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Sobue Gen  祖父江 元

… Alternative Names

祖父江 元  ソブエ ゲン

SOFUE Gen  祖父江 元

SOBUE Gen  祖父 江元

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Researcher Number 20148315
Other IDs
  • ORCIDhttps://orcid.org/0000-0002-9936-6664
External Links
Affiliation (Current) 2025: 愛知医科大学, 愛知医科大学, 学長
Affiliation (based on the past Project Information) *help 2023: 愛知医科大学, 愛知医科大学, 学長
2022 – 2023: 愛知医科大学, 災害医療研究センター, 理事長
2015 – 2019: 名古屋大学, 医学系研究科, 特任教授
2014 – 2016: 名古屋大学, 医学(系)研究科(研究院), 特任教授
2011 – 2016: 名古屋大学, 医学(系)研究科(研究院), 教授 … More
2015: 名古屋大学, 大学院医学系研究科, 教授
2015: 名古屋大学, 大学院医学系研究科, 特任教授
2014: 名古屋大学, 医学部神経内科, 教授
2010 – 2014: 名古屋大学, 医学系研究科, 教授
2007 – 2012: Nagoya University, 大学院・医学系研究科, Professor
2011: 名古屋大学, 医学部, 教授
2011: 名古屋大学, 医学部神経内科, 教授
2007: Nagoya University, Graduate School of Medicine, Professor
2004 – 2006: Nagoya Univesity, Department of Neurology, Professor, 大学院医学系研究科, 教授
2002 – 2005: Graduate School of Medicine, Professor, 大学院・医学系研究科, 教授
2004: 国立大学法人名古屋大学, 大学院・医学系研究科, 教授
2001: Graduate School of Medicine, Nagoya University, Professor, 大学院・医学研究科, 教授
1998 – 2000: 名古屋大学, 医学部, 教授
1995 – 1996: Department of Neurology School of Medicine Nagoya University Professor, 医学部, 教授
1994: 愛知医科大学, 医学部, 助教授
1990 – 1992: 愛知医科大学, 医学部, 助教授 Less
Review Section/Research Field
Principal Investigator
Neurology / Biological Sciences / Neurology / Biological Sciences
Except Principal Investigator
Neurology / Neurology / Basic Section 51030:Pathophysiologic neuroscience-related / Biological Sciences / Basic Section 52020:Neurology-related / General internal medicine(including psychosomatic medicine) … More / Laboratory medicine / Neurophysiology and muscle physiology / Neurochemistry/Neuropharmacology / 疼痛学 / Biological Sciences / Neurochemistry/Neuropharmacology Less
Keywords
Principal Investigator
神経変性疾患 / ポリグルタミン / 球脊髄性筋萎縮症 / アンドロゲン受容体 / 認知症 / 17-AAG / プロテアソーム / 運動ニューロン / heat shock protein / geranylgeranylaceone … More / mRNA / 脳タンパク質 / 神経科学 / 老化 / 脳・神経 / 神経変性 / CAGリピート / 分子シャペロン / 筋萎縮性側索硬化症 / GGA / HSP / ポリグルタミン病 / dynactin1 / histone / polyglutamine / motor neuron / テストステロン / 熱ショックタンパク質 / ヒストン / LHRHアナログ / 神経細胞死 / 末梢神経障害 / trk / NGF / 神経栄養因子 / タウ / 痴呆 / 蛋白質 / トランスレーショナルリサーチ / リュープロレリン / ユビキチン-プロテアソーム / 軸索輸送 / CHIP / ユビキチン / TGF-β / 転写障害 / 球脊髄性筋萎縮症(SBMA) / ALS / 治療反応性 / cDNAマイクロアレー / レーザーマイクロダイセクション法 / 神経 / 脳 / タンパク質 / 高次脳機能 / ネットワーク / 加齢 / PET / MRI / 高次機能 / 若手研究者育成 / 若手研究者の育成 / 国際ネットワークの構築 / 国際的拠点形成 / 国際共同研究 / 国際連携 / biomarker / ubiquitin-proteasome / molecular chaperone / spinal and bulbar muscular atrophy / バイオマーカー / androgen receptor / Neurodegeneration / フルタミド / LHRH analog / andorogen receptor / neurodegeneration / アンドロゲン受容体(AR) / 遺伝子発現解析 / DNA chip / 培養神経系細胞モデル / アデノウイルスベクター / ポリグルタミン鎖 / CAGリピート病 / Hsp / ホルモン治療 / びまん性核内蓄積 / HSP70 / 去勢術 / トランスジェニックマウス / アロドロゲン受容体 / Neuronal cell death / Neuro trophic factor / Neuro degenerative disease / trk-family / neurotrophin / sensory neuron / sympathetic neuron / laminin / neurotrophic factors / Peripheral nerves / NTー3 / BDNF / 神経成長因子 / 感覚神経 / 交感神経 / ラミニン / 末梢神経 / 線虫 / 低分子化合物 / 薬剤スクリーニング / 発現制御 / 核酸 / 遺伝子 / 脳神経疾患 / 神経変性疾患モデル細胞 / 検知システム / 改変GFP / 小胞体ストレス / FUS / calcitonin-related polypeptide(CGRP1) / calcitonin / calcitonin/calcitonin-related polypeptide(CGRP1) / セロトニン受容体アゴニスト / ユビチキン / )球脊髄性筋萎縮症 / オートファジー / ユビキチン-プロテアゾーム系 / JNK / 細胞周期 / 治療 / 分解 / 古細菌 / 熱ショック蛋白質 / ユビキチン・プロテアソーム / ユビキチンープロテアソーム / 神経分子病態学 / 分子標的療法 / Hsp90 / キメラタンパク質 / ユビキチンリガーゼ / 変異SOD1 / Dorfin / ニューロフィラメント / dnactin1 / モーター蛋白質 / 17-DMAG / 脊髄小脳失調症(SCA) / HLA多型 / 遺伝子多型 / 免疫グロブリン / 慢性炎症性脱髄性ポリニューロパチー / GAL4-UAS / SOD1 / dorfin / Drosophila / 遺伝子解析 / 免疫クロブリン / CIDP / 発現遺伝子プロファイル / 筋萎縮性側索硬化症(ALS) / 運動ニューロン疾患 / クローニング / 遺伝子発現 / 病態関連遺伝子 / 分子インデックス法 / パーキンソン病 … More
Except Principal Investigator
球脊髄性筋萎縮症 / 筋萎縮性側索硬化症 / 運動ニューロン / ALS / 神経変性疾患 / アンドロゲン受容体 / トランスジェニックマウス / CAGリピート / パーキンソン病 / Dorfin / バイオマーカー / 運動ニューロン疾患 / 神経変性 / ポリグルタミン / 遺伝子発現解析 / 神経栄養因子 / Charcot-Marie-Tooth disease / motor neuron / spinal and bulbar muscular atrophy / DNA chip / 脳神経疾患 / 認知症 / MRI / ノックアウトマウス / ユビキチンリガーゼ / 骨格筋 / オートファジー / ポリグルタミン病 / 軸索障害 / CIDP / 予後因子 / mouse model / Schwann cell / myelin protein zero / hereditary neuropathy / siRNA / p97 / VCP / IP-10 / RANTES / MIP-1β / MCP-1 / Th2 / Th1 / chemokine receptor / chemokine / transgenic mouse / CAG repeat / androgen receptor / HSP70 / LHRHアナログ / 自律神経障害 / 認知機能 / 加齢 / 幻覚 / マイクロアレイ / fractional anisotropy / voxel-based morphometry / 多系統萎縮症 / TAG-1 / 脱髄 / 脱髄性ニューロパチー / 孤発性ALS / dynactin-1 / 遺伝子診断 / サイクリン依存性キナーゼ / 細胞周期 / ミトコンドリア / 酸化ストレス / 非運動症状 / 事象関連電位 / 分子シャペロン / 核内封入体 / プロテオーム / ジスルフィド結合 / 変異SOD1 / dynactin1 / 脳科学 / BDNF / タンパク質品質管理機構 / iPS細胞 / missing heritability / ACSL5 / リピート伸長変異 / missing heritabbility / 次世代シークエンサー / 構造多型 / LRP1 / THSD7A / FGF1 / 疾患レジストリ / 神経病理解析 / 治療薬探索 / 予後関連因子 / 呼吸機能 / シスタチンC / 遺伝子多型 / ゲノム遺伝子 / 一塩基多型 / 重症度スケール / 疾患コホート / ウイルスベクター / 脳分子プロファイル / モデル動物 / 脳画像データベース / ブレインバンク / 技術開発支援 / 研究リソース支援 / 若手研究者育成支援 / 技術開発 / 研究リソース / 研究集会 / 研究支援 / 脳腫瘍 / ネットワーク / 機能的MRI / てんかん / リアルタイム / 高次脳機能 / 脳波 / 全ゲノム解析 / 末梢神経障害 / DWI / 皮膚生検 / 白質脳症 / レジストリ / X連鎖劣性遺伝 / 女性保因者 / 複合的臨床評価スケール / 成体神経新生 / タウ / 前頭側頭葉変性症 / adult neurogenesis / SFPQ / FUS / tau / FTLD / Adult neurogenesis / muscle weakness / muscle atrophy / neurotrophic factor / hepatocyte erowth factor / ダブルトランスジェニックマウス / ドランスジェニックマウス / 筋力低下 / 筋萎縮 / 肝細胞増殖因子 / mutation screening / inherited neuropathy / molecular diagnosis / genetic diagnosis / reseguencing method / CMT / 遺伝子検査 / multiple PCR / resequencing array / マイクロアイレ / Charcol-Marie-Tooth病 / 新規原因遺伝子発見 / リーシークエンスアレイ / 遺伝性ニューロパチー / Charcot-Marie-Tooth病 / disulfide bond / neurodegeneration / mutant SOD1 / Amyotrophic lateral sclerosis / オリゴマー / プロテアソーム / autophagy / gene expression analysis / cDNAマイクロアレイ / gene expression profiles / LHRH analog / polyglutamine / amyotrophic lateral sclerosis / ヒストン脱アセチル化 / 臨床試験 / Inflammatory myopathy / 封入体筋炎 / 皮膚筋炎 / 多発筋炎 / 炎症性筋疾患 / protein degradation / LHRH analogue / castration / Hsp / ホルモン治療 / テストステロン / 蛋白分解 / 去勢術 / Gene expression analysis / In vitro neuronal cell culture model / adenovirus vector / Spinal and bulbar muscular atrophy / neuronal cell death / polyglutamine tract / CAG repeat disease / ポリグルタミン凝集体 / 培養神経系細胞モデル / アデノウイルスベクター / 神経細胞死 / ポリグルタミン鎖 / CAGリピート病 / Transgenic mouse / Cancer invasion / Ganglioside / Dorfin gene / Midkine / RET gene / Malignant tumor / Neurodegenerative disease / 癌転移 / 浸潤・転移 / Src遺伝子 / 糖鎖合成酵素遺伝子 / 癌の浸潤 / 糖脂質糖鎖 / Dorfin遺伝子 / ミッドカイン / RET遺伝子 / 悪性腫瘍 / Ubiquitination / IBR Motif / Ring Finger / Novel Genes / Motor Neuron Death / Expressed-Gene Profile / Molecular Indexing / Amyotrophic Lateral Screlosis / 神経悪性疾患 / ユビキチン系 / リングフィンガーモチーフ / 新規遺伝子 / 運動ニューロン死 / 遺伝子発現プロファイル / 分子インデックス法 / クレアチン / 脳神経外科 / モデルマウス / 分子標的治療 / 病態 / RNA / 変異アンドロゲン受容体 / 病態解明 / アンチセンス核酸 / シグナル / リン酸化 / シグナル伝達 / 神経科学 / DNAメチル化 / Aktシグナル / NFkB / エピジェネティクス / Mean diffusivity / 安静時脳機能MRI / 安静時機能MRI / TBSS / VBM / 多系統萎縮症(MSA) / 予後 / 拡散テンソル / 脳容積 / 実験的自己免疫性神経炎 / 免疫グロブリン療法 / B7-2ノックアウトNODマウス / 軸索-髄鞘相互作用 / 免疫性脱髄性ニューロパチー / 実験的自己免疫性神経炎(EAN) / 自己免疫疾患 / 軸索ー髄鞘間相互作用 / 免疫性疾患 / 動物モデル / 傍ランビエ絞輪部 / 免疫介在性ニューロパチー / ニューロパチー / 急性自律性感覚性運動性ニューロパチー / 急性自律性感覚性ニューロパチー / ギランバレー症候群 / 急性自律性神経感覚性ニューロパチー / 免疫性自律神経ニューロパチー / 急性自律神経性感覚性ニューロパチー / 自己免疫性自律神経節障害 / 自律神経ニューロパチー / 再生 / 免疫 / 生活習慣病 / ストレス / メタボリックシンドローム / インスリンシグナル / 脂肪肝 / 2型糖尿病 / ERストレス / GADD34 / 老化 / magnetoencephalography / functional MRI / 抗コリンエステラーゼ阻害剤 / 予防 / 脳内神経回路 / 早期診断 / 神経放射線 / 神経画像 / 精神症状 / レプチン / グレリン / 食事性低血圧 / 起立性低血圧 / 前頭葉機能 / 痛み関連電位 / 認知症状 / 一次感覚野 / 一次視覚野 / 反回抑制 / 視覚誘発脳磁場 / 視覚感覚野 / 網膜 / 脳磁図 / 質量分析 / HRD1 / RNF19B / 神経細胞 / EDAD / 小胞体ストレス / 小胞体 / エンドソーム / RNF19B / 膜輸送 / γ-セクレターゼ / ERAD / アミロイドβ / APP / アルツハイマー病 / AAVベクター / Dicer / miR-196a / 運動ニューロン病 / CELF2 / miRNA / アンドロゲンレセプター / セロトニン受容体 / 神経ペプチド / 転写障害 / naratriptan / CGRP1 / JNK / mean diffusivity(MD) / fractional anisotropy(FA) / volumetry / 多系統萎縮症(MSA) / fractional anisotorpy / mean diffusivity / 一塩基多型(single nucleotide polymorphism,SNP) / 軸索機能障害 / Intravenous immunoglobulin(IVIg) / 慢性炎症性脱髄性多発ニューロパチー(CIDP) / axon-glial interaction / チャネル / 末梢神経 / イオンチャネル / 治療反応性 / Axon-myelin interaction / マウスモデル / 線虫モデル / 家族性ALS / 病因遺伝子 / エクソーム解析 / 次世代シーケンサー / CGRP-1 / 筋萎縮性側索硬化 / TGF-β / サーキット変性 / レンチウイルスベクター / heat shock factor-1 / 熱ショック蛋白質 / TGF-beta / 封入体 / GDNF / 2アミノ酸剤 / 認知検査 / 嗅覚検査 / 痛み閾値 / 体性感覚誘発電位 / 嗅覚機能 / 痛み認知 / olfactory function / somatosensory evoked potencial / dementia / non-motor / pain / Parkinson's disease / 脳画像 / 視覚認知 / 認知機能検査 / 幻視 / 多発神経炎 / 家族性アミロイドポリニューロパチー / トランスサイレチン / アミロイド / ユビキチンープロテアソーム系 / Hsp90阻害剤 / 17-DMAG / ユビキチン-プロテアソーム系 / ペオニ抽出物 / 連鎖解析 / NIHID / 翻訳後修飾 / TDP-43 / 核タンパク質 / ユビキチン化 / タンパク質凝集 / 筋萎縮性側索硬化症(ALS) / Tag-1 / 軸索機序 / CTDP / リュープロレリン / 一塩基多型解析 / Schwann cell axonal interaction / dynactinl / 疾患モデル / 線虫 / cyclin C / 精神疾患 / 変性疾患 / 神経疾患 / 病態脳 / 統合脳 / 神経発達 / グリア研究会 / 神経疾患治癒 / グリア細胞 / mRNA / RT-PCR / チロシンキナーゼ / 自己燐酸化 / TrkB Less
  • Research Projects

    (79 results)
  • Research Products

    (1,186 results)
  • Co-Researchers

    (256 People)
  •  ALSにおける老化によるタンパク質品質管理機構の発現変化と病態への影響

    • Principal Investigator
      藤内 玄規
    • Project Period (FY)
      2023 – 2025
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 51030:Pathophysiologic neuroscience-related
    • Research Institution
      Aichi Medical University
  •  Elucidating the heterogeneity of amyotrophic lateral sclerosis by neuropathological analysis linked to clinical genomic information

    • Principal Investigator
      熱田 直樹
    • Project Period (FY)
      2022 – 2024
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 51030:Pathophysiologic neuroscience-related
    • Research Institution
      Aichi Medical University
  •  筋萎縮性側索硬化症のmissing heritabilityに関わる遺伝子の探索

    • Principal Investigator
      中村 亮一
    • Project Period (FY)
      2022 – 2024
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Review Section
      Basic Section 52020:Neurology-related
    • Research Institution
      Aichi Medical University
  •  Brain Protein Aging and Dementia ControlPrincipal Investigator

    • Principal Investigator
      祖父江 元
    • Project Period (FY)
      2019
    • Research Category
      Grant-in-Aid for Scientific Research on Innovative Areas (Research in a proposed research area)
    • Review Section
      Biological Sciences
    • Research Institution
      Nagoya University
  •  Therapeutic development based on factors affecting progression and prognosis of amyotrophic lateral sclerosis

    • Principal Investigator
      Atsuta Naoki
    • Project Period (FY)
      2017 – 2019
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Adult neurogenesis in the mouse models of ALS/FTLD

    • Principal Investigator
      Ishigaki Shinsuke
    • Project Period (FY)
      2015 – 2017
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Biomarker study in the early phase patients with spinal and bulbar muscular atrophy

    • Principal Investigator
      Hashizume Atsushi
    • Project Period (FY)
      2015 – 2017
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Investigation of clinical picture and causative gene of NIID

    • Principal Investigator
      Sone Jun
    • Project Period (FY)
      2015 – 2017
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Analysis of temporal and spatial brain circuit using real-time simultaneous electroencephalography and functional magnetic resonance imaging

    • Principal Investigator
      WATANABE Hirohisa
    • Project Period (FY)
      2015 – 2016
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Brain Protein Aging and Dementia Control(International Research Activities Supporting Program)Principal Investigator

    • Principal Investigator
      Sobue Gen
    • Project Period (FY)
      2015 – 2018
    • Research Category
      Grant-in-Aid for Scientific Research on Innovative Areas (Research in a proposed research area)
    • Review Section
      Biological Sciences
    • Research Institution
      Nagoya University
  •  Development of biomarker and therapy for amyotrophic lateral sclerosis targeting cystatin C

    • Principal Investigator
      Katsuno Masahisa
    • Project Period (FY)
      2015
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Brain Protein Aging and Dementia ControlPrincipal Investigator

    • Principal Investigator
      Sobue Gen
    • Project Period (FY)
      2014 – 2018
    • Research Category
      Grant-in-Aid for Scientific Research on Innovative Areas (Research in a proposed research area)
    • Review Section
      Biological Sciences
    • Research Institution
      Nagoya University
  •  Therapy development for neuromuscular degeneration in motor neuron diseases

    • Principal Investigator
      KATSUNO Masahisa
    • Project Period (FY)
      2014 – 2016
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Dissection of the pathomechanisms of motor neuron disease using antisense therapeutics

    • Principal Investigator
      Sahashi Kentaro
    • Project Period (FY)
      2014 – 2016
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Elucidation of pathogenesis of sporadic ALS using motor neuron specific-dynactin-1 knockout mice

    • Principal Investigator
      KAWAI Kaori
    • Project Period (FY)
      2014 – 2016
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  A drug screening system for ALS by automated, quantitative motility analysis of C. elegans ALS modelPrincipal Investigator

    • Principal Investigator
      Sobue Gen
    • Project Period (FY)
      2014 – 2015
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Elucidation of the pathogenesis of creatine metabolism dysregulation in spinal and bulbar muscular atrophy (SBMA) and clinical trial of oral creatine for patients with SBMA

    • Principal Investigator
      KASTUNO Masahisa
    • Project Period (FY)
      2014
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Prevention of brain protein aging and dementiaArea Organizer

    • Area Organizer
      祖父江 元
    • Project Period (FY)
      2014 – 2018
    • Research Category
      Grant-in-Aid for Scientific Research on Innovative Areas (Research in a proposed research area)
  •  Visualization of brain protein aging and clarification of the mechanisms of neural circuit breakdownPrincipal Investigator

    • Principal Investigator
      Sobue Gen
    • Project Period (FY)
      2014 – 2018
    • Research Category
      Grant-in-Aid for Scientific Research on Innovative Areas (Research in a proposed research area)
    • Review Section
      Biological Sciences
    • Research Institution
      Nagoya University
  •  Age-related diseases analyzed by ER stresses and immune functions using murine models including iPSCs

    • Principal Investigator
      isobe ken-ichi
    • Project Period (FY)
      2013 – 2016
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      General internal medicine(including psychosomatic medicine)
    • Research Institution
      Nagoya Women's University
      Nagoya University
  •  Elucidation of the pathogenesis and development of novel therapies in immune-mediated autonomic neuropathies

    • Principal Investigator
      Koike Haruki
    • Project Period (FY)
      2013 – 2015
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Analysis of axonal vulnerability in immune-mediated demyelination: a role of TAG-1 for remyelination.

    • Principal Investigator
      IIJIMA MASAHIRO
    • Project Period (FY)
      2013 – 2015
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  統合的脳MRIネットワーク解析によるALSの運動機能-前頭葉機能間関連性の解明

    • Principal Investigator
      千田 譲
    • Project Period (FY)
      2013 – 2014
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  To elucidate the pattern of progression in multiple system atrophy

    • Principal Investigator
      Ito Mizuki
    • Project Period (FY)
      2013 – 2015
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Therapeutic strategy of neurodegenerative disease using microRNAPrincipal Investigator

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2013
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Searching for factors associated with progression and prognosis in patients with sporadic amyotrophic lateral sclerosis

    • Principal Investigator
      Atsuta Naoki
    • Project Period (FY)
      2013 – 2015
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Involvement of novel ubiquitin ligases in the pathogenic mechanism of Alzheimer's disease and drug discovery for fundamental therapeutic agent

    • Principal Investigator
      Nomura Yasuyuki
    • Project Period (FY)
      2012 – 2015
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurochemistry/Neuropharmacology
    • Research Institution
      Kurume University
      Yokohama College of Pharmacy
  •  The association between non-motor symptom and visual hallucination in Parkinson disease

    • Principal Investigator
      HIRAYAMA Masaaki
    • Project Period (FY)
      2012 – 2014
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurophysiology and muscle physiology
    • Research Institution
      Nagoya University
  •  Clarification of the involvement of leptin and ghrelin in cardiovascular dysautonomia and vision for treatment in Parkinson disease.

    • Principal Investigator
      NAKAMURA TOMOHIKO
    • Project Period (FY)
      2012 – 2014
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Laboratory medicine
    • Research Institution
      Nagoya University
  •  Efficacy of cholinesterase inhibitor drugs in early Parkinson's disease patients

    • Principal Investigator
      WATANABE hirohisa
    • Project Period (FY)
      2012 – 2014
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of therapy targeting dysregulation of cell cycle and JNK pathway in polyglutamine diseases

    • Principal Investigator
      KATSUNO MASAHISA
    • Project Period (FY)
      2011 – 2013
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Novel therapeutic approaches using the delivery of specific miRNAs for polyglutamine diseases

    • Principal Investigator
      ADACHI Hiroaki
    • Project Period (FY)
      2011 – 2013
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Identification of therapeutic targets for ALS by screening for TDP-43 and FUS associated moleculesPrincipal Investigator

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2011 – 2012
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Elucidation of molecular pathogenesis in motor neurocircuit degeneration and development of therapy for motor neuron diseases

    • Principal Investigator
      KATSUNO Masahisa
    • Project Period (FY)
      2010 – 2014
    • Research Category
      Grant-in-Aid for Scientific Research on Innovative Areas (Research in a proposed research area)
    • Review Section
      Biological Sciences
    • Research Institution
      Nagoya University
  •  Exploration of disease-related genes based on personal genome analysis and elucidation of pathogenesis in ALS

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2010 – 2014
    • Research Category
      Grant-in-Aid for Scientific Research on Innovative Areas (Research in a proposed research area)
    • Review Section
      Biological Sciences
    • Research Institution
      Yokohama City University
      Nagoya University
  •  Elucidation of pathogenesis and therapy development of sporadic ALS by disease model

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2010 – 2012
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Yokohama City University
      Nagoya University
  •  Association between axonal damage and molecular basis in demyelinating neuropathies: prognosis and response to treatment

    • Principal Investigator
      KAWAGASHIRA Yuichi
    • Project Period (FY)
      2010 – 2012
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Establishing the biomarker of multiple system atrophy

    • Principal Investigator
      ITO Mizuki
    • Project Period (FY)
      2010 – 2012
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Comprehensive Brain Science Network

    • Principal Investigator
      Kimura Minoru
    • Project Period (FY)
      2010 – 2015
    • Research Category
      Grant-in-Aid for Scientific Research on Innovative Areas (Research in a proposed research area)
    • Research Institution
      Center for Novel Science Initatives, National Institutes of Natural Sciences
  •  Development of Molecular Targeted Disease Modifying Therapy for Polyglutamine DiseasesPrincipal Investigator

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2009 – 2013
    • Research Category
      Grant-in-Aid for Scientific Research (S)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Clarifying the mechanisms of amyloid deposition in familial amyloid polyneuropathy and its application to therapy

    • Principal Investigator
      KOIKE Huaruki
    • Project Period (FY)
      2009 – 2011
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Elucidation of the pathogenesis of visual halllucination in Parkinson's disease

    • Principal Investigator
      WATANABE Hirohisa, 川合 圭成
    • Project Period (FY)
      2009 – 2011
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Impaired pain processing in Parkinson's disease and its relative association with the non-motor symptom

    • Principal Investigator
      HIRAYAMA Masaaki
    • Project Period (FY)
      2009 – 2011
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      疼痛学
    • Research Institution
      Nagoya University
  •  ポリグルタミン病の病態抑止治療と神経賦活治療の併用療法

    • Principal Investigator
      足立 弘明
    • Project Period (FY)
      2009 – 2010
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  孤発性ALSのオートファジー機能解明と新規疾患モデルの確立

    • Principal Investigator
      田中 章景
    • Project Period (FY)
      2009
    • Research Category
      Grant-in-Aid for Challenging Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Therapeutic strategy for polyglutamine-mediated motor neuron disease via molecular chaperone-ubiquitin proteasome system

    • Principal Investigator
      ADACHI Hiroaki
    • Project Period (FY)
      2008 – 2010
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Pathogenesis-based therapy development for polyglutamine diseasesPrincipal Investigator

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Scientific Research (A)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of animal model for sporadic ALS

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Pathogenesis of axonal dysfuction in Japanese CIDP patients

    • Principal Investigator
      HATTORI Naoki
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Research on the molecular pathogenetic mechanism of tissue-specific toxicity mediated by ALS-linked mutant SOD1

    • Principal Investigator
      NIWA Jun-ichi
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Aichi Medical University
  •  古細菌プロテアソームによる神経変性疾患の治療Principal Investigator

    • Principal Investigator
      祖父江 元
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  エオジン好性核内封入体(NIHID)の原因遺伝子の探索・同定

    • Principal Investigator
      田中 章景, 小池 春樹
    • Project Period (FY)
      2007 – 2008
    • Research Category
      Grant-in-Aid for Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  HSP90阻害剤、17-AAGによる神経変性疾患の分子標的治療Principal Investigator

    • Principal Investigator
      祖父江 元
    • Project Period (FY)
      2006
    • Research Category
      Grant-in-Aid for Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Comprehensive genetic analysis by DNA Chip in inherited neuropathies

    • Principal Investigator
      ARIMURA Kimiyoshi
    • Project Period (FY)
      2006 – 2007
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Kagoshima University
  •  Development of therapies in polyglutamine diseases using hepatocyte growth factor (HGF)

    • Principal Investigator
      ADACHI Hiroaki
    • Project Period (FY)
      2006 – 2007
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of pathogenesis-based therapy for polyglutamine diseasesPrincipal Investigator

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2005 – 2009
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas
    • Review Section
      Biological Sciences
    • Research Institution
      Nagoya University
  •  Dorfin-CHIP融合タンパク質による筋萎縮性側索硬化症(ALS)の治療Principal Investigator

    • Principal Investigator
      祖父江 元
    • Project Period (FY)
      2005
    • Research Category
      Grant-in-Aid for Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Treatment of polyglutamine disease using small molecular compoundPrincipal Investigator

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Scientific Research (A)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Exploration of Target Molecules Related to Pathogenesis and Development of Therapy for Sporadic ALS

    • Principal Investigator
      TANAKA Fumiaki
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  An study on the mechanism of selective toxicity to motor neurons by mutant SOD1

    • Principal Investigator
      NIWA Jun-ichi
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of transgenic mouse model of axonal-form CMT with MPZ mutation and therapeutic approach to CMT

    • Principal Investigator
      KOIKE Haruki
    • Project Period (FY)
      2005 – 2006
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Research on Pathomechanisms of Brain Disorders

    • Principal Investigator
      NUKINA Nobuyuki
    • Project Period (FY)
      2004 – 2010
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas
    • Review Section
      Biological Sciences
    • Research Institution
      The Institute of Physical and Chemical Research
  •  慢性炎症性脱随性ポリニューロパチー(CIDP)の治療反応性の遺伝子背景の解明Principal Investigator

    • Principal Investigator
      祖父江 元
    • Project Period (FY)
      2004
    • Research Category
      Grant-in-Aid for Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of low-molecular-weight compound therapy for polyglutamine diseases

    • Principal Investigator
      DOYU Manabu
    • Project Period (FY)
      2004 – 2005
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Drosophila ALSモデルの確立とDorfinの病態機能の解明Principal Investigator

    • Principal Investigator
      祖父江 元
    • Project Period (FY)
      2003
    • Research Category
      Grant-in-Aid for Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Development of Pathogenesis-based treatment for spinal and bulbar muscular atrophyPrincipal Investigator

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2003 – 2004
    • Research Category
      Grant-in-Aid for Scientific Research (A)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  慢性炎症性脱髄性多発ニューロパチー(CIDP)の治療反応性関連遺伝子に関する研究Principal Investigator

    • Principal Investigator
      祖父江 元
    • Project Period (FY)
      2002
    • Research Category
      Grant-in-Aid for Exploratory Research
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Investigation into pathology of CAG repeat diseases and development of therapies

    • Principal Investigator
      DOYU Manabu
    • Project Period (FY)
      2002 – 2003
    • Research Category
      Grant-in-Aid for Scientific Research (B)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  investigation of pathomechanism of inflammatory myopathy (in view of chemokines)

    • Principal Investigator
      INUKAI Akira
    • Project Period (FY)
      2002 – 2003
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      NAGOYA UNIVERSITY
  •  運動ニューロン疾患の神経細胞死に係わる分子群の同定Principal Investigator

    • Principal Investigator
      祖父江 元
    • Project Period (FY)
      2000
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas (A)
    • Research Institution
      Nagoya University
  •  Elucidation of molecular mechanism of neuronal cell death in spinal and bulbar muscular atrophyPrincipal Investigator

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      2000 – 2004
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas
    • Review Section
      Biological Sciences
    • Research Institution
      Nagoya University
  •  Elucidation of pathogenesis in CAG-repeat diseases using DNA chip

    • Principal Investigator
      DOYU Manabu
    • Project Period (FY)
      2000 – 2001
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  遺伝子発現プロファイリングによるパーキンソン病の病態関連遺伝子の同定Principal Investigator

    • Principal Investigator
      祖父江 元
    • Project Period (FY)
      1998
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas (A)
    • Research Institution
      Nagoya University
  •  Detection of Relating Molecules for the Pathology of Amyotrophic Lateral Screlosis by the Expressed-Gene Profiling

    • Principal Investigator
      DOYU Manabu
    • Project Period (FY)
      1998 – 1999
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
  •  Molecular Medicine of Neurodegenerative Disease and Malignant Tumor

    • Principal Investigator
      TAKAHASHI Masahide
    • Project Period (FY)
      1998 – 2002
    • Research Category
      Grant-in-Aid for COE Research
    • Research Institution
      Nagoya University
  •  グリア研究の最前線

    • Principal Investigator
      Ikenaka Kazuhiro
    • Project Period (FY)
      1995 – 1996
    • Research Category
      Grant-in-Aid for Scientific Research (C)
    • Research Field
      Neurochemistry/Neuropharmacology
    • Research Institution
      Okazaki National Research Institutes
  •  神経疾患におけるTrk受容体の病的意義解明

    • Principal Investigator
      武藤 多津郎
    • Project Period (FY)
      1994
    • Research Category
      Grant-in-Aid for Scientific Research on Priority Areas
    • Research Institution
      福井医科大学
  •  Neurotrophin and their receptor mRNA expressions in neurodegenerative diseases.Principal Investigator

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      1994 – 1995
    • Research Category
      Grant-in-Aid for General Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      Nagoya University
      Aichi Medical University
  •  GENE EXPRESSION AND REGULATION OF NEUROTROPHINS AND THEIR RECEPTORS IN PERIPHERAL NEUROPATHIESPrincipal Investigator

    • Principal Investigator
      SOBUE Gen
    • Project Period (FY)
      1990 – 1992
    • Research Category
      Grant-in-Aid for General Scientific Research (C)
    • Research Field
      Neurology
    • Research Institution
      AICHI MEDICAL UNIVERSITY

All 2024 2023 2022 2020 2019 2018 2017 2016 2015 2014 2013 2012 2011 2010 2009 2008 2007 2006 2005 2004 2003 2002 Other

All Journal Article Presentation Book Patent Other

  • [Book] Findings of MIBG Cardiac Scintigraphy: Dementia with Lewy Bodies and Related Dementia. Clinical Assessment of the Autonomic Nervous System2016

    • Author(s)
      Watanabe H., Sobue G.
    • Total Pages
      317
    • Publisher
      Springer
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Book] Clinical Assessment of the Autonomic Nervous System2016

    • Author(s)
      Watanabe H, Sobue G.
    • Total Pages
      317
    • Publisher
      indings of MIBG Cardiac Scintigraphy: Dementia with Lewy Bodies and Related Dementia
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Book] Technical Considerations for MIBG Cardiac Scintigraphy. Clinical Assessment of the Autonomic Nervous System2016

    • Author(s)
      Watanabe H., Sobue G.
    • Total Pages
      317
    • Publisher
      Springer
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Book] Clinical Assessment of the Autonomic Nervous System2016

    • Author(s)
      Watanabe H, Sobue G.
    • Total Pages
      317
    • Publisher
      Technical Considerations for MIBG Cardiac Scintigraphy
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Book] Findings of MIBG Cardiac Scintigraphy: Dementia with Lewy Bodies and Related Dementia.2016

    • Author(s)
      Watanabe H, Sobue G.
    • Publisher
      Clinical Assessment of the Autonomic Nervous System Springer Japan
    • Data Source
      KAKENHI-PROJECT-15K15338
  • [Book] 【認知症の予防と対策】 前頭側頭型認知症への新しいアプローチ2016

    • Author(s)
      石垣 診祐, 祖父江 元
    • Publisher
      Medical Science Digest
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Book] Technical Considerations for MIBG Cardiac Scintigraphy2016

    • Author(s)
      Watanabe H, Sobue G.
    • Publisher
      Clinical Assessment of the Autonomic Nervous System Springer Japan
    • Data Source
      KAKENHI-PROJECT-15K15338
  • [Book] 免疫症候群(第2版)I2015

    • Author(s)
      小池春樹、 祖父江元、田中正美、市山高志、黒澤和大、藤井敬之、藤田之彦、上田昌美、桑原基、神林隆道、小川剛、竹下幸雄、千葉厚郎、桑原聡、中根俊成、鈴木重明、白石一浩、中村龍文、松永晶子、原誠ら
    • Total Pages
      928
    • Publisher
      日本臨床社
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Book] 神経疾患最新の治療2015-20172015

    • Author(s)
      小池春樹、 祖父江元、陣上直人、高橋良輔、松本慎一、高尾洋之、村上雄一、鈴木謙介、兵頭明夫、矢坂正弘、小坂憲司、松井真、竹島多賀夫、武田篤、伊藤秀文、松尾秀徳、荒木信夫、伊藤康夫、城倉健、中島健一ら
    • Total Pages
      310
    • Publisher
      南光堂
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Book] 自律神経機能検査2015

    • Author(s)
      小池春樹、 祖父江元、田村直俊、岩瀬敏、朝比奈正人、榊原隆次、内田さえ、大林光念、小野弓絵、黒澤美枝子、仙波恵美子、谷山紘太郎、原直人、間野忠明、宮本智之、山元敏正、高橋昭、水本結、上山敬司、安東由喜雄ら
    • Total Pages
      508
    • Publisher
      文光堂
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Book] Clinical Neuroscience2014

    • Author(s)
      飯島 正博, 祖父江 元
    • Publisher
      中外医学社
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Book] 多系統萎縮症(MSA)のすべて 画像検査 Clinical Neuroscinece2013

    • Author(s)
      伊藤瑞規、渡辺宏久、祖父江元
    • Data Source
      KAKENHI-PROJECT-22590955
  • [Book] Handbook of Clinical Neurology2013

    • Author(s)
      Koike H, Sobue G.
    • Publisher
      Elsevier
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Book] すべてがわかるALS・運動ニューロン疾患2013

    • Author(s)
      勝野雅央、足立弘明、祖父江 元
    • Total Pages
      384
    • Publisher
      中山書店
    • Data Source
      KAKENHI-PROJECT-23390231
  • [Book] Annual Review神経20132013

    • Author(s)
      川頭 祐一, 飯島 正博, 小池 春樹, 祖父江 元
    • Publisher
      中外医学社
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Book] 日本医師会雑誌2013

    • Author(s)
      飯島 正博, 小池 春樹, 祖父江 元
    • Publisher
      南山堂
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Book] Clinical Neuroscience2013

    • Author(s)
      飯島 正博, 小池 春樹, 祖父江 元
    • Publisher
      中外医学社
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Book] 球脊髄性筋萎縮症に対する分子標的治療法の開発.すべてがわかるALS・運動ニューロン疾患辻省次, 祖父江元編2013

    • Author(s)
      勝野雅央, 足立弘明, 祖父江元
    • Publisher
      中山書店
    • Data Source
      KAKENHI-PROJECT-23390231
  • [Book] 多系統萎縮症(MSA)のすべて 日本の MSA Clinical Neuroscinece2013

    • Author(s)
      渡辺宏久、伊藤瑞規、祖父江元
    • Data Source
      KAKENHI-PROJECT-22590955
  • [Book] PROGRESS IN MEDICINE2012

    • Author(s)
      渡辺宏久, 加藤重典, 千田譲, 伊藤瑞規, 祖父江元
    • Publisher
      ライフ・サイエンス
    • Data Source
      KAKENHI-PROJECT-24591293
  • [Book] 脊髄小脳変性症の Up-To-Date 孤発性 SCD 多系統萎縮症(MSA) 最新医学 67 巻5 号2012

    • Author(s)
      伊藤瑞規、渡辺宏久、祖父江元
    • Data Source
      KAKENHI-PROJECT-22590955
  • [Book] Companion to peripheral neuropathy : Illustrated cases and new developments.2010

    • Author(s)
      Koike H, Sobue G.
    • Publisher
      Elsevier Saunders
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Book] Clinical features and Molecular Mechanisms of spinal and bulbar muscular atrophy (SBMA).(Shamim I. Ahmad ed., In Diseases of DNA Repair.)2009

    • Author(s)
      Katsuno, M., Banno, H., Suzuki, K., Adachi, H., Tanaka, F., Sobue, G.
    • Publisher
      Landes Bioscience
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Book] 医学のあゆみ2006

    • Author(s)
      祖父江元ら
    • Total Pages
      6
    • Publisher
      球脊髄性筋萎縮症に対する分子標的治療薬の開発-既存低分子化合物の臨床応用
    • Data Source
      KAKENHI-PROJECT-18659258
  • [Book] 看護のための最新医学講座 第1巻 脳・神経系疾患 第2版.2005

    • Author(s)
      丹羽淳一, 祖父江元
    • Total Pages
      696
    • Publisher
      中山書店
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] ALSFRS-R decline rate prior to baseline is not useful for stratifying subsequent progression of functional decline2024

    • Author(s)
      Hamatani Tatsuto、Atsuta Naoki、Sano Fumiya、Nakamura Ryoichi、Hayashi Yukikazu、Sobue Gen
    • Journal Title

      Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration

      Volume: 25 Issue: 3-4 Pages: 388-399

    • DOI

      10.1080/21678421.2024.2309989

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-19K07973, KAKENHI-PROJECT-22K07359, KAKENHI-PROJECT-22K07509
  • [Journal Article] An Exploratory Trial of EPI-589 in Amyotrophic Lateral Sclerosis (EPIC-ALS): Protocol for a Multicenter, Open-Labeled, 24-Week, Single-Group Study.2023

    • Author(s)
      Haji S, Fujita K, Oki R, Osaki Y, Miyamoto R, Morino H, Nagano S, Atsuta N, Kanazawa Y, Matsumoto Y, Arisawa A, Kawai H, Sato Y, Sakaguchi S, Yagi K, Hamatani T, Kagimura T, Yanagawa H, Mochizuki H, Doyu M, Sobue G, Harada M, Izumi Y.
    • Journal Title

      JMIR Res Protoc.

      Volume: 12 Pages: e42032-e42032

    • DOI

      10.2196/42032

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-22K07359, KAKENHI-PROJECT-23K18265, KAKENHI-PROJECT-23K06975, KAKENHI-PROJECT-19K07969, KAKENHI-PROJECT-21H02841, KAKENHI-PUBLICLY-22H04811
  • [Journal Article] Safety and Clinical Benefits of Laryngeal Closure in Patients with Amyotrophic Lateral Sclerosis.2023

    • Author(s)
      Yokoi S, Nishio N, Maruo T, Hiramatsu M, Mukoyama N, Tsuzuki H, Wada A, Atsuta N, Ito D, Tsuboi T, Sobue G, Katsuno M, Fujimoto Y, Sone M.
    • Journal Title

      Dysphagia.

      Volume: 38(1) Issue: 1 Pages: 211-219

    • DOI

      10.1007/s00455-022-10454-0

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-22K07359
  • [Journal Article] 多因子性神経難病の全ゲノム解析:筋萎縮性側索硬化症2023

    • Author(s)
      中村亮一、熱田直樹、祖父江元
    • Journal Title

      医学のあゆみ

      Volume: 285 Pages: 103-109

    • Data Source
      KAKENHI-PROJECT-22K07509
  • [Journal Article] 【神経疾患とゲノム医療】個別病態・疾患のゲノム医療 筋萎縮性側索硬化症2022

    • Author(s)
      中村 亮一, 熱田 直樹, 祖父江 元
    • Journal Title

      Clinical Neuroscience

      Volume: 40 Pages: 1138-1142

    • Data Source
      KAKENHI-PROJECT-22K07509
  • [Journal Article] Serum asymmetric dimethylarginine level correlates with the progression and prognosis of amyotrophic lateral sclerosis.2022

    • Author(s)
      Ikenaka K, Maeda Y, Hotta Y, Nagano S, Yamada S, Ito D, Torii R, Kakuda K, Tatebe H, Atsuta N, Aguirre C, Kimura Y, Baba K, Tokuda T, Katsuno M, Kimura K, Sobue G, Mochizuki H.
    • Journal Title

      Eur J Neurol.

      Volume: 29(5) Issue: 5 Pages: 1410-1416

    • DOI

      10.1111/ene.15254

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-22K07359, KAKENHI-PROJECT-21H02841
  • [Journal Article] The SYNGAP1 3'UTR Variant in ALS Patients Causes Aberrant SYNGAP1 Splicing and Dendritic Spine Loss by Recruiting HNRNPK.2022

    • Author(s)
      Yokoi S, Ito T, Sahashi K, Nakatochi M, Nakamura R, Tohnai G, Fujioka Y, Ishigaki S, Udagawa T, Izumi Y, Morita M, Kano O, Oda M, Sone T, Okano H, Atsuta N, Katsuno M, Okada Y, Sobue G.
    • Journal Title

      J Neurosci.

      Volume: 42(47) Pages: 8881-8896

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-22K07359
  • [Journal Article] The SYNGAP1 3'UTR variant in ALS patients causes aberrant SYNGAP1 splicing and dendritic spine loss by recruiting HNRNPK2022

    • Author(s)
      Yokoi S, Ito T, Sahashi K, Nakatochi M, Tohnai G, Nakamura R, Fujioka Y, Ishigaki S, Udagawa T, Izumi Y, Morita M, Kano O, Oda M, Sone T, Okano H, Atsuta N, Katsuno M, Okada Y*, Sobue G*
    • Journal Title

      Journal of Neuroscience

      Volume: 42 Issue: 47 Pages: 8881-8896

    • DOI

      10.1523/jneurosci.0455-22.2022

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07539, KAKENHI-PROJECT-19K07969, KAKENHI-PROJECT-19K07973, KAKENHI-PROJECT-21K07471, KAKENHI-PROJECT-22K07509, KAKENHI-PROJECT-22K07515, KAKENHI-PROJECT-22K07545, KAKENHI-PROJECT-20K16611, KAKENHI-PROJECT-21K15622, KAKENHI-PROJECT-17K19465, KAKENHI-PROJECT-18K15470, KAKENHI-PROJECT-19H03576, KAKENHI-PROJECT-23K24249, KAKENHI-PROJECT-23K21410
  • [Journal Article] Convenient Auditory-Based Language and Executive Function Test for Patients With Amyotrophic Lateral Sclerosis: A Pilot Study2022

    • Author(s)
      Ohdake Reiko、Watanabe Hirohisa、Kawabata Kazuya、Ogura Aya、Sato Maki、Tanaka Yasuhiro、Imai Kazunori、Masuda Michihito、Kato Toshiyasu、Yokoi Takamasa、Hara Kazuhiro、Nakamura Ryoichi、Atsuta Naoki、Nakagawa Masafumi、Katsuno Masahisa、Sobue Gen
    • Journal Title

      Archives of Clinical Neuropsychology

      Volume: 38 Issue: 1 Pages: 57-71

    • DOI

      10.1093/arclin/acac069

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-19K07973, KAKENHI-PROJECT-22K07359, KAKENHI-PROJECT-22K07509
  • [Journal Article] Mutation screening of the DNAJC7 gene in Japanese patients with sporadic amyotrophic lateral sclerosis2022

    • Author(s)
      Tohnai Genki、Nakamura Ryoichi、Atsuta Naoki、(他29名) Sobue Gen
    • Journal Title

      Neurobiology of Aging

      Volume: 113 Pages: 131-136

    • DOI

      10.1016/j.neurobiolaging.2021.12.002

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-19K06523, KAKENHI-PROJECT-22K07359, KAKENHI-PROJECT-22K07509, KAKENHI-PROJECT-19K07973
  • [Journal Article] Changes in white matter fiber density and morphology across the adult lifespan: A cross-sectionalfixel-based analysis.2020

    • Author(s)
      Choy SW, Bagarinao E, Watanabe H, Sobue G,et al.
    • Journal Title

      Hum Brain Mapp

      Volume: in press

    • Peer Reviewed
    • Data Source
      KAKENHI-WRAPUP-19H05447
  • [Journal Article] Prognosis of amyotrophic lateral sclerosis patients undergoing tracheostomy invasive ventilation therapy in Japan2020

    • Author(s)
      Hayashi Naoki、Atsuta Naoki、Yokoi Daichi、Nakamura Ryoichi、Nakatochi Masahiro、Katsuno Masahisa、Izumi Yuishin、Kanai Kazuaki、Hattori Nobutaka、Taniguchi Akira、Morita Mitsuya、Kano Osamu、Shibuya Kazumoto、Kuwabara Satoshi、Suzuki Naoki、Aoki Masashi、Aiba Ikuko、Mizoguchi Kouichi、Oda Masaya、Kaji Ryuji、Sobue Gen
    • Journal Title

      Journal of Neurology, Neurosurgery & Psychiatry

      Volume: 91 Issue: 3 Pages: 285-290

    • DOI

      10.1136/jnnp-2019-322213

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07519, KAKENHI-PROJECT-19K07973, KAKENHI-PROJECT-17K09778, KAKENHI-PROJECT-17K09811, KAKENHI-PROJECT-17K16110
  • [Journal Article] ALS is a multistep process in South Korean, Japanese, and Australian patients.2020

    • Author(s)
      Vucic S, Higashihara M, Sobue G, Atsuta N, Doi Y, Kuwabara S, Kim SH, Kim I, Oh KW, Park J, Kim EM, Talman P, Menon P, Kiernan MC; PACTALS Consortium.
    • Journal Title

      Neurology

      Volume: 94 Issue: 15

    • DOI

      10.1212/wnl.0000000000009015

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-17K09778
  • [Journal Article] Characteristic Features of FUS Inclusions in Spinal Motor Neurons of Sporadic Amyotrophic Lateral Sclerosis.2020

    • Author(s)
      Ikenaka K, Ishigaki S, Iguchi Y, Kawai K, Fujioka Y, Yokoi S, Abdelhamid RF, Nagano S, Mochizuki H, Katsuno M, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol.

      Volume: 79(4) Pages: 370-377

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-WRAPUP-19H05447
  • [Journal Article] Longitudinal Speech Change After Subthalamic Nucleus Deep Brain Stimulation in Parkinson's Disease Patients: A 2-Year Prospective Study.2020

    • Author(s)
      Tanaka Y, Tsuboi T, Watanabe H,Sobue G, et al.
    • Journal Title

      J Parkinsons Dis.

      Volume: 10(1) Issue: 1 Pages: 131-140

    • DOI

      10.3233/jpd-191798

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-WRAPUP-19H05447
  • [Journal Article] Reorganization of brain networks and its association with general cognitive performance over the adult lifespan.2019

    • Author(s)
      Epifanio Bagarinao, Hirohisa Watanabe, Satoshi Maesawa, Daisuke Mori, Kazuhiro Hara, Kazuya Kawabata, Noritaka Yoneyama, Reiko Ohdake,…他 Haruo Isoda, Shinji Naganawa, Gen Sobue
    • Journal Title

      Sci Rep.

      Volume: 9(1) Issue: 1 Pages: 11352-11352

    • DOI

      10.1038/s41598-019-47922-x

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K19510, KAKENHI-WRAPUP-19H05447, KAKENHI-PROJECT-15H01846, KAKENHI-PROJECT-17H04259, KAKENHI-PROJECT-17K10890, KAKENHI-PROJECT-19H04025
  • [Journal Article] Brain Protein Aging and Dementia Control2019

    • Author(s)
      G Sobue G,N Sahara.
    • Journal Title

      Frontiers

      Volume: -

    • DOI

      10.3389/fnins.2019.00029

    • Peer Reviewed
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Journal Article] 増大特集 ALS2019 ALSにおける患者レジストリの役割-JaCALSなど2019

    • Author(s)
      熱田 直樹、中村 亮一、林 直毅、藤内 玄規、勝野 雅央、祖父江 元
    • Journal Title

      BRAIN and NERVE

      Volume: 71 Issue: 11 Pages: 1215-1225

    • DOI

      10.11477/mf.1416201431

    • ISSN
      1344-8129, 1881-6096
    • Year and Date
      2019-11-01
    • Data Source
      KAKENHI-PROJECT-19K07973, KAKENHI-PROJECT-17K09778
  • [Journal Article] Pathogenesis of frontotemporal lobar degeneration: insights from loss of function theory and early involvement of the caudate nucleus2019

    • Author(s)
      Gen Sobue* ;Shinsuke Ishgaki and Hirohisa Watanabe
    • Journal Title

      Frontiers

      Volume: -

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-INTERNATIONAL-15K21714
  • [Journal Article] Alterations in Cognition-Related Networks in Multiple System Atrophy.2019

    • Author(s)
      Kawabata K, Hara K, Watanabe H,Sobue G, et al.
    • Journal Title

      Cerebellum.

      Volume: 18(4) Issue: 4 Pages: 770-780

    • DOI

      10.1007/s12311-019-01031-7

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-WRAPUP-19H05447
  • [Journal Article] Semantic deficits in ALS related to right lingual/fusiform gyrus network involvement2019

    • Author(s)
      Ogura Aya、Watanabe Hirohisa、Kawabata Kazuya、Ohdake Reiko、Tanaka Yasuhiro、Masuda Michihito、Kato Toshiyasu、Imai Kazunori、Yokoi Takamasa、Hara Kazuhiro、Bagarinao Epifanio、Riku Yuichi、Nakamura Ryoichi、Kawai Yoshinari、Nakatochi Masahiro、Atsuta Naoki、Katsuno Masahisa、Sobue Gen
    • Journal Title

      EBioMedicine

      Volume: 47 Pages: 506-517

    • DOI

      10.1016/j.ebiom.2019.08.022

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-19K07973, KAKENHI-PROJECT-17K09778
  • [Journal Article] Increase of arginine dimethylation correlates with the progression and prognosis of ALS.2019

    • Author(s)
      Ikenaka K, Atsuta N, Maeda Y, Hotta Y, Nakamura R, Kawai K, Yokoi D, Hirakawa A, Taniguchi A, Morita M, Mizoguchi K, Mochizuki H, Kimura K, Katsuno M, Sobue G.
    • Journal Title

      Neurology.

      Volume: 92 Issue: 16

    • DOI

      10.1212/wnl.0000000000007311

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K09778, KAKENHI-PROJECT-17K16116, KAKENHI-PROJECT-19K07973
  • [Journal Article] Tau Accumulation and Network Breakdown in Alzheimer’s Disease2019

    • Author(s)
      Watanabe Hirohisa、Bagarinao Epifanio、Yokoi Takamasa、Yamaguchi Hiroshi、Ishigaki Shinsuke、Mausuda Michihito、Katsuno Masahisa、Sobue Gen
    • Journal Title

      Adv Exp Med Biol

      Volume: 1184 Pages: 231-240

    • DOI

      10.1007/978-981-32-9358-8_19

    • ISBN
      9789813293571, 9789813293588
    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-WRAPUP-19H05447
  • [Journal Article] TDP-43 regulates early-phase insulin secretion via CaV1.2-mediated exocytosis in islets2019

    • Author(s)
      Araki Kunihiko、(他10名)、Ishigaki Shinsuke、Nakamichi Yoko、Tsunekawa Shin、Seino Yusuke、Yamamoto Akiko、Takayama Yasunori、Hidaka Shihomi、Tominaga Makoto、Ohara-Imaizumi Mica、Suzuki Atsushi、Ishiguro Hiroshi、Enomoto Atsushi、Yoshida Mari、Arima Hiroshi、Muramatsu Shin-ichi、Sobue Gen、Katsuno Masahisa
    • Journal Title

      Journal of Clinical Investigation

      Volume: 129 Issue: 9 Pages: 3578-3593

    • DOI

      10.1172/jci124481

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-WRAPUP-19H05447, KAKENHI-PROJECT-17H04195, KAKENHI-PROJECT-17K08547, KAKENHI-PROJECT-17K09753
  • [Journal Article] Tau isoform expression and phosphorylation in marmoset brains2019

    • Author(s)
      Sharma Govinda、Huo Anni、Kimura Taeko、Shiozawa Seiji、Kobayashi Reona、Sahara Naruhiko、Ishibashi Minaka、Ishigaki Shinsuke、Saito Taro、Ando Kanae、Murayama Shigeo、Hasegawa Masato、Sobue Gen、Okano Hideyuki、Hisanaga Shin-ichi
    • Journal Title

      Journal of Biological Chemistry

      Volume: 294 Issue: 30 Pages: 11433-11444

    • DOI

      10.1074/jbc.ra119.008415

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-PROJECT-19K06472, KAKENHI-PROJECT-19K06896, KAKENHI-PROJECT-19K06942, KAKENHI-PUBLICLY-19H05437, KAKENHI-WRAPUP-19H05447, KAKENHI-PROJECT-16H06277
  • [Journal Article] Distinct manifestation of cognitive deficits associate with different resting-state network disruptions in non-demented patients with Parkinson's disease.2018

    • Author(s)
      Kawabata K
    • Journal Title

      J Neurol.

