Hashiguchi S, Kunii M, Kishida H, Yokota T, Mizusawa H, Mitsui J, Tsuji S, Matsumoto N, Ishikawa K and Tanaka F.
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸国際会議場(兵庫)
    • Data Source
      KAKENHI-PROJECT-15K09344
  • [Presentation] 多系統萎縮症と尿酸との関連(病型別の検討)2016

    • Author(s)
      児矢野繁、上田直久,東山雄一,上木英人,岸田日帯,木村活生,齋藤麻美,中江啓晴,釘本千春,土井宏,田中章景
    • Organizer
      第57回神経学会総会
    • Place of Presentation
      神戸コンベンションセンター神戸国際会議場(兵庫県)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PROJECT-26461315
  • [Presentation] RNF213多型を認め、中大脳動脈領域に広範囲の脳梗塞を生じた39歳男性例2016

    • Author(s)
      浅野 敬一郎, 三宅 綾子, 中江 啓晴, 田中 健一, 多田 美紀子, 土井 宏, 児矢野 繁, 田中 章景
    • Organizer
      第217回日本神経学会関東・甲信越地方会
    • Place of Presentation
      砂防会館(東京都)
    • Year and Date
      2016-06-04
    • Data Source
      KAKENHI-PROJECT-15K18367
  • [Presentation] LOTUS protein, an endogenous Nogo receptor antagonist, is associated with induction of experimental autoimmune encephalomyelitis (EAE)2016

    • Author(s)
      Takahashi, K., Kurihara, Y., Takeuchi, H., Takei, K., Tanaka, F.
    • Organizer
      第3回MS Summer College
    • Place of Presentation
      ルネッサンスサッポロホテル(北海道札幌市)
    • Year and Date
      2016-08-06
    • Data Source
      KAKENHI-PROJECT-15K14353
  • [Presentation] 神経機能分子LOTUSは実験的自己免疫性脳炎の免疫病態にも関与する2016

    • Author(s)
      高橋慶太, 栗原裕司, 竹内英之, 竹居光太郎, 田中章景
    • Organizer
      第28回日本神経免疫学会
    • Place of Presentation
      長崎ブリックホール(長崎県長崎市)
    • Year and Date
      2016-09-29
    • Data Source
      KAKENHI-PROJECT-15K14353
  • [Presentation] 内在性Nogo受容体アンタゴニストLOTUSは実験的自己免疫性脳炎の病態に関与する2016

    • Author(s)
      高橋慶太, 栗原裕司, 田中章景, 竹居光太郎
    • Organizer
      第59回日本神経化学会
    • Place of Presentation
      福岡国際会議場(福岡県福岡市)
    • Year and Date
      2016-09-08
    • Data Source
      KAKENHI-PROJECT-15K14353
  • [Presentation] 内在性Nogo受容体アンタゴニストLOTUSは実験的自己免疫性脳炎の発症に関与する2016

    • Author(s)
      高橋慶太, 栗原裕司, 田中章景, 竹居光太郎
    • Organizer
      第39回日本神経科学会
    • Place of Presentation
      パシフィコ横浜(神奈川県横浜市)
    • Year and Date
      2016-07-20
    • Data Source
      KAKENHI-PROJECT-15K14353
  • [Presentation] IgG4関連ニューロパチーと鑑別を要した家族性アミロイドポリニューロパチー(ATTR-FAP)の71歳男性例2016

    • Author(s)
      古宮 裕泰, 多田 美紀子, 石戸 淳一, 多賀須 むつき, 田中 健一, 上木 英人, 児矢野 繁, 田中 章景
    • Organizer
      第218回日本神経学会関東・甲信越地方会
    • Place of Presentation
      砂防会館(東京都)
    • Year and Date
      2016-09-03
    • Data Source
      KAKENHI-PROJECT-15K18367
  • [Presentation] Association of CSF levels of LOTUS protein with disease activity in multiple sclerosis.2015

    • Author(s)
      Takahashi, K., Suzuki, Y., Takei, K., Tanaka, F.
    • Organizer
      第56回日本神経学会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K14353
  • [Presentation] Late-onset spastic ataxia phenotype related to a novel homozygous DDHD2 mutation2015

    • Author(s)
      土井 宏、吉田 邦広、牛山 雅夫、谷 佳津子、松本 直通、田中 章景
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市中央区)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-26670445
  • [Presentation] 孤発性筋萎縮性側索硬化症におけるMatrin3の病理学的検討2015

    • Author(s)
      多田 美紀子、土井 宏、児矢野 繁、田中 章景
    • Organizer
      第56回日本神経病理学会総会
    • Place of Presentation
      九州大学医学部百年講堂(福岡県福岡市東区)
    • Year and Date
      2015-06-03
    • Data Source
      KAKENHI-PROJECT-25293207
  • [Presentation] SCA2病変におけるTDP-43細胞内局在2015

    • Author(s)
      児矢野 繁、多田 美紀子、柳下 三郎、内原 俊記,田中 章景
    • Organizer
      第56回日本神経病理学会総会
    • Place of Presentation
      九州大学医学部百年講堂(福岡県福岡市東区)
    • Year and Date
      2015-06-03
    • Data Source
      KAKENHI-PROJECT-25293207
  • [Presentation] 孤発性筋萎縮性側索硬化症におけるMatrin3の病理学的検討2015

    • Author(s)
      多田美紀子,土井宏,児矢野繁,田中章景
    • Organizer
      第56回日本神経病理学会総会
    • Place of Presentation
      九州大学医学部百年講堂(福岡県福岡市)
    • Year and Date
      2015-06-03
    • Data Source
      KAKENHI-PROJECT-15K18367
  • [Presentation] SCA2病変におけるTDP-43細胞内局在2015

    • Author(s)
      児矢野 繁、多田 美紀子、柳下 三郎、内原 俊記、田中 章景
    • Organizer
      第56回日本神経病理学会総会
    • Place of Presentation
      九州大学医学部百年講堂(福岡県福岡市東区)
    • Year and Date
      2015-06-03
    • Data Source
      KAKENHI-PROJECT-26670445
  • [Presentation] Late-onset spastic ataxia phenotype related to a novel homozygous DDHD2 mutation.2015

    • Author(s)
      土井宏,吉田邦広,牛山雅夫,谷佳津子,松本直通,田中章景
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟)
    • Year and Date
      2015-05-23
    • Data Source
      KAKENHI-PROJECT-15K09344
  • [Presentation] Matrin 3 is a component of neuronal cytoplasmic inclusion of motor neuron in SALS2015