      Volume: 265(3) Issue: 3 Pages: 688-700

    • DOI

      10.1007/s00415-018-8755-5

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K16117, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-16K09713
  • [Journal Article] Modeling sporadic ALS in iPSC-derived motor neurons identifies a potential therapeutic agent.2018

    • Author(s)
      Fujimori K, Ishikawa M, Otomo A, Atsuta N, Nakamura R, Akiyama T, Hadano S, Aoki M, Saya H, Sobue G, Okano H.
    • Journal Title

      Nat Med.

      Volume: 24 Issue: 10 Pages: 1579-1589

    • DOI

      10.1038/s41591-018-0140-5

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K09778, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117007, KAKENHI-PROJECT-17H01401, KAKENHI-PROJECT-17K16116
  • [Journal Article] Biomarker-based analysis of preclinical progression in spinal and bulbar muscular atrophy.2018

    • Author(s)
      Hijikata Y, Hashizume A, Yamada S, Inagaki T, Ito D, Hirakawa A, Suzuki K, Atsuta N, Tsuboi T, Hattori M, Hori A, Banno H, Sobue G, Katsuno M.
    • Journal Title

      Neurology

      Volume: 90 Issue: 17 Pages: 1501-1509

    • DOI

      10.1212/wnl.0000000000005360

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17H04195, KAKENHI-PROJECT-15K09311
  • [Journal Article] Citrullination of RGG Motifs in FET Proteins by PAD4 Regulates Protein Aggregation and ALS Susceptibility2018

    • Author(s)
      Tanikawa Chizu、Ueda Koji、Suzuki Akari、Iida Aritoshi、Nakamura Ryoichi、Atsuta Naoki、Tohnai Genki、Sobue Gen、Saichi Naomi、Momozawa Yukihide、Kamatani Yoichiro、Kubo Michiaki、Yamamoto Kazuhiko、Nakamura Yusuke、Matsuda Koichi
    • Journal Title

      Cell Reports

      Volume: 22 Issue: 6 Pages: 1473-1483

    • DOI

      10.1016/j.celrep.2018.01.031

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-16KT0116, KAKENHI-PROJECT-16K08634, KAKENHI-PROJECT-17K09778, KAKENHI-PROJECT-17K16116, KAKENHI-PROJECT-26710007, KAKENHI-PUBLICLY-16H01566, KAKENHI-PROJECT-16H02676
  • [Journal Article] Silencing of FUS in the common marmoset (Callithrix jacchus) brainvia stereotaxic injection of an adeno-associated virus encoding shRNA.2018

    • Author(s)
      Endo K, Ishigaki S, Masamizu Y, Fujioka Y, Watakabe A, Yamamori T, Hatanaka N, Nambu A, Okado H, Katsuno M, Watanabe H, Matsuzaki M, Sobue G
    • Journal Title

      Neurosci Res

      Volume: in press Pages: 30183-9

    • DOI

      10.1016/j.neures.2017.08.006

    • Peer Reviewed
    • Data Source
      KAKENHI-INTERNATIONAL-15K21731, KAKENHI-PLANNED-15H05873, KAKENHI-ORGANIZER-15H05871, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-26250009, KAKENHI-PROJECT-15K09310, KAKENHI-PROJECT-18K07367
  • [Journal Article] Clinical and Imaging Features of Multiple System Atrophy: Challenges for an Early and Clinically Definitive Diagnosis.2018

    • Author(s)
      H Watanabe, Y. Riku, K Hara, K Kawabata, T Nakamura, M Ito, M Hirayama, M Yoshida, M Katsuno, G Sobue.
    • Journal Title

      J Mov Disord

      Volume: 11 (No3) Issue: 3 Pages: 107-120

    • DOI

      10.14802/jmd.18020

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-16K09713, KAKENHI-PROJECT-17K16117
  • [Journal Article] Corpus callosal involvement is correlated with cognitive impairment in multiple system atrophy.2018

    • Author(s)
      Hara K, Watanabe H, Bagarinao E, Kawabata K, Yoneyama N, Ohdake R, Imai K, Masuda M, Yokoi T, Ogura A, Tsuboi T, Ito M, Atsuta N, Niwa H, Taoka T, Maesawa S, Naganawa S, Katsuno M, Sobue G.
    • Journal Title

      J Neurol.

      Volume: 265 Issue: 9 Pages: 2079-2087

    • DOI

      10.1007/s00415-018-8923-7

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-17K09778, KAKENHI-PROJECT-17K10397, KAKENHI-PROJECT-18K19510, KAKENHI-ORGANIZER-26117001, KAKENHI-PROJECT-17H04259, KAKENHI-PROJECT-17K16117
  • [Journal Article] Frequency and characteristics of the TBK1 gene variants in Japanese patients with sporadic amyotrophic lateral sclerosis2018

    • Author(s)
      Tohnai Genki、Nakamura Ryoichi、Sone Jun、Nakatochi Masahiro、Yokoi Daichi、Katsuno Masahisa、Watanabe Hazuki、Watanabe Hirohisa、Ito Mizuki、Li Yuanzhe、Izumi Yuishin、et al. Atsuta Naoki、Sobue Gen
    • Journal Title

      Neurobiology of Aging

      Volume: 64 Pages: 158.e15-158.e19

    • DOI

      10.1016/j.neurobiolaging.2017.12.005

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K09778, KAKENHI-PROJECT-17K16116, KAKENHI-PROJECT-17K16118, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117006, KAKENHI-PROJECT-17J03762
  • [Journal Article] Age-related impairment in Addenbrooke's cognitive examination revised scores in patients with amyotrophic lateral sclerosis.2018

    • Author(s)
      Masuda M, Watanabe H, Tanaka Y, Ohdake R, Ogura A, Yokoi T, Imai K, Kawabata K, Riku Y, Hara K, Nakamura R, Atsuta N, Katsuno M, Sobue G.
    • Journal Title

      Amyotroph Lateral Scler Frontotemporal Degener.

      Volume: Epub ahead of print Issue: 7-8 Pages: 1-7

    • DOI

      10.1080/21678421.2018.1510009

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K09778, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-17K16116, KAKENHI-PROJECT-17K16117
  • [Journal Article] An unbiased data-driven age-related structural brain parcellation for the identification of intrinsic brain volume changes over the adult lifespan.2018

    • Author(s)
      Bagarinao E
    • Journal Title

      Neuroimage.

      Volume: 169 Pages: 134-144

    • DOI

      10.1016/j.neuroimage.2017.12.014

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-17K16117, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-17H04259, KAKENHI-PROJECT-15K09349, KAKENHI-PROJECT-17K10890
  • [Journal Article] Pathogenesis of Frontotemporal Lobar Degeneration: Insights From Loss of Function Theory and Early Involvement of the Caudate Nucleus2018

    • Author(s)
      Sobue Gen、Ishigaki Shinsuke、Watanabe Hirohisa
    • Journal Title

      Frontiers in Neuroscience

      Volume: 12 Pages: 473-473

    • DOI

      10.3389/fnins.2018.00473

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004
  • [Journal Article] Effects of Gradient Coil Noise and Gradient Coil Replacement on the Reproducibility of Resting State Networks2018

    • Author(s)
      Bagarinao Epifanio、Tsuzuki Erina、Yoshida Yukina、Ozawa Yohei、Kuzuya Maki、Otani Takashi、Koyama Shuji、Isoda Haruo、Watanabe Hirohisa、Maesawa Satoshi、Naganawa Shinji、Sobue Gen
    • Journal Title

      Frontiers in Human Neuroscience

      Volume: 12 Pages: 148-148

    • DOI

      10.3389/fnhum.2018.00148

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-17K10890, KAKENHI-PROJECT-18K19510, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-17H04259
  • [Journal Article] Involvement of the Precuneus/Posterior Cingulate Cortex Is Significant for the Development of Alzheimer’s Disease: A PET (THK5351, PiB) and Resting fMRI Study2018

    • Author(s)
      Yokoi Takamasa、Watanabe Hirohisa、Ishigaki Shinsuke、Katsuno Masahisa、Miyao Shinichi、Kato Katsuhiko、Naganawa Shinji、Harada Ryuichi、Okamura Nobuyuki、Yanai Kazuhiko、Yoshida Mari、Sobue Gen (ほか9名)
    • Journal Title

      Frontiers in Aging Neuroscience

      Volume: 10 Pages: 304-304

    • DOI

      10.3389/fnagi.2018.00304

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-PROJECT-18K19510, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-17H04259, KAKENHI-PROJECT-18H02771, KAKENHI-PROJECT-17K16117, KAKENHI-PROJECT-18K15538, KAKENHI-PLANNED-26117003
  • [Journal Article] Importance of Functional Loss of FUS in FTLD/ALS2018

    • Author(s)
      Ishigaki Shinsuke、Sobue Gen
    • Journal Title

      Frontiers in Molecular Biosciences

      Volume: 5 Pages: 44-44

    • DOI

      10.3389/fmolb.2018.00044

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-18K07367, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004
  • [Journal Article] Severe hyposmia and aberrant functional connectivity in cognitively normal Parkinson's disease.2018

    • Author(s)
      Yoneyama N
    • Journal Title

      PLoS One.

      Volume: 13(1) Issue: 1 Pages: e0190072-e0190072

    • DOI

      10.1371/journal.pone.0190072

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-17K16117, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-16K09713
  • [Journal Article] Quantitative Assessment of Swallowing Dysfunction in Patients with Spinal and Bulbar Muscular Atrophy2017

    • Author(s)
      Hashizume Atsushi、Banno Haruhiko、Katsuno Masahisa、Hijikata Yasuhiro、Yamada Shinichiro、Inagaki Tomonori、Suzuki Keisuke、Sobue Gen
    • Journal Title

      Intern. Med.

      Volume: 56 Issue: 23 Pages: 3159-3165

    • DOI

      10.2169/internalmedicine.8799-16

    • NAID

      130006235519

    • ISSN
      0918-2918, 1349-7235
    • Language
      English
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09311
  • [Journal Article] Reply: Neuronal intranuclear (hyaline) inclusion disease and fragile X-associated tremor/ataxia syndrome: a morphological and molecular dilemma2017

    • Author(s)
      Sone Jun、Nakamura Tomohiko、Koike Haruki、Katsuno Masahisa、Tanaka Fumiaki、Iwasaki Yasushi、Yoshida Mari、Sobue Gen
    • Journal Title

      BRAIN

      Volume: 140 Issue: 8 Pages: e52-e52

    • DOI

      10.1093/brain/awx158

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Journal Article] Long-term treatment with leuprorelin for spinal and bulbar muscular atrophy: natural history-controlled study2017

    • Author(s)
      Hashizume Atsushi、Katsuno Masahisa、Suzuki Keisuke、Hirakawa Akihiro、Hijikata Yasuhiro、Yamada Shinichiro、Inagaki Tomonori、Banno Haruhiko、Sobue Gen
    • Journal Title

      Journal of Neurology, Neurosurgery & Psychiatry

      Volume: 88 Issue: 12 Pages: 1026-1032

    • DOI

      10.1136/jnnp-2017-316015

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09311
  • [Journal Article] Adult-onset neuronal intranuclear inclusion disease presented transient global amnesia—a case report2017

    • Author(s)
      竹下 潤、小林 宏光、下江 豊、曽根 淳、祖父江 元、栗山 勝
    • Journal Title

      Rinsho Shinkeigaku

      Volume: 57 Issue: 6 Pages: 303-306

    • DOI

      10.5692/clinicalneurol.cn-000994

    • NAID

      130006882271

    • ISSN
      0009-918X, 1882-0654
    • Language
      Japanese
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Journal Article] Non-motor multiple system atrophy associated with sudden death: pathological observations of autonomic nuclei.2017

    • Author(s)
      Riku Y, Watanabe H, Mimuro M, Iwasaki Y, Ito M, Katsuno M, Sobue G, Yoshida M.
    • Journal Title

      J Neurol

      Volume: 264(11) Issue: 11 Pages: 2249-2257

    • DOI

      10.1007/s00415-017-8604-y

    • Peer Reviewed
    • Data Source
      KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002
  • [Journal Article] Altered tau isoform ratio caused by loss of Fus and Sfpq function leads to FTLD-like phenotypes2017

    • Author(s)
      Ishigaki S, Fujioka Y, Okada Y, Riku Y, Udagawa T, Honda D, Yokoi S, Endo K, Ikenaka K, Takagi S, Iguchi Y, Sahara N, Takashima A, Okano H, Yoshida M, Warita H, Aoki M, Watanabe H, Okado H, Katsuno H, Sobue G.
    • Journal Title

      Cell Reports

      Volume: 18 Issue: 5 Pages: 1118-1131

    • DOI

      10.1016/j.celrep.2017.01.013

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PUBLICLY-15H01568, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117007, KAKENHI-PROJECT-26290016, KAKENHI-PROJECT-16K15480, KAKENHI-PROJECT-25640038, KAKENHI-PROJECT-16K14569, KAKENHI-PROJECT-17K09753, KAKENHI-ORGANIZER-26117001, KAKENHI-PROJECT-15H04278, KAKENHI-PLANNED-26117004, KAKENHI-PLANNED-26117008, KAKENHI-PROJECT-17H04195, KAKENHI-PROJECT-15K06793, KAKENHI-PROJECT-15K09310
  • [Journal Article] Marked Involvement of the Striatal Efferent System in TAR DNA-Binding Protein 43 kDa-Related Frontotemporal Lobar Degeneration and Amyotrophic Lateral Sclerosis.2017

    • Author(s)
      Riku Y., Watanabe H., Yoshida M., Mimuro M., Iwasaki Y., Masuda M., Ishigaki S., Katsuno M., Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: in press Issue: 8 Pages: 801-811

    • DOI

      10.1093/jnen/nlw053

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-26461269, KAKENHI-PROJECT-15K15338, KAKENHI-PROJECT-15K19483, KAKENHI-PROJECT-15K09310, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Pathologic Involvement of Glutamatergic Striatal Inputs From the Cortices in TAR DNA-Binding Protein 43kDa-Related Frontotemporal Lobar Degeneration and Amyotrophic Lateral Sclerosis.2017

    • Author(s)
      Riku Y, Watanabe H, Yoshida M, Mimuro M, Iwasaki Y, Masuda M, Ishigaki S.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 76(9) Issue: 9 Pages: 759-768

    • DOI

      10.1093/jnen/nlx055

    • Peer Reviewed
    • Data Source
      KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15K09310
  • [Journal Article] 球脊髄性筋萎縮症の早期診断2017

    • Author(s)
      土方靖浩 橋詰 淳 勝野雅央 祖父江元
    • Journal Title

      神経内科

      Volume: 86 Pages: 17-22

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09311
  • [Journal Article] Correlation of insulin resistance and motor function in spinal and bulbar muscular atrophy.2017

    • Author(s)
      Nakatsuji H, Araki A, Hashizume A, Hijikata Y, Yamada S, Inagaki T, Suzuki K, Banno H, Suga N, Okada Y, Ohyama M, Nakagawa T, Kishida K, Funahashi T, Shimomura I, Okano H, Katsuno M, Sobue G.
    • Journal Title

      J Neurol.

      Volume: in press Issue: 5 Pages: 839-847

    • DOI

      10.1007/s00415-017-8405-3

    • NAID

      120006331845

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PUBLICLY-15H01568, KAKENHI-PROJECT-26293206, KAKENHI-PROJECT-25640038, KAKENHI-PROJECT-17K19465, KAKENHI-PUBLICLY-17H05707, KAKENHI-PROJECT-15H04278
  • [Journal Article] Structural MRI correlates of amyotrophic lateral sclerosis progression2017

    • Author(s)
      Senda Joe、Atsuta Naoki、Watanabe Hirohisa、Bagarinao Epifanio、Imai Kazunori、Yokoi Daichi、Riku Yuichi、Masuda Michihito、Nakamura Ryoichi、Watanabe Hazuki、Ito Mizuki、Katsuno Masahisa、Naganawa Shinji、Sobue Gen
    • Journal Title

      Journal of Neurology, Neurosurgery & Psychiatry

      Volume: 88 Issue: 11 Pages: 901-907

    • DOI

      10.1136/jnnp-2016-314337

    • NAID

      120006375888

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17K09778, KAKENHI-PROJECT-17K16116, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002
  • [Journal Article] Case of adult-onset neuronal intranuclear hyaline inclusion disease with negative electroretinogram2017

    • Author(s)
      Yamada W, Takekoshi A, Ishida K, Mochizuki K, Sone J, Sobue G, Hayashi Y, Inuzuka T, Miyake Y
    • Journal Title

      Doc Ophthalmol

      Volume: - Issue: 3 Pages: 221-226

    • DOI

      10.1007/s10633-017-9584-z

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-26462634, KAKENHI-PROJECT-15K09312
  • [Journal Article] Adult-Onset Neuronal Intranuclear Inclusion Disease in Two Female Siblings2017

    • Author(s)
      Yoshimoto T, Takamatsu K, Kurashige T, Sone J, Sobue G, Kuriyama M.
    • Journal Title

      BRAIN and NERVE

      Volume: 69 Issue: 3 Pages: 267-274

    • DOI

      10.11477/mf.1416200737

    • NAID

      40021133351

    • ISSN
      1344-8129, 1881-6096
    • Year and Date
      2017-03-01
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Journal Article] 発症後10年以上経過観察し得た神経核内封入体病の1例2017

    • Author(s)
      徳永 隆司, 西村 裕之, 立花 久大, 曽根 淳, 祖父江 元
    • Journal Title

      神経内科

      Volume: )86巻2号 Pages: 251-254

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Journal Article] Altered GluA1 (Gria1) Function and Accumbal Synaptic Plasticity in the ClockΔ19 Model of Bipolar Mania.2017

    • Author(s)
      Parekh PK, Becker-Krail D, Sundaravelu P, Ishigaki S, Okado H, Sobue G, Huang Y, McClung CA.
    • Journal Title

      Biol Psychiatry

      Volume: S0006 Issue: 11 Pages: 31721-3

    • DOI

      10.1016/j.biopsych.2017.06.022

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15K09310
  • [Journal Article] 3'UTR Length-Dependent Control of SynGAP Isoform α2 mRNA by FUS and ELAV-like Proteins Promotes Dendritic Spine Maturation and Cognitive Function.2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M.
    • Journal Title

      Cell Rep

      Volume: 20(13) Issue: 13 Pages: 3071-3084

    • DOI

      10.1016/j.celrep.2017.08.100

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-17H04195, KAKENHI-PROJECT-15K09310
  • [Journal Article] Neuronal Intranuclear Inclusion Disease2017

    • Author(s)
      曽根 淳、祖父江 元
    • Journal Title

      BRAIN and NERVE

      Volume: 69 Issue: 1 Pages: 5-16

    • DOI

      10.11477/mf.1416200628

    • ISSN
      1344-8129, 1881-6096
    • Year and Date
      2017-01-01
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Journal Article] R-spondin 2 promotes acetylcholine receptor clustering at the neuromuscular junction via Lgr5.2016

    • Author(s)
      Nakashima H., Ohkawara B., Ishigaki S., Fukudome T., Ito K., Tsushima M., Konishi H., Okuno T., Yoshimura T., Ito M., Masuda A., Sobue G., Kiyama H., Ishiguro N., Ohno K.
    • Journal Title

      Sci Rep

      Volume: 22 Issue: 1 Pages: 28512-28512

    • DOI

      10.1038/srep28512

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15H04840, KAKENHI-PROJECT-25430049, KAKENHI-PROJECT-15K06707, KAKENHI-PROJECT-15K06755, KAKENHI-PROJECT-15K09310, KAKENHI-PROJECT-16K07055, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Clinicopathological features of adult-onset neuronal intranuclear inclusion disease.2016

    • Author(s)
      Sone J., Nakamura T., Koike H., Takashima H., Hashiguchi A., Kohno Y., Kurashige T., Kuriyama M., Takiyama Y., Tsuchiya M., Kitagawa N., Kawamoto M., Yoshimura H., Suto Y., Nakayasu H., Uehara N., Sugiyama H., Takahashi M., Kokubun N., Konno T., Katsuno M., Tanaka F., Iwasaki Y., Yoshida M., Sobue G., et al
    • Journal Title

      Brain

      Volume: 139 Issue: 12 Pages: 3170-3186

    • DOI

      10.1093/brain/aww249

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-ORGANIZER-26117001
  • [Journal Article] HMGB1, a pathogenic molecule that induces neurite degeneration via TLR4-MARCKS, is a potential therapeutic target for Alzheimer's disease2016

    • Author(s)
      Fujita, K., Motoki, K., Tagawa, K., Chen, X., Hama, H., Nakajima, K., Homma, H., Tamura, T., Watanabe, H., Katsuno, M., Matsumi, C., Kajikawa, M., Saito, T., Saido, T., Sobue, G., Miyawaki, A., Okazawa, H.
    • Journal Title

      Scientific Reports

      Volume: 6 Issue: 1 Pages: 31895-31895

    • DOI

      10.1038/srep31895

    • Peer Reviewed / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-16H02655, KAKENHI-PROJECT-26290019, KAKENHI-PROJECT-15K15338, KAKENHI-PROJECT-16K07040
  • [Journal Article] Involvement of the caudate nucleus head and its networks in sporadic amyotrophic lateral sclerosis-frontotemporal dementia continuum.2016

    • Author(s)
      Masuda, M., Senda, J., Watanabe, H., Epifanio, B., Tanaka, Y., Imai, K., Riku, Y., Li, Y., Nakamura, R., Ito, M., Ishigaki, S., Atsuta, N., Koike, H., Katsuno, M., Hattori, N., Naganawa, S., and Sobue, G.
    • Journal Title

      Amyotroph Lateral Scler Frontotemporal Degener

      Volume: 17 Pages: 571-579

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Journal Article] Exosome secretion is a key pathway for clearance of pathological TDP-43.2016

    • Author(s)
      Iguchi Y,, Eid L,, Parent M,, Soucy G,, Bareil C,, Riku Y,, Kawai K,, Takagi S,, Yoshida M,, Katsuno M,, Sobue G., Julien JP.
    • Journal Title

      Brain

      Volume: 139 Issue: 12 Pages: 3187-3201

    • DOI

      10.1093/brain/aww237

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-26293206, KAKENHI-PROJECT-26461269, KAKENHI-PROJECT-16K15480, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Impaired muscle uptake of creatine in spinal and bulbar muscular atrophy.2016

    • Author(s)
      Hijikata Y., Katsuno M., Suzuki K., Hashizume A., Araki A., Yamada S., Inagaki T., Iida M., Noda S., Nakanishi H., Banno H., Mano T., Hirakawa A., Adachi H., Watanabe H., Yamamoto M., Sobue G.
    • Journal Title

      Ann Clin Transl Neurol

      Volume: 3 Issue: 7 Pages: 537-546

    • DOI

      10.1002/acn3.324

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-26293206, KAKENHI-PROJECT-26293207, KAKENHI-PROJECT-15K15338, KAKENHI-ORGANIZER-26117001
  • [Journal Article] 特集 認知症・神経変性疾患の克服への挑戦 Ⅱ.分子標的治療の確立を目指して 変異タンパク質凝集体への治療的アプローチ2016

    • Author(s)
      佐橋健太郎、祖父江元
    • Journal Title

      生体の科学

      Volume: 67 Issue: 4 Pages: 296-302

    • DOI

      10.11477/mf.2425200457

    • ISSN
      0370-9531, 1883-5503
    • Year and Date
      2016-08-15
    • Data Source
      KAKENHI-PROJECT-26461268
  • [Journal Article] MiR-298 Counteracts Mutant Androgen Receptor Toxicity in Spinal and Bulbar Muscular Atrophy2016

    • Author(s)
      Pourshafie N, Lee PR, Chen KL, Harmison GG, Bott LC, Katsuno M, Sobue G, Burnett BG, Fischbeck KH, Rinaldi C
    • Journal Title

      Mol Ther

      Volume: 24 Issue: 5 Pages: 937-45

    • DOI

      10.1038/mt.2016.13

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Journal Article] Decreased Peak Expiratory Flow Associated with Muscle Fiber-Type Switching in Spinal and Bulbar Muscular Atrophy.2016

    • Author(s)
      Yamada S, Hashizume A, Hijikata Y, Inagaki T, Suzuki K, Kondo N, Kawai K, Noda S, Nakanishi H, Banno H, Hirakawa A, Koike H, Halievski K, Jordan CL, Katsuno M, Sobue G.
    • Journal Title

      PLoS One.

      Volume: 11(12) Issue: 12 Pages: e0168846-e0168846

    • DOI

      10.1371/journal.pone.0168846

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-26293206, KAKENHI-PROJECT-26461269, KAKENHI-PROJECT-16K15480
  • [Journal Article] Gene Expression Profile of Inflammatory Myopathy with Malignancy is Similar to that of Dermatomyositis rather than Polymyositis2016

    • Author(s)
      Noda, T., Iijima, M., Noda, S., Maeshima, S., Nakanishi, H., Kimura, S., Koike, H., Ishigaki, S., Iguchi, Y., Katsuno, M., and Sobue, G.
    • Journal Title

      Intern. Med.

      Volume: 55 Issue: 18 Pages: 2571-2580

    • DOI

      10.2169/internalmedicine.55.6706

    • NAID

      130005414859

    • ISSN
      0918-2918, 1349-7235
    • Language
      English
    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15K09310, KAKENHI-PROJECT-16K09693, KAKENHI-ORGANIZER-26117001
  • [Journal Article] FUS/TLS acts as an aggregation-dependent modifier of polyglutamine disease model mice.2016

    • Author(s)
      Kino Y, Washizu C, Kurosawa M, Yamada M, Doi H, Takumi T, Adachi H, Katsuno M, Sobue G, Hicks GG, Hattori N, Shimogori T, Nukina N.
    • Journal Title

      Sci Rep.

      Volume: 6 Issue: 1 Pages: 35236-35236

    • DOI

      10.1038/srep35236

    • Peer Reviewed / Acknowledgement Compliant / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PUBLICLY-15H01567, KAKENHI-PLANNED-16H06463, KAKENHI-PROJECT-16H06316, KAKENHI-PROJECT-26293206, KAKENHI-PROJECT-26293207, KAKENHI-PROJECT-25461299, KAKENHI-PROJECT-16K09683
  • [Journal Article] Involvement of the caudate nucleus head and its networks in sporadic amyotrophic lateral sclerosis-frontotemporal dementia continuum.2016

    • Author(s)
      Masuda, M., Senda, J., Watanabe, H., Epifanio, B., Tanaka, Y., Imai, K., Riku, Y., Li, Y., Nakamura, R., Ito, M., Ishigaki, S., Atsuta, N., Koike, H., Katsuno, M., Hattori, N., Naganawa, S., and Sobue, G.
    • Journal Title

      Amyotroph Lateral Scler Frontotemporal Degener

      Volume: 17 Issue: 7-8 Pages: 571-579

    • DOI

      10.1080/21678421.2016.1211151

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-25293263, KAKENHI-PROJECT-15K15338, KAKENHI-PROJECT-15K19485, KAKENHI-PROJECT-16K09700, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Age of onset differentially influences the progression of regional dysfunction in sporadic amyotrophic lateral sclerosis.2016

    • Author(s)
      Yokoi D, Atsuta N, Watanabe H, Nakamura R, Hirakawa A, Ito M, Watanabe H, Katsuno M, Izumi Y, Morita M, Taniguchi A, Oda M, Abe K, Mizoguchi K, Kano O, Kuwabara S, Kaji R, Sobue G; JaCALS.
    • Journal Title

      J Neurol.

      Volume: Epub ahead of print

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-25461277
  • [Journal Article] Amyotrophic lateral sclerosis and motor neuron syndromes in Asia.2016

    • Author(s)
      Shahrizaila N., Sobue G., Kuwabara S., Kim SH., Birks C., Fan DS., Bae JS., Hu CJ., Gourie-Devi M., Noto Y., Shibuya K., Goh KJ., Kaji R., Tsai CP., Cui L., Talman P., Henderson RD., Vucic S., Kiernan MC.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 87 Issue: 8 Pages: 821-830

    • DOI

      10.1136/jnnp-2015-312751

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-PROJECT-16H06673, KAKENHI-ORGANIZER-26117001
  • [Journal Article] A rapid functional decline type of amyotrophic lateral sclerosis is linked to low expression of TTN.2016

    • Author(s)
      Watanabe H, Atsuta N, Hirakawa A, Nakamura R, Nakatochi M, Ishigaki S, Iida A, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: in press Issue: 8 Pages: 851-8

    • DOI

      10.1136/jnnp-2015-311541

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09310, KAKENHI-PROJECT-26461319, KAKENHI-PROJECT-25461277, KAKENHI-PROJECT-26670439, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15K15338, KAKENHI-PROJECT-15K19485
  • [Journal Article] Next-generation sequencing of 28 ALS-related genes in a Japanese ALS cohort2016

    • Author(s)
      Ryoichi Nakamura, Jun Sone, Naoki Atsuta, Genki Tohnai, Hazuki Watanabe, Daichi Yokoi, Masahiro Nakatochi, Hirohisa Watanabe, Mizuki Ito, Jo Senda, Masahisa Katsuno, Fumiaki Tanaka, Yuanzhe Li, Yuishin Izumi, Mitsuya Morita, Akira Taniguchi, Osamu Kano, Masaya Oda, Satoshi Kuwabara, Koji Abe.
    • Journal Title

      Neurobiology of Aging

      Volume: 39 Pages: 219-219

    • DOI

      10.1016/j.neurobiolaging.2015.11.030

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-15K19485, KAKENHI-PROJECT-221S0002, KAKENHI-PROJECT-25461277, KAKENHI-PROJECT-15K15337, KAKENHI-PROJECT-26670439, KAKENHI-PROJECT-26670445, KAKENHI-PROJECT-25860725, KAKENHI-PROJECT-25293207, KAKENHI-ORGANIZER-26117001, KAKENHI-PROJECT-15H05667, KAKENHI-PROJECT-26461319
  • [Journal Article] 抗MAG抗体陽性ニューロパチー2015

    • Author(s)
      川頭祐一、 小池春樹、 祖父江元
    • Journal Title

      日本臨床

      Volume: 73 増刊7 Pages: 440-445

    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Impaired peripheral vasoconstrictor response to orthostatic stress in patients with multiple system atrophy2015

    • Author(s)
      Suzuki, J. Nakamura, T. Hirayama, M. Mizutani, Y. Okada, A. Ito, M. Watanabe, H. Sobue, G.
    • Journal Title

      Parkinsonism Relat Disord

      Volume: 21 Issue: 8 Pages: 917-22

    • DOI

      10.1016/j.parkreldis.2015.05.023

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-15K09350, KAKENHI-PROJECT-25461313
  • [Journal Article] Efficacy of intravenous immunoglobulin for treatment of Lambert-Eaton myasthenic syndrome without anti-presynaptic P/Q-type voltage-gated calcium channel antibodies: A case report2015

    • Author(s)
      Okada A, Koike H, Nakamura T, Motomura M, Sobue G
    • Journal Title

      Neuromuscul Disord

      Volume: 25 Issue: 1 Pages: 70-2

    • DOI

      10.1016/j.nmd.2014.08.006

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-26461302
  • [Journal Article] Evaluation of resting state networks in patients with gliomas: connectivity changes in the unaffected side and its relation to cognitive function.2015

    • Author(s)
      Maesawa S, Bagarinao E, Fujii M, Futamura M, Motomura K, Watanabe H, Mori D, Sobue G, Wakabayashi T.
    • Journal Title

      PLoS One

      Volume: 10 Issue: 2 Pages: e0118072-e0118072

    • DOI

      10.1371/journal.pone.0118072

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-24591293, KAKENHI-PUBLICLY-25110715, KAKENHI-PROJECT-25460284, KAKENHI-PROJECT-26462202, KAKENHI-PLANNED-26117002, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Microglial keratan sulfate epitope elicits in central nervous tissues of transgenic model mice and patients with amyotrophic lateral sclerosis.2015

    • Author(s)
      Foyez T, Takeda-Uchimura Y, Ishigaki S, Narentuya, Zhang Z, Sobue G, Kadomatsu K, Uchimura K.
    • Journal Title

      Am J Pathol

      Volume: 185 Issue: 11 Pages: 3053-3065

    • DOI

      10.1016/j.ajpath.2015.07.016

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-15K08265, KAKENHI-PROJECT-15K09310, KAKENHI-ORGANIZER-23110001, KAKENHI-PLANNED-23110002, KAKENHI-PLANNED-26117004
  • [Journal Article] FUS regulates AMPA receptor function and FTLD/ALS-associated behaviour via GluA1 mRNA stabilization.2015

    • Author(s)
      Udagawa, T., Fujioka, Y., Tanaka, M., Honda, D., Yokoi, S., Riku, Y., Ibi, D., Nagai, T., Yamada, K., Watanabe, H., Katsuno, M., Inada, T., Ohno, K., Sokabe, M., Okado, H., Ishigaki S*., and Sobue, G.
    • Journal Title

      Nat Commun

      Volume: 6 Issue: 1 Pages: 7098-7098

    • DOI

      10.1038/ncomms8098

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-15K09310, KAKENHI-PUBLICLY-25118508, KAKENHI-PROJECT-221S0003, KAKENHI-PLANNED-26116003, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-24247028, KAKENHI-PROJECT-15H06719, KAKENHI-PROJECT-25460093, KAKENHI-PROJECT-15K15337, KAKENHI-PROJECT-26670439, KAKENHI-PROJECT-25860708, KAKENHI-PROJECT-26293206, KAKENHI-PLANNED-26117002, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Voice features of Parkinson's disease patients with subthalamic nucleus deep brain stimulation.2015

    • Author(s)
      Tanaka Y, Tsuboi T, Watanabe H, Kajita Y, Fujimoto Y, Ohdake R, Yoneyama N, Masuda M, Hara K, Senda J, Ito M, Atsuta N, Horiguchi S, Yamamoto M, Wakabayashi T, Sobue G.
    • Journal Title

      J Neurol.

      Volume: 262 Issue: 5 Pages: 1173-1181

    • DOI

      10.1007/s00415-015-7681-z

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-26117002, KAKENHI-ORGANIZER-26117001
  • [Journal Article] A functional scale for spinal and bulbar muscular atrophy: Cross-sectional and longitudinal study.2015

    • Author(s)
      Hashizume A, Katsuno M, Suzuki K, Banno H, Suga N, Mano T, Araki A, Hijikata Y, Grunseich C, Kokkinis A, Hirakawa A, Watanabe H, Yamamoto M, Fischbeck KH, Sobue G
    • Journal Title

      Neuromuscul Disord.

      Volume: 25 Issue: 7 Pages: 554-562

    • DOI

      10.1016/j.nmd.2015.03.008

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Journal Article] 脱髄性ニューロパチーランビエ絞輪部における分子病態2015

    • Author(s)
      川頭祐一、 小池春樹、 祖父江元
    • Journal Title

      Annual Review神経

      Volume: 2015 Pages: 219-225

    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Silencing neuronal mutant androgen receptor in a mouse model of spinal and bulbar muscular atrophy.2015

    • Author(s)
      Sahashi K, Katsuno M, Hung G, Adachi H, Kondo N, Nakatsuji H, Tohnai G, Iida M, Bennett CF, Sobue G.
    • Journal Title

      Hum Mol Genet.

      Volume: 24(21) Issue: 21 Pages: 5985-94

    • DOI

      10.1093/hmg/ddv300

    • Peer Reviewed / Acknowledgement Compliant / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26461268, KAKENHI-PROJECT-26670439, KAKENHI-PROJECT-26860665, KAKENHI-PROJECT-26293206
  • [Journal Article] Uncompacted Myelin Lamellae and Nodal Ion Channel Disruption in POEMS Syndrome.Uncompacted Myelin Lamellae and Nodal Ion Channel Disruption in POEMS Syndrome.J Neuropathol Exp Neurol.2015

    • Author(s)
      Hashimoto R, Koike H, Takahashi M, Ohyama K, Kawagashira Y, Iijima M, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol.

      Volume: 74 Issue: 12 Pages: 1127-1136

    • DOI

      10.1097/nen.0000000000000257

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-26461292, KAKENHI-PROJECT-25461278
  • [Journal Article] Astrocyte-Derived TGF-β1 Accelerates Disease Progression in ALS Mice by Interfering with the Neuroprotective Functions of Microglia and T Cells.2015

    • Author(s)
      Endo F, Komine O, Fujimori-Tonou N, Katsuno M, Jin S, Watanabe S, Sobue G, Dezawa M, Wyss-Coray T, Yamanaka K
    • Journal Title

      Cell Reports

      Volume: 11 Issue: 4 Pages: 592-604

    • DOI

      10.1016/j.celrep.2015.03.053

    • Peer Reviewed / Acknowledgement Compliant / Open Access / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-25860252, KAKENHI-PROJECT-26830046, KAKENHI-ORGANIZER-23111001, KAKENHI-PROJECT-26670439, KAKENHI-PROJECT-26293206, KAKENHI-PROJECT-26293208, KAKENHI-PLANNED-26117002, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Contractile dysfunction in muscle may underlie androgen-dependent motor dysfunction in spinal bulbar muscular atrophy2015

    • Author(s)
      Oki K, Halievski K, Vicente L, Xu Y, Zeolla D, Poort J, Katsuno M, Adachi H, Sobue G, Wiseman RW, Breedlove SM, Jordan CL
    • Journal Title

      J Appl Physiol

      Volume: 118 Issue: 7 Pages: 941-52

    • DOI

      10.1152/japplphysiol.00886.2014

    • Peer Reviewed
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Journal Article] Clinicopathologic features of folate-deficiency neuropathy.2015

    • Author(s)
      Koike H, Takahashi M, Ohyama K, Hashimoto R, Kawagashira Y, Iijima M, Katsuno M, Doi H, Tanaka F, Sobue G.
    • Journal Title

      Neurology

      Volume: 84 Issue: 10 Pages: 1026-1033

    • DOI

      10.1212/wnl.0000000000001343

    • Peer Reviewed / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09344, KAKENHI-PROJECT-26461292, KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-25461278
  • [Journal Article] Glycoprotein nonmetastatic melanoma protein B ameliorates skeletal muscle lesions in a SOD1G93A mouse model of amyotrophic lateral sclerosis.2015

    • Author(s)
      Nagahara Y, Shimazawa M, Tanaka H, Ono Y, Noda Y, Ohuchi K, Tsuruma K, Katsuno M, Sobue G, Hara H.
    • Journal Title

      J Neurosci Res.

      Volume: 93 Issue: 10 Pages: 1552-1566

    • DOI

      10.1002/jnr.23619

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K15337
  • [Journal Article] インフルエンザ感染を契機にFisher症候群の急激な症候悪化を呈したCIDPの1例2015

    • Author(s)
      両角佐織、 安井敬三、 長谷川康博、 小池春樹、 祖父江元
    • Journal Title

      Peripheral Nerve

      Volume: 26 Pages: 93-97

    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Myotonia-like symptoms in a patient with spinal and bulbar muscular atrophy.2015

    • Author(s)
      Araki K, Nakanishi H, Nakamura T, Atsuta N, Yamada S, Hijikata Y, Hashizume A, Suzuki K, Katsuno M, Sobue G
    • Journal Title

      Neuromuscul Disord.

      Volume: 25 Issue: 11 Pages: 913-915

    • DOI

      10.1016/j.nmd.2015.08.006

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Journal Article] 【免疫性神経疾患-基礎・臨床研究の最新知見-】 免疫性末梢神経疾患 慢性炎症性脱髄性多発根ニューロパチー(CIDP) CIDPの疫学・症状と神経症候2015

    • Author(s)
      飯島正博、祖父江元
    • Journal Title

      日本臨床

      Volume: 73 Pages: 400-7

    • Data Source
      KAKENHI-PROJECT-25461278
  • [Journal Article] Axonal loss influences the response to rituximab treatment in neuropathy associated with IgM monoclonal gammopathy with anti-myelin-associated glycoprotein antibody2015

    • Author(s)
      Kawagashira Y, Koike H, Ohyama K, Hashimoto R, Iijima M, Adachi H, Katsuno M, Chapman M, Lunn M, Sobue G
    • Journal Title

      J Neurol Sci

      Volume: 348 Issue: 1-2 Pages: 67-73

    • DOI

      10.1016/j.jns.2014.11.006

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-25461278, KAKENHI-PROJECT-26461292
  • [Journal Article] Overexpression of hepatocyte growth factor in SBMA model mice has an additive effect on combination therapy with castration.2015

    • Author(s)
      Ding Y, Adachi H, Katsuno M, Huang Z, Jiang YM, Kondo N, Iida M, Tohnai G, Nakatsuji H, Funakoshi H, Nakamura T, Sobue G
    • Journal Title

      Biochem Biophys Res Commun

      Volume: 468 Issue: 4 Pages: 677-683

    • DOI

      10.1016/j.bbrc.2015.11.015

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-26670439, KAKENHI-PROJECT-26860665
  • [Journal Article] Meclozine promotes longitudinal skeletal growth in transgenic mice with achondroplasia carrying a gain-of-function mutation in the FGFR3 gene2015

    • Author(s)
      Matsushita M, Hasegawa S, Kitoh H, Mori K, Ohkawara B, Yasoda A, Masuda A, Ishiguro N, Ohno K,
    • Journal Title

      Endocrinology

      Volume: 156 Issue: 1 Pages: 584-554

    • DOI

      10.1016/j.fob.2014.11.007

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-24500469, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002
  • [Journal Article] Voice features of Parkinson's disease patients with subthalamic nucleus deep brain stimulation.2015

    • Author(s)
      Tanaka Y, Tsuboi T, Watanabe H, Kajita Y, Fujimoto Y, Ohdake R, Yoneyama N, Masuda M, Hara K, Senda J, Ito M, Atsuta N, Horiguchi S, Yamamoto M, Wakabayashi T, Sobue G.
    • Journal Title

      J Neurol

      Volume: Epub

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24591293
  • [Journal Article] Immunoglobulin G4-related pathologic features in inflammatory neuropathies.2015

    • Author(s)
      Ohyama K, Koike H, Takahashi M, Kawagashira Y, Iijima M, Watanabe H, Sobue G.
    • Journal Title

      Neurology.

      Volume: 85 Issue: 16 Pages: 1400-1407

    • DOI

      10.1212/wnl.0000000000002039

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-26461292, KAKENHI-PROJECT-25461278, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Clinicopathological features of sarcoidosis manifesting as generalized chronic myopathy2015

    • Author(s)
      Maeshima S, Koike H, Noda S, Noda T, Nakanishi H, Iijima M, Ito M, Kimura S, Sobue G
    • Journal Title

      J Neurol

      Volume: 262 Issue: 4 Pages: 1035-45

    • DOI

      10.1007/s00415-015-7680-0

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-25461278
  • [Journal Article] Head Lift Exercise Improves Swallowing Dysfunction in Spinal and Bulbar Muscular Atrophy2015

    • Author(s)
      Mano T, Katsuno M, Banno H, Suzuki K, Suga N, Hashizume A, Araki A, Hijikata Y, Tanaka S, Takatsu J, Watanabe H, Yamamoto M, Sobue G
    • Journal Title

      Eur Neurol

      Volume: 74 Issue: 5-6 Pages: 251-258

    • DOI

      10.1159/000431088

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-26670439, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Intravenous immunoglobulin for chronic residual peripheral neuropathy in eosinophilic granulomatosis with polyangiitis (Churg-Strauss syndrome): A multicenter, double-blind trial2015

    • Author(s)
      Koike H, Akiyama K, Saito T, Sobue G
    • Journal Title

      J Neurol

      Volume: 262 Issue: 3 Pages: 752-9

    • DOI

      10.1007/s00415-014-7618-y

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Position-specific binding of FUS to nascent RNA regulates mRNA length.2015

    • Author(s)
      Masuda A, Takeda J, Okuno T, Okamoto T, Ohkawara B, Ito M, Ishigaki S, Sobue G, Ohno K.
    • Journal Title

      Genes Dev.

      Volume: 29(10) Issue: 10 Pages: 1045-57

    • DOI

      10.1101/gad.255737.114

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-15K06707, KAKENHI-PROJECT-15K06755, KAKENHI-PROJECT-15K09310, KAKENHI-PROJECT-25430049, KAKENHI-PUBLICLY-25118508, KAKENHI-PLANNED-26117002, KAKENHI-PLANNED-26117004, KAKENHI-PROJECT-15H04840, KAKENHI-PROJECT-24500469
  • [Journal Article] Transcriptional and post-transcriptional regulation of transmembrane protein 132A.2015

    • Author(s)
      Oh-Hashi, K., Sone, A., Hikiji, T., Hirata, Y., Vitiello, M., Fedele, M., Ishigaki S., Sobue, G., and Kiuchi, K.
    • Journal Title

      Mol Cell Biochem

      Volume: 405 Issue: 1-2 Pages: 291-299

    • DOI

      10.1007/s11010-015-2419-x

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09310, KAKENHI-PLANNED-26117004
  • [Journal Article] アミロイドニューロパチー2015

    • Author(s)
      小池春樹、 祖父江元
    • Journal Title

      Peripheral Nerve

      Volume: 26 Pages: 15-24

    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Characteristic laryngoscopic findings in Parkinson's disease patients after subthalamic nucleus deep brain stimulation and its correlation with voice disorder2015

    • Author(s)
      Tsuboi, T. Watanabe, H. Tanaka, Y. Ohdake, R. Yoneyama, N. Hara, K. Ito, M. Hirayama, M. Yamamoto, M. Fujimoto, Y. Kajita, Y. Wakabayashi, T. Sobue, G.
    • Journal Title

      J Neural Transm (Vienna)

      Volume: 122 Issue: 12 Pages: 1663-72

    • DOI

      10.1007/s00702-015-1436-y

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-15K09350, KAKENHI-PROJECT-15K15338, KAKENHI-PROJECT-25461313, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Neuronal intranuclear inclusion disease manifesting with new-onset epilepsy in the elderly2015

    • Author(s)
      Tomoko Toyota, Zhe Huang, Souhei Nohara, Kazumasa Okada, Shingo Kakeda, Yukunori Korogi, Toshiyuki Nakayama, Jun Sone, Gen Sobue, Hiroaki Adachi
    • Journal Title

      Neurology and Clinical Neuroscience

      Volume: 3 Issue: 6 Pages: 238-240

    • DOI

      10.1111/ncn3.12016

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Journal Article] 傍腫瘍性ニューロパチー2015

    • Author(s)
      大山健、 小池春樹、 祖父江元
    • Journal Title

      日本臨床

      Volume: 73 増刊7 Pages: 782-787

    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Pioglitazone suppresses neuronal and muscular degeneration caused by polyglutamine-expanded androgen receptors.2015

    • Author(s)
      Iida M, Katsuno M, Nakatsuji H, Adachi H, Kondo N, Miyazaki Y, Tohnai G, Ikenaka K, Watanabe H, Yamamoto M, Kishida K, Sobue G
    • Journal Title

      Hum Mol Genet.

      Volume: 24 Issue: 2 Pages: 314-329

    • DOI

      10.1093/hmg/ddu445

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PLANNED-22110005, KAKENHI-ORGANIZER-26117001, KAKENHI-PROJECT-26670439, KAKENHI-PROJECT-26670440, KAKENHI-PROJECT-26860665, KAKENHI-PROJECT-26293206, KAKENHI-PLANNED-26117002
  • [Journal Article] A highly sensitive assay of IRE1 activity using the small luciferase NanoLuc: Evaluation of ALS-related genetic and pathological factors.2015

    • Author(s)
      Hikiji, T., Norisada, J., Hirata, Y., Okuda, K., Nagasawa, H., Ishigaki S., Sobue, G., Kiuchi, K., and Oh-hashi, K.
    • Journal Title

      Biochem Biophys Res Commun

      Volume: 463 Issue: 4 Pages: 881-887

    • DOI

      10.1016/j.bbrc.2015.05.132

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-15K09310, KAKENHI-PLANNED-26117004
  • [Journal Article] 血管炎の新しい分類と基本的な考え方 – 中枢神経血管炎の位置づけ2015

    • Author(s)
      小池春樹、 祖父江元
    • Journal Title

      BRAIN and NERVE: 神経研究の進歩

      Volume: 67 Pages: 243-248

    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Factors affecting longitudinal functional decline and survival in amyotrophic lateral sclerosis patients.2014

    • Author(s)
      Watanabe H, Atsuta N, Nakamura R, Hirakawa A, Watanabe H, Ito M, Senda J, Katsuno M, Izumi Y, Morita M, Tomiyama H, Taniguchi A, Aiba I, Abe K, Mizoguchi K, Oda M, Kano O, Okamoto K, Kuwabara S, Hasegawa K, Imai T, Aoki M, Tsuji S, Nakano I, Kaji R, Sobue G.
    • Journal Title

      Amyotroph Lateral Scler Frontotemporal Degener.

      Volume: Epub ahead of print Issue: 3-4 Pages: 230-6

    • DOI

      10.3109/21678421.2014.990036

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-25461277, KAKENHI-PROJECT-26670439, KAKENHI-PLANNED-26117002, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Brugada syndrome in spinal and bulbar muscular atrophy.2014

    • Author(s)
      Araki A, Katsuno M, Suzuki K, Banno H, Suga N, Hashizume A, Mano T, Hijikata Y, Nakatsuji H, Watanabe H, Yamamoto M, Makiyama T, Ohno S, Fukuyama M, Morimoto S, Horie M, Sobue G
    • Journal Title

      Neurology

      Volume: 82 Issue: 20 Pages: 1813-1821

    • DOI

      10.1212/wnl.0000000000000434

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-24659428, KAKENHI-PROJECT-25461054, KAKENHI-ORGANIZER-26117001, KAKENHI-PROJECT-26293206, KAKENHI-PROJECT-26670440, KAKENHI-PLANNED-26117002
  • [Journal Article] Anti-androgen flutamide protects male mice from androgen-dependent toxicity in three models of spinal bulbar muscular atrophy2014

    • Author(s)
      Renier KJ, Troxell-Smith SM, Johansen JA, Katsuno M, Adachi H, Sobue G, Chua JP, Sun Kim H, Lieberman AP, Breedlove SM, Jordan CL
    • Journal Title

      Endocrinology.

      Volume: 155 Issue: 7 Pages: 2624-2634

    • DOI

      10.1210/en.2013-1756

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-26293206, KAKENHI-PROJECT-26670440
  • [Journal Article] Neuronal intranuclear inclusion disease cases with leukoencephalopathy diagnosed via skin biopsy.2014

    • Author(s)
      Sone J, Kitagawa N, Sugawara E, Iguchi M, Nakamura R, Koike H, Iwasaki Y, Yoshida M, Takahashi T, Chiba S, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 85(3) Issue: 3 Pages: 354-356

    • DOI

      10.1136/jnnp-2013-306084

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24591257, KAKENHI-PROJECT-25461276
  • [Journal Article] Anti-androgen flutamide protects male mice from androgen-dependent toxicity in three models of spinal bulbar muscular atrophy2014

    • Author(s)
      Renier KJ, Troxell-Smith SM, Johansen JA, Katsuno M, Adachi H, Sobue G, Chua JP, Sun Kim H, Lieberman AP, Breedlove SM, Jordan CL
    • Journal Title

      Endocrinology

      Volume: (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Journal Article] Role of cardiac sympathetic nerves in preventing orthostatic hypotension in Parkinson's disease2014

    • Author(s)
      Nakamura, T. Hirayama, M. Hara, T. Mizutani, Y. Suzuki, J. Watanabe, H. Sobue, G.
    • Journal Title

      Parkinsonism Relat Disord

      Volume: 20 Issue: 4 Pages: 409-14

    • DOI

      10.1016/j.parkreldis.2014.01.003

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-24500458, KAKENHI-PROJECT-24591293, KAKENHI-ORGANIZER-26117001
  • [Journal Article] 【神経系の慢性炎症】 神経変性疾患における慢性炎症 筋萎縮性側索硬化症(ALS)2014

    • Author(s)
      熱田 直樹、祖父江 元
    • Journal Title

      別冊Bio Clinica: 慢性炎症と疾患

      Volume: 3 Pages: 106-11

    • Data Source
      KAKENHI-PROJECT-25461277
  • [Journal Article] What is the prototype of familial amyloid polyneuropathy?2014

    • Author(s)
      Koike H, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 85 Issue: 7 Pages: 713-713

    • DOI

      10.1136/jnnp-2013-306241

    • Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Impact of albuminuria on early neurological deterioration and lesion volume expansion in lenticulostriate small infarcts.2014

    • Author(s)
      Umemura T, Senda J, Fukami Y, Mashita S, Kawamura T, Sakakibara T, Sobue G.
    • Journal Title

      Stroke

      Volume: 45 Issue: 2 Pages: 587-590

    • DOI

      10.1161/strokeaha.113.003164

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461312
  • [Journal Article] 【首下がり症候群】 筋萎縮性側索硬化症と首下がり2014

    • Author(s)
      熱田 直樹、祖父江 元
    • Journal Title

      神経内科

      Volume: 81 Pages: 57-61

    • Data Source
      KAKENHI-PROJECT-25461277
  • [Journal Article] Paeoniflorin eliminates a mutant AR via NF-YA-dependent proteolysis in spinal and bulbar muscular atrophy2014

    • Author(s)
      Tohnai G, Adachi H, Katsuno M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Iida M, Nakatsuji H, Qiang Q, Ding Y, Watanabe H, Yamamoto M, Ohtsuka K, Sobue G
    • Journal Title

      Hum Mol Genet

      Volume: (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Journal Article] Transcriptional activation of TFEB/ZKSCAN3 target genes underlies enhanced autophagy in spinobulbar muscular atrophy2014

    • Author(s)
      Chua JP, Reddy SL, Merry DE, Adachi H, Katsuno M, Sobue G, Robins DM, Lieberman AP
    • Journal Title

      Hum Mol Genet

      Volume: (Epub ahead of print) Issue: 5 Pages: 1376-1386

    • DOI

      10.1093/hmg/ddt527

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-24659428
  • [Journal Article] Clinicopathological features of neuropathy associated with IgG4-related disease2014

    • Author(s)
      Ohyama K, Koike H, Takahashi M, Kawagashira Y, Iijima M, Sobue G.
    • Journal Title

      Rinsho Shinkeigaku

      Volume: 54 Issue: 12 Pages: 1047-1049

    • DOI

      10.5692/clinicalneurol.54.1047

    • NAID

      130004921198

    • ISSN
      0009-918X, 1882-0654
    • Language
      Japanese
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Journal Article] An evolutionarily conserved protein CHORD regulates scaling of dendritic arbors with body size.2014

    • Author(s)
      Kohei Shimono, Kazuto Fujishima, Takafumi Nomura, Masayoshi Ohashi, Tadao Usui, Mineko Kengaku, Atsushi Toyoda, and Tadashi Uemura.
    • Journal Title

      Scientific Reports

      Volume: 4 Issue: 1 Pages: 4415-4415

    • DOI

      10.1038/srep04415

    • NAID

      120005399036

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PLANNED-22115006, KAKENHI-PROJECT-221S0003, KAKENHI-PUBLICLY-24111525, KAKENHI-PROJECT-24500410, KAKENHI-PROJECT-221S0002
  • [Journal Article] Mononeuritis multiplex with tumefactive cellular infiltration in a patient with reactive lymphoid hyperplasia with increased immunoglobulin G4-positive cells2014

    • Author(s)
      Yokoi S, Kawagashira Y, Ohyama K, Iijima M, Koike H, Watanabe H, Tatematsu A, Nakamura S, Sobue G
    • Journal Title

      Hum Pathol

      Volume: 45 Issue: 2 Pages: 427-30

    • DOI

      10.1016/j.humpath.2013.07.047

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-25461278
  • [Journal Article] Potential of a new MRI for visualizing cerebellar involvement in progressive supranuclear palsy.2014

    • Author(s)
      Hara K, Watanabe H, Ito M, Tsuboi T, Watanabe H, Nakamura R, Senda J, Atsuta N, Adachi H, Aiba I, Naganawa S, Sobue G.
    • Journal Title

      Parkinsonism Relat Disord.