    • Author(s)
      Mikiko Tada, Hiroshi Doi, Shigeru Koyano, Fumiaki Tanaka
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K18367
  • [Presentation] 孤発性筋萎縮性側索硬化症におけるMatrin3の病理学的検討2015

    • Author(s)
      多田 美紀子、土井 宏、児矢野 繁、田中 章景
    • Organizer
      第56回日本神経病理学会総会
    • Place of Presentation
      九州大学医学部百年講堂(福岡県福岡市東区)
    • Year and Date
      2015-06-03
    • Data Source
      KAKENHI-PROJECT-26670445
  • [Presentation] Association of LOTUS, a functional molecule for axonal growth, with disease activity in Multiple sclerosis and experimental autoimmune encephalomyelitis (EAE)2015

    • Author(s)
      Takahashi, K., Takei, K., Tanaka, F.
    • Organizer
      第2回MS Summer College
    • Place of Presentation
      ルネッサンスサッポロホテル(北海道札幌市)
    • Year and Date
      2015-08-01
    • Data Source
      KAKENHI-PROJECT-15K14353
  • [Presentation] Late-onset spastic ataxia phenotype related to a novel homozygous DDHD2 mutation2015

    • Author(s)
      土井 宏、吉田 邦広、牛山 雅夫、谷 佳津子、松本 直通、田中 章景
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市中央区)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-25293207
  • [Presentation] Analysis of major amyotrophic lateral sclerosis genes in Japan.2014

    • Author(s)
      Ryoichi Nakamura, Jun Sone, Naoki Atsuta, Hazuki Watanabe, Akihiro Hirakawa, Hirohisa Watanabe, Mizuki Ito, Jo Senda, Masahisa Katsuno, Fumiaki Tanaka, Yuishin Izumi, Mitsuya Morita, Kotaro Ogaki, Akira Taniguchi, Ikuko Aiba,Koichi Mizoguchi, Koichi Okamoto, Kazuko Hasegawa, Masashi Aoki, Akihiro Kawata
    • Organizer
      64th Annual Meeting of the American Society of Human Genetics
    • Place of Presentation
      San Diego convention center, San Diego, USA
    • Year and Date
      2014-10-21
    • Data Source
      KAKENHI-PROJECT-24591257
  • [Presentation] 皮膚生検により診断したNeuronal intranuclear inclusion disease 15例の検討2014

    • Author(s)
      曽根淳、荒木邦彦、藤岡祐介、稲垣智則、桝田道人、岩崎靖、吉田眞理、田中章景、祖父江元
    • Organizer
      第33回日本認知症学会学術集会
    • Place of Presentation
      パシフィコ横浜、神奈川県横浜市
    • Year and Date
      2014-12-01
    • Data Source
      KAKENHI-PROJECT-24591257
  • [Presentation] 皮膚生検により診断したNeuronal intranuclear inclusion disease 18 例の臨床学的特徴2014

    • Author(s)
      曽根淳、北川尚之、菅原恵梨子、違口正明、稲垣智則、吉村元、石井淳子、川本未知、森恵子、岩崎靖、吉田眞理、田中章景、祖父江元
    • Organizer
      第55回日本神経学会総会
    • Place of Presentation
      福岡国際会議場、福岡県福岡市
    • Year and Date
      2014-05-24
    • Data Source
      KAKENHI-PROJECT-24591257
  • [Presentation] Strategy to discover new ALS causative genetic variants in Japanese ALS patients.2014

    • Author(s)
      J.Sone, R.Nakamura, M.Nakatochi, H.Watanabe, N.Atsuta, F.Tanaka, G.Sobue.
    • Organizer
      64th Annual Meeting of the American Society of Human Genetics
    • Place of Presentation
      San Diego convention center, San Diego, USA
    • Year and Date
      2014-10-21
    • Data Source
      KAKENHI-PROJECT-24591257
  • [Presentation] 皮膚生検によるNeuronal intranuclear inclusion diseaseの診断について2014

    • Author(s)
      曽根淳、北川尚之、岩崎靖、吉田眞理、田中章景、祖父江 元
    • Organizer
      第32回日本神経治療学会総会
    • Place of Presentation
      東京ドームホテル、東京都文京区
    • Year and Date
      2014-11-22
    • Data Source
      KAKENHI-PROJECT-24591257
  • [Presentation] Antemortem diagnosis of Neuronal intranuclear inclusion disease.2014

    • Author(s)
      Jun Sone, Naoyuki Kitagawa, Tomonori Inagaki, Yasushi Iwasaki,Mari Yoshida, Fumiaki Tanaka, Gen Sobue
    • Organizer
      Neuroscience 2014
    • Place of Presentation
      Washington convention center, Washington, USA
    • Year and Date
      2014-11-19
    • Data Source
      KAKENHI-PROJECT-24591257
  • [Presentation] Clinical feature of 19 cases of Neuronal intranuclear inclusion disease diagnosed by skin biopsy.2014

    • Author(s)
      Jun Sone, Naoyuki Kitagawa, Eriko Sugawara, Masaaki Iguchi, Tomonori Inagaki, Hajime Yoshimura, Junko Ishii, Michi Kawamoto, Keiko Mori, Kunihiko Araki, Michihito Masuda, Mari Yoshida, Yasushi Iwasaki, Fumiaki Tanaka, Gen Sobue
    • Organizer
      XVIII International Congress of Neuropathology
    • Place of Presentation
      Sheraton Rio Hotel, Rio De Janeiro, Brasil
    • Year and Date
      2014-09-15
    • Data Source
      KAKENHI-PROJECT-24591257
  • [Presentation] 熱ショック因子1は球脊髄性筋萎縮症の運動神経変性を抑える2013

    • Author(s)
      近藤直英, 勝野雅央, 足立弘明, 南山 誠, 土井英樹, 松本慎二郎, 宮崎 雄, 飯田 円, 中辻秀朗, 藤内玄規, 石垣診祐, 藤岡祐介, 渡辺宏久, 田中章景, 祖父江元
    • Organizer
      第36回日本神経科学大会 Neuro 2013
    • Place of Presentation
      国立京都国際会館(京都府京都市左京区)
    • Data Source
      KAKENHI-PROJECT-25293207
  • [Presentation] Neuronal intranuclear inclusion disease 皮膚生検による診断について2013

    • Author(s)
      曽根淳、北川尚之、岩崎靖、吉田眞理、田中章景、祖父江元
    • Organizer
      第41回 臨床神経病理懇話会,愛知医科大学
    • Place of Presentation
      愛知医科大学、長久手市
    • Data Source
      KAKENHI-PROJECT-24591257
  • [Presentation] 皮膚生検によるNeuronal intranuclear inclusion diseaseの診断2013

    • Author(s)
      曽根淳、北川尚之、岩崎靖、吉田眞理、田中章景、祖父江元
    • Organizer
      第54回日本神経病理学会総会学術研究会
    • Place of Presentation
      タワーホール船堀、東京都江戸川区
    • Data Source
      KAKENHI-PROJECT-24591257
  • [Presentation] 運動ニューロン特異的TDP-43ノックアウトマウスの病理学的検討2013

    • Author(s)
      井口洋平, 勝野雅央, 丹羽淳一, 高木伸之介, 山中宏二, 三澤日出巳, 高橋良輔, 佐々木彰一, 田中章景, 祖父江元
    • Organizer
      第54回日本神経学会学術大会
    • Place of Presentation
      東京国際フォーラム(東京都千代田区)
    • Data Source
      KAKENHI-PROJECT-25293207
  • [Presentation] dynactin-1ノックアウトによる孤発性ALSモデルマウスの作成と病態解析2013

    • Author(s)
      河合香里, 池中建介, 勝野雅央, 井口洋平, 勝又 竜, 田中章景, 祖父江元
    • Organizer
      第54回日本神経学会学術大会
    • Place of Presentation
      東京国際フォーラム(東京都千代田区)
    • Data Source
      KAKENHI-PROJECT-25293207
  • [Presentation] Neuronal intranuclear inclusion diseaseの原因遺伝子探索2013

    • Author(s)
      曽根淳、田中章景、中村亮一、北川尚之、菅野純夫、鈴木穣、森下真一、祖父江元
    • Organizer
      第54回日本神経学会学術大会
    • Place of Presentation
      東京国際フォーラム、東京都千代田区
    • Data Source
      KAKENHI-PROJECT-24591257
  • [Presentation] ALS疾患関連遺伝子の探索2013

    • Author(s)
      田中章景
    • Organizer
      新学術領域研究 脳疾患ゲノム情報班会議
    • Place of Presentation
      東京大学小柴ホール(東京都)
    • Year and Date
      2013-02-09
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Presentation] Neuronal intranuclear inclusion diseaseの生前診断2013

    • Author(s)
      曽根淳、北川尚之、岩崎靖、吉田眞理、田中章景、祖父江元
    • Organizer
      第24回日本末梢神経学会学術集会
    • Place of Presentation
      朱鷺メッセ、新潟市
    • Data Source
      KAKENHI-PROJECT-24591257
  • [Presentation] miR-196aはSBMAにおいて異常ARmRNAの不安定化を促進し表現型を有意に改善させる2012

    • Author(s)
      宮崎雄, 足立弘明, 勝野雅央, 南山誠, 蒋月梅, 土井英樹, 松本慎二郎, 近藤直英, 飯田円, 藤内玄規, 田中章景, 村松慎一, 祖父江元
    • Organizer
      第53回日本神経学会総会
    • Place of Presentation
      東京千代田区(東京国際フォーラム)
    • Year and Date
      2012-05-24
    • Data Source
      KAKENHI-PROJECT-23390231
  • [Presentation] 孤発性および家族性ALS疾患関連遺伝子の探索2012

    • Author(s)
      田中章景
    • Organizer
      新学術領域研究 脳疾患ゲノム情報班会議
    • Place of Presentation
      東京大学小柴ホール(東京都)
    • Year and Date
      2012-09-01
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Presentation] Naratriptan ameliorates SBMA pathology by the repression of CGRP1-activated JNK pathway2012

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Iida M, Ishigaki S, Fujioka Y, Matsumoto S, Miyazaki Y, Tanaka F, Kurihara H, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Viral delivery of miR-196a ameliorates the SBMA phenotype via the silencing of CELF22012

    • Author(s)
      Miyazaki Y, Adachi H, Katsuno M, Tanaka F, Muramatsu SI, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] p62/SQSTM1 removes toxic mutant androgen receptor in spinal bulbar muscular atrophy model mouse2012

    • Author(s)
      Adachi H, Doi H, Katsuno M, Matsumoto S, Kondo N, Miyazaki Y, Tohnai G, Iida M, Tanaka F, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] 筋萎縮性側索硬化症、及びそのモデルマウスの腰髄におけるリン酸化Cofilinの評価2012

    • Author(s)
      勝又 竜, 勝野雅央, 田中章景, 祖父江元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京国際フォーラム(東京都)
    • Year and Date
      2012-05-25
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Naratriptan ameliorates SBMA pathology by the repression of CGRP1-activated JNK pathway.2012

    • Author(s)
      Minamiyama, M., Katsuno, M., Adachi, H., Doi, H., Kondo, N., Iida, M., Ishigaki, S., Fujioka, Y., Matsumoto, S., Miyazaki, Y., Tanaka, F., Kurihara, H., Sobue, G.
    • Organizer
      Neuroscience 2012.
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] p62/SQSTM1 removes toxic mutant androgen receptor in spinal bulbar muscular atrophy model mouse2012

    • Author(s)
      Adachi H, Doi H, Katsuno M, Matsumoto S, Kondo N, Miyazaki Y, Tohnai G, Iida M, Tanaka F, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Viral delivery of miR-196a ameliorates the SBMA phenotype via the silencing of CELF22012

    • Author(s)
      Miyazaki Y, Adachi H, Katsuno M, Tanaka F, Muramatsu S, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans
    • Year and Date
      2012-10-16
    • Data Source
      KAKENHI-PROJECT-23390231
  • [Presentation] Naratriptan ameliorates SBMA pathology by the repression of CGRP1-activated JNK pathway.2012

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Iida M, Ishigaki S, Fujioka Y, Matsumoto S, Miyazaki Y, Tanaka F, Kurihara H, Sobue G.
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Naratriptan ameliorates SBMA pathology by the repression of CGRP1-activated JNK pathway2012

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Iida M, Ishigaki S, Fujioka Y, Matsumoto S, Miyazaki Y, Tanaka F, Kurihara H, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Cell cycle dysregulation in motor neurons of spinal and bulbar muscular atrophy (SBMA).2012

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Nakatsuji H, Tanaka F, Sobue G.
    • Organizer
      23rd International Symposium on ALS/MND.
    • Place of Presentation
      Chicago, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Cell cycle dysregulation in motor neurons of spinal and bulbar muscular atrophy (SBMA)2012

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Nakatsuji H, Tanaka F, Sobue G
    • Organizer
      23rd International Symposium on ALS/MND
    • Place of Presentation
      Chicago, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] 運動ニューロン特異的TDP-43ノックアウトマウスの病態解析2012