      Volume: 20(2) Issue: 2 Pages: 157-161

    • DOI

      10.1016/j.parkreldis.2013.10.007

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461312, KAKENHI-PROJECT-25461313
  • [Journal Article] Voice Features of Parkinson’s Disease Patients With Subthalamic Nucleus Deep Brain Stimulation2014

    • Author(s)
      Y Tanaka, T Tsuboi, H Watanabe, Y Kajita, Y Fujimoto, R Oodake, N Yoneyama, M Masuda, K Hara, J Senda, M Ito, N Atsuta, S Horiguchi, M Yamamoto, T Wakabayashi, G Sobue.
    • Journal Title

      Movement Disorders

      Volume: in press

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461312
  • [Journal Article] Potential therapeutic targets in polyglutamine-mediated diseases.2014

    • Author(s)
      Katsuno M, Watanabe H, Yamamoto M, Sobue G
    • Journal Title

      Expert Rev Neurother.

      Volume: 14 Issue: 10 Pages: 1215-1228

    • DOI

      10.1586/14737175.2014.956727

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-26670440
  • [Journal Article] Paeoniflorin eliminates a mutant AR via NF-YA-dependent proteolysis in spinal and bulbar muscular atrophy.2014

    • Author(s)
      Tohnai G, Adachi H, Katsuno M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Iida M, Nakatsuji H, Qiang Q, Ding Y, Watanabe H, Yamamoto M, Ohtsuka K, Sobue G.
    • Journal Title

      Hum Mol Genet.

      Volume: 23 Issue: 13 Pages: 3552-3565

    • DOI

      10.1093/hmg/ddu066

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PLANNED-22110005, KAKENHI-ORGANIZER-26117001, KAKENHI-PROJECT-26293206, KAKENHI-PROJECT-26670440, KAKENHI-PROJECT-26860665, KAKENHI-PLANNED-26117002
  • [Journal Article] Tongue pressure as a novel biomarker of spinal and bulbar muscular atrophy (SBMA)2014

    • Author(s)
      Mano T, Katsuno M, Banno H, Suzuki K, Suga N, Hashizume A, Araki A, Watanabe H, Tanaka S, Yamamoto M, Sobue G
    • Journal Title

      Neurology

      Volume: 82 Issue: 3 Pages: 255-262

    • DOI

      10.1212/wnl.0000000000000041

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-24659428
  • [Journal Article] Paeoniflorin eliminates a mutant AR via NF-YA-dependent proteolysis in spinal and bulbar muscular atrophy2014

    • Author(s)
      Tohnai G, Adachi H, Katsuno M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Iida M, Nakatsuji H, Qiang Q, Ding Y, Watanabe H, Yamamoto M, Ohtsuka K, Sobue G
    • Journal Title

      Hum Mol Genet

      Volume: (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Speed control for neuronal migration in the postnatal brain by Gmip-mediated local inactivation of RhoA2014

    • Author(s)
      Haruko Ota, Takao Hikita, Masato Sawada, Tomoki Nishioka, Mami Matsumoto, Masayuki Komura, Akihisa Ohno, Yukiyo Kamiya, Takuya Miyamoto, Naoya Asai, Atsushi Enomoto, Masahide Takahashi, Kozo Kaibuchi, Kazuya Sobue, Kazunobu Sawamoto
    • Journal Title

      Nature Communications

      Volume: 5 Issue: 1 Pages: 4532-4532

    • DOI

      10.1038/ncomms5532

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-221S0003, KAKENHI-PROJECT-24390095, KAKENHI-PROJECT-24689021, KAKENHI-PLANNED-22122004, KAKENHI-PROJECT-26221304
  • [Journal Article] 【脊椎脊髄の科学-基礎と臨床の進歩Review 2014】 (第9章)保存療法 運動ニューロン疾患に対する治療法の開発2014

    • Author(s)
      熱田 直樹、祖父江 元
    • Journal Title

      脊椎脊髄ジャーナル

      Volume: 27 Pages: 445-50

    • Data Source
      KAKENHI-PROJECT-25461277
  • [Journal Article] Early pathologic changes in hereditary diffuse leukoencephalopathy with spheroids.2014

    • Author(s)
      Riku Y, Ando T, Goto Y, Mano K, Iwasaki Y, Sobue G, Yoshida M
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 73 Issue: 12 Pages: 1183-90

    • DOI

      10.1097/nen.0000000000000139

    • Peer Reviewed
    • Data Source
      KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002
  • [Journal Article] Schwann cell involvement in the peripheral neuropathy of spinocerebellar ataxia type 3.2014

    • Author(s)
      Suga N, Katsuno M, Koike H, Banno H, Suzuki K, Hashizume A, Mano T, Iijima M, Kawagashira Y, Hirayama M, Nakamura T, Watanabe H, Tanaka F, Sobue G
    • Journal Title

      Neuropathol Appl Neurobiol.

      Volume: 40 Issue: 5 Pages: 628-639

    • DOI

      10.1111/nan.12055

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-24500458, KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-25461278, KAKENHI-PROJECT-26293206, KAKENHI-PROJECT-26670445
  • [Journal Article] Anti-androgen flutamide protects male mice from androgen-dependent toxicity in three models of spinal bulbar muscular atrophy2014

    • Author(s)
      Renier KJ, Troxell-Smith SM, Johansen JA, Katsuno M, Adachi H, Sobue G, Chua JP, Sun Kim H, Lieberman AP, Breedlove SM, Jordan CL
    • Journal Title

      Endocrinology

      Volume: (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] 【神経疾患治療の進歩2013年】 運動ニューロン疾患の治療の進歩2014

    • Author(s)
      熱田 直樹、祖父江 元
    • Journal Title

      神経治療学

      Volume: 31 Pages: 405-8

    • Data Source
      KAKENHI-PROJECT-25461277
  • [Journal Article] Cutaneous arteritis associated with peripheral neuropathy: two case reports2014

    • Author(s)
      Riku Y, Ikenaka K, Koike H, Niimi Y, Senda J, Hashimoto R, Kawagashira Y, Tomita M, Iijima M, Sobue G
    • Journal Title

      J Dermatol

      Volume: 41 Issue: 3 Pages: 266-7

    • DOI

      10.1111/1346-8138.12416

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-25461278, KAKENHI-PROJECT-25461312
  • [Journal Article] Slowly progressive folate-deficiency myelopathy: Report of a case2014

    • Author(s)
      Okada A, Koike H, Nakamura T, Watanabe H, Sobue G
    • Journal Title

      J Neurol Sci

      Volume: 336 Issue: 1-2 Pages: 273-5

    • DOI

      10.1016/j.jns.2013.10.032

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Endolymphatic space size in patients with vestibular migraine and Meniere's disease.2014

    • Author(s)
      Nakada T, Yoshida T, Suga K, Kato M, Otake H, Kato K, Teranishi M, Sone M, Sugiura S, Kuno K, Pyykko I, Naganawa S, Watanabe H, Sobue G, Nakashima T.
    • Journal Title

      J Neurol.

      Volume: 261(11) Issue: 11 Pages: 2079-2084

    • DOI

      10.1007/s00415-014-7458-9

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24659562, KAKENHI-PROJECT-25293263, KAKENHI-PROJECT-25861548, KAKENHI-ORGANIZER-26117001
  • [Journal Article] 脳腱黄色腫症と認知症2014

    • Author(s)
      桝田 道人、勝野 雅央、渡辺 宏久、千田 譲、祖父江 元
    • Journal Title

      神経内科

      Volume: 80 Pages: 107-114

    • Data Source
      KAKENHI-PROJECT-25461312
  • [Journal Article] Differential motor neuron involvement in progressive muscular atrophy: a comparative study with amyotrophic lateral sclerosis2014

    • Author(s)
      Riku Y, Atsuta N, Yoshida M, Tatsumi S, Iwasaki Y, Mimuro M, Watanabe H, Ito M, Senda J, Nakamura R, Koike H, Sobue G
    • Journal Title

      BMJ Open

      Volume: 4 Issue: 5 Pages: e005213-e005213

    • DOI

      10.1136/bmjopen-2014-005213

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-25461277, KAKENHI-PROJECT-25461312, KAKENHI-ORGANIZER-26117001
  • [Journal Article] Lower motor neuron involvement in TAR DNA-binding protein of 43 kDa-related frontotemporal lobar degeneration and amyotrophic lateral sclerosis.2014

    • Author(s)
      Riku Y, Watanabe H, Yoshida M, Tatsumi S, Mimuro M, Iwasaki Y, Katsuno M, Iguchi Y, Masuda M, Senda J, Ishigaki S, Udagawa T, Sobue G
    • Journal Title

      JAMA Neurol.

      Volume: 71 Issue: 2 Pages: 172-179

    • DOI

      10.1001/jamaneurol.2013.5489

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-24659429, KAKENHI-PROJECT-25461312, KAKENHI-PROJECT-26293206
  • [Journal Article] Immunoglobulin G for the Treatment of Chronic Pain: Report of an Expert Workshop2014

    • Author(s)
      Tamburin S, Borg K, Caro XJ, Jann S, Clark AJ, Magrinelli F, Sobue G, Werhagen L, Zanette G, Koike H, Spath PJ, Vincent A, Goebel A
    • Journal Title

      Pain Med

      Volume: 15 Issue: 7 Pages: 1072-82

    • DOI

      10.1111/pme.12319

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Prevalence and Incidence of Amyotrophic Lateral Sclerosis in Japan2014

    • Author(s)
      Doi Y, Atsuta N, Sobue G, Morita M, Nakano I.
    • Journal Title

      Journal of Epidemiology

      Volume: 24 Issue: 6 Pages: 494-499

    • DOI

      10.2188/jea.JE20140059

    • NAID

      130004678109

    • ISSN
      0917-5040, 1349-9092
    • Language
      English
    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-25461277
  • [Journal Article] 病態解明・新規治療を目指した神経疾患の患者レジストリシステム(第1回) 筋萎縮性側索硬化症:JaCALS2014

    • Author(s)
      熱田 直樹, 中村 亮一, 渡辺 はづき, 祖父江 元
    • Journal Title

      BRAIN and NERVE: 神経研究の進歩

      Volume: 66 Pages: 1090-6

    • NAID

      40020203407

    • Data Source
      KAKENHI-PROJECT-25461277
  • [Journal Article] Muscle atrophy in chronic inflammatory demyelinating polyneuropathy: a computed tomography assessment2014

    • Author(s)
      Ohyama K, Koike H, Katsuno M, Takahashi M, Hashimoto R, Kawagashira Y, Iijima M, Adachi H, Watanabe H, Sobue G
    • Journal Title

      Eur J Neurol

      Volume: 21 Issue: 7 Pages: 1002-10

    • DOI

      10.1111/ene.12426

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-25461278, KAKENHI-PROJECT-26461292
  • [Journal Article] 進化するParkinson病の治療 症状とその対応 新たなステージへ 自律神経症状とその対応2014

    • Author(s)
      渡辺 宏久, 中村 友彦, 平山 正昭, 祖父江 元
    • Journal Title

      神経治療学

      Volume: 31 Pages: 175-179

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Journal Article] Distinct phenotypes of speech and voice disorders in Parkinson's disease after subthalamic nucleus deep brain stimulation.2014

    • Author(s)
      Tsuboi T, Watanabe H, Tanaka Y, Ohdake R, Yoneyama N, Hara K, Nakamura R, Watanabe H, Senda J, Atsuta N, Ito M, Hirayama M, Yamamoto M, Fujimoto Y, Kajita Y, Wakabayashi T, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: Epub Issue: 8 Pages: 856-64

    • DOI

      10.1136/jnnp-2014-308043

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-24591293, KAKENHI-PROJECT-25461312, KAKENHI-PROJECT-25461313, KAKENHI-PROJECT-15K09350, KAKENHI-PLANNED-26117002, KAKENHI-ORGANIZER-26117001
  • [Journal Article] 【痙性対麻痺】 痙性対麻痺で初発する筋萎縮性側索硬化症(ALS)2014

    • Author(s)
      熱田 直樹、祖父江 元
    • Journal Title

      脊椎脊髄ジャーナル

      Volume: 27 Pages: 761-6

    • Data Source
      KAKENHI-PROJECT-25461277
  • [Journal Article] Hyposmia and cardiovascular dysautonomia correlatively appear in early-stage Parkinson's disease2014

    • Author(s)
      Mizutani, Y. Nakamura, T. Okada, A. Suzuki, J. Watanabe, H. Hirayama, M. Sobue, G.
    • Journal Title

      Parkinsonism & related disorders

      Volume: 20 Issue: 5 Pages: 520-4

    • DOI

      10.1016/j.parkreldis.2014.02.010

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-24500458, KAKENHI-PROJECT-24591293, KAKENHI-ORGANIZER-26117001, KAKENHI-PLANNED-26117002
  • [Journal Article] Evaluation of SLC20A2 mutations that cause idiopathic basal ganglia calcification in Japan.2014

    • Author(s)
      Yamada, M., M. Tanaka, M. Takagi, S. Kobayashi, Y. Taguchi, S. Takashima, K. Tanaka, T. Touge, H. Hatsuta, S. Murayama, Y. Hayashi, M. Kaneko, H. Ishiura, J. Mitsui, N. Atsuta, G. Sobue, N. Shimozawa, T. Inuzuka, S. Tsuji and I. Hozumi
    • Journal Title

      Neurology

      Volume: 82 Issue: 8 Pages: 705-712

    • DOI

      10.1212/wnl.0000000000000143

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-221S0003, KAKENHI-PROJECT-24700371, KAKENHI-PROJECT-25461277, KAKENHI-PROJECT-25860700, KAKENHI-PROJECT-25860705
  • [Journal Article] Identification and characterization of GABAA receptor autoantibodies in autoimmune encephalitis2014

    • Author(s)
      Ohkawa T, Satake S, Yokoi N, Miyazaki Y, Ohshita T, Sobue G, Takashima H, Watanabe O, *Fukata Y, *Fukata M (*corresponding author).
    • Journal Title

      J Neurosci

      Volume: 34 Issue: 24 Pages: 8151-8163

    • DOI

      10.1523/jneurosci.4415-13.2014

    • Peer Reviewed / Acknowledgement Compliant / Open Access
    • Data Source
      KAKENHI-PUBLICLY-25110733, KAKENHI-PROJECT-25461286, KAKENHI-PROJECT-25890021, KAKENHI-ORGANIZER-26117001, KAKENHI-PROJECT-26291045, KAKENHI-PROJECT-26430079
  • [Journal Article] Translational research on disease-modifying therapies for neurodegenerative diseases2013

    • Author(s)
      Katsuno M, Watanabe H, Tanaka F, Sobue G
    • Journal Title

      Neurology and Clinical Neuroscience

      Volume: 1 Issue: 1 Pages: 3-10

    • DOI

      10.1002/ncn3.7

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-24659428
  • [Journal Article] ALSのパーソナルゲノム解析2013

    • Author(s)
      田中章景,曽根 淳,熱田直樹,中村亮一,土井 宏,児矢野 繁,祖父江 元
    • Journal Title

      Brain and Nerve

      Volume: 65 Pages: 257-265

    • Data Source
      KAKENHI-PLANNED-22129005
  • [Journal Article] Wide range of clinicopathological features in immune-mediated autonomic neuropathies.2013

    • Author(s)
      Koike H, Sobue G.
    • Journal Title

      Clin Exp Neuroimmunol

      Volume: 4 Pages: 46-59

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] mRNA搭載ウイルスベクターによる球脊髄性筋萎縮症の治療展望神経内科2013

    • Author(s)
      宮崎雄, 祖父江元
    • Journal Title

      科学評論社

      Volume: 79 Pages: 390-399

    • Data Source
      KAKENHI-PROJECT-25670418
  • [Journal Article] 血圧と自律神経障害 神経疾患の起立性低血圧2013

    • Author(s)
      中村 友彦, 平山 正昭, 祖父江 元
    • Journal Title

      自律神経

      Volume: 50 Pages: 179-182

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Journal Article] mRNA搭載ウイルスベクターによる球脊髄性筋萎縮症の治療展望2013

    • Author(s)
      宮崎雄, 祖父江元.
    • Journal Title

      神経内科

      Volume: 79 Pages: 390-399

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25670418
  • [Journal Article] RNP2 of RNA recognition motif 1 plays a central role in the aberrant modification of TDP-43.2013

    • Author(s)
      Takagi S, Iguchi Y, Katsuno M, Ishigaki S, Ikenaka K, Fujioka Y, Honda D, Niwa J, Tanaka F, Watanabe H, Adachi H, Sobue G.
    • Journal Title

      PLoS One.

      Volume: 28 Issue: 6 Pages: e66966-e66966

    • DOI

      10.1371/journal.pone.0066966

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-25293207
  • [Journal Article] A functional deficiency of TERA/VCP/p97 contributes to impaired DNA repair in multiple polyglutamine diseases.2013

    • Author(s)
      Fujita K, Nakamura Y, Oka T, Ito H, Tamura T, Tagawa K, Sasabe T, Katsuta A, Motoki K, Shiwaku H, Sone M, Yoshida C, Katsuno M, Eishi Y, Murata M, Taylor JP, Wanker EE, Kono K, Tashiro S, Sobue G, La Spada AR, Okazawa H.
    • Journal Title

      Nat Commun.

      Volume: 4 Issue: 1 Pages: 1816-1816

    • DOI

      10.1038/ncomms2828

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-ORGANIZER-22110001, KAKENHI-PLANNED-22110002, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23500401, KAKENHI-PROJECT-24500378, KAKENHI-PROJECT-24700374, KAKENHI-PROJECT-25640066
  • [Journal Article] Neck weakness is a potent prognostic factor in sporadic amyotrophic lateral sclerosis patients.2013

    • Author(s)
      Nakamura R, Atsuta N, Watanabe H, Hirakawa A, Watanabe H, Ito M, Senda J, Katsuno M, Tanaka F, Izumi Y, Morita M, Ogaki K, Taniguchi A, Aiba I, Mizoguchi K, Okamoto K, Hasegawa K, Aoki M, Kawata A, Abe K, Oda M, Konagaya M, Imai T, Nakagawa M, Tsuji S, Kaji R, Nakano I, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 84 Issue: 12 Pages: 1365-1371

    • DOI

      10.1136/jnnp-2013-306020

    • Peer Reviewed / Acknowledgement Compliant
    • Data Source
      KAKENHI-PLANNED-22129005, KAKENHI-PROJECT-23591231, KAKENHI-PROJECT-24406030, KAKENHI-PROJECT-25461277, KAKENHI-PROJECT-25461312
  • [Journal Article] Therapeutic strategy for CIDP (chronic inflammatory demyelinating polyneuropathy2013

    • Author(s)
      Iijima M, Koike H, Sobue G
    • Journal Title

      Nihon Rinsho

      Volume: 71 Pages: 855-860

    • NAID

      40019678675

    • Data Source
      KAKENHI-PROJECT-25461278
  • [Journal Article] 脳梗塞branch atheromatous disease(BAD)病型における回復期リハビリテーションでの治療成績2013

    • Author(s)
      千田 譲、伊東 慶一、大山 健、米山 典孝、原 一洋、中村 亮一、野田 智子、橋詰 淳、熱田 直樹、伊藤 瑞規、渡辺 宏久、安井 敬三、小竹 伴照、木田 義久、岸本 秀雄、祖父江 元
    • Journal Title

      脳卒中

      Volume: 35 Pages: 441-447

    • NAID

      130004873592

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461312
  • [Journal Article] Heat shock factor-1 influences pathological lesion distribution of polyglutamine-induced neurodegeneration2013

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Tohnai G, Nakatsuji H, Ishigaki S, Fujioka Y, Watanabe H, Tanaka F, Nakai A, Sobue G
    • Journal Title

      Nat Commun

      Volume: 4 Issue: 1 Pages: 1405-1405

    • DOI

      10.1038/ncomms2417

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-24659428, KAKENHI-PLANNED-22110005
  • [Journal Article] dnc-1/dynactin 1 knockdown disrupts transport of autophagosomes and induces motor neuron degeneration2013

    • Author(s)
      Ikenaka K, Kawai K, Katsuno M, Huang Z, Jiang YM, Iguchi Y, Kobayashi K, Kimata T, Waza M, Tanaka F, Mori I, Sobue G
    • Journal Title

      PLoS One

      Volume: 8

    • NAID

      120007001030

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Distinct acoustic features in spinal and bulbar muscular atrophy patients with laryngospasm.2013

    • Author(s)
      Tanaka S, Banno H, Katsuno M, Suzuki K, Suga N, Hashizume A, Mano T, Araki A, Watanabe H, Adachi H, Tatsumi H, Yamamoto M, Sobue G.
    • Journal Title

      J Neurol Sci.

      Volume: 337 Issue: 1-2 Pages: 193-200

    • DOI

      10.1016/j.jns.2013.12.010

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005
  • [Journal Article] Autoimmune autonomic ganglionopathy と acute autonomic and sensory neuropathy2013

    • Author(s)
      小池春樹,祖父江元
    • Journal Title

      臨床神経学

      Volume: 53 Pages: 1326-1329

    • NAID

      130004505433

    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Autonomic manifestations in acute sensory ataxic neuropathy: a case report.2013

    • Author(s)
      Ohyama K, Koike H, Masuda M, Sone J, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Nakamura T, Watanabe H, Sobue G.
    • Journal Title

      Auton Neurosci

      Volume: 179 Issue: 1-2 Pages: 155-158

    • DOI

      10.1016/j.autneu.2013.03.009

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461276, KAKENHI-PROJECT-25461278
  • [Journal Article] ERBB4 Mutations that Disrupt the Neuregulin-ErbB4 Pathway Cause Amyotrophic Lateral Sclerosis Type 19.2013

    • Author(s)
      Takahashi Y, Fukuda Y, Yoshimura J, Toyoda A, (33名省略), Morishita S, Goto J and Tsuji S.
    • Journal Title

      Am J Hum Genet

      Volume: 93 Issue: 5 Pages: 900-905

    • DOI

      10.1016/j.ajhg.2013.09.008

    • Peer Reviewed
    • Data Source
      KAKENHI-ORGANIZER-22129001, KAKENHI-PLANNED-22129002, KAKENHI-PLANNED-22129003, KAKENHI-PLANNED-22129008, KAKENHI-PUBLICLY-25110714, KAKENHI-PROJECT-25253065, KAKENHI-PROJECT-25461277, KAKENHI-PROJECT-25860700, KAKENHI-PROJECT-221S0002
  • [Journal Article] dnc-1/dynactin 1 knockdown disrupts transport of autophagosomes and induces motor neuron degeneration2013

    • Author(s)
      Ikenaka K
    • Journal Title

      PLoS One

      Volume: 8 Issue: 2 Pages: e54511-e54511

    • DOI

      10.1371/journal.pone.0054511

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175, KAKENHI-PROJECT-24247001, KAKENHI-PROJECT-25293207, KAKENHI-PLANNED-22110005, KAKENHI-PLANNED-22123010
  • [Journal Article] p62/SQSTM1 differentially removes the toxic mutant androgen receptor via autophagy and inclusion formation in a spinal and bulbar muscular atrophy mouse model2013

    • Author(s)
      Doi H, Adachi H, Katsuno M, Minamiyama M, Matsumoto S, Kondo N, Miyazaki Y, IidaM,Tohnai G, Qiang Q, Tanaka F, Yanagawa T, WarabiE,Ishii T, Sobue G
    • Journal Title

      J Neurosci

      Volume: 33 Issue: 18 Pages: 7710-7727

    • DOI

      10.1523/jneurosci.3021-12.2013

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23390231, KAKENHI-PROJECT-24659428, KAKENHI-PROJECT-25220103
  • [Journal Article] 各種疾患 末梢神経障害 抗MAG抗体陽性IgM-MGUSニューロパチーのリツキシマブによる新規治療の可能性2013

    • Author(s)
      川頭 祐一(名古屋大学 大学院・医学系研究科神経内科), 飯島 正博, 小池 春樹, 祖父江元
    • Journal Title

      Annual Review神経

      Volume: 2013巻 Pages: 223-229

    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Impaired pain processing in Parkinson's disease and its relative association with the sense of smell2013

    • Author(s)
      Hara, T. Hirayama, M. Mizutani, Y. Hama, T. Hori, N. Nakamura, T. Kato, S. Watanabe, H. Sobue, G.
    • Journal Title

      Parkinsonism Relat Disord

      Volume: 19 Issue: 1 Pages: 43-6

    • DOI

      10.1016/j.parkreldis.2012.06.020

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24500458, KAKENHI-PROJECT-24591293
  • [Journal Article] Clinicopathological features of neuropathy associated with lymphoma2013

    • Author(s)
      Tomita M, Koike H, Kawagashira Y, Iijima M, Adachi H, Taguchi J, Abe T, Sako K, Tsuji Y, Nakagawa M, Kanda F, Takeda F, Sugawara M, Toyoshima I, Asano N, Sobue G
    • Journal Title

      Brain

      Volume: 136 Issue: 8 Pages: 2563-2578

    • DOI

      10.1093/brain/awt193

    • NAID

      10027268001

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Journal Article] Spliceosome integrity is defective in the motor neuron diseases ALS and SMA2013

    • Author(s)
      Tsuiji H, Iguchi Y, Furuya A, Kataoka A, Hatsuta H, Atsuta N, Tanaka F, Hashizume Y, Akatsu H, Murayama S, Sobue G, Yamanaka K
    • Journal Title

      EMBO Mol Med

      Volume: 5 Issue: 2 Pages: 221-234

    • DOI

      10.1002/emmm.201202303

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PLANNED-22129005, KAKENHI-PROJECT-23700455, KAKENHI-PROJECT-24500431, KAKENHI-PROJECT-24700371, KAKENHI-PLANNED-23111006
  • [Journal Article] Cortical and subcortical brain atrophy in Parkinson's disease with visual hallucination2013

    • Author(s)
      Watanabe, H. Senda, J. Kato, S. Ito, M. Atsuta, N. Hara, K. Tsuboi, T. Katsuno, M. Nakamura, T. Hirayama, M. Adachi, H. Naganawa, S. Sobue, G.
    • Journal Title

      Mov Disord

      Volume: 28 Issue: 12 Pages: 1732-6

    • DOI

      10.1002/mds.25641

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24500458, KAKENHI-PROJECT-24591293, KAKENHI-PROJECT-25461312, KAKENHI-PROJECT-25461313
  • [Journal Article] Loss of TDP-43 causes age-dependent progressive motor neuron degeneration2013

    • Author(s)
      Iguchi Y, Katsuno M, Niwa JI, Takagi S, Ishigaki S, Ikenaka K, Kawai K, Watanabe H, Yamanaka K, Takahashi R, Misawa H, Sasaki S, Tanaka F, Sobue G
    • Journal Title

      Brain

      Volume: epub

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Journal Article] Genistein, a natural product derived from soybeans, ameliorates polyglutamine-mediated motor neuron disease2013

    • Author(s)
      Qiang Q, Adachi H, Huang Z, Jiang YM, Katsuno M, Minamiyama M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Iida M, Tohnai G, Sobue G
    • Journal Title

      J Neurochem

      Volume: 126 Issue: 1 Pages: 122-130

    • DOI

      10.1111/jnc.12172

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23390231, KAKENHI-PROJECT-24659428
  • [Journal Article] 【足の特異な症候】 Parkinson病における下肢不随意運動2013

    • Author(s)
      渡辺 宏久, 伊藤 瑞規, 坪井 崇, 中村 友彦, 平山 正昭, 祖父江 元
    • Journal Title

      脊椎脊髄ジャーナル

      Volume: 26 Pages: 747-751

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Journal Article] 【脳卒中超早期リハビリテーション戦略】 脳梗塞リハビリテーションにおける画像診断と障害像の分析/予後予測の進化2013

    • Author(s)
      千田 譲、熱田 直樹、伊藤 瑞規、伊東 慶一、小竹 伴照、木田 義久、岸本 秀雄、渡辺 宏久、祖父江 元
    • Journal Title

      MEDICAL REHABILITATION

      Volume: 161 Pages: 66-73

    • Data Source
      KAKENHI-PROJECT-25461312
  • [Journal Article] Loss of TDP-43 causes age-dependent progressive motor neuron degeneration2013

    • Author(s)
      Iguchi Y
    • Journal Title

      Brain

      Volume: 136 Issue: 5 Pages: 1371-1382

    • DOI

      10.1093/brain/awt029

    • Peer Reviewed / Open Access
    • Data Source
      KAKENHI-PROJECT-22390175, KAKENHI-PROJECT-22590965, KAKENHI-ORGANIZER-23111001, KAKENHI-PROJECT-23390232, KAKENHI-PROJECT-23659452, KAKENHI-PROJECT-25293020, KAKENHI-PLANNED-22110005
  • [Journal Article] Androgen receptor inclusions acquire GRP78/BiP to ameliorate androgen-induced protein misfolding stress in embryonic stem cells.2013

    • Author(s)
      Yang YC, Fu HC, Hsiao BL, Sobue G, Adachi H, Huang FJ, Hsuuw YD, Wei KT, Chang C, Huang KE, Kang HY.
    • Journal Title

      Cell Death Dis.

      Volume: 4 Issue: 4 Pages: e607-e607

    • DOI

      10.1038/cddis.2013.122

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Differential recovery in cardiac and vasomotor sympathetic functional markers in a patient with acute autonomic sensory and motor neuropathy.2013

    • Author(s)
      Ohyama K, Yasui K, Hasegawa Y, Morozumi S, Koike H, Sobue G.
    • Journal Title

      Intern Med

      Volume: 52 Pages: 497-502

    • NAID

      130003365895

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Amyotrophic lateral sclerosis: an update on recent genetic insights.2013

    • Author(s)
      Iguchi Y, Katsuno M, Ikenaka K, Ishigaki S, Sobue G.
    • Journal Title

      J Neurol.

      Volume: 260 Issue: 11 Pages: 2917-2927

    • DOI

      10.1007/s00415-013-7112-y

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Journal Article] Clinical and radiological impact of liver transplantation for brain in cirrhosis patients without hepatic encephalopathy.2013

    • Author(s)
      Ishihara T, Ito M, Niimi Y, Tsujimoto M, Senda J, Kawai Y, Watanabe H, Ishigami M, Ito T, Kamei H, Onishi Y, Nakamura T, Goto H, Naganawa S, Kiuchi T, Sobue G.
    • Journal Title

      Clin Neurol Neurosurg

      Volume: 115 Issue: 11 Pages: 2341-2347

    • DOI

      10.1016/j.clineuro.2013.08.015

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461312, KAKENHI-PROJECT-25461313
  • [Journal Article] The spectrum of immune-mediated autonomic neuropathies: insights from the clinicopathological features.2013

    • Author(s)
      Koike H, Watanabe H, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 84 Issue: 1 Pages: 98-106

    • DOI

      10.1136/jnnp-2012-302833

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Journal Article] Diagnostic accuracy of diffusion tensor imaging in amyotrophic lateral sclerosis: a systematic review and individual patient data meta-analysis.2013

    • Author(s)
      Foerster BR, Dwamena BA, Petrou M, Carlos RC, Callaghan BC, Churchill CL, Mohamed MA, Bartels C, Benatar M, Bonzano L, Ciccarelli O, Cosottini M, Ellis CM, Ehrenreich H, Filippini N, Ito M, Kalra S, Melhem ER, Pyra T, Roccatagliata L, Senda J, Sobue G, Turner MR, Feldman EL, Pomper MG.
    • Journal Title

      MEDICAL REHABILITATION

      Volume: 20 Issue: 9 Pages: 1099-1106

    • DOI

      10.1016/j.acra.2013.03.017

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-25461312
  • [Journal Article] Impact of aging on the progression of neuropathy after liver transplantation in transthyretin Val30Met amyloidosis.2012

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Nakamura T, Watanabe H, Kamei H, Kiuchi T, Sobue G
    • Journal Title

      Muscle Nerve

      Volume: 46 Pages: 964-70

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] MRI mean diffusivity detects widespread brain degeneration in multiple sclerosis2012

    • Author(s)
      Senda J, Watanabe H, Tsuboi T, Hara K, Watanabe H, Nakamura R, Ito M, Atsuta N, Tanaka F, Naganawa S, Sobue G
    • Journal Title

      J Neurol Sci

      Volume: 319(1-2) Pages: 105-10

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590955
  • [Journal Article] MRI mean diffusivity detects widespread brain degeneration in multiple sclerosis.2012

    • Author(s)
      Senda Joe
    • Journal Title

      Journal of the Neurological Sciences

      Volume: 319 Issue: 1-2 Pages: 105-110

    • DOI

      10.1016/j.jns.2012.04.019

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590955, KAKENHI-PROJECT-24591293
  • [Journal Article] Widespread cortical and subcortical brain atrophy in Parkinson's disease with excessive daytime sleepiness2012

    • Author(s)
      Kato S, et al
    • Journal Title

      Journal of Neurology

      Volume: 259 Issue: 2 Pages: 318-326

    • DOI

      10.1007/s00415-011-6187-6

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591111, KAKENHI-PROJECT-22590955, KAKENHI-PROJECT-24500458, KAKENHI-PROJECT-24591293
  • [Journal Article] Discrimination of spinal and bulbar muscular atrophy from amyotrophic lateral sclerosis using sensory nerve action potentials.2012

    • Author(s)
      Hama T, Hirayama M, Hara T, Nakamura T, Atsuta N, Banno H, Suzuki K, Katsuno M, Tanaka F, Sobue G.
    • Journal Title

      Muscle Nerve

      Volume: 45 Issue: 2 Pages: 169-174

    • DOI

      10.1002/mus.22291

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-21600003, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986, KAKENHI-PROJECT-24500458
  • [Journal Article] Natural history of trans thyretin Val 30 Met familial amyloid polyneuropathy : analysis of late-onset cases from non-endemic areas2012

    • Author(s)
      Koike H, Tanaka F, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Fujitake J, Kawanami T, Kato T, Yamamoto M, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 83 Pages: 152-158

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] c-Abl inhibition delays motor neuron degeneration in the G93A mouse2012

    • Author(s)
      Katsumata R, Ishigaki S, Katsuno M, Kawai K, Sone J, Huang Z, Adachi H,Tanaka F, Urano F, Sobue G
    • Journal Title

      an animal model of amyotrophic lateral sclerosis

      Volume: 7

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Viral delivery of miR-196a ameliorates the SBMA phenotype via the silencing of CELF22012

    • Author(s)
      Miyazaki Y, Adachi H, Katsuno M, Minamiyama M, Jiang YM, Huang Z, Doi H, Matsumoto S, Kondo N, Iida M, Tohnai G, Tanaka F, Muramatsu S, Sobue G
    • Journal Title

      Nat Med

      Volume: 18 Issue: 7 Pages: 1136-1141

    • DOI

      10.1038/nm.2791

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390231, KAKENHI-PROJECT-23590473, KAKENHI-PUBLICLY-23110515
  • [Journal Article] Naratriptan mitigates CGRP1-associated motor neuron degeneration caused by expanded polyglutamine2012

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Iida M, Ishigaki S, Fujioka Y, Matsumoto S, Miyazaki Y, Tanaka F, Kurihara H, Sobue G
    • Journal Title

      Nat Med

      Volume: 18 Issue: 10 Pages: 1531-1538

    • DOI

      10.1038/nm.2932

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PUBLICLY-23013007, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23659107, KAKENHI-PROJECT-24249047
  • [Journal Article] Differential change of clinical outcome measures in spinal and bulbar muscular atrophy: comparison of natural history with placebo-treated group.2012

    • Author(s)
      Hashizume A, Katsuno M, Banno H, Suzuki K, Suga N, Tanaka F, Sobue G.
    • Journal Title

      J Neurol.

      Volume: 259 Issue: 4 Pages: 712-719

    • DOI

      10.1007/s00415-011-6251-2

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986
  • [Journal Article] Late-onset familial amyloid polyneuropathy in Japan2012

    • Author(s)
      Koike H, Sobue G
    • Journal Title

      Amyloid

      Volume: (印刷中)(未定)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] A novel MPZ mutation in Charcot-Marie-Tooth disease type 1B with focally folded myelin and multiple entrapment neuropathies2012

    • Author(s)
      Iida M, Koike H, Ando T, Sugiura M, Yamamoto M, Tanaka F, Sobue G.
    • Journal Title

      Neuromuscul Disord

      Volume: 22 Pages: 166-169

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Defective axonal transport in motor neuron diseases.2012

    • Author(s)
      Ikenaka K, Katsuno M, Kawai K, Ishigaki S, Tanaka F, Sobue G.
    • Journal Title

      Int J Mol Sci.

      Volume: 13 Issue: 1 Pages: 1225-1238

    • DOI

      10.3390/ijms13011225

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230
  • [Journal Article] IGF-1 administration ameliorates disease manifestations in a mouse model of spinal and bulbar muscular atrophy2012

    • Author(s)
      Rinaldi C, Bott L, Chen K, Harmison G, Katsuno M, Sobue G, Pennuto M, Fischbeck KH
    • Journal Title

      Mol Med

      Volume: 18 Issue: 9 Pages: 1261-1268

    • DOI

      10.2119/molmed.2012.00271

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390230
  • [Journal Article] Current status of treatment of spinal and bulbar muscular atrophy2012

    • Author(s)
      Tanaka F, Katsuno M, Banno H, Suzuki K, Adachi H, Sobue G
    • Journal Title

      Neural Plast

      Volume: 2012 Pages: 369284-369284

    • DOI

      10.1155/2012/369284

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23790986, KAKENHI-PROJECT-24659428
  • [Journal Article] Molecular pathophysiology and disease-Modifying therapies for spinal and bulbar muscular atrophy2012

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Adachi H, Tanaka F, Sobue G
    • Journal Title

      Arch Neurol

      Volume: 69 Issue: 4 Pages: 436-440

    • DOI

      10.1001/archneurol.2011.2308

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986, KAKENHI-PROJECT-24659428
  • [Journal Article] Differential, size-dependent sensory neuron involvement in the painful and ataxic forms of primary Sogren's syndrome-associated neuropathy.2012

    • Author(s)
      Kawagashira Y, Koike H, Fujioka Y, Hashimoto R, Tomita M, Morozumi S, Iijima M, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Sci.

      Volume: 319 Pages: 319-319

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Widespread cortical and subcortical brain atrophy in Parkinson's disease with excessive daytime sleepiness. Kato S2012

    • Author(s)
      Watanabe H, Senda J, Hirayama M, Ito M, Atsuta N, Kaga T, Katsuno M, Naganawa S, Sobue G
    • Journal Title

      J Neurol

      Volume: 259(2) Pages: 318-26

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590955
  • [Journal Article] Crow-Fukase症候群における髄鞘の形態変化の特徴2012

    • Author(s)
      橋本 里奈(名古屋大学 神経内科), 小池 春樹, 冨田 稔, 川頭 祐一, 飯島 正博, 祖父江元
    • Journal Title

      末梢神経(0917-6772)

      Volume: 23巻1号 Pages: 95-101

    • NAID

      10030408686

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Cross-sectional and longitudinal analysis of an oxidative stress biomarker for spinal and bulbar muscular atrophy.2012

    • Author(s)
      Mano, T., Katsuno, M., Banno, H., Suzuki, K., Suga, N., Hashizume, A., Tanaka, F., Sobue, G.
    • Journal Title

      Muscle Nerve

      Volume: 46 Issue: 5 Pages: 692-697

    • DOI

      10.1002/mus.23413

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986
  • [Journal Article] Perspectives on molecular targeted therapies and clinical trials for neurodegenerative diseases2012

    • Author(s)
      Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 83 Issue: 3 Pages: 329-335

    • DOI

      10.1136/jnnp-2011-301307

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-24659428
  • [Journal Article] The spectrum of clinicopathological features in pure autonomic neuropathy.2012

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Koyano S, Momoo T, Yuasa H, Mitake S, Higashihara M, Kaida K, Yamamoto D, Hisahara S, Shimohama S, Nakae Y, Johkura K, Vernino S, Sobue G
    • Journal Title

      J Neurol

      Volume: 259 Pages: 2067-75

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Oxidative stress induced by glutathione depletion reproduces pathological modifications of TDP-43 linked to TDP-43 proteinopathies.2012

    • Author(s)
      Iguchi Y,Katsuno M,Takagi S.Ishigaki S,Niwa JI,Hasegawa M,Tanaka F,Sobue G
    • Journal Title

      Neurobiol Dis

      Volume: 45 Issue: 3 Pages: 862-870

    • DOI

      10.1016/j.nbd.2011.12.002

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PROJECT-22390175, KAKENHI-PUBLICLY-23110526, KAKENHI-PROJECT-23240050, KAKENHI-PROJECT-23659452
  • [Journal Article] TSUNAMI: an antisense method to phenocopy splicing-associated diseases in animals.2012

    • Author(s)
      Sahashi K, Hua Y, Ling KK, Hung G, Rigo F, Horev G, Katsuno M, Sobue G, Ko CP, Bennett CF, Krainer AR.
    • Journal Title

      Genes Dev.

      Volume: 26 Issue: 16 Pages: 1874-1884

    • DOI

      10.1101/gad.197418.112

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Journal Article] Natural history of transthyretin Val30Met familial amyloid polyneuropathy : analysis of late-onset cases from non-endemic areas2012

    • Author(s)
      Koike H, Tanaka F, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Fujitake J, Kawanami T, Kato T, Yamamoto M, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 83 Pages: 152-158

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Neuropathology and omics in motor neuron diseases2012

    • Author(s)
      Tanaka F, Ikenaka K, Yamamoto M, Sobue G
    • Journal Title

      Neuropathology

      Volume: 32 Pages: 458-462

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Loss of TDP-43 causes age-dependent progressive motor neuron degeneration2012

    • Author(s)
      Iguchi Y, Katsuno M, Niwa JI, Takagi S, Ishigaki S, Ikenaka K, Kawai K, Watanabe H, Yamanaka K, Takahashi R, Misawa H, Sasaki S, Tanaka F, Sobue G
    • Journal Title

      Brain

      Volume: 136 Pages: 1371-1382

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Disruption of axonal transport in motor neuron diseases2012

    • Author(s)
      Ikenaka K, Katsuno M, Kawai K, Ishigaki S, Tanaka F, Sobue G
    • Journal Title

      Int J Mol Sci

      Volume: 13 Pages: 1225-1238

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] The significance of folate deficiency in alcoholic and nutritional neuropathies: analysis of a case.2012

    • Author(s)
      Koike H, Hama T, Kawagashira Y, Hashimoto R, Tomita M, Iijima M, Sobue G
    • Volume
      28
    • Pages
      821-4
    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Longitudinal changes of outcome measures in spinal and bulbar muscular atrophy.2012

    • Author(s)
      Hashizume, A., Katsuno, M., Banno, H., Suzuki, K., Suga, N., Mano, T., Atsuta, N., Oe, H., Watanabe, H., Tanaka, F., Sobue, G.
    • Journal Title

      Brain

      Volume: 35 Issue: 9 Pages: 2838-2848

    • DOI

      10.1093/brain/aws170

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy (SBMA).2012

    • Author(s)
      Banno, H., Katsuno, M., Suzuki, K., Tanaka, F., Sobue, G.
    • Journal Title

      Cell Tissue Res

      Volume: 349 Issue: 1 Pages: 313-320

    • DOI

      10.1007/s00441-012-1377-9

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23790986, KAKENHI-PROJECT-24659428
  • [Journal Article] Pathogenesis and therapy of spinal and bulbar muscular atrophy (SBMA)2012

    • Author(s)
      Katsuno M, Tanaka F, Adachi H, Banno H, Suzuki K, Watanabe H, Sobue G
    • Journal Title

      Prog Neurobiol

      Volume: 99 Issue: 3 Pages: 246-256

    • DOI

      10.1016/j.pneurobio.2012.05.007

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390230, KAKENHI-PROJECT-23790986, KAKENHI-PROJECT-24659428
  • [Journal Article] c-Abl inhibition delays motor neuron degeneration in the G93A mouse, an animal model of amyotrophic lateral sclerosis2012

    • Author(s)
      Katsumata R
    • Journal Title

      PLoS One

      Volume: 7 Issue: 9 Pages: e46185-e46185

    • DOI

      10.1371/journal.pone.0046185

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175, KAKENHI-PLANNED-22110005
  • [Journal Article] Natural history of transthyretin Val30Met familial amyloid polyneuropathy: analysis of late-onset cases from non-endemic areas2012

    • Author(s)
      Koike H, Tanaka F, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Fujitake J, Kawanami T, Kato T, Yamamoto M, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 83(2) Pages: 152-8

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Position-dependent FUS-RNA interactions regulate alternative splicing events and transcriptions.2012

    • Author(s)
      Ishigaki S, Masuda A, Fujioka Y, Iguchi Y, Katsuno M, Shibata A, Urano F, Sobue G, Ohno K
    • Journal Title

      Sci Rep

      Volume: 2 Issue: 1 Pages: 529-529

    • DOI

      10.1038/srep00529

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-23659452, KAKENHI-PROJECT-24390221, KAKENHI-PROJECT-24500469, KAKENHI-PROJECT-24659429, KAKENHI-PLANNED-22110005
  • [Journal Article] Cerebellar ataxia rehabilitation trial in degenerative cerebellar diseases、Cerebellar Ataxia Rehabilitation Trialists Collaboration2012

    • Author(s)
      Miyai I, Ito M, Hattori N, Mihara M, Hatakenaka M, Yagura H, Sobue G, Nishizawa M
    • Journal Title

      Neurorehabil Neural Repair

      Volume: 26(5) Pages: 515-22

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590955
  • [Journal Article] Oxidative stress induced by glutathione depletion reproduces pathological modifications of TDP-43linked to TDP-43 proteinopathies2012

    • Author(s)
      Iguchi Y, Katsuno M, Takagi S, Ishigaki S, Niwa J, Hasegawa M, Tanaka F, Sobue G.
    • Journal Title

      Neurobiol Dis

      Volume: 45 Pages: 862-870

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Disruption of axonal transport in motor neuron diseases2012

    • Author(s)
      Ikenaka K, Katsuno M, Kawai K, Ishigaki S, Tanaka F, Sobue G
    • Journal Title

      Int J Mol Sci

      Volume: 13 Pages: 1225-1238

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] The TRK-fused gene is mutated in hereditary motor and sensory neuropathy with proximal do minant involvement.2012

    • Author(s)
      Ishiura H, Sako W, Yoshida M, Kawarai T, Tanabe O, Goto J, Takahashi Y, Date H, Mitsui J, Ahsan B, Ichikawa Y, Iwata A, Yoshino H, Izumi Y, Fujita K, Maeda K, Goto S, Koizumi H, Morigaki R, Ikemura M, Yamauchi N, Murayama S, Nicholson GA, Ito H, Sobue G, Nakagawa M, Kaji R, Tsuji S.
    • Journal Title

      Am J Hum Genet.

      Volume: 91 Pages: 320-9

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-221S0003
  • [Journal Article] Skin biopsy is usefui for the antcmortem diagnosis of neuronal intranuclear inclusion disease.2011

    • Author(s)
      Sone J, Tanaka F, Koike H, Inukai A, Katsuno M, Yoshida M, Watanabe H, Sobue G.
    • Journal Title

      Neurology

      Volume: in press

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] The wide range of clinical manifestations in leprous neuropathy : two case reports2011

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Nagamatsu M, Sobue G
    • Journal Title

      Intern Med

      Volume: 50 Pages: 2223-6

    • NAID

      130001087908

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Does cardiovascular autonomic dysfunction contribute to fatigue in Parkinson's disease2011

    • Author(s)
      Nakamura T, Hirayama M, Hara T, Hama T, Watanabe H, Sobue G.
    • Journal Title

      Mov Disord

      Volume: 26 Pages: 1869-74

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Journal Article] Tremor is attenuated during walking in essential tremor with resting tremor but not parkinsonian tremor2011

    • Author(s)
      Uchida K, Hirayama M, Yamashita F, Hori N, Nakamura T, Sobue G
    • Journal Title

      J Clin Neurosci

      Volume: 18 Pages: 1224-8

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Journal Article] Suppression of Alzheimer's disease-related phenotypes by expression of heat shock protein 70 in mice.2011

    • Author(s)
      Hoshino T, Murao N, Namba T, Takehara M, Adachi H, Katsuno M, Sobue G, Matsushima T, Suzuki T, Mizushima T.
    • Journal Title

      J Neurosci31

      Pages: 5225-5234

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Systemic but asymptomatic transthyretin amyloidosis 8 years after domino liver transplantation2011

    • Author(s)
      Koike H, Kiuchi T, Iijima M, Ueda M, Ando Y, Morozumi S, Tomita M, Kawagashira Y, Watanabe H, Katsuno M, Shimoyama Y, Okazaki Y, Kamei H, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 82 Pages: 1287-1290

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Macroautophagy is regulated by the UPR-mediator CHOP and accentuates the phenotype of SBMA mice2011

    • Author(s)
      Yu Z, Wang AM, Adachi H, Katsuno M, Sobue G, Yue Z, Robins DM, Lieberman AP
    • Journal Title

      PLoS Genet

      Volume: 7 Issue: 10 Pages: e1002321-e1002321

    • DOI

      10.1371/journal.pgen.1002321

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-23390230
  • [Journal Article] Spatial distribution of nerve fiber pathology and vasculitis in microscopic polyangiitis-associated neuropathy2011

    • Author(s)
      Morozumi S, Koike H, Tomita M, Kawagashira Y, Iijima M, Katsuno M, Hattori N, Tanaka F, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 70 Pages: 340-348

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Diagnosis of sporadic trans thyretin Val 30 Metfamilial amyloid polyneuropathy : a practical analysis2011

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Tanaka F, Sobue G.
    • Journal Title

      Amyloid

      Volume: 18 Pages: 53-62

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Systemic but asymptomatic transthyretin amyloidosis 8 years after domino liver transplantation2011

    • Author(s)
      Koike H, Kiuchi T, Iijima M, Ueda M, Ando Y, Morozumi S, Tomita M, Kawagashira Y, Watanabe H, Katsuno M, Shimoyama Y, Okazaki Y, Kamei H, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 82(11) Pages: 1287-90

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Diagnosis of sporadic transthyretin Val30Met familial amyloid polyneuropathy : a practical analysis2011

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Tanaka F, Sobue G
    • Journal Title

      Amyloid

      Volume: 18 Pages: 53-62

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Acute autonomic and sensory neuropathyの臨床と病理2011

    • Author(s)
      小池春樹, 祖父江元
    • Journal Title

      自律神経

      Volume: 48 Pages: 96-100

    • NAID

      10029303837

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Transforming growth factor-β signaling in motor neuron diseases.2011

    • Author(s)
      Katsuno M, Adachi H, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      Current Mol Med.

      Volume: 11 Pages: 48-56

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Transforming growth factor-β signaling in motor neuron diseases2011

    • Author(s)
      Katsuno M, Adachi H, Banno H, Suzuki K, Tanaka F, Sobue G
    • Journal Title

      Curr Mol Med

      Volume: 11 Pages: 48-56

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Transforming Growth Factor-β Signaling in Motor Neuron Diseases.2011

    • Author(s)
      Katsuno M, Adachi H, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      Curr Mol Med 11

      Pages: 48-56

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] 家族性アミロイドポリニューロパチーの臨床と病理2011

    • Author(s)
      小池春樹, 祖父江元
    • Journal Title

      臨床神経学

      Volume: 51 Pages: 1134-1137

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] ANCA関連血管炎による神経障害2011

    • Author(s)
      小池春樹, 祖父江元
    • Journal Title

      医学のあゆみ

      Volume: 236 Pages: 788-790

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Central nervous system involvement in n-hexane polyneuropathy demonstrated by MRI and proton MR spectroscopy2011

    • Author(s)
      Hashizume A, Koike H, Kawagashira Y, Banno H, Suzuki K, Ito M, Katsuno M, Watanabe H, Tanaka F, Naganawa S, Kaneko R, Ishii A, Sobue G
    • Journal Title

      Clin Neurol Neurosurg

      Volume: 113(6) Pages: 493-5

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] The wide range of clinical manifestations in leprous neuropathy: two case reports2011

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Nagamatsu M, Sobue G
    • Journal Title

      Intern Med

      Volume: 50(19) Pages: 2223-6

    • NAID

      130001087908

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Acute superficial sensory neuropathy with generalized an hidrosis, anosmia, and ageusia2011

    • Author(s)
      Miyazaki Y, Koike H, Ito M, Atsuta N, Watanabe H, Katsuno M, Kusunoki S, Sobue G.
    • Journal Title

      Muscle Nerve

      Volume: 43 Pages: 286-288

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Spatial distribution of nerve fiber pathology and vasculitis in microscopic polyangiitis-associated neuropathy2011

    • Author(s)
      Morozumi S, Koike H, Tomita M, Kawagashira Y, Iijima M, Kasuno M, Hattori N, Tanaka F, Sobue G
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 70 Pages: 340-8

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] The wide range of clinical manifestations in leprous neuropathy : two case reports2011

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Nagamatsu M, SobueG.
    • Journal Title

      Intern Med

      Volume: 50 Pages: 2223-2226

    • NAID

      130001087908

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] しびれとは2011

    • Author(s)
      小池春樹, 祖父江元
    • Journal Title

      日本医師会雑誌

      Volume: 140 Pages: 328-330

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] シャルコー・マリー・トゥース病200例のマイクロアレイDNAチップによる遺伝子診断2011

    • Author(s)
      橋口昭大, 徳永章子, 中村友紀, 岡本裕嗣, 有村公良, 小池春樹, 田中章景, 祖父江元, 高嶋博
    • Journal Title

      Peripheral Nerve

      Volume: 22 Pages: 64-71

    • NAID

      10029413624

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Acute superficial sensory neuropathy with generalized anhidrosis, anosmia, and ageusia.2011

    • Author(s)
      Miyazaki Y, Koike H, Ito M, Atsuta N, Watanabe H, Katsuno M, Kusunoki S, Sobue G.
    • Journal Title

      Muscle Nerve

      Volume: 43 Pages: 286-288

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Progressive and widespread brain damage in ALS: MRI voxel-based morphometry and diffusion tensor imaging study.2011

    • Author(s)
      Senda J, Kato S, Kaga T, Ito M, Atsuta N, Nakamura T, Watanabe H, Tanaka F, Naganawa S, Sobue G
    • Journal Title

      Amyotroph Lateral Scler

      Volume: 12(1) Pages: 59-69

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590955
  • [Journal Article] Systemic but asymptomatic trans thyretin amyloidosis 8 years after domino liver transplantation2011

    • Author(s)
      Koike H, Kiuchi T, Iijima M, Ueda M, Ando Y, Morozumi S, Tomita M, Kawagashira Y, Watanabe H, Katsuno M, Shimoyama Y, Okazaki Y, Kamei H, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 82 Pages: 1287-1290

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Polymorphism of transient axonal glycoprotein 1 in chronic inflammatory demyelinating polyneuropathy.2011

    • Author(s)
      Iijima M, Koike H, Katsuno M, Sobue G.
    • Journal Title

      J Peripher Nerv Syst

      Volume: in press

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Does cardiovascular autonomic dysfunction contribute to fatigue in Parkinson's disease?2011

    • Author(s)
      Nakamura T, et al
    • Journal Title

      Movement disorders

      Volume: 26 Issue: 10 Pages: 1869-74

    • DOI

      10.1002/mds.23744

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591111, KAKENHI-PROJECT-21600003
  • [Journal Article] Dutasteride for spinal and bulbar muscular atrophy : another advance to wards disease-modifying therapy.2011

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Sobue G.
    • Journal Title

      Lancet Neurol.

      Volume: 10 Pages: 113-115

    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Para neoplastic neuropathy : wide-ranging clinicopathological manifestations2011

    • Author(s)
      Koike H, Tanaka F, Sobue G.
    • Journal Title

      Curr Opin Neurol

      Volume: 24 Pages: 504-510

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Skin biopsy is useful for the antemortem diagnosis of neuronal intranuclear inclusion disease2011

    • Author(s)
      Sone J, Tanaka F, Koike H, Inukai A, Katsuno M, Yoshida M, Watanabe H, Sobue G.
    • Journal Title

      Neurology

      Volume: 76 Pages: 1372-1376

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Suppression of Alzheimer's disease-related phenotypes by expression of heat shock protein 70 in mice.2011

    • Author(s)
      Hoshino T, Murao N, Namba T, Takehara M, Adachi H, Katsuno M, Sobue G, Matsushima T, Suzuki T, Mizushima T.
    • Journal Title

      J Neurosci.

      Volume: 31 Issue: 14 Pages: 5225-5234

    • DOI

      10.1523/jneurosci.5478-10.2011

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PROJECT-22659011, KAKENHI-PUBLICLY-23113701, KAKENHI-PROJECT-23390017
  • [Journal Article] Spinal cord stimulation markedly ameliorated refractory neuropathicpain in transthyretin Val 30 Met familial amyloid polyneuropathy2011

    • Author(s)
      Miyazaki Y, Koike H, Akane A, Shibata Y, Nishiwaki K, Sobue G.
    • Journal Title

      Amyloid

      Volume: 18 Pages: 87-90

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] A functional variant in ZNF512B is associated with susceptibility to amyotrophic lateral sclerosis in Japanese.2011

    • Author(s)
      Iida A
    • Journal Title

      Hum Mol Genet

      Volume: 20 Issue: 18 Pages: 3684-3692

    • DOI

      10.1093/hmg/ddr268

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011, KAKENHI-PLANNED-22110005, KAKENHI-PLANNED-22116010, KAKENHI-PLANNED-22129005, KAKENHI-PROJECT-22590923, KAKENHI-PROJECT-22790179, KAKENHI-PROJECT-23500433
  • [Journal Article] Spatial distribution of nerve fiber pathology and vasculitis in microscopic polyangiitis-associated neuropathy.2011

    • Author(s)
      Morozumi S, Koike H, Tomita M, Kawagashira Y, Iijima M, Katsuno M, Hattori N, Tanaka F, Sobue G
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 70(5) Pages: 340-8

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Systemic but asymptomatic transthyretin amyloidosis 8 years after domino liver transplantation. J Neurol Neurosurg Psychiatry.2011

    • Author(s)
      Koike H. Kiuchi T, Iijima M, Ueda M, Ando Y, Morozumi S, Tomita M, Kawagashira Y, Watanabe H, Katsuno M, Shimoyama Y, Okazaki Y, Kamei H, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: in press

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Diagnosis of sporadic transthyretin Val30Met familial amyloid polyneuropathy: a practical analysis2011

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Tanaka F, Sobue G
    • Journal Title

      Amyloid

      Volume: 18(2) Pages: 53-62

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Polymorphism of transient axonal glycoprotein-1in chronic in flammatory demy elinating polyneuropathy2011

    • Author(s)
      Iijima M, Koike H, Katsuno M, Sobue G.
    • Journal Title

      J Peripher Nerv Syst

      Volume: 16 Suppl 1 Pages: 52-55

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Paraneoplastic neuropathy.2011

    • Author(s)
      Koike H, Sobue G.
    • Journal Title

      Handb Clin Neurol

      Volume: In press

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] CIDPの遺伝子多型と治療反応性2011

    • Author(s)
      飯島正博, 小池春樹, 祖父江元
    • Journal Title

      Annual review神経

      Pages: 300-309

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Central nervous system invoivement in n-hexane polyneuropathy demonstrated by MRI and proton MR spectroscopy.2011

    • Author(s)
      Hashizume A, Koike H, Kawagashira Y, Banno H, Suzuki K, Ito M, Katsuno M, Watanabe H, Tanaka F, Naganawa S, Kaneko R, Ishii A, Sobue G.
    • Journal Title

      Clin Neurol Neurosurg

      Volume: in press

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Central nervous system involvement in n-hexane polyneuropathy demonstrated by MRI and proton MR spectroscopy2011

    • Author(s)
      Hashizume A, Koike H, Kawagashira Y, Banno H, Suzuki K, Ito M, Katsuno M, Watanabe H, Tanaka F, Naganawa S, Kaneko R, Ishii A, Sobue G.
    • Journal Title

      Clin Neurol Neurosurg

      Volume: 113 Pages: 493-495

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Clinical features and molecular mechanisms of spinal and bulbar muscular atrophy (SBMA).2010

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Adachi H, Tanaka F, Sobue G.
    • Journal Title

      Adv Exp Med Biol 685

      Pages: 64-74

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Expanding the concept of inflammatory neuropathies2010

    • Author(s)
      Koike H, Sobue G
    • Journal Title

      Brain

      Volume: 133 Pages: 2848-2851

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis2010

    • Author(s)
      Sone J, Niwa J, Kawai K, Ishigaki S, Yamada S, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci Res

      Volume: 88 Pages: 123-135

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Morphological progression of myelin abnormalities in IgM-monoclonal gammopathy of undetermined significance anti-myelin-associated glycoprotein neuropathy.2010

    • Author(s)
      Kawagashira Y, Koike H, Tomita M, Morozumi S, Iijima M, Nakamura T, Katsuno M, Tanaka F, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 69 Pages: 1143-1157

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Differential response to intravenous immunoglobulin (IVIg) therapy among multifocal and polyneuropathy types of painful diabetic neuropathy2010

    • Author(s)
      Kawagashira Y, Watanabe H, Morozumi S, Iijima M, Koike H, Hattori N, Sobue G
    • Journal Title

      J Clin Neurosci

      Volume: 17(8) Pages: 1003-8

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Microarray analysis of gene expression by skeletal muscle of three mouse models of kennedy disease/spinal bulbar muscular atrophy.2010

    • Author(s)
      Mo K, Razak Z, Rao P, Yu Z, Adachi H, Katsuno M, Sobue G, Lieberman AP, Westwood JT, Monks DA.
    • Journal Title

      PLoS One

      Volume: 5

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Clinic pathological features of acute autonomic and sensory neuropathy2010

    • Author(s)
      Koike H, Atsuta N, Adachi H, Iijima M, Katsuno M, Yasuda T, Fukada Y, Yasui K, Nakashima K, Horiuchi M, Shiomi K, Fukui K, Takashima S, Morita Y, Kuniyoshi K, Hasegawa Y, Toribe Y, Kajiura M, Takeshita S, Mukai E, Sobue G.
    • Journal Title

      Brain

      Volume: 133 Pages: 2881-2896

    • NAID

      10029303837

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Pyramidal tract involvement in Guillain-Barre syndrome associated withanti-GM1 antibody2010

    • Author(s)
      Tomita M, Watanabe H, Morozumi S, Kawagashira Y, Iijima M, Nakamura T, Katsuno M, Koike H, Hattori N, Hirayama M, Kusunoki S, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 81 Pages: 583-585

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] 末梢神経障害抗アセチルコリン受容体抗体陽性の自律神経傷害性ニューロパチー2010

    • Author(s)
      小池春樹, 祖父江元
    • Journal Title

      Annual review神経

      Pages: 223-228

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Diagnosis of familial amyloid polyneuropathy : wide-ranged clinicopathological features2010

    • Author(s)
      Koike H, Sobue G.
    • Journal Title

      Expert Opin Med Diagn

      Volume: 4 Pages: 323-331

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Transforming growth factor-beta signaling in motor neuron diseases.2010

    • Author(s)
      Katsuno M, Adachi H, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      Current Mol Med.

      Volume: 11 Pages: 48-56

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Journal Article] Segmental copy-number gain within the region of isopentenyl diphosphate isomerase genes in sporadic amyotrophic lateral sclerosis2010

    • Author(s)
      Kato T, Emi M, Sato H, Arawaka S, Wada M, Kawanami T, Katagiri T, Tsuburaya K, Toyoshima I, Tanaka F, Sobue G, Matsubara K
    • Journal Title

      Biophys Res Commun

      Volume: 402 Pages: 438-442

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis.2010

    • Author(s)
      Sone J, Niwa J, Kawai K, Ishigaki S, Yamada S, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci Res 88

      Pages: 123-135

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy.2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Doi H, Kondo N, Mizoguchi H, Nitta A, Yamada K, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      J Neurosci.

      Volume: 30 Pages: 5702-5707

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis2010

    • Author(s)
      Sone J, Niwa JI, Kawai K, Ishigaki S, Yamada SI, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci Res. 88

      Pages: 123-135

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Doi H, Kondo N, Mizoguchi H, Nitta A, Yamada K, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      J Neurosci. 30

      Pages: 5702-5712

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Microarray analysis of gene expression by skeletal muscle of three mouse models of kennedy disease/spinal bulbar muscular atrophy.2010

    • Author(s)
      Mo K, Razak Z, Rao P, Yu Z, Adachi H, Katsuno M, Sobue G, Lieberman AP, Westwood JT, Monks DA.
    • Journal Title

      PLoS One

      Volume: 5

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Journal Article] Clinical features and molecular mechanisms of spinal and bulbar muscular atrophy (SBMA).2010

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Adachi H, Tanaka F, Sobue G.
    • Journal Title

      Adv Exp Med Biol.

      Volume: 685 Pages: 64-74

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy2010

    • Author(s)
      Katsuno, M., Adachi, H., Minamiyama, M., Waza, M., Doi, H., Kondo, N., Mizoguchi, H., Nitta, A., Yamada, K., Banno, H., Suzuki, K., Tanaka, F., Sobue, G.
    • Journal Title

      J. Neurosci 30

      Pages: 5702-5712

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Prevention of ultraviolet B radiation-induced epidermal damage by expression of heat shock protein 70.2010

    • Author(s)
      Matsuda M, Hoshino T, Yamashita Y, Tanaka KI, Maji D, Sato K, Adachi H, Sobue G, Ihn H, Funasaka Y, Mizushima T.
    • Journal Title

      J Biol Chem 285

      Pages: 5848-5858

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] The profile of motor unit number estimation (MUNE) in spinal and bulbar Museular atrophy.2010

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Takeuchi Y, Kawashima M, Suga N, Hashizume A, Hama T, Uchida K, Yamashita F, Nakamura T, Hirayama M, Tanaka F, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry 81

      Pages: 567-571

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Urinary 8-hydroxydeoxyguanosine correlate with hallucinations rather than motor symptoms in Parkinson's disease2010

    • Author(s)
      Hirayama, M., Nakamura, T., Watanabe, H., Uchida, K., Hama, T., Niimi, Y., Ito, M., Ohno, K., Sobue, G.
    • Journal Title

      Parkinsonism Relat Disorder

      Volume: 17 Pages: 46-49

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Journal Article] Putaminal magnetic resonance imaging features at various magnetic field strengths in multiple system atrophy2010

    • Author(s)
      Watanabe H, Ito M, Fukatsu H, Senda J, Atsuta N, Kaga T, Kato S, Katsuno M, Tanaka F, Hirayama M, Naganawa S, Sobue G
    • Journal Title

      Mov Disord

      Volume: 25(12) Pages: 1916-23

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590955
  • [Journal Article] Pupillary autonomic dysfunction in multiple system atrophy and Parkinson's disease : an assessment by eye-drop tests2010

    • Author(s)
      Yamashita, F., Hirayama, M., Nakamura, T., Takamori, M., Hori, N., Uchida, K., Hama, T., Sobue, G.
    • Journal Title

      Clin auton res

      Volume: 20 Pages: 191-197

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Journal Article] Pyramidal tract involvement in Guillain-Barre syndrome associated with anti-GM1 antibody2010

    • Author(s)
      Tomita M, Watanabe H, Morozumi S, Kawagashira Y, Iijima M, Nakamura T, Katsuno M, Koike H, Hattori N, Hirayama M, Kusunoki S, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 81(5) Pages: 583-5

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] 膠原病における神経病理末梢神経2010

    • Author(s)
      小池春樹, 祖父江元
    • Journal Title

      日本内科学会雑誌

      Volume: 99 Pages: 1853-1857

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Pyramidal tract involvement in Guillain-Barre syndrome associated with anti-GM1 antibody.2010

    • Author(s)
      Tomita M, Watanabe H, Morozumi S, Kawagashira Y, Iijima M, Nakamura T, Katsuno M, Koike H, Hattori N, Hirayama M, Kusunoki S, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 81 Pages: 583-585

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis.2010

    • Author(s)
      Sone J, Niwa JI, Kawai K, Ishigaki S, Yamada SI, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci Res. 88

      Pages: 123-135

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] IgM MGUS anti-MAG neuropathy with predominant muscle weakness and extensive muscle atrophy2010

    • Author(s)
      Kawagashira Y, Kondo N, Atsuta N, Iijima M, Koike H, Katsuno M, Tanaka F, Kusunoki S, Sobue G
    • Journal Title

      Muscle Nerve

      Volume: 42(3) Pages: 433-5

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Differential response to intravenous immunoglobulin(IVIg) therapy among multifocal and polyneuropathy types of painful diabetic neuropathy2010

    • Author(s)
      Kawagashira Y, Watanabe H, Morozumi S, Iijima I, Koike H, Hattori N, Sobue G.
    • Journal Title

      J Clin Neurosci

      Volume: 17 Pages: 1003-1008

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Disrupted transforming growth factor-beta signaling in spinal and bulbar muscular atrophy.2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Doi H, Kondo N, Mizoguchi H, Nitta A, Yamada K, Banno H, Suzuki K, Tanaka F, Sobue G
    • Journal Title

      J Neurosci

      Volume: 30 Pages: 5702-5712

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Putaminal magnetic resonance imaging features at various magnetic field strengths in multiple system atrophy2010

    • Author(s)
      Watanabe, H., Ito, M., Fukatsu, H., Senda, J., Atsuta, N., Kaga, T., Kato, S., Katsuno, M., Tanaka, F., Hirayama, M., Naganawa, S., Sobue, G.
    • Journal Title

      Mov Disord

      Volume: 25 Pages: 1916-1923

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Journal Article] Slowly progressive autonomic neuropathy with antiganglionic acetylcholine receptor antibody2010

    • Author(s)
      Koike H, Koyano S, Morozumi S, Kawagashira Y, Iijima M, Katsuno M, Hattori N, Vernino S, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 81 Pages: 586-587

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] The profile of motor unit number estimation (MUNE) in spinal and bulbar muscular atrophy2010

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Takeuchi Y, Kawashima M, Suga N, Hashizume A, Hama T, Uchida K, Yamashita F, Nakamura T, Hirayama M, Tanaka F, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry 81

      Pages: 567-571

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Dutasteride for spinal and bulbar muscular atrophy : another advance to wards disease-modifying therapy.2010

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Sobue G.
    • Journal Title

      Lancet Neurol.

      Volume: 10 Pages: 113-115

    • Data Source
      KAKENHI-PLANNED-22110005
  • [Journal Article] Diagnosis of familial amyloid polyneuropathy : wide-ranged clinicopathological features.2010

    • Author(s)
      Koike H, Sobue G.
    • Journal Title

      Expert Opin Med Diagn

      Volume: 4 Pages: 323-331

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Morphological progression of myelin abnormalities in IgM-monoclonal gammopathy of undetermined significance anti-myelin-associated glycoprotein neuropathy2010

    • Author(s)
      Kawagashira Y, Koike H, Tomita M, Morozumi S, Iijima M, Nakamura T, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 69(11) Pages: 1143-57

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Differential response to intravenous immunoglobulin (IVIg) therapy among multifocal and polyneuropathy types of painful diabetic neuropathy.2010

    • Author(s)
      Kawagashira Y, Watanabe H, Morozumi S, Iijima I, Koike H, Hattori N, Sobue G.
    • Journal Title

      J Clin Neurosci

      Volume: 17 Pages: 1003-1008

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Slowly progressive autonomic neuropathy with antiganglionic acetylcholine receptor antibody.2010

    • Author(s)
      Koike H, Koyano S, Morozumi S, Kawagashira Y, Iijima M, Katsuno M, Hattori N, Vernino S, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 81 Pages: 586-587

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] IgM MGUS anti-MAG neuropathy with predominant muscle weakness and extensive muscle atrophy2010

    • Author(s)
      Kawagashira Y, Kondo N, Atsuta N, Iijima M, Koike H, Katsuno M, Tanaka F, Kusunoki S, Sobue G.
    • Journal Title

      Muscle Nerve

      Volume: 42 Pages: 433-435

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Disrupted transforming growth factor-beta signaling in spinal and bulbar muscular atrophy.2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Doi H, Kondo N, Mizoguchi H, Nitta A, Yamada K, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      J Neurosci 30

      Pages: 5702-5712

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Morphological progression of myelin abnormalities in Ig M-monoclonal gammopathy of undetermined significance anti-myelin-associated glycoprotein neuropathy2010

    • Author(s)
      Kawagashira Y, Koike H, Tomita M, Morozumi S, Iijima M, Nakamura T, Katsuno M, Tanaka F, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol

      Volume: 69 Pages: 1143-1157

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] The profile of motor unit number estimation (MUNE) in spinal and bulbar muscular atrophy.2010

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Takeuchi Y, Kawashima M, Suga N, Hashizume A, Hama T, Uchida K, Yamashita F, Nakamura T, Hirayama M, Tanaka F, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 81 Pages: 567-571

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Journal Article] Expanding the concept of inflammatory neuropathies.2010

    • Author(s)
      Koike H, Sobue G.
    • Journal Title

      Brain

      Volume: 133 Pages: 2848-2851

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Efficacy and safety of leuprorelin in patients with spinal and bulbar muscular atrophy (JASMITT study) : a multicentre, randomised, double-blind, placebo-controlled trial.2010

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Takeuchi Y, Kawashima M, Yabe I, Sasaki H, Aoki M, Morita M, Nakano I, Kanai K, Ito S, Ishikawa K, Mizusawa H, Yamamoto T, Tsuji S, Hasegawa K, Shimohata T, Nishizawa M, Miyajima H, Kanda F, Watanabe Y, Nakashima K, Tsujino A, Yamashita T, Uchino M, Fujimoto Y, Tanaka F, Sobue G ; for the Japan SBMA Interventional Trial for TAP-144-SR (JASMITT) study group.
    • Journal Title

      Lancet Neurol.

      Volume: 9 Pages: 875-884

    • Peer Reviewed
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Journal Article] Suppression of melanin production by expression of HSP70.2010

    • Author(s)
      Hoshino T, Matsuda M, Yamashita Y, Takehara M, Fukuya M, Mineda K, Maji D, Ihn H, Adachi H, Sobue G, Funasaka Y, Mizushima T.
    • Journal Title

      J Biol Chem 285

      Pages: 13254-13263

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy.2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Doi H, Kondo N, Mizoguchi H, Nitta A, Yamada K, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Journal Title

      J Neurosci. 30

      Pages: 5702-5712

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] IgM MGUS anti-MAG neuropathy with predominant muscle weakness and extensive muscle atrophy.2010

    • Author(s)
      Kawagashira Y, Kondo N, Atsuta N, Iijima M, Koike H, Katsuno M, Tanaka F, Kusunoki S, Sobue G.
    • Journal Title

      Muscle Nerve

      Volume: 42 Pages: 433-435

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Slowly progressive autonomic neuropathy with antiganglionic acetylcholine receptor antibody2010

    • Author(s)
      Koike H, Koyano S, Morozumi S, Kawagashira Y, Iijima M, Katsuno M, Hattori N, Vernino S, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 81(5) Pages: 586-7

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Journal Article] Pyramidal tract involvement in Guillain-Barre syndrome associated with anti-GM1 antibody2010

    • Author(s)
      Tomita, M., Watanabe, H., Morozumi, S., Kawagashira, Y., Iijima, M., Nakamura, T., Katsuno, M., Koike, H., Hattori, N., Hirayama, M., Kusunoki, S., Sobue, G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 81 Pages: 583-585

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Journal Article] Lowered cardiac sympathetic nerve performance in response to exercise in Parkinson's disease2010

    • Author(s)
      Nakamura, T., Hirayama, M., Yamashita, F., Uchida, K., Hama, T., Watanabe, H., Sobue, G.
    • Journal Title

      Mov Disord

      Volume: 25 Pages: 1183-1189

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Journal Article] Clinicopathological features of acute autonomic and sensory neuropathy.2010

    • Author(s)
      Koike H, Atsuta N, Adachi H, Iijima M, Katsuno M, Yasuda T, Fukada Y, Yasui K, Nakashima K, Horiuchi M, Shiomi K, Fukui K, Takashima S, Morita Y, Kuniyoshi K, Hasegawa Y, Toribe Y, Kajiura M, Takeshita S, Mukai E, Sobue G.
    • Journal Title

      Brain 133(10)

      Pages: 2881-2896

    • NAID

      10025625514

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Doi H, Kondo N, Mizoguchi H, Nitta A, Yamada K, Banno H, Suzuki K, Tanaka F, Sobue G
    • Journal Title

      J Neurosci

      Volume: 30 Issue: 16 Pages: 5702-5712

    • DOI

      10.1523/jneurosci.0388-10.2010

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Efficacy and safety of leuprorelin in patients with spinal and bulbar muscular atrophy (JASMITT study) : a multicentre, randomised, double-blind, placebo-controlled trial.2010

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Takeuchi Y, Kawashima M, Yabe I, Sasaki H, Aoki M, Morita M, Nakano I, Kanai K, Ito S, Ishikawa K, Mizusawa H, Yamamoto T, Tsuji S, Hasegawa K, Shimohata T, Nishizawa M, Miyajima H, Kanda F, Watanabe Y, Nakashima K, Tsujino A, Yamashita T, Uchino M, Fujimoto Y, Tanaka F, Sobue Cr ; for the Japan SBMA Interventional Trial for TAP-144-SR (JASMITT) study group.
    • Journal Title

      Lancet Neurol.

      Volume: 9 Pages: 875-884

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] The profile of motor unit number estimation (MUNE) in spinal and bulbar muscular atrophy2010

    • Author(s)
      Suzuki, K., Katsuno, M., Banno, H., Takeuchi, Y., Kawashima, M., Suga, N., Hashizume, A., Hama, T., Uchida, K., Yamashita, F., Nakamura, T., Hirayama, M., Tanaka, F., Sobue, G.
    • Journal Title

      J Neurol Neurosurg Psychiatry

      Volume: 81 Pages: 567-571

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Journal Article] Microarray Analysis of Gene Expression by Skeletal Muscle of Three Mouse Models of Kennedy Disease/Spinal Bulbar Muscular Atrophy.2010

    • Author(s)
      Mo K, Razak Z, Rao Y, Yu Z, Adachi H, Katsuno M, Sobue G, Lieberman AP, Westwood JT, Monks DA.
    • Journal Title

      PLoS ONE 5

      Pages: 12922-12922

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Journal Title

      J Biol Chem (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] The significance of carpal tunnel syndrome in transthyretin Val30Met familial amyloid polyneuropathy2009

    • Author(s)
      Koike H, Morozumi S, Kawagashira Y, Iijima M, Yamamoto M, Hattori N, Tanaka F, Nakamura T, Hirayama M, Ando Y, Ikeda SI, Sobue G.
    • Journal Title

      Amyloid

      Volume: 15 Pages: 1-7

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Correlation between pyramidal tract degeneration and widespread white matter involvement in amyotrophic lateral sclerosis: A study with tractography and diffusion-tensor imaging2009

    • Author(s)
      Senda J, Ito M, Watanabe H, Atsuta N, Kawai Y, Katsuno M, Tanaka F, Naganawa S, Fukatsu H, Sobue G.
    • Journal Title

      Amyotroph Lateral Scler. (in press)

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Correlation between pyramidal tract degeneration and widespread white matter involvement in amyotrophic lateral sclerosis : a study with tractography and diffusion-tensor imaging2009

    • Author(s)
      Senda J, Ito M, Watanabe H, Atsuta N, Kawai Y, Katsuno M, Tanaka F, Naganawa S, Fukatsu H, Sobue G.
    • Journal Title

      Amyotroph Lateral Scler. 10

      Pages: 288-294

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Getting a handle on Huntington's disease, the case for cholesterol2009

    • Author(s)
      Katsuno, M., Adachi, H., Sobue, G.
    • Journal Title

      Nat. Med. 15

      Pages: 253-254

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno, H., Katsuno, M., Suzuki, K., Takeuchi, Y., Kawashima, M., Suga, N., Takamori, M., Ito, M., Nakamura, T., Matsuo, K., Yamada, S., Oki, Y., Adachi, H., Minamiyama, M., Waza, M., Atsuta, N., Watanabe, H., Fujimoto, Y., Nakashima, T., Tanaka, F., Doyu, M., Sobue, G.
    • Journal Title

      Ann Neurol 65

      Pages: 140-150

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Overexpression of IGF-1 in muscle attenuates disease in a mouse model of spinal and bulbar muscular atrophy.2009

    • Author(s)
      Palazzolo I, Stack C, Kong L, Musaro A, Adachi H, Katsuno M, Sobue G, Taylor JP, Sumner CJ, Fischbeck KH, Pennuto M.
    • Journal Title

      Neuron 63

      Pages: 316-328

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Intravenous immunoglobulin treatment for painful sensory neuropathy associated with Sjogren's syndrome2009

    • Author(s)
      Morozumi S, Kawagashira Y, Iijima M, Koike H, Hattori N, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Sci 15 ; 279

      Pages: 57-61

    • NAID

      10025625884

    • Data Source
      KAKENHI-PROJECT-19590986
  • [Journal Article] Single nucleotide polymorphism of TAG-1influences IVIg responsiveness of Japanese patients with CIDP2009

    • Author(s)
      Iijima M, Tomita M, Morozumi S, Kawagashira Y, Nakamura T, Koike H, Katsuno M, Hattori N, Tanaka F, Yamamoto M, Sobue G.
    • Journal Title

      Neurology

      Volume: 73 Pages: 1348-1352

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] 17-DMAG ameliorates polyglutamine-mediated motor neuron degeneration through well-preserved proteasome function in a SBMA model mouse2009

    • Author(s)
      Tokui K, Adachi H, Waza M, Katsuno M, Minamiyama M, Doi H, Tanaka K, Hamazaki J, Murata S, Tanaka F, Sobue G
    • Journal Title

      Hum. Mol. Genet 18

      Pages: 898-910

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Getting a handle on Huntington's disease : the case for cholesterol2009

    • Author(s)
      Katsuno M, Adachi H, Sobue G
    • Journal Title

      Nat. Med 15

      Pages: 253-254

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Intravenous immunoglobulin treatment for painful sensory neuropathy associated with Sjogren's syndrome2009

    • Author(s)
      Morozumi S, Kawagashira Y, Iijima M, Koike H, Hattori N, Katsuno M, Tanaka F, Sobue G.
    • Journal Title

      J Neurol Sci

      Volume: 279 Pages: 57-61

    • NAID

      10025625884

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      Ann Neurol. 65

      Pages: 140-150

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Walking capacity evaluated by the 6-minute walk test in spinal and bulbar muscular atrophy2009

    • Author(s)
      Takeuchi Y, Katsuno M, Banno H, Suzuki K, Kawashima M, Atsuta N, Ito M, Watanabe H, Tanaka F, Sobue G
    • Journal Title

      Muscle Nerve 38

      Pages: 964-971

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] TDP-43 Depletion Induces Neuronal Cell Damage through Dysregulation of Rho Family GTPases.2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Journal Title

      J Biol Chem. 284

      Pages: 22059-22066

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Correlation between pyramidal tract degeneration and widespread white matter involvement in amyotrophic lateral sclerosis : A study with tractography and diffusion-tensor imaging2009

    • Author(s)
      Senda J, Ito M, Watanabe H, Atsuta N, Kawai Y, Katsuno M, Tanaka F, Naganawa S, Fukatsu H, Sobue G
    • Journal Title

      Amyotroph. Lateral Scler (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis2009

    • Author(s)
      Sone J, Niwa J, Kawai K, Ishigaki S, Yamada S, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci Res (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] 17-DMAG ameliorates polyglutamine-mediated motor neuron degeneration through well-preserved proteasome function in a SBMA model mouse2009

    • Author(s)
      Tokui, K., Adachi, H., Waza, M., Katsuno, M., Minamiyama, M., Doi, H., Tanaka, K., Hamazaki, J., Murata, S., Tanaka, F., Sobue, G.
    • Journal Title

      Hum. Mol. Genet. 18

      Pages: 898-910

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis2009

    • Author(s)
      Sone J, Niwa J, Kawai K, Is higaki S, Yamada S, Adachi H, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci Res (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy.2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      Ann Neurol 65

      Pages: 140-150

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] 17-DMAG ameliorates polyglutamine-mediated motor neuron degeneration through well-preserved proteasome function in a SBMA model mouse.2009

    • Author(s)
      Tokui K*, Adachi H*, Waza M, Katsuno M, Minamiyama M, Doi H, Tanaka K, Hamazaki J, Murata S, Tanaka F, Sobue G.
    • Journal Title

      Hum Mol Genet(* Evenly contributed to the study) 18

      Pages: 898-910

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] A role for HSP70 in protecting against indomethacin-induced gastric lesions.2009

    • Author(s)
      Suemasu S, Tanaka KI, Namba T, Ishihara T, Katsu T, Fujimoto M, Adachi H, Sobue G, Takeuchi K, Nakai A, Mizushima T.
    • Journal Title

      J Biol Chem 284

      Pages: 19705-19715

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Heat shock proteins in neurodegenerative diseases : pathogenic roles and therapeutic implications.2009

    • Author(s)
      Adachi H, Katsuno M, Waza M, Minamiyama M, Tanaka F, Sobue G.
    • Journal Title

      Int J Hyperthermia 25

      Pages: 647-654

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Overexpression of IGF-1 in muscle attenuates disease in a mouse model of spinal and bulbar muscular atrophy.2009

    • Author(s)
      Palazzolo I, Stack C, Kong L, Musaro A, Adachi H, Katsuno M, Sobue G, Taylor JP, Sumner CJ, Fischbeck KH, Pennuto M.
    • Journal Title

      Neuron 63

      Pages: 316-328

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Distinct characteristics of amyloid deposits in early-and late-onset transthyretinVal30Met familial amyloid polyneuropathy2009

    • Author(s)
      Koike H, Ando Y, Ueda M, Kawagashira Y, Iijima M, Fujitake J, Hayashi M, Yamamoto M, Mukai E, Nakamura T, Katsuno M, Hattori N, Sobue G.
    • Journal Title

      J Neurol Sci

      Volume: 287 Pages: 178-184

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Neuropathology and therapeutic intervention in spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Tanaka F, Sobue G
    • Journal Title

      Int. J. Mol. Sci (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Correlation between pyramidal tract degeneration and widespread white matter involvement in amyotrophic lateral sclerosis : a study with tractography and diffusion-tensor imaging.2009

    • Author(s)
      Senda J, Ito M, Watanabe H, Atsuta N, Kawai Y, Katsuno M, Tanaka F, Naganawa S, Fukatsu H, Sobue G.
    • Journal Title

      Amyotroph Lateral Scler. 10

      Pages: 288-294

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] 17-DMAG ameliorates polyglutamine-mediated motor neuron degeneration through well-preserved proteasome function in an SBMA model mouse2009

    • Author(s)
      Tokui K, Adachi H, Waza M, Katsuno M, Minamiyama M, Doi H, Tanaka K, Hamazaki J, Murata S, Tanaka F, Sobue G.
    • Journal Title

      Hum Mol Genet 18

      Pages: 898-910

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Research Committee on the Neurodegenerative Diseases of Japan. Age at onset influences on wide-ranged clinical features of sporadic amyotrophic lateral sclerosis2009

    • Author(s)
      Atsuta N, Watanabe H, Ito M, Tanaka F, Tamakoshi A, Nakano I, Aoki M, Tsuji S, Yuasa T, Takano H, Hayashi H, Kuzuhara S, Sobue G.
    • Journal Title

      J Neurol Sci. 276

      Pages: 163-169

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] TDP-43 Depletion Induces Neuronal Cell Damage through Dysregulation of Rho Family GTPases2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Journal Title

      J Biol Chem. 284

      Pages: 22059-22066

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G
    • Journal Title

      J Biol Chem. (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Overexpression of IGF-1 in muscle attenuates disease in a mouse model of spina I and bulbar muscular atrophy2009

    • Author(s)
      Palazzolo I, Stack C, Kong L, Musaro A, Adachi H, Katsuno M, Sobue G, Taylor JP, Sumner CJ, Fischbeck KH, Pennuto M.
    • Journal Title

      Neuron 63

      Pages: 316-328

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Heat shock proteins in neurodegenerative diseases : Pathogenic roles and therapeutic implications.2009

    • Author(s)
      Adachi H, Katsuno M, Waza M, Minamiyama M, Tanaka F, Sobue G.
    • Journal Title

      Int J Hyperthermia 25

      Pages: 647-654

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Overexpression of IGF-1 in muscle attenuates disease in a mouse model of spinal and bulbar muscular atrophy2009

    • Author(s)
      Palazzolo, I., Stack, C., Kong, L., Musaro, A., Adachi, H., Katsuno, M., Sobue, G., Taylor, J.P., Sumner, C.J., Fischbeck, K.H., Pennuto, M.
    • Journal Title

      Neuron 63

      Pages: 316-328

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] The case for cholesterol2009

    • Author(s)
      Katsuno M, Adachi H, Sobue G.
    • Journal Title

      .Nature Med. (in press)

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] TDP-43 Depletion Induces Neuronal Cell Damage through Dysregulation of Rho Family GTPases2009

    • Author(s)
      Iguchi, Y., Katsuno, M., Niwa, J., Yamada, S., Sone, J., Waza, M., Adachi, H., Tanaka, F., Nagata, K., Arimura, N., Watanabe, T., Kaibuchi, K., Sobue, G.
    • Journal Title

      J Biol Chem. 284

      Pages: 22059-22066

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Electrophysiological features of late-onset transthyretin Met30 familial amyloid polyneuropathy unrelated to endemic foci2009

    • Author(s)
      Koike H, Kawagashira Y, Iijima M, Yamamoto M, Hattori N, Tanaka F, Hirayama M,Ando Y, Ikeda S, Sobue G
    • Journal Title

      J Neurol 255

      Pages: 1526-33

    • Data Source
      KAKENHI-PROJECT-19590986
  • [Journal Article] HSP70 Confers Protection against Indomethacin-Induced Lesions of the Small Intestine.2009

    • Author(s)
      Teita A, Tanaka KI, Yamakawa N, Adachi H, Sobue G, Goto H, Takeuchi K, Mizushima T.
    • Journal Title

      J Pharmacol Exp Ther 330

      Pages: 458-467

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Pathogenesis-targeting Therapeutics for Spinal and Bulbar Muscular Atrophy (SBMA)2009

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Sobue G
    • Journal Title

      Neuropathology (in press)

    • NAID

      10028192075

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases.2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa JI, Yamada SI, Sone J, Waza M, Adachi H, Tanaka F, Nagata KI, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Journal Title

      J Biol Chem 284

      Pages: 22059-22066

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Getting a handle on Huntington's disease : the case for cholesterol.2009

    • Author(s)
      Katsuno M, Adachi H, Sobue G.
    • Journal Title

      Nat Med 15

      Pages: 253-254

    • Data Source
      KAKENHI-PROJECT-20390243
  • [Journal Article] Heat shock proteins in neurodegenerative diseases : Pathogenic roles and therapeutic implications2009

    • Author(s)
      Adachi H, Katsuno M, Waza M, Minamiyama M, Tanaka F, Sobue G.
    • Journal Title

      Int J Hyperthermia 25

      Pages: 647-654

    • Data Source
      KAKENHI-PROJECT-21229011
  • [Journal Article] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann. Neurol 65

      Pages: 140-150

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] CAG repeat size correlates to electrophysiological motor and sensory phenotypes in SBMA2008

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Takeuchi Y, Atsuta N, Ito M, Watanabe H, Yamashita F, Hori N, Nakamura T, Hirayama M, Tanaka F, Sobue G.
    • Journal Title

      Brain 131

      Pages: 229-239

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Molecular Genetics and Biomarkers of Polyglutamine Diseases2008

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Takeuchi Y, Kawashima M, Adachi H, Tanaka F, Sobue G
    • Journal Title

      Current Mol. Med. 8

      Pages: 221-234

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Refractory Peripheral Neuropathy Study Group of Japan. Prevalence and incidence rates of chronic inflammatory demyelinating polyneuropathy in the Japanese population2008

    • Author(s)
      Iijima M, Koike H, Hattori N, Tamakoshi A, Katsuno M, Tanaka F, Yamamoto M, Arimura K, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry 79

      Pages: 1040-1043

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Refractory Peripheral Neuropathy Study Group of Japan. Prevalence and incidence rates of chronic inflammatory demyelinating polyneuropathy in the Japanese population2008

    • Author(s)
      Iijima M, Koike H, Hattori N, Tamakoshi A, Katsuno M, Tanaka F, Yamamoto M, Arimura K, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 79

      Pages: 1040-3

    • Data Source
      KAKENHI-PROJECT-19590986
  • [Journal Article] Cognitive impairment in spinocerebellar ataxia type 62008

    • Author(s)
      Suenaga M, Kawai Y, Watanabe H, Atsuta N, Ito M, Tanaka F, Katsuno M, Fukatsu H, Naganawa S, Sobue G
    • Journal Title

      J. Neurol .Neurosurg. Psychiatry 79

      Pages: 496-499

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] CAG repeat size correlates to electrophysiological motor and sensory phenotypes in SBMA2008

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Takeuchi Y, Atsuta N, Ito M, Watanabe H, Yamashita F, Hori N, Nakamura T, Hirayama M, Tanaka F, Sobue G
    • Journal Title

      Brain 131

      Pages: 229-239

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] CAG repeat size correlates to electrophysiological motor and sensory phenotypes in SBMA2008

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Yamashita F, Hori N, Nakamura T, Hirayama M, Tanaka F, Sobue G
    • Journal Title

      Brain 131

      Pages: 229-239

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Molecular genetics and biomarkers of polyglutamine diseases2008

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Takeuchi Y, Kawashima M, Tanaka F, Adachi H, Sobue G.
    • Journal Title

      Curr Mol Med. 8

      Pages: 221-234

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] CAG repeat size correlates to electrophysiological motor and sensory phenotypes in SBMA2008

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Takeuchi Y, Atsuta N, Ito M, Watanabe H, Yamashita F, Hori N, Nakamura T, Hirayama M, Tanaka F, Sobue G
    • Journal Title

      Brain 131

      Pages: 229-239

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Prevalence and incidence rates of chronic inflammatory demyelinating polyneuropathy in the Japanese population2008

    • Author(s)
      Iijima, M., Koike, H., Hattori, N., Tamakoshi, A., Katsuno, M., Tanaka, F., Yamamoto, M., Arimura, K., Sobue, G
    • Journal Title

      J Neurol Neurosurg Psychiatry (in press)

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18390262
  • [Journal Article] CAG repeat size correlates to electrophysiological motor and sensory phenotypes in SBMA2008

    • Author(s)
      Suzuki, K., Katsuno, M., Banno, H., Takeuchi, Y., Atsuta, N., Ito, M., Watanabe, H., Yamashita, F., Hori, N., Nakamura, T., Hirayama, M., Tanaka, F., Sobue, G.
    • Journal Title

      Brain 131

      Pages: 229-239

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] A strategy for developing effective amyotropic lateral sclerosis pharmacotherapy: from clinical trials to novel pharmacotherapeutic strategies2008

    • Author(s)
      Yamamoto M, Tanaka F, Tatsumi H, Sobue G.
    • Journal Title

      Expert Opin Pharmacother 9

      Pages: 1845-1857

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Rapidly developing weakness mimicking Guillain-Barre syndrome in beriberi neuropathy : two case reports2008

    • Author(s)
      Koike H, Ito S, Morozumi S, Kawagashira Y, Iijima M, Hattori N, Tanaka F, Sobue G
    • Journal Title

      Nutrition 24

      Pages: 776-80

    • Data Source
      KAKENHI-PROJECT-19590986
  • [Journal Article] Neuropathic pain correlates with myelinated fibre loss and cytokine profile in POEMS syndrome2008

    • Author(s)
      Koike H, Iijima M, Mori K, Yamamoto M, Hattori N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 79

      Pages: 1171-9

    • Data Source
      KAKENHI-PROJECT-19590986
  • [Journal Article] Walking capacity evaluated by the 6-minute walk test in spinal and bulbar muscular atrophy2008

    • Author(s)
      Takeuchi Y, Katsuno M, Banno H, Suzuki K, Kawashima M, Atsuta N, Ito M, Watanabe H, Tanaka F, Sobue G
    • Journal Title

      Muscle Nerve 38

      Pages: 946-971

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Ataxic vs painful form of paraneoplastic neuropathy. Intravenous immunoglobulin therapy markedly ameliorates muscle weakness and severe pain in proximal diabetic neuropathy2007

    • Author(s)
      Oki Y, Koike H, Iijima M, Mori K, Hattori N, Katsuno M, Nakamura T, Hirayama M, Tanaka F, Shiraishi M, Yazaki S, Nokura K, Yamamoto H, Sobue G
    • Journal Title

      Neurology 69

      Pages: 564-72

    • Data Source
      KAKENHI-PROJECT-19590986
  • [Journal Article] Enhanced aquaporin-4 immunoreactivity in sporadic creutzfeldt-Jakob disease2007

    • Author(s)
      Iwasaki Y, Mimuro M, Yoshida M. Hashizume Y, Ito M, Kitamoto T, Wakayama Y, Sobue G
    • Journal Title

      Neuropathology 27

      Pages: 314-323

    • NAID

      10021235965

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity.2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G
    • Journal Title

      Neurobiol Dis. 25

      Pages: 331-341

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity.2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G
    • Journal Title

      Neurobiol of Dis 25

      Pages: 331-341

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2007

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G.
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 1-10

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Therapeutic strategies for spinal and bulbar musculara atrophy (SBMA)2007

    • Author(s)
      Katsuno M, Bannno H, Suzuki K, Takeuchi Y, Minamiyama M, Waza M, Adachi H, Tanaka F, Sobue G
    • Journal Title

      Drugns of the Future 32

      Pages: 907-917

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Pyramidal tract degeneration in sporadic Creutzfeldt-Jakob disease2007

    • Author(s)
      Iwasaki Y, Yoshida M, Hashizume Y, Kitamoto T, Sobue G
    • Journal Title

      Neuropathology 27

      Pages: 434-441

    • NAID

      10021236410

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Usefulness of combined fractional anisotropy and apparent diffusion coefficient values for detection of involvement in multiple system atropyh2007

    • Author(s)
      Ito M, Watanabe H, Kawai Y, Atsuta N, Tanaka F, Naganawa S, Fukatsu H, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 78

      Pages: 722-728

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Gene expressions specifically detected in motor neurons (dynactin 1, early growth response 3, Acetyl-CoA transporter, death receptor 5, and cyclin C) differentially correlate to athologic markers in sporadic amyotrophic lateral sclerosis2007

    • Author(s)
      Jiang Y, Yamamoto M, Tanaka F, Ishigaki S, Katsuno M, Adachi H, Niwia J, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Neuropathol Exp Neurol 66

      Pages: 617-627

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD12007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 282

      Pages: 28087-28095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Ataxic vs painful form of paraneoplastic neuropathy2007

    • Author(s)
      Oki Y, Koike H, Iijima M, Mori K, Hattori N, Katsuno M, Nakamura T, Hirayama M, Tanaka F, Shiraishi M, Yazaki S, Nokura K, Yamamoto H,Sobue G
    • Journal Title

      Neurology 69

      Pages: 564-572

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] ASC-J9 ameliorates spinal and bulbar muscular atrophy phenotype via degradation of androgen receptor2007

    • Author(s)
      Yang Z, Chang YJ, Yu IC, Yeh S, Wu CC, Miyamoto H, Merry DE, Sobue G, Chen LM, Chang SS, Chang C
    • Journal Title

      Nat. Med 13

      Pages: 348-353

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] CHIP overexpression reduces mutant androgen receptor protein and ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2007

    • Author(s)
      Adachi, H., Waza, M., Tokui, K., Katsuno, M., Minamiyama, M., Tanaka, F., Doyu, M., Sobue, G.
    • Journal Title

      J. Neurosci 27

      Pages: 5115-5126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Reduces Mutant Androgen Receptor Protein and Ameliorates Phenotypes of the Spinal and Bulbar Muscular Atrophy Transgenic Mouse Model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Minamiyama M, Tanak F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 27

      Pages: 5115-5126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Gene expressions specifically detected in motor neurons (dynactin 1, early growth response 3, acetyl-CoA transporter, death receptor 5, and cyclin C) differentially correlate to pathologic markers in sporadic amyotrophic lateral sclerosis2007

    • Author(s)
      Jiang YM, Yamamoto M, Tanaka F, Ishigaki S, Katsuno M, Adachi H, Niwa J, Doyu M, Yoshida M, Hashizume Y, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 617-627

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] In vitro and in silico analysis reveals an efficient algorithm to predict the splicing consequences of mutations at the 5'splice sites2007

    • Author(s)
      Sahashi K, Masuda A, Matsuura T, Shinmi J, Zhang Z, Takeshima Y, Matsuo M, Sobue G, Ohno K
    • Journal Title

      Nucleic Acids Res 35

      Pages: 5995-6003

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Altered venous capacitanec as a cause of postprandial hypotension in multiple system atrophy2007

    • Author(s)
      Takamori M, Hirayama M, Kobayashi R, Ito H, Mabuchi N, Nakamura T, Hori N, Koike Y, Sobue G
    • Journal Title

      Clin Auton Res 17

      Pages: 20-25

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Nonmyelinating Schwann cell involvement with well-preserved unmyelinated axons in Charco-Matie-Tooth disease type 1A2007

    • Author(s)
      Koike H, Iijima M, Mori K, Yamamoto M, Hattori N, Katsuno M, Tanaka F, Watanabe H, Doyu M, Yoshikawa H, Sobue G
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 1027-1036

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene Expressions Specifically Detected in Motor Neurons (Dynactin, 1, Early Growth Response 3, Acetyl-CoA Transporter, Death Receptor 5, and Cyclin C) Differentially Correlate to Pathologic Markers in Sporadic Amyotrophic Lateral Sclerosis2007

    • Author(s)
      Jiang, YM, Yamamoto, M, Tanaka, F, Ishigaki, S, Katsuno, M, Adachi, H, Doyu M, Yoshida, M, Hashizume, Y, Sobue, G
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 617-627

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18599002
  • [Journal Article] Scientific highlights. 17th International Symposium on ALS/MND Yokohama, Japan, November 30, 2006 through December 2, 20062007

    • Author(s)
      Sobue G
    • Journal Title

      Amyotroph Lateral Scler 2

      Pages: 121-123

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Neuropathol Appl Neurobiol 33

      Pages: 135-151

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD12007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Biol Chem 282

      Pages: 28087-28095

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Genetic evidence for a protective role for heat shock factor 1 and heat shock protein 70 against colitis2007

    • Author(s)
      Tanaka K, Namba T, Arai Y, Fujimoto M, Adachi H, Sobue G, Takeuchi K, Nakai A, Mizushima T
    • Journal Title

      J Biol Chem 282

      Pages: 23240-23252

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Hypophosphataemic neuropathy in a patient who received intravenous hyperalimentation2007

    • Author(s)
      Iguchi Y, Mori K, Koike H, Mano K, Goto Y, Kato T, Nakano T, Furukawa D, Sobue G
    • Journal Title

      Neurol Neurosurg Psychiatry 78

      Pages: 1159-1160

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Intravenous immunoglobulin therapy markedly ameliorates muscle weakness and severe pain in proximal diabetic neuropathy2007

    • Author(s)
      Kawagashira Y, Watanabe H, Oki Y, Iijima M, Koike H, Hattori N, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 78

      Pages: 899-901

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Widespread spinal cord invovement in progressive supranuclear palsy2007

    • Author(s)
      Iwasaki Y, Yoshida M. Hashizume Y, Hattori M, Aiba I, Sobue G
    • Journal Title

      Neuropathology 27

      Pages: 331-340

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Congenial fibrosis of the extraocular muscles (CFEOM) sydrome associated with progressive cerebellar ataxia2007

    • Author(s)
      Yoshida K, Okano T, Hoshi K, Yahikozawa H, Suzuki K, Bannno H, Tamura T, Sobue G, Ikeda S
    • Journal Title

      AM J Med Genet 143A

      Pages: 1494-1501

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expressions specifically detected in motor neurons (dynactin l, early growth response 3, Acetyl-CoA transporter, death receptor 5, and cyclin C) differentially correlate to athologic markers in sporadic amyotrophic lateral sclerosis2007

    • Author(s)
      Jiang Y, Yamamoto M, Tanaka F, Ishigaki S, Katsuno M, Adachi H, Niwia J, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Neuropathol Exp Neurol 66

      Pages: 617-627

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      Neuropathol Appl Neurobiol 33

      Pages: 135-151

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G
    • Journal Title

      Neurobiol of Dis 25

      Pages: 331-341

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G
    • Journal Title

      Neurobiol of Dis 25

      Pages: 331-341

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Genetic evidence for a protective role for heat shock factor l and heat shock protein 70 against colitis2007

    • Author(s)
      Tanaka K, Namba T, Arai Y, Fujimoto M, Adachi H, Sobue G, Takeuchi K, Nakai A, Mizushima T
    • Journal Title

      J Biol Chem 282

      Pages: 23240-23252

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] In vitro and in silico analysis reveals an efficient algorithm to predict the splicing consequences of mutations at the 5'splice sites2007

    • Author(s)
      Sahashi K, Masuda A, Matsuura T, Shinmi J, Zhang Z, Takeshima Y, Matsuo M, Sobue G, Ohno K
    • Journal Title

      Nucleic Acids Res 35

      Pages: 5995-6003

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G.
    • Journal Title

      Neurobiol Dis 25

      Pages: 331-341

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Ataxic vs painful form of paraneoplastic neuropathy2007

    • Author(s)
      Oki Y, Koike H, Iijima M, Mori K, Hattori N, Katsuno M, Nakamura T, Hirayama M, Tanaka F, Shiraishi M, Yazaki S, Nokura K, Yamamoto H, Sobue G
    • Journal Title

      Neurology 69

      Pages: 564-572

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Recent progress in alcoholic and thiamine-deficiency neuropathy2007

    • Author(s)
      Koike H, Oki Y, Iijima M, katsuno M, Hattori N, Sobue G
    • Journal Title

      Current trend in Neurology 2

      Pages: 79-85

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Therapeutic strategies for spinal and bulbar muscular atrophy (SBMA)2007

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Takeuchi Y, Minamiyama M, Waza M, Adachi H, Tanaka F, Sobue G
    • Journal Title

      Drug Future 32

      Pages: 907-917

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Nonmyelinating Schwann cell involvement with well-preserved unmyelinated axons in Charcot-Marie-Tooth disease type 1A2007

    • Author(s)
      Koike H, Iijima M, Mori K, Yamamoto M, Hattori N, Katsuno M, Tanaka F, Watanabe H, Doyu M, Yoshikawa H, Sobue G
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 1027-36

    • Data Source
      KAKENHI-PROJECT-19590986
  • [Journal Article] Intravenous immunoglobulin therapy markedly ameliorates muscle weakness and severe pain in proximal diabetic neuropathy2007

    • Author(s)
      Kawagashira Y, Watanabe H, Oki Y, Iijima M, Koike H, Hattori N, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 78

      Pages: 899-901

    • Data Source
      KAKENHI-PROJECT-19590986
  • [Journal Article] ASC-J9 ameliorates spinal and bulbar muscular atrophy phenotype via degradation of androgen receptor2007

    • Author(s)
      Yang, Z., Chang, Y. J., Yu, I. C., Yeh, S., Wu, C.C., Miyamoto, H., Merry, D. E., Sobue, G., Chen, L. M., Chang, S.S. & Chang, C
    • Journal Title

      Nat. Med 13

      Pages: 348-353

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi, H, Waza, M, Katsuno, M, Tanaka, F, Doyu, M, Sobue, G
    • Journal Title

      Neuropathol Appl Neurobiol 33

      Pages: 135-151

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18599002
  • [Journal Article] CHIP overexpression reduces mutant androgen receptor protein and ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurosci 27

      Pages: 5115-5126

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] CHIP Overexpression Reduces Mutant Androgen Receptor Protein and Ameliorates Phenotypes of the Spinal and Bulbar Muscular Atrophy Transgenic Mouse Model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J. Neurosci 27

      Pages: 5115-5126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Nonmyelinating Schwann cell involvement with well-preserved unmyelinated axons in Charcot-Marie-Tooth disease type 1A2007

    • Author(s)
      Koike, H., Iijima, M., Mori, K., Yamamoto, M., Hattoi-i, N., Katsuno, M., Tanaka, F., Watanabe, H., Doyu, M., Yoshikawa, H., Sobue, G
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 1027-36