    • Author(s)
      井口洋平, 勝野雅央, 丹羽淳一, 高木伸之介, 田中章景, 祖父江元
    • Organizer
      第53回日本神経学会学術大会.
    • Place of Presentation
      東京国際フォーラム(東京都)
    • Year and Date
      2012-05-25
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] p62/SQSTM1 removes toxic mutant androgen receptor in spinal bulbar muscular atrophy model mouse.2012

    • Author(s)
      Adachi, H., Doi, H., Katsuno, M., Matsumoto, S., Kondo, N., Miyazaki, Y., Tohnai, G., Iida, M., Tanaka, F., Sobue, G.
    • Organizer
      Neuroscience 2012.
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Viral delivery of miR-196a ameliorates the SBMA phenotype via the silencing of CELF2.2012

    • Author(s)
      Miyazaki, Y., Adachi, H., Katsuno, M., Tanaka, F., Muramatsu, S.I., Sobue, G.
    • Organizer
      Neuroscience 2012.
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Viral delivery of miR-196a ameliorates the SBMA phenotype via the silencing of CELF22012

    • Author(s)
      Miyazaki Y, Adachi H, Katsuno M, Tanaka F, Muramatsu SI, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Longitudinal changes of outcome measures in spinal and bulbar muscular atrophy.2012

    • Author(s)
      Hashizume A, Katsuno M, Banno H, Suzuki K, Suga N, Mano T, Atsuta N, Oe H, Watanabe H, Tanaka F, Sobue G.
    • Organizer
      23rd International Symposium on ALS/MND.
    • Place of Presentation
      Chicago, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] CGRP1 is the new therapeutic target for SBMA (Spinal and Bulbar Muscular Atrophy).2012

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Iida M, Ishigaki S, Fujioka Y, Matsumoto S, Miyazaki Y, Tanaka F, Kurihara H, Sobue G.
    • Organizer
      11th Biennial Meeting of the Asian Pacific Society for Neurochemistry.
    • Place of Presentation
      神戸国際会議場(神戸)
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Cell cycle dysregulation in motor neurons of spinal and bulbar muscular atrophy (SBMA)2012

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Nakatsuji H, Tanaka F, Sobue G
    • Organizer
      23rd International Symposium on ALS/MND
    • Place of Presentation
      Chicago, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] dynactin-1ノックアウトによる孤発性ALSモデルマウスの作成と病態解析2012

    • Author(s)
      河合 香里, 池中建介, 勝又 竜, 井口洋平, 勝野雅央, 田中章景, 祖父江元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京国際フォーラム(東京都)
    • Year and Date
      2012-05-25
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Heat shock factor-1(HSF-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA).2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Tanaka F, Sobue G.
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      パシフィコ横浜(神奈川)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 神経変性疾患の病態抑止治療への展望2011

    • Author(s)
      田中章景, ら
    • Organizer
      第6回臨床ストレス応答学会大会
    • Place of Presentation
      名古屋大学医学部附属病院3階講堂(名古屋)(招待講演)
    • Year and Date
      2011-11-04
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Cell cycle dysregulation in spinal and bulbar muscular atrophy (SBMA).2011

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G.
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy,
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] A peony extract enhances protein degradation systems and exerts therapeutic effects in the polyglutamine-mediated motor neuron disease2011

    • Author(s)
      Adachi H, Tohnai G, Katsuno M, Minamiyama M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Tanaka F, Ohtsuka K, Sobue G
    • Organizer
      Neuroscience 2011
    • Place of Presentation
      Washington DC, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Cell cycle dysregulation in spinal and bulbar muscular atrophy (SBMA).2011

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Kondo N, Doi H, Matsumoto S, Miyazaki Y, Tanaka F, Sobue G.
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      パシフィコ横浜(神奈川)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Dynactin-1を標的とした孤発性ALS モデルの開発2011

    • Author(s)
      田中章景, 池中建介, 祖父江元
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知県)
    • Year and Date
      2011-05-20
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] 神経変性疾患の病態抑止治療への展望2011

    • Author(s)
      田中章景, 祖父江元
    • Organizer
      第6回臨床ストレス応答学会大会
    • Place of Presentation
      名古屋大学医学部 (愛知県)
    • Year and Date
      2011-11-05
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Heat shock factor-1 (Hsf-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Central motor conduction time (CMCT) in patients with spinal and bulbar muscular atrophy (SBMA).2011

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Suga N, Hashizume A, Hara T, Hama T, Nakamura T, Hirayama M, Tanaka F, Sobue G.
    • Organizer
      15th Congress of the European Federation of Neurological Societies
    • Place of Presentation
      Budapest, Hungary
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 球脊髄性筋萎縮症モデルマウスにおける異常蛋白凝集の病理学的分布はHsf-1の影響を受ける2011

    • Author(s)
      近藤直英, 勝野雅央, 足立弘明, 南山誠, 土井英樹, 松本慎二郎, 宮崎雄, 飯田円, 田中章景, 祖父江元
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Molecular pathology of SBMA (Spinal Bulbar Muscular Atrophy) related gene CGRP1.2011

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Tanaka F, Sobue G, Kurihara H.
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      パシフィコ横浜(神奈川)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] パーソナルゲノム解析に基づくALSの疾患関連遺伝子探索と病態解明2011

    • Author(s)
      田中章景, ら
    • Organizer
      パーソナルゲノム情報に基づく脳疾患メカニズムの解明班班会議
    • Place of Presentation
      東京大学本郷キャンパス理学部1号館小柴ホール(東京)
    • Year and Date
      2011-09-10
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Presentation] Diagnosis of sporadic transthyretin Val30Met familial amyloid polyneuropathy : a practicalanalysis2011

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Tanaka F, Sobue G
    • Organizer
      2011 PNS Biennial Meeting, Potomac
    • Place of Presentation
      Maryland
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Presentation] 球脊髄性筋萎縮症(SBMA)病態関連遺伝子CGRP1の分子機構2011

    • Author(s)
      南山 誠, 勝野雅央, 足立弘明, 土井英樹, 近藤直英, 田中章景, 祖父江 元, 栗原裕基.
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Molecular pathology of SBMA (Spinal Bulbar Muscular Atrophy) related gene CGRP12011

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Tanaka F, Sobue G, Kurihara H
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Diagnosis of sporadic transthyretin Val30Met familial amyloid polyneuropathy: a practical analysis2011

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Tanaka F, Sobue G
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto, Japan
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Presentation] 球脊髄性筋萎縮症における細胞周期異常.2011