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18390262
  • [Journal Article] Dobutamine stress test unmasks cardiac sympathetic denervation in Parkinson's disease2007

    • Author(s)
      Nakamura T, Hirayama M, Ito H, Takamori M, Hamada K, Takeuchi S, Watanabe H, Koike Y, Sobue G
    • Journal Title

      J Neurol Sci 263

      Pages: 133-138

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Hypophosphataemic neuropathy in a patient who received intravenous hyperalimentation2007

    • Author(s)
      Iguchi Y, Mori K, Koike H, Mano K, Goto Y, Kato T, Nakano T, Furukawa D, Sobue G
    • Journal Title

      Neurol Neurosurg Psychiatry 78

      Pages: 1159-1160

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Recent progress in alcoholic and thiamine-deficiency neuropathy2007

    • Author(s)
      Koike H, Oki Y, Iijima M, katsuno M, Hattori N, Sobue G
    • Journal Title

      Current trend in Neurology 2

      Pages: 79-85

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] CHIP overexpression reduces the mutant AR protein and ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2007

    • Author(s)
      Adachi, H, Waza, M, Tokui, K, Katsuno, M, Minamiyama, M, Tanaka, F, Doyu, M, Sobue, G
    • Journal Title

      J Neurosci 27

      Pages: 5115-5126

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18599002
  • [Journal Article] ASC-J9 ameliorates spinal and bulbar muscular atrophy phenotype via degradation of androgen receptor2007

    • Author(s)
      Yang Z, Chang YJ, Yu IC, Yeh S, Wu CC, Miyamoto H, Merry DE, Sobue G, Chen LM, Chang SS, Chang C
    • Journal Title

      Nat Med 13

      Pages: 348-353

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Scientific highlights. 17th International Symposium on ALS/MND Yokohama, Japan, November 30, 2006 through December 2, 20062007

    • Author(s)
      Sobue G.
    • Journal Title

      Amyotroph Lateral Scler 8

      Pages: 121-123

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] ASC-J9 ameliorates spinal and bulbar muscular atrophy phenotype via degradation of androgen receptor2007

    • Author(s)
      Yang Z, Chang YJ, Yu IC, Yeh S, Wu CC, Miyamoto H, Merry DE, Sobue G, Chen LM, Chang SS, Chang C.
    • Journal Title

      Nauret Med 13

      Pages: 348-353

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Pyramidal tract degeneration in sporadic Creutzfeldt-Jakob disease2007

    • Author(s)
      Iwasaki Y, Yoshida M, Hashizume Y, Kitamoto T, Sobue G
    • Journal Title

      Neuropathology 27

      Pages: 434-441

    • NAID

      10021236410

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis.2007

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G.
    • Journal Title

      Ann N Y Acad Sci. 1086

      Pages: 1-10

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] ASC-J9 ameliorates spinal and bulbar muscular atrophy phenotype via degradation of androgen receptor2007

    • Author(s)
      Yang Z, Chang YJ, Yu IC, Yeh S, Wu CC, Miyamoto H, Merry DE, Sobue G, Chen LM, Chang SS, Chang C
    • Journal Title

      Nat Med 13

      Pages: 348-353

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SODI proteins and reduce their cellular toxicity2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G
    • Journal Title

      Neurobiol Dis 25

      Pages: 331-241

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Congenial fibrosis of the extraocular muscles (CFEOM) sydrome associated with progressive cerebellar ataxia2007

    • Author(s)
      Yoshida K, Okano T, Hoshi K, Yahikozawa H, Suzuki K, Bannno H, Tamura T, Sobue G, Ikeda S
    • Journal Title

      AM J Med Genet 143A

      Pages: 1494-1501

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Neuropathol. Appl. Neurobiol 33

      Pages: 135-151

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Gene expressions specifically detected in motor neurons (dynactin 1, early growth response 3, acetyl-CoA transporter, death receptor 5, and cyclin C) differentially correlate to pathologic markers in sporadic amyotrophic lateral sclerosis2007

    • Author(s)
      Jiang YM, Yamamoto M, Tanaka F, Ishigaki S, Katsuno M, Adachi H, Niwa J, Doyu M, Yoshida M, Hashizume Y, Sobue G.
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 617-627

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Scientific highlights. 17th International Symposium on ALS/MND Yokohama, Japan, November 30, 2006 through December 2, 20062007

    • Author(s)
      Sobue G
    • Journal Title

      Amyotroph Lateral Scler (2)

      Pages: 121-123

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of famlial amyotrophic lateral sclerosis-linked mutant SOD1.2007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Biol Chem. 282

      Pages: 28087-28095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G.
    • Journal Title

      Neurobiol Dis 25

      Pages: 331-341

    • Data Source
      KAKENHI-PROJECT-19390238
  • [Journal Article] Enhanced aquaporin-4 immunoreactivity in sporadic Creutzfeldt-Jakob disease2007

    • Author(s)
      Iwasaki Y, Mimuro M, Yoshida M. Hashizume Y, Ito M, Kitamoto T, Wakayama Y, Sobue G
    • Journal Title

      Neuropathology 27

      Pages: 314-323

    • NAID

      10021235965

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD12007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Biol Chem 282

      Pages: 28087-28095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Pathogenesis and molecular targeted therapy of spinal and bulbar muscular atrophy2007

    • Author(s)
      Adachi H, Waza M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Neuropathol Appl Neurobiol 33

      Pages: 135-151

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expressions specifically detected in motor neurons(dynactin 1, early growth response 3, acetyl-CoA transporter, death receptor 5, and cyclin C)differentially correlate to pathologic markers in sporadic amyotrophic lateral sclerosis.2007

    • Author(s)
      Jiang YM, Yamamoto M, Tanaka F, shigaki S, Katsuno M, Adachi H, Niwa J, Doyu M, Yoshida M, Hashizune Y, Sobue G.
    • Journal Title

      J Neuropathol Exp Neural. 66

      Pages: 617-627

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Dobutamine stress test unmasks cardiac sympathetic denervation in Parkinson's disease2007

    • Author(s)
      Nakamura T, Hirayama M, Ito H, Takamori M, Hamada K, Takeuchi S, Watanabe H, Koike Y, Sobue G
    • Journal Title

      J Neurol Sci 263

      Pages: 133-138

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD12007

    • Author(s)
      Niwa J, Yamada S, Ishigaki S, Sone J, Takahashi M, Katsuno M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 282

      Pages: 28087-28095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity.2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G.
    • Journal Title

      Neurobiol Dis. 25

      Pages: 331-41

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SOD1 proteins and reduce their cellular toxicity.2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takaiashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G.
    • Journal Title

      Neurobiol Dis. 25

      Pages: 331-341

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Journal Article] Widespread Spinal cord invovement in progressive in supranuclear plasy2007

    • Author(s)
      Iwasaki Y, Yoshida M. Hashizume Y, Hattori M, Aiba I, Sobue G
    • Journal Title

      Neuropathology 27

      Pages: 331-340

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Altered venous capacitance as a cause of postprandial hypotension in multiple system atrophy2007

    • Author(s)
      Takamori M, Hirayama M, Kobayashi R, Ito H, Mabuchi N, Nakamura T, Hori N, Koike Y, Sobue G
    • Journal Title

      Clin Auton Res 17

      Pages: 20-25

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Reduces Mutant Androgen Receptor protein and Ameliorates Phenotypes of the Spinal and Bulbar Muscular Atrophy Transgenic Mouse Model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Minamiyama M, Tanak F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 27

      Pages: 5115-5126

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] ASC-J9 ameliorates spinal and bulbar muscular atrophy phenotype via degradation of androgen receptor2007

    • Author(s)
      Yang, Z., Chang, Y.J., Yu, I.C., Yeh, S., Wu, C.C., Miyamoto, H., Merry, D.E., Sobue, G., Chen, L.M, Chang, S.S.& Chang, C
    • Journal Title

      Nat. Med 13

      Pages: 348-353

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Ataxic vs painful form of paraneoplastic neuropathy2007

    • Author(s)
      Oki, Y., Koike, H., Iijima, M., Mori, K., Hatlori, N., Katsuno, M., Nakamura, T., Hirayama, M., Tanaka, F., Shiraishi, M., Yazaki, S., Nokura, K., Yamamoto, H., Sobue, G
    • Journal Title

      J Neurol Neurosurg Psychiatry 78

      Pages: 899-901

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18390262
  • [Journal Article] Dorfin-CHIP chimeric proteins potently ubiquitylate and degrade familial ALS-related mutant SODI proteins and reduce their cellular toxicity2007

    • Author(s)
      Ishigaki S, Niwa J, Yamada S, Takahashi M, Ito T, Sone J, Doyu M, Urano F, Sobue G
    • Journal Title

      Neurobiol Dis 25

      Pages: 331-241

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Nonmyelinating Schwann cell involvement with well-preserved unmyelinated axons in Charco-Matie-Tooth disease type 1A2007

    • Author(s)
      Koike H, Iijima M, Mori K, Yamamoto M, Hattori N, Katsuno M, Tanaka F, Watanabe H, Doyu M, Yoshikawa H, Sobue G
    • Journal Title

      J Neuropathol Exp Neurol 66

      Pages: 1027-1036

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Journal Article] Intravenous immunoglobulin therapy markedly ameliorates muscle weakness and severe pain in proximal diabetic neuropathy2007

    • Author(s)
      Kawagashira Y, Watanabe H, Oki Y, Iijima M, Koike H, Hattori N, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 78

      Pages: 899-901

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Usefulness of combined fractional anisotropy and apparent diffusion coefficient values for detection of involvement in multiple system atrophy2007

    • Author(s)
      Ito M, Watanabe H, Kawai Y, Atsuta N, Tanaka F, Naganawa S, Fukatsu H, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 78

      Pages: 722-728

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Therapeutic strategies for spinal and bulbar musculara atrophy (SBMA)2007

    • Author(s)
      Katsuno M, Bannno H, Suzuki K, Takeuchi Y, Minamiyama M, Waza M, Adachi H, Tanaka F, Sobue G
    • Journal Title

      Drugns of the Future 32

      Pages: 907-917

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol in press

    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular-targeted therapy against disease-causing protein2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Alleviating neurodegeneration by an anticancer agent : an Hsp90 inhibitor (17-AAG)2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Sobue G
    • Journal Title

      Ann NY Acad Sci 1086

      Pages: 21-34

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 1-10

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Clinicopathologic features of nonsystemic vasculitic neuropathy and microscopic polyangiitis-associated neuropathy : a comparative study.2006

    • Author(s)
      Sugiura M, Koike H, Iijima M, Mori K, Hattori N, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Neurol Sci 241

      Pages: 31-37

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular-targeted therapy against disease-causing protein.2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular targeted therapy against disease-causing protein.2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med (in press)

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann NY Acad Sci 1086

      Pages: 1-10

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Underediting of GluR2 mRNA, a neuronal death inducing molecular change in sporadic ALS, does not occur in motor neurons in ALS1 or SBMA2006

    • Author(s)
      Kawahara Y, Sun H, Ito K, Hideyama T, Aoki M, Sobue G, Tsuji S, Kwak S
    • Journal Title

      Neurosci Res 54

      Pages: 11-14

    • NAID

      10020613977

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Underediting of GIuR2 mRNA, a neuronal death inducing molecular change in sporadic ALS, does not occur in motor neurons in ALS1 or SBMA.2006

    • Author(s)
      Kawahara Y, Sun H, Ito K, Hideyama T, Aoki M, Sobue G, Tsuji S, Kwak S
    • Journal Title

      Neurosci Res 54

      Pages: 11-14

    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker.2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Disease progression of human SOD1 (G93A) transgenic ALS model rats.2006

    • Author(s)
      Matsumoto A, Okada Y, Nakamichi M, Nakamura M, Toyama Y, Sobue G, Nagai M, Aoki M, Itoyama Y, Okano H
    • Journal Title

      J Neurosci Res 83

      Pages: 119-133

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis.2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann NY Acad Sci 1086

      Pages: 1-10

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Underediting of GlluR2 mRNA, a neuronal death inducing molecular change in sporadic ALS, dose not occur in motor neurons in ALS1 or SBMA2006

    • Author(s)
      Kawahara Y, Sun H, Ito K, Hideyama T, Aoki M, Sobue G, Tsuji S, Kwak S
    • Journal Title

      Neurosci Res 54

      Pages: 11-14

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Alleviating neurodegeneration by an anticancer agent : an Hsp90 inhibitor (17-AAG)2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Sobue G
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 21-34

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Intravenous immunoglobulin treatmet in painful sensory neuropathy without sensory ataxia associate with Sjogren's syndrome.2006

    • Author(s)
      Kizawa M, Mori K, Iijima M, Koike H, Hattori N, Sobue G
    • Journal Title

      J Neurol Neurosura Psychiatry 77

      Pages: 967-969

    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Pathogenesis, animal models and therapeutics in Spinal and bulbar muscular atrophy (SBMA)2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol 200

      Pages: 8-18

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Myopathy in thiamine deficiency : analysis of a case.2006

    • Author(s)
      Koike H, Watanabe H, Inukai A, Iijima M, Mori K, Hattori N, Sobue G.
    • Journal Title

      Neurol Sci 249

      Pages: 175-179

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 1-10

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Natural history of spinal and bulbar muscular atrophy (SBMA) : a study of 223 Japanese patients.2006

    • Author(s)
      Atsuta N, Watanabe H, Ito M, Banno H, Sobue G, et al.
    • Journal Title

      Brain 129(Pt 6)

      Pages: 1446-1455

    • Data Source
      KAKENHI-PROJECT-18390262
  • [Journal Article] Calcium-sensing receptor ubiquitination and degradation mediated by the E3 ubiquitin ligase dorfin.2006

    • Author(s)
      Huang Y, Niwa J, Sobue G, Breitwieser GE
    • Journal Title

      J Biol Chem. 281

      Pages: 11610-11617

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Underediting of GluR2 mRNA, a neuronal death inducing molecular change in sporadic ALS, does not occur in motor neurons in ALS1 or SBMA.2006

    • Author(s)
      Kawahara Y, Sun H, Ito K, Hideyama T, Aoki M, Sobue G, Tsuji S, Kwak S
    • Journal Title

      Neurosci Res 54

      Pages: 11-14

    • NAID

      10020613977

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol (in press)

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Disease progression of human SOD1 (G93A) transgenic ALS model rats.2006

    • Author(s)
      Matsumoto A, Okada Y, Nakamichi M, Nakamura M, Toyama Y, Sobue G, Nagai M, Aoki M, Itoyama Y, Okano H
    • Journal Title

      J Neurosci Res 83

      Pages: 119-133

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Archaeal proteasomes effectively degrade aggregation-prone proteins and reduce cellular toxicities in mammalian cells.2006

    • Author(s)
      Yamada S, Niwa J, Ishigaki S, Takahashi M, Ito T, Sone J, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 281

      Pages: 23842-23851

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis.2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G.
    • Journal Title

      Ann N Y Acad Sci. 1086

      Pages: 1-10

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Underediting of GluR2 mRNA, a neuronal death inducing molecular change in sporadic ALS, does not occur in motor neurons in ALS1 or SBMA.2006

    • Author(s)
      Kawahara Y, Sun H, Ito K, Hideyama T, Aoki M, Sobue G, Tsuji S, Kwak S
    • Journal Title

      Neurosci Res 54

      Pages: 11-14

    • NAID

      10020613977

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Natural history of spinal and bulbar muscular atrophy (SBMA) : A study of 223 Japanese patients.2006

    • Author(s)
      Atsuta N, Watanabe H, Ito M, Banno H, Suzuki K, Katsuno M, Tanaka F, Tamakoshi A, Sobue G
    • Journal Title

      Brain 129

      Pages: 1446-1455

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Reversible disruption of dynactin 1-mediated retrograde axonal transport in polyglutamine-induced motor neuron degeneration2006

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Tokui K, Banno H, Suzuki K, Onoda Y, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 26

      Pages: 12106-12117

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Archaeal proteasomes effectively degrade aggregation-prone proteins and reduce cellular toxicities in mammalian cells2006

    • Author(s)
      Yamada S, Niwa J, Ishigaki S, Takahashi M, Ito T, Sone J, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 281

      Pages: 23842-23851

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Intravenous immunoglobulin treatment in painful sensory neuropathy without sensory ataxia associated with Sjogren's syndrome.2006

    • Author(s)
      Kizawa M, Mori K, Iijima M, Koike H, Hattori N, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry 77

      Pages: 967-969

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] 運動ニューロン病とユビキチン.2006

    • Author(s)
      丹羽 淳一, 祖父江 元
    • Journal Title

      蛋白質核酸酵素 51

      Pages: 1423-1427

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Alcoholic neuropathy.2006

    • Author(s)
      Koike H, Sobue G.
    • Journal Title

      Curr Opin Neurol 19

      Pages: 481-486

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Disease progression of human SOD1 (G93A) transgenic ALS model rats.2006

    • Author(s)
      Matsumoto A, Okada Y, Nakamichi M, Nakamura M, Toyama Y, Sobue G, Nagai M, Aoki M, Itoyama Y, Okano H
    • Journal Title

      J Neurosci Res 83

      Pages: 119-133

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Clinicopathologic features of nonsystematic vasculitic neuropathy and microscopic polyangiitis-associated neuropathy : a comparative study.2006

    • Author(s)
      Sugiura M, Koike H, Iijima M, Mori K, Hattori N, Katsuno M, Tanaka F, Sobue G
    • Journal Title

      J Nuerol Sci 241

      Pages: 31-37

    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis.2006

    • Author(s)
      Tanaka F, Niwa J, Ishigaki S, Katsuno M, Waza M, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Ann N Y Acad Sci. 1086

      Pages: 1-10

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Alleviating neurodegeneration by an anticancer agent : an Hsp90 inhibitor (17-AAG).2006

    • Author(s)
      G Sobue et al.
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 21-34

    • Data Source
      KAKENHI-PROJECT-18659258
  • [Journal Article] Calcium sensing receptor ubiquitination and degradation mediated by the E3 uboquitin ligase dorfin2006

    • Author(s)
      Huang Y, Niwa J, Sobue G, Breitwieser GE
    • Journal Title

      J Biol Chem 281

      Pages: 11610-11617

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Calcium sensing receptor ubiquitination and degradation mediated by the E3 uboquitin ligase dorfin2006

    • Author(s)
      Huang Y, Niwa J, Sobue G, Breitwieser GE
    • Journal Title

      J Biol Chem 281

      Pages: 11610-11617

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Underediting of GluR2 mRNA, a neuronal death inducing molecular change in sporadic ALS, does not occur in motor neurons in ALS1 or SBMA.2006

    • Author(s)
      Kawahara Y, Sun H, Ito K, Hideyama T, Aoki M, Sobue G, Tsuji S, Kwak S
    • Journal Title

      Neurosci Res 54

      Pages: 11-14

    • NAID

      10020613977

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : amolecular-targeted therapy against disease-causing protein2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular targeted therapy against disease-causing protein.2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med (in press)

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol (in press)

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular-targeted therapy against disease-causing protein2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med 84

      Pages: 635-646

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol (in press)

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker.2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Alcoholic neuropathy.2006

    • Author(s)
      Koike H, Sobue G
    • Journal Title

      Curr Opin Neurol 19

      Pages: 481-486

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Pathogenesis, animal models and therapeutics in spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol (in press)

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Myopathy in thiamine deficiency : analysis of a case.2006

    • Author(s)
      Koike H, Watanabe H, Inukai A, Iijima M, Mori K, Hattori N, Sobue G
    • Journal Title

      J Neurol Sci 249

      Pages: 175-179

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Calcium-sensing receptor ubiquitination and degradation mediated by the E3 ubiquitin ligase dorfin.2006

    • Author(s)
      Huang Y, Niwa J, Sobue G, Breitwieser GE.
    • Journal Title

      J Biol Chem. 281

      Pages: 11610-7

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Underediting of GluR2 mRNA, a neuronal death inducing molecular change in sporadic ALS, does not occur in motor neurons in ALS 1 or SBMA.2006

    • Author(s)
      Kawahara Y, Sun H, Ito K, Hideyama T, Aoki M, Sobue G, Tsuji S, Kwak S
    • Journal Title

      Neurosci Res 54

      Pages: 11-14

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Alleviating neurodegeneration by an anticancer agent : an Hsp90 inhibitor (17-AAG).2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Sobue G
    • Journal Title

      Ann NY Acad Sci 1086

      Pages: 21-34

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Pathogenesis, animal models and therapeutics in Spinal and bulbar muscular atrophy (SBMA).2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol 200

      Pages: 8-18

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Disease progression of human SOD1 (G93A) transgenic ALS model rats.2006

    • Author(s)
      Matsumoto A, Okada Y, Nakamichi M, Nakamura M, Toyama Y, Sobue G, Nagai M, Aoki M, Itoyama Y, Okano H
    • Journal Title

      J Neurosci Res 83

      Pages: 119-133

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Alleviating neurodegeneration by an anticancer agent : an Hsp90 inhibitor (17-AAG)2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Sobue G
    • Journal Title

      Ann N Y Acad Sci 1086

      Pages: 21-34

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Reversible disruption of dynactin 1-mediated retrograde axonal transport in polyglutamine-induced motor neuron degeneration2006

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Tokui K, Banno H, Suzuki K, Onoda Y, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 26

      Pages: 12106-12117

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Calcium sensing receptor ubiquitination and degradation mediated by the E3 ubiquitin ligase dorfin.2006

    • Author(s)
      Huang Y, Niwa J, Sobue G, Breitwieser GE
    • Journal Title

      J Biol Chem 281

      Pages: 11610-11617

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Archaeal proteasomes effectively degrade aggregation-prone proteins and reduce cellular toxicities in mammalian cells.2006

    • Author(s)
      Yamada S, Niwa J, Ishigaki S, Takahashi M, Ito T, Sone J, Doyu M, Sobue G.
    • Journal Title

      J Biol Chem.

      Pages: 28123842-51

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Motor neuron disease and ubiquitin-proteasome system dysfunction2006

    • Author(s)
      Niwa J, Sobue G.
    • Journal Title

      Tanpakushitsu Kakusan Koso. 51

      Pages: 1423-7

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Natural history of spinal and bulbar muscular atrophy (SBMA) : A study of 223 Japanes patients2006

    • Author(s)
      Atsuta N, Watanabe H, Ito M, Banno H, Suzuki K, Katsuno M, Tanaka F, Tamakoshi A, Sobue G
    • Journal Title

      Brain 129

      Pages: 1446-1455

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker.2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Gene expression profiling toward understanding of ALS pathogenesis.2006

    • Author(s)
      G Sobue et al.
    • Journal Title

      J Neurosci. 26・47

      Pages: 12106-12117

    • Data Source
      KAKENHI-PROJECT-18659258
  • [Journal Article] Pathogenesis, animal models and therapeutics in Spinal and bulbar muscular atrophy (SBMA)2006

    • Author(s)
      Katsuno M, Adachi H, Waza M, Banno H, Suzuki K, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Exp Neurol 200

      Pages: 8-18

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Mutant androgen receptor accumulation in spinal and bulbar muscular atrophy scrotal skin : A pathogenic marker.2006

    • Author(s)
      Banno H, Adachi H, Katsuno M, Suzuki K, Atsuta N, Watanabe H, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Ann Neurol 59

      Pages: 520-526

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Archaeal proteasomes effectively degrade aggregation-prone proteins and reduce cellular toxicities in mammalian cells.2006

    • Author(s)
      Yamada S, Niwa J, Ishigaki S, Takahashi M, Ito T, Sone J, Doyu M, Sobue G
    • Journal Title

      J Biol Chem. 281

      Pages: 23842-23851

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Intravenous immunoglobulin treatment in painful sensory neuropathy without sensory ataxia associated with Sjogren's syndrome.2006

    • Author(s)
      Kizawa M, Mori K, Iijima M, Koike H, Hattori N, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 77

      Pages: 967-969

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular-targeted therapy against disease-causing protein.2006

    • Author(s)
      G Sobue et al.
    • Journal Title

      J Mol Med. 84・8

      Pages: 635-646

    • Data Source
      KAKENHI-PROJECT-18659258
  • [Journal Article] Reversible disruption of dynactin 1-mediated retrograde axonal transport in polyglutamine-induced motor neuron degeneration.2006

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Waza M, Tokui K, Banno H, Suzuki K, Onoda Y, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurosci 26

      Pages: 12106-12117

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Modulation of Hsp90 function in neurodegenerative disorders : a molecular targeted therapy against disease-causing protein.2006

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Mol Med (in press)

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Archaeal proteasomes effectively degrade aggregation-prone proteins and reduce cellular toxicities in mammalian cells2006

    • Author(s)
      Yamada S, Niwa J, Ishigaki S, Takahashi M, Ito T, Sone J, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 281

      Pages: 23842-23851

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Natural history of spinal and bulbar muscular atrophy (SBMA) : A study of 223 Japanese patients2006

    • Author(s)
      Atsuta N, Watanabe H, Ito M, Banno H, Suzuki K, Katsuno M, Tanaka F, Tamakoshi A, Sobue G
    • Journal Title

      Brain 129

      Pages: 1446-1455

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2006

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci USA 102

      Pages: 16801-16806

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Calcium sensing receptor ubiquitination and degradation mediated by the E3 ubiquitin ligase dorfin.2006

    • Author(s)
      Huang Y, Niwa J, Sobue G, Breitwieser GE
    • Journal Title

      J Biol Chem. (in press)

    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Clinicopathologic features of nonsystemic vasculitic neuropathy and microscopic polyangiitis-associated neuropathy : a comparative study.2006

    • Author(s)
      Sugiura M, Koike H, Iijima M, Mori K, Hattori N, Katsuno M, Tanaka F, Sobue G.
    • Journal Title

      J Neurol Sci 241

      Pages: 31-37

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Underediting of GluR2 mRNA, a neuronal death inducing molecular change in sporadic ALS, does not occur in motor neurons in ALS1 or SBMA.2006

    • Author(s)
      Kawahara Y, Sun H, Ito K, Hideyama T, Aoki M, Sobue G, Tsuji S, Kwak S
    • Journal Title

      Neurosci Res 54

      Pages: 11-14

    • NAID

      10020613977

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Widespread nuclear and cytoplasmic accumulation of mutant androgen receptor in SBMA patients.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Thiamine deficiency neuropathy in Japan.2005

    • Author(s)
      Haruki Koike, Masahiro Iijima, Keiko Mori, Naoki Hattori, Gen Sobue.
    • Journal Title

      Recent Advances in Neurology 2

      Pages: 45-55

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci USA 102

      Pages: 16801-16806

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Interferon alfa treatment for Sjogren syndrome associated neuropathy.2005

    • Author(s)
      Yamada S, Mori K, Matsuo K, Inukai A, Kawagashira Y, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 76

      Pages: 576-578

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] The wide spectrum of clinical manifestations in Sjogren's syndrome-associated neuropathy.2005

    • Author(s)
      Mori K, Iijima M, Koike H, Hattori N, Tanaka F, Watanabe H, Katsuno M, Fujita A, Aiba I, Ogata A, Saito T, Asakura K, Yoshida M, Hirayama M, Sobue G
    • Journal Title

      Brain 128

      Pages: 2518-2534

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration.2005

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Sang C, Tanaka F, Inukai A, Doyu M, Sobue G
    • Journal Title

      Nature Med 11

      Pages: 1088-1095

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Clinical and electrophysiologic correlates of IVIg responsiveness in CIDP.2005

    • Author(s)
      Iijima M, Yamamoto M, Hirayama M, Tanaka F, Katsuno M, Mori K, Koike H, Hattori N, Arimura K, Nakagawa M, Yoshikawa H, Hayasaka K, Onodera O, Baba M, Yasuda H, Saito T, Nakazato M, Nakashima K, Kira J, Kaji R, Oka N, Sobue G
    • Journal Title

      Neurology 64

      Pages: 1471-1475

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Clinical and electrophysiologic correlates of IVIg responsiveness in CIDP.2005

    • Author(s)
      Iiijima M, Yamamoto M, Hirayama M, Tanaka F, Katsuno M, Mori K, Koike H, Nattori N, Arimura K, Nakagawa M, Yoshikawa H, Hayasaka K, Onodera O, Baba M, Yasauda H, Saito T, Nakazato M, Nakashima K, Kira J, Kaji R, Oka N, Sobue G.
    • Journal Title

      Neurology 64

      Pages: 1471-1475

    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] The wide spectrum of clinical manifestations in Sjogren's syndrome-associated neuropathy.2005

    • Author(s)
      Mori K, Iijima M, Koike H, Hattori N, Tanaka F, Watanabe H, Katsuno M, Fujita A, Aiba I, Ogata A, Saito T, Asakura K, Yoshida M, Hirayama M, Sobue G.
    • Journal Title

      Brain 128

      Pages: 2518-2534

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Widespread active inflammatory lesions in a case of HTLV-I-associated myelopathy lasting 29 years.2005

    • Author(s)
      Iwasaki Y, Sawada K, Aiba I, Mukai E, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Acta Neuropathol 108

      Pages: 546-551

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Neuronal intranuclear hyaline inclusion disease showing motor-sensory and automatic neuropathy.2005

    • Author(s)
      Sone J, Hishikawa N, Koike H, Hattori N, Hirayama M, Nagamatsu M, Yamamoto M, Tanaka F, Yoshida M, Hashizume Y, Imamura H, Yamada E, Sobue G.
    • Journal Title

      Neurology 65

      Pages: 1538-1543

    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Clinical and electrophysiologic correlates of IVIg responsiveness in CIDP.2005

    • Author(s)
      Iijima M, Yamamoto M, Hirayama M, Tanaka F, Katsuno M, Mori K, Koike H, Hattori N, Arimura K, Nakagawa M, Yoshikawa H, Hayasaka K, Onodera O, Baba M, Yasuda H, Saito T, Nakazato M, Nakashima K, Kira J, Kaji R, Oka N, Sobue G
    • Journal Title

      Neurology 64

      Pages: 1471-1475

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Widespread nuclear and cytoplasmic mutant androgen receptor accum ulation in spinal and bulbar muscular atrophy.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Waza M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] The wide spectrum of clinical manifestations in Sjogren's syndrome-associated neuropathy.2005

    • Author(s)
      Mori K, Iijima M, Koike H, Hattori N, Tanaka F, Watanabe H, Katsuno M, Fujita A, Aiba I, Ogata A, Saito T, Asakura K, Yoshida M, Hirayama M, Sobue G
    • Journal Title

      Brain 128

      Pages: 2158-2535

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease2005

    • Author(s)
      Katsuno, M., Sang, C., Adachi, H., Minamiyama, M., Waza, M., Tanaka, F., Doyu, M., Sobue, G.
    • Journal Title

      Proc. Natl. Acad. Sci. U.S.A. 102

      Pages: 16801-16806

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration.2005

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Sang C, Tanaka F, Inukai A, Doyu M, Sobue G
    • Journal Title

      Nature Med 11

      Pages: 1088-1095

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Progression and prognosis in pure autonomic failure (PAF) : comparison with multiple system atrophy.2005

    • Author(s)
      Mabuchi N, Hirayama M, Koike Y, Watanabe H, Ito H, Kobayashi R, Hamada K, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 76

      Pages: 947-952

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Age associated axonal features in HNPP with l7p11.2 deletion in Japan.2005

    • Author(s)
      Koike H, Hirayama M, Yamamoto M, Ito H, Hattori N, Umehara F, Arimura K, Ikeda S, Ando Y, Nakazato M, Kaji R, Hayasaka K, Nakagawa M, Sakoda S, Masumura K, Onodera O, Baba M, Yasuda H, Saito T, Kira J, Nakashima K, Oka N, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 76

      Pages: 1109-1114

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Thiamine-deficiency neuropathy in Japan2005

    • Author(s)
      Koike H, Iijima M, Mori K, Hattori N, Sobue G
    • Journal Title

      Res Adv in Neurology 2

      Pages: 45-55

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Age associated axonal features in HNPP with 17p11.2 deletion in Japan.2005

    • Author(s)
      Koike H, Hirayama M, Yamamoto M, Ito H, Hattori N, Umehara F, Arimura K, Ikeda S, Ando Y, Nakazato M, Kaji R, Hayasaka K, Nakagawa M, Sakoda S, Masumura K, Onodera O, Baba M, Yasuda H, Saito T, Kira J, Nakashima K, Oka N, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 76

      Pages: 1109-1114

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Neuronal intranuclear hyaline inclusion disease showing motor-sensory and autonomic neuropathy.2005

    • Author(s)
      Sone J, Hishikawa N, Koike H, Hattori N, Hirayama M, Nagamatsu M, Yamamoto M, Tanaka F, Yoshida M, Hashizume Y, Imamura H, Yamada E, Sobue G
    • Journal Title

      Neurology 65

      Pages: 1538-1543

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Neuronal intranuclear hyaline inclusion disease showing motor-sensory and autonomic neuropathy.2005

    • Author(s)
      Sone J, Hishikawa N, Koike H, Hattori N, Hirayama M, Nagamatsu M, Yamamoto M, Tanaka F, Yoshida M, Hashizume Y, Imamura H, Yamada E, Sobue G
    • Journal Title

      Neurology 65

      Pages: 1538-1543

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Neuronal intranuclear hyaline inclusion disease showing motor-sensory and autonomic neuropathy.2005

    • Author(s)
      Sone J, Hishikawa N, Koike H, Hattori N, Hirayama M, Nagamatsu M, Yamamoto M, Tanaka F, Yoshida M, Hashizume Y, Imamura H, Yamada E, Sobue G.
    • Journal Title

      Neurology 65

      Pages: 1538-1543

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Neuronal intranuclear hyaline inclusion disease showing motor-sensory and autonomic neuropathy.2005

    • Author(s)
      Sone J, Hishikawa N, Koike H, Hattori N, Hirayama M, Nagamatsu M, Yamamoto M, Tanaka F, Yoshida M, Hashizume Y, Imamura H, Yamada E, Sobue G
    • Journal Title

      Neurology 65

      Pages: 1538-1543

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration.2005

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Sang C, Tanaka F, Inukai A, Doyu M, Sobue G
    • Journal Title

      Nature Med 11

      Pages: 1088-1095

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration2005

    • Author(s)
      Waza, M., Adachi, H., Katsuno, M., Minamiyama, M., Sang, C., Tanaka, F., Inukai, A., Doyu, M., Sobue, G.
    • Journal Title

      Nat. Med. 11

      Pages: 1088-1095

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Neuronal intranuclear hyaline inclusion disease showing motor-sensory and autonomic neuropathy.2005

    • Author(s)
      Sone J, Hishikawa N, Koike H, Hattori N, Hirayama M, Nagamatsu M, Yamamoto M, Tanaka F, Yoshida M, Hashizume Y, Imamura H. Yamada E, Sobue G
    • Journal Title

      Neurology 65

      Pages: 1538-1543

    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] The wide spectrum of clinical manifestations in Sjogren's syndrome-associated neuropathy.2005

    • Author(s)
      Mori K, Iijima M, Koike H, Hattori N, Tanaka F, Watanabe H, Katsuno M, Fujita A, Aiba I, Ogata A, Saito T, Asakura K, Yoshida M, Hirayama M, Sobue G
    • Journal Title

      Brain 128

      Pages: 2518-2534

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profile of spinal motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G.
    • Journal Title

      Ann Neurol. 57

      Pages: 236-51

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Thiamine-deficiency neuropathy in Japan.2005

    • Author(s)
      Koike H, Iijima M, Mori K, Hattori N, Sobue G
    • Journal Title

      Res Adv in Neurology 2

      Pages: 45-55

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Widespread nuclear and cytoplasmic mutant androgen receptor accumulation in spinal and bulbar muscular atrophy.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Waza M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] The wide spectrum of clinical manifestations in Sjogren's syndrome-associated neuropathy.2005

    • Author(s)
      Mori K, Iijima M, Koike H, Hattori N, Tanaka F, Watanabe H, Katsuno M, Fujita A, Aiba I, Ogata A, Saito T, Asakura K, Yoshida M, Hirayama M, Sobue G
    • Journal Title

      Brain 128

      Pages: 2518-2534

    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Thiamine-deficiency neuropathy in Japan.2005

    • Author(s)
      Koike H, Iijima M, Mori K, Hattori N, Sobue G
    • Journal Title

      Res Adv in Neurology 2

      Pages: 45-55

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Tuft-shaped astrocytes in Lewy body disease.2005

    • Author(s)
      Hishikawa N, Hashizume Y, Yoshida M, Niwa J, Tanaka F, Sobue G.
    • Journal Title

      Acta Neuropathol (Berl). 109

      Pages: 373-80

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] The wide spectrum of clinical manifestations in Sjogren's syndrome-associated neuropathy.2005

    • Author(s)
      Mori K, Iijima M, Koike H, Hattori N, Tanaka F, Watanabe H, Katsuno M, Fujita A, Aiba I, Ogata A, Saito T, Asakura K, Yoshida M, Hirayama M, Sobue G
    • Journal Title

      Brain 128

      Pages: 2158-2534

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Clinical and electrophysiologic correlates of IVIg responsiveness in CIDP.2005

    • Author(s)
      Iijima M, Yamamoto M, Hirayama M, Tanaka F, Katsuno M, Mori K, Koike H, Hattori N, Arimura K, Nakagawa M, Yoshikawa H, Hayasaka K, Onodera O, Baba M, Yasuda H, Saito T, Nakazato M, Nakashima K, Kira J, Kaji R, Oka N, Sobue G
    • Journal Title

      Neurology 64

      Pages: 1471-1475

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Widespread nuclear and cytoplasmic mutant androgen receptor accumulation in spinal and bulbar muscular atrophy.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Waza M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Thiamine-deficiency neuropathy in Japan.2005

    • Author(s)
      Koike H, Iijima M, Mori K, Hattori N, Sobue G
    • Journal Title

      Res Adv in Neurology 2

      Pages: 45-55

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Clinical and electrophysiologic correlates of IVIg responsiveness in CIDP.2005

    • Author(s)
      Iijima M, Yamamoto M, Hirayama M, Tanaka F, Katsuno M, Mori K, Koike H, Hattori N, Arimura K, Nakagawa M, Yoshikawa H, Hayasaka K, Onodera O, Baba M, Yasuda H, Saito T, Nakazato M, Nakashima K, Kira J, Kaji R, Oka N, Sobue G
    • Journal Title

      Neurology 64

      Pages: 1471-1475

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Widespread nuclear and cytoplasmic mutant androgen receptor accumulation in spinal and bulbar muscular atrophy.2005

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Waza M, Sang C, Nakagomi Y, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Brain 128

      Pages: 659-670

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Thiamine deficiency neuropathy in Japan.2005

    • Author(s)
      Haruki Koike, Masahiro Iijima, Keiko Mori, Naoki Hattori, Gen Sobue
    • Journal Title

      Recent Advances in Neurology 2

      Pages: 45-55

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Thiamine-deficiency neuropathy in Japan.2005

    • Author(s)
      Koike H, Iijima M, Mori K, Hattori N, Sobue G
    • Journal Title

      Res Adv in Neurology 2

      Pages: 45-55

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Age associated axonal features in HNPP with 17p11.2 deletion in Japan.2005

    • Author(s)
      Koike H, Hirayama M, Yamamoto M, Ito H, Hattori N, Umehara F, Arimura K, Ikeda S, Ando Y, Nakazato M, kaji R, Hayasaka K, Nakagawa M, Sakoda S, Matsumura K, Onodera O, Baba M, Yasuda H, Saito T, Kira J, Nakashima K, Oka N, Sobue G
    • Journal Title

      J Nuerol Neurosurg Psychiatry 76

      Pages: 1109-1114

    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci Usa 102

      Pages: 16801-16806

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci USA 102

      Pages: 16801-16806

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Age associated axonal features in HNPP with 17p11.2 deletion in Japan.2005

    • Author(s)
      Koike H, Hirayama M, Yamamoto M, Ito H, Hattori N, Umehara F, Arimura K, Ikeda S, Ando Y, Nakazato M, Kaji R, Hayasaka K, Nakagawa M, Sakoda S, Matsumura K, Onodera 0, Baba M, Yasuda H, Saito T, Kira J, Nakashima K, Oka N, Sobue G.
    • Journal Title

      J Neurol Neurosurg Psychiatry 76

      Pages: 1109-1114

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Clinical and electrophy siologic correlates of IVIg responsiveness in CIDP.2005

    • Author(s)
      Iijima M, Yamamoto M, Hirayama M, Tanaka F, Katsuno M, Mori K, Koike H, Hattori N, Arimura K, Nakagawa M, Yoshikawa H, Hayasaka K, Onodera O, Baba M, Yasuda H, Saito T, Nakazato M, Nakashima K, Kira J, Kaji R, Oka N, Sobue G
    • Journal Title

      Neurology 64

      Pages: 1471-1475

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Clinical and electrophysiologic correlates of IVIg responsiveness in CIDP.2005

    • Author(s)
      Iijima M, Yamamoto M, Hirayama M, Tanaka F, Katsuno M, Mori K, Koike H, Hattori N, Arimura K, Nakagawa M, Yoshikawa H, Hayasaka K, Onodera O, Baba M, Yasuda H, Saito T, Nakazato M, Nakashima K, Kira J, Kaji R, Oka N, Sobue G.
    • Journal Title

      Neurology 64

      Pages: 1471-1475

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-17590871
  • [Journal Article] Tuft-shaped astrocytes in Lewy body disease. Acta Neuropathol (Berl).2005

    • Author(s)
      Hishikawa N, Hashizume Y, Yoshida M, Niwa J, Tanaka F, Sobue G
    • Journal Title

      Acta Neuropathol (Berl). 109

      Pages: 373-380

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Journal Article] Neuronal intranuclear hyaline inclusion disease showing motor-sensory and autonomic neuropathy.2005

    • Author(s)
      Sone J, Hishikawa N, Koike H, Hattori N, Hirayama M, Nagamatsu M, Yamamoto M, Tanaka F, Yoshida M, Hashizume Y, Imamura H, Yamada E, Sobue G
    • Journal Title

      Neurology 65

      Pages: 1538-1543

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Data Source
      KAKENHI-PROJECT-17659261
  • [Journal Article] Pharmacological induction of heat-shock proteins alleviates polyglutamine-mediated motor neuron disease.2005

    • Author(s)
      Katsuno M, Sang C, Adachi H, Minamiyama M, Waza M, Tanaka F, Doyu M, Sobue G
    • Journal Title

      Proc Natl Acad Sci USA 102

      Pages: 16801-16806

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] 17-AAG, an Hsp90 inhibitor, ameliorates polyglutamine-mediated motor neuron degeneration.2005

    • Author(s)
      Waza M, Adachi H, Katsuno M, Minamiyama M, Sang C, Tanaka F, Inukai A, Doyu M, Sobue G
    • Journal Title

      Nature Med 11

      Pages: 1088-1095

    • Data Source
      KAKENHI-PROJECT-17209032
  • [Journal Article] Gene expression profile of motor neurons in sporadic amyotrophic lateral sclerosis.2005

    • Author(s)
      Jiang YM, Yamamoto M, Kobayashi Y, Yoshihara T, Liang Y, Terao S, Takeuchi H, Ishigaki S, Katsuno M, Adachi H, Niwa J, Tanaka F, Doyu M, Yoshida M, Hashizume Y, Sobue G
    • Journal Title

      Ann Neurol 57

      Pages: 236-251

    • Data Source
      KAKENHI-PROJECT-17025020
  • [Journal Article] Spinal and bulbar muscular atrophy : ligand-dependent pathogenes is and therapeutic perspectives.2004

    • Author(s)
      Katsuno M, Adachi H, Tanaka F, Sobue G
    • Journal Title

      J Mol Med 82

      Pages: 298-307

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Sweet relief for Huntington disease.2004

    • Author(s)
      Katsuno M, Adachi H, Sobue G
    • Journal Title

      Nature Med 10

      Pages: 123-124

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Wide range of lineages of cells expressing nerve growth factor mRNA in the nerve lesions of patients with vasculitic neuropathy : An implication of endoneurial macrophage for nerve regeneration.2004

    • Author(s)
      Mitsuma N, Yamamoto M, Iijima M, Hattori N, Ito Y, Tanaka F, Sobue G
    • Journal Title

      Neuroscience 129

      Pages: 109-117

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Field strengths and sequences influence putaminal MRI findings in multiple system atrophy.2004

    • Author(s)
      Watanabe H, Fukatsu H, Hisikawa N, Hashizume Y, Sobue G
    • Journal Title

      Neurology 62

      Pages: 671-671

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Sodium butyrate ameliorates phenotypic expression in a transgenic mouse model of spinal and bulbar muscular atrophy.2004

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Waza M, Sang C, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Sobue G.
    • Journal Title

      Hum Mol Genet 13

      Pages: 1183-1192

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] The effects of levodopa on apraxia of lid opening : A case report.2004

    • Author(s)
      Yamada S, Matsuo K, Hirayama M, Sobue G
    • Journal Title

      Neurology 62

      Pages: 830-831

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Spinal and bulbar muscular atrophy : ligand-dependent pathogenesis and therapeutic perspectives.2004

    • Author(s)
      Katsuno M, Adachi H, Tanaka F, Sobue G.
    • Journal Title

      J Mol Med 82

      Pages: 298-307

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Sodium butyrate ameliorates phenotypic expression in a transgenic mouse model of spinal and bulbar muscular atrophy.2004

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Waza M, Sang C, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Sobue G
    • Journal Title

      Hum Mol Genet 13

      Pages: 1183-1192

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Multiple regional 1H-MR spectroscopy in multiple system atrophy : NAA/Cr reduction in pontine base as a valuable diagnostic marker.2004

    • Author(s)
      Watanabe H, Fukatsu H, Katsuno M, Sugiura M, Hamada K, Okada Y, Hirayama M, Ishigkai T, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 75

      Pages: 103-109

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Dorfin prevents cell death by reducing mitochondrial localising mutant superoxide dismutase 1 in a neuronal cell model of familial amyotrophic lateral sclerosis.2004

    • Author(s)
      Takeuchi H, Niwa J, Hishikawa N, Ishigaki S, Tanaka F, Doyu M, Sobue G
    • Journal Title

      J Neurochem 89

      Pages: 64-72

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Pathology of early-vs late-onset TTR Met30 familial amyloid polyneuropathy.2004

    • Author(s)
      Koike H, Misu K, Sugiura M, Iijima M, Mori K, Yamamoto M, Hattori N, Mukai E, Ando Y, Dceda S, Sobue G
    • Journal Title

      Neurology 63

      Pages: 129-138

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Physical and functional interaction between Dorfin and Valosin-containing protein that are colocalized in ubiquitylated inclusions in neurodegenerative disorders.2004

    • Author(s)
      Ishigaki S, Hishikawa N, Niwa J, Iemura S, Natsume T, Hori S, Kakizuka A, Tanaka K, Sobue G
    • Journal Title

      J Biol Chem 279

      Pages: 51376-51385

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Retinoic-acid-concentration-dependent acquisition of neural cell identity during in vitro differentiation of mouse embryonic stem cells.2004

    • Author(s)
      Okada Y, Shimazaki T, Sobue G, Okano H
    • Journal Title

      Dev Biol 275

      Pages: 124-142

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Dorfin prevents cell death by reducing mitochondrial localizing mutant superoxide dismutase 1 in a neuronal cell model of familial amyotrophic lateral sclerosis.2004

    • Author(s)
      Takeuchi H, Niwa J, Hishikawa N, Ishigaki S, Tanaka F, Doyu M, Sobue G.
    • Journal Title

      J Neurochem. 89

      Pages: 64-72

    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Journal Article] Polyglutamine diminishes VEGF : Passage to motor neuron death?2004

    • Author(s)
      Katsuno M, Sobue G
    • Journal Title

      Neuron 41

      Pages: 677-679

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Sodium butyrate ameliorates phenotypic expression in a transgenic mouse model of spinal and bulbar muscular atrophy.2004

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Waza M, Sang C, Kobayashi Y, Tanaka F, Doyu M, Inukai A, Sobue G
    • Journal Title

      Hum Mol Genet 13

      Pages: 1183-1192

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Spinal and bulbar muscular atrophy : ligand-dependent pathogenesis and therapeutic perspectives.2004

    • Author(s)
      Katsuno M, Sobue G
    • Journal Title

      J Mol Med 82

      Pages: 298-307

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Dorfin localizes to the ubiquitilated inclusions in Parkinson's disease, dementia with Lewy bodies, multiple system atrophy, and amyotrophic lateral sclerosis.2003

    • Author(s)
      Hishikawa N, Niwa J, Doyu M, Ito T, Ishigaki S, Hashizume Y, Sobue G
    • Journal Title

      Am J Pathol 163(2)

      Pages: 609-619

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Hsp 105 a suppresses the aggregation of truncated androgen receptor with expanded CAG repeats and cell toxicity.2003

    • Author(s)
      Ishihara K, Yamagishi N, Saito Y, Adachi H, Kobayashi Y, Sobue G, Otsuka K, Hatayama T
    • Journal Title

      J Biol Chem 278(27)

      Pages: 25143-25150

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Alcoholic neuropathy is clinicopathologically distinct from thiamine-deficiency neuropathy.2003

    • Author(s)
      Koike H, Iijima M, Sugiura M, Mori K, Hattori N, Ito H, Hirayama M, Sobue G
    • Journal Title

      Ann Neurol 54

      Pages: 19-29

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Sequential constriction of upper airway and vocal cords in sleep apnoea of multiple system atrophy : low field magnetic resonance fluoroscopic study.2003

    • Author(s)
      Hirayama M, Fukatsu H, Watanabe H, Koike Y, Noda A, Ito H, Kobayashi R, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 74(5)

      Pages: 642-645

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Transgenic mouse models of spinal and bulbar muscular atrophy(SBMA).2003

    • Author(s)
      Katsuno M, Adachi H, Inukai A, Sobue G
    • Journal Title

      Cytogenet Genome Res 100

      Pages: 243-251

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Occipital hypoperfusion in Parkinson's disease without dementia : correlation to impaired cortical visual processing.2003

    • Author(s)
      Abe Y, Kachi T, Arahata Y, Yamada T, Washimi Y, Iwai K, Ito K, Yanagisawa N, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 74(4)

      Pages: 419-422

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Onset age and severity impairment are associated with reduction of myocardial ^<123>I-MIBG uptake in Parkinson's disease.2003

    • Author(s)
      Hamada K, Hirayama M, Watanabe H, Kobayashi R, Ito H, Ieda T, Koike Y, Sobue G
    • Journal Title

      J Neurol Neurosurg Psychiatry 74(4)

      Pages: 423-426

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Nerve excitability properties in Charcot-Marie-Tooth disease type 1A.2003

    • Author(s)
      Nodera H, Bostock H, Kuwabara S, Sakamoto T, Asanuma K, Jia-Ying S, Ogawara K, Hattori N, Hirayama M, Sobue G, Kaji R
    • Journal Title

      Brain 127

      Pages: 203-211

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Leuprorelin rescue polyglutamine-dependent phenotypes in a transgenic mouse model of spinal and bulbar muscular atrophy.2003

    • Author(s)
      Katsuno M, Adachi H, Doyu M, Minamiyama M, Sang C, Kobayashi Y, Inukai A, Sobue G
    • Journal Title

      Nature Medicine 9(6)

      Pages: 768-773

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Heat shock protein 70 chaperone overexpression ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model by reducing nuclear-localized mutant androgen receptor protein.2003

    • Author(s)
      Adachi H, Katsuno M, Minamiyama M, Sang C, Pagoulatous G, Angelidis C, Kusakabe M, Yoshiki A, Kobayashi Y, Doyu M, Sobue G
    • Journal Title

      J Neurosci 23(6)

      Pages: 2203-2211

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] α-Synuclein-positive structures in associations with diffuse neurofibrillary tangles with calcification.2003

    • Author(s)
      Hishikawa N, Hashizume Y, Ujihara N, Okada Y, Yoshida M, Sobue G
    • Journal Title

      Neuropathol Appl Neurobiology 29

      Pages: 280-287

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Demyelinating and axonal features of Charcot-Marie-Tooth disease with mutations of myelin-related proteins (PMP22,MPZ and Cx32) : a clinicopathological study of 205 Japanese patients.2003

    • Author(s)
      Hattori N, Yamamoto M, Yoshihara T, Koike H, Nakagawa N, Yoshikawa H, Ohnishi A, Hayasaka K, Onodera O, Baba M, Yasuda H, Saito T, Nakashima K, Kira J, Kaji R, Oka N, Sobue G, the Study Group for Hereditary Neuropathy in Japan
    • Journal Title

      Brain 126

      Pages: 134-151

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Clinical and neuropathological correlates of Lewy body disease.2003

    • Author(s)
      Hishikawa N, Hashizume Y, Yoshida M, Sobue G
    • Journal Title

      Acta Neuropathol 105

      Pages: 341-350

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Caspase-1 and -3 are differentially upregulated in motor neurons and glial cells in mutant SOD1 transgenic mouse spinal cord : a study usign laser microdissection and real time RT-PCR.2003

    • Author(s)
      Ando Y, Liang Y, Ishigaki S, Niwa J, Jiang Y, Kobayashi Y, Yamamoto M, Doyu M, Sobue G
    • Journal Title

      Neurochem Res 28

      Pages: 839-846

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Dorfin localizes to Lewy bodies and ubiquitylates synphilin-1.2003

    • Author(s)
      Ito T, Niwa J, Hishikawa N, Ishigaki S, Doyu M, Sobue G
    • Journal Title

      J Biol Chem 278(31)

      Pages: 29106-29114

    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Journal Article] Para neoplastic neuropathy

    • Author(s)
      Koike H, Sobue G.
    • Journal Title

      Handb Clin Neurol

      Volume: (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] The significance of folate deficiency in alcoholic and nutritional neuropathies : Analysis of a case

    • Author(s)
      Koike H, Hama T, Kawagashira Y, Hashimoto R, Tomita M, Iijima M, Sobue G.
    • Journal Title

      Nutrition

      Volume: (in press)

    • Peer Reviewed
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] 脚気ニューロパチーの神経病理

    • Author(s)
      小池春樹, 祖父江元
    • Journal Title

      神経内科

      Volume: (in press)

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Journal Article] Transthyretin Val30 Met familial amyloid polyneuropathy in Japan. In : Halcheck IP, Vernon NR editors Amyloids : Composition, Functions and Pathology.