    • Author(s)
      勝野雅央, 足立弘明, 南山 誠, 土井英樹, 近藤直英, 松本慎二郎, 宮崎 雄, 坂野晴彦, 鈴木啓介, 田中章景, 祖父江 元.
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] A peony extract enhances protein degradation systems and exerts therapeutic effects in the polyglutamine-mediated motor neuron disease2011

    • Author(s)
      Adachi H, Tohnai G, Katsuno M, Minamiyama M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Tanaka F, Ohtsuka K, Sobue G
    • Organizer
      Neuroscience 2011
    • Place of Presentation
      Washington DC, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 球脊髄性筋萎縮症(SBMA)病態関連遺伝子CGRP1の分子機構2011

    • Author(s)
      南山誠, 勝野雅央, 足立弘明, 土井英樹, 近藤直英, 田中章景, 祖父江元, 栗原裕基
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Heat shock factor-1(Hsf-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Heat shock factor-1(HSF-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Tanaka F, Sobue G
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Dynactin-1を標的とした孤発性ALSモデルの開発2011

    • Author(s)
      田中章景, ら
    • Organizer
      第52回日本神経学会学術大会シンポジウム
    • Place of Presentation
      名古屋国際会議場(名古屋)(招待講演)
    • Year and Date
      2011-05-20
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] dynactin-1ノックダウン線虫を用いた孤発性ALS (SALS) 軸索輸送障害モデルの作成2011

    • Author(s)
      池中建介, 河合香里, 蒋月梅, 黄哲, 勝野雅央, 田中章景, 祖父江元
    • Organizer
      第54回日本神経化学大会
    • Place of Presentation
      山代温泉瑠璃光(石川県)
    • Year and Date
      2011-09-28
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] 球脊髄性筋萎縮症モデルマウスにおける異常蛋白凝集の病理学的分布はHsf-1の影響を受ける.2011

    • Author(s)
      近藤直英, 勝野雅央, 足立弘明, 南山誠, 土井英樹, 松本慎二郎, 宮崎雄, 飯田円, 田中章景, 祖父江元.
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Central motor conduction time (CMCT) in patients with spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Suga N, Hashizume A, Hara T, Hama T, Nakamura T, Hirayama M, Tanaka F, Sobue G
    • Organizer
      15th Congress of the European Federation of Neurological Societies
    • Place of Presentation
      Budapest, Hungary
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Heat shock factor-1 (Hsf-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA).2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G.
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy,
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Cell cycle dysregulation in spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Heat shock factor-1(Hsf-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] dynactin-1ノックダウンによる孤発性ALS線虫モデルの作成と病態解析2011

    • Author(s)
      池中建介, 勝野雅央, 河合香里, 黄哲, 蒋月梅, 田中章景, 祖父江元
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      パシフィコ横浜(神奈川県)
    • Year and Date
      2011-09-17
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Effect of leuprorelin in patients with spinal and bulbar muscular atrophy (SBMA) : a multicenter, randomized, double-blind, placebo-controlled trial2011

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Yabe I, Sasaki H, Aoki M, Morita M, Nakano I, Kanai K, Ito S, Ishikawa K, Mizusawa H, Yamamoto T, Tsuji S, Hasegawa K, Shimohata T, Nishizawa M, Miyajima H, Kanda F, Watanabe Y, Nakashima K, Tsujino A, Yamashita T, Uchino M, Fujimoto Y, Tanaka F, Sobue G; for the Japan SBMA Interventional Trial for TAP-144-SR (JASMITT) study group
    • Organizer
      63rd American Academy of Neurology Annual Meeting
    • Place of Presentation
      Honolulu, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Cell cycle dysregulation in spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 神経変性疾患におけるdynactin-1と細胞周期関連分子の発現解析.2010

    • Author(s)
      池中建介, 蒋月梅, 田中章景, 勝又竜, 河合香里, 黄哲, 勝野雅央, 山本正彦, 祖父江元
    • Organizer
      第51回日本神経学会総会
    • Place of Presentation
      東京国際フォーラム(東京都)
    • Year and Date
      2010-05-22
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] A peony extract alleviates polyglutamine-mediated motor neuron disease2010

    • Author(s)
      Adachi H, Tohnai G, Katsuno M, Minamiyama M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Tanaka F, Sobue G.
    • Organizer
      Neuroscience 2010
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2010-11-16
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] パーソナルゲノム解析に基づくALSの疾患関連遺伝子探索と病態解明2010

    • Author(s)
      田中章景, ら
    • Organizer
      パーソナルゲノム情報に基づく脳疾患メカニズムの解明班班会議
    • Place of Presentation
      神戸ポートピアホテル(神戸)
    • Year and Date
      2010-08-20
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Presentation] パーソナルゲノム解析に基づくALSの疾患関連遺伝子探索と病態解明2010

    • Author(s)
      田中章景, ら
    • Organizer
      パーソナルゲノム情報に基づく脳疾患メカニズムの解明班班会議
    • Place of Presentation
      学術総合センター(東京)
    • Year and Date
      2010-12-16
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Presentation] Dynactin-1ノックダウン線虫における神経変性2010

    • Author(s)
      田中章景, 黄哲, 勝又竜, 池中建介, 河合香里, 蒋月梅, 和座雅浩, 勝野雅央, 祖父江元.
    • Organizer
      第51回日本神経学会総会
    • Place of Presentation
      東京国際フォーラム(東京都)
    • Year and Date
      2010-05-22
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Dynactin-lノックダウン線虫における神経変性2010

    • Author(s)
      田中章景, ら
    • Organizer
      第51回日本神経学会総会
    • Place of Presentation
      東京フォーラム
    • Year and Date
      2010-05-21
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] A peony extract alleviates polyglutamine-mediated motor neuron disease2010

    • Author(s)
      Adachi H, Tohnai G, Katsuno M, Minamiyama M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Tanaka F, Ohtsuka K, Sobue G.
    • Organizer
      40th Annual Meeting for the Society for Neuroscience
    • Place of Presentation
      San Diego
    • Year and Date
      2010-11-17
    • Data Source
      KAKENHI-PROJECT-20390243
  • [Presentation] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy.2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Doi H, Kondo N, Matsumoto S, Miyazaki Y, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Organizer
      21st International Symposium on ALS/MND.
    • Place of Presentation
      Orlando, USA
    • Year and Date
      2010-12-12
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases.2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Organizer
      Neuroscience 2009
    • Place of Presentation
      Chicago, USA
    • Year and Date
      2009-10-17
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Organizer
      Neuroscience 2009
    • Place of Presentation
      Chicago, USA
    • Year and Date
      2009-10-17
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy.2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G.
    • Organizer
      61th American Academy of Neurology Annual Meeting
    • Place of Presentation
      Seattle, USA
    • Year and Date
      2009-04-26
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] 孤発性ALS疾患モデルによる病態解明と治療法開発2009

    • Author(s)
      田中章景, ら
    • Organizer
      第50回日本神経学会総会
    • Place of Presentation
      仙台
    • Year and Date
      2009-05-21
    • Data Source
      KAKENHI-PROJECT-21659221
  • [Presentation] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa JI, Sone J, Waza M, Adachi H, Tanaka F, Nagata KI, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Organizer
      39th Annual Meeting for the Society for Neuroscience
    • Place of Presentation
      Chicago, IL(一般演題)
    • Year and Date
      2009-10-18
    • Data Source
      KAKENHI-PROJECT-20390243
  • [Presentation] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases2009

    • Author(s)
      Iguchi, Y., Katsuno, M., Niwa, J., Yamada, S., Sone, J., Waza, M., Adachi, H., Tanaka, F., Nagata, K., Arimura, N., Watanabe, T., Kaibuchi, K., Sobue G.
    • Organizer
      Neuroscience 2009
    • Place of Presentation
      Chicago, USA
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno, H., Katsuno, M., Suzuki, K., Takeuchi, Y., Kawashima, M., Suga, N., Takamori, M., Ito, M., Nakamura, T., Matsuo, K., Yamada, S., Oki, Y., Adachi, H., Minamiyama, M., Waza, M., Atsuta, N., Watanabe, H., Fujimoto, Y., Nakashima, T., Tanaka, F., Doyu, M., Sobue, G.
    • Organizer
      61th American Academy of Neurology Annual Meeting
    • Place of Presentation
      Seattle, USA
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] Medical induction of stress response alleviates polyglutamine-mediated motor neuron disease The 4th International Congress Responses in Biology and Medicine (CSSI)2009

    • Author(s)
      Tohnai G, Adachi H, Tokui K, Waza M, Katsuno M, Minamiyama M, Doi H, Tanaka F, Ohtsuka K, Sobue G.
    • Organizer
      The 4th Annual Meeting of The Biomedical Society for Stress Response (BSSR)
    • Place of Presentation
      Sapporo(一般演題)
    • Data Source
      KAKENHI-PROJECT-20390243
  • [Presentation] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G.
    • Organizer
      61th American Academy of Neurology Annual Meeting
    • Place of Presentation
      Seattle, USA
    • Year and Date
      2009-04-26
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Skeletal muscle involvement in spinal and bulbar muscular atrophy2008

    • Author(s)
      Katsuno M, Kawashima M, Banno H, Suzuki K, Takeuchi Y, Suga N, Adachi H, Tanaka F, Sobue G
    • Organizer
      The 19th International Symposium on ALS/MND
    • Place of Presentation
      Birmingham, UK
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 孤発性ALS病ALS病態関連分子の探索と疾患モデルの開発2008

    • Author(s)
      田中章景, ら
    • Organizer
      第49回日本神経学会総会シンポジウム
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-17
    • Data Source
      KAKENHI-PROJECT-19390238
  • [Presentation] 孤発性ALS病態関連分子の探索と疾患モデルの開発.2008

    • Author(s)
      田中章景, et al
    • Organizer
      第49回日本神経学会総会. シンポジウム
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-16
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 孤発性ALS病態関連分子の探索と疾患モデルの開発2008

    • Author(s)
      田中章景, 和座雅浩, 丹羽淳一, 山本正彦, 祖父江元
    • Organizer
      第49回日本神経学会総会
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-17
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Presentation] 孤発性ALS病態関連分子の探索と疾患モデルの開発2008

    • Author(s)
      田中章景、和座雅浩、丹羽淳一、祖父江 元
    • Organizer
      第49回日本神経学会総会シンポジウム
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-17
    • Data Source
      KAKENHI-PROJECT-19390238
  • [Presentation] An oral Hsp90 inhibitor ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2008

    • Author(s)
      Adachi, H., Tokui, K., Waza, M., Katsuno, M., Minamiyama, M., Doi, H., Tanaka, F., Sobue G.
    • Organizer
      Neuroscience 2008
    • Place of Presentation
      Washington DC, USA
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] Dynactin-1ノックダウン線虫モデルの作成2008

    • Author(s)
      和座雅浩、田中章景、蒋月梅、黄哲、勝野雅央、足立弘明、山本正彦、祖父江元
    • Organizer
      第49回日本神経学会総会
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-16
    • Data Source
      KAKENHI-PROJECT-19390238
  • [Presentation] 孤発性ALS病態関連分子の探索と疾患モデルの開発2008

    • Author(s)
      田中章景、和座雅浩、丹羽淳、祖父江元
    • Organizer
      第49回日本神経学会総会. シンポジウム
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-16
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 孤発性ALS病態関連分子の探索と疾患モデルの開発2008

    • Author(s)
      田中章景, et.al.
    • Organizer
      第49回日本神経学会総会、シンポジウム
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-16
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] 孤発陛ALS病態関連分子の探索と疾患モデルの開発2008

    • Author(s)
      田中章景, ら
    • Organizer
      第49回日本神経学会総会シンポジウム
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-17
    • Data Source
      KAKENHI-PROJECT-19659225
  • [Presentation] An oral Hsp90 inhibitor ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2008

    • Author(s)
      Adachi H, Tokui K, Waza M, Katsuno M, Minamiyama M, Doi H, Tanaka F, Sobue G
    • Organizer
      Neuroscience 2009
    • Place of Presentation
      Washington DC, USA
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] An oral Hsp9O inhibitor ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2008

    • Author(s)
      Adachi H, Tokui K, Katsuno M, Minamiyama M, Doi H, Tanaka F, Sobue G.
    • Organizer
      第38回The Society for Neuroscience Annual meeting
    • Place of Presentation
      Washington DC(一般演題)
    • Data Source
      KAKENHI-PROJECT-20390243
  • [Presentation] 孤発性ALS疾患モデルの開発 : dynactin1ノックダウン細胞の解析2007

    • Author(s)
      田中章景、黄哲、蒋月梅、松尾幸治、和座雅浩、山本正彦、道勇学、祖父江元
    • Organizer
      第48回日本神経学会総会
    • Place of Presentation
      名古屋
    • Year and Date
      2007-05-16
    • Data Source
      KAKENHI-PROJECT-19390238
  • [Presentation] CHIP overexpression reduces the mutant AR protein and ameliorates phenotypes of the SBMA transgenic mouse model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Tanaka F, Sobue G
    • Organizer
      Neuroscience 2007
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] Myocardial involvement in spinal and bulbar muscular atrophy2007