    • Author(s)
      Koike H, Tanaka F, Sobue G.
    • Journal Title

      Nova Science Publishers

      Volume: (in press)

    • Data Source
      KAKENHI-PROJECT-21591076
  • [Patent] タウのスプライシングを制御するアンチセンスオリゴヌクレオチド及びその用途2019

    • Inventor(s)
      祖父江元,石垣診祐,佐橋健太郎, 他4名
    • Industrial Property Rights Holder
      名古屋大学、神戸天然物化学株式会社
    • Industrial Property Rights Type
      特許
    • Filing Date
      2019
    • Overseas
    • Data Source
      KAKENHI-WRAPUP-19H05447
  • [Patent] TDP-43の発現量を調節するアンチセンスオリゴヌクレオチド及びその用途2018

    • Inventor(s)
      祖父江元、石垣診祐、永井義隆、前田和宏、武内敏秀、閨正博、他
    • Industrial Property Rights Holder
      名古屋大学、大阪大学、神戸天然物化学㈱
    • Industrial Property Rights Type
      特許
    • Filing Date
      2018
    • Overseas
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Patent] タウのスプライシングを制御するアンチセンスオリゴヌクレオチド及びその用途2018

    • Inventor(s)
      祖父江元、石垣診祐、佐橋健太郎、遠藤邦幸、閨正博、他
    • Industrial Property Rights Holder
      名古屋大学、神戸天然物化学㈱
    • Industrial Property Rights Type
      特許
    • Filing Date
      2018
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Patent] タウのスプライシングを制御するアンチセンスオリゴヌクレオチド及びその用途2018

    • Inventor(s)
      祖父江元、石垣診祐、佐橋健太郎、遠藤邦幸、閨正博、藤原健志、他
    • Industrial Property Rights Holder
      名古屋大学、神戸天然物化学㈱
    • Industrial Property Rights Type
      特許
    • Filing Date
      2018
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Patent] TDP-43の発現量を調節するアンチセンスオリゴヌクレオチド及びその用途2018

    • Inventor(s)
      祖父江元、石垣診祐、佐橋健太郎、永井義隆、前田和宏、武内敏秀、他
    • Industrial Property Rights Holder
      名古屋大学、大阪大学、神戸天然物化学㈱
    • Industrial Property Rights Type
      特許
    • Filing Date
      2018
    • Overseas
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Patent] TDP-43の発現量を調節するアンチセンスオリゴヌクレオチド及びその用途2017

    • Inventor(s)
      祖父江元、石垣診祐、他7名
    • Industrial Property Rights Holder
      名古屋大学、大阪大学、神戸天然物化学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2017
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Patent] TDP-43の発現量を調節するアンチセンスオリゴヌクレオチド及びその用途2017

    • Inventor(s)
      祖父江 元、石垣 診祐、佐橋 健太郎、永井 義隆、前田 和宏 他
    • Industrial Property Rights Holder
      名古屋大学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2017
    • Overseas
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Patent] TDP-43の発現量を調節するアンチセンスオリゴヌクレオチド及びその用途2017

    • Inventor(s)
      祖父江 元、石垣 診祐、佐橋 健太郎、永井 義隆 他
    • Industrial Property Rights Holder
      名古屋大学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2017
    • Overseas
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Patent] 疾患モデル動物および疾患治療剤2016

    • Inventor(s)
      祖父江元、石垣
    • Industrial Property Rights Holder
      名古屋大学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2016
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Patent] 疾患モデル動物および疾患治療剤2016

    • Inventor(s)
      祖父江元、石垣診祐、横井聡
    • Industrial Property Rights Holder
      国立大学法人名古屋大学
    • Industrial Property Rights Type
      特許
    • Industrial Property Number
      2016-139308
    • Filing Date
      2016-07-14
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Patent] 疾患モデル動物および疾患治療剤2016

    • Inventor(s)
      祖父江元、石垣診祐、横井聡
    • Industrial Property Rights Holder
      名古屋大学
    • Industrial Property Rights Type
      特許
    • Filing Date
      2016-07-14
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Patent] 急速進行型孤発性ALSの検査方法、検査キット、及び医薬のスクリーニング方法2015

    • Inventor(s)
      祖父江元、熱田直樹、渡邉はづき、平川晃弘、中杤昌弘
    • Industrial Property Rights Holder
      名古屋大学
    • Industrial Property Rights Type
      特許
    • Industrial Property Number
      2015-051093
    • Filing Date
      2015-03-13
    • Data Source
      KAKENHI-PROJECT-25461277
  • [Patent] 抗神経変性疾患剤2012

    • Inventor(s)
      祖父江 元・勝野 雅央
    • Industrial Property Rights Holder
      祖父江 元・勝野 雅央
    • Industrial Property Rights Type
      特許
    • Filing Date
      2012-09-03
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Patent] 球脊髄性筋萎縮症治療薬2009

    • Inventor(s)
      祖父江元、勝野雅央、南山誠
    • Industrial Property Rights Holder
      名古屋大学
    • Industrial Property Number
      2009-277101
    • Filing Date
      2009-12-05
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Patent] 球脊髄性筋萎縮症治療薬2009

    • Inventor(s)
      祖父江元, 勝野雅央, 南山誠
    • Industrial Property Rights Holder
      名古屋大学
    • Industrial Property Number
      2009-277101
    • Filing Date
      2009-12-05
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Patent] 球脊髄性筋萎縮症治療薬2009

    • Inventor(s)
      祖父江元、勝野雅央、南山誠
    • Industrial Property Rights Holder
      未定
    • Filing Date
      2009-12-05
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Patent] 凝集体形成性タンパク質分解用の発現コントラクト、及び凝集体形成性タンパク質が凝集体を形成することを抑制する方法2006

    • Inventor(s)
      山田 新一, 丹羽 淳一, 祖父江 元
    • Industrial Property Rights Holder
      山田 新一, 丹羽 淳一, 祖父江 元
    • Filing Date
      2006-03-20
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-17590870
  • [Patent] 抗ポリグルタミン病剤.2004

    • Inventor(s)
      勝野雅央, 祖父江元
    • Industrial Property Rights Holder
      勝野雅央, 祖父江元
    • Industrial Property Number
      2004-246980
    • Filing Date
      2004
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-12210010
  • [Patent] 抗グルタミン病剤:2004

    • Inventor(s)
      祖父江 元
    • Industrial Property Rights Holder
      祖父江 元
    • Filing Date
      2004-08-26
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Patent] 抗グルタミン病剤2004

    • Inventor(s)
      祖父江 元
    • Industrial Property Rights Holder
      祖父江 元
    • Industrial Property Number
      2004-246980
    • Filing Date
      2004-08-26
    • Data Source
      KAKENHI-PROJECT-12210010
  • [Patent] 抗グルタミン病剤2004

    • Inventor(s)
      祖父江 元
    • Industrial Property Rights Holder
      祖父江 元
    • Industrial Property Number
      2004-246980
    • Filing Date
      2004-08-26
    • Data Source
      KAKENHI-PROJECT-15209031
  • [Patent] 抗ポリグルタミン病剤2004

    • Inventor(s)
      祖父江 元
    • Industrial Property Rights Holder
      祖父江 元
    • Industrial Property Number
      2004-246980
    • Filing Date
      2004-08-26
    • Data Source
      KAKENHI-PROJECT-16390250
  • [Patent] 球脊髄性筋萎縮症の病態を再現する非ヒト動物、及び球脊髄性筋萎縮症治療剤.2002

    • Inventor(s)
      勝野雅央, 足立弘明, 祖父江元
    • Industrial Property Rights Holder
      勝野雅央, 足立弘明, 祖父江元
    • Industrial Property Number
      2002-238599
    • Filing Date
      2002
    • Description
      「研究成果報告書概要(和文)」より
    • Data Source
      KAKENHI-PROJECT-12210010
  • [Presentation] ALSの早期診断:遺伝子診断2023

    • Author(s)
      中村 亮一、熱田 直樹、藤内 玄規、丹羽 淳一、道勇 学、祖父江 元
    • Organizer
      第64回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-PROJECT-22K07509
  • [Presentation] Development of Therapeutic Drugs Using iPS Cell-Derived Motor Neurons from ALS Patients2023

    • Author(s)
      Genki Tohnai, Ryoichi Nakamura, Naoki Atsuta, Kazunari Onodera, Youhei Okada, Gen Sobue
    • Organizer
      PACTALS 2023
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-23K06835
  • [Presentation] ALSに対するprecision medicineに向けて2022

    • Author(s)
      熱田 直樹, 中村 亮一, 藤内 玄規, 祖父江 元
    • Organizer
      第63回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-22K07509
  • [Presentation] SOD1-G93S変異陽性筋萎縮性側索硬化症患者の臨床遺伝学的特徴2022

    • Author(s)
      中村 亮一, 中杤 昌弘, 熱田 直樹, 藤内 玄規, 伊藤 大輔, 和泉 唯信, 橋本 里奈, 饗場 郁子, 溝口 功一, 金井 数明, 青木 正志, 柴田 俊, 伊藤 千弘, 湯淺 知子, 徳井 啓介, 川頭 祐一, 丹羽 淳一, 道勇 学, 勝野 雅央, 祖父江 元
    • Organizer
      第63回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-22K07509
  • [Presentation] SOD1-G93S変異陽性筋萎縮性側索硬化症患者の臨床遺伝学的及び病理学的特徴2022

    • Author(s)
      中村 亮一、中杤 昌弘、陸 雄一、 熱田 直樹、藤内 玄規、伊藤 大輔、和泉 唯信、橋本 里奈、饗場 郁子、溝口 功一、金井 数明、青木 正志、徳井 啓介、川頭 祐一、丹羽 淳一、 道勇 学、 岩崎 靖、 吉田 眞理、 勝野 雅央、祖父江 元
    • Organizer
      日本人類遺伝学会第67回大会
    • Data Source
      KAKENHI-PROJECT-22K07509
  • [Presentation] ALS治療開発への展望2019

    • Author(s)
      祖父江 元
    • Organizer
      日本ALS協会愛知県支部総会
    • Invited
    • Data Source
      KAKENHI-WRAPUP-19H05447
  • [Presentation] Lessons from SBMA study: Pathophysiology, clinical characteristics and treatment strategies2019

    • Author(s)
      祖父江 元
    • Organizer
      30th International Symposium on ALS/MND
    • Int'l Joint Research
    • Data Source
      KAKENHI-WRAPUP-19H05447
  • [Presentation] 筋萎縮性硬化症(ALS)の患者レジストリ研究( JaCALS)から見えてくるもの病態解明・創薬に向けて2019

    • Author(s)
      祖父江 元
    • Organizer
      第30回 日本医学会総会
    • Invited
    • Data Source
      KAKENHI-WRAPUP-19H05447
  • [Presentation] 神経変性疾患に対する医師主導治験とエビデンス構築2019

    • Author(s)
      祖父江 元
    • Organizer
      第37回日本神経治療学会シンポジウム
    • Invited
    • Data Source
      KAKENHI-WRAPUP-19H05447
  • [Presentation] ALSの治療法開発の時代へ:レジストリ研究(JaCALS)から病態解明・創薬に向けて2019

    • Author(s)
      祖父江 元
    • Organizer
      日本ALS協会埼玉県支部総会
    • Invited
    • Data Source
      KAKENHI-WRAPUP-19H05447
  • [Presentation] 大規模臨床、ゲノム、不死化細胞リソースを基盤としたオミックス解析による孤発性ALS治療法開発研究2019

    • Author(s)
      祖父江 元
    • Organizer
      AMED難治性疾患実用化研究事業成果報告会 東京
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 機能的MRIで見えるこれから見なければいけない脳機能2018

    • Author(s)
      祖父江元、渡辺宏久、勝野雅央
    • Organizer
      第59回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] JaCALS Registry Based Therapeutic Research in ALS2018

    • Author(s)
      祖父江 元
    • Organizer
      International Meeting of Pan-Asian Consortium for Treatment and Research in ALS (PACTALS), Seoul,
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] JaCALS Registry Based Therapeutic Research in ALS2018

    • Author(s)
      祖父江 元
    • Organizer
      International Meeting of Pan-Asian Consortium for Treatment and Research in ALS (PACTALS), Seoul,
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] FTLD/ALSの神経回路病態解明に基づく革新的診断治療開発2018

    • Author(s)
      祖父江 元
    • Organizer
      平成30年度第一回 革新脳臨床研究G分科会 東京
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] ALSレジストリー研究(JaCALS)から見えるもの2018

    • Author(s)
      祖父江 元
    • Organizer
      第59回日本神経学会学術集会 シンポジウム「レジストリー・コホート研究が目指すもの - 病態解明・創薬に向けて」 札幌
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 神経変性疾患のdisease-modifying therapyの開発2018

    • Author(s)
      祖父江 元
    • Organizer
      創薬薬理フォーラム 第63回談話会
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 神経変性疾患のdisease-modifying therapyの開発に向けて2018

    • Author(s)
      祖父江 元
    • Organizer
      第59回日本神経学会学術集会 イブニングセミナー 札幌
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 大規模臨床、ゲノム、不死化細胞リソースを基盤としたオミックス解析による孤発性ALS治療法開発研究2018

    • Author(s)
      祖父江 元
    • Organizer
      AMED難治性疾患実用化研究事業成果報告会 東京
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Role of cerebellar atrophy on cognitive-related functional connectivity in multiple system atrophy2018

    • Author(s)
      祖父江元、渡辺宏久、川畑和也、原一洋、大嶽れい子、バガリナオ エピファニオ、加藤隼康、小倉礼、桝田道人、横井孝政、勝野雅央
    • Organizer
      The 6th International Multiple System Atrophy Congress, 2018
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] RNA結合タンパク質FUSの機能と神経変性疾患への関わり2018

    • Author(s)
      祖父江元、石垣診祐
    • Organizer
      第41回日本分子生物学会年会 ワークショップ 横浜
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 日常診療における難治性疾患への対応とピットフォール2018

    • Author(s)
      祖父江 元
    • Organizer
      第115回日本内科学会講演会 京都
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] タウ蛋白は摂食量及び体重を制御する2018

    • Author(s)
      祖父江元、石垣診祐、河合香里、岩出展行、石橋みなか、渡辺宏久、勝野雅央
    • Organizer
      The 41st annual Meeting of the Japan Neuroscience Society Kobe
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] FTLD/ALSの神経回路病態解明に基づく革新的診断治療開発2018

    • Author(s)
      祖父江 元
    • Organizer
      平成30年度第一回 革新脳臨床研究G分科会 東京
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Involvement of cerebello-cerebral functional networks and cognitive decline in multiple system atrophy2018

    • Author(s)
      祖父江元、渡辺宏久
    • Organizer
      75th fujihara Seminar, Tokyo
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 前頭側頭型認知症の分子標的治療薬・バイオマーカー開発によるdisease-modifying therapyへの展開2018

    • Author(s)
      祖父江 元
    • Organizer
      融合脳・認知症チーム第5回分科会 東京
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Alterations of brain connectivity in healthy aging and early dementia: Results from the Nagoya BMRC cohort study2018

    • Author(s)
      祖父江元、渡辺宏久、バガリナオ エピファニオ、前澤聡、森大輔、礒田治夫、長縄慎二
    • Organizer
      3rd Scientific Meeting of ISMRM Japanese Chapter
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 前頭側頭型認知症の分子標的治療薬・バイオマーカー開発によるdisease-modifying therapyへの展開2018

    • Author(s)
      祖父江 元
    • Organizer
      認知症チーム第5回分科会 東京
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 神経変性疾患のdisease-modifying therapyの開発2018

    • Author(s)
      祖父江 元
    • Organizer
      第41回日本神経科学大会 特別教育講演 神戸
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 神経変性疾患のdisease-modifying therapyの開発に向けて2018

    • Author(s)
      祖父江 元
    • Organizer
      第59回日本神経学会学術集会 イブニングセミナー 札幌
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Development of disease-modifying therapy for neurodegenerative diseases2018

    • Author(s)
      祖父江 元
    • Organizer
      10回NAGOYAグローバルリトリート
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] ALSFRS-Rを用いた 筋萎縮性側索硬化症患者の 進行、予後予測と治験デザイン2018

    • Author(s)
      熱田直樹、中村亮一、林直毅、横井大知、伊藤瑞規、渡辺宏久、勝野雅央、和泉唯信、森田光哉、谷口彰、織田雅也、阿部康二、狩野修、桑原聡、青木正志、金井数明、服部信孝、梶龍兒、祖父江元、JaCALS
    • Organizer
      第59回日本神経学会学術大会
    • Data Source
      KAKENHI-PROJECT-17K09778
  • [Presentation] マーモセット尾状核でのFUS KDは、グリア炎症を伴い神経線維の短縮を引き起こす2018

    • Author(s)
      祖父江元、石垣診祐、渡辺宏久、勝野雅央
    • Organizer
      41st annual Meeting of the Japan Neuroscience Society Kobe
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 神経変性疾患のdisease-modifying therapyの開発2018

    • Author(s)
      祖父江 元
    • Organizer
      創薬薬理フォーラム 第63回談話会
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Development of disease-modifying therapy for neurodegenerative diseases2018

    • Author(s)
      祖父江 元
    • Organizer
      第10回NAGOYAグローバルリトリート
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] タウisoformの成体神経新生における役割2018

    • Author(s)
      石垣診祐、岩出展行、藤岡祐介、遠藤邦幸、河合香里、石橋みなか、勝野雅央、渡辺宏久、宮坂知宏、祖父江元
    • Organizer
      第13回 臨床ストレス応答学会大会 小樽
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] FTLDの人および動物脳画像研究2018

    • Author(s)
      祖父江 元
    • Organizer
      平成29年度 第2回 革新脳臨床研究グループ分科会
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 運動ニューロン疾患の病態と治療 球脊髄性筋萎縮症(SBMA)に筋萎縮性硬化症(ALS)について2018

    • Author(s)
      祖父江 元
    • Organizer
      第14回日本神経筋摂食嚥下栄養研究会 名古屋
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Brain network reorganization in aging and dementia2018

    • Author(s)
      祖父江元、渡辺宏久、バガリナオ エピファニオ、前澤聡、森大輔、長縄慎二
    • Organizer
      BrainConnects 2018, 2018, Singapore
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 運動ニューロン疾患の病態と治療 球脊髄性筋萎縮症(SBMA)に筋萎縮性硬化症(ALS)について2018

    • Author(s)
      祖父江 元
    • Organizer
      第14回日本神経筋摂食嚥下栄養研究会 名古屋
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] FTLDの病態解明とそれに基づくタウisoformを標的とした核酸治療薬の開発2018

    • Author(s)
      祖父江 元
    • Organizer
      新学術領域(研究提案型)脳タンパク質老化と認知症制御 第8回班会議・第4回リトリート 東京
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 神経変性疾患のdisease-modifying therapyの開発2018

    • Author(s)
      祖父江 元
    • Organizer
      第41回日本神経科学大会 特別教育講演 神戸
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 筋萎縮性側索硬化症患者のレジストリ構築:創薬促進に向けて2018

    • Author(s)
      祖父江 元
    • Organizer
      AMEDクリニカル・イノベーション・ネットワーク推進支援事業公開シンポジウム 東京
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 筋萎縮性側索硬化症患者のレジストリ構築:創薬促進に向けて2018

    • Author(s)
      祖父江 元
    • Organizer
      AMEDクリニカル・イノベーション・ネットワーク推進支援事業公開シンポジウム 東京
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Real world data analysis and modifier gene survey on ALS patients registry (JaCALS)2018

    • Author(s)
      祖父江 元
    • Organizer
      3rd Global ARO Network Workshop, Tokyo
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Prognosis of Japanese patients with amyotrophic lateral sclerosis according to motor phenotype2018

    • Author(s)
      Naoki Atsuta, Daichi Yokoi, Ryoichi Nakamura, Hazuki Watanabe, Naoki Hayashi, Mizuki Ito, Hirohisa Watanabe, Masahisa Katsuno, Yuishin Izumi, Mitsuya Morita, Akira Taniguchi, Masaya Oda, Koji Abe, Kouichi Mizoguchi, Osamu Kano, Satoshi Kuwabara, Masashi Aoki, Nobutaka Hattori, Ryuji Kaji, & Gen Sobue, JaCALS
    • Organizer
      PACTALS 2018
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-17K09778
  • [Presentation] ALS/FTLDおよび4R-tau優位のタウオパチーにおけるFUSとSFPQの結合性の低下2018

    • Author(s)
      祖父江元、石垣診祐
    • Organizer
      The 41st annual Meeting of the Japan Neuroscience Society Kobe
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 認知症の病態と治療2018

    • Author(s)
      祖父江 元
    • Organizer
      第115回日本内科学会講演会 パネルディスカッション「日常診療における難治性疾患への対応とピットフォール」 京都
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 新しい手法によるレヴィ小体病の画像解析 レヴィ小体病の機能的結合性(functional connectivity)解析2018

    • Author(s)
      祖父江元、渡辺宏久、勝野雅央
    • Organizer
      第12回パーキンソン病運動障害疾患コングレス
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] FTLDの病態解明とそれに基づくタウisoformを標的とした核酸治療薬の開発2018

    • Author(s)
      祖父江 元
    • Organizer
      新学術領域(研究提案型)脳タンパク質老化と認知症制御 第8回班会議・第4回リトリート 東京
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] レジストリー・コホート研究が目指すもの - 病態解明・創薬に向けて2018

    • Author(s)
      祖父江 元
    • Organizer
      第59回日本神経学会学術集会 シンポジウム 札幌
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] FTLDの人および動物脳画像研究2018

    • Author(s)
      祖父江 元
    • Organizer
      平成29年度 第2回 革新脳臨床研究グループ分科会
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Clinical, genetic, and imaging features of multiple system atrophy2017

    • Author(s)
      渡辺宏久、祖父江元
    • Organizer
      2017 KMDS Autumn Symposium
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Clinical, genetic, and imaging features of multiple system atrophy2017

    • Author(s)
      渡辺宏久、祖父江元
    • Organizer
      2017 KMDS Autumn Symposium
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Cooperative control of SynGAP isoform α2 mRNA stability by FUS and ELAV-like proteins promotes dendritic spine maturation and cognitive function2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      The 40th annual Meeting of the Japan Neuroscience Society
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Perspectives of Large-scale ALS Patient Registry Study.2017

    • Author(s)
      祖父江 元
    • Organizer
      The 5th Kyoto Course on Bioinformatics for Genomic Medicine International Symposium on Genomic Medicine-Genomics of Rare and Intractable Diseases,
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Aberrant interaction between FUS and SFPQ in 4R-tau dominant tauopathy brains.2017

    • Author(s)
      Ishigaki S, Riku Y, Fujioka Y, Honda D, Yokoi S, Endo K., Kawai K, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 200年目のパーキンソン病:早期病態理解の進歩と展望2017

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第49回日本臨床分子形態学会学術集会
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Silencing of FUS in the non-human primate brain via stereotaxic injection of an adeno-associated virus encoding shRNA2017

    • Author(s)
      Endo K, Ishigaki S, Fujioka Y, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] JaCALS/FTLD-J2017

    • Author(s)
      祖父江 元
    • Organizer
      JaCALS/FTLD-J. Joint meeting of PACTALS and BRAIN PROTEIN AGING AND DEMENTIA CONTROL PROJECT
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 皮膚生検で確定診断し得た神経核内封入体病の1例2017

    • Author(s)
      岡本光佑, 金藤公人, 井出 渉, 幸原伸夫, 曽根 淳, 祖父江 元
    • Organizer
      第100回日本神経学会北海道地方会
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Presentation] STN-DBS 後のパーキンソン病で認める発声・発話障害:その病態と対策2017

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第43回関東機能的脳外科カンファレンス
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Our interprofessional collaboration approach for favourable outcome of voice and speech in patient with Parkinson's disease after deep brain stimulation2017

    • Author(s)
      渡辺宏久、坪井崇、田中康博、藤本保志、中坪大輔、前澤聡、梶田泰一、勝野雅央、祖父江元
    • Organizer
      第76回日本脳神経外科学会学術集会
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Silencing of FUS in the brain of non-human primates via stereotaxic injection of an adeno-associated virus encoding shRNA.2017

    • Author(s)
      Endo K, Ishigaki S, Fujioka Y, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      WCN 2017
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] FUS and ELAV-like proteins cooperatively control SynGAP isoform α2 in a 3'UTR length-dependent manner to promote dendritic spine maturation and cognitive function.2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 3’UTR length-dependent control of SynGAP isoform α2 mRNA by FUS and ELAV-like proteins promotes dendritic spine maturation and cognitive function.2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      WCN 2017
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] THK5351 imaging and neural network.2017

    • Author(s)
      祖父江 元
    • Organizer
      Brain Protein Aging and Dementia Control International Tau Symposium
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 長期に画像所見を追跡し得た神経核内封入体病の1例2017

    • Author(s)
      松本 美紀, 野田 智子, 田村 拓也, 中薮 幹也, 伊藤 宏樹, 曽根 淳, 祖父江 元
    • Organizer
      第 148 回日本神経学会東海・北陸地方会
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Presentation] 前頭側頭型認知症の分子標的治療薬・バイオマーカー開発によるdisease-modifying therapyへの展開2017

    • Author(s)
      祖父江 元
    • Organizer
      平成29年度融合脳認知症チーム進捗報告会
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 一過性の健忘症状を呈した成人発症神経核内封入体病の1例2017

    • Author(s)
      竹下 潤, 小林 宏光, 下江 豊, 曽根 淳, 祖父江 元, 栗山 勝
    • Organizer
      第 107 回日本神経学会近畿地方会
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Presentation] Aberrant interaction between FUS and SFPQ in 4R-tau dominant tauopathy brains.2017

    • Author(s)
      Ishigaki S, Riku Y, Fujioka Y, Honda D, Yokoi S, Endo K., Kawai K, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Perspectives of patient registry study for ALS From JaCALS2017

    • Author(s)
      祖父江 元
    • Organizer
      Summit Meeting for Global Registries of Stroke, Parkinson's disease, and ALS’ to construct a global stroke registry
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Prognosis of Japanese patients with amyotrophic lateral sclerosis according to motor phenotype2017

    • Author(s)
      Naoki Atsuta, Daichi Yokoi, Ryoichi Nakamura, Hazuki Watanabe, Naoki Hayashi, Mizuki Ito, Hirohisa Watanabe, Masahisa Katsuno, Yuishin Izumi, Mitsuya Morita, Akira Taniguchi, Masaya Oda, Koji Abe, Kouichi Mizoguchi, Osamu Kano, Satoshi Kuwabara, Masashi Aoki, Nobutaka Hattori, Ryuji Kaji, & Gen Sobue, JaCALS
    • Organizer
      XXIII World Congress of Neurology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-17K09778
  • [Presentation] Perspectives of patient registry study for ALS From JaCALS.2017

    • Author(s)
      祖父江 元
    • Organizer
      Summit Meeting for Global Registries of Stroke, Parkinson's disease, and ALS’ to construct a global stroke registry
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 名古屋神経変性疾患のdisease-modifying therapyをめざして2017

    • Author(s)
      祖父江 元
    • Organizer
      第39回神経組織培養研究会
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 200年目のパーキンソン病:早期病態理解の進歩と展望2017

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第49回日本臨床分子形態学会学術集会
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Neural network imaging and clinical features in patients with amyotrophic lateral sclerosis & frontotemporal lobar degeneration spectrum2017

    • Author(s)
      渡辺宏久、祖父江元
    • Organizer
      BrainConnects 2017
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Cooperative control of SynGAP isoform α2 mRNA stability by FUS and ELAV-like proteins promotes dendritic spine maturation and cognitive function2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      The 40th annual Meeting of the Japan Neuroscience Society
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] JaCALS/FTLD-J2017

    • Author(s)
      祖父江 元
    • Organizer
      JaCALS/FTLD-J. Joint meeting of PACTALS and BRAIN PROTEIN AGING AND DEMENTIA CONTROL PROJECT
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] エオジン好性核内封入体病の頭部画像所見2017

    • Author(s)
      高木 伸之介, 岸本 祥之, 毛利 尚裕, 青木 真一郎, 中藪 幹也, 曽根 淳, 祖父江 元
    • Organizer
      第 142 回日本神経学会東海・北陸地方会
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Presentation] 前頭側頭型認知症の分子標的治療薬・バイオマーカー開発によるdisease-modifying therapyへの展開2017

    • Author(s)
      祖父江 元
    • Organizer
      平成29年度融合脳認知症チーム進捗報告会
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Typical feature of MSA with videos2017

    • Author(s)
      渡辺宏久、祖父江元
    • Organizer
      2017 KMDS Autumn Symposium
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Silencing of FUS in the non-human primate brain via stereotaxic injection of an adeno-associated virus encoding shRNA.2017

    • Author(s)
      Endo K, Ishigaki S, Fujioka Y, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Silencing of FUS in the non-human primate brain via stereotaxic injection of an adeno-associated virus encoding shRNA.2017

    • Author(s)
      Endo K, Ishigaki S, Fujioka Y, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] タウタンパク質の蓄積とconnectomics2017

    • Author(s)
      渡辺宏久、石垣診祐、祖父江元
    • Organizer
      タウ研究会2017
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] STN-DBS 後のパーキンソン病で認める発声・発話障害:その病態と対策2017

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第43回関東機能的脳外科カンファレンス
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] パーキンソン病の衝動制御障害 update2017

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第11回パーキンソン病・運動障害疾患コングレス
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 蛋白特異的PETならびにMRI等を用いた、加齢およびパーキンソン病と関連疾患の可視化の現状2017

    • Author(s)
      渡辺宏久、祖父江元
    • Organizer
      第27回ブレイン・ファンクション・イメージング・カンファレンス
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Establishment of adeno-associated virus vector system for silencing FUS in common marmoset brain2017

    • Author(s)
      Endo K, Ishigaki S, Masamizu Y, Hatanaka N, Fujioka Y, Watakabe A, Yamamori T, Katsuno M, Watanabe H, Matsuzaki M, Nambu A, Sobue G.
    • Organizer
      The 40th annual Meeting of the Japan Neuroscience Society
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Molecular mechanism and therapeutic approach for FUS-mediated FTLD/ALS.2017

    • Author(s)
      祖父江 元
    • Organizer
      2nd International Symposium on Protein Aging and Dementia Control
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 放射線科医が知っておくべき神経内科領域の最近の話題2017

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第37回神経放射線ワークショップ モーニングセミナー
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Our interprofessional collaboration approach for favourable outcome of voice and speech in patient with Parkinson's disease after deep brain stimulation2017

    • Author(s)
      渡辺宏久、坪井崇、田中康博、藤本保志、中坪大輔、前澤聡、梶田泰一、勝野雅央、祖父江元
    • Organizer
      第76回日本脳神経外科学会学術集会
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] SBMA (Kennedy’s disease) and ALS: Development of disease-modifying therapy.2017

    • Author(s)
      祖父江 元
    • Organizer
      XXIII World Congress of Neurology
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Silencing of FUS in the brain of non-human primates via stereotaxic injection of an adeno-associated virus encoding shRNA.2017

    • Author(s)
      Endo K, Ishigaki S, Fujioka Y, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      WCN 2017
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Aberrant interaction between FUS and SFPQ in 4R-tau dominant tauopathy brains.2017

    • Author(s)
      Ishigaki S, Riku Y, Fujioka Y, Honda D, Yokoi S, Endo K., Kawai K, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] 神経核内封入体病の一家系2017

    • Author(s)
      前田 憲吾, 杉原 芳子, 曽根 淳, 祖父江 元
    • Organizer
      第 108 回日本神経学会近畿地方会
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Presentation] Molecular mechanism and therapeutic approach for FUS-mediated FTLD/ALS.2017

    • Author(s)
      祖父江 元
    • Organizer
      2nd International Symposium on Protein Aging and Dementia Control
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] THK5351 imaging and neural network.2017

    • Author(s)
      祖父江 元
    • Organizer
      Brain Protein Aging and Dementia Control International Tau Symposium
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] パーキンソン病の薬物療法の課題:ヒトにおける可視化技術の果たす役割2017

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第32回日本大脳基底核研究会
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Typical feature of MSA with videos2017

    • Author(s)
      渡辺宏久、祖父江元
    • Organizer
      2017 KMDS Autumn Symposium
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] パーキンソン病の衝動制御障害 update2017

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第11回パーキンソン病・運動障害疾患コングレス
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Perspectives of Large-scale ALS Patient Registry Study.2017

    • Author(s)
      祖父江 元
    • Organizer
      The 5th Kyoto Course on Bioinformatics for Genomic Medicine International Symposium on Genomic Medicine - Genomics of Rare and Intractable Diseases,
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 名古屋神経変性疾患のdisease-modifying therapyをめざして2017

    • Author(s)
      祖父江 元
    • Organizer
      第39回神経組織培養研究会
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 頸部と右上肢の振戦が中心症状だった神経核内封入体病の一例2017

    • Author(s)
      兒玉 憲人, 武井 藍, 牧 美充, 中村 友紀, 橋口 昭大, 野妻 智嗣, 田代 雄一, 曽根 淳, 祖父江 元, 高嶋 博
    • Organizer
      第217 回日本神経学会九州地方会
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Presentation] 神経難病の治療研究の現状と将来展望 球脊髄性筋萎縮症(SBMA)と筋萎縮性側索硬化症(ALS)の治験・レジストリ研究から2017

    • Author(s)
      祖父江 元
    • Organizer
      日本臨床試験学会第8回学術集会総会
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 3’UTR length-dependent control of SynGAP isoform α2 mRNA by FUS and ELAV-like proteins promotes dendritic spine maturation and cognitive function.2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      WCN 2017
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] FUS and ELAV-like proteins cooperatively control SynGAP isoform α2 in a 3'UTR length-dependent manner to promote dendritic spine maturation and cognitive function.2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] タウタンパク質の蓄積とconnectomics2017

    • Author(s)
      渡辺宏久、石垣診祐、祖父江元
    • Organizer
      タウ研究会2017
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] パーキンソン病の薬物療法の課題:ヒトにおける可視化技術の果たす役割2017

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第32回日本大脳基底核研究会
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 放射線科医が知っておくべき神経内科領域の最近の話題2017

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第37回神経放射線ワークショップ モーニングセミナー
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Development of a single cell analysis tool for neurological disorders on 2D-plate with positional information.2017

    • Author(s)
      Ishigaki S., Uno H., Wang Z-H., Ukita Y., Bhardwaj R., Tue P. T., Yurino H., Hashimoto S., Oka T., Kawahara K., Urisu T., Takamura Y., and Sobue G.
    • Organizer
      The 40th annual Meeting of the Japan Neuroscience Society
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Neural network imaging and clinical features in patients with amyotrophic lateral sclerosis & frontotemporal lobar degeneration spectrum2017

    • Author(s)
      渡辺宏久、祖父江元
    • Organizer
      BrainConnects 2017
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] FUS and ELAV-like proteins cooperatively control SynGAP isoform α2 in a 3'UTR length-dependent manner to promote dendritic spine maturation and cognitive function.2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      The 47th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] 3’UTR length-dependent control of SynGAP isoform α2 mRNA by FUS and ELAV-like proteins promotes dendritic spine maturation and cognitive function.2017

    • Author(s)
      Yokoi S, Udagawa T, Fujioka Y, Honda D, Okado H, Watanabe H, Katsuno M, Ishigaki S, Sobue G.
    • Organizer
      WCN 2017
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Silencing of FUS in the brain of non-human primates via stereotaxic injection of an adeno-associated virus encoding shRNA.2017

    • Author(s)
      Endo K, Ishigaki S, Fujioka Y, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      WCN 2017
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Establishment of adeno-associated virus vector system for silencing FUS in common marmoset brain2017

    • Author(s)
      Endo K, Ishigaki S, Masamizu Y, Hatanaka N, Fujioka Y, Watakabe A, Yamamori T, Katsuno M, Watanabe H, Matsuzaki M, Nambu A, Sobue G.
    • Organizer
      The 40th annual Meeting of the Japan Neuroscience Society
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 蛋白特異的PETならびにMRI等を用いた、加齢およびパーキンソン病と関連疾患の可視化の現状2017

    • Author(s)
      渡辺宏久、祖父江元
    • Organizer
      第27回ブレイン・ファンクション・イメージング・カンファレンス
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Development of a single cell analysis tool for neurological disorders on 2D-plate with positional information.2017

    • Author(s)
      Ishigaki S., Uno H., Wang Z-H., Ukita Y., Bhardwaj R., Tue P. T., Yurino H., Hashimoto S., Oka T., Kawahara K., Urisu T., Takamura Y., and Sobue G.
    • Organizer
      The 40th annual Meeting of the Japan Neuroscience Society
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] SBMA (Kennedy’s disease) and ALS: Development of disease-modifying therapy.2017

    • Author(s)
      祖父江 元
    • Organizer
      XXIII World Congress of Neurology
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 脳タンパク質老化とマクロ神経回路破綻2016

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第46回新潟神経学夏期セミナー
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Perspectives on therapeutic research for ALS2016

    • Author(s)
      祖父江 元
    • Organizer
      3rd World Centenarians Initiative International Symposium on Amyotrophic Lateral Sclerosis
    • Place of Presentation
      千里ライフサイエンスセンター(大阪府豊中市)
    • Year and Date
      2016-02-19
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Perspectives on therapeutic research for ALS2016

    • Author(s)
      祖父江 元
    • Organizer
      3rd World Centenarians Initiative International Symposium on Amyotrophic Lateral Sclerosis
    • Place of Presentation
      千里ライフサイエンスセンター(大阪府豊中市)
    • Year and Date
      2016-02-19
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Presentation] Skin-related dysautonomia and bladder dysfunction in PD.2016

    • Author(s)
      Watanabe H., Sobue G.
    • Organizer
      4th World Parkinson Congress Parallel Sessions Practical Management of Autonomic Dysfunction
    • Place of Presentation
      Portland(USA)
    • Year and Date
      2016-09-20
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Accumulation of phosphorylated tau in neurons in FUS-silenced mice.2016

    • Author(s)
      Ishigaki S, Fujioka Y., Honda D, Yokoi S, Endo K, Okado H, Watanabe H, Katsuno M, Takashima A, Sobue G.
    • Organizer
      The 46th Society for Neuroscience annual meeting
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Accumulation of phosphorylated tau in neurons in FUS-silenced mice.2016

    • Author(s)
      27.Ishigaki S, Fujioka Y, Honda D, Yokoi S, Endo K., Okado H, Watanabe H, Katsuno M, Takashima A., Sobue G.
    • Organizer
      The 46th Society for Neuroscience annual meeting
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2016-11-12
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Skin-related dysautonomia and bladder dysfunction in PD.2016

    • Author(s)
      Watanabe H, Sobue G.
    • Organizer
      4th World Parkinson Congress Parallel Sessions
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Loss of PSF/SFPQ, an intra-nuclear counterpart of FUS causes FTLD-like phenotypes2016

    • Author(s)
      Fujioka Y, Ishigaki S, Yokoi S, Honda D, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 39th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      パシフィコ横浜(神奈川県 横浜市)
    • Year and Date
      2016-07-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Loss of SFPQ, an intra-nuclear counterpart of FUS causes FTLD-like phenotypes.2016

    • Author(s)
      28.Fujioka Y, Ishigaki S, Yokoi S, Honda D, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 46th Society for Neuroscience annual meeting
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2016-11-12
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Loss of SFPQ, an intra-nuclear counterpart of FUS causes FTLD-like phenotypes.2016

    • Author(s)
      Fujioka Y., Ishigaki S., Yokoi S., Honda D., Okado H., Watanabe H., Katsuno M., Sobue G.
    • Organizer
      The 46th Society for Neuroscience annual meeting
    • Place of Presentation
      San Diego(USA)
    • Year and Date
      2016-11-12
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 認知症の病態に基づく治療開発 神経変性性認知症を中心に2016

    • Author(s)
      祖父江 元
    • Organizer
      認知症研究を知る若手研究者の集まり
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Functional linkage between FUS and tau in ALS/FTLD2016

    • Author(s)
      Ishigaki S, Fujioka Y, Honda D, Yokoi S, Okado H, Watanabe H, Katsuno M, Sobue G
    • Organizer
      The 39th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      パシフィコ横浜(神奈川県 横浜市)
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Perspectives on therapeutic research for ALS2016

    • Author(s)
      祖父江元
    • Organizer
      ALS病治療戦略国際シンポジウム
    • Place of Presentation
      千里ライフサイエンスセンター(大阪府豊中市)
    • Year and Date
      2016-02-19
    • Invited
    • Data Source
      KAKENHI-PROJECT-26461269
  • [Presentation] Dysregulated Akt signaling pathway in spinal and bulbar muscular atrophy (SBMA)2016

    • Author(s)
      飯田円,勝野雅央,佐橋健太郎,中辻秀朗,近藤直英,藤内玄規,祖父江元
    • Organizer
      第39回日本神経科学大会
    • Place of Presentation
      パシフィコ横浜(神奈川県 横浜市)
    • Year and Date
      2016-07-20
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] Skin-related dysautonomia and bladder dysfunction in PD.2016

    • Author(s)
      Watanabe H, Sobue G.
    • Organizer
      4th World Parkinson Congress PARALLEL SESSION SPRACTICAL MANAGEMENT OF AUTONOMIC DYSFUNCTION.
    • Place of Presentation
      Portland,USA
    • Year and Date
      2016-09-20
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K15338
  • [Presentation] 認知症に寄り添う~地域生活継続可能な社会に向けて~ 認知症の診断2016

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      日本医師会生涯教育協力講座
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Dysregulated Akt signaling pathway in spinal and bulbar muscular atrophy (SBMA).2016

    • Author(s)
      飯田円,勝野雅央,佐橋健太郎,中辻秀朗,近藤直英,藤内玄規,祖父江元
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸コンベンションセンター(兵庫県 神戸市)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] 認知症の克服に向けて2016

    • Author(s)
      祖父江 元
    • Organizer
      第70回日本交通医学会総会
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 脳タンパク質老化とマクロ、ミクロ神経回路破綻2016

    • Author(s)
      祖父江 元
    • Organizer
      新学術領域(研究提案型)脳タンパク質老化と認知症制御 第4回班会議・第2回学術領域研究リトリート
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 前頭側頭葉変性症(FTLD)/筋萎縮性側索硬化症(ALS)の神経回路破綻解明に基づく革新的治療開発2016

    • Author(s)
      祖父江 元
    • Organizer
      革新脳 臨床グループ・変性チーム分科会
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 前頭側頭型認知症の病態診断2016

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第30回老年期認知症研究会
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 球脊髄性筋萎縮症のdisease-modifying therapyの開発について2016

    • Author(s)
      祖父江 元
    • Organizer
      第57回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Accumulation of phosphorylated tau in neurons in FUS-silenced mice.2016

    • Author(s)
      Ishigaki S., Fujioka Y., Honda D., Yokoi S., Endo K., Okado H., Watanabe H., Katsuno M., Takashima A., Sobue G.
    • Organizer
      The 46th Society for Neuroscience annual meeting
    • Place of Presentation
      San Diego(USA)
    • Year and Date
      2016-11-12
    • Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 神経変性疾患モデルにおけるタクロリムスとその誘導体の治療効果2016

    • Author(s)
      藤内玄規, 勝野雅央, 足立弘明, 佐橋健太郎, 近藤直英, 中辻秀朗, 飯田円, 祖父江元
    • Organizer
      第39回日本分子生物学会年会
    • Place of Presentation
      パシフィコ横浜(神奈川県 横浜市)
    • Year and Date
      2016-11-30
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] The effect of exercise in a mouse model of spinal and bulbar muscular atrophy.2016

    • Author(s)
      中辻秀朗, 勝野雅央, 近藤直英, 藤内玄規, 佐橋健太郎, 飯田円, 祖父江元
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸コンベンションセンター(兵庫県 神戸市)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] Perspectives on therapeutic research for ALS -General review of therapeutics, and edaravone treatment-2016

    • Author(s)
      祖父江 元
    • Organizer
      大韓神経筋肉疾患学会
    • Place of Presentation
      Seoul(Korea)
    • Year and Date
      2016-03-25
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Presentation] Dissection of mechanisms of neuronal degeneration in polyglutamine disease2016

    • Author(s)
      Kentaro Sahashi, Naohide Kondo, Hideaki Nakatsuji, Genki Tohnai, Madoka Iida, Masahisa Katsuno, and Gen Sobue
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸コンベンションセンター
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PROJECT-26461268
  • [Presentation] Perspectives on therapeutic research for ALS -General review of therapeutics, and edaravone treatment-2016

    • Author(s)
      祖父江 元
    • Organizer
      大韓神経筋肉疾患学会
    • Place of Presentation
      Seoul(Korea)
    • Year and Date
      2016-03-25
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Motor neuron-specific dynactin-1 knockout mice exhibit ALSlike neurodegeneration2016

    • Author(s)
      Kaori Kawai, Masahisa Katsuno, Kensuke Ikenaka, Yohei Iguchi, Ryu Katsumata, Kunihiko Araki, Fumiaki Tanaka, Gen Sobue
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸国際会議場(兵庫県 神戸市)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PROJECT-26461269
  • [Presentation] 新専門医制度にどう対応していくのか2016

    • Author(s)
      祖父江 元
    • Organizer
      第57回日本神経学会学術大会
    • Invited
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Antisense inhibition of neuronal androgen receptor in spinal and bulbar muscular atrophy2016

    • Author(s)
      Kentaro Sahashi, Masahisa Katsuno, Gene Hung, Hiroaki Adachi, Naohide Kondo, Hideaki Nakatsuji, Genki Tohnai, Madoka Iida, C. Frank Bennett, and Gen Sobue
    • Organizer
      第8回NAGOYAグローバルリトリート
    • Place of Presentation
      あいち健康プラザ(愛知県知多郡)
    • Year and Date
      2016-02-12
    • Data Source
      KAKENHI-PROJECT-26461268
  • [Presentation] パーキンソン病の脳内神経回路解析2016

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第10回 パーキンソン病・運動障害疾患コングレス
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 認知症の病態を可視化する:脳血管障害および脳タンパク質老化とマクロ神経回路破綻2016

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第15回釧路ニューロサイエンスワークショップ
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Dissection of mechanisms of neuronal degeneration in polyglutamine disease.2016

    • Author(s)
      佐橋健太郎, 近藤直英, 中辻秀朗, 藤内玄規, 飯田円, 勝野雅央, 祖父江元
    • Organizer
      第57回日本神経学会学術大会
    • Place of Presentation
      神戸コンベンションセンター(兵庫県 神戸市)
    • Year and Date
      2016-05-18
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] 脳タンパク質老化とマクロ神経回路破綻の可視化2016

    • Author(s)
      渡辺宏久、勝野雅央、祖父江元
    • Organizer
      第8回お茶の水 Neuroimaging Conference
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] Visualization of tau protein accumulation and neural network breakdown with aging and dementia.2016

    • Author(s)
      祖父江 元
    • Organizer
      Brain Connects 2016
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 神経変性疾患のdisease-modifying therapy開発をめざして2015

    • Author(s)
      祖父江元
    • Organizer
      第88回日本薬理学会年会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-03-18
    • Data Source
      KAKENHI-PROJECT-26461269
  • [Presentation] Intracerebroventricular administration of antisense oligonucleotides improves disease phenotypes in SBMA mice.2015

    • Author(s)
      Sahashi K, Katsuno M, Hung G, Adachi H, Kondo N, Nakatsuji H, Tohnai G, Iida M, Bennett CF, Sobue G.
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] 顕微鏡的多発血管炎と非全身性血管炎性ニューロパチーの臨床病理学的差異2015

    • Author(s)
      高橋美江、小池春樹、飯島正博、大山健、川頭祐一、祖父江元
    • Organizer
      第58回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] FTLD様のフェノタイプを呈するFUS機能喪失モデルマウスにおけるadult neurogenesisの低下2015

    • Author(s)
      石垣診祐, 藤岡祐介, 本田大祐, 横井聡, 岡戸晴生、渡辺宏久、勝野雅央、祖父江元 ,藤岡祐介, 石垣診祐, 横井聡, 本田大祐, 宇多川剛, 岡戸晴生, 渡辺宏久, 勝野雅央, 祖父江元
    • Organizer
      第38回日本神経科学大会
    • Place of Presentation
      神戸国際会議場(神戸市中央区)
    • Year and Date
      2015-07-30
    • Data Source
      KAKENHI-PROJECT-221S0003
  • [Presentation] 封入体筋炎におけるTGF-βシグナル伝達の異常2015

    • Author(s)
      野田 成哉, 前嶋伸哉、中西 浩隆, 木村 正剛, 飯島正博、小池春樹、近藤直英、勝野雅央、祖父江 元
    • Organizer
      第58回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] FUSの質的機能喪失によるALS/FTLDの病態機構 Quality loss of FUS is involved in the pathogenesis of ALS/FTLD.2015

    • Author(s)
      Ishigaki S, Sobue G
    • Organizer
      第56回神経学会学術大会 シンポジウム
    • Place of Presentation
      新潟県 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-22
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Loss of FUS affects adult neurogenesis by modulating Tau isoforms2015

    • Author(s)
      石垣 診祐、藤岡 祐介、本田 大祐、横井 聡、岡田 洋平、岡戸 晴生、渡辺 宏久、勝野 雅央、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Expression and role of TFEB in spinal and bulbar muscular atrophy2015

    • Author(s)
      藤内 玄規, 足立 弘明, 勝野 雅央, 近藤 直英, 宮崎 雄, 飯田 円, 中辻 秀朗, 丁 瑩, 渡辺 宏久, 祖父江 元.
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] Impact of aging on anatomical and functional human brain connectivity-toward early detection of dementia.2015

    • Author(s)
      祖父江 元
    • Organizer
      9th International Congress of the Asian Society Against Dementia (ASAD)
    • Place of Presentation
      ホテルKKR熊本(熊本県熊本市)
    • Year and Date
      2015-09-15
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 神経変性疾患のdisease-modifying therapy開発をめざして2015

    • Author(s)
      祖父江 元
    • Organizer
      日本脳神経外科学会第74回学術総会
    • Place of Presentation
      ロイトン札幌(北海道札幌市)
    • Year and Date
      2015-10-15
    • Invited
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Presentation] Novel imaging biomarker for early detection of AD.2015

    • Author(s)
      祖父江 元
    • Organizer
      2nd World Centenarian Initiative International Symposium on Alzheimer’s Disease Prevention Strategy
    • Place of Presentation
      JA共済ビル カンファレンスホール(東京都千代田区)
    • Year and Date
      2015-06-27
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] The effects of pioglitazone on spinal and bulbar muscular atrophy.2015

    • Author(s)
      Iida M, Katsuno M, Nakatsuji H, Adachi H, Kondo N, Miyazaki Y, Tohnai G, Watanabe H, Yamamoto M, Kishida K, Sobue G.
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] FUS regulates AMPA receptor function and FTLD/ALS-associated behavior via GluA1 mRNA stabilization2015

    • Author(s)
      Honda D, Udagawa T, Fujioka Y, Tanaka M, Yokoi S, Nagai T, Yamada K, Ishigaki S, Watanabe H, Katsuno M, Ohno K, Sokabe M, Okado H, Sobue G.
    • Organizer
      The 38th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      兵庫県 神戸市 神戸国際会議場
    • Year and Date
      2015-07-28
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] FUS knockdown causes the morphologic abnormities of dendritic spines2015

    • Author(s)
      Yokoi S, Ishigaki S, Honda D, Fujioka Y, Udagawa T, Katsuno M, Sobue G.
    • Organizer
      The 38th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      兵庫県 神戸市 神戸国際会議場
    • Year and Date
      2015-07-28
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Impaired muscular creatine metabolism in spinal and bulbar muscular atrophy (SBMA).2015

    • Author(s)
      Hijikata Y, Katsuno M, Suzuki K, Banno H, Hashizume A, Yamada S, Sobue G.
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K15337
  • [Presentation] 神経変性疾患のdisease-modifying therapyをめざした我国初の医師主導治験の経験から2015

    • Author(s)
      祖父江 元
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Invited
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Presentation] Aberrant adult neurogenesis in FUS-knockdown mice which exhibited FTLD-like phenotypes2015

    • Author(s)
      Ishigaki S, Fujioka Y, Honda D, Yokoi S, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 38th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      兵庫県 神戸市 神戸国際会議場
    • Year and Date
      2015-07-28
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] CLINICOPATHOLOGICAL FEATURES OF SARCOID PERIPHRAL NEUROPATHY2015

    • Author(s)
      Takahashi M, Koike H, Iijima M, Ohyama K, Hashimoto R, Kawagashira Y, Sobue G.
    • Organizer
      Peripheral Nerve Society
    • Place of Presentation
      Canada Quebec City
    • Year and Date
      2015-06-27
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] Suppression of FUS induces the morphologic abnormities of dendritic spines2015

    • Author(s)
      横井 聡、石垣 診祐、宇田川 剛、本田 大祐、藤岡 祐介、勝野 雅央、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Antisense inhibition of neuronal androgen receptor in spinal and bulbar muscular atrophy.2015

    • Author(s)
      Sahashi K, Katsuno M, Hung G, Adachi H, Kondo N, Nakatsuji H, Tohnai G, Iida M, Bennett CF, Sobue G
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] MRIで前根優位の馬尾Gd造影を伴う神経根痛に対し、ステロイドパルス療法が著効したCIDPの小児例2015

    • Author(s)
      竹中 宏幸, 遠藤 邦彦, 飯島 正博, 勝野 雅央, 祖父江 元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] Dysregulated nuclear factor-κB (NFκB) signaling in spinal and bulbar muscular atrophy (SBMA).2015

    • Author(s)
      Iida M, Katsuno M, Nakatsuji H, Adachi H, Kondo N, Tohnai G, Sobue G.
    • Organizer
      第38回日本神経科学大会
    • Place of Presentation
      神戸国際会議場(兵庫県神戸市)
    • Year and Date
      2015-07-26
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] 末梢神経 発作性夜間血色素尿症を合併した慢性炎症性脱髄性多発根ニューロパチーの1例2015

    • Author(s)
      辻河 高陽, 飯島 正博, 川頭 祐一, 小池 春樹, 勝野 雅央, 祖父江 元
    • Organizer
      第27回日本神経免疫学会学術集会
    • Place of Presentation
      長良川国際会議場(岐阜県岐阜市)
    • Year and Date
      2015-09-15
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 球脊髄性筋萎縮症患者における呼吸 機能-筋萎縮性側索硬化症との比較-2015

    • Author(s)
      山田晋一郎、勝野雅央、鈴木啓介、 橋詰淳、土方靖浩、祖父江元
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K15337
  • [Presentation] Clinical features of 32 cases of Neuronal intranuclear inclusion disease diagnosed by skin biopsy2015

    • Author(s)
      曽根淳、北川尚之、菅原恵梨子、違口正明、稲垣智則、荒木邦彦、吉田眞理、岩崎靖、田中章景、祖父江元
    • Organizer
      第56回日本神経病理学会総会学術研究会
    • Place of Presentation
      九州大学(福岡県福岡市)
    • Year and Date
      2015-06-04
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Presentation] 多系統萎縮症の脳内神経回路解析2015

    • Author(s)
      原 一洋, 渡辺 宏久, 今井 和憲, 川畑 和也, 桝田 道人, 大嶽 れい子, 伊藤 瑞規, バガリナオ・エピファニオチラ , 勝野 雅央, 祖父江 元
    • Organizer
      第33回日本神経治療学会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-25461313
  • [Presentation] 神経変性疾患のdisease-modifying therapyへの展望2015

    • Author(s)
      祖父江元
    • Organizer
      第104回日本病理学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-04-30
    • Invited
    • Data Source
      KAKENHI-PROJECT-26461269
  • [Presentation] Involvement of caudate nucleus head connectivities in ALS2015

    • Author(s)
      渡辺 宏久、桝田 道人、千田 譲、Bagarinao, Epifanio、田中 康博、陸 雄一、中村 良一、渡辺 はづき、伊藤 瑞規、石垣 診祐、熱田 直樹、勝野 雅央、長縄 慎二、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Disruped muscle uptake of creatine in spinal and bulbar muscular atrophy.2015