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Takeuchi Y, Kawashima M, Tanaka F, Sobue G
    • Organizer
      18th International symposium on ALS/MND
    • Place of Presentation
      Toronto, Canada
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] CHIP over-expression reduces the mutant AR protein and ameliorates phenotypes of the SBMA transgenic mouse model2007

    • Author(s)
      Adachi, H, Waza, M, Tokui, K, Katsuno, M, Minamiyama, M. Tanaka, F, Sobue, G
    • Organizer
      The 49th Annual Meeting of the Japanese Society of Neurology
    • Place of Presentation
      Nagoya
    • Year and Date
      2007-05-17
    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18599002
  • [Presentation] Gen expression profile of spinal motor neurons in sporadic amyotrophic lateral sclerosis2006

    • Author(s)
      Tanaka, F., Jiang, Y.M., Yamamoto, M., Huang, Z., Katsuno, M., Adachi, H., Niwa, J.I., Doyu, M., Sobue, G.
    • Organizer
      17th International Symposium on ALS/MND
    • Place of Presentation
      Yokohama, Japan
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] Reversible disruption of retrograde axonal transport in spinal and bulbar muscular atrophy2006

    • Author(s)
      Katsuno, M., Adachi, H., Minamiyama, M., Waza, M., Tokui, K., Jiang, Y.M., Banno, H., Suzuki, K., Tanaka, F., Sobue, G.
    • Organizer
      17th International Symposium on ALS/MND
    • Place of Presentation
      Yokohama, Japan
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] RNA病からみた認知症関連疾患 C9orf72遺伝子変異と前頭側頭型認知症

    • Author(s)
      田中章景
    • Organizer
      第33回日本認知症学会学術集会
    • Place of Presentation
      パシフィコ横浜(神奈川県横浜市)
    • Year and Date
      2014-11-29 – 2014-12-01
    • Invited
    • Data Source
      KAKENHI-PROJECT-25293207
  • [Presentation] RNA病からみた認知症関連疾患 C9orf72遺伝子変異と前頭側頭型認知症

    • Author(s)
      田中章景
    • Organizer
      第33回日本認知症学会学術集会
    • Place of Presentation
      パシフィコ横浜(神奈川県横浜市)
    • Year and Date
      2014-11-29 – 2014-12-01
    • Invited
    • Data Source
      KAKENHI-PROJECT-26670445
  • [Presentation] Analysis of major amyotrophic lateral sclerosis genes in Japan

    • Author(s)
      Nakamura R, Sone J, Atsuta N, Watanabe H, Hirakawa A, Watanabe H, Ito M, Senda J, Katsuno K, Tanaka F, Izumi Y, Morita M, Ogaki K, Taniguchi A, Aiba A, Mizoguchi K, Okamoto K, Hasegawa K, Aoki M, Kawata A, Abe K, Oda M, Konagaya M, Imai T, Nakagawa M, Tsuji S, Kaji R, Nakano I, Sobue G
    • Organizer
      64th Annual Meeting of the American Society of Human Genetics
    • Place of Presentation
      San Diego Convention Center, San Diego, CA, USA
    • Year and Date
      2014-10-18 – 2014-10-22
    • Data Source
      KAKENHI-PROJECT-26670445
  • [Presentation] ALSの呼吸機能評価における横隔膜エコーと横隔神経M波振幅の組み合わせの有用性

    • Author(s)
      釘本千春、岩橋幸子、小林絵礼奈、斎藤麻美、山崎舞子、東山雄一、上木英人,  田中章景
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      福岡国際会議場(福岡県福岡市)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-25293207
  • [Presentation] 神経変性疾患のトランスレーショナルリサーチ

    • Author(s)
      勝野雅央, 坂野晴彦, 鈴木啓介, 橋詰 淳, 足立弘明, 田中章景, 祖父江 元.
    • Organizer
      第109回日本内科学会総会・講演会シンポジウム「わが国のトランスレーショナルリサーチとEBM」
    • Place of Presentation
      みやこめっせ(京都)
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] パーソナルゲノム解析に基づくALSの疾患関連遺伝子探索と病態解明

    • Author(s)
      田中章景
    • Organizer
      新学術領域研究 脳疾患ゲノム情報班会議
    • Place of Presentation
      東京大学小柴ホール(東京都)
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Presentation] 運動ニューロン特異的TDP-43ノックアウトマウスの病理学的検討

    • Author(s)
      井口洋平, 勝野雅央, 丹羽淳一, 高木伸之介, 山中宏二, 三澤日出巳, 高橋良 輔, 佐々木彰一, 田中章景, 祖父江元
    • Organizer
      第54回日本神経学会学術大会
    • Place of Presentation
      東京国際フォーラム(東京都千代田)
    • Year and Date
      2013-05-29 – 2013-06-01
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Presentation] SCARB2遺伝子に変異を認めた高齢発症の進行性ミオクローヌスてんかん兄妹例

    • Author(s)
      東山雄一,土井宏,阿部弘基,中村治子,工藤洋祐,上木英人,児矢野 繁,鈴木ゆめ,黒岩義之,松本直通,田中章景
    • Organizer
      第54回日本神経学会学術大会
    • Place of Presentation
      東京国際フォーラム(東京都千代田)
    • Year and Date
      2013-05-29 – 2013-06-01
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Presentation] 渦巻き描記を用いた小脳性運動失調の他覚的評価法の検討(第7報)

    • Author(s)
      上田直久,波木井靖人,黒岩義之,田中章景
    • Organizer
      第54回日本神経学会総会
    • Place of Presentation
      国際フォーラム(東京)
    • Data Source
      KAKENHI-PROJECT-25461287
  • [Presentation] Molecular pathogenesis and therapy of polyglutamine-induced motor neuron degeneration.

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Doi H, Kondo N, Miyazaki Y, Iida M, Tanaka F, Sobue G.
    • Organizer
      35th Annual Meeting of the Japan Neuroscience Society.
    • Place of Presentation
      名古屋国際会議場(名古屋)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Analysis of major amyotrophic lateral sclerosis genes in Japan

    • Author(s)
      Nakamura R, Sone J, Atsuta N, Watanabe H, Hirakawa A, Watanabe H, Ito M, Senda J, Katsuno K, Tanaka F, Izumi Y, Morita M, Ogaki K, Taniguchi A, Aiba A, Mizoguchi K, Okamoto K, Hasegawa K, Aoki M, Kawata A, Abe K, Oda M, Konagaya M, Imai T, Nakagawa M, Tsuji S, Kaji R, Nakano I, Sobue G
    • Organizer
      64th Annual Meeting of the American Society of Human Genetics
    • Place of Presentation
      San Diego Convention Center, San Diego, CA, USA
    • Year and Date
      2014-10-18 – 2014-10-22
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Presentation] Analysis of major amyotrophic lateral sclerosis genes in Japan

    • Author(s)
      Nakamura R, Sone J, Atsuta N, Watanabe H, Hirakawa A, Watanabe H, Ito M, Senda J, Katsuno K, Tanaka F, Izumi Y, Morita M, Ogaki K, Taniguchi A, Aiba A, Mizoguchi K, Okamoto K, Hasegawa K, Aoki M, Kawata A, Abe K, Oda M, Konagaya M, Imai T, Nakagawa M, Tsuji S, Kaji R, Nakano I, Sobue G
    • Organizer
      64th Annual Meeting of the American Society of Human Genetics
    • Place of Presentation
      San Diego Convention Center, San Diego, CA, USA
    • Year and Date
      2014-10-18 – 2014-10-22
    • Data Source
      KAKENHI-PROJECT-25293207
  • [Presentation] Toward identifying the causative gene of neuronal intranuclear inclusion disease (NIID)

    • Author(s)
      田中 章景
    • Organizer
      第35回日本神経科学大会
    • Place of Presentation
      名古屋国際会議場(名古屋)
    • Data Source
      KAKENHI-PROJECT-24591257
  • []

  • 1.  DOI Hiroshi (10326035)
    # of Collaborated Projects: 23 results
    # of Collaborated Products: 77 results
  • 2.  SOBUE Gen (20148315)
    # of Collaborated Projects: 18 results
    # of Collaborated Products: 286 results
  • 3.  TAKEUCHI Hideyuki (30362213)
    # of Collaborated Projects: 11 results
    # of Collaborated Products: 45 results
  • 4.  DOYU Manabu (90293703)
    # of Collaborated Projects: 8 results
    # of Collaborated Products: 66 results
  • 5.  KATSUNO Masahisa (50402566)
    # of Collaborated Projects: 7 results
    # of Collaborated Products: 182 results
  • 6.  ADACHI Hiroaki (40432257)
    # of Collaborated Projects: 7 results
    # of Collaborated Products: 97 results
  • 7.  KOYANO Shigeru (50315818)
    # of Collaborated Projects: 7 results
    # of Collaborated Products: 12 results
  • 8.  TADA Mikiko (30722467)
    # of Collaborated Projects: 7 results
    # of Collaborated Products: 13 results
  • 9.  KOIKE Haruki (80378174)
    # of Collaborated Projects: 5 results
    # of Collaborated Products: 22 results
  • 10.  國井 美紗子 (80725200)
    # of Collaborated Projects: 5 results
    # of Collaborated Products: 19 results
  • 11.  TANAKA Ken-ichi (50722881)
    # of Collaborated Projects: 4 results
    # of Collaborated Products: 20 results
  • 12.  IIJIMA Masahiro (40437041)
    # of Collaborated Projects: 4 results
    # of Collaborated Products: 14 results
  • 13.  Ueda Naohisa (00305442)
    # of Collaborated Projects: 4 results
    # of Collaborated Products: 1 results
  • 14.  Yuichi HIGASHIYAMA (10722449)
    # of Collaborated Projects: 4 results
    # of Collaborated Products: 0 results
  • 15.  TAKAHASHI Keita (20773740)
    # of Collaborated Projects: 4 results
    # of Collaborated Products: 3 results
  • 16.  SONE Jun (40513750)
    # of Collaborated Projects: 3 results
    # of Collaborated Products: 12 results
  • 17.  MATSUMOTO Naomichi (80325638)
    # of Collaborated Projects: 3 results
    # of Collaborated Products: 4 results
  • 18.  KISHIDA Hitaru (20405004)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 0 results
  • 19.  TAKEI Kohtaro (40202163)
    # of Collaborated Projects: 2 results
    # of Collaborated Products: 12 results
  • 20.  NIWA Jun-ichi (50378022)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 11 results
  • 21.  OKADA Youhei (30383714)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 22.  OKANO Hideyuki (60160694)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 23.  TANAKA Keiji (10108871)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 54 results
  • 24.  ITO Mizuki (50437042)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 2 results
  • 25.  ATSUTA Naoki (90547457)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 4 results
  • 26.  MORISHITA Shinichi (90292854)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 1 results
  • 27.  SUGANO Sumio (60162848)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 1 results
  • 28.  NUKINA Nobuyuki (10134595)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 29.  SUZUKI Yume (70236024)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 1 results
  • 30.  YAMAMOTO Masahiko (40378039)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 31.  FUNAKOSHI Hiroshi (40273685)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 32.  ISHIKAWA Kinya (30313240)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 2 results
  • 33.  KATSUMOTO Atsuko (20806161)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 2 results
  • 34.  服部 直樹 (10402570)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 6 results
  • 35.  吉田 眞理 (60288545)
    # of Collaborated Projects: 1 results
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  • 36.  石川 太郎 (50547916)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 3 results
  • 37.  森本 悟 (00816952)
    # of Collaborated Projects: 1 results
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  • 38.  中村 治子 (70806223)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 39.  森原 啓介 (80806216)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 40.  岩崎 靖 (60378172)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 41.  石井 一弘 (70323293)
    # of Collaborated Projects: 1 results
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  • 42.  窪田 瞬 (60891851)
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 0 results
  • 43.  MIYAZAKI Yu
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 2 results
  • 44.  KURIHARA Yuji
    # of Collaborated Projects: 1 results
    # of Collaborated Products: 5 results
  • 45.  FRITH Martin
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 46.  KUROIWA Yoshiyuki
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 47.  HANAJIMA Ritsuko
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 48.  Hashiguchi Syunta
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 49.  Ohba Chihiro
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 50.  ITO S
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 51.  内原 俊記
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 52.  水口 剛
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 2 results
  • 53.  三橋 里美
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 2 results
  • 54.  鈴木 啓介
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 55.  鶴崎 美徳
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 56.  木村 活生
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 57.  宮武 聡子
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 3 results
  • 58.  堀内 浩
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 59.  高尾 昌樹
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 60.  三宅 紀子
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results
  • 61.  中村 亮一
    # of Collaborated Projects: 0 results
    # of Collaborated Products: 1 results

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