    • Author(s)
      Hijikata Y, Katsuno M, Hashizume A, Yamada S, Inagaki T, Suzuki K, Banno H, Sobue G.
    • Organizer
      The 26th International Symposium on ALS/MND
    • Place of Presentation
      Orland, USA
    • Year and Date
      2015-12-11
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] Loss of FUS causes a decrease in brain volume accompanied with neuronal loss2015

    • Author(s)
      Fujioka Y, Ishigaki S, Yokoi S, Honda D, Udagawa T, Okado H, Yoshikawa M, Takashima A, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 45th Society for Neuroscience annual meeting
    • Place of Presentation
      Chicago, IL USA
    • Year and Date
      2015-10-17
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP ATTR Val30Met)における末梢神経病変の超微形態学的検討2015

    • Author(s)
      小池 春樹, 池田 昇平, 高橋 美江, 川頭 祐一, 飯島 正博, 勝野 雅央, 祖父江 元
    • Organizer
      第68回日本自律神経学会総会
    • Place of Presentation
      ウインク愛知(愛知県名古屋市)
    • Year and Date
      2015-10-29
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 臨床症状が異なった家族性神経核内封入体病の57歳男性例と59歳女性例2015

    • Author(s)
      小林 史和、 土屋 舞、福元 恵、山城 亘央、新藤 和雅、曽根 淳、祖父江 元、瀧山 嘉久
    • Organizer
      第213回日本神経学会関東甲信越地方会
    • Place of Presentation
      砂防会館シェーンバッハ・サボー(東京都千代田区)
    • Year and Date
      2015-06-06
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Presentation] The loss of FUS leads to brain atrophy accompanied with neuronal loss.2015

    • Author(s)
      Fujioka Y, Ishigaki S, Yokoi S, Honda D, Udagawa T, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 38th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      兵庫県 神戸市 神戸国際会議場
    • Year and Date
      2015-07-28
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP)における肝移植後の自律神経症候の推移2015

    • Author(s)
      小池 春樹, 池田 昇平, 高橋 美江, 川頭 祐一, 飯島 正博, 中村 友彦, 亀井 秀弥, 小倉 靖弘, 祖父江 元
    • Organizer
      第68回日本自律神経学会総会
    • Place of Presentation
      ウインク愛知(愛知県名古屋市)
    • Year and Date
      2015-10-29
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] Disrupted functional connectivity in Parkinson's disease patients with severe olfactory dysfunction.2015

    • Author(s)
      Watanabe H, Yoneyama N, Bagarinao E, Hara K, Kawabata K, Imai K, Hirayama M, Tsuboi T, Katsuno M, Sobue G
    • Organizer
      The 9th International Congress of the Asian Society Against Dementia in Kumamoto
    • Place of Presentation
      KKR HOTEL KUMAMOTO(熊本県熊本市)
    • Year and Date
      2015-09-15
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] 神経変性疾患のdisease-modifying therapy開発をめざして2015

    • Author(s)
      祖父江 元
    • Organizer
      第88回日本薬理学会年会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-03-18
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] The future of clinical neuroscience2015

    • Author(s)
      祖父江 元
    • Organizer
      Brain connects 2015
    • Place of Presentation
      野依記念館(愛知県名古屋市)
    • Year and Date
      2015-07-31
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Presentation] サルコイドニューロパチーの臨床病理学的特徴と治療反応性及び治療経過2015

    • Author(s)
      高橋 美江, 小池 春樹, 飯島 正博, 池田 昇平, 川頭 祐一, 祖父江 元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] DISRUPTION OF BLOOD-NERVE BARRIER IN TRANSTHYRETIN VAL30MET FAMILIAL AMYLOID POLYNEUROPATHY2015

    • Author(s)
      Koike H, Ikeda S, Takahashi M, Ohyama K, Kawagashira Y, Iijima M, Sobue G.
    • Organizer
      Peripheral Nerve Society
    • Place of Presentation
      Canada Quebec City
    • Year and Date
      2015-06-27
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 葉酸欠乏性ニューロパチーの臨床病理学的特徴と食事および補充療法の反応性2015

    • Author(s)
      小池 春樹, 池田 昇平, 高橋 美江, 川頭 祐一, 飯島 正博, 土井 宏, 田中 章景, 祖父江 元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 自律神経障害を合併した急性感覚性ニューロパチーの1例2015

    • Author(s)
      大山 健, 小池 春樹, 桝田 道人, 曽根 淳, 川頭 祐一, 飯島 正博, 中村 友彦, 渡辺 宏久, 勝野 雅央, 祖父江 元
    • Organizer
      第68回日本自律神経学会総会
    • Place of Presentation
      ウインク愛知(愛知県名古屋市)
    • Year and Date
      2015-10-29
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] パーキンソン病における重度嗅覚低下と安静時脳機能MRIの検討2015

    • Author(s)
      米山典孝,渡辺宏久,原一洋,川畑和也,平山正昭,今井和憲,坪井崇,桝田道人,横井大知,渡辺はづき,熱田直樹,伊藤瑞規,田中康博,大嶽れい子,祖父江元
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-25461313
  • [Presentation] The future of clinical neuroscience.2015

    • Author(s)
      祖父江 元
    • Organizer
      Brain connects 2015
    • Place of Presentation
      野依記念館(愛知県名古屋市)
    • Year and Date
      2015-07-31
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] dynactin-1ノックアウトマウスにおける進行性運動機能障害2015

    • Author(s)
      河合香里、池中建介、勝野雅央、井口洋平、荒木邦彦、田中章景、祖父江元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-26461269
  • [Presentation] Quality loss of FUS and SFPQ alters the ratio of Tau isoforms, which recapitulates FTLD accompanied with aberrant adult neurogenesis.2015

    • Author(s)
      Ishigaki S, Fujioka Y, Honda D, Yokoi S, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 45th Society for Neuroscience annual meeting
    • Place of Presentation
      Chicago, IL USA
    • Year and Date
      2015-10-17
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Disruped muscle uptake of creatine in spinal and bulbar muscular atrophy2015

    • Author(s)
      Hijikata Y, Katsuno M, Suzuki K, Banno H, Hashizume A, Yamada S, Sobue G.
    • Organizer
      The 26th International Symposium on ALS/MND
    • Place of Presentation
      Orlando(USA)
    • Year and Date
      2015-12-11
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K15337
  • [Presentation] 家族性アミロイドポリニューロパチーにおける肝移植後の末梢神経障害の進行に対する加齢の影響2015

    • Author(s)
      小池 春樹, 池田 昇平, 高橋 美江, 川頭 祐一, 飯島 正博, 亀井 秀弥, 小倉 靖弘, 祖父江 元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] tract-based spatial statisticsを用いた多系統萎縮症の画像解析2015

    • Author(s)
      原一洋,渡辺宏久,今井和憲,川畑和也,米山典孝,桝田道人,坪井崇,渡邉はづき,中村亮一,伊藤瑞規,熱田直樹,バガリナオエピファニオジュニア,辻河高陽,加藤重典,安井敬三,長谷川康博,祖父江元
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-25461313
  • [Presentation] FTLD-like phenotypes accompanied with aberrant adult neurogenesis are regulated by altered Tau isoforms in FUS-silenced mice2015

    • Author(s)
      Ishigaki S, Fujioka Y, Honda D, Yokoi S, Okado H, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 10th brain research conference
    • Place of Presentation
      Chicago, IL USA
    • Year and Date
      2015-10-15
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Striatum is systematically affected in TDP-43-related FTLD; a pathological study2015

    • Author(s)
      陸 雄一、渡辺 宏久、吉田 眞理、三室 マヤ、岩崎 靖、桝田 道人、勝野 雅央、石垣 診祐、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] POEMS症候群における表皮内神経線維密度2015

    • Author(s)
      大山健、橋本里奈、川頭祐一、飯島正博、小池春樹、祖父江元
    • Organizer
      第58回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 神経変性疾患のdisease-modifying therapyをめざした我国初の医師主導治験の経験から2015

    • Author(s)
      祖父江 元
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      新潟コンベンションセンター(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] A rapid functional decline type of sporadic ALS is linked to low expression of TTN2015

    • Author(s)
      Naoki Atsuta, Hazuki Watanabe, Akihiro Hirakawa, Ryoichi Nakamura, Masahiro Nakatochi, Shinsuke Ishigaki, Aritoshi Iida, Shiro Ikegawa, Masahisa Katsuno, Yuishin Izumi, Mitsuya Morita, Akira Taniguchi, Koji Abe, Kouichi Mizoguchi, Osamu Kano, Takashi Imai, Masashi Aoki, Kenji Nakashima, Ryuji Kaji, Gen Sobue
    • Organizer
      26th International Symposium on ALS/MND
    • Place of Presentation
      Orlando( USA)
    • Year and Date
      2015-12-12
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-25461277
  • [Presentation] 神経変性疾患のdisease-modifying therapy開発をめざして2015

    • Author(s)
      祖父江 元
    • Organizer
      日本脳神経外科学会第74回学術総会
    • Place of Presentation
      ロイトン札幌(北海道札幌市)
    • Year and Date
      2015-10-15
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 発作性夜間血色素尿症を合併した慢性炎症性脱髄性多発根ニューロパチー1症例における治療経験2015

    • Author(s)
      辻河 高陽, 飯島 正博, 勝野 雅央, 祖父江 元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] FUSの機能喪失はTau isoform依存的にadult neurogenesis抑制を引き起こす2015

    • Author(s)
      石垣 診祐、 藤岡 祐介、本田 大祐、横井 聡、渡辺 宏久、勝野 雅央、祖父江 元
    • Organizer
      第34回日本認知症学会学術集会
    • Place of Presentation
      青森県 青森市 リンクステーション青森
    • Year and Date
      2015-10-02
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Impact of aging on anatomical and functional human brain connectivity-toward early detection of dementia2015

    • Author(s)
      祖父江 元
    • Organizer
      9th International Congress of the Asian Society Against Dementia (ASAD)
    • Place of Presentation
      KKR熊本(熊本県熊本市)
    • Year and Date
      2015-09-15
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Presentation] 脳容積・拡散テンソル画像を用いた前頭側頭型認知症とアルツハイマー型認知症における大脳病変の比較検討2015

    • Author(s)
      桝田 道人, 今井 和憲, 大嶽 れい子, 田中 康博, 伊藤 瑞規, 熱田 直樹, 渡辺 宏久, 勝野 雅央, 祖父江 元
    • Organizer
      第33回日本神経治療学会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-25461313
  • [Presentation] 神経変性疾患のdisease-modifying therapy開発をめざして2015

    • Author(s)
      祖父江元
    • Organizer
      日本脳神経外科学会第74回学術総会
    • Place of Presentation
      ロイトン札幌(北海道札幌市)
    • Year and Date
      2015-10-14
    • Invited
    • Data Source
      KAKENHI-PROJECT-26461269
  • [Presentation] 抗MAG抗体陽性ニューロパチーにおけるランビエ絞輪部周辺分子の分布異常2015

    • Author(s)
      川頭祐一、高橋美江、大山健、飯島正博、小池春樹、祖父江元
    • Organizer
      第58回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] Loss of FUS causes a decrease in brain volume accompanied with neuronal loss2015

    • Author(s)
      Fujioka Y, Ishigaki S, Yokoi S, Honda D, Udagawa T, Okado H, Yoshikawa M, Takashima A, Watanabe H, Katsuno M, Sobue G.
    • Organizer
      The 10th brain research conference
    • Place of Presentation
      Chicago, IL USA
    • Year and Date
      2015-10-15
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] 抗SRP抗体陽性筋炎の臨床病理学的特徴2015

    • Author(s)
      中西 浩隆, 小池 春樹, 飯島 正博,稲垣智則、野田 成哉, 前嶋伸哉、木村 正剛, 久留聡, 祖父江 元
    • Organizer
      第58回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 抗Myelin-associated-glycoprotein抗体陽性ニューロパチーに対するRituximabの有用性2015

    • Author(s)
      川頭 祐一, 池田 昇平, 高橋 美枝, 飯島 正博, 小池 春樹, 勝野 雅央, 祖父江 元
    • Organizer
      第27回日本神経免疫学会学術集会
    • Place of Presentation
      長良川国際会議場(岐阜県岐阜市)
    • Year and Date
      2015-09-15
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 教育講演「一歩進んだALS診療」いかに予後予測を行うか2015

    • Author(s)
      熱田直樹、祖父江元
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-21
    • Invited
    • Data Source
      KAKENHI-PROJECT-25461277
  • [Presentation] Pathogenesis of neurodegeneration in motor neuron-specific dynactin-1 knockout mice2015

    • Author(s)
      河合香里、池中建介、勝野雅央、井口洋平、勝又竜、田中章景、祖父江元
    • Organizer
      第38回日本神経科学大会
    • Place of Presentation
      神戸国際会議場(兵庫県神戸市)
    • Year and Date
      2015-07-28
    • Data Source
      KAKENHI-PROJECT-26461269
  • [Presentation] Antisense inhibition of neuronal androgen receptor in spinal and bulbar muscular atrophy2015

    • Author(s)
      Kentaro Sahashi, Masahisa Katsuno, Gene Hung, Hiroaki Adachi, Naohide Kondo, Hideaki Nakatsuji, Genki Tohnai, Madoka Iida, C. Frank Bennett, and Gen Sobue
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-26461268
  • [Presentation] Disrupted functional connectivity of amygdala-based networks in Parkinson's disease patients with severe olfactory dysfunction.2015

    • Author(s)
      Watanabe H, Bagarinao E, Yoneyama N, Hara K, Kawabata K, Imai K, Hirayama M, Tsuboi T, Sobue G
    • Organizer
      The 67th AAN Annual Meeting Washington, DC.
    • Place of Presentation
      The Walter E. Washington Convention Center in Washington, DC
    • Year and Date
      2015-04-23
    • Int'l Joint Research
    • Data Source
      KAKENHI-ORGANIZER-26117001
  • [Presentation] ALSの病態と治療:コホート研究から得られるもの2015

    • Author(s)
      祖父江 元
    • Organizer
      第3回日本難病医療ネットワーク学会学術集会
    • Place of Presentation
      仙台国際センター(宮城県仙台市)
    • Year and Date
      2015-11-13
    • Invited
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Presentation] 抗Myelin-associated-glycoprotein抗体陽性ニューロパチーにおけるRituximab療法の有用性2015

    • Author(s)
      川頭 祐一, 池田 昇平, 高橋 美江, 飯島 正博, 小池 春樹, 祖父江 元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] ALSの病態と治療:コホート研究から得られるもの2015

    • Author(s)
      祖父江 元
    • Organizer
      第3回日本難病医療ネットワーク学会学術集会
    • Place of Presentation
      仙台国際センター(宮城県仙台市)
    • Year and Date
      2015-11-13
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 我が国のALS患者に対する非侵襲的換気補助療法(NPPV)の転帰と予後2015

    • Author(s)
      熱田 直樹, 渡辺 はづき, 中村 亮一, 横井 大知, 渡辺 宏久, 伊藤 瑞規, 勝野 雅央, 和泉 唯信, 森田 光哉, 谷口 彰, 織田 雅也, 狩野 修, 溝口 功一, 阿部 康二, 桑原 聡, 梶 龍兒, 祖父江 元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-27
    • Data Source
      KAKENHI-PROJECT-25461277
  • [Presentation] FUS regulates AMPA receptor function and FTLD-associated behavior2015

    • Author(s)
      本田 大祐、宇田川 剛、藤岡 祐介、田中 基樹、永井 拓、山田 清文、横井 聡、石垣 診祐、渡辺 宏久、勝野 雅央、大野 欽司、曽我部 正博、岡戸 晴生、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] 抗SRP抗体陽性筋症の臨床病理学的特徴2015

    • Author(s)
      中西 浩隆, 小池 春樹, 飯島 正博, 野田 成哉, 木村 正剛, 勝野 雅央, 祖父江 元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] MMSEが正常のパーキンソン病に対するACE-Rを用いた高次機能の検討2015

    • Author(s)
      川畑和也,渡辺宏久,米山典孝,原一洋,大嶽れい子,田中康博,坪井崇,渡辺はづき,中村亮一,伊藤瑞規,熱田直樹,祖父江元
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-25461313
  • [Presentation] 封入体筋炎ではTGF-βシグナル伝達の発現が亢進している2015

    • Author(s)
      野田 成哉, 中西 浩隆, 木村 正剛, 飯島 正博, 小池 春樹, 勝野 雅央, 祖父江 元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 認知症制御へ向けた脳タンパク質老化と神経回路の可視化2015

    • Author(s)
      祖父江 元
    • Organizer
      第29回日本医学会総会2015関西
    • Place of Presentation
      京都国際会館(京都府京都市)
    • Year and Date
      2015-04-12
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] ALS/FTLDの病態におけるFUSの役割 Quality loss of function of FUS in ALS/FTLD2015

    • Author(s)
      石垣 診祐、祖父江 元
    • Organizer
      第15回日本蛋白質科学会年会 ワークショップ
    • Place of Presentation
      徳島県 徳島市 あわぎんホール
    • Year and Date
      2015-06-26
    • Invited
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] Cell cycle inhibitor ameliorates motor neuron degeneration induced by polyglutamine-expanded androgen receptor.2015

    • Author(s)
      Katsuno M, Adachi H, Sahashi K, Kondo N, Iida M, Nakatsuji H, Tohnai G, Sobue G.
    • Organizer
      The 26th International Symposium on ALS/MND
    • Place of Presentation
      Orland, USA
    • Year and Date
      2015-12-11
    • Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] 神経変性疾患のdisease-modifying therapyへの展望2015

    • Author(s)
      祖父江 元
    • Organizer
      第104回日本病理学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-05-02
    • Invited
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Presentation] Novel imaging biomarker for early detection of AD2015

    • Author(s)
      祖父江 元
    • Organizer
      nd World Centenarian Initiative International Symposium on Alzheimer’s Disease Prevention Strategy
    • Place of Presentation
      JA共済ビル カンファレンスホール(東京都千代田区)
    • Year and Date
      2015-06-27
    • Invited / Int'l Joint Research
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Presentation] パーキンソン病の自律神経障害2015

    • Author(s)
      祖父江 元
    • Organizer
      第68回日本自律神経学会総会
    • Place of Presentation
      ウインクあいち(愛知県名古屋市)
    • Year and Date
      2015-10-29
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 孤発性 Neuronal intranuclear inclusion disease の臨床症候2015

    • Author(s)
      曽根 淳、 稲垣 智則、勝又 竜、高木 伸之介、森 恵子、荒木 邦彦、岩崎 靖、吉田 眞理、田中 章景、祖父江 元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-25
    • Data Source
      KAKENHI-PROJECT-15K09312
  • [Presentation] dynactin-1ノックアウトマウスを用いた孤発性ALSの病態解析2015

    • Author(s)
      河合香里、池中建介、勝野雅央、井口洋平、勝又竜、田中章景、祖父江元
    • Organizer
      第56回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-26461269
  • [Presentation] 球脊髄性筋萎縮症モデルにおけるタクロリムス誘導体の治療効果2015

    • Author(s)
      藤内玄規, 足立弘明, 勝野雅央, 佐橋健太郎, 近藤直英, 中辻秀朗, 飯田円, 祖父江 元.
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] Loss of FUS causes a decrease in brain volume accompanied with neuronal loss2015

    • Author(s)
      藤岡 祐介、石垣 診祐、横井 聡、本田 大祐、宇田川 剛、岡戸 晴生、渡辺 宏久、勝野 雅央、祖父江 元
    • Organizer
      第56回神経学会学術大会
    • Place of Presentation
      新潟 新潟市 朱鷺メッセ
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-15K09310
  • [Presentation] 神経変性疾患のdisease-modifying therapyへの展望2015

    • Author(s)
      祖父江 元
    • Organizer
      第104回日本病理学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-05-02
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] 認知症制御へ向けた脳タンパク質老化と神経回路の可視化2015

    • Author(s)
      祖父江 元
    • Organizer
      第29回日本医学会総会2015関西
    • Place of Presentation
      京都国際会館(京都府京都市)
    • Year and Date
      2015-04-12
    • Invited
    • Data Source
      KAKENHI-PROJECT-26670439
  • [Presentation] 葉酸欠乏性ニューロパチーの臨床病理学的検討2015

    • Author(s)
      小池春樹、高橋美江、大山健、川頭祐一、飯島正博、土井宏、田中章景、祖父江元
    • Organizer
      第58回日本神経学会学術大会
    • Place of Presentation
      朱鷺メッセ(新潟県新潟市)
    • Year and Date
      2015-05-20
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 筋生検組織病理検査による疾患の診断率と治療法選択への関与2015

    • Author(s)
      木村 正剛, 中西 浩隆, 野田 成哉, 飯島 正博, 小池 春樹, 勝野 雅央, 祖父江 元
    • Organizer
      第33回日本神経治療学会総会
    • Place of Presentation
      名古屋国際会議場(愛知県名古屋市)
    • Year and Date
      2015-11-26
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] ALSとFTLDの研究・治療の現在地を知る 分子病態からみたALSとFTLDの治療戦略2014

    • Author(s)
      熱田 直樹、祖父江 元
    • Organizer
      第32回日本神経治療学会総会
    • Place of Presentation
      東京都文京区(東京ドームホテル)
    • Year and Date
      2014-11-21
    • Invited
    • Data Source
      KAKENHI-PROJECT-25461277
  • [Presentation] Pathogenesis of selective neurodegeneration in polyglutamine-mediated motor neuron disease2014

    • Author(s)
      Katsuno M, Sobue G
    • Organizer
      International symposium. New Frontier of Molecular Neuropathology 2014
    • Place of Presentation
      Tokyo Medical and Dental University, Bunkyo-ku, Tokyo, Japan
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] 回復期脳梗塞リハビリテーションに対するスタチンの効果2014

    • Author(s)
      千田 譲、大山 健、橋詰 淳、伊東 慶一、加納 浩一、小竹 伴照、伊藤 瑞規、熱田 直樹、渡辺 宏久、岸本 秀雄、祖父江 元
    • Organizer
      第39回日本脳卒中学会総会
    • Place of Presentation
      大阪国際会議場(大阪市)
    • Invited
    • Data Source
      KAKENHI-PROJECT-25461312
  • [Presentation] 創薬における医学と薬学の連携2014

    • Author(s)
      祖父江 元
    • Organizer
      第35回日本臨床薬理学会学術総会
    • Place of Presentation
      ひめぎんホール(愛媛県松山市)
    • Year and Date
      2014-12-04
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] ALSの進行を規定する因子の探索同定2014

    • Author(s)
      熱田直樹、渡辺はづき、中村亮一、平川晃弘、中杤昌弘、渡辺宏久、伊藤瑞規、千田譲、和泉唯信、梶龍兒、森田光哉、富山弘幸、谷口彰、溝口功一、狩野修、阿部康二、中野今治、飯田有俊、池川志郎、祖父江元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡県福岡市(福岡国際会議場)
    • Year and Date
      2014-05-24
    • Data Source
      KAKENHI-PROJECT-25461277
  • [Presentation] パーキンソン病における起立時末梢血管収縮不全 を来す背景因子の検討2014

    • Author(s)
      中村 友彦, 岡田 暁典, 鈴木 淳一郎, 水谷 泰彰, 平山 正昭, 祖父江 元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡国際会議場
    • Year and Date
      2014-05-21
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] Pathogenesis of selective neurodegeneration in polyglutamine-mediated motor neuron disease.2014

    • Author(s)
      Katsuno, M., Sobue, G.
    • Organizer
      New Frontier of Molecular Neuropathology 2014
    • Place of Presentation
      東京大学本郷キャンパス 伊藤国際学術研究センター、東京都文京区
    • Invited
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Leptin and ghrelin concentrations and cardiovascular dysautonomia in Parkinson’s disease2014

    • Author(s)
      Tomohiko Nakamura, Yui Okada, Akinori Okada, Junichiro Suzuki, Yasuaki Mizutani, Masaaki Hirayama, Gen Sobue
    • Organizer
      18TH INTERNATIONAL CONGRESS OF PARKINSON'S DISEASE AND MOVEMENT DISORDERS
    • Place of Presentation
      Stockholm, Sweden
    • Data Source
      KAKENHI-PROJECT-24590691
  • [Presentation] Factors affecting longitudinal functional decline and survival in amyotrophic lateral sclerosis patients2014

    • Author(s)
      Hazuki Watanabe, Naoki Atsuta, Ryoichi Nakamura, Akihiro Hirakawa, Hirohisa Watanabe, Mizuki Ito, Masahisa Katsuno, Yuishin Izumi, Mitsuya Morita, Hiroyuki Tomiyama, Akira Taniguchi, Koji Abe, Kouichi Mizoguchi, Osamu Kano, Satoshi Kuwabara, Takashi Imai, Masashi Aoki, Ryuji Kaji, Imaharu Nakano, Gen Sobue
    • Organizer
      The 25th international symposium on ALS/MND
    • Place of Presentation
      Brussels, Belgium,The Square, Brussels Meeting Centre
    • Year and Date
      2014-12-06
    • Data Source
      KAKENHI-PROJECT-25461277
  • [Presentation] perspectives of disease modifying therapy for neurodegenerative disease. Japan - Canada Collaborative Symposium: Motor Neuron Disease Update; En Route to Therapeutic Targets2014

    • Author(s)
      祖父江 元
    • Organizer
      The 37th Annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      パシフィコ横浜(神奈川県横浜市)
    • Year and Date
      2014-09-12
    • Invited
    • Data Source
      KAKENHI-PLANNED-26117002
  • [Presentation] Genistein, a natural product derived from soybeans, ameliorates polyglutamine-mediated motor neuron disease.2013

    • Author(s)
      Adachi, H., Qiang, Q., Hunag, Z., Jinag, Y.M., Katsuno, M., Kondo, N., Miyazaki, Y., Iida, M., Tohnai, G., Nakatsuji, H., Sobue, G.
    • Organizer
      Neuroscience 2013
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Genistein, a natural product derived from soybeans, ameliorates polyglutamine-mediated motor neuron disease.2013

    • Author(s)
      Adachi, H., Qiang, Q., Hunag, Z., Jinag, Y.M., Katsuno, M., Kondo, N., Miyazaki, Y., Iida, M., Tohnai, G., Nakatsuji, H., Sobue, G.
    • Organizer
      Neuroscience 2013
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] miR-196aはCELF2の発現抑制を介しSBMAの表現型を有意に改善する2013

    • Author(s)
      宮崎 雄, 足立弘明, 勝野雅央, 村松慎一, 祖父江 元
    • Organizer
      第54回日本神経学会総会
    • Place of Presentation
      東京都千代田区 (東京国際フォーラム)
    • Data Source
      KAKENHI-PROJECT-23390231
  • [Presentation] 筋萎縮性側索硬化症の大脳病変脳容積・拡散テンソルVoxel-Based Analysis法を用いた検討2013

    • Author(s)
      千田 譲、陸 雄一、桝田 道人、坪井 崇、原 一洋、渡辺 はづき、中村 亮一、伊藤 瑞規、熱田 直樹、渡辺 宏久、長縄 慎二、祖父江 元
    • Organizer
      第54回日本神経学会学術大会
    • Place of Presentation
      東京国際フォーラム(東京都千代田区)
    • Invited
    • Data Source
      KAKENHI-PROJECT-25461312
  • [Presentation] Heat shock factor-1 (Hsf-1) controls pathological lesion distribution of polyglutamine-induced motor neuron disease.2013

    • Author(s)
      Kondo, N., Katsuno, M., Adachi, H., Minamiyama, M., Matsumoto, S., Nakatsuji, H., Miyazaki, Y., Iida, M., Tohnai, G., Sobue, G.
    • Organizer
      The 24th International Symposium on ALS/MND
    • Place of Presentation
      Milan, Italy
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 多系統萎縮症のhead-up tilt試験における末梢血管抵抗変化と起立性低血圧との関連2013

    • Author(s)
      岡田暁典 鈴木淳一郎 水谷泰彰 中村友彦 平山正昭 祖父江元
    • Organizer
      日本自律神経学会総会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] miR-196aはCELF2の発現抑制を介しSBMAの表現型を有意に改善する2013

    • Author(s)
      宮崎雄, 足立弘明 , 勝野雅央, 村松慎一, 祖父江元
    • Organizer
      第54回日本神経学会総会, 東京都千代田区
    • Place of Presentation
      東京国際フォーラム
    • Year and Date
      2013-05-31
    • Data Source
      KAKENHI-PROJECT-23390231
  • [Presentation] Genistein, a natural product derived from soybeans, ameliorates polyglutamine-mediated motor neuron disease.2013

    • Author(s)
      Adachi, H., Qiang, Q., Hunag, Z., Jinag, Y.M., Katsuno, M., Kondo, N., Miyazaki, Y., Iida, M., Tohnai, G., Nakatsuji, H., Sobue, G.
    • Organizer
      Neuroscience 2013
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Heat shock factor-1 (Hsf-1) controls pathological lesion distribution of polyglutamine-induced motor neuron disease.2013

    • Author(s)
      Kondo, N., Katsuno, M., Adachi, H., Minamiyama, M., Matsumoto, S., Nakatsuji, H., Miyazaki, Y., Iida, M., Tohnai, G., Sobue, G.
    • Organizer
      The 24th International Symposium on ALS/MND
    • Place of Presentation
      Milan, Italy
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] 尿中8-OHdGを用いたパーキンソン病における酸化的ストレスの変化2013

    • Author(s)
      平山正昭、後藤沙絵、中村友彦、水谷泰彰、鈴木淳一郎、渡邊宏久、祖父江元
    • Organizer
      パーキンソン病・運動障害疾患コングレス
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] Molecular targeted therapy for spinal and bulbar muscular atrophy2013

    • Author(s)
      Sobue G
    • Organizer
      Gordon Research Conference CAG Triplet Repeat Disorders
    • Place of Presentation
      Waterville Valley, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Genistein, a natural product derived from soybeans, ameliorates polyglutamine-mediated motor neuron disease2013

    • Author(s)
      Adachi H, Qiang Q, Hunag Z, Jinag YM, Katsuno M, Kondo N, Miyazaki Y, Iida M, Tohnai G, Nakatsuji H, Sobue G
    • Organizer
      Neuroscience 2013
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] パーキンソン病における起立時末梢血管収縮不全を来す背景因子に関する検討2013

    • Author(s)
      中村 友彦 岡田 暁典 鈴木 淳一郎 水谷 泰彰 平山 正昭 祖父江元
    • Organizer
      日本自律神経学会総会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] パーキンソン病では早期から嗅覚機能と心血管系自律神経機能が並行して障害される2013

    • Author(s)
      水谷 泰彰 岡田 暁典 鈴木 淳一郎 中村 友彦 平山 正昭 祖父江 元
    • Organizer
      日本自律神経学会総会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] TAG-1欠損マウスにおける 実験的自己免疫性神経炎による臨床病理学的解析2013

    • Author(s)
      飯島正博、小池春樹、川頭祐一、橋本里奈、大山健、高橋美江、祖父江元
    • Organizer
      第24回日本末梢神経学会
    • Place of Presentation
      朱鷺メッセ 新潟コンベンションセンター、新潟市
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] Deficits in brain-derived neurotrophic factor may underlie motor dysfunction in spinal bulbar muscular atrophy.2013

    • Author(s)
      Hlievski, K., Henley, C.L., Fu, M., Katsuno, M., Adachi, H., Sobue, G., Breedlove, S.M., Jordan, C.L.
    • Organizer
      Neuroscience 2013
    • Place of Presentation
      San Diego,USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Molecular targeted therapy for spinal and bulbar muscular atrophy.2013

    • Author(s)
      Sobue G.
    • Organizer
      Gordon Research Conference CAG Triplet Repeat Disorders
    • Place of Presentation
      Waterville Valley, USA
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Deficits in brain-derived neurotrophic factor may underlie motor dysfunction in spinal bulbar muscular atrophy.2013

    • Author(s)
      Hlievski, K., Henley, C.L., Fu, M., Katsuno, M., Adachi, H., Sobue, G., Breedlove, S.M., Jordan, C.L.
    • Organizer
      Neuroscience 2013
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] What can we learn from Kennedy's disease for amyotrophic lateral sclerosis/motor neuron disease2013

    • Author(s)
      Sobue G
    • Organizer
      World Congress of Neurology 2013
    • Place of Presentation
      Vienna
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] RESOLVEを用いた進行性核上性麻痺に おける上小脳脚病変の検討2013

    • Author(s)
      原一洋、渡辺宏久、伊藤瑞規、祖父江元他
    • Organizer
      第54回日本神経学会学術大会
    • Place of Presentation
      東京都千代田区、国際フォーラム
    • Data Source
      KAKENHI-PROJECT-25461313
  • [Presentation] What can we learn from Kennedy's disease for amyotrophic lateral sclerosis/motor neuron disease.2013

    • Author(s)
      Sobue G.
    • Organizer
      World Congress of Neurology 2013
    • Place of Presentation
      Vienna, Austria
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Cortical and subcortical brain atrophy in Parkinson’s disease with visual hallucination.2013

    • Author(s)
      H. Watanabe, J. Senda, S. Kato, M. Ito, N. Atsuta, K. Hara, T. Tsuboi, M. Katsuno, T. Nakamura, M. Hirayama, S. Naganawa, G. Sobue.
    • Organizer
      17th International Congress of Parkinson’s Disease and Movement Disorders
    • Place of Presentation
      Australia,Sydney
    • Data Source
      KAKENHI-PROJECT-24591293
  • [Presentation] Deficits in brain-derived neurotrophic factor may underlie motor dysfunction in spinal bulbar muscular atrophy.2013

    • Author(s)
      Hlievski, K., Henley, C.L., Fu, M., Katsuno, M., Adachi, H., Sobue, G., Breedlove, S.M., Jordan, C.L.
    • Organizer
      Neuroscience 2013
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Genistein, a natural product derived from soybeans, ameliorates polyglutamine-mediated motor neuron disease2013

    • Author(s)
      Adachi H, Qiang Q, Hunag Z, Jinag YM, Katsuno M, Kondo N, Miyazaki Y, Iida M, Tohnai G, Nakatsuji H, Sobue G
    • Organizer
      Neuroscience 2013
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] パーキンソン病の心血管系自律神経障害におけるグレリン、レプチンの関与の検討2013

    • Author(s)
      中村友彦 岡田ゆい 岡田暁典 鈴木淳一郎 水谷泰彰 平山正昭 祖父江元
    • Organizer
      第7回パーキンソン病・運動障害疾患コングレス
    • Place of Presentation
      京王プラザホテル(東京都 新宿区)
    • Data Source
      KAKENHI-PROJECT-24590691
  • [Presentation] 123I-meta-iodobenzylguanidine(MIBG)心筋シンチグラフィー2013

    • Author(s)
      渡辺 宏久 中村 友彦 平山 正昭 祖父江 元
    • Organizer
      日本自律神経学会総会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] Brain degeneration in ALS patients as detected by VBM and DTI: similarities with FTLD2013

    • Author(s)
      Joe Senda, Michihito Masuda, Yuichi Riku, Kazuhiro Hara, Takashi Tsuboi, Ryoichi Nakamura, Hazuki Watanabe, Mizuki Ito, Naoki Atsuta, Hirohisa Watanabe, Shinji Naganawa, Gen Sobue.
    • Organizer
      19th Organization of Human Brain Mapping
    • Place of Presentation
      Seattle. USA
    • Invited
    • Data Source
      KAKENHI-PROJECT-25461312
  • [Presentation] Heat shock factor-1 (Hsf-1) controls pathological lesion distribution of polyglutamine-induced motor neuron disease.2013

    • Author(s)
      Kondo, N., Katsuno, M., Adachi, H., Minamiyama, M., Matsumoto, S., Nakatsuji, H., Miyazaki, Y., Iida, M., Tohnai, G., Sobue, G.
    • Organizer
      The 24th International Symposium on ALS/MND
    • Place of Presentation
      Milan, Italy
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] 感覚神経伝導速度を用いた球脊髄性筋萎縮症と筋萎縮性側索硬化症の鑑別2012

    • Author(s)
      後藤 沙絵, 岡田 有以, 平山 正昭, 濱 哲夫, 中村 友彦, 勝野 雅央, 坂野 晴彦, 鈴木 啓介, 祖父江 元
    • Organizer
      第23回日本末梢神経学会
    • Place of Presentation
      福岡
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] miR-196aはSBMAにおいて異常ARmRNAの不安定化を促進し表現型を有意に改善させる2012

    • Author(s)
      宮崎雄, 足立弘明, 勝野雅央, 南山誠, 蒋月梅, 土井英樹, 松本慎二郎, 近藤直英, 飯田円, 藤内玄規, 田中章景, 村松慎一, 祖父江元
    • Organizer
      第53回日本神経学会総会
    • Place of Presentation
      東京千代田区(東京国際フォーラム)
    • Year and Date
      2012-05-24
    • Data Source
      KAKENHI-PROJECT-23390231
  • [Presentation] 血圧と自律神経障害 神経疾患の起立性低血圧2012

    • Author(s)
      中村 友彦, 平山 正昭, 祖父江 元
    • Organizer
      第65回日本自律神経学会
    • Place of Presentation
      東京
    • Invited
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] FUS regulates alternative splicing patterns of Mapt by cooperating with PSF/SFPQ: a novel link between FUS and Tau in the pathogenesis of ALS and FTLD2012

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Yohei Okada, Akio Masuda, Kinji Ohno, and Gen Sobue
    • Organizer
      The 35th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      Nagoya, Japan
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] ALS における FUS/TLSの質的機能喪失と病態:FUS/TLS の核内高分子複合体の機能解析から2012

    • Author(s)
      石垣 診祐、藤岡 祐介、田中 章景、祖父江 元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] Naratriptan ameliorates SBMA pathology by the repression of CGRP1-activated JNK pathway2012

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Iida M, Ishigaki S, Fujioka Y, Matsumoto S, Miyazaki Y, Tanaka F, Kurihara H, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Viral delivery of miR-196a ameliorates the SBMA phenotype via the silencing of CELF22012

    • Author(s)
      Miyazaki Y, Adachi H, Katsuno M, Tanaka F, Muramatsu SI, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] 家族性ALS原因遺伝子FUS/TLSノックダウンに伴う選択的splicing変化2012

    • Author(s)
      藤岡 祐介、石垣 診祐、増田 章男、大野 欽司、祖父江 元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] パーキンソン病の自律神経進展形式の検討2012

    • Author(s)
      平山 正昭, 中村 友彦, 原 敬史, 水谷 泰彰, 後藤 沙絵, 渡邊 宏久, 祖父江 元
    • Organizer
      第53回日本神経学会総会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] 抗Myelin-Associated Glycoprotein (MAG)抗体陽性IgM-MGUSニューロパチーにおける重症度と治療効果に影響する因子2012

    • Author(s)
      川頭祐一(名古屋大学 神経内科),橋本里奈,冨田稔,飯島正博,小池春樹,祖父江元
    • Organizer
      日本末梢神経学会
    • Place of Presentation
      福岡
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Presentation] 族性 ALS 原因遺伝子 FUS/TLS ノックダウンに伴う選択的 splicing 変化2012

    • Author(s)
      藤岡 祐介、石垣 診祐、増田 章男、大野 欽司、祖父江 元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] p62/SQSTM1 removes toxic mutant androgen receptor in spinal bulbar muscular atrophy model mouse2012

    • Author(s)
      Adachi H, Doi H, Katsuno M, Matsumoto S, Kondo N, Miyazaki Y, Tohnai G, Iida M, Tanaka F, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] 筋萎縮性側索硬化症、及びそのモデルマウスの腰髄におけるリン酸化Cofilinの評価2012

    • Author(s)
      勝又 竜, 勝野雅央, 田中章景, 祖父江元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京国際フォーラム(東京都)
    • Year and Date
      2012-05-25
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Naratriptan ameliorates SBMA pathology by the repression of CGRP1-activated JNK pathway.2012

    • Author(s)
      Minamiyama, M., Katsuno, M., Adachi, H., Doi, H., Kondo, N., Iida, M., Ishigaki, S., Fujioka, Y., Matsumoto, S., Miyazaki, Y., Tanaka, F., Kurihara, H., Sobue, G.
    • Organizer
      Neuroscience 2012.
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 多系統萎縮症における volmetry・拡散テンソル画像を用いた大脳病変の広がり2012

    • Author(s)
      伊藤瑞規、渡辺宏久、熱田直樹、千田譲、加藤重典、中村亮一、渡辺はづき、原一洋、坪井崇、長縄慎二、祖父江元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-22590955
  • [Presentation] FUS regulates alternative splicing patterns of Mapt by cooperating with PSF/SFPQ: a novel link between FUS and Tau in the pathogenesis of ALS and FTLD.2012

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Yohei Okada, Akio Masuda, Kinji Ohno, and Gen Sobue
    • Organizer
      The 35th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] Comparison of Fus-regulating gene expression and alternative splicing profiles among different cell lineages in the central nervous system.2012

    • Author(s)
      Ishigaki S, Fujioka Y, Masuda A, Iguchi Y, Katsuno M, Ohno K, Sobue G.
    • Organizer
      42nd Society for Neuroscience annual meeting
    • Place of Presentation
      New Orleans, USA
    • Year and Date
      2012-10-13
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] p62/SQSTM1 removes toxic mutant androgen receptor in spinal bulbar muscular atrophy model mouse2012

    • Author(s)
      Adachi H, Doi H, Katsuno M, Matsumoto S, Kondo N, Miyazaki Y, Tohnai G, Iida M, Tanaka F, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 高度の神経肥厚を特徴とする慢性炎症性脱髄性多発根ニューロパチーの臨床病理学的検討2012

    • Author(s)
      飯島 正博(名古屋大学 神経内科), 両角佐織, 小池 春樹, 川頭 祐一, 冨田 稔,橋本 里奈, 大山 健, 祖父江 元
    • Organizer
      日本神経免疫学会
    • Place of Presentation
      軽井沢
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Presentation] Comparison of Fus-regulating gene expression and alternative splicing profiles among different primary cells in central nervous system2012

    • Author(s)
      Yusuke Fujioka, Shinsuke Ishigaki, Akio Masuda, Kinji Ohno, and Gen Sobue
    • Organizer
      The 35th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      Nagoya, Japan
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] Viral delivery of miR-196a ameliorates the SBMA phenotype via the silencing of CELF22012

    • Author(s)
      Miyazaki Y, Adachi H, Katsuno M, Tanaka F, Muramatsu S, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans
    • Year and Date
      2012-10-16
    • Data Source
      KAKENHI-PROJECT-23390231
  • [Presentation] Naratriptan ameliorates SBMA pathology by the repression of CGRP1-activated JNK pathway.2012

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Iida M, Ishigaki S, Fujioka Y, Matsumoto S, Miyazaki Y, Tanaka F, Kurihara H, Sobue G.
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Loss of TDP-43 Results In Age-dependent Progressive Motor Impairment And Neuropathological Alterations, Mimicking Motor Neuron Disease.2012

    • Author(s)
      Iguchi Y, Katsuno M, Niwa JI, Yamanaka K, Takahashi R, Misawa H, Sasaki S, Sobue G.
    • Organizer
      24th ALS/MND international symposium.
    • Place of Presentation
      Chicago, USA
    • Year and Date
      2012-12-04
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Naratriptan ameliorates SBMA pathology by the repression of CGRP1-activated JNK pathway2012

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Iida M, Ishigaki S, Fujioka Y, Matsumoto S, Miyazaki Y, Tanaka F, Kurihara H, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] FUS regulates alternative splicing patterns of Mapt by cooperating with PSF/SFPQ in neurons: a novel link between FUS and Tau in the pathogenesis of ALS and FTLD2012

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, and Gen Sobue
    • Organizer
      6th International Symposium of Nanomedicine
    • Place of Presentation
      Matsue, Japan
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] Characteristics of hypertrophic form in chronic inflammatory demyelinating polyneuropathy. Inflammatory Neuropathy consortium2012

    • Author(s)
      Masahiro Iijima, Ken Ohyama, Rina Hashimoto, Minoru Tomita, Yuichi Kawagashira, Haruki Koike, Gen Sobue
    • Organizer
      Inflammatory Neuropathy Consortium
    • Place of Presentation
      Rotterdam, Netherland.
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Presentation] Cell cycle dysregulation in motor neurons of spinal and bulbar muscular atrophy (SBMA).2012

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Nakatsuji H, Tanaka F, Sobue G.
    • Organizer
      23rd International Symposium on ALS/MND.
    • Place of Presentation
      Chicago, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] 抗Myelin-associated-glycoprotein抗体陽性IgM-MGUSニューロパチーにおけるRituximab療法の有用性2012

    • Author(s)
      川頭祐一(名古屋大学 神経内科),大山健,橋本里奈,冨田稔,飯島正博,小池春樹,祖父江元
    • Organizer
      日本神経免疫学会
    • Place of Presentation
      軽井沢
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Presentation] Cell cycle dysregulation in motor neurons of spinal and bulbar muscular atrophy (SBMA)2012

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Nakatsuji H, Tanaka F, Sobue G
    • Organizer
      23rd International Symposium on ALS/MND
    • Place of Presentation
      Chicago, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] 運動ニューロン特異的TDP-43ノックアウトマウスの病態解析2012

    • Author(s)
      井口洋平, 勝野雅央, 丹羽淳一, 高木伸之介, 田中章景, 祖父江元
    • Organizer
      第53回日本神経学会学術大会.
    • Place of Presentation
      東京国際フォーラム(東京都)
    • Year and Date
      2012-05-25
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] p62/SQSTM1 removes toxic mutant androgen receptor in spinal bulbar muscular atrophy model mouse.2012

    • Author(s)
      Adachi, H., Doi, H., Katsuno, M., Matsumoto, S., Kondo, N., Miyazaki, Y., Tohnai, G., Iida, M., Tanaka, F., Sobue, G.
    • Organizer
      Neuroscience 2012.
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 幻視を呈するパーキンソン病におけるvoxel based morphometry所見2012

    • Author(s)
      渡辺 宏久, 千田 譲, 加藤 重典, 伊藤 瑞規, 熱田 直樹, 渡辺 はづき, 原 一洋, 坪井 崇, 中村 亮一, 長縄 慎二, 祖父江 元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-24591293
  • [Presentation] Impaired pain processing in Parkinson's disease and its relative association with the sense of smell2012

    • Author(s)
      Masaaki Hirayama, Takashi Hara, Yasuaki Mizutani, Tetsuo Hama , Norio Hori Tomohiko Nakamura, Shigenori Kato, Hirohisa Watanabe,Gen Sobue
    • Organizer
      16 th international congress of Parkinson7S disease and movement disorders
    • Place of Presentation
      dublin
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] Comparison of Fus-regulating gene expression and alternative splicing profiles among different cell lineages in the central nervous system2012

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Akio Masuda, Yohei Iguchi, Masahisa Katsuno, Kinji Ohno, and Gen Sobue
    • Organizer
      The 42nd Society for Neuroscience annual meeting
    • Place of Presentation
      New Orleans, LA USA
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] Viral delivery of miR-196a ameliorates the SBMA phenotype via the silencing of CELF2.2012

    • Author(s)
      Miyazaki, Y., Adachi, H., Katsuno, M., Tanaka, F., Muramatsu, S.I., Sobue, G.
    • Organizer
      Neuroscience 2012.
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Comparison of Fus-regulating gene expression and alternative splicing profiles among different primary cells in central nervous system2012

    • Author(s)
      Yusuke Fujioka, Shinsuke Ishigaki, Akio Masuda, Kinji Ohno, and Gen Sobue
    • Organizer
      The 35th annual Meeting of the Japan Neuroscience Society
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] Comparison of Fus-regulating gene expression and alternative splicing profiles among different cell lineages in the central nervous system2012

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, Akio Masuda, Yohei Iguchi, Masahisa Katsuno, Kinji Ohno, and Gen Sobue
    • Organizer
      The 42nd Society for Neuroscience annual meeting
    • Place of Presentation
      New Orleans, LA
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] Viral delivery of miR-196a ameliorates the SBMA phenotype via the silencing of CELF22012

    • Author(s)
      Miyazaki Y, Adachi H, Katsuno M, Tanaka F, Muramatsu SI, Sobue G
    • Organizer
      Neuroscience 2012
    • Place of Presentation
      New Orleans, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Longitudinal changes of outcome measures in spinal and bulbar muscular atrophy.2012

    • Author(s)
      Hashizume A, Katsuno M, Banno H, Suzuki K, Suga N, Mano T, Atsuta N, Oe H, Watanabe H, Tanaka F, Sobue G.
    • Organizer
      23rd International Symposium on ALS/MND.
    • Place of Presentation
      Chicago, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Impaired cardiac response and its relationship with orthostatic hypotension in Parkinson's disease2012

    • Author(s)
      Tomohiko Nakamura, Takashi Hara, Yasuaki Mizutani, Hirohisa Watanabe, Masaaki Hirayama, Gen Sobue
    • Organizer
      16th International Congress of Parkinson's Disease and Movement Disorders
    • Place of Presentation
      dublin
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] ALSにおけるFUS/TLSの質的機能喪失と病態:FUS/TLSの核内高分子複合体の機能解析から2012

    • Author(s)
      石垣 診祐、 藤岡 祐介、 田中 章景、 祖父江 元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] 高度の神経肥厚を特徴とする慢性炎症性脱髄性多発根ニューロパチーの検討2012

    • Author(s)
      飯島 正博(名古屋大学 神経内科), 両角佐織, 小池 春樹, 川頭 祐一, 冨田 稔, 橋本 里奈, 大山 健, 祖父江 元
    • Organizer
      日本末梢神経学会
    • Place of Presentation
      福岡
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Presentation] CGRP1 is the new therapeutic target for SBMA (Spinal and Bulbar Muscular Atrophy).2012

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Iida M, Ishigaki S, Fujioka Y, Matsumoto S, Miyazaki Y, Tanaka F, Kurihara H, Sobue G.
    • Organizer
      11th Biennial Meeting of the Asian Pacific Society for Neurochemistry.
    • Place of Presentation
      神戸国際会議場(神戸)
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Cell cycle dysregulation in motor neurons of spinal and bulbar muscular atrophy (SBMA)2012

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Nakatsuji H, Tanaka F, Sobue G
    • Organizer
      23rd International Symposium on ALS/MND
    • Place of Presentation
      Chicago, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] dynactin-1ノックアウトによる孤発性ALSモデルマウスの作成と病態解析2012

    • Author(s)
      河合 香里, 池中建介, 勝又 竜, 井口洋平, 勝野雅央, 田中章景, 祖父江元
    • Organizer
      第53回日本神経学会学術大会
    • Place of Presentation
      東京国際フォーラム(東京都)
    • Year and Date
      2012-05-25
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Heat shock factor-1(HSF-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA).2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Tanaka F, Sobue G.
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      パシフィコ横浜(神奈川)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Cell cycle dysregulation in spinal and bulbar muscular atrophy (SBMA).2011

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G.
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy,
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] A peony extract enhances protein degradation systems and exerts therapeutic effects in the polyglutamine-mediated motor neuron disease2011

    • Author(s)
      Adachi H, Tohnai G, Katsuno M, Minamiyama M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Tanaka F, Ohtsuka K, Sobue G
    • Organizer
      Neuroscience 2011
    • Place of Presentation
      Washington DC, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Cell cycle dysregulation in spinal and bulbar muscular atrophy (SBMA).2011

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Kondo N, Doi H, Matsumoto S, Miyazaki Y, Tanaka F, Sobue G.
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      パシフィコ横浜(神奈川)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Dynactin-1を標的とした孤発性ALS モデルの開発2011

    • Author(s)
      田中章景, 池中建介, 祖父江元
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知県)
    • Year and Date
      2011-05-20
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Cell cycle dysregulation in spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Molecular pathology of SBMA (Spinal Bulbar Muscular Atrophy) related gene CGRP12011

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Tanaka F, Sobue G, Kurihara H
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Pain related SEP and cortical SEP in Parkinson's disease Asian and Oceanian Par2011

    • Author(s)
      Masaaki HIRAYAMA, Tetsuo HAMA, Takashi HARA, Tomohiko NAKAMURA, Gen SOBUE
    • Organizer
      Asian and Oceanian Parkinson's disease and movement disorder
    • Year and Date
      2011-03-25
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Presentation] 神経変性疾患の病態抑止治療への展望2011

    • Author(s)
      田中章景, 祖父江元
    • Organizer
      第6回臨床ストレス応答学会大会
    • Place of Presentation
      名古屋大学医学部 (愛知県)
    • Year and Date
      2011-11-05
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Cell cycle dysregulation in spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Kondo N, Doi H, Matsumoto S, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Heat shock factor-1 (Hsf-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Correlations between fatigue and cardiovascular autonomic dysfunction in Parkinson's disease2011

    • Author(s)
      Tomohiko Nakamura, Takashi Hara, Tetsuo Hama, Hirohisa Watanabe, Masaaki Hirayama, Gen Sobue
    • Organizer
      Asian and Oceanian Parkinson's disease and movement disorder
    • Place of Presentation
      Taipei
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Presentation] Gene expression analysis of biopsied nerve in Japanese CIDP patients2011

    • Author(s)
      Masahiro Iijima, Haruki Koike, Yuichi Kawagashira, Minoru Tomita, Rina Hashimoto, Gen Sobue
    • Organizer
      Peripheral Nerve Society
    • Place of Presentation
      Washington DC., U.S.A
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Presentation] Central motor conduction time (CMCT) in patients with spinal and bulbar muscular atrophy (SBMA).2011

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Suga N, Hashizume A, Hara T, Hama T, Nakamura T, Hirayama M, Tanaka F, Sobue G.
    • Organizer
      15th Congress of the European Federation of Neurological Societies
    • Place of Presentation
      Budapest, Hungary
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Heat shock factor-1 (Hsf-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] 球脊髄性筋萎縮症モデルマウスにおける異常蛋白凝集の病理学的分布はHsf-1の影響を受ける2011

    • Author(s)
      近藤直英, 勝野雅央, 足立弘明, 南山誠, 土井英樹, 松本慎二郎, 宮崎雄, 飯田円, 田中章景, 祖父江元
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Long-term effects of the luteinizing hormone-releasing hormone analogues for spinal and bulbar muscular atrophy.2011

    • Author(s)
      Ota K, Ishikawa K, Suzuki K, Banno H, Katsuno M, Sobue G, Mizusawa H.
    • Organizer
      63rd American Academy of Neurology Annual Meeting
    • Place of Presentation
      Honolulu, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Molecular pathology of SBMA (Spinal Bulbar Muscular Atrophy) related gene CGRP1.2011

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Tanaka F, Sobue G, Kurihara H.
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      パシフィコ横浜(神奈川)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Diagnosis of sporadic transthyretin Val30Met familial amyloid polyneuropathy : a practicalanalysis2011

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Tanaka F, Sobue G
    • Organizer
      2011 PNS Biennial Meeting, Potomac
    • Place of Presentation
      Maryland
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Presentation] 球脊髄性筋萎縮症(SBMA)病態関連遺伝子CGRP1の分子機構2011

    • Author(s)
      南山 誠, 勝野雅央, 足立弘明, 土井英樹, 近藤直英, 田中章景, 祖父江 元, 栗原裕基.
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 球脊髄性筋萎縮症における細胞周期異常2011

    • Author(s)
      勝野雅央, 足立弘明, 南山誠, 土井英樹, 近藤直英, 松本慎二郎, 宮崎雄, 坂野晴彦, 鈴木啓介, 田中章景, 祖父江元
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Molecular pathogenesis and translational research in spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Sobue G
    • Organizer
      22th International Symposium on ALS/MND
    • Place of Presentation
      Sydney, Australia
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Heat shock factor-1 (HSF-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Tanaka F, Sobue G
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Molecular pathology of SBMA (Spinal Bulbar Muscular Atrophy) related gene CGRP12011

    • Author(s)
      Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Tanaka F, Sobue G, Kurihara H
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Diagnosis of sporadic transthyretin Val30Met familial amyloid polyneuropathy: a practical analysis2011

    • Author(s)
      Koike H, Hashimoto R, Tomita M, Kawagashira Y, Iijima M, Tanaka F, Sobue G
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto, Japan
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Presentation] Long-term effects of the luteinizing hormone-releasing hormone analogues for spinal and bulbar muscular atrophy2011

    • Author(s)
      Ota K, Ishikawa K, Suzuki K, Banno H, Katsuno M, Sobue G, Mizusawa H
    • Organizer
      63rd American Academy of Neurology Annual Meeting
    • Place of Presentation
      Honolulu, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Late-onset familial amyloid polyneuro pathy in Japan2011

    • Author(s)
      Koike H, Sobue G
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto, Japan
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Presentation] Quality loss of FUS function is involved in the pathogenesis of ALS.2011

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, and Gen Sobue
    • Organizer
      The 41th Society for Neuroscience annual meeting.
    • Place of Presentation
      Washington, DC.
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] 球脊髄性筋萎縮症における細胞周期異常.2011

    • Author(s)
      勝野雅央, 足立弘明, 南山 誠, 土井英樹, 近藤直英, 松本慎二郎, 宮崎 雄, 坂野晴彦, 鈴木啓介, 田中章景, 祖父江 元.
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 多系統萎縮症における経時的なvolumetry・拡散テンソル像の検討~第三報~2011

    • Author(s)
      伊藤瑞規、渡辺宏久、熱田直樹、千田譲、加藤重典、中村亮一、長縄慎二、祖父江元
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-22590955
  • [Presentation] 分化運動ニューロンを用いたFUS/TLSノックダウンモデルの作成と機能解析2011

    • Author(s)
      藤岡祐介、石垣診祐、祖父江元
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場 名古屋
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] 球脊髄性筋萎縮症モデルマウスにおける異常蛋白凝集の病理学的分布はHsf-1の影響を受ける2011

    • Author(s)
      近藤直英, 勝野雅央, 足立弘明, 南山誠, 土井英樹, 松本慎二郎, 宮崎雄, 飯田円, 田中章景, 祖父江元
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] A peony extract enhances protein degradation systems and exerts therapeutic effects in the polyglutamine-mediated motor neuron disease2011

    • Author(s)
      Adachi H, Tohnai G, Katsuno M, Minamiyama M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Tanaka F, Ohtsuka K, Sobue G
    • Organizer
      Neuroscience 2011
    • Place of Presentation
      Washington DC, USA
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Profiles of differential gene expression and alternative splicing in FUS knock-down primary motor neurons.2011

    • Author(s)
      Yusuke Fujioka, Shinsuke Ishigaki, and Gen Sobue
    • Organizer
      The 41th Society for Neuroscience annual meeting
    • Place of Presentation
      Washington, DC.
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] 球脊髄性筋萎縮症(SBMA)病態関連遺伝子CGRP1の分子機構2011

    • Author(s)
      南山誠, 勝野雅央, 足立弘明, 土井英樹, 近藤直英, 田中章景, 祖父江元, 栗原裕基
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Heat shock factor-1(Hsf-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Heat shock factor-1(HSF-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Tanaka F, Sobue G
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] 球脊髄性筋萎縮症(SBMA)病態関連遺伝子CGRP1の分子機構2011

    • Author(s)
      南山誠, 勝野雅央, 足立弘明, 土井英樹, 近藤直英, 田中章景, 祖父江元, 栗原裕基.
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Quality loss of FUS function is involved in the pathogenesis of ALS.2011

    • Author(s)
      Shinsuke Ishigaki, Yusuke Fujioka, and Gen Sobue
    • Organizer
      The 3rd Global COE International Symposium .
    • Place of Presentation
      ミッドランドホール Nagoya, Japan.
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] dynactin-1ノックダウン線虫を用いた孤発性ALS (SALS) 軸索輸送障害モデルの作成2011

    • Author(s)
      池中建介, 河合香里, 蒋月梅, 黄哲, 勝野雅央, 田中章景, 祖父江元
    • Organizer
      第54回日本神経化学大会
    • Place of Presentation
      山代温泉瑠璃光(石川県)
    • Year and Date
      2011-09-28
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] 運動ニューロンにおけるALS関連変異FUS/TLSの機能障害2011

    • Author(s)
      石垣診祐、藤岡祐介、田中章景、祖父江元
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場 名古屋
    • Data Source
      KAKENHI-PROJECT-23659452
  • [Presentation] 球脊髄性筋萎縮症モデルマウスにおける異常蛋白凝集の病理学的分布はHsf-1の影響を受ける.2011

    • Author(s)
      近藤直英, 勝野雅央, 足立弘明, 南山誠, 土井英樹, 松本慎二郎, 宮崎雄, 飯田円, 田中章景, 祖父江元.
    • Organizer
      第52回日本神経学会学術大会
    • Place of Presentation
      名古屋国際会議場(愛知)
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Central motor conduction time (CMCT) in patients with spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Suga N, Hashizume A, Hara T, Hama T, Nakamura T, Hirayama M, Tanaka F, Sobue G
    • Organizer
      15th Congress of the European Federation of Neurological Societies
    • Place of Presentation
      Budapest, Hungary
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Central motor conduction time (CMCT) in patients with spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Suzuki K, Katsuno M, Banno H, Suga N, Hashizume A, Hara T, Hama T, Nakamura T, Hirayama M, Tanaka F, Sobue G
    • Organizer
      15th Congress of the European Federation of Neurological Societies
    • Place of Presentation
      Budapest, Hungary
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] パーキンソン病における痛み関連電位および皮質SEP2011

    • Author(s)
      濱哲夫、平山正昭、原敬史、中村友彦、祖父江元
    • Organizer
      第52回日本神経学会学術大会
    • Year and Date
      2011-05-18
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Presentation] Long-term effects of the luteinizing hormone-releasing hormone analogues for spinal and bulbar muscular atrophy2011

    • Author(s)
      Ota K, Ishikawa K, Suzuki K, Banno H, Katsuno M, Sobue G, Mizusawa H
    • Organizer
      63rd American Academy of Neurology Annual Meeting
    • Place of Presentation
      Honolulu, USA
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Effect of leuprorelin in patients with spinal and bulbar muscular atrophy (SBMA) : a multicenter, randomized, double-blind, placebo-controlled trial2011

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Yabe I, Sasaki H, Aoki M, Morita M, Nakano I, Kanai K, Ito S, Ishikawa K, Mizusawa H, Yamamoto T, Tsuji S, Hasegawa K, Shimohata T, Nishizawa M, Miyajima H, Kanda F, Watanabe Y, Nakashima K, Tsujino A, Yamashita T, Uchino M, Fujimoto Y, Tanaka F, Sobue G; for the Japan SBMA Interventional Trial for TAP-144-SR (JASMITT) study group
    • Organizer
      63rd American Academy of Neurology Annual Meeting
    • Place of Presentation
      Honolulu, USA
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Heat shock factor-1 (Hsf-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA).2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G.
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy,
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Cell cycle dysregulation in spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] PAIN RELATED SEP AND CORTICAL SEP IN PARKINSON'S DISEASE2011

    • Author(s)
      Masaaki HIRAYAMA, Tetsuo HAMA, Takashi HARA, Tomohiko NAKAMURA, Gen SOBUE
    • Organizer
      Asian and Oceanian Parkinson's disease and movement disorder
    • Place of Presentation
      Taipei
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Presentation] Heat shock factor-1(Hsf-1) influences distribution of pathogenic androgen receptor aggregations in model mouse of spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Systemic but asymptomatic transthyretin amyloidosis eight years after domino liver transplantation2011

    • Author(s)
      Koike H, Kiuchi T, Iijima M, Ueda M, Ando Y, Morozumi S, Tomita M, Kawagashira Y, Watanabe H, Katsuno M, Shimoyama Y, Okazaki Y, Kamei H, Sobue G
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto, Japan
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Presentation] Late-onset familial amyloid polyneuropathy in Japan2011

    • Author(s)
      Koike H, Sobue G
    • Organizer
      VIIIth International Symposium on Familial Amyloidotic Polyneuropathy
    • Place of Presentation
      Kumamoto, Japan
    • Year and Date
      2011-11-21
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Presentation] dynactin-1ノックダウンによる孤発性ALS線虫モデルの作成と病態解析2011

    • Author(s)
      池中建介, 勝野雅央, 河合香里, 黄哲, 蒋月梅, 田中章景, 祖父江元
    • Organizer
      第34回日本神経科学大会
    • Place of Presentation
      パシフィコ横浜(神奈川県)
    • Year and Date
      2011-09-17
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Effect of leuprorelin in patients with spinal and bulbar muscular atrophy (SBMA) : a multicenter, randomized, double-blind, placebo-controlled trial2011

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Yabe I, Sasaki H, Aoki M, Morita M, Nakano I, Kanai K, Ito S, Ishikawa K, Mizusawa H, Yamamoto T, Tsuji S, Hasegawa K, Shimohata T, Nishizawa M, Miyajima H, Kanda F, Watanabe Y, Nakashima K, Tsujino A, Yamashita T, Uchino M, Fujimoto Y, Tanaka F, Sobue G; for the Japan SBMA Interventional Trial for TAP-144-SR (JASMITT) study group
    • Organizer
      63rd American Academy of Neurology Annual Meeting
    • Place of Presentation
      Honolulu, USA
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] Molecular pathogenesis and translational research in spinal and bulbar muscular atrophy (SBMA).2011

    • Author(s)
      Sobue G.
    • Organizer
      22th International Symposium on ALS/MND
    • Place of Presentation
      Sydney, Australia
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Cell cycle dysregulation in spinal and bulbar muscular atrophy (SBMA)2011

    • Author(s)
      Katsuno M, Adachi H, Kondo N, Minamiyama M, Doi H, Matsumoto S-J, Miyazaki Y, Tanaka F, Sobue G
    • Organizer
      Gordon conference on CAG triplet repeat disorders
    • Place of Presentation
      Il Ciocco, Italy
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 神経変性疾患におけるdynactin-1と細胞周期関連分子の発現解析.2010

    • Author(s)
      池中建介, 蒋月梅, 田中章景, 勝又竜, 河合香里, 黄哲, 勝野雅央, 山本正彦, 祖父江元
    • Organizer
      第51回日本神経学会総会
    • Place of Presentation
      東京国際フォーラム(東京都)
    • Year and Date
      2010-05-22
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] A peony extract alleviates polyglutamine-mediated motor neuron disease2010

    • Author(s)
      Adachi H, Tohnai G, Katsuno M, Minamiyama M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Tanaka F, Sobue G.
    • Organizer
      Neuroscience 2010
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2010-11-16
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Oxidative stress induces TDP-43 modification, recapitulating its pathological feature.2010

    • Author(s)
      Iguchi Y, Katsuno M, Takagi S, Sobue G.
    • Organizer
      Neuroscience 2010
    • Place of Presentation
      San Diego, USA
    • Year and Date
      2010-11-15
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 神経変性疾患の病態に基づく治療への展望2010

    • Author(s)
      祖父江元
    • Organizer
      平成22年度「包括脳ネットワーク」夏のワークショップ病態脳科学関連ワークショップ「脳疾患研究の新しい潮流」
    • Place of Presentation
      東京
    • Year and Date
      2010-07-28
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Rituximab療法を施行した抗Myelin-Associated-Glycoprotein (MAG)抗体陽性IgM-MGUSニューロパチーの4例2010

    • Author(s)
      川頭祐一(名古屋大学 神経内科),橋本里奈,冨田稔,飯島正博,小池春樹,祖父江元
    • Organizer
      日本末梢神経学会
    • Place of Presentation
      仙台
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Presentation] 球脊髄性筋萎縮症(SBMA)におけるナトリウムチャンネルの発現異常2010

    • Author(s)
      勝野雅央、足立弘明、南山誠、土井英樹、近藤直英、松本慎二郎、坂野晴彦、鈴木啓介、田中章景、祖父江元
    • Organizer
      Neuro2010
    • Place of Presentation
      神戸
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] 多系統萎縮症における経時的なvolumetry・拡散テンソル像の検討~第二報~2010

    • Author(s)
      伊藤瑞規、渡辺宏久、熱田直樹、千田譲、加藤重典、中村亮一、長縄慎二、祖父江元
    • Organizer
      第51回日本神経学会学術大会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-22590955
  • [Presentation] Dynactin-1ノックダウン線虫における神経変性2010

    • Author(s)
      田中章景, 黄哲, 勝又竜, 池中建介, 河合香里, 蒋月梅, 和座雅浩, 勝野雅央, 祖父江元.
    • Organizer
      第51回日本神経学会総会
    • Place of Presentation
      東京国際フォーラム(東京都)
    • Year and Date
      2010-05-22
    • Data Source
      KAKENHI-PROJECT-22390175
  • [Presentation] Molecular targeted therapy for Spinal and Bulbar Muscular Atrophy(SBMA)2010

    • Author(s)
      祖父江元
    • Organizer
      第51回日本神経学会総会シンポジウム「Academia-based development of disease-modifying therapy (アカデミア発の創薬・治療研究)
    • Place of Presentation
      東京
    • Year and Date
      2010-05-21
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy.2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Doi H, Kondo N, Matsumoto S, Miyazaki Y, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Organizer
      21st International Symposium on ALS/MND.
    • Place of Presentation
      Orlando, USA
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] A peony extract alleviates polyglutamine-mediated motor neuron disease.2010

    • Author(s)
      Adachi H, Tohnai G, Katsuno M, Minamiyama M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Tanaka F, Sobue G.
    • Organizer
      Neuroscience 2010
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] A peony extract alleviates polyglutamine-mediated motor neuron disease2010

    • Author(s)
      Adachi H, Tohnai G, Katsuno M, Minamiyama M, Doi H, Matsumoto S, Kondo N, Miyazaki Y, Tanaka F, Ohtsuka K, Sobue G.
    • Organizer
      40th Annual Meeting for the Society for Neuroscience
    • Place of Presentation
      San Diego
    • Year and Date
      2010-11-17
    • Data Source
      KAKENHI-PROJECT-20390243
  • [Presentation] 神経変性疾患の分子標的治療への展開:球脊髄性筋萎縮症について2010

    • Author(s)
      祖父江元
    • Organizer
      第47回日本臨床分子医学会学術集会特別講演
    • Place of Presentation
      東京
    • Year and Date
      2010-04-10
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] シェーグレン症候群に伴うニューロパチー: Ataxic form とPainful formの病理学的特徴2010

    • Author(s)
      川頭祐一(名古屋大学 神経内科),藤岡祐介,冨田稔,両角佐織,飯島正博,小池春樹,祖父江元
    • Organizer
      日本神経免疫学会
    • Place of Presentation
      東京
    • Data Source
      KAKENHI-PROJECT-22590928
  • [Presentation] 球脊髄性筋萎縮症に対する分子標的治療法の開発2010

    • Author(s)
      祖父江元
    • Organizer
      第51回日本神経病理学会総会学術研究会シンポジウム
    • Place of Presentation
      東京
    • Year and Date
      2010-04-23
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Oxidative stress induces TDP-43 modification, recapitulating its pathological feature.2010

    • Author(s)
      Iguchi Y, Katsuno M, Takagi S, Sobue G.
    • Organizer
      Neuroscience 2010
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] Disrupted TGF-beta signaling in spinal and bulbar muscular atrophy.2010

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Doi H, Kondo N, Matsumoto S, Miyazaki Y, Banno H, Suzuki K, Tanaka F, Sobue G.
    • Organizer
      21st International Symposium on ALS/MND.
    • Place of Presentation
      Orlando, USA
    • Year and Date
      2010-12-12
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] パーキンソン病における痛み関連脳電位及び皮質SEPパーキンソン病2010

    • Author(s)
      濱哲夫,原敬史,中村友彦,平山正昭,祖父江元
    • Organizer
      運動障害疾患コングレス
    • Year and Date
      2010-10-07
    • Data Source
      KAKENHI-PROJECT-21600003
  • [Presentation] Morpholo gicale volution of de myelination in Ig M-MGUS anti-MAG associated neuro pathy2009

    • Author(s)
      Kawagashira Y, Tomita M, Morozumi S, Iijima M, Koike H, Hattori N, Sobue G.
    • Organizer
      Peripheral Nerve Society 2009 Biennial Meeting
    • Place of Presentation
      Wurzburg, Germany
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Presentation] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases.2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Organizer
      Neuroscience 2009
    • Place of Presentation
      Chicago, USA
    • Year and Date
      2009-10-17
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa J, Yamada S, Sone J, Waza M, Adachi H, Tanaka F, Nagata K, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Organizer
      Neuroscience 2009
    • Place of Presentation
      Chicago, USA
    • Year and Date
      2009-10-17
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy.2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G.
    • Organizer
      61th American Academy of Neurology Annual Meeting
    • Place of Presentation
      Seattle, USA
    • Year and Date
      2009-04-26
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases2009

    • Author(s)
      Iguchi Y, Katsuno M, Niwa JI, Sone J, Waza M, Adachi H, Tanaka F, Nagata KI, Arimura N, Watanabe T, Kaibuchi K, Sobue G.
    • Organizer
      39th Annual Meeting for the Society for Neuroscience
    • Place of Presentation
      Chicago, IL(一般演題)
    • Year and Date
      2009-10-18
    • Data Source
      KAKENHI-PROJECT-20390243
  • [Presentation] TDP-43 depletion induces neuronal cell damage through dysregulation of Rho family GTPases2009

    • Author(s)
      Iguchi, Y., Katsuno, M., Niwa, J., Yamada, S., Sone, J., Waza, M., Adachi, H., Tanaka, F., Nagata, K., Arimura, N., Watanabe, T., Kaibuchi, K., Sobue G.
    • Organizer
      Neuroscience 2009
    • Place of Presentation
      Chicago, USA
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno, H., Katsuno, M., Suzuki, K., Takeuchi, Y., Kawashima, M., Suga, N., Takamori, M., Ito, M., Nakamura, T., Matsuo, K., Yamada, S., Oki, Y., Adachi, H., Minamiyama, M., Waza, M., Atsuta, N., Watanabe, H., Fujimoto, Y., Nakashima, T., Tanaka, F., Doyu, M., Sobue, G.
    • Organizer
      61th American Academy of Neurology Annual Meeting
    • Place of Presentation
      Seattle, USA
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] Medical induction of stress response alleviates polyglutamine-mediated motor neuron disease The 4th International Congress Responses in Biology and Medicine (CSSI)2009

    • Author(s)
      Tohnai G, Adachi H, Tokui K, Waza M, Katsuno M, Minamiyama M, Doi H, Tanaka F, Ohtsuka K, Sobue G.
    • Organizer
      The 4th Annual Meeting of The Biomedical Society for Stress Response (BSSR)
    • Place of Presentation
      Sapporo(一般演題)
    • Data Source
      KAKENHI-PROJECT-20390243
  • [Presentation] Phase 2 trial of leuprorelin in patients with spinal and bulbar muscular atrophy2009

    • Author(s)
      Banno H, Katsuno M, Suzuki K, Takeuchi Y, Kawashima M, Suga N, Takamori M, Ito M, Nakamura T, Matsuo K, Yamada S, Oki Y, Adachi H, Minamiyama M, Waza M, Atsuta N, Watanabe H, Fujimoto Y, Nakashima T, Tanaka F, Doyu M, Sobue G.
    • Organizer
      61th American Academy of Neurology Annual Meeting
    • Place of Presentation
      Seattle, USA
    • Year and Date
      2009-04-26
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Distinct characteristics of amyloid de posits in early-and late-onset transthyretin Val30 Met fami lial amyloid polyneuropathy2009

    • Author(s)
      Koike H, Ando Y, Ueda M, Kawagashira Y, Iijima M, Fujitake J, Hayashi M, Yamamoto M, Mukai E, Hattori N, Sobue G.
    • Organizer
      Peripheral Nerve Society 2009 Biennial Meeting
    • Place of Presentation
      Wurzburg, Germany
    • Data Source
      KAKENHI-PROJECT-21591076
  • [Presentation] Skeletal muscle involvement in spinal and bulbar muscular atrophy2008

    • Author(s)
      Katsuno M, Kawashima M, Banno H, Suzuki K, Takeuchi Y, Suga N, Adachi H, Tanaka F, Sobue G
    • Organizer
      The 19th International Symposium on ALS/MND
    • Place of Presentation
      Birmingham, UK
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 神経変性疾患の病態抑止治療2008

    • Author(s)
      祖父江元
    • Organizer
      第39回日本内科学会北海道支部生涯教育講演会
    • Place of Presentation
      北海道
    • Year and Date
      2008-06-16
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 神経変性疾患の病態に基づく治療開発.2008

    • Author(s)
      祖父江元
    • Organizer
      第四回神経内科の基礎と臨床
    • Place of Presentation
      京都
    • Year and Date
      2008-11-21
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 神経変性疾患の病態抑止治療2008

    • Author(s)
      祖父江元
    • Organizer
      第39回日本内科学会北海道支部生涯教育講演会
    • Place of Presentation
      北海道
    • Year and Date
      2008-06-16
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] 神経変性疾患の分子標的治療 : 球脊髄性筋萎縮症を中心に2008

    • Author(s)
      祖父江元
    • Organizer
      第49回日本神経病理学会総会学術集会シンポジウムI 「末梢神経・筋疾患の臨床病理-病因解明と治療開発にはたす新たな役割-」
    • Place of Presentation
      東京
    • Year and Date
      2008-05-20
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] 孤発性ALS病態関連分子の探索と疾患モデルの開発2008

    • Author(s)
      田中章景, 和座雅浩, 丹羽淳一, 山本正彦, 祖父江元
    • Organizer
      第49回日本神経学会総会
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-17
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Presentation] 本邦におけるCIDPの現状 全国調査より : 末梢神経2008

    • Author(s)
      飯島正博, 冨田稔, 両角佐織, 川頭祐一, 小池春樹, 服部直樹, 有村公良, 祖父江元
    • Organizer
      第19回日本末梢神経学会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-19590986
  • [Presentation] 孤発性ALS病態関連分子の探索と疾患モデルの開発2008

    • Author(s)
      田中章景、和座雅浩、丹羽淳一、祖父江 元
    • Organizer
      第49回日本神経学会総会シンポジウム
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-17
    • Data Source
      KAKENHI-PROJECT-19390238
  • [Presentation] An oral Hsp90 inhibitor ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2008

    • Author(s)
      Adachi, H., Tokui, K., Waza, M., Katsuno, M., Minamiyama, M., Doi, H., Tanaka, F., Sobue G.
    • Organizer
      Neuroscience 2008
    • Place of Presentation
      Washington DC, USA
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] 分子シャペロンによる神経変性疾患の治療への展望2008

    • Author(s)
      祖父江元
    • Organizer
      日本ハイパーサーミア学会第25回大会
    • Place of Presentation
      名古屋
    • Year and Date
      2008-09-12
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] Dynactin-1ノックダウン線虫モデルの作成2008

    • Author(s)
      和座雅浩、田中章景、蒋月梅、黄哲、勝野雅央、足立弘明、山本正彦、祖父江元
    • Organizer
      第49回日本神経学会総会
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-16
    • Data Source
      KAKENHI-PROJECT-19390238
  • [Presentation] 神経変性疾患の分子標的治療への展望-SBMAを中心に-2008

    • Author(s)
      祖父江元
    • Organizer
      Academic Conference in Tokyo
    • Place of Presentation
      東京
    • Year and Date
      2008-02-07
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 神経変性疾患の分子標的治療 : 球脊髄性筋萎縮症を中心に2008

    • Author(s)
      祖父江元
    • Organizer
      第49回日本神経病理学会総会学術集会シンポジウムI「末梢神経・筋疾患の臨床病理-病因解明と治療開発にはたす新たな役割-」
    • Place of Presentation
      東京
    • Year and Date
      2008-05-20
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 炎症性末梢神経疾患 CIDPの長期予後と治療反応性 : 神経免疫学2008

    • Author(s)
      飯島正博, 両角佐織, 川頭祐一, 小池春樹, 服部直樹, 祖父江元, 有村公良
    • Organizer
      第20回日本神経免疫学会
    • Place of Presentation
      新潟
    • Data Source
      KAKENHI-PROJECT-19590986
  • [Presentation] 孤発性ALS病態関連分子の探索と疾患モデルの開発2008

    • Author(s)
      田中章景、和座雅浩、丹羽淳、祖父江元
    • Organizer
      第49回日本神経学会総会. シンポジウム
    • Place of Presentation
      横浜
    • Year and Date
      2008-05-16
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] CIDPの臨床・電気生理所見の経過 : 臨床神経2008

    • Author(s)
      飯島正博, 両角佐織, 川頭祐一, 小池春樹, 服部直樹, 有村公良, 祖父江元
    • Organizer
      第49回日本神経学会総会
    • Place of Presentation
      横浜
    • Data Source
      KAKENHI-PROJECT-19590986
  • [Presentation] 分子シャペロンによる神経変性疾患の治療への展望2008

    • Author(s)
      祖父江元
    • Organizer
      日本ハイパーサーミア学会第25回大会
    • Place of Presentation
      名古屋
    • Year and Date
      2008-09-12
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] 神経変性疾患の病態に基づく治療開発2008

    • Author(s)
      祖父江元
    • Organizer
      第四回神経内科の基礎と臨床
    • Place of Presentation
      京都
    • Year and Date
      2008-11-21
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 神経変性疾患の分子標的治療 : 球脊髄性筋萎縮症を中心に.2008

    • Author(s)
      祖父江元
    • Organizer
      第49回日本神経病理学会総会学術集会シンポジウムI「末梢神経・筋疾患の臨床病理一病因解明と治療開発にはたす新たな役割-」
    • Place of Presentation
      東京
    • Year and Date
      2008-05-20
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 神経変性疾患の病態に基づく治療開発2008

    • Author(s)
      祖父江元
    • Organizer
      第四回神経内科の基礎と臨床
    • Place of Presentation
      京都
    • Year and Date
      2008-11-21
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] 分子シャペロンによる神経変性疾患の治療への展望.2008

    • Author(s)
      祖父江元
    • Organizer
      日本ハイパーサーミア学会第25回大会
    • Place of Presentation
      名古屋
    • Year and Date
      2008-09-12
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] An oral Hsp90 inhibitor ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2008

    • Author(s)
      Adachi H, Tokui K, Waza M, Katsuno M, Minamiyama M, Doi H, Tanaka F, Sobue G
    • Organizer
      Neuroscience 2009
    • Place of Presentation
      Washington DC, USA
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] An oral Hsp9O inhibitor ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model2008

    • Author(s)
      Adachi H, Tokui K, Katsuno M, Minamiyama M, Doi H, Tanaka F, Sobue G.
    • Organizer
      第38回The Society for Neuroscience Annual meeting
    • Place of Presentation
      Washington DC(一般演題)
    • Data Source
      KAKENHI-PROJECT-20390243
  • [Presentation] Reversible dysfunction in polyglutamine disease2007

    • Author(s)
      Sobue G
    • Organizer
      Neuro2007
    • Place of Presentation
      Yokohama, Japan
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] Translational approaches for polyglutamine disease2007

    • Author(s)
      Sobue G
    • Organizer
      第4回21世紀COE国際シンポジウム(The 21st century center for excellence (COE) program 4th international symposium on functional molecules linked to neurodegeneration and oncogenesis-toward molecular targeted therapy-)
    • Place of Presentation
      Nagoya, Japan
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] Mutant SOD1 and protein aggregation/degradation in motoneuronal cells2007

    • Author(s)
      Sobue G
    • Organizer
      Mutant SOD1 and familial ALS : from molecule to man
    • Place of Presentation
      Milano, Italy
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 神経変性疾患の病態抑止治療2007

    • Author(s)
      祖父江元
    • Organizer
      第48回日本神経学会総会 シンポジウム「神経変性疾患の動物モデル」
    • Place of Presentation
      名古屋
    • Year and Date
      2007-05-16
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] CIDPの臨床経過と重症度分布 : 臨床神経学2007

    • Author(s)
      飯島正博, 川頭祐一, 沖祐美子, 小池春樹, 服部直樹, 祖父江元, 有村公良
    • Organizer
      第48回日本神経学会総会
    • Place of Presentation
      名古屋
    • Data Source
      KAKENHI-PROJECT-19590986
  • [Presentation] 分子シャペロンによる神経変性疾患の治療への展望2007

    • Author(s)
      祖父江元
    • Organizer
      第2回臨床ストレス応答学会大会ランチョンセミナー
    • Place of Presentation
      福岡
    • Year and Date
      2007-11-30
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] 慢性炎症性脱髄性多発ニューロパチー(CIDP)全国調査続報 経過および重症度を中心に : 神経免疫学2007

    • Author(s)
      飯島正博, 川頭祐一, 沖祐美子, 松尾幸治, 木村正剛, 小池春樹, 服部直樹, 有村公良, 祖父江元
    • Organizer
      第19回日本神経免疫学会
    • Place of Presentation
      金沢
    • Data Source
      KAKENHI-PROJECT-19590986
  • [Presentation] 孤発性ALS疾患モデルの開発 : dynactin1ノックダウン細胞の解析2007

    • Author(s)
      田中章景、黄哲、蒋月梅、松尾幸治、和座雅浩、山本正彦、道勇学、祖父江元
    • Organizer
      第48回日本神経学会総会
    • Place of Presentation
      名古屋
    • Year and Date
      2007-05-16
    • Data Source
      KAKENHI-PROJECT-19390238
  • [Presentation] CHIP overexpression reduces the mutant AR protein and ameliorates phenotypes of the SBMA transgenic mouse model2007

    • Author(s)
      Adachi H, Waza M, Tokui K, Katsuno M, Tanaka F, Sobue G
    • Organizer
      Neuroscience 2007
    • Place of Presentation
      San Diego, USA
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] Myocardial involvement in spinal and bulbar muscular atrophy2007

    • Author(s)
      Katsuno M, Banno H, Suzuki K, Takeuchi Y, Kawashima M, Tanaka F, Sobue G
    • Organizer
      18th International symposium on ALS/MND
    • Place of Presentation
      Toronto, Canada
    • Data Source
      KAKENHI-PROJECT-19209033
  • [Presentation] CHIP over-expression reduces the mutant AR protein and ameliorates phenotypes of the SBMA transgenic mouse model2007

    • Author(s)
      Adachi, H, Waza, M, Tokui, K, Katsuno, M, Minamiyama, M. Tanaka, F, Sobue, G
    • Organizer
      The 49th Annual Meeting of the Japanese Society of Neurology
    • Place of Presentation
      Nagoya
    • Year and Date
      2007-05-17
    • Description
      「研究成果報告書概要(欧文)」より
    • Data Source
      KAKENHI-PROJECT-18599002
  • [Presentation] 変異SOD1と特異的に結合するタンパク質の探索同定2007

    • Author(s)
      丹羽淳一、山田新一、曽根淳、高橋美穂、道勇学、祖父江元
    • Organizer
      第48回日本神経学会総会
    • Place of Presentation
      名古屋
    • Year and Date
      2007-05-17
    • Data Source
      KAKENHI-PROJECT-19590987
  • [Presentation] Gen expression profile of spinal motor neurons in sporadic amyotrophic lateral sclerosis2006

    • Author(s)
      Tanaka, F., Jiang, Y.M., Yamamoto, M., Huang, Z., Katsuno, M., Adachi, H., Niwa, J.I., Doyu, M., Sobue, G.
    • Organizer
      17th International Symposium on ALS/MND
    • Place of Presentation
      Yokohama, Japan
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] Reversible disruption of retrograde axonal transport in spinal and bulbar muscular atrophy2006

    • Author(s)
      Katsuno, M., Adachi, H., Minamiyama, M., Waza, M., Tokui, K., Jiang, Y.M., Banno, H., Suzuki, K., Tanaka, F., Sobue, G.
    • Organizer
      17th International Symposium on ALS/MND
    • Place of Presentation
      Yokohama, Japan
    • Data Source
      KAKENHI-PROJECT-17025020
  • [Presentation] 神経変性疾患の病体抑止治療を目指して

    • Author(s)
      祖父江 元
    • Organizer
      第35回日本神経科学大会特別講演
    • Place of Presentation
      名古屋国際会議場(名古屋)
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] dynactin-1ノックアウトマウスを用いた孤発性ALSの病態解析

    • Author(s)
      河合香里、池中建介、勝野雅央、井口洋平、勝又竜、田中章景、祖父江元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡国際会議場(福岡県福岡市)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-26461269
  • [Presentation] Oxdative stress maker (urinary 8-hydroxy-2-deoxyguanosine) was modified by treatment of various Parkinson’s drug

    • Author(s)
      Masaaki Hirayama, Sae Goto, Tomohiko Nakamura, Yasuaki Mizutani, Jun-ichiro Suzuki, Hirohisa Watanabe, Gen Sobue
    • Organizer
      18th International Congress of Parkinson's Disease and Movement Disorder
    • Place of Presentation
      Stockholmsmassen
    • Year and Date
      2014-06-08 – 2014-06-12
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] 運動ニューロン病研究の進歩と治療への展望

    • Author(s)
      祖父江 元
    • Organizer
      第109回日本内科学会講演会
    • Place of Presentation
      みやこめっせ(京都)
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] FAP ATTR Val30Metの末梢神経病変の超微形態学的検討

    • Author(s)
      小池春樹、高橋美江、大山健、橋本里奈、川頭祐一、飯島正博、祖父江元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡県福岡市(福岡国際会議場)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] サルコイドーシスによる末梢神経障害の病理学的特徴

    • Author(s)
      高橋美江、小池春樹、飯島正博、大山健、橋本里奈、川頭祐一、祖父江 元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡県福岡市(福岡国際会議場)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 脱髄性ニューロパチーにおけるランビエ絞輪部周辺のチャネル、接着分子の分布異常(口演)

    • Author(s)
      川頭祐一、高橋美江、大山健、橋本里奈、飯島正博、小池春樹、祖父江元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡県福岡市(福岡国際会議場)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] TAG-1ノックアウトによる再髄鞘化機転への影響と軸索脆弱性の解析

    • Author(s)
      飯島正博、小池春樹、川頭祐一、橋本里奈、大山健、高橋美江、祖父江元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡県福岡市(福岡国際会議場)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] MORPHOLOGY OF NONMYELINATING SCHWANN CELLS IN CHRONIC INFLAMMATORY DEMYELINATING POLYNEUROPATHY

    • Author(s)
      Haruki Koike, Mie Takahashi, Ken Ohyama, Yuichi Kawagashira, Masahiro Iijima, and Gen Sobue
    • Organizer
      Inflammatory Neuropathy Consortium
    • Place of Presentation
      Germany, Dusserdorf, Hyatt Regency
    • Year and Date
      2014-07-13 – 2014-07-16
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] パーキンソン病における痛み関連脳電位と認知機 能との関連性

    • Author(s)
      岡田 暁典, 鈴木 淳一郎, 水谷 泰彰, 中村 友彦, 平山 正昭, 祖父江 元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡国際会議場
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] Leptin and ghrelin concentrations and cardiovascular dysautonomia in Parkinson’s disease

    • Author(s)
      Tomohiko Nakamura, Suzuki Masashi, Akinori Okada, Junichiro Suzuki, Sarotu Hasegawa, Masaaki Hirayama, Gen Sobue
    • Organizer
      4th Asian and Oceanian Parkinson's Disease and Movement Disorders Congress
    • Place of Presentation
      Pattaya, Thailand,at the Pattaya Exhibition and Conventon Hall
    • Year and Date
      2014-11-28 – 2014-11-30
    • Data Source
      KAKENHI-PROJECT-24590691
  • [Presentation] Androgen-dependent deficits in muscle-derived BDNF correlate with motor dysfunction in two mouse models of spinal bulbar muscular atrophy.

    • Author(s)
      Halievski K, Xu Y, Henley CL, Katsuno M, Adachi H, Sobue G, Breedlove S, Jordan CL.
    • Organizer
      Neuroscience 2014
    • Place of Presentation
      Washington DC, USA
    • Year and Date
      2014-11-15 – 2014-11-19
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] 球脊髄性筋萎縮症に対する抗アンドロゲン療法.

    • Author(s)
      勝野雅央, 祖父江 元.
    • Organizer
      第53回日本神経学会学術大会シンポジウム
    • Place of Presentation
      東京国際フォーラム(東京)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] 運動ニューロン疾患における耐糖能異常の解析.

    • Author(s)
      荒木周, 中辻秀朗, 勝野雅央, 鈴木啓介, 坂野晴彦, 須賀徳明, 橋詰淳, 土方靖浩, 祖父江 元.
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡県福岡市(福岡国際会議場)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-26670440
  • [Presentation] The involvement of glial cells in FUS-related ALS/FTLD pathophysiology -FUS knock-down glial cells have a neuro-protective effect.

    • Author(s)
      Fujioka Y, Ishigaki S, Shiromizu T,, Udagawa T, Honda D, Yokoi S, Ikenaka K, Katsuno M, Tomonaga T, Sobue G
    • Organizer
      Neuroscience 2014
    • Place of Presentation
      Washington DC, USA
    • Year and Date
      2014-11-15 – 2014-11-19
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] 神経変性疾患のトランスレーショナルリサーチ

    • Author(s)
      勝野雅央, 坂野晴彦, 鈴木啓介, 橋詰 淳, 足立弘明, 田中章景, 祖父江 元.
    • Organizer
      第109回日本内科学会総会・講演会シンポジウム「わが国のトランスレーショナルリサーチとEBM」
    • Place of Presentation
      みやこめっせ(京都)
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP ATTR Val30Met)の末梢神経病変の超微形態学的検討

    • Author(s)
      小池春樹、高橋美江、大山健、橋本里奈、川頭祐一、飯島正博、祖父江元
    • Organizer
      第55回日本神経病理学会総会学術研究会
    • Place of Presentation
      東京都千代田区(学術総合センター)
    • Year and Date
      2014-06-05 – 2014-06-07
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 運動ニューロン特異的TDP-43ノックアウトマウスの病理学的検討

    • Author(s)
      井口洋平, 勝野雅央, 丹羽淳一, 高木伸之介, 山中宏二, 三澤日出巳, 高橋良 輔, 佐々木彰一, 田中章景, 祖父江元
    • Organizer
      第54回日本神経学会学術大会
    • Place of Presentation
      東京国際フォーラム(東京都千代田)
    • Year and Date
      2013-05-29 – 2013-06-01
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Presentation] パーキンソン病の心血管系自律神経障害におけるグレリン、レプチンの関与の検討

    • Author(s)
      中村 友彦 ,鈴木 将史 ,岡田 暁典 ,鈴木 淳一郎 ,長谷川 聖 ,平山 正昭 ,祖父江 元
    • Organizer
      第8回パーキンソン病・運動障害疾患コングレス
    • Place of Presentation
      京都府京都市(京都ホテルオークラ)
    • Year and Date
      2014-10-02 – 2014-10-04
    • Data Source
      KAKENHI-PROJECT-24590691
  • [Presentation] 家族性アミロイドポリニューロパチー(FAP ATTR Val30Met)の末梢神経病変の超微形態学的検討

    • Author(s)
      小池春樹、高橋美江、大山健、橋本里奈、川頭祐一、飯島正博、祖父江元
    • Organizer
      第25回日本末梢神経学会学術集会
    • Place of Presentation
      京都府京都市(ルビノ京都堀川)
    • Year and Date
      2014-08-29 – 2014-08-30
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] Atypical parkinsonism focusing on natural history of MSA.

    • Author(s)
      Sobue G.
    • Organizer
      20th World Congress of Neurology
    • Place of Presentation
      Marrakesh, Morocco
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 慢性炎症性脱髄性多発神経炎(CIDP)における筋萎縮の検討(ポスター)

    • Author(s)
      大山健、小池春樹、勝野雅央、高橋美江、川頭祐一、飯島正博、渡辺宏久、祖父江元
    • Organizer
      第26回日本神経免疫学会
    • Place of Presentation
      石川県金沢市(金沢歌劇座)
    • Year and Date
      2014-09-14 – 2014-09-16
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] ALSの進行を規定する因子の探索同定

    • Author(s)
      熱田直樹、渡辺はづき、中村亮一、平川晃弘、中杤昌弘、渡辺宏久、伊藤瑞規、千田譲、和泉唯信、梶龍兒、森田光哉、富山弘幸、谷口彰、溝口功一、狩野修、阿部康二、中野今治、飯田有俊、池川志郎、祖父江元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡国際会議場(福岡市)
    • Data Source
      KAKENHI-PROJECT-25461277
  • [Presentation] Androgen-dependent deficits in muscle-derived BDNF correlate with motor dysfunction in two mouse models of spinal bulbar muscular atrophy.

    • Author(s)
      Halievski K, Xu Y, Henley CL, Katsuno M, Adachi H, Sobue G, Breedlove S, Jordan CL
    • Organizer
      Neuroscience 2014
    • Place of Presentation
      Washington DC, USA
    • Year and Date
      2014-11-15 – 2014-11-19
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] 抗MAG抗体陽性ニューロパチーにおけるランビエ絞輪部周辺のイオンチャンネル、接着分子の分布異常(口演)

    • Author(s)
      川頭祐一、高橋美江、大山健、飯島正博、小池春樹、祖父江元
    • Organizer
      第25回日本末梢神経学会学術集会
    • Place of Presentation
      京都府京都市(ルビノ京都堀川)
    • Year and Date
      2014-08-29 – 2014-08-30
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] Muscle Atrophy in Chronic Inflammatory Demyelinating Polyneuropathy: A Computed Tomography Assessment (Poster)

    • Author(s)
      Ken Ohyama, Haruki Koike, Masahisa Katsuno, Mie Takahashi, Rina Hashimoto, Yuichi Kawagashira, Masahiro Iijima, Hiroaki Adachi, and Gen Sobue
    • Organizer
      Inflammatory Neuropathy Consortium
    • Place of Presentation
      Germany, Dusserdorf, Hyatt Regency
    • Year and Date
      2014-07-13 – 2014-07-16
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] アミノ酸系除草剤グリホサートカリウム塩による過敏性血管炎に伴う末梢神経障害の1例(ポスター)

    • Author(s)
      川頭祐一、川畑和也、高橋美江、大山健、橋本里奈、飯島正博、小池春樹、祖父江元
    • Organizer
      第25回日本末梢神経学会学術集会
    • Place of Presentation
      京都府京都市(ルビノ京都堀川)
    • Year and Date
      2014-08-29 – 2014-08-30
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] パーキンソン病では早期から嗅覚機能と心血管系自律神経機能が並行して障害される

    • Author(s)
      水谷 泰彰, 岡田 暁典, 鈴木 淳一郎, 中村 友彦, 平山 正昭, 祖父江 元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡国際会議場
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] MRI脳容積・拡散テンソル画像を用いた前頭側頭型認知症における大脳病変の解析

    • Author(s)
      桝田道人、陸雄一、坪井崇、原一洋、渡辺はづき、中村亮一、千田譲、伊藤瑞規、熱田直樹、渡辺宏久、祖父江元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡県福岡市(福岡国際会議場)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-25461313
  • [Presentation] 神経変性疾患の病態抑止治療への展望

    • Author(s)
      祖父江 元
    • Organizer
      第46回日本内科学会中国支部生涯教育講演会
    • Place of Presentation
      出雲医師会館(出雲)
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Neuropathy associated with primary systemic vasculitides.

    • Author(s)
      Sobue G.
    • Organizer
      The Asian Pacific Meeting of Vasculitis and ANCA Workshop 2012
    • Place of Presentation
      Tokyo, Japan
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] 顕微鏡的多発血管炎に伴うニューロパチーと非全身性血管炎性ニューロパチーの臨床病理学的対比

    • Author(s)
      高橋美江、小池春樹、飯島正博、大山健、橋本里奈、川頭祐一、祖父江 元
    • Organizer
      第25回日本末梢神経学会学術集会
    • Place of Presentation
      京都府京都市(ルビノ京都堀川)
    • Year and Date
      2014-08-29 – 2014-08-30
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 脳容積・拡散テンソル解析での筋萎縮性側索硬化症と前頭側頭葉変性症の共通性障害

    • Author(s)
      千田 譲, 桝田 道人, 陸 雄一, 今井 和憲, 川畑 和也, 伊藤 瑞規, 熱田 直樹, 渡辺 宏久, 祖父江 元
    • Organizer
      第33回日本認知症学会学術大会
    • Place of Presentation
      神奈川県横浜市(パシフィコ横浜)
    • Year and Date
      2014-11-29 – 2014-12-01
    • Data Source
      KAKENHI-PROJECT-25461313
  • [Presentation] MRI大脳容積画像を用いた前頭側頭型認知症とアルツハイマー型認知症の鑑別

    • Author(s)
      桝田 道人, 今井 和憲, 陸 雄一, 千田 譲, 伊藤 瑞規, 熱田 直樹, 渡辺 宏久, 祖父江 元
    • Organizer
      第33回日本認知症学会学術大会
    • Place of Presentation
      神奈川県横浜市(パシフィコ横浜)
    • Year and Date
      2014-11-29 – 2014-12-01
    • Data Source
      KAKENHI-PROJECT-25461313
  • [Presentation] 球脊髄性筋萎縮症(SBMA)におけるインスリン抵抗性と運動機能の関連.

    • Author(s)
      中辻秀朗, 荒木 周, 勝野雅央, 鈴木啓介, 坂野晴彦, 須賀徳明, 橋詰 淳, 土方靖浩, 祖父江元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡県福岡市(福岡国際会議場)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-26670440
  • [Presentation] ニューロパチーの病態におけるIgG4の意義(口演)

    • Author(s)
      大山健、小池春樹、飯島正博、高橋美江、橋本里奈、川頭祐一、祖父江元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡県福岡市(福岡国際会議場)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 多系統萎縮症の末梢血管抵抗の反応性:Head-up tilt, ノルアドレナリン負荷試験を通して

    • Author(s)
      鈴木淳一郎, 水谷 泰彰, 中村 友彦, 平山 正昭, 祖父江 元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡国際会議場
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] POEMS症候群における表皮内神経線維密度(口演)

    • Author(s)
      大山健、橋本里奈、高橋美江、川頭祐一、飯島正博、小池春樹、祖父江元
    • Organizer
      第25回日本末梢神経学会学術集会
    • Place of Presentation
      京都府京都市(ルビノ京都堀川)
    • Year and Date
      2014-08-29 – 2014-08-30
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 球脊髄性筋萎縮症患者の進行に対する各種薬剤の影響.

    • Author(s)
      勝野雅央, 鈴木啓介, 坂野晴彦, 須賀徳明, 橋詰 淳, 荒木 周, 土方靖浩, 祖父江 元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡県福岡市(福岡国際会議場)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-26670440
  • [Presentation] Muscle Atrophy in Chronic Inflammatory Demyelinating Polyneuropathy: A Computed Tomography Assessment

    • Author(s)
      Ken Ohyama, Haruki Koike, Masahisa Katsuno, Mie Takahashi, Rina Hashimoto, Yuichi Kawagashira, Masahiro Iijima, Hiroaki Adachi, and Gen Sobue
    • Organizer
      Inflammatory Neuropathy Consortium
    • Place of Presentation
      Hyatt Regency Hotel, Dusseldorf, Germany
    • Year and Date
      2014-07-13 – 2014-07-16
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Presentation] 神経疾患のdisease modifying therapyへの展開

    • Author(s)
      祖父江 元
    • Organizer
      包括型脳科学研究推進支援ネットワーク 夏のワークショップ 脳科学研究戦略推進プログラム・包括脳合同企画
    • Place of Presentation
      仙台国際センター(仙台)
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] MORPHOLOGY OF NONMYELINATING SCHWANN CELLS IN CHRONIC INFLAMMATORY DEMYELINATING POLYNEUROPATHY

    • Author(s)
      Haruki Koike, Mie Takahashi, Ken Ohyama, Yuichi Kawagashira, Masahiro Iijima, and Gen Sobue
    • Organizer
      Inflammatory Neuropathy Consortium
    • Place of Presentation
      Hyatt Regency Hotel, Dusseldorf, Germany
    • Year and Date
      2014-07-13 – 2014-07-16
    • Data Source
      KAKENHI-PROJECT-25461276
  • [Presentation] Leptin and ghrelin concentrations and cardiovascular dysautonomia in Parkinson’s disease

    • Author(s)
      Tomohiko Nakamura, Yui Okada, Akinori Okada, Junichiro Suzuki, Yasuaki Mizutani, Masaaki Hirayama, Gen Sobue
    • Organizer
      18th International Congress of Parkinson's Disease and Movement Disorders
    • Place of Presentation
      Stockholm, Sweden,Stockholmsmassen (Stockholm Convention Centre)
    • Year and Date
      2014-06-08 – 2014-06-12
    • Data Source
      KAKENHI-PROJECT-24590691
  • [Presentation] 尿中8-OHdGを用いたパーキンソン病における酸化的ストレスの変化の検討

    • Author(s)
      平山 正昭, 中村 友彦, 鈴木 淳一郎, 渡邊 宏久, 祖父江 元
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡国際会議場
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-24500458
  • [Presentation] ALSの神経病理とオミックス

    • Author(s)
      祖父江 元
    • Organizer
      第52回日本神経病理学会総会学術研究会シンポジウム「オミックスサイエンスの展開と神経病理学」
    • Place of Presentation
      京都テルサ(京都)
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Molecular pathogenesis and therapy of polyglutamine-induced motor neuron degeneration.

    • Author(s)
      Katsuno M, Adachi H, Minamiyama M, Doi H, Kondo N, Miyazaki Y, Iida M, Tanaka F, Sobue G.
    • Organizer
      35th Annual Meeting of the Japan Neuroscience Society.
    • Place of Presentation
      名古屋国際会議場(名古屋)
    • Invited
    • Data Source
      KAKENHI-PROJECT-23390230
  • [Presentation] 高度の神経肥厚を特徴とするCIDPの臨床的検討(口演)

    • Author(s)
      飯島正博、小池春樹、川頭祐一、大山 健、高橋 美江、祖父江 元
    • Organizer
      第25回日本末梢神経学会学術集会
    • Place of Presentation
      京都府京都市(ルビノ京都堀川)
    • Year and Date
      2014-08-29 – 2014-08-30
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] The blood-spinal cord barrier is temporarily impaired in TDP-43 conditional knockout mice.

    • Author(s)
      Sasaki S, Iguchi Y, Katsuno M, Sobue G.
    • Organizer
      The 13th International Congress on Neuromuscular Diseases.
    • Place of Presentation
      Nice, France
    • Year and Date
      2014-07-05 – 2014-07-10
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] Sporadic ALS: Search for pathogenesis and therapeutic approach.

    • Author(s)
      Sobue G.
    • Organizer
      20th World Congress of Neurology
    • Place of Presentation
      Marrakesh, Morocco
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] Analysis of major amyotrophic lateral sclerosis genes in Japan

    • Author(s)
      Nakamura R, Sone J, Atsuta N, Watanabe H, Hirakawa A, Watanabe H, Ito M, Senda J, Katsuno K, Tanaka F, Izumi Y, Morita M, Ogaki K, Taniguchi A, Aiba A, Mizoguchi K, Okamoto K, Hasegawa K, Aoki M, Kawata A, Abe K, Oda M, Konagaya M, Imai T, Nakagawa M, Tsuji S, Kaji R, Nakano I, Sobue G
    • Organizer
      64th Annual Meeting of the American Society of Human Genetics
    • Place of Presentation
      San Diego Convention Center, San Diego, CA, USA
    • Year and Date
      2014-10-18 – 2014-10-22
    • Data Source
      KAKENHI-PLANNED-22129005
  • [Presentation] 神経変性疾患のdisease-modifying therapyへの展望

    • Author(s)
      祖父江 元
    • Organizer
      フォーラム2012衛生薬学・環境トキシコロジー 特別講演
    • Place of Presentation
      名古屋観光ホテル(名古屋)
    • Invited
    • Data Source
      KAKENHI-PROJECT-21229011
  • [Presentation] The involvement of glial cells in FUS-related ALS/FTLD pathophysiology -FUS knock-down glial cells have a neuro-protective effect.

    • Author(s)
      Fujioka Y, Ishigaki S, Shiromizu T,, Udagawa T, Honda D, Yokoi S, Ikenaka K, Katsuno M, Tomonaga T, Sobue G
    • Organizer
      Neuroscience 2014
    • Place of Presentation
      Washington DC, USA
    • Year and Date
      2014-11-15 – 2014-11-19
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] SBMA motor dysfunction may be due to failed neuromuscular transmission.

    • Author(s)
      Xu, Atchison W, Adachi H, Katsuno M, Sobue G, Breedlove S, Jordan CL.
    • Organizer
      Neuroscience 2014
    • Place of Presentation
      Washington DC, USA
    • Year and Date
      2014-11-15 – 2014-11-19
    • Data Source
      KAKENHI-PLANNED-22110005
  • [Presentation] SBMA motor dysfunction may be due to failed neuromuscular transmission.

    • Author(s)
      Xu, Atchison W, Adachi H, Katsuno M, Sobue G, Breedlove S, Jordan CL
    • Organizer
      Neuroscience 2014
    • Place of Presentation
      Washington DC, USA
    • Year and Date
      2014-11-15 – 2014-11-19
    • Data Source
      KAKENHI-PROJECT-26293206
  • [Presentation] EANによる脱髄に伴う軸索障害機序の解明(口演)

    • Author(s)
      飯島正博、小池春樹、川頭祐一、大山 健、高橋 美江、祖父江 元
    • Organizer
      第26回日本神経免疫学会
    • Place of Presentation
      石川県金沢市(金沢歌劇座)
    • Year and Date
      2014-09-14 – 2014-09-16
    • Data Source
      KAKENHI-PROJECT-25461278
  • [Presentation] 球脊髄性筋萎縮症におけるクレアチン代謝異常.

    • Author(s)
      土方靖浩,勝野雅央,鈴木啓介,坂野晴彦,須賀徳明,橋詰淳,荒木周,祖父江元.
    • Organizer
      第55回日本神経学会学術大会
    • Place of Presentation
      福岡県福岡市(福岡国際会議場)
    • Year and Date
      2014-05-21 – 2014-05-24
    • Data Source
      KAKENHI-PROJECT-26670440
  • [Presentation] The blood-spinal cord barrier is temporarily impaired in TDP-43 conditional knockout mice.

    • Author(s)
      Sasaki S, Iguchi Y, Katsuno M, Sobue G
    • Organizer
      The 13th International Congress on Neuromuscular Diseases.
    • Place of Presentation
      Nice, France
    • Year and Date
      2014-07-05 – 2014-07-10
    • Data Source
      KAKENHI-PLANNED-22110005
  • []

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  • 256.  深田 優子
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